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  Mitochondrial Biogenesis - Eurytemora carolleeae

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I C Mitochondrial respiratory chain complex III C Cytochrome c oxidase D 111702477 LOW QUALITY PROTEIN: uncharacterized protein LOC111702477 K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 111695542 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 111700044 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 111700059 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 111694886 translation initiation factor IF-2, mitochondrial-like K02519 infB; translation initiation factor IF-2 D 111706816 elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts D 111696741 uncharacterized protein LOC111696741 K02358 tuf; elongation factor Tu D 111698692 uncharacterized protein LOC111698692 K02358 tuf; elongation factor Tu D 111714937 uncharacterized protein LOC111714937 K02358 tuf; elongation factor Tu D 111698885 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 111712055 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 111706848 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 111700836 translation factor Guf1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 111706709 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 111705225 ribonuclease P/MRP protein subunit POP5-like K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 111699108 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 111710530 uncharacterized protein LOC111710530 isoform X1 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 111700268 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 111716013 uncharacterized protein LOC111716013 K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 111695633 uncharacterized protein LOC111695633 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 111700363 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 111704027 uncharacterized protein LOC111704027 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 111699914 pentatricopeptide repeat-containing protein 1, mitochondrial isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 111694975 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 (small subunit ribosomal protein S39) D 111697132 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 111711291 putative ATPase N2B isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 111702124 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 111710439 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 111713718 ATP-dependent RNA helicase SUV3 homolog, mitochondrial-like K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 111708346 beta-lactamase-like protein 2 homolog K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 111702959 ADP,ATP carrier protein 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 111704709 ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 111717400 ADP,ATP carrier protein 3, mitochondrial K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 111702398 mitoferrin K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 111697389 GTPase Era, mitochondrial K03595 era; GTPase D 111713324 tyrosine--tRNA ligase, mitochondrial-like K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 111715209 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 111701823 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 111701833 leucine--tRNA ligase, cytoplasmic-like K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 111705131 probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 111694748 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 111700754 glycine--tRNA ligase isoform X1 K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 111699793 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 111700739 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 111699837 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial-like K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 111709998 uncharacterized protein LOC111709998 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 111709738 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 111701191 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 111703207 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 111709762 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 111708583 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 111695098 5-methylcytosine rRNA methyltransferase NSUN4-like K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 111700948 mitochondrial mRNA pseudouridine synthase RPUSD3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 111702728 uncharacterized protein LOC111702728 isoform X1 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 111708327 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 111717994 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 111709307 uncharacterized protein LOC111709307 K23496 NGRN; neugrin D 111694974 FAST kinase domain-containing protein 3, mitochondrial K27755 FASTKD3; FAST kinase domain-containing protein 3 D 111701698 protein TBRG4 K27756 TBRG4; FAST kinase domain-containing protein 4 D 111694966 probable peptide chain release factor C12orf65, mitochondrial K23498 COXPD7; peptide chain release factor D 111712133 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 111698693 heterogeneous nuclear ribonucleoprotein H K24984 GRSF1; G-rich sequence factor 1 D 111712254 UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 111704981 DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 111712502 DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 111704268 endonuclease G, mitochondrial isoform X1 K01173 ENDOG; endonuclease G, mitochondrial D 111696089 mitochondrial genome maintenance exonuclease 1-like K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 111703472 nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial D 111697155 twinkle protein, mitochondrial K17680 TWNK; twinkle mtDNA helicase [EC:5.6.2.3] D 111696885 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 111699093 single-stranded DNA-binding protein, mitochondrial isoform X1 K03111 ssb; single-strand DNA-binding protein D 111710495 ATPase family AAA domain-containing protein 3-A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 111697325 mitochondrial Rho GTPase-like K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 111704824 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111704938 