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Mitochondrial Biogenesis - Colossoma macropomum (tambaqui)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 118818921 polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 118809177 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 118823243 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 118824164 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 118808126 mtif2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 118814823 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 118808275 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 118805355 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 118797211 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 118814365 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 118797255 mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 118805644 mterf3; transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 118812783 transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 118818382 mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 118806414 guf1; translation factor Guf1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 118800423 pop1; LOW QUALITY PROTEIN: ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 118817656 pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 118813098 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 118809563 rpp30; ribonuclease P protein subunit p30 isoform X1 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 118826579 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 118798808 rpp25l; LOW QUALITY PROTEIN: ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 118811310 rpp25a; ribonuclease P protein subunit p25a K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 118817835 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 118798824 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 118801998 rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 118797852 trmt10c; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 118822580 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 118823765 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 118813219 mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 118814808 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 118808609 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 118798269 ptcd1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 118814377 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 118807320 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 118825792 dhx30; ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 118808693 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 118815902 afg1lb; lactation elevated protein 1 homolog B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 118823432 afg1la; AFG1 like ATPase a isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 118812253 atp23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 118810586 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 118801966 lactb2; endoribonuclease LACTB2 isoform X1 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 118807177 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 118807507 ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 118814835 si:dkey-251i10.1; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 118817054 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 118819751 slc25a6; ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 118810396 slc25a28; mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 118813290 slc25a37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 118820903 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 118814779 eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 118805517 yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 118811851 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 118800378 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 118820049 lars1b; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 118826420 dars2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 118798956 gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 118816029 rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 118819987 rars1; LOW QUALITY PROTEIN: arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 118823504 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 118817118 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 118827797 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 118809320 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 118799946 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 118810612 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 118821698 noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 118803001 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 118797040 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 118799479 rpusd4; mitochondrial RNA pseudouridine synthase rpusd4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 118814335 rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 118813783 ngrn; neugrin K23496 NGRN; neugrin
D 118808333 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 118807057 fastkd1; FAST kinase domain-containing protein 1, mitochondrial K27754 FASTKD1; FAST kinase domain-containing protein 1
D 118802324 fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 118825798 fastkd3; FAST kinase domain-containing protein 3, mitochondrial isoform X1 K27755 FASTKD3; FAST kinase domain-containing protein 3
D 118799052 tbrg4; FAST kinase domain-containing protein 4 isoform X1 K27756 TBRG4; FAST kinase domain-containing protein 4
D 118814853 FAST kinase domain-containing protein 5, mitochondrial K27757 FASTKD5; FAST kinase domain-containing protein 5
D 118827215 cunh12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor
D 118823311 rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 118826853 grsf1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1
D 118817633 mettl15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 118799364 myg1; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 118811015 mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 118811577 polg; LOW QUALITY PROTEIN: DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 118807941 polg2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 118816855 primpol; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 118813831 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 118810910 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 118821131 nuclease EXOG, mitochondrial-like K15050 EXOG; nuclease EXOG, mitochondrial
