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Mitochondrial Biogenesis - Alligator sinensis (Chinese alligator)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 806142 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 806141 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 806131 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 806135 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 806130 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 806134 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 806133 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 806132 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 806140 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 806139 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 806136 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 806138 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 806137 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 102368495 POLRMT; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 102376972 TFAM; transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
D 102371213 TFB1M; dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 102379114 TFB2M; dimethyladenosine transferase 2, mitochondrial isoform X1 K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 102380159 MTIF2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 102385441 MTIF3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 102383163 TSFM; elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts
D 102382043 TUFM; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 102367993 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 102385312 GFM2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 102367992 MTERF3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 102369961 MTERF4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 102372240 MTERF1; LOW QUALITY PROTEIN: transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 102387348 MTERF2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 102374979 GUF1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 102376800 POP1; ribonucleases P/MRP protein subunit POP1 isoform X1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 102376506 POP4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 102372131 POP5; ribonuclease P/MRP protein subunit POP5 isoform X1 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 102369938 RPP30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 112551235 ribonuclease P protein subunit p20-like K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 102378876 RPP25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 102388351 RPP25L; ribonuclease P protein subunit p25-like protein isoform X2 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 102385858 RPP38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 102385678 RPP40; ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 102373421 TRMT10C; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 102377997 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 isoform X1 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 102382197 KIAA0391; mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 102368086 MSS51; putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 102368494 TEFM; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 102371477 PTCD1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 102371320 PTCD3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 102384555 DHX30; LOW QUALITY PROTEIN: putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 102383391 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 102373834 AFG1L; AFG1-like ATPase isoform X2 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 102372128 ATP23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 102375284 SUPV3L1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 102387394 LACTB2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 102371094 SLC25A4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 102376128 SLC25A5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 102384953 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 102387986 SLC25A31; ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 102379379 SLC25A28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 102383300 SLC25A37; mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 102369524 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 102372180 ERAL1; GTPase Era, mitochondrial K03595 era; GTPase
D 102368929 YARS; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 102383035 YARS2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 102375967 LARS; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 102388430 LARS2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 102386487 DARS2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 102388340 GARS; glycine--tRNA ligase isoform X2 K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 102376202 RARS2; probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 102385724 RARS; arginine--tRNA ligase, cytoplasmic isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 102387086 QRSL1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial isoform X1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 102375266 GATB; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 102371376 GATC; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 102367945 MTPAP; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 102370098 PDE12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 102386461 MTG1; LOW QUALITY PROTEIN: mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 102380262 NOA1; LOW QUALITY PROTEIN: nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 102372920 NSUN3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 102379078 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 isoform X2 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 102386969 RPUSD3; mitochondrial mRNA pseudouridine synthase RPUSD3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 102370100 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 102382641 RCC1L; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 102371391 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 102382653 FASTKD2; FAST kinase domain-containing protein 2, mitochondrial isoform X1 K18190 FASTKD2; FAST kinase domain-containing protein 2
D 102381688 TBRG4; FAST kinase domain-containing protein 4 isoform X1 K27756 TBRG4; FAST kinase domain-containing protein 4
D 102372961 FASTKD5; FAST kinase domain-containing protein 5, mitochondrial K27757 FASTKD5; FAST kinase domain-containing protein 5
