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Mitochondrial Biogenesis - Cynoglossus semilaevis (tongue sole)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 7996493 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 7996492 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 7996486 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 7996488 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 7996487 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 7996489 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 7996490 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 7996491 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 7996481 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 7996482 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 7996485 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 7996483 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 7996484 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 103399915 polrmt; DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 103381843 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 103383511 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 103379002 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 103383412 mtif2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 103381177 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 103385964 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 103392980 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 103378460 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 103390000 gfm2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 103380399 transcription termination factor 2, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 103382560 transcription termination factor 2, mitochondrial-like isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 103394424 mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 103395995 transcription termination factor 4, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 103391139 guf1; translation factor GUF1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 103388647 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 103387800 pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 103396928 ribonuclease P/MRP protein subunit POP5-like K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 103398100 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 103382269 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 103391095 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 103378985 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 103388092 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 103388180 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 103398741 rpp40; ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 103378890 trmt10c; mitochondrial ribonuclease P protein 1 K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 103385214 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 103377783 kiaa0391; mitochondrial ribonuclease P protein 3 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 103381990 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 103381991 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 103384151 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 103383492 pentatricopeptide repeat-containing protein 1, mitochondrial-like K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 103390077 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X2 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 103391486 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 103396265 dhx30; putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 103386211 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 103379330 lactation elevated protein 1-like K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 103380651 lace1; lactation elevated protein 1 isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 103382964 atp23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 103379129 supv3l1; LOW QUALITY PROTEIN: ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 103396757 lactb2; beta-lactamase-like protein 2 isoform X1 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 103377438 ADP/ATP translocase 3-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 103383664 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 103390748 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 103395576 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 103383198 mitoferrin-2-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 103387294 slc25a28; mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 103397178 mitoferrin-1-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 103398227 slc25a37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 107989008 mitoferrin-2-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 103388363 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 103394899 eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 103380342 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 103394662 yars; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 103388476 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 103394851 lars; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 103396547 dars2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 103377215 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 103377216 glycine--tRNA ligase-like K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 103381231 rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 103395599 rars; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 103378189 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 103383618 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 103397324 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial isoform X1 K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 103376863 mtpap; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 103386664 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 103387347 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 103390792 noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 103378845 nsun3; putative methyltransferase NSUN3 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 103395852 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 103399057 rpusd4; RNA pseudouridylate synthase domain-containing protein 4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 103395341 rcc1l; Williams-Beuren syndrome chromosomal region 16 protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 103384805 ngrn; neugrin isoform X1 K23496 NGRN; neugrin
D 103385773 probable tRNA pseudouridine synthase 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 103385789 probable tRNA pseudouridine synthase 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 103392233 fastkd1; FAST kinase domain-containing protein 1, mitochondrial K27754 FASTKD1; FAST kinase domain-containing protein 1
D 103389878 fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 103377457 fastkd3; FAST kinase domain-containing protein 3, mitochondrial K27755 FASTKD3; FAST kinase domain-containing protein 3
D 103388565 tbrg4; protein TBRG4 K27756 TBRG4; FAST kinase domain-containing protein 4
D 103392021 fastkd5; FAST kinase domain-containing protein 5, mitochondrial isoform X1 K27757 FASTKD5; FAST kinase domain-containing protein 5
D 107990250 czh12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor
D 103380295 rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 103397816 uncharacterized protein LOC103397816 K24984 GRSF1; G-rich sequence factor 1
D 103378700 mettl15; probable methyltransferase-like protein 15 isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 103386380 c11h12orf10; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 103383651 c1h6orf203; uncharacterized protein C6orf203 homolog isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 103380522 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 103383781 polg2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 103383667 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 103397935 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 103387555 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 103381557 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 103395855 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 103382599 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 103385847 atad3a; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 103385763 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 103381793 mucin-5AC-like isoform X3 K27759 MTNAP1; mitochondrial nucleoid-associated protein 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 103379231 dnaja2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 103380092 dnaJ homolog subfamily A member 2-like K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 103386798 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 103383612 LOW QUALITY PROTEIN: mitochondrial Rho GTPase 1-A-like K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 103392922 mitochondrial Rho GTPase 1-A isoform X4 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 103378288 heat shock cognate 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 103388515 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 103393458 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 103395051 LOW QUALITY PROTEIN: heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 103395053 heat shock cognate 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 103378084 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 103383801 aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
D 103390533 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 103395698 mitochondrial fission factor-like K28235 FATE1; fetal and adult testis-expressed transcript protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 103389007 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 103393950 tomm40; mitochondrial import receptor subunit TOM40 homolog isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 103395689 LOW QUALITY PROTEIN: mitochondrial import receptor subunit TOM40B-like K11518 TOM40; mitochondrial import receptor subunit TOM40
D 103392712 tomm70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 103382088 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 103383373 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 103387620 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 103394619 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 103385762 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 103390969 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 103379807 sorting and assembly machinery component 50 homolog A isoform X2 K07277 SAM50; outer membrane protein insertion porin family
D 103382427 sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 103394861 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 103381510 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 103386924 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 103389976 voltage-dependent anion-selective channel protein 2-like isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
D 103397766 voltage-dependent anion-selective channel protein 2 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 103387714 mtx2; metaxin-2 K17776 MTX; metaxin
D 103388113 metaxin-1-like K17776 MTX; metaxin
D 103398281 mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 103394915 myo19; unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX
D 103381488 mitochondrial amidoxime-reducing component 1-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 103381797 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 103384223 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 103395085 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 103377765 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 103390583 timm8a; LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 103393854 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 103386164 chchd4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 103393251 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 103384661 minos1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 103391450 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 103399921 c2h19orf70; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 103380574 leucine-rich repeat extensin-like protein 3 K17563 CHCHD3; MICOS complex subunit MIC19
D 103382748 chchd3; MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 103384750 MICOS complex subunit mic25a-like K17564 CHCHD6; MICOS complex subunit MIC25
D 103386125 MICOS complex subunit mic25a-like isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 103377171 apoo; MICOS complex subunit MIC26 K24625 APOO; MICOS complex subunit MIC26
D 103396786 MICOS complex subunit MIC26-like K24625 APOO; MICOS complex subunit MIC26
D 103391361 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 103384661 minos1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 103391450 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 103394875 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 103381787 timm23; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 103385386 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B isoform X1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 103386698 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 103376987 timm21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 103378358 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 103387579 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 103387580 micu1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 103394787 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 103399085 calcium uptake protein 2, mitochondrial-like K22828 MICU2; calcium uptake protein 2, mitochondrial
D 103383852 ccdc109b; calcium uniporter regulatory subunit MCUb, mitochondrial isoform X1 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 103390115 calcium uniporter regulatory subunit MCUb, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 103383985 essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial
D 103393368 smdt1; essential MCU regulator, mitochondrial isoform X1 K22830 SMDT1; essential MCU regulator, mitochondrial
D 103377068 mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 103383212 letm1; LETM1 and EF-hand domain-containing protein 1, mitochondrial isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 103397006 LETM1 domain-containing protein LETM2, mitochondrial-like isoform X2 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 103397783 LETM1 domain-containing protein LETM2, mitochondrial-like K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 103379138 immp1l; mitochondrial inner membrane protease subunit 1 isoform X3 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 103379773 immp2l; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 103391021 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 103379125 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 103391675 mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 103384275 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial isoform X1 K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