D 118809383 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 118797145 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 118812237 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 118799813 atad3; ATPase family AAA domain containing 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 118808313 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 118809366 si:dkey-21c1.4; uncharacterized protein si:dkey-21c1.4 K27759 MTNAP1; mitochondrial nucleoid-associated protein 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 118817626 dnaja2a; dnaJ homolog subfamily A member 2a K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 118818563 dnaja2b; dnaJ homolog subfamily A member 2b K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 118808700 tomm34; mitochondrial import receptor subunit TOM34 isoform X1 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 118805683 rhot1a; mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 118808610 rhot1b; mitochondrial Rho GTPase 1b isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 118800213 hspa8b; heat shock protein family A (Hsp70) member 8b K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 118803729 hsc70; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 118813786 hspa1b; LOW QUALITY PROTEIN: heat shock 70 kDa protein 1B K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 118821360 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 118821361 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 118821362 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 118821363 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 118824749 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 118824892 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 118801427 aipl1; LOW QUALITY PROTEIN: aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 118807106 golgin subfamily A member 6-like protein 22 K17767 AIP; AH receptor-interacting protein
D 118810802 AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein
D 118819898 mitochondrial fission factor-like isoform X1 K28235 FATE1; fetal and adult testis-expressed transcript protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 118807280 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
D 118808315 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 118806160 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 118810732 tomm20a; translocase of outer mitochondrial membrane 20 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 118818788 tomm20b; mitochondrial import receptor subunit TOM20 homolog B K17770 TOM20; mitochondrial import receptor subunit TOM20
D 118800250 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 118806052 tomm40l; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 118814973 si:dkey-71l1.1; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 118823166 tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 118808021 tomm70a; mitochondrial import receptor subunit TOM70 isoform X1 K17768 TOM70; mitochondrial import receptor subunit TOM70
C TOB/SAM complex
D 118806737 samm50; sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family
D 118812561 samm50l; sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 118820044 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 118809001 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2
D 118810340 vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 118813513 vdac3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
D 118824602 zgc:56235; voltage-dependent anion-selective channel protein 2 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 118805250 mtx1b; metaxin-1b K17776 MTX; metaxin
D 118807815 mtx2; metaxin-2 K17776 MTX; metaxin
D 118816776 mtx1a; metaxin-1a K17776 MTX; metaxin
D 118827521 mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 118814770 unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX
D 118823255 marc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 118823763 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 118810558 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
C TIM8/13 complex
D 118807091 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 118814741 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 118818953 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 118799963 chchd4a; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 118805697 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 118799593 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 118821934 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 118807319 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 118819469 micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 118811614 chchd3b; coiled-coil-helix-coiled-coil-helix domain containing 3b isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 118812588 chchd3a; coiled-coil-helix-coiled-coil-helix domain containing 3a isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 118808388 chchd6b; coiled-coil-helix-coiled-coil-helix domain containing 6b isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 118821926 chchd6a; MICOS complex subunit mic25a isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 118799065 apoob; apolipoprotein O, b K24625 APOO; MICOS complex subunit MIC26
D 118814942 apooa; apolipoprotein O, a isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 118807262 MICOS complex subunit MIC27-like K24626 APOOL; MICOS complex subunit MIC27
D 118814420 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 118799593 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 118821934 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 118807319 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 118802458 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 118809359 timm23a; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 118810199 timm23b; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 118799644 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 118813633 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 118799019 timm21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 118801001 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 118810162 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 118810164 micu1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 118814501 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 118810855 calcium uniporter regulatory subunit MCUb, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 118800348 essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial
D 118800621 essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial
D 118805880 essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial
D 118826239 mcur1; mitochondrial calcium uniporter regulator 1 isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 118810286 letm1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 118819187 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 118806750 immp2l; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 118824596 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 118816722 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 118802027 mpc2a; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 118816047 mpc2b; mitochondrial pyruvate carrier 2b K22139 MPC2; mitochondrial pyruvate carrier 2
D 118820653 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
D 118815376 ociad1; OCIA domain-containing protein 1 K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 118797426 mitochondrial import inner membrane translocase subunit TIM44-like K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 118819215 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 118807226 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 118819799 grpel2; grpE protein homolog 2, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE
D 118825646 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 118818785 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
C Other matrix factors
