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  Mitochondrial Biogenesis - Chanodichthys erythropterus (predatory carp)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 20160558 ND1; (RefSeq) NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 20160548 ND2; (RefSeq) NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 20160552 ND3; (RefSeq) NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 20160554 ND4; (RefSeq) NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 20160553 ND4L; (RefSeq) NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 20160555 ND5; (RefSeq) NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 20160556 ND6; (RefSeq) NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 20160557 CYTB; (RefSeq) cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 20160546 COX1; (RefSeq) cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 20160547 COX2; (RefSeq) cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 20160550 COX3; (RefSeq) cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 20160549 ATP8; (RefSeq) ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 20160551 ATP6; (RefSeq) ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 137027739 polrmt; (RefSeq) DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 137008261 tfam; (RefSeq) transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 137007115 tfb1m; (RefSeq) dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 137006688 tfb2m; (RefSeq) dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 137011105 mtif2; (RefSeq) translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 137034560 mtif3; (RefSeq) translation initiation factor IF-3, mitochondrial isoform X1 K02520 infC; translation initiation factor IF-3 D 137010673 tsfm; (RefSeq) elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 137017890 tufm; (RefSeq) elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 137005350 gfm1; (RefSeq) elongation factor G, mitochondrial K02355 fusA; elongation factor G D 137033818 gfm2; (RefSeq) ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 137003449 mterf4; (RefSeq) transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 137022782 mterf2; (RefSeq) transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 137037380 transcription termination factor 1a, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 137037919 mterf3; (RefSeq) transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 137018854 guf1; (RefSeq) translation factor Guf1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 137002261 pop1; (RefSeq) LOW QUALITY PROTEIN: ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 137031244 pop4; (RefSeq) ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 137026566 pop5; (RefSeq) ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 137007636 rpp30; (RefSeq) ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 137030263 pop7; (RefSeq) ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 137014789 rpp25a; (RefSeq) ribonuclease P protein subunit p25a K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 137022944 rpp25b; (RefSeq) ribonuclease P protein subunit p25b K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 137027776 rpp25l; (RefSeq) ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 137034853 rpp38; (RefSeq) ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 137003066 rpp40; (RefSeq) ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 137031868 trmt10c; (RefSeq) tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 137009352 hsd17b10; (RefSeq) 3-hydroxyacyl-CoA dehydrogenase type-2 isoform X1 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 137006449 prorp; (RefSeq) mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 137014107 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 137014222 mss51; (RefSeq) putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 137011039 tefm; (RefSeq) transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 137032739 ptcd1; (RefSeq) pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 137034173 ptcd2; (RefSeq) pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 137019328 ptcd3; (RefSeq) small ribosomal subunit protein mS39 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 137002489 dhx30; (RefSeq) ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 137010921 uqcc1; (RefSeq) ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 137006504 afg1la; (RefSeq) AFG1 like ATPase a K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 137019043 afg1lb; (RefSeq) lactation elevated protein 1 homolog B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 137024138 atp23; (RefSeq) mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 137020043 supv3l1; (RefSeq) ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 137003031 lactb2; (RefSeq) endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 137021018 slc25a5; (RefSeq) ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 137031887 slc25a4; (RefSeq) ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 137034241 si:dkey-251i10.1; (RefSeq) ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 137035849 slc25a6; (RefSeq) ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 137020856 slc25a28; (RefSeq) mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 137027343 slc25a37; (RefSeq) mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 137028879 malsu1; (RefSeq) mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 137035068 eral1; (RefSeq) GTPase Era, mitochondrial isoform X1 K03595 era; GTPase D 137015006 yars2; (RefSeq) tyrosine--tRNA ligase, mitochondrial isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 137037562 yars1; (RefSeq) tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 137012976 leucine--tRNA ligase, cytoplasmic-like K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 137029970 lars2; (RefSeq) probable leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 137002767 dars2; (RefSeq) aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 137013829 gars1; (RefSeq) glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 137012984 rars1; (RefSeq) arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 137018787 rars2; (RefSeq) probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 137006122 qrsl1; (RefSeq) glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 137032882 gatb; (RefSeq) glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 137034176 gatc; (RefSeq) glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 137007794 mtpap; (RefSeq) poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 137021373 pde12; (RefSeq) 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 137020027 mtg1; (RefSeq) mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 137023090 noa1; (RefSeq) nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 137032241 nsun3; (RefSeq) tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 137002938 nsun4; (RefSeq) 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 137021614 rpusd4; (RefSeq) pseudouridylate synthase RPUSD4, mitochondrial K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 137034813 rcc1l; (RefSeq) RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein D 137027131 ngrn; (RefSeq) neugrin K23496 NGRN; neugrin D 137035866 fastkd1; (RefSeq) FAST kinase domain-containing protein 1, mitochondrial isoform X1 K27754 FASTKD1; FAST kinase domain-containing protein 1 D 137032728 fastkd2; (RefSeq) FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 137030006 fastkd3; (RefSeq) FAST kinase domain-containing protein 3, mitochondrial isoform X1 K27755 FASTKD3; FAST kinase domain-containing protein 3 D 137027082 tbrg4; (RefSeq) FAST kinase domain-containing protein 4 K27756 TBRG4; FAST kinase domain-containing protein 4 D 137034138 FAST kinase domain-containing protein 5, mitochondrial K27757 FASTKD5; FAST kinase domain-containing protein 5 D 137034644 mtrfr; (RefSeq) mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor D 137006171 rmnd1; (RefSeq) required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 137033695 grsf1; (RefSeq) G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1 D 137030459 mettl15; (RefSeq) probable methyltransferase-like protein 15 isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 137021799 myg1; (RefSeq) UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 137020655 mtres1; (RefSeq) mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 137014999 polg; (RefSeq) DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 137011083 polg2; (RefSeq) DNA polymerase subunit gamma-2 K02333 POLG2; DNA polymerase gamma 2 D 137031770 primpol; (RefSeq) DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 137004075 histone-lysine N-methyltransferase, H3 lysine-79 specific-like K01173 ENDOG; endonuclease G, mitochondrial D 137008897 uncharacterized protein K01173 ENDOG; endonuclease G, mitochondrial D 137008950 endonuclease G, mitochondrial-like K01173 ENDOG; endonuclease G, mitochondrial D 137026259 endog; (RefSeq) endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 137020686 mgme1; (RefSeq) mitochondrial genome maintenance exonuclease 1 isoform X1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 137013951 nuclease EXOG, mitochondrial-like K15050 EXOG; nuclease EXOG, mitochondrial D 137007622 twnk; (RefSeq) twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3] D 137003518 pif1; (RefSeq) ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 137024226 ssbp1; (RefSeq) single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 137028429 atad3; (RefSeq) ATPase family AAA domain containing 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 137011471 uqcc2; (RefSeq) ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 137007591 si:dkey-21c1.4; (RefSeq) mitochondrial nucleoid-associated protein 1 isoform X1 K27759 MTNAP1; mitochondrial nucleoid-associated protein 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 137022731 dnaja2b; (RefSeq) dnaJ homolog subfamily A member 2b K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 137031260 dnaja2a; (RefSeq) dnaJ homolog subfamily A member 2a K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 137011299 tomm34; (RefSeq) mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 137011037 rhot1b; (RefSeq) mitochondrial Rho GTPase 1b isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 137017507 rhot1a; (RefSeq) mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 137004395 hsc70; (RefSeq) heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 137005049 hspa8b; (RefSeq) heat shock protein family A (Hsp70) member 8b isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 137010905 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 137011142 hsp70.3; (RefSeq) heat shock cognate 70-kd protein, tandem duplicate 3 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 137017497 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 137017498 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 137017499 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 137026442 hspa1b; (RefSeq) heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 137028700 hspa8; (RefSeq) heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 137005168 