D 103383785 ociad1; OCIA domain-containing protein 1 K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 103393901 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 103395888 mitochondrial import inner membrane translocase subunit TIM44-like isoform X1 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 103390505 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 103385704 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 103399577 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 103393057 pam16; mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 103396952 mitochondrial-processing peptidase subunit alpha-like K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 103397903 LOW QUALITY PROTEIN: mitochondrial-processing peptidase subunit alpha-like K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 103389856 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 103377613 mipep; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 103391646 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 103391647 10 kDa heat shock protein, mitochondrial isoform X2 K04078 groES; chaperonin GroES
D 103383220 dnaJ homolog subfamily A member 3, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 103393058 dnaja3; dnaJ homolog subfamily A member 3, mitochondrial K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 103385622 tamm41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 103385633 phosphatidate cytidylyltransferase, mitochondrial-like K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 103388847 ethe1; persulfide dioxygenase ETHE1, mitochondrial isoform X2 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 103377779 poldip2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
#
AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 103389560 cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 103391910 cyclic AMP-responsive element-binding protein 1-like isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 103378460 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 103390000 gfm2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 103386384 sp1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1
D 103376874 transcriptional repressor protein YY1-like K09201 YY; transcription factor YY
D 103381010 transcriptional repressor protein YY1-like isoform X1 K09201 YY; transcription factor YY
D 103393834 gabpb2; GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta
D 103381843 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 103382801 nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 103385131 nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 103391873 nfe2l2; nuclear factor erythroid 2-related factor 2 isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 103379551 metallothionein A K14739 MT1_2; metallothionein 1/2
C Coactivators
D 103390541 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X2 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 103391053 peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 103387378 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 103395649 crtc1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 103395874 CREB-regulated transcription coactivator 1-like isoform X6 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 103382144 histone acetyltransferase p300-like isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 103384092 CREB-binding protein-like isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 103393050 crebbp; CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 103393331 ep300; LOW QUALITY PROTEIN: histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 103386453 cysteine desulfurase, mitochondrial-like K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 103390116 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 103377281 lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 103397368 fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 103389745 fdx1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 103384169 fdx1l; adrenodoxin-like protein, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 103382155 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 103390505 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 103397835 hscb; iron-sulfur cluster co-chaperone protein HscB, mitochondrial isoform X1 K04082 hscB; molecular chaperone HscB
D 103391475 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 103380725 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 103397907 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial isoform X1 K22063 ISCA1; iron-sulfur cluster assembly 1
D 103398449 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 103396382 iba57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 103387332 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 103398243 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 103388812 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 103398416 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 103387200 sideroflexin-1-like K23500 SFXN1_3; sideroflexin-1/3
D 103391209 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 103381775 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2
D 103387504 sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4
D 103383284 sideroflexin-5-like K23503 SFXN5; sideroflexin-5
D 103390596 sideroflexin-5-like K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 103380127 cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 103380373 cpt1a; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 103382008 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 103393672 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 103380546 dhtkd1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 103388577 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 103384375 hcfc1; host cell factor 1 isoform X3 K14966 HCFC1; host cell factor 1
D 103386409 host cell factor 1-like isoform X3 K14966 HCFC1; host cell factor 1
D 103383033 hcfc2; LOW QUALITY PROTEIN: host cell factor 2 K27390 HCFC2; host cell factor 2
D 103384197 htt; huntingtin isoform X1 K04533 HD; huntingtin
D 103394741 esrra; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 103376742 steroid hormone receptor ERR2 isoform X3 K08553 NR3B2; estrogen-related receptor beta
D 103380809 steroid hormone receptor ERR2-like K08553 NR3B2; estrogen-related receptor beta
D 103378383 steroid hormone receptor ERR1-like K08554 NR3B3; estrogen-related receptor gamma
D 103379008 estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma
D 103381066 estrogen-related receptor gamma-like isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 103394793 nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 103376655 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 103390073 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 103396817 lonp1; lon protease homolog, mitochondrial isoform X1 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 103391355 sirt1; LOW QUALITY PROTEIN: NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 103380665 serac1; protein SERAC1 K23504 SERAC1; protein SERAC1
D 103384387 protein UXT-like K26537 UXT; protein UXT