D 102384237 CUNH12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial isoform X1 K23498 COXPD7; peptide chain release factor
D 102376872 RMND1; required for meiotic nuclear division protein 1 homolog isoform X2 K23499 RMND1; required for meiotic nuclear division protein 1
D 102386121 GRSF1; G-rich sequence factor 1 isoform X1 K24984 GRSF1; G-rich sequence factor 1
D 102383541 METTL15; probable methyltransferase-like protein 15 isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 102376893 CUNH12orf10; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 102388247 CUNH6orf203; uncharacterized protein C6orf203 homolog isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 102383875 POLG; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 102380421 PRIMPOL; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 102380410 ENDOG; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 102376892 MGME1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 102380886 EXOG; nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial
D 102370952 TWNK; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 102379486 PIF1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 102371415 SSBP1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 102369537 LOW QUALITY PROTEIN: ATPase family AAA domain-containing protein 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 102375543 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 102385294 CUNH17orf80; uncharacterized protein C17orf80 homolog isoform X1 K27759 MTNAP1; mitochondrial nucleoid-associated protein 1
D 102369077 GTPase IMAP family member 4 K27758 GIMAP1_3_5; GTPase IMAP family member 1/3/5
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 102372588 DNAJA2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 102385250 TOMM34; mitochondrial import receptor subunit TOM34 isoform X1 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 102368254 RHOT1; mitochondrial Rho GTPase 1 isoform X3 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 102368266 LOW QUALITY PROTEIN: heat shock 70 kDa protein 1A-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 102368981 heat shock 70 kDa protein II-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 102387087 HSPA8; heat shock cognate 71 kDa protein isoform X2 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 102378817 AIP; AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein
D 102383295 spore wall protein 2-like isoform X1 K17767 AIP; AH receptor-interacting protein
D 102386147 mitochondrial fission factor homolog A K28235 FATE1; fetal and adult testis-expressed transcript protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 102370385 TOMM5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
D 102388020 TOMM6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 102377586 TOMM7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 102378503 TOMM20; mitochondrial import receptor subunit TOM20 homolog isoform X1 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 102379368 TOMM22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 102378022 TOMM40L; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 102385489 TOMM40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 102368418 TOMM70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
C TOB/SAM complex
D 102378454 SAMM50; sorting and assembly machinery component 50 homolog isoform X2 K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 102383593 VDAC1; voltage-dependent anion-selective channel protein 1 isoform X1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 102381104 VDAC2; voltage-dependent anion-selective channel protein 2 isoform X1 K15040 VDAC2; voltage-dependent anion channel protein 2
D 102370144 VDAC3; voltage-dependent anion-selective channel protein 3 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 102368428 MTX2; metaxin-2 isoform X1 K17776 MTX; metaxin
D 102380400 MTX3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 102388037 MTX1; metaxin-1 K17776 MTX; metaxin
D 102369178 MYO19; unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX
D 102379916 MARC1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 102370963 TIMM9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 102381182 TIMM10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
C TIM8/13 complex
D 102368957 TIMM8B; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 102380024 TIMM8A; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
C Mitochondrial intermembrane space assembly (MIA) complex
D 102386242 CHCHD4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 102387767 GFER; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
D 112550372 FAD-linked sulfhydryl oxidase ALR-like K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 102371328 MINOS1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 102370407 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 102371532 CUNH19orf70; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 102371923 CHCHD3; MICOS complex subunit MIC19 isoform X3 K17563 CHCHD3; MICOS complex subunit MIC19
D 102382455 CHCHD6; MICOS complex subunit MIC25 isoform X2 K17564 CHCHD6; MICOS complex subunit MIC25
D 102388416 APOO; MICOS complex subunit MIC26 isoform X2 K24625 APOO; MICOS complex subunit MIC26
D 102388769 APOOL; MICOS complex subunit MIC27 isoform X3 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 102371328 MINOS1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 102370407 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
C TIM23 complex
D 102377904 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 102368634 TIMM17A; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 102380926 TIMM17B; mitochondrial import inner membrane translocase subunit Tim17-B isoform X1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 102368626 TIMM21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 102370337 TIMM50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 102378241 MCU; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 102368624 calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial
D 102377998 calcium uptake protein 1, mitochondrial-like K22827 MICU1; calcium uptake protein 1, mitochondrial
D 102388070 MICU2; calcium uptake protein 2, mitochondrial isoform X1 K22828 MICU2; calcium uptake protein 2, mitochondrial