aipl1; (RefSeq) aryl-hydrocarbon-interacting protein-like 1 isoform X1 K17767 AIP; AH receptor-interacting protein D 137030443 titin homolog K17767 AIP; AH receptor-interacting protein D 137032735 aip; (RefSeq) AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein D 137012028 mitochondrial fission factor-like isoform X1 K28235 FATE1; fetal and adult testis-expressed transcript protein B Outer membrane C Transporter outer membrane (TOM) complex D 137017190 tomm5; (RefSeq) mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 D 137011473 tomm6; (RefSeq) mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 137002102 tomm7; (RefSeq) mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 137019920 tomm20a; (RefSeq) translocase of outer mitochondrial membrane 20 K17770 TOM20; mitochondrial import receptor subunit TOM20 D 137021330 tomm20b; (RefSeq) mitochondrial import receptor subunit TOM20 homolog B K17770 TOM20; mitochondrial import receptor subunit TOM20 D 137007859 tomm22; (RefSeq) mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 137034434 si:dkey-71l1.1; (RefSeq) mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40 D 137035421 tomm40; (RefSeq) mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 137037703 tomm40l; (RefSeq) mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40 D 137011313 tomm70a; (RefSeq) mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 C TOB/SAM complex D 137015001 samm50; (RefSeq) sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family D 137023808 samm50l; (RefSeq) sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family C Porin D 137012328 vdac1; (RefSeq) voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 137007574 voltage-dependent anion-selective channel protein 2-like isoform X1 K15040 VDAC2; voltage-dependent anion channel protein 2 D 137020398 vdac2; (RefSeq) voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 137026794 vdac3; (RefSeq) voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3 D 137028496 zgc:56235; (RefSeq) voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 137011293 mtx2; (RefSeq) metaxin-2 K17776 MTX; metaxin D 137034904 mtx3; (RefSeq) metaxin-3 isoform X1 K17776 MTX; metaxin D 137036341 mtx1a; (RefSeq) metaxin-1a K17776 MTX; metaxin D 137037938 mtx1b; (RefSeq) metaxin-1b K17776 MTX; metaxin D 137033768 unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX D 137006497 marc1; (RefSeq) mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 137006703 timm9; (RefSeq) mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 137032881 timm10; (RefSeq) mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 137028754 timm10b; (RefSeq) mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 137021603 timm8a; (RefSeq) mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 137034020 timm8b; (RefSeq) mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 137029226 timm13; (RefSeq) mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 137011331 chchd4b; (RefSeq) coiled-coil-helix-coiled-coil-helix domain containing 4b K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 137021010 chchd4a; (RefSeq) mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 137017763 gfer; (RefSeq) FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 137008927 micos10; (RefSeq) MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 137019331 immt; (RefSeq) MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 D 137029146 micos13; (RefSeq) MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 137014720 chchd3b; (RefSeq) coiled-coil-helix-coiled-coil-helix domain containing 3b isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 137024408 chchd3a; (RefSeq) coiled-coil-helix-coiled-coil-helix domain containing 3a isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 137009261 chchd6a; (RefSeq) MICOS complex subunit mic25a isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 137011152 chchd6b; (RefSeq) coiled-coil-helix-coiled-coil-helix domain containing 6b K17564 CHCHD6; MICOS complex subunit MIC25 D 137014274 apoob; (RefSeq) apolipoprotein O, b isoform X1 K24625 APOO; MICOS complex subunit MIC26 D 137033773 apooa; (RefSeq) apolipoprotein O, a isoform X1 K24625 APOO; MICOS complex subunit MIC26 D 137034695 apool; (RefSeq) MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 137008927 micos10; (RefSeq) MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 137019331 immt; (RefSeq) MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 137033853 timm22; (RefSeq) mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 137007695 timm23a; (RefSeq) mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 137020780 timm23b; (RefSeq) mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 137021082 timm17a; (RefSeq) mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 137027286 timm17b; (RefSeq) mitochondrial import inner membrane translocase subunit Tim17-B isoform X1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 137014143 timm21; (RefSeq) mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 137004686 timm50; (RefSeq) mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 137020746 mcu; (RefSeq) calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 137020745 micu1; (RefSeq) calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial D 137034320 micu2; (RefSeq) calcium uptake protein 2, mitochondrial isoform X1 K22828 MICU2; calcium uptake protein 2, mitochondrial D 137008133 essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial D 137031749 smdt1b; (RefSeq) single-pass membrane protein with aspartate-rich tail 1b K22830 SMDT1; essential MCU regulator, mitochondrial D 