D 103391172 ES1 protein homolog, mitochondrial-like K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 103391930 ES1 protein homolog, mitochondrial-like K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 103398074 tango2; transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2
D 103392335 c16h2orf69; UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 103381174 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 103385837 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 103380625 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 103383389 ndufaf5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 103388066 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 103381321 ndufaf7; NADH dehydrogenase [ubiquinone] complex I, assembly factor 7 isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 107988868 c8h17orf89; uncharacterized protein C17orf89 homolog K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 103391720 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 103386611 acad9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 103382536 nubpl; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 103395352 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 103376979 rtn4ip1; LOW QUALITY PROTEIN: reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 103380937 reticulon-4-interacting protein 1 homolog, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 103389595 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 103398017 succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 107988206 succinate dehydrogenase assembly factor 1, mitochondrial-like K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 103378757 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 103380769 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 103398720 ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 103387125 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 103386211 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 103385763 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 103397484 ubiquinol-cytochrome-c reductase complex assembly factor 3-like K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 103385484 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 103379810 c6h12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 103382890 c8h7orf73; uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 103388618 cmc1; COX assembly mitochondrial protein homolog isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1
D 103379152 cmc2; COX assembly mitochondrial protein 2 homolog isoform X2 K18172 CMC2; COX assembly mitochondrial protein 2
D 103381571 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 103393604 cytochrome c oxidase assembly factor 3 homolog, mitochondrial-like K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 103395240 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 103391699 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 103383071 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 103376743 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 103381808 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 103382260 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 103386747 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 103387386 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 103391990 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 103390779 mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18
D 103382057 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 103386948 cytochrome c oxidase protein 20 homolog isoform X1 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 103381990 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 103381991 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 103392866 pet100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 103383400 pet117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 103388641 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 103390087 surf1; surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 103392507 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 103382464 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 103381604 translational activator of cytochrome c oxidase 1 isoform X1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 103387121 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 103382873 apopt1; apoptogenic protein 1, mitochondrial K23506 APOPT1; apoptogenic protein 1
D 103382890 c8h7orf73; uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1
D 103385484 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 103392280 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
D 103396385 HIG1 domain family member 1A, mitochondrial-like K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 103391233 higd2a; HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial
C Complex-V assembly factors
D 103399898 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 103382330 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 103396545 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 103384010 usmg5; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 103393094 mfn1; mitofusin-1 isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 103384844 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 103393818 opa1; dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 103377854 opa3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein
D 103378346 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 103378338 parl; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 103392613 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 103393523 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 103380582 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 103382891 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 103398237 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 103388077 fis1; mitochondrial fission 1 protein isoform X1 K17969 FIS1; mitochondrial fission 1 protein
D 103378402 small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier
D 103383557 small ubiquitin-related modifier 2-like isoform X1 K12160 SUMO; small ubiquitin-related modifier
D 103389507 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 103392195 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 103392908 sumo2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 107988215 small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier
D 103377018 endophilin-B1-like isoform X1 K11248 SH3GLB1; endophilin-B1
D 103378957 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 103384880 mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier
D 103377558 mff; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor
D 103396111 mitochondrial fission factor homolog A-like isoform X1 K22076 MFF; mitochondrial fission factor
D 103376999 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 103385185 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 103381459 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 103393131 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 103383490 mief2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 103393312 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 103384162 pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 103390092 fam73b; mitoguardin-2 K27289 MIGA; mitoguardin
D 103396697 fam73a; LOW QUALITY PROTEIN: mitoguardin-1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 103383494 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 103393304 actb; actin, beta K05692 ACTB_G1; actin beta/gamma 1