D 102387600 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 102374655 SMDT1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 112550865 MCUR1; mitochondrial calcium uniporter regulator 1 isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 102374565 LETM1; mitochondrial proton/calcium exchanger protein isoform X2 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 102380673 IMMP1L; mitochondrial inner membrane protease subunit 1 isoform X2 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 102384824 IMMP2L; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 102369080 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A
D 102374117 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A
D 102377459 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A
D 102382674 MPC1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 102368264 MPC2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 102385341 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
D 102375436 OCIAD1; OCIA domain-containing protein 1 isoform X3 K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 102384775 TIMM44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 102370358 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 102376006 GRPEL1; grpE protein homolog 1, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE
D 102377406 GRPEL2; grpE protein homolog 2, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE
D 102385164 DNAJC19; LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 112548169 PAM16; mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 102379886 PMPCA; mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 102388493 PMPCB; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 102387822 MIPEP; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 102373513 HSPD1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 102376155 DNAJA3; dnaJ homolog subfamily A member 3, mitochondrial K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 102375735 TAMM41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 112548278 DNLZ; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 102372675 ETHE1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 102368391 POLDIP2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 102385124 CREB1; cyclic AMP-responsive element-binding protein 1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 102367993 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 102385312 GFM2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 102370562 SP1; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 102373936 YY1; transcriptional repressor protein YY1 K09201 YY; transcription factor YY
D 102367964 GABPB1; GA-binding protein subunit beta-1 isoform X6 K09454 GABPB; GA-binding protein transcription factor, beta
D 102380044 GABPB2; GA-binding protein subunit beta-2 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 102376972 TFAM; transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 102379859 NRF1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 102387558 NFE2L2; nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
C Coactivators
D 102370719 PPARGC1A; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 102378359 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 102385548 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 102384868 CRTC1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 102369497 CREBBP; CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 102371912 EP300; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 102383238 NFS1; cysteine desulfurase, mitochondrial isoform X2 K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 102369771 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 102386758 LYRM4; LYR motif-containing protein 4 isoform X2 K22069 LYRM4; LYR motif-containing protein 4
D 102377672 FDX1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 102374472 adrenodoxin-like K22071 FDX2; ferredoxin-2, mitochondrial
D 102373045 FDXR; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 102370358 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 102374365 SIL1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 102384836 ISCA1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 102386800 ISCA2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 102369407 IBA57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 102377208 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X2 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 102385795 BOLA1; bolA-like protein 1 isoform X2 K22066 BOLA1; BolA-like protein 1
D 102380438 BOLA3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 102383611 SFXN3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 102388456 SFXN1; sideroflexin-1 isoform X3 K23500 SFXN1_3; sideroflexin-1/3
D 102385756 SFXN2; sideroflexin-2 isoform X3 K23501 SFXN2; sideroflexin-2
D 102371970 SFXN5; sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 102370264 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 102377631 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 102369422 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform isoform X1 K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 102376609 DHTKD1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 102382132 FBXL4; F-box/LRR-repeat protein 4 isoform X2 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 102375077 host cell factor 1 K14966 HCFC1; host cell factor 1
D 102368359 HCFC2; host cell factor 2 K27390 HCFC2; host cell factor 2
D 102381087 HTT; huntingtin isoform X4 K04533 HD; huntingtin
D 102369254 ESRRB; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 102381098 estrogen-related receptor gamma isoform X2 K08554 NR3B3; estrogen-related receptor gamma
D 102378528 NRIP1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 102374152 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 102375567 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 102369643 SIRT1; NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 102368431 SERAC1; protein SERAC1 isoform X2 K23504 SERAC1; protein SERAC1
D 102382519 UXT; protein UXT isoform X2 K26537 UXT; protein UXT
D 102386494 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
D 102379154 GATD3A; ES1 protein homolog, mitochondrial isoform X1 K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 102383566 ES1 protein homolog, mitochondrial-like K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 102372718 TANGO2; transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2
D 102374917 CUNH2orf69; UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69
D 102382613 FAM214A; protein FAM214A isoform X1 K28528 ATOS; protein Atossa
D 102385279 FAM214B; protein FAM214B K28528 ATOS; protein Atossa
