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  Mitochondrial Biogenesis - Austrofundulus limnaeus (annual killifish)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 106511533 LOW QUALITY PROTEIN: NADH-ubiquinone oxidoreductase chain 5-like K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III C Cytochrome c oxidase C F-type ATPase B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 106515001 polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 106511210 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial D 106518988 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 106519091 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 106510857 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 106536926 mtif2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 106522417 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3 D 106518039 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 106528137 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 106511067 gfm2; LOW QUALITY PROTEIN: ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 106533309 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 106510823 ribosome-releasing factor 2, mitochondrial-like K02355 fusA; elongation factor G D 106520339 ribosome-releasing factor 2, mitochondrial-like K02355 fusA; elongation factor G D 106518134 mterf1; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 106523207 mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 106528159 transcription termination factor 4, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein D 106536029 mterf3; transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 106518954 translation factor Guf1, mitochondrial-like K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 106528369 pop1; ribonucleases P/MRP protein subunit POP1 isoform X1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 106512948 pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 106533097 pop5; ribonuclease P/MRP protein subunit POP5 isoform X1 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 106528210 rpp30; ribonuclease P protein subunit p30 isoform X1 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 106532372 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 106517249 ribonuclease P protein subunit p25-like K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 106527355 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 106522587 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 106535665 rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 106534422 trmt10c; mitochondrial ribonuclease P protein 1 K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 106511017 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 106527473 kiaa0391; mitochondrial ribonuclease P protein 3 K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 106517413 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 106517414 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 106515263 tefm; transcription elongation factor, mitochondrial isoform X1 K17658 TEFM; transcription elongation factor, mitochondrial D 106519626 pentatricopeptide repeat-containing protein 1, mitochondrial-like K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 106516309 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 106511385 pentatricopeptide repeat domain-containing protein 3, mitochondrial-like K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 106533013 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 106533832 dhx30; putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 106522321 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 106533323 lactation elevated protein 1-like K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 106518642 lace1; lactation elevated protein 1 isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 106531215 xrcc6bp1; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 106513163 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 106530249 lactb2; beta-lactamase-like protein 2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 106515500 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 106515506 ADP/ATP translocase 3-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 106526139 ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 106536224 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 106528520 slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 106520454 slc25a37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 106537277 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 106534948 eral1; GTPase Era, mitochondrial K03595 era; GTPase D 106526493 yars; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 106528188 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 106527903 lars2; probable leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 106524946 lars; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 106524911 dars2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 106513385 gars; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 106525683 rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 106514676 rars; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 106518934 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 106526170 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 106521696 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 106524836 mtpap; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 106525044 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 106522520 mtg1; mitochondrial ribosome-associated GTPase 1 isoform X1 K19828 MTG1; mitochondrial GTPase 1 D 106511963 nitric oxide-associated protein 1-like K19832 NOA1; nitric oxide-associated protein 1 D 106513987 nsun3; putative methyltransferase NSUN3 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 106510750 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 106516177 RNA pseudouridylate synthase domain-containing protein 4-like K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 106514643 wbscr16; Williams-Beuren syndrome chromosomal region 16 protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 106525770 ngrn; neugrin K23496 NGRN; neugrin D 106535126 trub2; probable tRNA pseudouridine synthase 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 106512136 FAST kinase domain-containing protein 2-like K18190 FASTKD2; FAST kinase domain-containing protein 2 D 106523820 probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor D 106526667 rmnd1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1 D 106530454 mettl15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 106514728 UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 106518406 uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 106515620 polg; LOW QUALITY PROTEIN: DNA polymerase subunit gamma-1 isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 106518768 polg2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2 D 106517032 primpol; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 106532142 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 106515913 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 106535522 twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3] D 106511717 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 106510751 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 