KEGG   Vicugna pacos (alpaca): 102531254
Entry
102531254         CDS       T08098                                 
Symbol
BCKDHB
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
  KO
K00167  2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
Organism
vpc  Vicugna pacos (alpaca)
Pathway
vpc00280  Valine, leucine and isoleucine degradation
vpc00640  Propanoate metabolism
vpc00785  Lipoic acid metabolism
vpc01100  Metabolic pathways
vpc01210  2-Oxocarboxylic acid metabolism
Brite
KEGG Orthology (KO) [BR:vpc00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    102531254 (BCKDHB)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    102531254 (BCKDHB)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    102531254 (BCKDHB)
Enzymes [BR:vpc01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     102531254 (BCKDHB)
SSDB
Motif
Pfam: Transket_pyr Transketolase_C
Other DBs
NCBI-GeneID: 102531254
NCBI-ProteinID: XP_015103458
UniProt: A0A6J0AZB4
LinkDB
Position
8
AA seq 392 aa
MAAVPVAACRLLRLRAAGAEGHWRRLRGAGLPRAFLQPPSADADATQRREVAHFTFQPDP
EPLEYGQTQKMNLFQAVTSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRSPWGCVGHGALYHSQSPEAFFAHCPGIKVVVPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAVEQVPIEPYNIPLSQAEVIQEGSDVTLVAWGTQVHVIREVASMAQEKLGVSCE
VIDLRTILPWDVDTVCKSVVKTGRLLVSHEAPLTGGFASEISSTVQEECFLNLEAPISRV
CGYDTPFPHIFEPFYIPDKWKCYDALRKMINY
NT seq 1179 nt   +upstreamnt  +downstreamnt
atggcggcggtgccggtggctgcgtgccggctgctgcggctccgtgcggcaggggctgag
ggacactggcgtcggctccgtggcgcggggctgccgcgggccttcctgcagcccccctcg
gccgacgcggatgcgacccagaggcgggaggtggctcacttcactttccagcccgacccg
gagcccctggagtacgggcaaactcagaaaatgaatctcttccaggcagtaacaagtgcc
ttggataactcgttggccaaagatcctactgcagtaatattcggtgaagatgttgccttt
ggcggagtctttcgatgtactgttggcttgcgagacaagtatggtaaagatagagtattt
aataccccattgtgcgaacaaggaattgttggctttggaattggaattgcagtcactggt
gctactgccattgcggaaattcagtttgcagattatattttccctgctttcgatcagatt
gttaatgaagctgccaagtaccgctatcgctctggggacctttttaattgtggaagcctc
accatccggtccccttggggctgtgtcggccacggggctctctatcactctcagagtcct
gaagcgttttttgcccactgcccaggcatcaaggtggttgtacccagaagccctttccag
gccaaaggacttcttttgtcatgcatagaggataaaaatccttgtatattttttgaacct
aaaatactttacagggcagcagtggagcaggttcccatagaaccatacaacatccccttg
tcccaagccgaggtcatccaggaagggagtgatgttacgctcgttgcctggggcactcag
gttcatgtgatccgagaggtggcttccatggctcaagagaagctaggagtgtcttgtgaa
gtcattgatctgaggactatactaccttgggatgtggatacagtttgcaagtctgtggtc
aaaacagggcgactgctagtcagtcatgaagctcccttgactggcggctttgcttcagag
atcagctccacggttcaggaagaatgtttcctgaacctggaggctcctatctcaagagtg
tgtgggtatgacaccccgttccctcacatttttgagccgttctacatcccagataaatgg
aagtgctatgacgccctccgaaaaatgatcaactattga

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