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  Mitochondrial Biogenesis - Arvicanthis niloticus (African grass rat)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I C Mitochondrial respiratory chain complex III C Cytochrome c oxidase C F-type ATPase B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 117696478 Polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 117724651 Tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 117700166 Tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 117722066 Tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 117712485 Mtif2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2 D 117697934 Mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3 D 117696427 Tsfm; elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts D 117697113 Tufm; elongation factor Tu, mitochondrial isoform X1 K02358 tuf; elongation factor Tu D 117700439 Gfm2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G D 117706973 Gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 117696253 Mterf2; transcription termination factor 2, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 117718620 Mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 117720528 Mterf1; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 117720708 LOW QUALITY PROTEIN: transcription termination factor 1b, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein D 117722393 Mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 117712335 Guf1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 117718403 Pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 117699202 Pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 117697999 Pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 117721646 Rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 117698010 Pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 117698979 Rpp25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 117708319 Rpp25l; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 117713856 Rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 117713939 Rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 117717488 Trmt10c; LOW QUALITY PROTEIN: tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 117694035 Hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 117716877 Prorp; LOW QUALITY PROTEIN: mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 117705540 Mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 117711861 Tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 117697980 pentatricopeptide repeat-containing protein 1, mitochondrial isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 117700612 Ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 117714923 Ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 117693291 Dhx30; ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 117703911 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 117724443 Afg1l; AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 117696092 Atp23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 117724769 Supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 117698479 Lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 117695364 Slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 117698523 ADP/ATP translocase 1-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 117707501 Slc25a31; ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 117713753 ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 117721894 Slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 117705378 Slc25a37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 117719021 Slc25a28; mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 117720357 Malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 117711897 Eral1; GTPase Era, mitochondrial isoform X1 K03595 era; GTPase D 117708526 Yars1; tyrosine--tRNA ligase, cytoplasmic isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 117717875 Yars2; tyrosine--tRNA ligase, mitochondrial isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 117693562 Lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 117719868 Lars1; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 117716208 Dars2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 117720626 Gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 117698658 Rars2; probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 117711291 Rars1; arginine--tRNA ligase, cytoplasmic isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 117724432 Qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 117706933 Gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 117697855 Gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 117714259 Mtpap; poly(A) RNA polymerase, mitochondrial isoform X1 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 117704916 Pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 117717088 Mtg1; mitochondrial ribosome-associated GTPase 1 isoform X1 K19828 MTG1; mitochondrial GTPase 1 D 117713113 Noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 117717543 Nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 117708211 Nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 117714644 Rpusd3; mitochondrial mRNA pseudouridine synthase RPUSD3 isoform X1 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 117698913 Rpusd4; mitochondrial RNA pseudouridine synthase RPUSD4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 117697958 Rcc1l; RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein D 117724793 Ngrn; neugrin K23496 NGRN; neugrin D 117704107 Trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 117704194 Fastkd1; FAST kinase domain-containing protein 1, mitochondrial isoform X1 K27754 FASTKD1; FAST kinase domain-containing protein 1 D 117705896 Fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 117724052 Fastkd3; FAST kinase domain-containing protein 3, mitochondrial K27755 FASTKD3; FAST kinase domain-containing protein 3 D 117712870 Tbrg4; FAST kinase domain-containing protein 4 isoform X1 K27756 TBRG4; FAST kinase domain-containing protein 4 D 117703634 Fastkd5; FAST kinase domain-containing protein 5, mitochondrial K27757 FASTKD5; FAST kinase domain-containing protein 5 D 117698145 CUNH12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor D 117700242 Rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 117712697 Grsf1; LOW QUALITY PROTEIN: G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1 D 117704480 Mettl15; 12S rRNA N4-methylcytidine (m4C) methyltransferase K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 117718929 Myg1; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 117724967 Mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 117708619 Polg; DNA polymerase subunit gamma-1 isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 117711772 Polg2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2 D 117721594 Primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 117702752 Endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 117703072 Mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 117693680 Exog; nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial D 117693398 Twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3] D 117699400 Pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 