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Mitochondrial Biogenesis - Diuraphis noxia (Russian wheat aphid)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 17428420 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 17428421 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 17428414 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 17428416 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 17428417 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 17428415 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 17428418 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 17428419 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 17428409 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 17428410 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 17428413 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 17428411 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 17428412 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 107171776 DNA-directed RNA polymerase, mitochondrial-like K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
D 107172190 DNA-directed RNA polymerase, mitochondrial-like K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 107166833 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 107166361 mitochondrial dimethyladenosine transferase 1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 107162080 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 107166182 translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 107162877 translation initiation factor IF-3, mitochondrial-like K02520 infC; translation initiation factor IF-3
D 107165198 elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 107169099 elongation factor Tu-like K02358 tuf; elongation factor Tu
D 107164748 elongation factor Tu, mitochondrial-like K02358 tuf; elongation factor Tu
D 107167611 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 107162977 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 107169303 uncharacterized protein LOC107169303 K15031 MTERF; mitochondrial transcription termination factor family protein
D 107169304 uncharacterized protein LOC107169304 isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 107161652 uncharacterized protein LOC107161652 K15031 MTERF; mitochondrial transcription termination factor family protein
D 107170604 transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 107171884 transcription termination factor 3, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 107161535 translation factor GUF1 homolog, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 107166040 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 107166042 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 107174054 ribonuclease P/MRP protein subunit POP5 isoform X1 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 107165623 ribonuclease P protein subunit p30 isoform X1 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 107166910 ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 107171189 ribonuclease P protein subunit p40-like K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 107171989 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 107170240 3-hydroxyacyl-CoA dehydrogenase type-2-like isoform X1 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 107173425 mitochondrial ribonuclease P protein 3 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 107172214 uncharacterized protein LOC107172214 isoform X1 K17658 TEFM; transcription elongation factor, mitochondrial
D 107162862 pentatricopeptide repeat-containing protein 1, mitochondrial isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 107173782 pentatricopeptide repeat-containing protein 2, mitochondrial-like K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 107164220 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 107170873 putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 107166475 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 107166072 putative ATPase N2B isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 107169092 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 107174139 ATP-dependent RNA helicase SUV3 homolog, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 107167167 beta-lactamase-like protein 2 homolog isoform X1 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 107162647 ADP,ATP carrier protein 1-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 107164715 ADP/ATP translocase 4-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 107163307 ADP,ATP carrier protein 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 107164567 mitoferrin-1-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 107164359 mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 107162486 GTPase Era, mitochondrial K03595 era; GTPase
D 107173871 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 107164406 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 107167615 probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 107163848 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 107172560 aspartate--tRNA ligase, mitochondrial-like K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 107170601 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 107170178 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 107169363 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 107173551 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 107173970 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 107161297 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 107163353 poly(A) RNA polymerase, mitochondrial-like K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 107167409 2',5'-phosphodiesterase 12 isoform X1 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 107169511 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 107166138 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 107170594 5-methylcytosine rRNA methyltransferase NSUN4-like K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 107162419 Williams-Beuren syndrome chromosomal region 16 protein homolog K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 107172642 uncharacterized protein LOC107172642 K23496 NGRN; neugrin
D 107167950 probable tRNA pseudouridine synthase 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 107162202 uncharacterized protein LOC107162202 K18190 FASTKD2; FAST kinase domain-containing protein 2
D 107163211 probable peptide chain release factor C12orf65, mitochondrial K23498 COXPD7; peptide chain release factor
D 107163029 uncharacterized protein LOC107163029 K23499 RMND1; required for meiotic nuclear division protein 1