137031279 mcur1; (RefSeq) mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 137020361 letm1; (RefSeq) mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 137030856 immp1l; (RefSeq) mitochondrial inner membrane protease subunit 1 isoform X1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 137015426 immp2l; (RefSeq) mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 137028707 tmem126a; (RefSeq) transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 137020230 mpc1; (RefSeq) mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 137031991 mpc2a; (RefSeq) mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 137035802 mpc2b; (RefSeq) mitochondrial pyruvate carrier 2b K22139 MPC2; mitochondrial pyruvate carrier 2 D 137012516 chchd10; (RefSeq) coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 D 137018898 ociad1; (RefSeq) OCIA domain-containing protein 1 K28215 OCIAD1; OCIA domain-containing protein 1 B Matrix C MMC/PAM proteins D 137028068 timm44; (RefSeq) mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 137023936 hspa9; (RefSeq) stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 137012340 grpel2; (RefSeq) grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 137031294 grpel1; (RefSeq) grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 137027611 dnajc19; (RefSeq) mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 137017248 pam16; (RefSeq) mitochondrial import inner membrane translocase subunit tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 137034249 pmpca; (RefSeq) mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 137024170 pmpcb; (RefSeq) mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 137004947 mipepa; (RefSeq) mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 137028604 mipepb; (RefSeq) mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 137035329 hspd1; (RefSeq) 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 137017246 dnaja3a; (RefSeq) dnaJ heat shock protein family (Hsp40) member A3a isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 137029199 dnaja3b; (RefSeq) dnaJ heat shock protein family (Hsp40) member A3b isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 137021303 tamm41; (RefSeq) phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 137013035 dnlz; (RefSeq) DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 137028404 ethe1; (RefSeq) persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 137004712 poldip2; (RefSeq) polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 137032528 creb1a; (RefSeq) cyclic AMP-responsive element-binding protein 1a K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 137036017 creb1b; (RefSeq) cyclic AMP-responsive element-binding protein 1b K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 137005350 gfm1; (RefSeq) elongation factor G, mitochondrial K02355 fusA; elongation factor G D 137033818 gfm2; (RefSeq) ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 137021797 sp1; (RefSeq) transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1 D 137006365 yy1a; (RefSeq) transcriptional repressor protein YY1a K09201 YY; transcription factor YY D 137018665 yy1b; (RefSeq) transcriptional repressor protein YY1b isoform X1 K09201 YY; transcription factor YY D 137023517 gabpb1; (RefSeq) GA-binding protein subunit beta-1 K09454 GABPB; GA-binding protein transcription factor, beta D 137026612 gabpb2b; (RefSeq) GA-binding protein subunit beta-2b K09454 GABPB; GA-binding protein transcription factor, beta D 137037293 gabpb2a; (RefSeq) GA-binding protein subunit beta-2a isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 137008261 tfam; (RefSeq) transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 137024407 nrf1; (RefSeq) nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1 D 137035856 nfe2l2a; (RefSeq) nuclear factor erythroid 2-related factor 2a isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 137022805 mt2; (RefSeq) metallothionein-2 K14739 MT1_2; metallothionein 1/2 D 137029827 mtbl; (RefSeq) metallothionein-B-like K14739 MT1_2; metallothionein 1/2 C Coactivators D 137030043 ppargc1a; (RefSeq) peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 137020000 ppargc1b; (RefSeq) peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 137020343 pprc1; (RefSeq) peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 137003210 crtc1a; (RefSeq) CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 137021712 crtc1b; (RefSeq) CREB-regulated transcription coactivator 1b K15309 CRTC1; CREB-regulated transcription coactivator 1 D 137008167 ep300a; (RefSeq) histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 137017252 CREB-binding protein-like isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 137017372 ep300b; (RefSeq) histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 137027824 crebbpa; (RefSeq) CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 137021088 nfs1; (RefSeq) cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 137034213 iscub; (RefSeq) iron-sulfur cluster assembly enzyme b K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 137034330 iscua; (RefSeq) iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 137003205 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 137014321 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 137026252 fxn; (RefSeq) frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 137035056 fdx1b; (RefSeq) ferredoxin 1b K22070 FDX1; ferredoxin-1, mitochondrial D 137036243 fdx1; (RefSeq) adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial D 137011571 fdx2; (RefSeq) ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 