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Mitochondrial Biogenesis - Electrophorus electricus (electric eel)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 113576191 polrmt; LOW QUALITY PROTEIN: DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 113577015 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 113572155 tfb1m; dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 113571113 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 113579774 mtif2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 113587483 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 113575981 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 113591399 tufm; LOW QUALITY PROTEIN: elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 113573724 gfm2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 113583462 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 113592087 mterf2; LOW QUALITY PROTEIN: transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 113567753 mterf1; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 113578436 mterf3; transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 113592164 mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 113581584 guf1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 113576036 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 113591788 pop4; ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 113567911 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 113579487 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 113589000 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 113574389 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 113576618 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 113577032 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 113585013 rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 113576750 trmt10c; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 113575440 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 113571100 kiaa0391; mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 113567772 mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 113578861 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 113580935 pentatricopeptide repeat-containing protein 1, mitochondrial-like K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 113576037 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 113576542 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 113588170 dhx30; ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 113574253 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 113567533 AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 113580765 afg1l; LOW QUALITY PROTEIN: AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 113585498 atp23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 113571539 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 113584106 lactb2; endoribonuclease LACTB2 isoform X1 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 113592058 ADP/ATP translocase 1-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 113582436 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 113583269 ADP/ATP translocase 1-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 113587350 ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 113568074 ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 113577416 slc25a28; mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 113578172 mitoferrin-1-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 113574757 mitochondrial assembly of ribosomal large subunit protein 1-like isoform X1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 113577584 eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 113575048 yars; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 113583570 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 113585517 lars; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 113572469 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 113590212 dars2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 113581216 gars; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 113582948 rars2; probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 113571270 rars; arginine--tRNA ligase, cytoplasmic isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 113589228 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial isoform X1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 113582233 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 113588108 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 113588620 mtpap; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 113572401 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 113579895 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 113587935 noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 113576639 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 113590043 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 113568242 mitochondrial RNA pseudouridine synthase rpusd4-like isoform X1 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 113573776 rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 113575541 ngrn; neugrin K23496 NGRN; neugrin
D 113575987 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 113587234 fastkd2; FAST kinase domain-containing protein 2, mitochondrial isoform X1 K18190 FASTKD2; FAST kinase domain-containing protein 2
D 113581613 cunh12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor
D 113578152 rmnd1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 113589471 grsf1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1
D 113582091 mettl15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 113578906 cunh12orf10; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 113576227 cunh6orf203; uncharacterized protein C6orf203 homolog isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 113588520 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 113583272 polg2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2
D 113589648 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 113577367 endog; endonuclease G, mitochondrial isoform X1 K01173 ENDOG; endonuclease G, mitochondrial
D 113581877 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 113568489 exog; nuclease EXOG, mitochondrial isoform X1 K15050 EXOG; nuclease EXOG, mitochondrial
D 113577642 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 113591151 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 113575808 ssbp1; single-stranded DNA-binding protein, mitochondrial isoform X1 K03111 ssb; single-strand DNA-binding protein
D 113582809 atad3a; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 113576022 ubiquinol-cytochrome-c reductase complex assembly factor 2 isoform X1 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 113588914 dnaja2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 113570898 dnaJ homolog subfamily A member 2-like K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 113574212 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 113584944 mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 113578848 mitochondrial Rho GTPase 1-A-like isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 113578453 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 113580846 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 113568294 heat shock cognate 71 kDa protein-like isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 113585214 AH receptor-interacting protein-like K17767 AIP; AH receptor-interacting protein
D 113580366 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 113569732 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 113570458 AH receptor-interacting protein-like K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 113578381 tomm40; mitochondrial import receptor subunit TOM40 homolog isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 113575684 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 113591362 mitochondrial import receptor subunit TOM40B-like K11518 TOM40; mitochondrial import receptor subunit TOM40
D 113575900 tomm70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 113574813 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 113586503 tomm20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 113590952 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 113572040 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 113576024 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 113582657 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 113586427 samm50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 113578039 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 113583300 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 113576328 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2
D 113584917 voltage-dependent anion-selective channel protein 2-like isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
D 113591667 voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 113574997 mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 113582740 mtx2; metaxin-2 isoform X1 K17776 MTX; metaxin
D 113588568 metaxin-1-like isoform X1 K17776 MTX; metaxin
D 113571227 metaxin-1-like K17776 MTX; metaxin
D 113577582 myo19; unconventional myosin-XIX K25838 MYO19; myosin XIX
