+D
#
Mitochondrial Biogenesis - Acanthopagrus latus (yellowfin seabream)
%
!
AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 119028734 polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 119009650 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 119005126 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 119018491 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 119027641 mtif2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 119012604 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 119020879 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 119013374 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 119029674 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 119032347 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 119011396 mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 119017057 mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 119017149 transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 119025063 mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 119032197 transcription termination factor 2, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 119008048 guf1; translation factor Guf1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 119006152 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 119006129 pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 119019061 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 119010053 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 119027481 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 119006839 rpp25l; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 119017707 uncharacterized protein LOC119017707 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 119024170 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 119005503 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 119011401 rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 119018578 trmt10c; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 119022692 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 119034406 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 119009870 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 119009872 putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 119021250 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 119021774 ptcd1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 119030031 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 119007069 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 119010742 dhx30; ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 119021413 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 119004996 afg1la; AFG1 like ATPase a K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 119012213 afg1lb; lactation elevated protein 1 homolog B isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 119032337 atp23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 119018800 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 119011336 lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 119007288 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 119023274 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 119031444 si:dkey-251i10.1; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 119019183 mitoferrin-2-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 119019962 slc25a37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 119033507 slc25a28; mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 119005544 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 119031860 eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 119016556 yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 119023779 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 119006479 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 119031123 leucine--tRNA ligase, cytoplasmic-like K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 119011714 dars2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 119008946 gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 119008961 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 119012367 rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 119031738 rars1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 119005078 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 119020392 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 119020188 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 119008522 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 119021493 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 119033954 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 119007282 noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 119018280 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 119011279 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 119020824 mitochondrial RNA pseudouridine synthase rpusd4-like K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 119031785 rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 119022229 ngrn; neugrin K23496 NGRN; neugrin
D 119021613 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 119025523 fastkd1; FAST kinase domain-containing protein 1, mitochondrial K27754 FASTKD1; FAST kinase domain-containing protein 1
D 119015615 fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 119008761 fastkd3; FAST kinase domain-containing protein 3, mitochondrial K27755 FASTKD3; FAST kinase domain-containing protein 3
D 119005674 tbrg4; FAST kinase domain-containing protein 4 K27756 TBRG4; FAST kinase domain-containing protein 4
D 119025983 FAST kinase domain-containing protein 5, mitochondrial K27757 FASTKD5; FAST kinase domain-containing protein 5
D 119019849 c5h12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor
D 119005143 rmnd1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 119019346 grsf1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1
D 119017973 mettl15; probable methyltransferase-like protein 15 isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 119021673 myg1; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 119004510 mtres1; mitochondrial transcription rescue factor 1 isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 119024421 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 119026717 polg2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2
D 119019389 primpol; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 119019359 endog; endonuclease G, mitochondrial isoform X1 K01173 ENDOG; endonuclease G, mitochondrial
D 119033163 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 119009352 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 119011278 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 119032211 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 119020807 atad3; ATPase family AAA domain containing 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 119023348 ATPase family AAA domain-containing protein 3-A-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 119021423 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 119009745 si:dkey-21c1.4; uncharacterized protein C17orf80 homolog K27759 MTNAP1; mitochondrial nucleoid-associated protein 1
#
AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 119017988 dnaja2a; dnaJ homolog subfamily A member 2a K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 119024601 dnaja2b; dnaJ homolog subfamily A member 2b K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 119021489 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 119014276 rhot1a; mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 119021201 rhot1b; mitochondrial Rho GTPase 1b isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 119005818 hsc70; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119013548 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119013549 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119022925 hspa1b; heat shock 70 kDa protein 1B K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119030964 hspa8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119034488 hspa8b; heat shock protein family A (Hsp70) member 8b K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119007421 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 119019859 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
D 119034372 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 119007122 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
D 119021424 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 119017430 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 119024222 tomm20b; mitochondrial import receptor subunit TOM20 homolog B K17770 TOM20; mitochondrial import receptor subunit TOM20
D 119033066 tomm20a; translocase of outer mitochondrial membrane 20 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 119009471 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 119006771 tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 119016749 tomm40l; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 119031106 si:dkey-71l1.1; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 119028904 tomm70a; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
C TOB/SAM complex
D 119023959 samm50; sorting and assembly machinery component 50 homolog A isoform X1 K07277 SAM50; outer membrane protein insertion porin family