117720515 Ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 117709009 ATPase family AAA domain-containing protein 3 isoform X1 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 117724535 ubiquinol-cytochrome-c reductase complex assembly factor 2 isoform X1 K17682 MNF1; mitochondrial nucleoid factor 1 D 117710194 C6H17orf80; uncharacterized protein C17orf80 homolog isoform X1 K27759 MTNAP1; mitochondrial nucleoid-associated protein 1 D 117720983 GTPase IMAP family member 3-like K27758 GIMAP1_3_5; GTPase IMAP family member 1/3/5 D 117720984 Gimap1; GTPase IMAP family member 1 K27758 GIMAP1_3_5; GTPase IMAP family member 1/3/5 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 117723155 Dnaja2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 117704244 Tomm34; mitochondrial import receptor subunit TOM34 isoform X1 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 117710182 Rhot1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 117698957 Hspa8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 117705832 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 117712747 Hspa6; LOW QUALITY PROTEIN: heat shock 70 kDa protein 6 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 117724403 heat shock 70 kDa protein 1A K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 117724405 heat shock 70 kDa protein 1A K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 117724950 Hspa1l; heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 117724951 heat shock 70 kDa protein 1A K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 117705725 Aip; AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein D 117711362 Aipl1; aryl-hydrocarbon-interacting protein-like 1 isoform X1 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 117698485 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 D 117709036 Tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 D 117722514 Tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 117717600 mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 117720667 Tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 117697063 Tomm20l; TOMM20-like protein 1 K17770 TOM20; mitochondrial import receptor subunit TOM20 D 117723258 Tomm20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 117718790 Tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 117706526 Tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 117721543 Tomm40l; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40 D 117717780 Tomm70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 C TOB/SAM complex D 117718951 Samm50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family C Porin D 117711430 Vdac1; voltage-dependent anion-selective channel protein 1 isoform X1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 117717634 LOW QUALITY PROTEIN: voltage-dependent anion-selective channel protein 1-like K05862 VDAC1; voltage-dependent anion channel protein 1 D 117705417 Vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 117721707 Vdac3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 117700569 Mtx3; metaxin-3 K17776 MTX; metaxin D 117704195 Mtx2; metaxin-2 isoform X1 K17776 MTX; metaxin D 117707071 Mtx1; metaxin-1 K17776 MTX; metaxin D 117710507 Myo19; unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX D 117695334 Armcx1; armadillo repeat-containing X-linked protein 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1 D 117694410 Armcx2; armadillo repeat-containing X-linked protein 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2 D 117694490 Armcx3; armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3 D 117722664 LOW QUALITY PROTEIN: armadillo repeat-containing X-linked protein 3-like K26189 ARMCX3; armadillo repeat-containing X-linked protein 3 D 117694460 Armcx6; protein ARMCX6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6 D 117716277 Mtarc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] D 117716517 Mtarc2; mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 117697064 Timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 117703617 Timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 117698919 Timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 117693981 Timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 117699340 Timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 117706300 putative mitochondrial import inner membrane translocase subunit Tim8 A-B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 117696854 Timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 117702554 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 117714694 Chchd4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 117710719 Gfer; FAD-linked sulfhydryl oxidase ALR isoform X1 K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 117709157 Micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 117714746 Immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 117704991 Micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 117721038 Chchd3; MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 117715116 Chchd6; MICOS complex subunit MIC25 K17564 CHCHD6; MICOS complex subunit MIC25 D 117695361 Apoo; MICOS complex subunit MIC26 isoform X1 K24625 APOO; MICOS complex subunit MIC26 D 117694027 Apool; MICOS complex subunit MIC27 isoform X1 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 117709157 Micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 117714746 Immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 117711694 Timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 117705039 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 117693994 Timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 117716541 Timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 117719553 Timm21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 117696701 Timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 117724924 Mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 117724311 Micu1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 117705377 Micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 117706529 Mcub; calcium uniporter regulatory subunit MCUb, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 117719095 Smdt1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 117714083 Mcur1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 117712478 Letm1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 117703043 Immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 117717091 Immp2l; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 117697180 Tmem126a; transmembrane protein 126A isoform X1 K18157 TMEM126A; transmembrane protein 126A D 117695491 Mpc1l; mitochondrial pyruvate carrier 1-like protein K22138 MPC1; mitochondrial pyruvate carrier 1 D 117700292 Mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 117719042 mitochondrial pyruvate carrier 1-like K22138 MPC1; mitochondrial pyruvate carrier 1 D 117715987 Mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 117724527 Chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 D 117712679 Ociad1; OCIA domain-containing protein 1 K28215 OCIAD1; OCIA domain-containing protein 1 B Matrix C MMC/PAM proteins D 117698209 Timm44; mitochondrial import inner membrane translocase