KEGG   Xiphophorus maculatus (southern platyfish): 102219548
Entry
102219548         CDS       T02923                                 
Symbol
bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
xma  Xiphophorus maculatus (southern platyfish)
Pathway
xma00280  Valine, leucine and isoleucine degradation
xma00640  Propanoate metabolism
xma00785  Lipoic acid metabolism
xma01100  Metabolic pathways
xma01210  2-Oxocarboxylic acid metabolism
Module
xma_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:xma00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    102219548 (bckdha)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    102219548 (bckdha)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    102219548 (bckdha)
Enzymes [BR:xma01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     102219548 (bckdha)
SSDB
Motif
Pfam: E1_dh DXP_synthase_N TPP_enzyme_C
Other DBs
NCBI-GeneID: 102219548
NCBI-ProteinID: XP_005796899
Ensembl: ENSXMAG00000007649
UniProt: M3ZZN7
LinkDB
Position
18:complement(5400759..5413108)
AA seq 447 aa
MAAVSGMSRISGLCRHAVRQTAALKTPRLLQRRSFIVTAVQQQQQPFDSSLEKPQFPGAS
AEFVDRLEFIQPNVISGIPVYRVMDRQGNIINPSEDPQLSKETVLNFYQKMTLLNTMDRI
LYESQRQGRISFYMTNYGEEGTHIGSAAALESNDLVFGQYREAGVLMYRGFPLDLFMAQC
YANADDLGKGRQMPVHYGCKDLHFVTISSPLATQIPQAAGAAYALKRENMNRAVICYFGE
GAASEGDAHAGFNFSATLECPLIFFCRNNGYAISTPTNEQYRGDGIAARGPGYGMLSIRV
DGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQD
HPISRLRHYMTARGWWSEDDERSWRKQSRKTVMEAFEKAERRLKPNPELLFTDVYQEMNP
TLAKQRESLFRHIQQYKEHYPLDLYEK
NT seq 1344 nt   +upstreamnt  +downstreamnt
atggcggctgttagcggtatgagcagaatatctgggttatgtcgtcatgctgttcggcaa
acggctgcactgaagacgccgaggctgctgcagcgtcggtccttcatagttactgctgta
cagcagcagcagcagccctttgactcgtctctggaaaagccccagtttcctggcgcctca
gcagagtttgtggaccgtcttgaattcattcagcccaatgttatttctgggattcccgtg
taccgggtgatggacaggcagggcaacataatcaacccctctgaggacccccagctctcc
aaagagacggttctaaacttctaccagaaaatgacgctgctgaacacgatggaccggatt
ctctacgagtctcagagacagggtcgaatctccttctacatgaccaactacggagaggag
gggacgcacatcggcagcgctgcagctctcgagtctaatgatttggtttttggtcaatac
agagaagctggagtgctgatgtaccgcggtttccccctggatctgttcatggctcagtgc
tacgccaacgccgacgaccttgggaagggccgccagatgcctgtccactacggctgcaaa
gatctgcacttcgtcaccatctcgtctcctctggccacgcagattcctcaggcggcggga
gctgcgtacgcgctgaagagggagaacatgaaccgcgcggtgatctgttacttcggggag
ggagcggccagcgaaggggacgcacacgccggcttcaacttctcagcgaccctcgagtgt
ccgctgatcttcttctgtcgcaacaacggctacgcgatctccaccccgaccaacgagcag
tacagaggcgacggcatcgctgctagagggcctggttatggcatgctgtccatccgtgtc
gatggaaacgacgtgttcgccgtctacaacgccacaaaggaagcgcggcgcagggctgtg
gctgaaaaccagcctttccttatcgaggcgatgacttacagaatcgggcatcacagcacc
agcgacgacagctcggcctaccgctccgtggacgaggtgaactattgggacaagcaggac
caccccatctcccggctcaggcactacatgacggcgcgcggctggtggagcgaggacgac
gagcgcagctggaggaaacagtcacgcaagactgtgatggaggcgtttgagaaggcggag
aggcgcctgaagcccaacccagagctgctgtttaccgacgtctaccaggaaatgaacccc
accctggccaagcagagagagtccctcttcaggcacatccagcagtacaaagagcactac
cccctcgacctgtacgagaaataa

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