137007640 fdxr; (RefSeq) NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 137023936 hspa9; (RefSeq) stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 137033952 hscb; (RefSeq) iron-sulfur cluster co-chaperone protein HscB isoform X1 K04082 hscB; molecular chaperone HscB D 137021509 sil1; (RefSeq) nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1 D 137018726 glrx5; (RefSeq) glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 137034457 isca1; (RefSeq) iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 137006769 isca2; (RefSeq) iron-sulfur cluster assembly 2 homolog, mitochondrial isoform X1 K22072 ISCA2; iron-sulfur cluster assembly 2 D 137003038 iba57; (RefSeq) putative transferase CAF17 homolog, mitochondrial isoform X1 K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 137019971 zgc:110319; (RefSeq) NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 137026638 nfu1; (RefSeq) NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 137028190 bola1; (RefSeq) bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 137030930 bola3; (RefSeq) bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 137019966 sfxn3; (RefSeq) sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 137022538 sfxn1; (RefSeq) sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 137007666 sfxn2; (RefSeq) sideroflexin-2 K23501 SFXN2; sideroflexin-2 D 137020481 sfxn4; (RefSeq) sideroflexin-4 K23502 SFXN4; sideroflexin-4 D 137019955 sfxn5a; (RefSeq) sideroflexin-5a isoform X1 K23503 SFXN5; sideroflexin-5 D 137021765 sfxn5b; (RefSeq) sideroflexin-5b K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 137014375 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 137014478 cpt1ab; (RefSeq) carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 137017593 cpt1a2b; (RefSeq) carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 137023232 cpt1b; (RefSeq) carnitine O-palmitoyltransferase 1, muscle isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 137031222 cpt1aa; (RefSeq) carnitine palmitoyltransferase 1Aa (liver) K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 137015167 dhtkd1; (RefSeq) 2-oxoadipate dehydrogenase complex component E1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 137026838 fbxl4; (RefSeq) F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 137021536 hcfc1a; (RefSeq) host cell factor 1a K14966 HCFC1; host cell factor 1 D 137026847 hcfc1b; (RefSeq) host cell factor 1b K14966 HCFC1; host cell factor 1 D 137024237 hcfc2; (RefSeq) host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2 D 137031614 htt; (RefSeq) huntingtin isoform X1 K04533 HD; huntingtin D 137012075 esrra; (RefSeq) steroid hormone receptor ERR1 isoform X1 K08552 NR3B1; estrogen-related receptor alpha D 137006846 esrrb; (RefSeq) steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 137006367 esrrga; (RefSeq) estrogen-related receptor gamma a isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 137019198 esrrgb; (RefSeq) estrogen-related receptor gamma b isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 137022534 esrrd; (RefSeq) estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma D 137004878 nrip1a; (RefSeq) nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 137028623 nrip1b; (RefSeq) nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 137019395 prkaa2; (RefSeq) 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 137034156 prkaa1; (RefSeq) 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 137028081 lonp1; (RefSeq) lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 137020319 sirt1; (RefSeq) NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 137018374 serac1; (RefSeq) protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 137026244 uxt; (RefSeq) protein UXT K26537 UXT; protein UXT D 137017910 si:ch211-153b23.5; (RefSeq) glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 137026224 gatd3l; (RefSeq) ES1 protein, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 137035477 zgc:162944; (RefSeq) glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 137035510 gatd3; (RefSeq) glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial isoform X1 K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 137033612 tango2; (RefSeq) transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2 D 137036321 c14h2orf69; (RefSeq) LOW QUALITY PROTEIN: mitochondrial protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69 D 137023137 atosa; (RefSeq) atos homolog protein A K28528 ATOS; protein Atossa D 137034481 atos homolog protein B K28528 ATOS; protein Atossa D 137017015 ddx47; (RefSeq) probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7] B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 137020678 ndufaf1; (RefSeq) complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 137026945 ndufaf2; (RefSeq) NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 137028440 ndufaf3; (RefSeq) NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 137018707 ndufaf4; (RefSeq) NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 137031594 ndufaf5; (RefSeq) arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 137032714 ndufaf6; (RefSeq) NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 137019340 ndufaf7; (RefSeq) protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 137008160 ndufaf8; (RefSeq) NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 137029923 ecsit; (RefSeq) evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 137021520 acad9; (RefSeq) complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 137006495 nubpl; (RefSeq) iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning D 137029519 foxred1; (RefSeq) FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 137006124 rtn4ip1; (RefSeq) reticulon-4-interacting protein 1 homolog, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 137032669 timmdc1; (RefSeq) complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 137012581 sdhaf1; (RefSeq) succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 137030300 sdhaf2; (RefSeq) succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 137035980 bcs1l; (RefSeq) mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 137002779 ttc19; (RefSeq) tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 137027534 lyrm7; (RefSeq) complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 137010921 uqcc1; (RefSeq) ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 137011471 uqcc2; (RefSeq) ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 137029654 uqcc3; (RefSeq) ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 137014303 uqcc4; (RefSeq) protein CCSMST1-like K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 137009819 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 137014647 uqcc6; (RefSeq) ubiquinol-cytochrome-c reductase complex assembly factor 6 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 137024424 stmp1; (RefSeq) short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 137001969 cmc1; (RefSeq) COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 137022621 cmc2; (RefSeq) COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 137003514 coa1; (RefSeq) cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1 D 137007767 coa3a; (RefSeq) cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 137029572 coa4; (RefSeq) cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 137036067 coa5; (RefSeq) cytochrome c oxidase assembly factor 5 isoform X1 K18178 COA5; cytochrome c oxidase assembly factor 5 D 137023798 coa6; (RefSeq) cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 137018738 coa7; (RefSeq) cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 137007691 cox10; (RefSeq) protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 137007489 cox11; (RefSeq) cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 137028008 cox14; (RefSeq) cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14 D 137020819 cox15; (RefSeq) cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 137020169 cox16; (RefSeq) cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 137036399 cox17; (RefSeq) cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 137017568 cox18; (RefSeq) cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18 D 137007928 cox19; (RefSeq) cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 137020194 cox20; (RefSeq) cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 137014107 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 137014222 mss51; (RefSeq) putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 137013001 pet100; (RefSeq) protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 137027814 pet117; (RefSeq) protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 137029886 oxa1l; (RefSeq) mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 137033978 surf1; (RefSeq) surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 137017906 sco1; (RefSeq) protein SCO1 homolog, mitochondrial isoform X1 K07152 SCO1; protein SCO1 D 137023939 sco2; (RefSeq) protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 137007976 taco1; (RefSeq) translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 137020470 lrpprc; (RefSeq) leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 137019981 coa8; (RefSeq) cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1 D 137024424 stmp1; (RefSeq) short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 137009819 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 137002566 higd1a; (RefSeq) HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 137022958 higd2a; (RefSeq) HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial C Complex-V assembly factors D 137029118 atpaf1; (RefSeq) ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 137008345 atpaf2; (RefSeq) ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 137002795 tmem70; (RefSeq) transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 137018348 atp5mj; (RefSeq) ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid D 137031841 atp5md; (RefSeq) ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 137003414 mfn1a; (RefSeq) LOW QUALITY PROTEIN: mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 137021372 mfn1b; (RefSeq) mitofusin-1b K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 137027314 mfn2; (RefSeq) mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 137010972 opa1; (RefSeq) dynamin-like GTPase OPA1, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 137022961 opa3; (RefSeq) optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein D 137028482 triap1; (RefSeq) TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 137004536 parlb; (RefSeq) presenilin-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 137017735 apoptosis regulator BAX-like isoform X1 K02159 BAX; apoptosis regulator BAX D 137030078 zgc:153993; (RefSeq) apoptosis regulator BAX isoform X1 K02159 BAX; apoptosis regulator BAX D 137014602 dnm1l; (RefSeq) dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 137027335 si:dkey-32e23.4; (RefSeq) dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 137030255 fis1; (RefSeq) mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 137033686 mitochondrial fission 1 protein-like isoform X1 K17969 