subunit TIM44 isoform X1 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 117719545 Hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 117713169 Grpel1; grpE protein homolog 1, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE D 117719845 Grpel2; grpE protein homolog 2, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE D 117707295 Dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 C Other matrix factors D 117711523 Pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 117707712 Pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 117706251 Mipep; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 117693637 LOW QUALITY PROTEIN: 60 kDa heat shock protein, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 117700686 60 kDa heat shock protein, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 117705537 Hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 117695201 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 117714170 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 117716383 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 117720226 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 117710511 Dnaja3; dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 117714685 Tamm41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 117710137 Dnlz; DNL-type zinc finger protein isoform X1 K17808 ZIM17; mitochondrial protein import protein ZIM17 D 117724048 Ethe1; persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 117711011 Poldip2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 117705049 Creb1; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 117700439 Gfm2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G D 117706973 Gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 117718542 Sp1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1 D 117694502 Yy2; transcription factor YY2 K09201 YY; transcription factor YY D 117697130 Yy1; transcriptional repressor protein YY1 K09201 YY; transcription factor YY D 117704223 Gabpb1; GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 117706915 Gabpb2; GA-binding protein subunit beta-2 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 117724651 Tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 117720553 Nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1 D 117703103 Nfe2l2; nuclear factor erythroid 2-related factor 2 isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 117699070 metallothionein-2 K14739 MT1_2; metallothionein 1/2 D 117705158 metallothionein-1-like K14739 MT1_2; metallothionein 1/2 D 117723486 metallothionein-2-like K14739 MT1_2; metallothionein 1/2 D 117723529 metallothionein-2 isoform X1 K14739 MT1_2; metallothionein 1/2 D 117723214 Mt3; metallothionein-3 K14740 MT3; metallothionein 3 D 117723421 Mt4; metallothionein-4 K14741 MT4; metallothionein 4 C Coactivators D 117712664 Ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 117719765 Ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 117714640 Pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 117721560 Crtc1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 117710697 Crebbp; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 117718741 Ep300; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 117703054 Nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 117698266 Iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 117714116 Lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 117716184 Fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 117698905 Fdx1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 117713757 ferredoxin-2, mitochondrial-like K22071 FDX2; ferredoxin-2, mitochondrial D 117713824 Fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 117710860 Fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 117719545 Hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 117697660 Hscb; iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB D 117720155 Sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1 D 117697292 Glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 117714107 Isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 117697322 Isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 117711973 Iba57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 117715601 Nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 117707545 Bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 117714754 Bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 117714351 Sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 117723968 Sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 117698478 Sfxn2; sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2 D 117702667 Sfxn4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4 D 117715327 Sfxn5; sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 117704625 Cpt1a; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 117718598 Cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21] D 117719424 Cpt1c; carnitine O-palmitoyltransferase 1, brain isoform isoform X1 K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21] D 117713635 Dhtkd1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 117698759 Fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 117694168 Hcfc1; host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1 D 117696364 Hcfc2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2 D 117712477 Htt; huntingtin K04533 HD; huntingtin D 117694867 Esrra; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha D 117697341 Esrrb; steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta D 117716260 Esrrg; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 117717861 Nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 117708512 Prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 117723868 Prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 117705103 Lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 117724644 Sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 117700150 Serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 117694456 Uxt; protein UXT K26537 UXT; protein UXT D 117719992 protein UXT-like K26537 UXT; protein UXT D 117709057 Perm1; PGC-1 and ERR-induced regulator in muscle protein 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 D 117724553 Gatd3a; glutamine amidotransferase-like class 1 domain-containing protein 3A, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 117717932 Tango2; transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2 D 117705166 C3H2orf69; UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69 D 117709576 Fam214b; protein FAM214B isoform X1 K28528 ATOS; protein Atossa D 117712533 Fam214a; protein FAM214A K28528 ATOS; protein Atossa D 117715459 Ddx47; probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7] B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 117703533 Ndufaf1; complex I intermediate-associated protein 30, mitochondrial isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 117723945 Ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 117693340 Ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 117698770 Ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 117719552 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 117704163 Ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 117698767 Ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 117716770 Ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 117711300 Ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 117724223 Tmem126b; complex I assembly factor TMEM126B, mitochondrial isoform X1 K18165 TMEM126B; complex I assembly factor TMEM126B D 117714365 Ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 117707478 Acad9; complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 117716740 Nubpl; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning D 117699355 Foxred1; FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 117724433 Rtn4ip1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 117717539 Timmdc1; complex I assembly factor TIMMDC1, mitochondrial isoform X1 K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 117714918 Sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 117697771 Sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 117706140 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 117712011 Ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 117711083 Lyrm7; complex III assembly factor LYRM7 isoform X1 K18170 LYRM7; complex III assembly factor LYRM7 D 117703911 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 117724535 ubiquinol-cytochrome-c reductase complex assembly factor 2 isoform X1 K17682 MNF1; mitochondrial nucleoid factor 1 D 117714599 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 117709845 C6H16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 117704915 Smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 117696116 CUNH12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 117721030 Stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 117693484 Cmc1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 117723481 Cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 117711314 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 117713515 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 117722383 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 117723062 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 117708955 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 117711601 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 117710682 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 117719142 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14 D 117707299 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 117697222 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 117718013 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 117713092 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18 D 117697706 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 117721415 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 117705540 Mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 117698329 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 117703847 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 117705268 Oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 117703722 surfeit locus protein 1 isoform X1 K14998 SURF1; surfeit locus 1 family protein D 117710163 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 117718467 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 117711983 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 117716985 Lrpprc; leucine-rich PPR motif-containing protein, mitochondrial isoform X1 K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 117697382 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1 D 117721030 Stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 117704915 Smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 117706834 Tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 D 117693504 Higd1a; HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 117701631 HIG1 domain family member 1C K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 117719370 Higd1c; HIG1 domain family member 1C K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 117714320 Higd2a; HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial C Complex-V assembly factors D 117708577 Atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 117710220 Atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 117698775 Tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 117697333 Atp5mpl; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid D 117700362 ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid D 117725054 ATP synthase subunit ATP5MPL, mitochondrial-like K18193 MP68; 6.8 kDa mitochondrial proteolipid D 117695352 ATP synthase membrane subunit DAPIT, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5 D 117704837 Atp5md; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 117706578 Mfn1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 117708335 Mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 117717689 Opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 117712989 Opa3; optic atrophy 3 protein isoform X1 K23166 OPA3; optic atrophy 3 protein D 117697995 Triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 117718175 Parl; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 117724492 Bak1; bcl-2 homologous antagonist/killer isoform X1 K14021 BAK; Bcl-2 homologous antagonist/killer D 117722249 Bax; apoptosis regulator BAX isoform X1 K02159 BAX; apoptosis regulator BAX D 117717873 Dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 117698170 Fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 117705970 Sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 117711785 Sumo2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 117712909 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 117722044 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 117722632 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 117724785 Sumo3; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 117724893 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier D 117706528 Sh3glb1; endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1 D 117701544 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier D 117704260 Mtch2; mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier D 117713923 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier D 117724159 Mtch1; mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier D 117722159 Mff; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor D 117698681 Gdap1; ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 117704585 Gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 117710225 Vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 117711697 Mief2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 117712844 mitochondrial dynamics protein MID51-like K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 117718888 Mief1; mitochondrial dynamics protein MID51 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 117710188 Pld6; mitochondrial cardiolipin hydrolase isoform X1 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 117701545 LOW QUALITY PROTEIN: mitoguardin 2-like K27289 MIGA; mitoguardin D 117703574 Miga2; mitoguardin 2 isoform X1 K27289 MIGA; mitoguardin D 117707148 Miga1; mitoguardin 1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 117697924 