106511849 uncharacterized protein LOC106511849 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 106510943 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 106511753 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 106524440 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 106516153 atad3a; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 106516108 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 106524269 dnaJ homolog subfamily A member 2-like K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 106514291 dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 106528728 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 106522087 mitochondrial Rho GTPase 1-A K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 106515256 mitochondrial Rho GTPase 1-A-like isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 106535866 heat shock cognate 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 106525681 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 106517696 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 106520367 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 106522528 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 106515046 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein D 106515405 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein D 106511547 uncharacterized protein LOC106511547 K17767 AIP; AH receptor-interacting protein D 106520897 aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 106530088 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 106514068 mitochondrial import receptor subunit TOM40B-like K11518 TOM40; mitochondrial import receptor subunit TOM40 D 106523746 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 106525868 tomm70a; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 106532245 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 106532408 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 106515879 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 106515713 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 106516113 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 106517196 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 106533173 sorting and assembly machinery component 50 homolog A-like K07277 SAM50; outer membrane protein insertion porin family D 106529600 samm50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family D 106530823 sorting and assembly machinery component 50 homolog B-like K07277 SAM50; outer membrane protein insertion porin family C Porin D 106524568 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 106517011 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 106515335 vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 106536415 voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3 D 106512179 voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3 D 106533592 voltage-dependent anion-selective channel protein 2-like isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 106517535 mtx3; metaxin-3 K17776 MTX; metaxin D 106533521 metaxin-1-like K17776 MTX; metaxin D 106523979 mtx2; metaxin-2 K17776 MTX; metaxin D 106525410 myo19; unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX D 106524295 mitochondrial amidoxime-reducing component 1-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 106537255 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 106527276 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 106524624 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 106514031 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 106514509 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 106533071 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 106510877 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 106525174 mitochondrial intermembrane space import and assembly protein 40-A K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 106511516 mitochondrial intermembrane space import and assembly protein 40-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 106518003 mitochondrial intermembrane space import and assembly protein 40-B-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 106516509 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 106516147 MICOS complex subunit Mic10-like isoform X1 K17784 MICOS10; MICOS complex subunit MIC10 D 106522396 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10 D 106519997 MICOS complex subunit MIC60-like K17785 IMMT; MICOS complex subunit MIC60 D 106535986 MICOS complex subunit MIC60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 106536194 MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 106515150 chchd3; MICOS complex subunit MIC19 K17563 CHCHD3; MICOS complex subunit MIC19 D 106523635 formin-like protein 3 K17563 CHCHD3; MICOS complex subunit MIC19 D 106518377 chchd6; MICOS complex subunit MIC25 isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 106522376 MICOS complex subunit mic25a-like isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 106520804 apolipoprotein O-like K24625 APOO; MICOS complex subunit MIC26 D 106531831 apoo; MICOS complex subunit MIC26 K24625 APOO; MICOS complex subunit MIC26 D 106527243 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 106516147 MICOS complex subunit Mic10-like isoform X1 K17784 MICOS10; MICOS complex subunit MIC10 D 106522396 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10 D 106519997 MICOS complex subunit MIC60-like K17785 IMMT; MICOS complex subunit MIC60 D 106535986 MICOS complex subunit MIC60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 106525427 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 106516670 timm23; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 106515117 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 106519281 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 106513498 timm21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 106511432 mitochondrial import inner membrane translocase subunit TIM50-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 D 106511934 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 106515933 mcu; calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial D 106515932 micu1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 106531370 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 106517067 ccdc109b; calcium uniporter regulatory subunit MCUb, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 106536775 smdt1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 106517132 mitochondrial calcium uniporter regulator 1-like K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 106519947 letm1; LETM1 and EF-hand domain-containing protein 1, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 106513638 letm2; LETM1 domain-containing protein LETM2, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 106513177 immp1l; mitochondrial inner membrane protease subunit 1 isoform X1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 106532947 immp2l; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 106514354 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A D 106513166 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 106523958 mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 B Matrix C MMC/PAM proteins D 106535028 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 