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111704940 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111706680 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111707610 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111711631 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111711752 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111711805 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111717003 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111717007 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111712757 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 111695211 mitochondrial import receptor subunit TOM20 homolog B K17770 TOM20; mitochondrial import receptor subunit TOM20 D 111707012 uncharacterized protein LOC111707012 K17769 TOM22; mitochondrial import receptor subunit TOM22 D 111709111 mitochondrial import receptor subunit TOM40 homolog 1-like K11518 TOM40; mitochondrial import receptor subunit TOM40 D 111700738 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 111703877 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 C TOB/SAM complex D 111706358 sorting and assembly machinery component 50 homolog A-like K07277 SAM50; outer membrane protein insertion porin family D 111712026 sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family C MIM complex C Porin D 111710622 voltage-dependent anion-selective channel K15040 VDAC2; voltage-dependent anion channel protein 2 D 111713987 voltage-dependent anion-selective channel K15040 VDAC2; voltage-dependent anion channel protein 2 D 111714095 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 C Other outer membrane factor D 111701959 metaxin-2 K17776 MTX; metaxin D 111708818 metaxin-3 K17776 MTX; metaxin D 111699385 mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 111701360 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 111695553 mitochondrial import inner membrane translocase subunit Tim10-like K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 111709632 mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 111715639 mitochondrial import inner membrane translocase subunit Tim8 A-like K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 C Mitochondrial intermembrane space assembly (MIA) complex D 111703969 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 111698450 FAD-linked sulfhydryl oxidase ALR-like K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 111700747 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 111697947 MICOS complex subunit MIC60-1 K17785 IMMT; MICOS complex subunit MIC60 D 111716174 uncharacterized protein LOC111716174 K24624 MICOS13; MICOS complex subunit MIC13 D 111696651 MICOS complex subunit mic25a isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 111698904 MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 111700747 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 111697947 MICOS complex subunit MIC60-1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 111711174 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 111712465 mitochondrial import inner membrane translocase subunit Tim23-like K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 111700564 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 111705136 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 111696064 mitochondrial import inner membrane translocase subunit TIM50-C K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 111713278 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 111696573 calcium uptake protein 1 homolog, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial D 111706220 calcium uptake protein 1 homolog, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 111716368 calcium uptake protein 1 homolog, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial C Other inner membrane factors D 111705943 mitochondrial proton/calcium exchanger protein K17800 LETM1; mitochondrial proton/calcium exchanger protein D 111704068 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 111694780 mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 111694781 mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 111704994 uncharacterized protein LOC111704994 K18157 TMEM126A; transmembrane protein 126A D 111709712 OCIA domain-containing protein 1-like K28215 OCIAD1; OCIA domain-containing protein 1 B Matrix C MMC/PAM proteins D 111718375 mitochondrial import inner membrane translocase subunit TIM44-like K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 111715061 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 111707465 grpE protein homolog, mitochondrial K03687 GRPE; molecular chaperone GrpE D 111706229 uncharacterized protein LOC111706229 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 111708790 mitochondrial import inner membrane translocase subunit TIM14-like K09539 DNAJC19; DnaJ homolog subfamily C member 19 C Other matrix factors D 111698067 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 111705523 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 111710630 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 111707818 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 111694779 protein tumorous imaginal discs, mitochondrial K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 111696570 protein tumorous imaginal discs, mitochondrial-like K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 111698423 protein tumorous imaginal discs, mitochondrial-like K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 111704173 dnaJ homolog subfamily A member 3, mitochondrial K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 111710227 phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 111708010 DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 111703142 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 111703614 polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 111716715 cyclic AMP-responsive element-binding protein isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 111717943 cyclic AMP-responsive element-binding protein K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 111698885 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 111712055 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 111696249 transcriptional repressor protein YY1 K09201 YY; transcription factor YY D 111705945 ankyrin-2 K09454 GABPB; GA-binding protein transcription factor, beta D 111700044 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 111708884 DNA-binding protein Ewg isoform