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  Mitochondrial Biogenesis - Anopheles gambiae (malaria mosquito)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 85940932 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 85940915 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 85940922 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 85940929 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 85940908 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 85940928 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 85940931 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 85940910 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 85940918 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 85940919 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 85940904 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 85940921 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 85940903 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 1278185 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 1277472 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 1280551 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 1281454 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 1281504 translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 1280385 translation initiation factor IF-3 K02520 infC; translation initiation factor IF-3 D 1280189 elongation factor Ts, mitochondrial isoform X2 K02357 tsf; elongation factor Ts D 1270103 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 1274806 elongation factor Tu K02358 tuf; elongation factor Tu D 1278061 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 1279146 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 1274239 transcription termination factor 5, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 1279843 transcription termination factor, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 1280534 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 133393210 uncharacterized protein LOC133393210 K15031 MTERF; mitochondrial transcription termination factor family protein D 1279391 translation factor GUF1 homolog, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 5668019 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 1280926 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 1276628 uncharacterized protein LOC1276628 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 1277497 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 3290606 ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 1269864 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 1272435 ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 1269920 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 1272787 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 1281154 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 3291558 uncharacterized protein LOC3291558 K17658 TEFM; transcription elongation factor, mitochondrial D 1276723 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 3290322 pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 1279178 small ribosomal subunit protein mS39 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 1269517 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 1279286 putative ATPase N2B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 1278928 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 1270921 ATP-dependent RNA helicase SUV3 homolog, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 1274081 beta-lactamase-like protein 2 homolog K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 1270282 ADP,ATP carrier protein 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 1273606 ADP,ATP carrier protein 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 4576278 mitoferrin K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 1275767 uncharacterized protein LOC1275767 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 1271336 GTPase Era, mitochondrial K03595 era; GTPase D 1272264 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 1272950 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 1277687 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 1281104 leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 1278116 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 1275455 glycine--tRNA ligase isoform X2 K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 1278518 probable arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 1279516 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 1270907 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 1272824 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 11175511 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 1279775 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 1280034 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 1278489 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 1279694 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 3291733 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 1269720 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 1281845 uncharacterized protein LOC1281845 K23496 NGRN; neugrin D 1281037 pseudouridylate synthase TRUB2, mitochondrial K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 5667405 uncharacterized protein LOC5667405 K18190 FASTKD2; FAST kinase domain-containing protein 2 D 5667395 FAST kinase domain-containing protein 3, mitochondrial K27755 FASTKD3; FAST kinase domain-containing protein 3 D 1281046 FAST kinase domain-containing protein 3, mitochondrial K27756 TBRG4; FAST kinase domain-containing protein 4 D 5666756 uncharacterized protein LOC5666756 K27757 FASTKD5; FAST kinase domain-containing protein 5 D 133390941 mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor D 1273130 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 1273554 MYG1 exonuclease K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 1270498 mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 1272128 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 1270476 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 C Mitochondrial DNA maintenance factors D 1278115 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 1275306 mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 1272521 mitochondrial DNA helicase K17680 PEO1; twinkle protein [EC:5.6.2.3] D 1278190 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 1273482 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 1281323 ATPase family AAA domain-containing protein 3A homolog K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 11175696 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 1277953 mitochondrial Rho GTPase isoform X2 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 1275756 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 133391047 heat shock protein 70 A1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 133391048 heat shock protein 70 A1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 133391192 heat shock protein 70 A1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 133391326 heat shock protein 70 A1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 4397608 heat shock protein 70 A1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 5667627 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 1272316 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein D 1280952 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 4578431 mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 1280364 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 1276077 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 1273376 mitochondrial import receptor subunit TOM40 homolog 2 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 1278084 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 1271413 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 C TOB/SAM complex D 11175826 SAM50-like protein CG7639 K07277 SAM50; outer membrane protein insertion porin family C Porin D 1279252 voltage-dependent anion-selective channel K15040 VDAC2; voltage-dependent anion channel protein 2 C ERMES