D 119032744 samm50l; sorting and assembly machinery component 50 homolog B isoform X1 K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 119031553 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 119009719 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2
D 119033916 vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 119019040 vdac3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
D 119029867 zgc:56235; voltage-dependent anion-selective channel protein 2 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 119005861 mtx1a; metaxin-1a K17776 MTX; metaxin
D 119019003 mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 119034171 mtx2; metaxin-2 isoform X1 K17776 MTX; metaxin
D 119031572 unconventional myosin-XIX K25838 MYO19; myosin XIX
D 119005140 marc1; mitochondrial amidoxime-reducing component 1 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 119004303 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 119021130 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 119031938 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 119006929 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 119011632 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 119028994 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 119021915 chchd4b; coiled-coil-helix-coiled-coil-helix domain containing 4b K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 119021960 chchd4a; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 119014546 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 119020849 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 119023449 micos10; MICOS complex subunit MIC10 isoform X1 K17784 MICOS10; MICOS complex subunit MIC10
D 119007871 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
D 119028539 micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 119024355 proline-rich extensin-like protein EPR1 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 119032401 chchd3a; coiled-coil-helix-coiled-coil-helix domain containing 3a isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 119021433 chchd6b; coiled-coil-helix-coiled-coil-helix domain containing 6b isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 119023294 chchd6a; MICOS complex subunit mic25a isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 119009099 apoob; apolipoprotein O, b isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 119011793 LOW QUALITY PROTEIN: MICOS complex subunit MIC26-like K24625 APOO; MICOS complex subunit MIC26
D 119007029 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 119020849 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 119023449 micos10; MICOS complex subunit MIC10 isoform X1 K17784 MICOS10; MICOS complex subunit MIC10
D 119007871 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 119031672 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 119010372 timm23a; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 119021821 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 119022440 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 119008589 timm21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 119004349 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 119033611 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 119033521 micu1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 119031102 micu2; calcium uptake protein 2, mitochondrial isoform X1 K22828 MICU2; calcium uptake protein 2, mitochondrial
D 119018263 calcium uniporter regulatory subunit MCUb, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 119026783 calcium uniporter protein, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 119014278 essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial
D 119021516 smdt1b; single-pass membrane protein with aspartate-rich tail 1b K22830 SMDT1; essential MCU regulator, mitochondrial
D 119008450 mcur1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 119004481 letm1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 119018377 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 119025130 immp2l; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 119007000 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 119017796 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 119026285 mpc2b; mitochondrial pyruvate carrier 2b K22139 MPC2; mitochondrial pyruvate carrier 2
D 119021733 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial isoform X1 K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
D 119018581 OCIA domain-containing protein 1-like K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 119011525 mitochondrial import inner membrane translocase subunit TIM44-like isoform X1 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 119028427 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 119007302 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 119027121 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 119029278 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 119014442 pam16; mitochondrial import inner membrane translocase subunit tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 119019502 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 119032855 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 119010273 mitochondrial intermediate peptidase-like K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 119025307 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 119014438 dnaja3a; dnaJ heat shock protein family (Hsp40) member A3a isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 119028346 dnaJ homolog subfamily A member 3, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 119020969 tamm41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 119029772 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 119006749 ethe1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 119004398 poldip2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
#
AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 119015544 cyclic AMP-responsive element-binding protein 1-like isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 119026205 creb1b; cyclic AMP-responsive element-binding protein 1b K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 119029674 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 119032347 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 119020987 sp1; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 119004537 yy1a; transcriptional repressor protein YY1a K09201 YY; transcription factor YY
D 119012482 yy1b; transcriptional repressor protein YY1b isoform X1 K09201 YY; transcription factor YY
D 119017294 gabpb2a; GA-binding protein subunit beta-2a K09454 GABPB; GA-binding protein transcription factor, beta
D 119009650 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 119032737 nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 119022555 nfe2; transcription factor NF-E2 45 kDa subunit K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 119025482 nfe2l2a; nuclear factor erythroid 2-related factor 2a K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 119024361 mt2; metallothionein-2 K14739 MT1_2; metallothionein 1/2
C Coactivators
D 119027281 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 119007364 ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 119016725 si:dkey-93h22.8; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 119033196 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 119011299 crtc1a; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 119028304 crtc1b; CREB-regulated transcription coactivator 1b isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 119007182 crebbpa; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 119009531 ep300a; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 119013337 ep300b; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 119014113 crebbpb; CREB binding protein b isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 119021603 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 119019142 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 119029563 iron-sulfur cluster assembly scaffold protein IscU-like K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 119009129 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 119019423 fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 119015421 fdx1; adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial
D 119020772 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 119010381 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 119007302 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 119020125 hscb; iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 119007851 sil1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 119012402 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 119020120 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 119005191 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 119011192 iba57; putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 119019567 nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 119033035 zgc:110319; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 119006523 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 119017770 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 119007216 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 119033513 sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 119009480 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2