D 118827203 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 118812008 pmpcb; LOW QUALITY PROTEIN: mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 118803038 mipepa; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 118824611 mipepb; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 118812092 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 118804654 dnaja3b; dnaJ heat shock protein family (Hsp40) member A3b K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 118821426 dnaja3a; dnaJ heat shock protein family (Hsp40) member A3a isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 118799954 tamm41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 118820154 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 118798912 ethe1; persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 118801366 poldip2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
D 118814793 polymerase delta-interacting protein 2-like isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 118803049 creb1a; cyclic AMP-responsive element-binding protein 1a K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 118808824 creb1b; cyclic AMP-responsive element-binding protein 1b K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 118797211 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 118814365 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 118799824 sp1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1
D 118815581 yy1b; transcriptional repressor protein YY1b K09201 YY; transcription factor YY
D 118823153 yy1a; LOW QUALITY PROTEIN: transcriptional repressor protein YY1a K09201 YY; transcription factor YY
D 118804022 gabpb1; GA-binding protein subunit beta-1 K09454 GABPB; GA-binding protein transcription factor, beta
D 118805206 gabpb2a; GA-binding protein subunit beta-2a K09454 GABPB; GA-binding protein transcription factor, beta
D 118809177 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 118812245 nrf1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1
D 118805823 nfe2l2a; nuclear factor erythroid 2-related factor 2a K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 118817951 metallothionein K14739 MT1_2; metallothionein 1/2
D 118817952 metallothionein-like K14739 MT1_2; metallothionein 1/2
D 118817953 metallothionein-like K14739 MT1_2; metallothionein 1/2
D 118818296 metallothionein-like K14739 MT1_2; metallothionein 1/2
D 118818297 metallothionein K14739 MT1_2; metallothionein 1/2
D 118819224 mtbl; metallothionein-B-like K14739 MT1_2; metallothionein 1/2
C Coactivators
D 118825477 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 118806851 ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 118818644 crtc1b; CREB-regulated transcription coactivator 1b isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 118804602 LOW QUALITY PROTEIN: CREB-binding protein-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 118805374 ep300b; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 118809498 ep300a; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 118799942 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 118802445 iscub; LOW QUALITY PROTEIN: iron-sulfur cluster assembly enzyme b K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 118826910 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 118816105 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 118813841 fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 118798427 adrenodoxin-like K22070 FDX1; ferredoxin-1, mitochondrial
D 118810563 fdx1; adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial
D 118815026 fdx1b; ferredoxin 1b K22070 FDX1; ferredoxin-1, mitochondrial
D 118807901 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 118809110 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 118807226 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 118827238 hscb; iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 118807231 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 118815970 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 118826911 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 118823251 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 118826339 iba57; putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 118810330 zgc:110319; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 118813266 nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 118799069 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 118819488 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 118810318 sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 118812170 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 118809377 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2
D 118810630 sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4
D 118806820 sfxn5b; sideroflexin-5b K23503 SFXN5; sideroflexin-5
D 118810299 sfxn5a; sideroflexin-5a isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 118800502 cpt1cb; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 118811541 cpt1ab; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 118817531 cpt1aa; LOW QUALITY PROTEIN: carnitine palmitoyltransferase 1Aa (liver) K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 118817818 cpt1b; LOW QUALITY PROTEIN: carnitine O-palmitoyltransferase 1, muscle isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 118822381 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 118811883 dhtkd1; LOW QUALITY PROTEIN: probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 118797150 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 118799274 hcfc1a; host cell factor 1a K14966 HCFC1; host cell factor 1
D 118813883 hcfc1b; host cell factor 1b K14966 HCFC1; host cell factor 1
D 118812555 hcfc2; host cell factor 2 K27390 HCFC2; host cell factor 2
D 118810775 htt; huntingtin isoform X1 K04533 HD; huntingtin
D 118819791 esrra; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 118823865 esrrb; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 118815169 esrrgb; estrogen-related receptor gamma b K08554 NR3B3; estrogen-related receptor gamma
D 118817990 esrrd; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma
D 118823968 esrrga; estrogen-related receptor gamma a K08554 NR3B3; estrogen-related receptor gamma
D 118804117 nrip1a; LOW QUALITY PROTEIN: nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 118824388 nrip1b; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 118802406 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 118815456 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 118818869 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 118810738 sirt1; NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 118815707 serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 118812960 uxt; protein UXT K26537 UXT; protein UXT
D 118804961 zgc:162944; glutamine amidotransferase-like class 1 domain-containing protein 3A, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 118807359 si:ch211-153b23.5; glutamine amidotransferase-like class 1 domain-containing protein 3A, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 118810467 gatd3a; glutamine amidotransferase-like class 1 domain-containing protein 3A, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 118813466 es1; ES1 protein, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 118827145 tango2; transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2
D 118801544 cunh2orf69; UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69
D 118818267 fam214a; protein FAM214A K28528 ATOS; protein Atossa
D 118827207 protein FAM214B K28528 ATOS; protein Atossa
D 118805895 ddx47; probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7]