complex C Other outer membrane factor D 1277812 metaxin-2 K17776 MTX; metaxin D 1278799 metaxin-1 homolog K17776 MTX; metaxin D 1272285 mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] D 1272286 mitochondrial amidoxime reducing component 2 isoform X4 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 1272373 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 133390929 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 4576533 mitochondrial import inner membrane translocase subunit Tim10B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 1275330 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 1269282 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 1273025 mitochondrial intermembrane space import and assembly protein 40-B K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 3290174 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 1273598 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 1274785 MICOS complex subunit MIC13 homolog QIL1 K24624 MICOS13; MICOS complex subunit MIC13 D 1271881 uncharacterized protein LOC1271881 K17563 CHCHD3; MICOS complex subunit MIC19 D 1273178 MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 1273598 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 1273871 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 1279632 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 1277310 mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 1275435 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 1282055 mitochondrial import inner membrane translocase subunit TIM50-C K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 1276945 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 4578197 calcium uptake protein 1 homolog, mitochondrial isoform X2 K22827 MICU1; calcium uptake protein 1, mitochondrial D 1270642 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial C Other inner membrane factors D 1279756 mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 3290502 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 1269784 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 1277413 uncharacterized protein LOC1277413 K18157 TMEM126A; transmembrane protein 126A D 1281759 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 1275713 mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 1269610 OCIA domain-containing protein 1 K28215 OCIAD1; OCIA domain-containing protein 1 B Matrix C MMC/PAM proteins D 1271968 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 1275400 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 1271080 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 1268932 grpE protein homolog, mitochondrial K03687 GRPE; molecular chaperone GrpE D 1274190 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 11175691 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 1277865 mitochondrial-processing peptidase subunit alpha isoform X2 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 1270421 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 1276241 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 1281408 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 1269518 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 1278824 heat shock protein 60A K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 1281670 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 1269663 protein tumorous imaginal discs, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 5667045 chaperone protein DnaJ K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 1274087 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 1276078 DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 1275013 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 1282013 polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 3289643 cyclic AMP response element-binding protein B isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 1278061 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 1279146 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 133392824 transcriptional repressor protein YY1 K09201 YY; transcription factor YY D 1276996 ankyrin repeat and sterile alpha motif domain-containing protein 1B K09454 GABPB; GA-binding protein transcription factor, beta D 1277472 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 1273469 DNA-binding protein Ewg isoform X1 K11831 NRF1; nuclear respiratory factor 1 C Coactivators D 1274509 uncharacterized protein LOC1274509 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 1272249 histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 1280047 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 1276480 iron-sulfur cluster assembly scaffold protein IscU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 4576796 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 1272401 frataxin homolog, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 1273888 adrenodoxin-like protein 2, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 1270266 adrenodoxin-like protein 1, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 1276117 NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 1271080 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 1278506 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB D 1270944 nucleotide exchange factor Sil1 K14001 SIL1; nucleotide exchange factor SIL1 D 1273462 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 1273238 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 1279503 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 133393865 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 1271629 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 1274383 bolA-like protein DDB_G0274169 K22066 BOLA1; BolA-like protein 1 D 1278449 bolA-like protein 3 isoform X1 K22075 BOLA3; BolA-like protein 3 D 1274665 sideroflexin-1-3 K23500 SFXN1_3; sideroflexin-1/3 D 1269987 sideroflexin-2 isoform X2 K23501 SFXN2; sideroflexin-2 C Other regulator of mitochondrial biogenesis D 1279583 carnitine O-palmitoyltransferase 1, liver isoform isoform X2 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 1271673 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial isoform X1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 1271769 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 1280501 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 1278452 host cell factor isoform X1 K14966 HCFC1; host cell factor 1 D 4576838 huntingtin isoform X1 K04533 HD; huntingtin D 1273276 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 1272588 lon protease homolog, mitochondrial isoform X1 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 1268369 uncharacterized protein LOC1268369 isoform X1 K23504 SERAC1; protein SERAC1 D 1269460 protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 1270893 protein UXT homolog K26537 UXT; protein UXT D 1273001 transport and Golgi organization protein 2 K28098 TANGO2; transport and Golgi organization protein 2 D 1272193 mitochondrial protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69 D 1279329 protein Atossa isoform X1 K28528 ATOS; protein Atossa D 1279222 ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7] B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 1277355 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 4577778 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 1271559 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 1269604 protein NDUFAF4 homolog isoform X2 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 1271116 arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 1271934 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 homolog K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 1275716 protein arginine methyltransferase NDUFAF7 homolog, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 133393905 uncharacterized protein LOC133393905 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 1270387 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 1271781 complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 1279796 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 1280035 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 