D 119033326 sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4
D 119004670 sfxn5a; sideroflexin-5a K23503 SFXN5; sideroflexin-5
D 119008128 sfxn5b; sideroflexin-5b isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 119009379 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 119013880 cpt1cb; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 119024059 cpt1ab; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 119024968 cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 119024840 dhtkd1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 119006456 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 119020508 hcfc1a; host cell factor 1a K14966 HCFC1; host cell factor 1
D 119023057 host cell factor 1-like K14966 HCFC1; host cell factor 1
D 119032608 hcfc2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2
D 119026077 htt; huntingtin isoform X1 K04533 HD; huntingtin
D 119031524 esrra; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 119012713 steroid hormone receptor ERR2-like isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 119034453 esrrb; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 119005344 esrrd; steroid hormone receptor ERR2 K08554 NR3B3; estrogen-related receptor gamma
D 119012913 estrogen-related receptor gamma-like isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 119018486 esrrga; estrogen-related receptor gamma a isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 119031237 nrip1b; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 119028669 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 119030122 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 119028929 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 119033184 sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 119012164 serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 119023233 uxt; protein UXT K26537 UXT; protein UXT
D 119008144 si:ch211-153b23.5; glutamine amidotransferase-like class 1 domain-containing protein 3A, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 119019053 es1; ES1 protein, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 119025715 zgc:162944; glutamine amidotransferase-like class 1 domain-containing protein 3A, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 119019058 tango2; transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2
D 119026247 c9h2orf69; UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69
D 119017877 fam214a; protein FAM214A isoform X1 K28528 ATOS; protein Atossa
D 119018991 protein FAM214B K28528 ATOS; protein Atossa
D 119014810 ddx47; probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7]
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 119034399 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 119019966 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 119020844 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 119012049 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 isoform X1 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 119024081 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 119006030 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 119012639 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 119009425 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 119027535 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 119021247 acad9; complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 119004807 nubpl; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 119031476 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 119005079 rtn4ip1; reticulon-4-interacting protein 1 homolog, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 119012160 reticulon-4-interacting protein 1 homolog, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 119015435 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 119019176 sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 119018374 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 119026141 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 119011571 ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 119033444 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 119021413 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 119021423 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 119019447 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 119009783 c20h16orf91; protein CCSMST1 isoform X1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 119023624 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 119023966 c8h12orf73; protein BRAWNIN isoform X1 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 119032302 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 119005619 cmc1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 119018264 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 119010939 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 119010182 cytochrome c oxidase assembly factor 3 homolog, mitochondrial isoform X1 K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 119014627 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 119030740 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 119026295 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 119032162 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 119028949 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 119010196 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 119009786 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 119021572 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 119033697 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 119034502 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 119025469 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 119007331 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18
D 119009854 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 119033600 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 119009870 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 119009872 putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 119014814 protein PET100 homolog, mitochondrial isoform X1 K18186 PET100; protein PET100, animal type
D 119024239 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 119027476 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 119030370 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 119014654 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 119032522 protein SCO2 homolog, mitochondrial isoform X1 K23755 SCO2; protein SCO2
D 119009345 translational activator of cytochrome c oxidase 1 isoform X1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 119033397 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 119004407 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1
D 119032302 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 119023624 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 119025732 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
D 119011457 higd1a; HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 119007594 higd2a; HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial
C Complex-V assembly factors
D 119029162 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 119009411 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 119011620 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 119011999 atp5mpl; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 119016593 atp5md; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 119027586 ATP synthase membrane subunit DAPIT, mitochondrial-like isoform X1 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 119011918 mfn1a; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 119028849 mfn1b; mitofusin-1b isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 119022817 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 119028620 opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 119034332 opa3; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 119004394 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 119011114 parla; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 119013528 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 119013666 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 119014265 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 119017934 zgc:153993; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 119018977 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 119024569 dnm1l; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 119032296 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 119027297 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 119004811 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 119013875 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 119015285 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 119025512 sumo3b; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 119027081 sumo2a; small ubiquitin like modifier 2a K12160 SUMO; small ubiquitin-related modifier
D 119004479 endophilin-B1-like K11248 SH3GLB1; endophilin-B1
D 119008764 sh3glb1a; endophilin-B1a K11248 SH3GLB1; endophilin-B1