106524907 mitochondrial import inner membrane translocase subunit TIM44-like K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 106526870 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 106523713 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 106531535 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 106518702 mitochondrial import inner membrane translocase subunit TIM16-like isoform X1 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 106528770 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 106533176 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 106533599 mipep; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 106530742 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 106522510 dnaJ homolog subfamily A member 3, mitochondrial-like K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 106518700 dnaja3; dnaJ homolog subfamily A member 3, mitochondrial K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 106514707 tamm41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 106516287 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 106530059 persulfide dioxygenase ETHE1, mitochondrial-like K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 106530060 ethe1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 106532738 poldip2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 106536062 cyclic AMP-responsive element-binding protein 1-like K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 106526083 cyclic AMP-responsive element-binding protein 1-like K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 106511067 gfm2; LOW QUALITY PROTEIN: ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 106533309 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 106510823 ribosome-releasing factor 2, mitochondrial-like K02355 fusA; elongation factor G D 106520339 ribosome-releasing factor 2, mitochondrial-like K02355 fusA; elongation factor G D 106514730 sp1; transcription factor Sp1 K04684 SP1; transcription factor Sp1 D 106537185 transcriptional repressor protein YY1-like isoform X1 K09201 YY; transcription factor YY D 106521404 transcriptional repressor protein YY1-like K09201 YY; transcription factor YY D 106529688 gabpb2; GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta D 106511210 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial D 106518988 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 106515155 nrf1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1 D 106512445 nuclear respiratory factor 1-like K11831 NRF1; nuclear respiratory factor 1 D 106524498 nfe2; transcription factor NF-E2 45 kDa subunit K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 106512895 nfe2l2; nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 106536745 metallothionein K14739 MT1_2; metallothionein 1/2 C Coactivators D 106514857 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 106513767 peroxisome proliferator-activated receptor gamma coactivator 1-beta-like K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 106535004 peroxisome proliferator-activated receptor gamma coactivator-related protein 1-like K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 106518771 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 106535321 crtc1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 106520639 ep300; histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 106532533 CREB-binding protein-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 106511457 CREB-binding protein-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 106518707 CREB-binding protein-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 106524470 histone acetyltransferase p300-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 106511288 histone acetyltransferase p300-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 106522855 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 106521683 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 106533390 lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 106531756 fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 106519153 fdx1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 106515238 fdx1l; adrenodoxin-like protein, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 106532010 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 106526870 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 106528767 hscb; iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB D 106530993 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1 D 106513823 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 106519884 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 106520656 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 106533279 iba57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 106520164 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 106530914 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 106529953 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 106531331 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 106534397 sideroflexin-1-like K23500 SFXN1_3; sideroflexin-1/3 D 106517750 sideroflexin-1 isoform X1 K23500 SFXN1_3; sideroflexin-1/3 D 106531702 sideroflexin-1-like K23500 SFXN1_3; sideroflexin-1/3 D 106516652 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2 D 106510922 sideroflexin-4-like K23502 SFXN4; sideroflexin-4 D 106525600 sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4 D 106525360 sideroflexin-5-like K23503 SFXN5; sideroflexin-5 D 106524277 sideroflexin-5-like K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 106532762 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 106530034 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 106515663 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 106517433 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 106523641 dhtkd1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 106528263 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 106531380 hcfc1; host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1 D 106530523 hcfc2; host cell factor 2 K27390 HCFC2; host cell factor 2 D 106524348 htt; huntingtin isoform X1 K04533 HD; huntingtin D 106534575 steroid hormone receptor ERR1-like K08552 NR3B1; estrogen-related receptor alpha D 106525281 steroid hormone receptor ERR2-like K08553 NR3B2; estrogen-related receptor beta D 106520414 esrrb; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 106536408 estrogen-related receptor gamma-like K08554 NR3B3; estrogen-related receptor gamma D 106523689 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 106520052 estrogen-related receptor gamma-like isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 106536113 estrogen-related receptor gamma-like K08554 NR3B3; estrogen-related receptor gamma D 106530917 nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 106516315 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 106530689 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 106517295 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 106525621 sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 106518654 protein SERAC1-like K23504 SERAC1; protein SERAC1 D 106511095 serac1; protein SERAC1 K23504 SERAC1; protein SERAC1 D 106510874 uxt; protein UXT K26537 UXT; protein UXT