D 103381315 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 103389973 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 103393133 phb; prohibitin K17080 PHB1; prohibitin 1
D 103396759 phb2; prohibitin-2 K17081 PHB2; prohibitin 2
D 103395514 ktn1; kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 103380582 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 103382891 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 103398237 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 103379426 myo5a; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
D 103380483 unconventional myosin-Va-like isoform X1 K10357 MYO5; myosin V
D 103380485 myo5c; unconventional myosin-Vc K10357 MYO5; myosin V
D 103390388 LOW QUALITY PROTEIN: unconventional myosin-Vb-like K10357 MYO5; myosin V
D 103399937 unconventional myosin-Va-like K10357 MYO5; myosin V
D 103391373 E3 ubiquitin-protein ligase XIAP-like isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 103378040 diablo homolog, mitochondrial-like K10522 DIABLO; diablo
D 103378169 diablo homolog, mitochondrial-like isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 103391455 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25
D 103383612 LOW QUALITY PROTEIN: mitochondrial Rho GTPase 1-A-like K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 103392922 mitochondrial Rho GTPase 1-A isoform X4 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 103391450 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 103390240 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 103388256 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 103398358 nedd4; LOW QUALITY PROTEIN: E3 ubiquitin-protein ligase NEDD4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 103388630 oxr1; oxidation resistance protein 1 isoform X2 K25437 OXR1; oxidation resistance protein 1
D 103393984 msto1; LOW QUALITY PROTEIN: protein misato homolog 1 K27320 MSTO1; protein misato
D 103383530 PRELI domain-containing protein 1, mitochondrial-like isoform X1 K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 103391110 prelid1; PRELI domain-containing protein 1, mitochondrial K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 103384506 PRELI domain containing protein 3B-like K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
D 103386686 prelid3b; PRELI domain containing protein 3B K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 103390830 atg2a; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 103398366 atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 103389583 atg3; ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 103376817 atg4b; cysteine protease ATG4B isoform X6 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 103383989 cysteine protease ATG4D-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 103393732 atg4d; cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 103395436 atg4c; cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 103388689 atg5; autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 103381462 becn1; beclin-1 isoform X1 K08334 BECN; beclin
D 103385619 atg7; LOW QUALITY PROTEIN: ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 103378875 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 103379687 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 103387166 gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 103388004 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 103378436 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 103396326 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 103396654 atg10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 103387824 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 103381790 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 103378116 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 103378401 autophagy-related protein 16-2 isoform X3 K20868 ATG16L2; autophagy-related protein 16-2
D 103382375 wipi1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
D 103393297 wipi2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 103393541 WD repeat domain phosphoinositide-interacting protein 1-like K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 103387132 park2; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 103385574 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 103393232 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 103385276 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 103378338 parl; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 103390783 sequestosome-1 K14381 SQSTM1; sequestosome 1
D 103388421 tax1bp1; LOW QUALITY PROTEIN: tax1-binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1
D 103394223 tax1-binding protein 1 homolog A-like isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 103381884 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 103379694 ambra1; activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 103389330 atg13; autophagy-related protein 13 K08331 ATG13; autophagy-related protein 13
D 103389416 ulk1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 103377644 ulk2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 103396317 rb1cc1; RB1-inducible coiled-coil protein 1 isoform X2 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 103380891 heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 103380988 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 103380989 heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG
D 103383248 hsp90 co-chaperone Cdc37-like K09554 CDC37; cell division cycle protein 37
D 103392580 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 103383976 smurf2; E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 103393300 E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 103393707 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 103389295 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 103397700 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 103389706 FUN14 domain-containing protein 1 isoform X3 K17986 FUNDC1; FUN14 domain-containing protein 1
D 103391556 fundc1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 103376655 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 103390073 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 103383383 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 103386752 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 103390809 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 103399056 microtubule-associated proteins 1A/1B light chain 3B-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 103381848 nbr1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 103393528 next to BRCA1 gene 1 protein-like K17987 NBR1; next to BRCA1 gene 1 protein
D 103382351 tectonin beta-propeller repeat-containing protein 1-like K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 103392887 tecpr1; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 103380759 zinc finger FYVE domain-containing protein 1-like isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 103399926 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 103381493 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 103383218 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 103378617 c5h19orf12; protein C19orf12 homolog K23168 MPAN; protein MPAN
D 103380414 protein C19orf12 homolog K23168 MPAN; protein MPAN
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: April 30, 2025