Xiphophorus maculatus (southern platyfish): 102219548
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Entry
102219548 CDS
T02923
Symbol
bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
xma
Xiphophorus maculatus (southern platyfish)
Pathway
xma00280
Valine, leucine and isoleucine degradation
xma00640
Propanoate metabolism
xma00785
Lipoic acid metabolism
xma01100
Metabolic pathways
xma01210
2-Oxocarboxylic acid metabolism
Module
xma_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
xma00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
102219548 (bckdha)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
102219548 (bckdha)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
102219548 (bckdha)
Enzymes [BR:
xma01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
102219548 (bckdha)
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Motif
Pfam:
E1_dh
DXP_synthase_N
TPP_enzyme_C
Motif
Other DBs
NCBI-GeneID:
102219548
NCBI-ProteinID:
XP_005796899
Ensembl:
ENSXMAG00000007649
UniProt:
M3ZZN7
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Position
18:complement(5400759..5413108)
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AA seq
447 aa
AA seq
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MAAVSGMSRISGLCRHAVRQTAALKTPRLLQRRSFIVTAVQQQQQPFDSSLEKPQFPGAS
AEFVDRLEFIQPNVISGIPVYRVMDRQGNIINPSEDPQLSKETVLNFYQKMTLLNTMDRI
LYESQRQGRISFYMTNYGEEGTHIGSAAALESNDLVFGQYREAGVLMYRGFPLDLFMAQC
YANADDLGKGRQMPVHYGCKDLHFVTISSPLATQIPQAAGAAYALKRENMNRAVICYFGE
GAASEGDAHAGFNFSATLECPLIFFCRNNGYAISTPTNEQYRGDGIAARGPGYGMLSIRV
DGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQD
HPISRLRHYMTARGWWSEDDERSWRKQSRKTVMEAFEKAERRLKPNPELLFTDVYQEMNP
TLAKQRESLFRHIQQYKEHYPLDLYEK
NT seq
1344 nt
NT seq
+upstream
nt +downstream
nt
atggcggctgttagcggtatgagcagaatatctgggttatgtcgtcatgctgttcggcaa
acggctgcactgaagacgccgaggctgctgcagcgtcggtccttcatagttactgctgta
cagcagcagcagcagccctttgactcgtctctggaaaagccccagtttcctggcgcctca
gcagagtttgtggaccgtcttgaattcattcagcccaatgttatttctgggattcccgtg
taccgggtgatggacaggcagggcaacataatcaacccctctgaggacccccagctctcc
aaagagacggttctaaacttctaccagaaaatgacgctgctgaacacgatggaccggatt
ctctacgagtctcagagacagggtcgaatctccttctacatgaccaactacggagaggag
gggacgcacatcggcagcgctgcagctctcgagtctaatgatttggtttttggtcaatac
agagaagctggagtgctgatgtaccgcggtttccccctggatctgttcatggctcagtgc
tacgccaacgccgacgaccttgggaagggccgccagatgcctgtccactacggctgcaaa
gatctgcacttcgtcaccatctcgtctcctctggccacgcagattcctcaggcggcggga
gctgcgtacgcgctgaagagggagaacatgaaccgcgcggtgatctgttacttcggggag
ggagcggccagcgaaggggacgcacacgccggcttcaacttctcagcgaccctcgagtgt
ccgctgatcttcttctgtcgcaacaacggctacgcgatctccaccccgaccaacgagcag
tacagaggcgacggcatcgctgctagagggcctggttatggcatgctgtccatccgtgtc
gatggaaacgacgtgttcgccgtctacaacgccacaaaggaagcgcggcgcagggctgtg
gctgaaaaccagcctttccttatcgaggcgatgacttacagaatcgggcatcacagcacc
agcgacgacagctcggcctaccgctccgtggacgaggtgaactattgggacaagcaggac
caccccatctcccggctcaggcactacatgacggcgcgcggctggtggagcgaggacgac
gagcgcagctggaggaaacagtcacgcaagactgtgatggaggcgtttgagaaggcggag
aggcgcctgaagcccaacccagagctgctgtttaccgacgtctaccaggaaatgaacccc
accctggccaagcagagagagtccctcttcaggcacatccagcagtacaaagagcactac
cccctcgacctgtacgagaaataa
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