D 102381806 DDX47; probable ATP-dependent RNA helicase DDX47 isoform X1 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7]
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 102382634 NDUFAF1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 102386508 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 102385584 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 102381827 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 isoform X1 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 102380664 NDUFAF5; arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 102373804 NDUFAF6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 102377104 NDUFAF7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 102379195 ECSIT; LOW QUALITY PROTEIN: evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 102372971 ACAD9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 102384433 NUBPL; iron-sulfur protein NUBPL isoform X3 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 102385099 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 102387506 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 102370532 TIMMDC1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 106722709 SDHAF1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 112550672 SDHAF2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 102386059 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 102368153 TTC19; tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 102386210 LYRM7; complex III assembly factor LYRM7 isoform X1 K18170 LYRM7; complex III assembly factor LYRM7
D 102383391 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 102375543 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 102382231 CUNH12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 106722137 STMP1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 102384686 CMC1; COX assembly mitochondrial protein homolog isoform X2 K18171 CMC1; COX assembly mitochondrial protein 1
D 102374415 CMC2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 102370122 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 106722036 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 102367880 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 102374490 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 102369136 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 102373916 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 102382988 protoheme IX farnesyltransferase, mitochondrial-like K02257 COX10; heme o synthase [EC:2.5.1.141]
D 102383279 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 102371499 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 102378894 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 102377416 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X2 K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 112548165 forkhead box protein C1 K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 102381120 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 102386834 LOW QUALITY PROTEIN: cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 102368086 MSS51; putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 102379964 PET100; protein PET100 homolog, mitochondrial isoform X2 K18186 PET100; protein PET100, animal type
D 102377752 PET117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 102368242 mitochondrial inner membrane protein OXA1L-like K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 102370754 mitochondrial inner membrane protein OXA1L-like K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 102381244 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 102378748 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 112551887 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 102379122 translational activator of cytochrome c oxidase 1 isoform X1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 102379518 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 102371370 APOPT1; apoptogenic protein 1, mitochondrial isoform X1 K23506 APOPT1; apoptogenic protein 1
D 106722137 STMP1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 102375138 HIGD1A; HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 102387870 HIGD1C; HIG1 domain family member 1C K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
C Complex-V assembly factors
D 102370843 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 102369731 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 102388645 TMEM70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 102387588 ATP5MD; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 102386983 MFN1; mitofusin-1 isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 102374370 MFN2; mitofusin-2 isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 102386033 OPA1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 102369584 OPA3; LOW QUALITY PROTEIN: optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein
D 102371115 TRIAP1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 102376993 presenilins-associated rhomboid-like protein, mitochondrial isoform X3 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 102374149 BAK1; bcl-2 homologous antagonist/killer isoform X1 K14021 BAK; Bcl-2 homologous antagonist/killer
D 102384471 BAX; apoptosis regulator BAX isoform X1 K02159 BAX; apoptosis regulator BAX
D 102380635 DNM1L; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 102378187 FIS1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 102370284 SUMO1; small ubiquitin-related modifier 1 isoform X7 K12160 SUMO; small ubiquitin-related modifier
D 102375514 SUMO2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 102382249 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 102371701 SH3GLB1; endophilin-B1 isoform X4 K11248 SH3GLB1; endophilin-B1
D 102378700 MTCH1; mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier
D 102380457 MTCH2; mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier
D 102370223 MFF; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor
D 102376663 GDAP1L1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 102383834 GDAP1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 102380730 VAT1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 102370733 MIEF1; mitochondrial dynamics protein MID51 isoform X3 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 102370470 PLD6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 102383210 MIGA2; mitoguardin 2 isoform X1 K27289 MIGA; mitoguardin
D 102386503 MIGA1; mitoguardin 1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 102368398 ACTG1; actin, cytoplasmic 2 isoform X1 K05692 ACTB_G1; actin beta/gamma 1