1270737 reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 1280134 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 1281750 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 1280494 succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 1274111 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 1277919 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 1270200 complex III assembly factor LYRM7 isoform X2 K18170 LYRM7; complex III assembly factor LYRM7 D 1269517 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 11175696 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 1275776 uncharacterized protein LOC1275776 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 1280003 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 133392888 ubiquinol-cytochrome c reductase complex assembly factor 6 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 C Complex-IV assembly factors D 5668175 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 1273507 COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 1276810 uncharacterized protein LOC1276810 K18173 COA1; cytochrome c oxidase assembly factor 1 D 133392915 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 133393656 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 1280827 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 11175644 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 133393866 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7 D 1279852 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 1272595 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 1281430 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 1272980 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 3291440 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 5667359 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18 D 1280676 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 5668172 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 1276120 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 1277131 SURF1-like protein K14998 SURF1; surfeit locus 1 family protein D 1275633 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 1281543 probable transcriptional regulatory protein TTE1135 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 1275629 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 1281076 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 1280003 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 1274829 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 D 1272515 HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 1271749 HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial C Complex-V assembly factors D 1275874 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 1279845 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 1275710 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 5667225 ATP synthase membrane subunit K, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 1281313 transmembrane GTPase Marf isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 1270645 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 1281776 putative OPA3-like protein CG13603 isoform X2 K23166 OPA3; optic atrophy 3 protein D 1278805 TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 1273337 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 1279863 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 1279269 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 1277365 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 1281474 small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier D 1272668 endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1 D 1270122 mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 1281428 transport and Golgi organization protein 11 isoform X2 K22076 MFF; mitochondrial fission factor D 1276804 ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 1280948 mitoguardin K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 1274770 actin, muscle K05692 ACTB_G1; actin beta/gamma 1 D 1275975 actin-87E K05692 ACTB_G1; actin beta/gamma 1 D 1281498 actin, muscle-type A2 K05692 ACTB_G1; actin beta/gamma 1 D 133392886 actin, indirect flight muscle-like K05692 ACTB_G1; actin beta/gamma 1 D 133393145 actin-1 K05692 ACTB_G1; actin beta/gamma 1 D 133393485 actin-5C K05692 ACTB_G1; actin beta/gamma 1 D 1281245 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 1281170 phagocyte signaling-impaired protein K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 1271235 prohibitin 1 K17080 PHB1; prohibitin 1 D 1279019 prohibitin-2 isoform X1 K17081 PHB2; prohibitin 2 C Retention of mitochondria D 1279863 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 1277086 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V C Morphogenesis factors D 1277426 sorting nexin-25 K17887 SNX25; sorting nexin-25 D 1277953 mitochondrial Rho GTPase isoform X2 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 1273598 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 1281571 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 1277407 small ribosomal subunit protein mS29 K17408 DAP3; small subunit ribosomal protein S29 D 1272379 E3 ubiquitin-protein ligase Nedd-4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 1273805 E3 ubiquitin-protein ligase Nedd-4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 1273191 protein misato K27320 MSTO1; protein misato D 3291200 protein preli-like K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial D 1277924 protein slowmo K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial B Mitophagy factors C Autophagy-related proteins D 1274010 autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 1271177 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 1277474 cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 1278841 cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 1271014 autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 1271595 beclin-1-like protein K08334 BECN; beclin D 4578408 uncharacterized protein LOC4578408 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 1273277 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 1281414 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 1270419 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 1269871 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12 D 1273655 autophagy-related protein 16-1 K17890 ATG16L1; autophagy-related protein 16-1 D 1276577 WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 D 1277979 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 1277163 E3 ubiquitin-protein ligase parkin isoform X2 K04556 PARK2; parkin [EC:2.3.2.31] D 1281240 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 1273188 protein CLEC16A homolog K19513 CLEC16A; protein CLEC16A D 1274459 serine/threonine-protein kinase Pink1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 1273337 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] C Parkin-independent mechanism factors D 1276385 autophagy-related protein 13 homolog isoform X2 K08331 ATG13; autophagy-related protein 13 D 1270635 serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 1279842 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 1270125 heat shock protein 83-like K04079 HSP90A; molecular chaperone HtpG D 1270127 heat shock protein 83-like K04079 HSP90A; molecular chaperone HtpG D 1270128 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG D 1281212 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 1270684 E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 1277468 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 1273276 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 1275738 tectonin beta-propeller repeat-containing protein isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 1281077 zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 1276153 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 1278413 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 1271813 protein C19orf12 homolog K23168 MPAN; protein MPAN ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025