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  Mitochondrial Biogenesis - Astyanax mexicanus (Mexican tetra)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I C Mitochondrial respiratory chain complex III C Cytochrome c oxidase C F-type ATPase B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 103025872 polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 103030287 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 103029804 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 103033367 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 103033708 mtif2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 103023322 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3 D 103022184 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 103026053 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 103024908 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 103042390 mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 103037364 transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 103022240 mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 103029969 mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 103023681 guf1; translation factor Guf1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 103038599 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 103040071 pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 103044522 pop5; ribonuclease P/MRP protein subunit POP5 isoform X1 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 103021733 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 103031509 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 103040714 rpp25l; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 103021700 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 103046970 rpp25a; ribonuclease P protein subunit p25a K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 125785614 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 103042462 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 103044162 rpp40; ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 103044792 trmt10c; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 103024621 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 103027370 prorp; mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 103029896 mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 103025460 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 103038602 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 103041319 ptcd1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 103022311 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 107196966 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 103047400 dhx30; ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 103029047 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 103026430 afg1la; AFG1 like ATPase a K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 103023529 afg1lb; lactation elevated protein 1 homolog B isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 103036278 atp23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 103046703 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 103030826 lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 103035973 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 103040979 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 103047840 si:dkey-251i10.1; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 103023085 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 103035274 slc25a37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 103035916 slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 103028916 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 103029521 eral1; GTPase Era, mitochondrial K03595 era; GTPase D 103025615 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 103038774 yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 103029454 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 103037167 lars1b; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 103023857 dars2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 103022557 gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 103037201 rars1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 103046938 rars2; probable arginine--tRNA ligase, mitochondrial isoform X2 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 103028286 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 103021966 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 103039125 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 103037561 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 103036143 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 103040798 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 103034327 noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 103035728 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 111191537 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 103024327 rpusd4; pseudouridylate synthase RPUSD4, mitochondrial K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 103023798 rcc1l; RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein D 103045160 ngrn; neugrin K23496 NGRN; neugrin D 103032065 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 103034825 fastkd2; FAST kinase domain-containing protein 2, mitochondrial isoform X1 K18190 FASTKD2; FAST kinase domain-containing protein 2 D 103037254 mtrfr; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor D 103045364 rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 103035220 mettl15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 103038060 myg1; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 103046561 mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 103040749 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 103047389 polg2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 D 103037694 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 103041659 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 103025245 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 103039129 nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial D 103026372 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3] D 103025728 pif1; ATP-dependent DNA helicase PIF1 isoform X1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 103023330 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 103042431 atad3; ATPase family AAA domain containing 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 103031109 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 103026191 dnaja2b; dnaJ homolog subfamily A member 2b K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 103044841 dnaja2a; dnaJ homolog subfamily A member 2a K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 103026659 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 103038910 rhot1b; mitochondrial Rho GTPase 1b isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 103041754 rhot1a; mitochondrial Rho GTPase 1-A isoform X2 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 103043364 hspa8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 103045816 hsc70; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111193176 hsp70.1; heat shock cognate 70-kd protein, tandem duplicate 1 isoform X2 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 103047344 hspa8b; heat shock protein family A (Hsp70) member 8b K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 103043955 hspa1b; heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 103039436 hsp70.3; heat shock cognate 70-kd protein, tandem duplicate 3 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 103044419 golgin subfamily A member 6-like protein 6 K17767 AIP; AH receptor-interacting protein D 103034758 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein D 103033614 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 103030645 si:dkey-71l1.1; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40 D 103028148 tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 103036618 tomm40l; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40 D 103032171 tomm70a; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 103023388 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 103029137 tomm20a; translocase of outer mitochondrial membrane 20 K17770 TOM20; mitochondrial import receptor subunit TOM20 D 103040423 tomm20b; mitochondrial import receptor subunit TOM20 homolog B isoform X1 K17770 TOM20; mitochondrial import receptor subunit TOM20 D 107197931 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 103031637 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 103041552 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 103043640 samm50; sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family