D 107172106 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 107167387 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 107173039 UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 107162811 uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 107169323 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 107170709 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 107173826 DNA-directed primase/polymerase protein-like K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 107172439 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 107167545 mitochondrial genome maintenance exonuclease 1-like isoform X1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 107161889 twinkle protein, mitochondrial isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 107170577 uncharacterized protein LOC107170577 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107167881 uncharacterized protein LOC107167881 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107172453 ATP-dependent DNA helicase pif1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107169272 ATP-dependent DNA helicase pif1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107171935 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107171805 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107161580 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107172890 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107168290 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107173274 uncharacterized protein LOC107173274 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107166369 uncharacterized protein LOC107166369 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 107170291 ATP-dependent DNA helicase PIF6-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 107173799 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 107170095 ATPase family AAA domain-containing protein 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 107165229 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 107168869 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 107167443 heat shock protein 70 B2-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 107163650 heat shock protein 70 A1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 107167510 heat shock protein 70 A1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 107169808 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 107163583 heat shock 70 kDa protein cognate 4-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 107172656 heat shock protein 70 B2-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 107163219 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 107174071 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 107169434 uncharacterized protein LOC107169434 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 107170015 mitochondrial import receptor subunit TOM40 homolog 2-like K11518 TOM40; mitochondrial import receptor subunit TOM40
D 107171448 mitochondrial import receptor subunit TOM70-like K17768 TOM70; mitochondrial import receptor subunit TOM70
D 107166840 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 107171692 mitochondrial import receptor subunit TOM7 homolog isoform X1 K17771 TOM7; mitochondrial import receptor subunit TOM7
C TOB/SAM complex
D 107165053 sorting and assembly machinery component 50 homolog B-like K07277 SAM50; outer membrane protein insertion porin family
D 107161436 sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 107164306 voltage-dependent anion-selective channel-like K15040 VDAC2; voltage-dependent anion channel protein 2
C ERMES complex
C Other outer membrane factor
D 107163538 metaxin-1 K17776 MTX; metaxin
D 107172977 metaxin-2 K17776 MTX; metaxin
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 107173092 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 107172181 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 107161276 mitochondrial import inner membrane translocase subunit Tim9-like K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 107163038 mitochondrial import inner membrane translocase subunit Tim8-like K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
C Mitochondrial intermembrane space assembly (MIA) complex
D 107162244 mitochondrial intermembrane space import and assembly protein 40-B K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 107168624 FAD-linked sulfhydryl oxidase ALR-like K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
D 107165087 FAD-linked sulfhydryl oxidase ALR-like K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
D 107162699 FAD-linked sulfhydryl oxidase ALR-like K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 107166543 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 107173327 LOW QUALITY PROTEIN: MICOS complex subunit Mic60-like K17785 IMMT; MICOS complex subunit MIC60
D 107173659 MICOS complex subunit Mic60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 107167431 MICOS complex subunit MIC13 homolog QIL1 K24624 MICOS13; MICOS complex subunit MIC13
D 107163870 uncharacterized protein LOC107163870 K17563 CHCHD3; MICOS complex subunit MIC19
C MICOS complex (yeast)
D 107166543 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 107173327 LOW QUALITY PROTEIN: MICOS complex subunit Mic60-like K17785 IMMT; MICOS complex subunit MIC60
D 107173659 MICOS complex subunit Mic60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 107165412 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 107165189 mitochondrial import inner membrane translocase subunit Tim23-like K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 107165195 mitochondrial import inner membrane translocase subunit Tim23-like K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 107174129 mitochondrial import inner membrane translocase subunit TIM50-C-like isoform X1 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
D 107161568 mitochondrial import inner membrane translocase subunit TIM50-C-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 107168861 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 107164033 calcium uptake protein 1 homolog, mitochondrial-like K22827 MICU1; calcium uptake protein 1, mitochondrial
D 107174056 protein EMRE homolog, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
C Other inner membrane factors
D 107165825 LETM1 and EF-hand domain-containing protein anon-60Da, mitochondrial-like K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 107167091 LETM1 and EF-hand domain-containing protein anon-60Da, mitochondrial-like K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 107174142 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 107169165 mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 107164140 uncharacterized protein LOC107164140 K18157 TMEM126A; transmembrane protein 126A
D 107168058 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 107170459 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
B Matrix
C MMC/PAM proteins