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 118810995 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 118813859 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 118799393 ndufaf3; LOW QUALITY PROTEIN: NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 118816052 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 118797909 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 118821659 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 118816192 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 118808840 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 118826698 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 118799369 acad9; complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 118823587 nubpl; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 118824254 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 118823505 rtn4ip1; reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 118798317 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 118820624 sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 118819394 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 118807254 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 118826426 ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 118824634 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 118808693 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 118808313 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 118824289 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 118822092 cunh16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 118821984 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 118806388 cunh12orf73; protein BRAWNIN K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 118812625 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 118798797 cmc1; COX assembly mitochondrial protein homolog isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1
D 118817928 cmc2; COX assembly mitochondrial protein 2 homolog isoform X1 K18172 CMC2; COX assembly mitochondrial protein 2
D 118825908 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 118809765 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 118800895 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 118827254 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 118812242 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 118815429 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 118809077 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 118809336 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 118799285 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 118816739 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 118811054 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 118799882 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 118821712 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 118808865 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 118810109 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 118813219 mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 118814808 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 118806129 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 118804648 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 118826709 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 118802410 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 118821688 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 118812056 LOW QUALITY PROTEIN: protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 118809703 translational activator of cytochrome c oxidase 1 isoform X1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 118810233 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 118810358 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1
D 118812625 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 118821984 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 118820438 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
D 118799473 HIG1 domain family member 1C-like K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 118826377 higd1a; HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 118801268 higd2a; HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial
C Complex-V assembly factors
D 118819176 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 118809598 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 118797120 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 118815534 atp5mpl; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 118798283 atp5md; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 118809944 ATP synthase membrane subunit DAPIT, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 118797087 mfn1a; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 118818779 mfn1b; mitofusin-1b isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 118813604 mfn2; LOW QUALITY PROTEIN: mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 118808203 opa1; dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 118818342 opa3; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 118824864 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 118796801 parla; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 118798606 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 118819120 zgc:153993; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 118821229 baxa; BCL2 associated X, apoptosis regulator a K02159 BAX; apoptosis regulator BAX
D 118806770 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 118813277 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 118814953 mitochondrial fission 1 protein-like K17969 FIS1; mitochondrial fission 1 protein
D 118826208 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 118805332 sumo2b; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 118807809 sumo3a; small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier
D 118807838 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 118808135 sumo2a; small ubiquitin like modifier 2a K12160 SUMO; small ubiquitin-related modifier
D 118797244 sh3glb1b; endophilin-B1b isoform X1 K11248 SH3GLB1; endophilin-B1
D 118817387 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 118797264 mffb; mitochondrial fission factor homolog A K22076 MFF; mitochondrial fission factor
D 118799010 mffa; mitochondrial fission factor homolog B isoform X1 K22076 MFF; mitochondrial fission factor
D 118799174 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 118822550 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 118809636 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 118821773 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 118798012 mief2; mitochondrial dynamics protein MID49 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 118805372 mief1; mitochondrial dynamics protein MID51 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 118804351 pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 118819687 miga2; mitoguardin 2 K27289 MIGA; mitoguardin
D 118826039 miga1; mitoguardin 1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 118798271 actb1; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 118805712 actb2; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 118820883 actin, cytoplasmic-like K05692 ACTB_G1; actin beta/gamma 1
D 118815802 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 118824568 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 118821381 phb; prohibitin K17080 PHB1; prohibitin 1
D 118797110 phb2a; prohibitin-2a K17081 PHB2; prohibitin 2
D 118807999 phb2b; prohibitin-2b isoform X1 K17081 PHB2; prohibitin 2