D 103023007 samm50l; sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family C Porin D 103024199 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 103037680 vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 103040512 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 103039704 vdac3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3 D 103039814 zgc:56235; voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 103040731 mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin D 103026555 mtx1b; metaxin-1b K17776 MTX; metaxin D 103041144 mtx2; metaxin-2 K17776 MTX; metaxin D 103044318 mtx1a; metaxin-1a K17776 MTX; metaxin D 103043962 unconventional myosin-XIX K25838 MYO19; myosin XIX B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 103035126 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 103033111 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 103043096 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 103027997 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 107197049 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 103034199 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 103027030 chchd4a; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 103035841 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 103045175 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 103047888 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 103027233 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 103030686 micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 103027493 chchd3b; coiled-coil-helix-coiled-coil-helix domain containing 3b isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 103024492 chchd3a; coiled-coil-helix-coiled-coil-helix domain containing 3a isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 103044854 chchd6a; MICOS complex subunit mic25a isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 103046590 chchd6b; coiled-coil-helix-coiled-coil-helix domain containing 6b isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 103027169 apooa; apolipoprotein O, a isoform X2 K24625 APOO; MICOS complex subunit MIC26 D 103027916 apoob; apolipoprotein O, b isoform X1 K24625 APOO; MICOS complex subunit MIC26 D 103025840 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27 D 103038878 MICOS complex subunit Mic27 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 103045175 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 103047888 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 103027233 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 103045596 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 103025585 timm23b; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 103030206 timm23a; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 103023671 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 103042884 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A isoform X2 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 103046293 timm21; mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 103024746 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 103027768 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 103028098 micu1; calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial D 103045181 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 103042391 calcium uniporter protein, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 103023443 smdt1b; single-pass membrane protein with aspartate-rich tail 1b K22830 SMDT1; essential MCU regulator, mitochondrial D 103036919 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 103039460 mcur1; mitochondrial calcium uniporter regulator 1 isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 103046373 letm1; mitochondrial proton/calcium exchanger protein isoform X3 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 103035700 immp1l; mitochondrial inner membrane protease subunit 1 isoform X2 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 103022072 immp2l; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 103030510 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 103032677 mpc1; LOW QUALITY PROTEIN: mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 103029922 mpc2b; mitochondrial pyruvate carrier 2b K22139 MPC2; mitochondrial pyruvate carrier 2 D 103033906 mpc2a; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 103024891 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 103030968 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 103031346 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 103036922 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 103032477 grpel2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 103024820 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 103042432 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 103028256 pam16; mitochondrial import inner membrane translocase subunit tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 103030900 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 103027638 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 103023218 mipepa; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 103038131 mipepb; LOW QUALITY PROTEIN: mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 103043207 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 103043505 hspe1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 103024933 dnaja3b; dnaJ heat shock protein family (Hsp40) member A3b K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 103029110 dnaja3a; dnaJ heat shock protein family (Hsp40) member A3a K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 103036757 tamm41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 103030185 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 111197379 persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 125781328 ethe1; persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 103032170 polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2 D 103037164 poldip2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 103036831 creb1b; cyclic AMP-responsive element-binding protein 1b K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 103024012 creb1a; cyclic AMP-responsive element-binding protein 1a isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 103026053 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 103024908 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 103027197 sp1; transcription factor Sp1 K04684 SP1; transcription factor Sp1 D 103029419 yy1b; transcriptional repressor protein YY1b K09201 YY; transcription factor YY D 103039658 yy1a; transcriptional repressor protein YY1a K09201 YY; transcription factor YY D 111197554 gabpb1; GA-binding protein subunit beta-1 K09454 GABPB; GA-binding protein transcription factor, beta D 103043833 gabpb2a; GA-binding protein subunit beta-2a K09454 GABPB; GA-binding protein transcription factor, beta D 103030287 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 103046627 nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1 D 103035998 nfe2l2a; nuclear factor erythroid 2-related factor 2a K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 103040845 nfe2l2b; nuclear factor erythroid 2-related factor 2b K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 103041352 metallothionein-1 K14739 MT1_2; metallothionein 1/2 D 103041858 metallothionein K14739 MT1_2; metallothionein 1/2 D 107197617 metallothionein-1 K14739 MT1_2; metallothionein 1/2 D 107197618 metallothionein K14739 MT1_2; metallothionein 1/2 C Coactivators D 103037640 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X2 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 103046861 ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X2 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 103035322 si:dkey-93h22.8; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 103032399 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X2 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 103042200 crtc1b; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 103044365 ep300a; histone acetyltransferase p300 isoform X4 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 103032522 ep300b; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 103035824 crebbpa; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 125780395 histone acetyltransferase p300-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 103043755 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 103046629 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 103036122 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 107197449 fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 111194933 fdx1; adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial D 103037318 adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial D 103037324 fdx1b; ferredoxin 1b K22070 FDX1; ferredoxin-1, mitochondrial D 103046893 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 103036922 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 103030933 hscb; iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB D 103036316 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1 D 103034922 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 103023651 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 103030996 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 103035458 iba57; putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 103021881 nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 103031995 zgc:110319; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 103035317 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 103036689 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 103040609 sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 103041177 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 103023557 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2 D 103033880 sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4 D 103033496 sfxn5b; sideroflexin-5b K23503 SFXN5; sideroflexin-5 D 103045503 sfxn5a; sideroflexin-5a isoform X1 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 103025592 cpt1ab; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 103024546 cpt1a2b; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 103035972 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 103027125 cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 103022273 cpt1aa; carnitine palmitoyltransferase 1Aa (liver) isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 103041509 dhtkd1; 2-oxoadipate dehydrogenase complex component E1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 103033315 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 103044501 hcfc1b; host cell factor 1b K14966 HCFC1; host cell factor 1 D 103047617 hcfc2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2 D 103040957 htt; huntingtin isoform X4 K04533 HD; huntingtin D 103027185 esrra; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha D 103031345 esrrb; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 103042449 esrrgb; estrogen-related receptor gamma b K08554 NR3B3; estrogen-related receptor gamma D 103040340 esrrd; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma D 103043477 esrrga; estrogen-related receptor gamma a isoform X2 K08554 NR3B3; estrogen-related receptor gamma D 103041157 nrip1a; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 103043914 nrip1b; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 103022500 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 103028619 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 103026089 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 103031674 sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 103044342 serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 103033924 uxt; protein UXT K26537 UXT; protein UXT B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 103039289 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 103033596 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 103039223 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 103026779 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 103024722 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 103028969 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 103032488 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 107197902 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 103031013 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 107196955 acad9; complex I assembly factor ACAD9, mitochondrial isoform X1 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 103042104 nubpl; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning D 103034571 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 103027749 rtn4ip1; reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 103033360 timmdc1; complex I assembly factor TIMMDC1, mitochondrial isoform X1 K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 103042070 sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 103026876 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 103024599 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 103041539 ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 103028273 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 103029047 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 103031109 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 103027177 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 103029432 c6h16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 103029172 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 103044960 c10h12orf73; protein BRAWNIN K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 103034379 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 111188582 cmc1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 103036039 cmc2; COX assembly mitochondrial protein 2 homolog isoform X1 K18172 CMC2; COX assembly mitochondrial protein 2 D 103038044 cytochrome c oxidase assembly factor 1 homolog isoform X1 K18173 COA1; cytochrome c oxidase assembly factor 1 D 103045739 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 103044870 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 103042106 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 103022513 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 103029237 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 103036871 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 103039244 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 103045965 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14 D 103027427 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 103031497 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 103026843 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 103035388 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18 D 103023950 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 103042356 cytochrome c oxidase assembly protein COX20, mitochondrial isoform X1 K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 103029896 mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 103025460 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 103037501 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 111191186 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 103035939 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 103047738 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 103027271 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 103036150 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 103043171 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 103023848 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 103021591 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1 D 103034379 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 103029172 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 103025405 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 103027065 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 103034150 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 103030425 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 111190231 atp5mj; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid D 111193560 ATP synthase membrane subunit K, mitochondrial isoform X1 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 D 103039040 atp5md; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 103034819 mfn1a; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 103030239 mfn1b; mitofusin-1b isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 103030025 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 103029389 opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 103037513 opa3; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein D 103033830 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 103025472 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 103027172 parla; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 103023787 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 103047816 zgc:153993; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 103025681 apoptosis regulator BAX isoform X1 K02159 BAX; apoptosis regulator BAX D 103042396 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 103036512 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 103030788 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 103041559 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 103032948 