D 107170932 mitochondrial import inner membrane translocase subunit TIM44-like K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 107169200 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 107161832 grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 107162143 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 107164483 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 107168028 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 107163593 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 107166347 mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 107163621 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 107162038 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 107165289 uncharacterized protein LOC107165289 K04078 groES; chaperonin GroES
D 107164899 protein tumorous imaginal discs, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 107163050 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 107165076 DNL-type zinc finger protein-like K17808 ZIM17; mitochondrial protein import protein ZIM17
D 107163962 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 107165293 uncharacterized protein LOC107165293 isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 107169737 polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
#
AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 107166267 cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 107167611 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 107162977 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 107165654 transcriptional repressor protein YY1-like isoform X1 K09201 YY; transcription factor YY
D 107167422 uncharacterized protein LOC107167422 K09454 GABPB; GA-binding protein transcription factor, beta
D 107166833 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 107161277 DNA-binding protein Ewg-like isoform X1 K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 107173687 CREB-regulated transcription coactivator 1-like isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 107172505 histone acetyltransferase p300-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 107173067 CREB-binding protein-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 107166570 probable cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 107167955 iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 107161696 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 107162495 frataxin homolog, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1]
D 107169062 adrenodoxin isoform X1 K22070 FDX1; ferredoxin-1, mitochondrial
D 107167269 adrenodoxin-like protein, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 107162313 NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 107169200 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 107169493 co-chaperone protein HscB homolog K04082 hscB; molecular chaperone HscB
D 107167232 nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 107173879 uncharacterized monothiol glutaredoxin ycf64-like K07390 grxD; monothiol glutaredoxin
D 107170887 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 107173516 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 107171659 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 107173846 putative bolA-like protein K11H12.1 K22066 BOLA1; BolA-like protein 1
D 107168006 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 107165572 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 107162226 sideroflexin-2-like K23501 SFXN2; sideroflexin-2
D 107165157 sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2
C Other regulator of mitochondrial biogenesis
D 107165513 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 107166247 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 107170117 host cell factor 1-like isoform X1 K14966 HCFC1; host cell factor 1
D 107173018 huntingtin-like K04533 HD; huntingtin
D 107165577 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 107169899 lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 107171649 NAD-dependent histone deacetylase Sir2-like K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 107168836 protein SERAC1 K23504 SERAC1; protein SERAC1
D 107171977 protein SERAC1 K23504 SERAC1; protein SERAC1
D 107161938 uncharacterized protein LOC107161938 K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 107168543 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 107164388 mimitin, mitochondrial K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 107162735 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 107171313 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 107162940 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 107166239 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 107165911 NADH dehydrogenase [ubiquinone] complex I, assembly factor 7 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 107172015 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 107162775 acyl-CoA dehydrogenase family member 9, mitochondrial-like K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 107173455 acyl-CoA dehydrogenase family member 9, mitochondrial-like K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 107167128 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 107169937 FAD-dependent oxidoreductase domain-containing protein 1-like K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 107172141 FAD-dependent oxidoreductase domain-containing protein 1-like K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 107168445 reticulon-4-interacting protein 1, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 107174095 reticulon-4-interacting protein 1 homolog, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 107174113 reticulon-4-interacting protein 1 homolog, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 107166411 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 107167308 succinate dehydrogenase assembly factor 2-B, mitochondrial-like K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 107168560 mitochondrial chaperone BCS1-like K08900 BCS1; mitochondrial chaperone BCS1
D 107166059 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 107164518 tetratricopeptide repeat protein 19 homolog, mitochondrial-like K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 107173667 tetratricopeptide repeat protein 19 homolog, mitochondrial-like K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 107162668 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 107166475 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 107165529 uncharacterized protein LOC107165529 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
C Complex-IV assembly factors
D 107167848 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 107172936 COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 107166362 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 107169038 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 107164212 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 107162284 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7