FIS1; mitochondrial fission 1 protein D 137010620 sumo3a; (RefSeq) small ubiquitin-related modifier 3-like isoform X1 K12160 SUMO; small ubiquitin-related modifier D 137010922 sumo2a; (RefSeq) small ubiquitin like modifier 2a K12160 SUMO; small ubiquitin-related modifier D 137011050 sumo1; (RefSeq) small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 137017201 sumo2b; (RefSeq) small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 137035983 sumo3b; (RefSeq) small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 137003405 sh3glb1b; (RefSeq) endophilin-B1b isoform X1 K11248 SH3GLB1; endophilin-B1 D 137014047 sh3glb1a; (RefSeq) endophilin-B1a isoform X1 K11248 SH3GLB1; endophilin-B1 D 137030391 mtch2; (RefSeq) mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier D 137002668 mffb; (RefSeq) mitochondrial fission factor homolog A K22076 MFF; mitochondrial fission factor D 137004658 mffa; (RefSeq) mitochondrial fission factor homolog B isoform X1 K22076 MFF; mitochondrial fission factor D 137009479 gdap1l1; (RefSeq) ganglioside-induced differentiation-associated protein 1-like 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 137014148 gdap1; (RefSeq) ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 137017439 vat1; (RefSeq) synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 137017369 mief1; (RefSeq) mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 137031961 mief2; (RefSeq) mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 137032368 pld6; (RefSeq) mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 137003549 miga1; (RefSeq) mitoguardin 1 K27289 MIGA; mitoguardin D 137012464 miga2; (RefSeq) mitoguardin 2 isoform X1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 137017775 actb2; (RefSeq) actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 137032175 actb1; (RefSeq) actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 137018612 naa20; (RefSeq) N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 137028493 naa25; (RefSeq) N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 137010933 phb; (RefSeq) prohibitin K17080 PHB1; prohibitin 1 D 137002575 phb2a; (RefSeq) prohibitin-2a K17081 PHB2; prohibitin 2 D 137010781 phb2b; (RefSeq) prohibitin-2b isoform X1 K17081 PHB2; prohibitin 2 D 137006117 ktn1; (RefSeq) kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 137014602 dnm1l; (RefSeq) dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 137027335 si:dkey-32e23.4; (RefSeq) dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 137012463 myo5b; (RefSeq) unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V D 137014702 myo5c; (RefSeq) unconventional myosin-Vc isoform X1 K10357 MYO5; myosin V D 137015607 myo5ab; (RefSeq) unconventional myosin-Va isoform X1 K10357 MYO5; myosin V D 137023136 myo5aa; (RefSeq) unconventional myosin-Va K10357 MYO5; myosin V D 137027741 si:dkey-110c1.10; (RefSeq) unconventional myosin-Va isoform X1 K10357 MYO5; myosin V D 137020368 xiap; (RefSeq) E3 ubiquitin-protein ligase XIAP isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 137004620 diabloa; (RefSeq) diablo, IAP-binding mitochondrial protein a isoform X1 K10522 DIABLO; diablo D 137012556 diablob; (RefSeq) diablo, IAP-binding mitochondrial protein b K10522 DIABLO; diablo C Morphogenesis factors D 137026001 snx25; (RefSeq) sorting nexin-25 K17887 SNX25; sorting nexin-25 D 137011037 rhot1b; (RefSeq) mitochondrial Rho GTPase 1b isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 137017507 rhot1a; (RefSeq) mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 137019331 immt; (RefSeq) MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 D 137035107 mtfp1; (RefSeq) mitochondrial fission process protein 1 isoform X1 K17981 MTFP1; mitochondrial fission process protein 1 D 137031630 dap3; (RefSeq) 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 137023475 nedd4a; (RefSeq) E3 ubiquitin-protein ligase NEDD4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 137036443 oxr1a; (RefSeq) oxidation resistance protein 1a isoform X1 K25437 OXR1; oxidation resistance protein 1 D 137037826 oxr1b; (RefSeq) oxidation resistance protein 1b isoform X1 K25437 OXR1; oxidation resistance protein 1 D 137037538 msto1; (RefSeq) protein misato homolog 1 K27320 MSTO1; protein misato D 137009325 PRELI domain-containing protein 1, mitochondrial-like K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial D 137019341 prelid1a; (RefSeq) PRELI domain containing 1a K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial D 137011592 prelid3b; (RefSeq) PRELI domain containing protein 3B isoform X1 K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial D 137027300 prelid3a; (RefSeq) PRELI domain containing protein 3A isoform X1 K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial B Mitophagy factors C Autophagy-related proteins D 137006156 atg2b; (RefSeq) autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2 D 137019002 atg2a; (RefSeq) autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2 D 137011544 atg3; (RefSeq) ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 137009034 cysteine protease atg4da-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 137010756 atg4b; (RefSeq) cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 137010769 atg4c; (RefSeq) cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 137012503 atg4a; (RefSeq) cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 137033085 atg4da; (RefSeq) cysteine protease atg4da isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 137024246 atg5; (RefSeq) autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 137007804 