B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 106529553 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 106513732 ndufaf2; mimitin, mitochondrial K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 106516170 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 106531124 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 106535417 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5-like K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 106524897 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 106527676 ndufaf7; NADH dehydrogenase [ubiquinone] complex I, assembly factor 7 isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 106528796 uncharacterized protein C17orf89 homolog K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 106535334 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 106527408 acad9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 106531559 nubpl; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 106514636 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 106522613 reticulon-4-interacting protein 1 homolog, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 106518943 rtn4ip1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 106519175 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 106527795 sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 106530747 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 106532709 mitochondrial chaperone BCS1-like K08900 BCS1; mitochondrial chaperone BCS1 D 106524009 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 106534224 ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 106535304 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 106522321 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 106516108 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 106534820 protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 106523131 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 106525553 uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 106514234 cmc1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 106513191 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 106535475 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 106533312 cytochrome c oxidase assembly factor 3 homolog, mitochondrial-like K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 106523452 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 106519839 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 106524585 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 106533006 cytochrome c oxidase assembly factor 7-like K18180 COA7; cytochrome c oxidase assembly factor 7 D 106531731 cytochrome c oxidase assembly factor 7-like K18180 COA7; cytochrome c oxidase assembly factor 7 D 106535259 protoheme IX farnesyltransferase, mitochondrial-like K02257 COX10; heme o synthase [EC:2.5.1.141] D 106535274 protoheme IX farnesyltransferase, mitochondrial-like K02257 COX10; heme o synthase [EC:2.5.1.141] D 106528229 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 106536837 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14 D 106526398 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 106537055 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial-like K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 106530134 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial-like K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 106535350 mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18 D 106536190 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 106528951 cytochrome c oxidase protein 20 homolog K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 106517413 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 106517414 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 106529539 pet100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 106526449 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 106516301 surf1; surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 106535064 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 106526198 protein SCO2 homolog, mitochondrial-like K23755 SCO2; protein SCO2 D 106521405 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 106534333 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 106527264 apopt1; apoptogenic protein 1, mitochondrial K23506 APOPT1; apoptogenic protein 1 D 106525553 uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1 D 106523131 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 106519712 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 106532796 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 106525160 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 106521320 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 106518797 usmg5; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 106511486 mfn1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 106511134 mitofusin-1-like K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 106530038 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 106510941 opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 106529667 opa3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein D 106534073 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 106535003 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 106536115 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 106528358 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX D 106528364 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX D 106526563 apoptosis regulator BAX-like isoform X1 K02159 BAX; apoptosis regulator BAX D 106525485 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 106528635 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 106525549 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 106533335 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 106531443 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 106515271 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 106522075 sumo2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 106518458 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 106523318 small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier D 106513005 endophilin-B1-like K11248 SH3GLB1; endophilin-B1 D 106526557 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 106529344 mtch1; mitochondrial carrier homolog 1 K17885 MTCH; mitochondrial carrier D 106524358 mff; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor D 106529161 mitochondrial fission factor homolog A-like K22076 MFF; mitochondrial fission factor D 106513487 gdap1; ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 106527622 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 106536618 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 106527714 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 106519630 mitochondrial dynamics protein MID51-like K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 106520646 mief1; LOW QUALITY PROTEIN: mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 106515168 pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 106516292 fam73b; protein FAM73B K27289 MIGA; mitoguardin D 106511563 protein FAM73A-like K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 106535353 actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 106519625 