X1 K11831 NRF1; nuclear respiratory factor 1 C Coactivators D 111704063 CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 111709063 probable cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 111712054 frataxin homolog, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 111702264 adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial D 111715243 adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial D 111695740 uncharacterized protein LOC111695740 K22071 FDX2; ferredoxin-2, mitochondrial D 111695764 NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 111699508 NADPH:adrenodoxin oxidoreductase, mitochondrial-like K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 111715061 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 111706003 iron-sulfur cluster co-chaperone protein HscB, mitochondrial-like isoform X1 K04082 hscB; molecular chaperone HscB D 111699686 nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1 D 111701096 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 111710846 iron-sulfur cluster assembly 1 homolog, mitochondrial-like K22063 ISCA1; iron-sulfur cluster assembly 1 D 111700346 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 111695117 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 111714030 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 111709635 bolA-like protein DDB_G0274169 K22066 BOLA1; BolA-like protein 1 D 111717404 sideroflexin-1-like K23500 SFXN1_3; sideroflexin-1/3 D 111715024 sideroflexin-2 K23501 SFXN2; sideroflexin-2 C Other regulator of mitochondrial biogenesis D 111701102 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 111698449 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 111705112 host cell factor 1 K14966 HCFC1; host cell factor 1 D 111707916 huntingtin K04533 HD; huntingtin D 111718284 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 111715911 lon protease homolog, mitochondrial K08675 LONP1; ATP-dependent Lon protease [EC:3.4.21.53] D 111701567 NAD-dependent histone deacetylase Sir2 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 111713068 protein SERAC1 K23504 SERAC1; protein SERAC1 D 111704174 protein UXT homolog K26537 UXT; protein UXT D 111718355 ES1 protein homolog, mitochondrial isoform X1 K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 111702228 transport and Golgi organization protein 2 homolog K28098 TANGO2; transport and Golgi organization protein 2 D 111698500 UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69 D 111713386 uncharacterized protein LOC111713386 K28528 ATOS; protein Atossa D 111710144 LOW QUALITY PROTEIN: probable ATP-dependent RNA helicase ddx49 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7] B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 111714780 complex I intermediate-associated protein 30, mitochondrial-like K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 111711279 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 111702936 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 111697049 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 isoform X1 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 111705224 arginine-hydroxylase NDUFAF5, mitochondrial-like K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 111705135 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 111698002 protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 111711320 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 111699823 acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 111706357 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 111701157 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 111707147 FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 111709888 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 111713059 reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 111713430 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 111697931 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 111696071 succinate dehydrogenase assembly factor 1, mitochondrial-like K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 111713362 succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 111698880 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 111702947 mitochondrial chaperone BCS1 isoform X1 K08900 BCS1; mitochondrial chaperone BCS1 D 111712806 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 111697714 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 111697132 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 C Complex-IV assembly factors D 111716634 uncharacterized protein LOC111716634 isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1 D 111711334 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 111715305 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7 D 111697163 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 111700049 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 111698659 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 111695593 mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18 D 111695633 uncharacterized protein LOC111695633 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 111700363 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 111704027 uncharacterized protein LOC111704027 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 111711818 protein PET100 homolog, mitochondrial-like K18186 PET100; protein PET100, animal type D 111702582 mitochondrial inner membrane protein OXA1L isoform X1 K03217 yidC; YidC/Oxa1 family membrane protein insertase D 111704299 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 111713997 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 111699049 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 111715020 uncharacterized protein LOC111715020 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 111713114 apoptogenic protein 1, mitochondrial K23506 APOPT1; apoptogenic protein 1 D 111705875 HIG1 domain family member 1A, mitochondrial isoform X1 K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 111714253 HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial C Complex-V assembly factors D 111697126 ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 111716158 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 111700896 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial B Mitochondrial dynamics C Fission and Fusion factors D 111716950 transmembrane GTPase Marf K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 111706698 dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 111705846 optic atrophy 3 protein isoform X1 K23166 OPA3; optic atrophy 3 protein D 111709096 putative OPA3-like protein CG13603 K23166 OPA3; optic atrophy 3 protein D 111709112 TP53-regulated inhibitor of apoptosis 1-B-like K17968 TRIAP1; TRIAP1/MDM35 family protein D 111695152 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 111699078 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 111700264 mitochondrial fission 1 protein isoform X1 K17969 FIS1; mitochondrial fission 1 protein D 111696272 small ubiquitin-related modifier K12160 SUMO; small ubiquitin-related modifier D 111698669 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 111707458 small ubiquitin-related modifier 1 isoform X1 K12160 SUMO; small ubiquitin-related modifier D 111710334 endophilin-B2 isoform X1 K11248 SH3GLB1; endophilin-B1 D 111694734 mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 111705756 transport and Golgi organization protein 11 isoform X1 K22076 MFF; mitochondrial fission factor D 111707022 ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 111697390 mitochondrial cardiolipin hydrolase isoform X1 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 111697391 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] C Actin cytoskeleton organization D 111695310 actin-5C K05692 ACTB_G1; actin beta/gamma 1 D 111695448 actin-5C K05692 ACTB_G1; actin beta/gamma 1 D 111695450 actin-5C K05692 ACTB_G1; actin beta/gamma 1 D 111695889 actin-5C K05692 ACTB_G1; actin beta/gamma 1 D 111696032 actin, clone 403 K05692 ACTB_G1; actin beta/gamma 1 D 111696550 actin, clone 205 K05692 ACTB_G1; actin beta/gamma 1 D 111698281 actin-5C K05692 ACTB_G1; actin beta/gamma 1 D 111705646 actin, clone 403 K05692 ACTB_G1; actin beta/gamma 1 D 111711181 actin-5C K05692 ACTB_G1; actin beta/gamma 1 D 111711299 actin, clone 403 K05692 ACTB_G1; actin beta/gamma 1 D 111711517 actin-5C K05692 ACTB_G1; actin beta/gamma 1 D 111713604 actin-5C isoform X1 K05692 ACTB_G1; actin beta/gamma 1 D 111714159 actin-5C isoform X1 K05692 ACTB_G1; actin beta/gamma 1 D 111717718 actin, muscle K05692 ACTB_G1; actin beta/gamma 1 D 111711332 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 111713523 N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 111695293 protein l(2)37Cc isoform X1 K17080 PHB1; prohibitin 1 D 111698014 LOW QUALITY PROTEIN: prohibitin-2-like K17081 PHB2; prohibitin 2 C Retention of mitochondria D 111699078 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 111715138 unconventional myosin-Va K10357 MYO5; myosin V D 111699210 uncharacterized protein LOC111699210 isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] C Morphogenesis factors D 111697325 mitochondrial Rho GTPase-like K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 111697947 MICOS complex subunit MIC60-1 K17785 IMMT; MICOS complex subunit MIC60 D 111717475 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 111705452 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 111710788 E3 ubiquitin-protein ligase Nedd-4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 111717078 protein misato homolog 1 K27320 MSTO1; protein misato D 111698665 PRELI domain-containing protein 1, mitochondrial K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial D 111706432 PRELI domain containing protein 3A K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial D 111704050 TM2 domain-containing protein 3 isoform X1 K28688 TM2D3; TM2 domain-containing protein 3 B Mitophagy factors C Autophagy-related proteins D 111699230 autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2 D 111716457 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 111697407 cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 111705676 cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 111711277 autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5 D 111704565 beclin-1-like protein K08334 BECN; beclin D 111709827 ubiquitin-like modifier-activating enzyme atg7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 111699316 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 111714028 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 111704661 ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 111709019 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12 D 111714023 beclin 1-associated autophagy-related key regulator isoform X1 K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 111713901 autophagy-related protein 16-1 K17890 ATG16L1; autophagy-related protein 16-1 D 111696447 WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 D 111701349 WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 111707271 E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31] D 111707647 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 111710920 protein CLEC16A homolog K19513 CLEC16A; protein CLEC16A D 111714268 serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 111695152 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 111695328 sequestosome-1 K14381 SQSTM1; sequestosome 1 D 111696442 sequestosome-1 K14381 SQSTM1; sequestosome 1 D 111702089 sequestosome-1 K14381 SQSTM1; sequestosome 1 D 111714555 sequestosome-1 K14381 SQSTM1; sequestosome 1 C Parkin-independent mechanism factors D 111704045 autophagy-related protein 13 K08331 ATG13; autophagy-related protein 13 D 111715505 serine/threonine-protein kinase ULK3 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 111715984 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 111707609 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG D 111708769 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG D 111704395 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 111711158 E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] C Other mitophagy factors D 111718284 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 111701254 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 111715769 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 111715980 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 111698977 tectonin beta-propeller repeat-containing protein K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 111707999 bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 111710089 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 111698738 protein C19orf12 K23168 MPAN; protein MPAN D 111707267 FUN14 domain-containing protein 2 isoform X1 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: July 24, 2026