becn1; (RefSeq) beclin-1 isoform X1 K08334 BECN; beclin D 137021813 atg7; (RefSeq) ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 137015530 gabarapl2; (RefSeq) gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 137030054 gabarapb; (RefSeq) GABA(A) receptor-associated protein b K08341 GABARAP; GABA(A) receptor-associated protein D 137031916 zgc:92606; (RefSeq) gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 137034798 gabarapa; (RefSeq) GABA(A) receptor-associated protein a K08341 GABARAP; GABA(A) receptor-associated protein D 137011362 atg9a; (RefSeq) autophagy-related protein 9A isoform X1 K17907 ATG9; autophagy-related protein 9 D 137013453 atg9b; (RefSeq) autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9 D 137028573 atg10; (RefSeq) ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 137025505 atg12; (RefSeq) ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12 D 137006933 atg14; (RefSeq) beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 137004581 atg16l1; (RefSeq) autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 137004535 protein Atg16l2-like K20868 ATG16L2; autophagy-related protein 16-2 D 137007498 WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 137017709 wipi1; (RefSeq) WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 137017781 wipi2; (RefSeq) WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 137020782 prkn; (RefSeq) E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31] D 137009043 rnf41; (RefSeq) E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 137017516 clec16a; (RefSeq) protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 137008932 pink1; (RefSeq) serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 137004536 parlb; (RefSeq) presenilin-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 137019265 sqstm1; (RefSeq) sequestosome-1 K14381 SQSTM1; sequestosome 1 D 137031301 tax1bp1b; (RefSeq) tax1-binding protein 1 homolog B isoform X1 K21347 TAX1BP1; Tax1-binding protein 1 D 137037302 tax1bp1a; (RefSeq) tax1-binding protein 1 homolog A K21347 TAX1BP1; Tax1-binding protein 1 D 137007979 calcoco2; (RefSeq) calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 137014611 ambra1b; (RefSeq) activating molecule in BECN1-regulated autophagy protein 1B K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 D 137031308 ambra1a; (RefSeq) activating molecule in BECN1-regulated autophagy protein 1A isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 137031311 atg13; (RefSeq) autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13 D 137012583 ulk1b; (RefSeq) serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 137027191 ulk1a; (RefSeq) serine/threonine-protein kinase ULK1a K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 137004293 ulk2; (RefSeq) serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 137013533 rb1cc1; (RefSeq) RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 137019229 hsp90ab1; (RefSeq) heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 137019271 hsp90aa1.2; (RefSeq) heat shock protein 90, alpha (cytosolic), class A member 1, tandem duplicate 2 isoform X1 K04079 HSP90A; molecular chaperone HtpG D 137019273 hsp90aa1.1; (RefSeq) heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG D 137032089 cdc37; (RefSeq) hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 137017363 smurf2; (RefSeq) E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 137017777 smurf1; (RefSeq) E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 137026820 bnip3la; (RefSeq) BCL2 interacting protein 3 like a K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 137028820 bnip3lb; (RefSeq) BCL2 interacting protein 3 like b K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 137011734 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1 D 137035970 fundc1; (RefSeq) FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 137019395 prkaa2; (RefSeq) 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 137034156 prkaa1; (RefSeq) 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 137015064 map1lc3b; (RefSeq) microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 137020908 map1lc3c; (RefSeq) microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 137021521 map1lc3a; (RefSeq) microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 137021796 map1lc3cl; (RefSeq) microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 137008264 nbr1a; (RefSeq) NBR1 autophagy cargo receptor a K17987 NBR1; next to BRCA1 gene 1 protein D 137017637 nbr1b; (RefSeq) next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 137007885 tecpr1a; (RefSeq) tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 137013281 tecpr1b; (RefSeq) tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 137004952 si:ch211-11n16.2; (RefSeq) zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 137018994 zfyve1; (RefSeq) zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 137014160 coasy; (RefSeq) bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 137029043 pla2g6; (RefSeq) 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 137023271 zgc:112052; (RefSeq) protein C19orf12 homolog K23168 MPAN; protein MPAN D 137030331 protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN D 137030363 zgc:101715; (RefSeq) protein C19orf12 homolog-like isoform X1 K23168 MPAN; protein MPAN D 137030454 protein C19orf12 homolog K23168 MPAN; protein MPAN D 137031242 si:ch211-260e23.8; (RefSeq) protein C19orf12 homolog K23168 MPAN; protein MPAN D 137012613 fundc2; (RefSeq) FUN14 domain-containing protein 2 isoform X1 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025