D 107162962 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 107168097 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 107170523 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 107173541 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 107166143 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 107166409 mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18
D 107173301 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 107164471 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 107163977 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 107164032 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 107161614 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 107170498 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 107168077 translational activator of cytochrome c oxidase 1-like K18189 TACO1; translational activator of cytochrome c oxidase 1
D 107166282 leucine-rich PPR motif-containing protein, mitochondrial-like K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 107161958 APOPT family protein CG14806, mitochondrial K23506 APOPT1; apoptogenic protein 1
D 107163771 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 107161375 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 107161655 ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 107174141 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 107167625 up-regulated during skeletal muscle growth protein 5-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 107168084 transmembrane GTPase Marf-like K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 107170746 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 107173317 putative OPA3-like protein CG13603 K23166 OPA3; optic atrophy 3 protein
D 107167098 TP53-regulated inhibitor of apoptosis 1-like K17968 TRIAP1; TRIAP1/MDM35 family protein
D 107173758 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 107162767 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 107167094 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 107162242 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 107173211 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 107163416 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 107165371 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 107167961 small ubiquitin-related modifier-like K12160 SUMO; small ubiquitin-related modifier
D 107169748 endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1
D 107163208 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier
D 107172275 transport and Golgi organization protein 11 K22076 MFF; mitochondrial fission factor
D 107169756 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 107171738 mitochondrial cardiolipin hydrolase-like K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 107165035 mitochondrial cardiolipin hydrolase-like isoform X1 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 107165327 protein FAM73B-like K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 107168325 actin-5C K05692 ACTB_G1; actin beta/gamma 1
D 107163963 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 107162135 N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 107166582 protein l(2)37Cc K17080 PHB1; prohibitin 1
D 107170198 prohibitin-2 isoform X1 K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 107162767 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 107167094 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 107162242 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 107173211 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 107169347 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
C Morphogenesis factors
D 107165229 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 107173327 LOW QUALITY PROTEIN: MICOS complex subunit Mic60-like K17785 IMMT; MICOS complex subunit MIC60
D 107173659 MICOS complex subunit Mic60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 107165044 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 107167213 E3 ubiquitin-protein ligase NEDD4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 107167687 protein misato K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 107163014 autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2
D 107173009 ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 107171841 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 107169944 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 107170916 cysteine protease ATG4B-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 107165855 autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 107167550 beclin-1-like protein K08334 BECN; beclin
D 107173413 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 107167856 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 107164744 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 107165379 ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 107171698 ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 107165202 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 107168225 autophagy-related protein 16-1-like K17890 ATG16L1; autophagy-related protein 16-1
D 107169412 autophagy-related protein 16-1-like K17890 ATG16L1; autophagy-related protein 16-1
C Parkin-dependent mechanism factors
D 107171531 E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 107165425 E3 ubiquitin-protein ligase NRDP1-like K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 107166745 protein CLEC16A K19513 CLEC16A; protein CLEC16A
D 107170068 serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 107173758 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
C Parkin-independent mechanism factors
D 107165431 autophagy-related protein 13 homolog isoform X1 K08331 ATG13; autophagy-related protein 13
D 107162961 serine/threonine-protein kinase unc-51 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 107161659 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 107167047 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG
D 107171792 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 107169830 hsp90 co-chaperone Cdc37-like K09554 CDC37; cell division cycle protein 37
D 107166677 E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 107162282 FUN14 domain-containing protein 2-like K17986 FUNDC1; FUN14 domain-containing protein 1
D 107168532 FUN14 domain-containing protein 1-like isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 107165577 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 107165214 tectonin beta-propeller repeat-containing protein K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 107162476 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 107162179 bifunctional coenzyme A synthase-like K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 107165067 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 107165973 protein C19orf12 homolog K23168 MPAN; protein MPAN
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024