D 119017664 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 119022947 mitochondrial carrier homolog 1-like isoform X1 K17885 MTCH; mitochondrial carrier
D 119010930 mitochondrial fission factor homolog A-like isoform X1 K22076 MFF; mitochondrial fission factor
D 119030320 mffa; mitochondrial fission factor homolog B isoform X1 K22076 MFF; mitochondrial fission factor
D 119008542 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 119022356 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 119010128 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 119013448 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 119013683 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 119025396 mief2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 119021361 pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 119011544 miga1; mitoguardin 1 K27289 MIGA; mitoguardin
D 119029956 miga2; mitoguardin 2 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 119009432 actb1; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 119013388 actb2; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 119020270 actin, non-muscle 6.2 isoform X1 K05692 ACTB_G1; actin beta/gamma 1
D 119012307 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 119029790 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 119013449 phb; prohibitin K17080 PHB1; prohibitin 1
D 119010677 phb2a; prohibitin-2a K17081 PHB2; prohibitin 2
D 119034222 ktn1; kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 119018977 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 119024569 dnm1l; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 119032296 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 119018000 myo5aa; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
D 119024808 unconventional myosin-Va-like K10357 MYO5; myosin V
D 119024810 myo5c; unconventional myosin-Vc isoform X1 K10357 MYO5; myosin V
D 119028400 si:dkey-110c1.10; unconventional myosin-Vb K10357 MYO5; myosin V
D 119029680 myo5b; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 119007067 E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 119011837 diablo homolog, mitochondrial-like K10522 DIABLO; diablo
D 119011846 diabloa; diablo, IAP-binding mitochondrial protein a isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 119007792 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25
D 119014276 rhot1a; mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 119021201 rhot1b; mitochondrial Rho GTPase 1b isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 119007871 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
D 119030340 mtfp1; mitochondrial fission process protein 1 isoform X1 K17981 MTFP1; mitochondrial fission process protein 1
D 119006818 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 119018038 nedd4a; E3 ubiquitin-protein ligase NEDD4a isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 119005854 oxr1a; oxidation resistance protein 1a isoform X1 K25437 OXR1; oxidation resistance protein 1
D 119016740 msto1; protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato
D 119006934 prelid1a; PRELI domain containing 1a K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 119018217 PRELI domain-containing protein 1, mitochondrial-like K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 119026738 PRELI domain-containing protein 1, mitochondrial-like isoform X1 K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 119021481 prelid3b; PRELI domain containing protein 3B K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
D 119022327 PRELI domain containing protein 3B-like isoform X1 K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 119005189 atg2b; autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2
D 119008092 atg2a; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 119015342 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 119014531 cysteine protease ATG4D-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 119027529 atg4da; cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 119028380 atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 119029148 atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 119006095 atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 119009417 becn1; beclin-1 K08334 BECN; beclin
D 119021834 atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 119006400 zgc:92606; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 119017806 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 119024929 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 119027794 gabarapa; GABA(A) receptor-associated protein a K08341 GABARAP; GABA(A) receptor-associated protein
D 119004999 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 119010918 atg9b; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 119011911 atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 119006399 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 119005214 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 119031272 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 119011178 protein Atg16l2-like isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 119009335 WD repeat domain phosphoinositide-interacting protein 1-like K17908 WIPI1_2; autophagy-related protein 18
D 119014485 wipi2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
D 119014576 wipi1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 119005230 ankar; ankyrin and armadillo repeat-containing protein K08332 VAC8; vacuolar protein 8
C Parkin-dependent mechanism factors
D 119033279 prkn; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 119022368 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 119013342 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 119022791 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 119011114 parla; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 119013528 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 119007148 sqstm1; sequestosome-1 K14381 SQSTM1; sequestosome 1
D 119006287 tax1bp1b; tax1-binding protein 1 homolog B isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 119015437 tax1bp1a; tax1-binding protein 1 homolog A K21347 TAX1BP1; Tax1-binding protein 1
D 119009564 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 119024226 ambra1b; activating molecule in BECN1-regulated autophagy protein 1b isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 119015627 atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 119019164 ulk1a; serine/threonine-protein kinase ULK1a K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 119029738 ulk1b; serine/threonine-protein kinase ULK1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 119033636 ulk2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 119010749 rb1cc1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 119012297 hsp90ab1; heat shock protein HSP 90-beta isoform X1 K04079 HSP90A; molecular chaperone HtpG
D 119012301 hsp90aa1.2; heat shock protein 90, alpha (cytosolic), class A member 1, tandem duplicate 2 K04079 HSP90A; molecular chaperone HtpG
D 119012302 hsp90aa1.1; heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG
D 119014638 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 119017211 cdc37; hsp90 co-chaperone Cdc37 isoform X1 K09554 CDC37; cell division cycle protein 37
D 119014273 smurf2; E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 119014286 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 119023193 E3 ubiquitin-protein ligase SMURF2-like K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 119019330 bnip3la; BCL2 interacting protein 3 like a K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 119029584 bnip3lb; BCL2 interacting protein 3 like b K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 119015662 FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
D 119026127 fundc1; FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 119028669 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 119030122 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 119007552 map1lc3cl; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 119020853 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 119024228 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 119024750 map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 119009559 nbr1a; NBR1 autophagy cargo receptor a K17987 NBR1; next to BRCA1 gene 1 protein
D 119014978 nbr1b; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 119009845 tecpr1a; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 119013690 tecpr1b; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 119005947 si:ch211-11n16.2; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 119012179 zfyve1; zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 119034428 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 119009848 coasy; bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 119025764 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 119018175 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 119018551 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 119024419 zgc:112052; protein C19orf12 homolog K23168 MPAN; protein MPAN
!
#
#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025