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 106524231 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 106527567 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 106527723 phb; prohibitin K17080 PHB1; prohibitin 1 D 106531185 phb2; prohibitin-2 K17081 PHB2; prohibitin 2 D 106520916 ktn1; kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 106525485 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 106528635 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 106525549 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 106518982 unconventional myosin-Va-like isoform X1 K10357 MYO5; myosin V D 106515019 unconventional myosin-Vb-like K10357 MYO5; myosin V D 106521141 myo5a; unconventional myosin-Va K10357 MYO5; myosin V D 106521142 myo5c; unconventional myosin-Vc K10357 MYO5; myosin V D 106536211 myo5b; unconventional myosin-Vb K10357 MYO5; myosin V D 106529727 diablo homolog, mitochondrial-like isoform X1 K10522 DIABLO; diablo D 106529743 diablo; diablo homolog, mitochondrial K10522 DIABLO; diablo C Morphogenesis factors D 106534124 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25 D 106522087 mitochondrial Rho GTPase 1-A K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 106515256 mitochondrial Rho GTPase 1-A-like isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 106519997 MICOS complex subunit MIC60-like K17785 IMMT; MICOS complex subunit MIC60 D 106535986 MICOS complex subunit MIC60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 106514424 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 106512148 28S ribosomal protein S29, mitochondrial-like K17408 DAP3; small subunit ribosomal protein S29 D 106531576 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 106531836 nedd4; E3 ubiquitin-protein ligase NEDD4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 106523618 oxr1; oxidation resistance protein 1 isoform X1 K25437 OXR1; oxidation resistance protein 1 D 106529382 msto1; protein misato homolog 1 K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 106515843 atg2a; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 106520695 atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2 D 106535325 atg3; ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 106521634 atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 106532030 atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 106515248 atg4d; cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 106517859 cysteine protease ATG4D-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 106526895 atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5 D 106521426 becn1; beclin-1 K08334 BECN; beclin D 106514708 atg7; ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 106520490 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 106536380 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 isoform X1 K08341 GABARAP; GABA(A) receptor-associated protein D 106525327 gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 106518461 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 106533474 autophagy-related protein 9A-like K17907 ATG9; autophagy-related protein 9 D 106521315 atg10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 106520505 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12 D 106527304 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 106534440 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 106510803 autophagy-related protein 16-2-like K20868 ATG16L2; autophagy-related protein 16-2 D 106520660 wipi2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 D 106528784 wipi1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 106531494 park2; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31] D 106522971 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 106516521 clec16a; protein CLEC16A K19513 CLEC16A; protein CLEC16A D 106529073 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 106535003 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 106536115 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 106533286 sqstm1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1 D 106517752 tax1-binding protein 1 homolog B-like K21347 TAX1BP1; Tax1-binding protein 1 D 106519499 tax1bp1; tax1-binding protein 1 isoform X1 K21347 TAX1BP1; Tax1-binding protein 1 D 106521975 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 106527974 ambra1; activating molecule in BECN1-regulated autophagy protein 1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 106529645 atg13; autophagy-related protein 13 K08331 ATG13; autophagy-related protein 13 D 106528300 serine/threonine-protein kinase ULK1-like isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 106513539 ulk1; serine/threonine-protein kinase ULK1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 106528320 serine/threonine-protein kinase ULK2-like K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 106533605 rb1cc1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 106533043 LOW QUALITY PROTEIN: heat shock protein HSP 90-alpha-like K04079 HSP90A; molecular chaperone HtpG D 106533044 heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG D 106522460 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 106522714 hsp90 co-chaperone Cdc37-like K09554 CDC37; cell division cycle protein 37 D 106529107 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 106523873 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 106520661 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 106528474 E3 ubiquitin-protein ligase SMURF2-like K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 106520124 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 106513563 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 106528447 fundc1; FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1 D 106536279 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 106516315 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 106530689 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 106522328 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 106516028 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 106535047 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 106536570 microtubule-associated proteins 1A/1B light chain 3A-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 106525260 next to BRCA1 gene 1 protein-like K17987 NBR1; next to BRCA1 gene 1 protein D 106534857 next to BRCA1 gene 1 protein-like isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 106535703 nbr1; next to BRCA1 gene 1 protein K17987 NBR1; next to BRCA1 gene 1 protein D 106522060 tectonin beta-propeller repeat-containing protein 1-like isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 106532091 tecpr1; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 106518599 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 106522118 zinc finger FYVE domain-containing protein 1-like isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 106520320 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 106516999 coasy; bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 106522507 pla2g6; 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 106516733 protein C19orf12 homolog K23168 MPAN; protein MPAN D 106523190 protein C19orf12 homolog K23168 MPAN; protein MPAN ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024