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 103038972 sumo3a; small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier D 103044284 sumo2b; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 103045390 sumo2a; small ubiquitin like modifier 2a K12160 SUMO; small ubiquitin-related modifier D 103028680 sh3glb1a; endophilin-B1a isoform X1 K11248 SH3GLB1; endophilin-B1 D 103025133 sh3glb1b; endophilin-B1b isoform X1 K11248 SH3GLB1; endophilin-B1 D 111196472 mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 111191950 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 125803865 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier D 125803866 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier D 111194468 mffb; mitochondrial fission factor homolog A isoform X1 K22076 MFF; mitochondrial fission factor D 103034990 mitochondrial fission factor-like isoform X1 K22076 MFF; mitochondrial fission factor D 103031778 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 103044188 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 103035393 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 103030721 mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 103042026 mief2; mitochondrial dynamics protein MID49 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 125794064 mitochondrial dynamics protein MID51-like K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 103033815 pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 103027239 miga2; mitoguardin 2 K27289 MIGA; mitoguardin D 103029709 miga1; mitoguardin 1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 103039558 actb1; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 103030443 actb2; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 103034291 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 103039509 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 103031128 phb; prohibitin K17080 PHB1; prohibitin 1 D 103047478 phb2b; prohibitin-2b K17081 PHB2; prohibitin 2 D 103035142 phb2a; prohibitin-2a K17081 PHB2; prohibitin 2 D 103028986 ktn1; kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 103036512 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 103030788 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 103036881 myo5b; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V D 103034187 myo5c; unconventional myosin-Vc K10357 MYO5; myosin V D 103045116 myo5aa; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V D 103035272 myo5ab; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V D 103037921 E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 103032753 diablob; diablo, IAP-binding mitochondrial protein b K10522 DIABLO; diablo D 103028190 diabloa; diablo, IAP-binding mitochondrial protein a K10522 DIABLO; diablo C Morphogenesis factors D 103034035 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25 D 103038910 rhot1b; mitochondrial Rho GTPase 1b isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 103041754 rhot1a; mitochondrial Rho GTPase 1-A isoform X2 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 103027233 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 103022897 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 103037648 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 103044630 nedd4a; E3 ubiquitin-protein ligase NEDD4a isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 103022741 oxr1a; oxidation resistance protein 1a isoform X4 K25437 OXR1; oxidation resistance protein 1 B Mitophagy factors C Autophagy-related proteins D 103031414 atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2 D 103041242 atg2a; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 103036858 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 103025276 atg4a; cysteine protease ATG4A isoform X2 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 103037279 atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 103041107 cysteine protease atg4da K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 103029112 atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 103025250 atg4da; cysteine protease atg4da K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 103047871 atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5 D 103023868 becn1; beclin-1 K08334 BECN; beclin D 103035842 atg7; ubiquitin-like modifier-activating enzyme ATG7 isoform X2 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 103044705 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 103031579 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 103027931 zgc:92606; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 103039768 gabarapb; GABA(A) receptor-associated protein b K08341 GABARAP; GABA(A) receptor-associated protein D 103030028 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 103032422 atg9b; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9 D 103033268 atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 103031408 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 103023450 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 103034420 protein Atg16l2 K20868 ATG16L2; autophagy-related protein 16-2 D 103028226 wipi2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 D 103046600 wipi1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 103031223 uncharacterized protein LOC103031223 K08332 VAC8; vacuolar protein 8 C Parkin-dependent mechanism factors D 103027813 prkn; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31] D 103035049 rnf41; E3 ubiquitin-protein ligase NRDP1 D 103042374 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 103044294 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 103025472 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 103027172 parla; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 103026459 sqstm1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1 D 103024102 tax1bp1a; tax1-binding protein 1 homolog A isoform X1 K21347 TAX1BP1; Tax1-binding protein 1 D 103026163 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 103040690 ambra1b; activating molecule in BECN1-regulated autophagy protein 1B isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 103039487 atg13; autophagy-related protein 13 isoform X2 K08331 ATG13; autophagy-related protein 13 D 103042154 ulk1b; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 103026407 ulk2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 103038395 rb1cc1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 103024454 hsp90aa1.1; heat shock protein 90, alpha (cytosolic), class A member 1, tandem duplicate 1 K04079 HSP90A; molecular chaperone HtpG D 103047517 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 103024139 hsp90aa1.2; heat shock protein 90, alpha (cytosolic), class A member 1, tandem duplicate 2 K04079 HSP90A; molecular chaperone HtpG D 107197351 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 103025443 smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 103027089 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 103046280 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 103036208 bnip3lb; BCL2 interacting protein 3 like b K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 103024632 bnip3la; BCL2 interacting protein 3 like a K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 103032748 fundc1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 D 103021389 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 103022500 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 103028619 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 103031430 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 103038765 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C isoform X2 K10435 MAP1LC; microtubule-associated protein 1 light chain D 103035726 map1lc3cl; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 103034733 nbr1b; next to BRCA1 gene 1 protein K17987 NBR1; next to BRCA1 gene 1 protein D 103031771 nbr1a; NBR1 autophagy cargo receptor a isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 103030324 tecpr1b; LOW QUALITY PROTEIN: tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 103031308 tecpr1a; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 103027738 si:ch211-11n16.2; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 103031100 zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 103045691 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 103024703 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 103038570 zgc:112052; protein C19orf12 homolog K23168 MPAN; protein MPAN D 103040374 protein C19orf12 homolog K23168 MPAN; protein MPAN D 103040695 protein C19orf12 homolog K23168 MPAN; protein MPAN D 103030554 fundc2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024