D 102370707 actin, cytoplasmic type 5-like K05692 ACTB_G1; actin beta/gamma 1
D 102380881 actin, cytoplasmic type 5 K05692 ACTB_G1; actin beta/gamma 1
D 102386754 ACTB; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 102372684 NAA20; N-alpha-acetyltransferase 20 isoform X1 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 102372014 NAA25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 102372300 PHB; prohibitin K17080 PHB1; prohibitin 1
D 102374115 PHB2; prohibitin-2 K17081 PHB2; prohibitin 2
D 102369023 KTN1; kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 102380635 DNM1L; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 102368182 MYO5C; unconventional myosin-Vc K10357 MYO5; myosin V
D 102375640 unconventional myosin-Vb K10357 MYO5; myosin V
D 102376880 unconventional myosin-Vb-like isoform X1 K10357 MYO5; myosin V
D 102382119 MYO5A; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
D 102386593 XIAP; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
C Morphogenesis factors
D 102370844 SNX25; sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 102368254 RHOT1; mitochondrial Rho GTPase 1 isoform X3 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 102370407 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 102378343 MTFP1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 102386075 NEDD4; E3 ubiquitin-protein ligase NEDD4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 102385101 OXR1; oxidation resistance protein 1 isoform X3 K25437 OXR1; oxidation resistance protein 1
D 102368233 PRELID1; PRELI domain-containing protein 1, mitochondrial K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 102376467 PRELID2; PRELI domain-containing protein 2 isoform X1 K27965 PRELID2; PRELI domain-containing protein 2 mitochondrial
D 102370108 PRELID3A; PRELI domain containing protein 3A isoform X1 K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
D 102384594 PRELID3B; LOW QUALITY PROTEIN: PRELI domain containing protein 3B K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 102381230 ATG2B; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 102388712 ATG2A; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 102380811 ATG3; ubiquitin-like-conjugating enzyme ATG3 isoform X2 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 102370103 ATG4B; cysteine protease ATG4B isoform X2 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 102380359 ATG4A; cysteine protease ATG4A isoform X4 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 102384296 ATG4C; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 102384588 ATG4D; cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 102386084 ATG5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 102382555 BECN1; beclin-1 isoform X1 K08334 BECN; beclin
D 102375484 ATG7; ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 102367983 GABARAPL2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 102382529 GABARAPL1; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 102385155 GABARAP; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 102370017 ATG9A; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 102376409 ATG10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 102375610 ATG12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 102376598 ATG14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 102372195 ATG16L1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 102387727 ATG16L2; autophagy-related protein 16-2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 102372972 WIPI2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 102386150 WIPI1; WD repeat domain phosphoinositide-interacting protein 1 isoform X3 K17908 WIPI1_2; autophagy-related protein 18
D 102374835 vacuolar protein 8-like isoform X1 K08332 VAC8; vacuolar protein 8
C Parkin-dependent mechanism factors
D 102381887 PRKN; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 102368472 RNF41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 102375495 CLEC16A; protein CLEC16A isoform X5 K19513 CLEC16A; protein CLEC16A
D 106723111 PINK1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 102376993 presenilins-associated rhomboid-like protein, mitochondrial isoform X3 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 102373404 SQSTM1; sequestosome-1 isoform X2 K14381 SQSTM1; sequestosome 1
D 102387448 TAX1BP1; tax1-binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1
D 102368522 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 102372892 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 102371750 ATG13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 102372779 ULK1; LOW QUALITY PROTEIN: serine/threonine-protein kinase ULK1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 102371419 ULK2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 102384853 RB1CC1; RB1-inducible coiled-coil protein 1 isoform X4 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 102369112 HSP90AB1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 102379894 HSP90AA1; heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 102385354 CDC37; hsp90 co-chaperone Cdc37 isoform X2 K09554 CDC37; cell division cycle protein 37
D 102371977 SMURF1; E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 102387152 SMURF2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 102386525 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 102375581 FUNDC1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 102374152 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 102375567 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 102369726 MAP1LC3C; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 102377513 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 102377782 MAP1LC3A; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 102381056 MAP1LC3B; microtubule-associated proteins 1A/1B light chain 3B isoform X1 K10435 MAP1LC; microtubule-associated protein 1 light chain
D 102388014 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 102379912 NBR1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 102385953 TECPR1; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 102377993 ZFYVE1; zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 102382044 COASY; bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 102376997 CUNH19orf12; LOW QUALITY PROTEIN: protein C19orf12 homolog K23168 MPAN; protein MPAN
D 102374404 FUNDC2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
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#
#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025