D 118824082 ktn1; kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 118806770 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 118813277 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 118803991 myo5aa; unconventional myosin-Va K10357 MYO5; myosin V
D 118811901 myo5ab; LOW QUALITY PROTEIN: unconventional myosin-Va K10357 MYO5; myosin V
D 118811902 myo5c; LOW QUALITY PROTEIN: unconventional myosin-Vc K10357 MYO5; myosin V
D 118818692 si:dkey-110c1.10; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 118819731 myo5b; LOW QUALITY PROTEIN: unconventional myosin-Vb K10357 MYO5; myosin V
D 118806894 E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 118799288 diabloa; diablo, IAP-binding mitochondrial protein a isoform X1 K10522 DIABLO; diablo
D 118820425 diablob; diablo, IAP-binding mitochondrial protein b K10522 DIABLO; diablo
C Morphogenesis factors
D 118806931 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25
D 118805683 rhot1a; mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 118808610 rhot1b; mitochondrial Rho GTPase 1b isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 118807319 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 118814540 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 118825417 dap3; 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29
D 118817877 nedd4a; LOW QUALITY PROTEIN: E3 ubiquitin-protein ligase NEDD4a K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 118799198 oxr1a; LOW QUALITY PROTEIN: oxidation resistance protein 1a K25437 OXR1; oxidation resistance protein 1
D 118812764 msto1; protein misato homolog 1 K27320 MSTO1; protein misato
D 118802064 PRELI domain-containing protein 1, mitochondrial-like isoform X1 K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 118807323 prelid1a; PRELI domain containing 1a K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 118810748 PRELI domain-containing protein 1, mitochondrial-like isoform X1 K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 118808620 prelid3b; PRELI domain containing protein 3B K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
D 118814250 prelid3a; PRELI domain containing protein 3A K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 118806907 atg2a; autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 118823346 atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 118808081 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 118798163 atg4da; cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 118805323 atg4db; cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 118807970 atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 118808049 atg4b; cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 118820025 atg4a; cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 118796986 atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 118809639 becn1; beclin-1 K08334 BECN; beclin
D 118799506 atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 118806558 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 118814956 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 118824886 zgc:92606; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 118826752 gabarapb; GABA(A) receptor-associated protein b K08341 GABARAP; GABA(A) receptor-associated protein
D 118807805 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 118822660 atg9b; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 118824565 atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 118814353 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 118824226 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 118798524 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 118802426 protein Atg16l2 K20868 ATG16L2; autophagy-related protein 16-2
D 118805718 wipi2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
D 118820927 wipi1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 118816100 vacuolar protein 8-like K08332 VAC8; vacuolar protein 8
C Parkin-dependent mechanism factors
D 118810201 prkn; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 118822336 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 118820929 clec16a; protein CLEC16A K19513 CLEC16A; protein CLEC16A
D 118822289 pink1; LOW QUALITY PROTEIN: serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 118796801 parla; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 118798606 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 118807315 sqstm1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1
D 118805840 tax1bp1a; tax1-binding protein 1 homolog A K21347 TAX1BP1; Tax1-binding protein 1
D 118816554 tax1bp1b; tax1-binding protein 1 homolog B isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 118809479 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 118811891 ambra1b; LOW QUALITY PROTEIN: activating molecule in BECN1-regulated autophagy protein 1b K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
D 118817358 ambra1a; activating molecule in BECN1-regulated autophagy protein 1a isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 118817368 atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 118813117 ulk1a; serine/threonine-protein kinase ULK1a K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 118820416 ulk1b; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 118800916 ulk2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 118822709 rb1cc1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 118815595 hsp90aa1.2; heat shock protein 90, alpha (cytosolic), class A member 1, tandem duplicate 2 K04079 HSP90A; molecular chaperone HtpG
D 118815596 hsp90aa1.1; heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG
D 118815825 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 118804448 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 118805716 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 118807936 E3 ubiquitin-protein ligase SMURF2-like isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 118821128 smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 118813460 bnip3la; BCL2 interacting protein 3 like a K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 118824345 bnip3lb; BCL2 interacting protein 3 like b K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 118808104 FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
D 118817334 fundc1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 118802406 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 118815456 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 118799875 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 118806541 map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 118806824 map1lc3cl; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 118819018 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 118809466 nbr1a; NBR1 autophagy cargo receptor a K17987 NBR1; next to BRCA1 gene 1 protein
D 118821342 nbr1b; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 118809589 tecpr1a; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 118821583 tecpr1b; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 118799170 si:ch211-11n16.2; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 118815686 zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 118822613 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 118804609 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 118817652 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 118818158 zgc:112052; protein C19orf12 homolog K23168 MPAN; protein MPAN
D 118820427 fundc2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025