Actb; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 117710865 Actg1; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 117704523 Naa20; N-alpha-acetyltransferase 20 isoform X1 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 117697879 Naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 117710724 prohibitin-like isoform X1 K17080 PHB1; prohibitin 1 D 117711545 Phb; prohibitin K17080 PHB1; prohibitin 1 D 117715347 Phb2; prohibitin-2 K17081 PHB2; prohibitin 2 D 117704992 Ktn1; kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 117717873 Dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 117712733 Myo5c; unconventional myosin-Vc K10357 MYO5; myosin V D 117712993 Myo5a; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V D 117719805 Myo5b; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V D 117694154 Xiap; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 117698251 Diablo; diablo homolog, mitochondrial K10522 DIABLO; diablo C Morphogenesis factors D 117722021 Snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25 D 117710182 Rhot1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 117714746 Immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 117712685 Mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 117707082 Dap3; 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29 D 117699624 Nedd4; E3 ubiquitin-protein ligase NEDD4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 117718516 Oxr1; oxidation resistance protein 1 isoform X1 K25437 OXR1; oxidation resistance protein 1 D 117707046 Msto1; protein misato homolog 1 K27320 MSTO1; protein misato D 117714231 Prelid1; PRELI domain-containing protein 1, mitochondrial K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial D 117717934 PRELI domain-containing protein 1, mitochondrial-like K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial D 117719842 Prelid2; PRELI domain-containing protein 2 isoform X1 K27965 PRELID2; PRELI domain-containing protein 2 mitochondrial D 117704620 Prelid3b; PRELI domain containing protein 3B K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial D 117719772 Prelid3a; PRELI domain containing protein 3A K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial B Mitophagy factors C Autophagy-related proteins D 117697093 Atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2 D 117711991 Atg2a; autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2 D 117717693 Atg3; ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 117694279 Atg4a; cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 117709287 Atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 117713630 Atg4d; cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 117719085 LOW QUALITY PROTEIN: cysteine protease ATG4A-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 117722205 Atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 117701603 autophagy protein 5-like K08339 ATG5; autophagy-related protein 5 D 117724902 Atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5 D 117711312 Becn1; beclin-1 isoform X1 K08334 BECN; beclin D 117714642 Atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 117695176 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 117711642 Gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 117713064 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 117715156 Gabarapl1; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 117723225 Gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 117705325 Atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 117720752 Atg9b; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9 D 117700335 Atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 117719580 Atg12; ubiquitin-like protein ATG12 isoform X1 K08336 ATG12; ubiquitin-like protein ATG12 D 117705923 Atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 117722237 Atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 117697316 Atg16l2; autophagy-related protein 16-2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2 D 117697865 Wipi2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 117710623 Wipi1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 117700262 Prkn; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31] D 117694895 E3 ubiquitin-protein ligase NRDP1-like K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 117694907 E3 ubiquitin-protein ligase NRDP1-like K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 117695353 E3 ubiquitin-protein ligase NRDP1-like K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 117696270 Rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 117710503 Clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 117708934 Pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 117718175 Parl; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 117710045 Sqstm1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1 D 117720363 Tax1bp1; tax1-binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1 D 117711384 Calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 117702984 Ambra1; activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 117703349 Atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13 D 117697702 Ulk1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 117710542 Ulk2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 117698566 Rb1cc1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 117694347 LOW QUALITY PROTEIN: heat shock protein HSP 90-beta-like K04079 HSP90A; molecular chaperone HtpG D 117695077 LOW QUALITY PROTEIN: heat shock protein HSP 90-beta-like K04079 HSP90A; molecular chaperone HtpG D 117697557 Hsp90aa1; heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG D 117721709 heat shock protein HSP 90-beta-like K04079 HSP90A; molecular chaperone HtpG D 117722670 Hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 117713330 Cdc37; hsp90 co-chaperone Cdc37 isoform X1 K09554 CDC37; cell division cycle protein 37 D 117697919 Smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 117710472 Smurf2; E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 117705396 Bnip3l; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 117695308 Fundc1; FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 117708512 Prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 117723868 Prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 117703848 Map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 117722274 LOW QUALITY PROTEIN: microtubule-associated proteins 1A/1B light chain 3B-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 117723322 Map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 117710454 Nbr1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 117697707 Tecpr1; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 117697268 Zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 117710090 Coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 117718827 Pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 117721688 C1H19orf12; protein C19orf12 homolog K23168 MPAN; protein MPAN D 117722536 protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN D 117694859 Fundc2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2 D 117706963 FUN14 domain-containing protein 2-like K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025