D 113574154 mitochondrial amidoxime-reducing component 1-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 113578601 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 113571523 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 113581674 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 113573357 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 113570227 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 113577827 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 113581444 chchd4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 113584965 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 113580160 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 113582808 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 113576546 immt; LOW QUALITY PROTEIN: MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
D 113576182 cunh19orf70; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 113587059 chchd3; MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 113576426 MICOS complex subunit mic25a-like isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 113569206 MICOS complex subunit mic25a-like K17564 CHCHD6; MICOS complex subunit MIC25
D 113570206 apoo; MICOS complex subunit MIC26 isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 113573871 MICOS complex subunit MIC26-like isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 113574159 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 113580160 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 113582808 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 113576546 immt; LOW QUALITY PROTEIN: MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 113570246 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 113577633 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 113572746 mitochondrial import inner membrane translocase subunit Tim23-like K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 113578763 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 113578930 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 113588757 timm21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 113569699 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 113585469 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 113585366 micu1; LOW QUALITY PROTEIN: calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial
D 113589723 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 113588323 calcium uniporter regulatory subunit MCUb, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 113586146 smdt1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 113591348 essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial
D 113583193 mitochondrial calcium uniporter regulator 1-like isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 113589681 letm1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 113578127 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 113586443 immp2l; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 113579047 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 113586660 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 113574321 mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 113574912 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
D 113590045 coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial-like K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 113592153 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 113584803 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 113591180 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 113573418 grpE protein homolog 2, mitochondrial-like K03687 GRPE; molecular chaperone GrpE
D 113577811 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 isoform X1 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 113576813 pam16; mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 113572911 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 113578008 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 113578643 LOW QUALITY PROTEIN: mitochondrial intermediate peptidase-like K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 113587569 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 113568395 dnaJ homolog subfamily A member 3, mitochondrial-like K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 113576793 dnaja3; dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 113589603 tamm41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 113588023 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 113574425 persulfide dioxygenase ETHE1, mitochondrial-like K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 113569737 polymerase delta-interacting protein 2-like isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
D 113582109 polymerase delta-interacting protein 2-like isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 113577247 cyclic AMP-responsive element-binding protein 1-like K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 113567647 creb1; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 113573724 gfm2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 113583462 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 113581441 sp1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1
D 113576645 transcriptional repressor protein YY1-like K09201 YY; transcription factor YY
D 113591254 transcriptional repressor protein YY1 isoform X1 K09201 YY; transcription factor YY
D 113571956 GA-binding protein subunit beta-1-like isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 113582917 GA-binding protein subunit beta-1-like K09454 GABPB; GA-binding protein transcription factor, beta
D 113585362 gabpb1; GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 113577015 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 113591005 nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 113582319 nfe2l2; LOW QUALITY PROTEIN: nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 113579130 metallothionein A-like K14739 MT1_2; metallothionein 1/2
C Coactivators
D 113580475 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 113573375 peroxisome proliferator-activated receptor gamma coactivator 1-beta-like K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 113589687 peroxisome proliferator-activated receptor gamma coactivator-related protein 1-like K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 113585835 peroxisome proliferator-activated receptor gamma coactivator-related protein 1-like isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 113581912 crtc1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 113580680 LOW QUALITY PROTEIN: CREB-binding protein-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 113588922 histone acetyltransferase p300-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 113576788 crebbp; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 113574829 ep300; LOW QUALITY PROTEIN: histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 113578915 nfs1; cysteine desulfurase, mitochondrial isoform X1 K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 113576912 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 113579391 lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 113580070 fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 113568993 adrenodoxin-like K22070 FDX1; ferredoxin-1, mitochondrial
D 113576558 fdx1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 113579543 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 113581986 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 113584803 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 113577758 hscb; iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB
D 113590584 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 113571728 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 113576904 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 113583326 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial isoform X1 K22072 ISCA2; iron-sulfur cluster assembly 2
D 113590808 iba57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 113585789 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 113567855 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 113579569 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 113578507 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 113585809 sideroflexin-1-like K23500 SFXN1_3; sideroflexin-1/3
D 113588599 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 113577630 sfxn2; sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2
D 113579914 sfxn4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4
D 113585302 sfxn5; sideroflexin-5 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 113580509 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 113579687 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 113583373 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 113589507 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 113584502 dhtkd1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 113591153 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 113572359 host cell factor 1-like K14966 HCFC1; host cell factor 1
D 113575846 hcfc1; LOW QUALITY PROTEIN: host cell factor 1 K14966 HCFC1; host cell factor 1
D 113584413 hcfc2; host cell factor 2 K27390 HCFC2; host cell factor 2
D 113571465 htt; huntingtin K04533 HD; huntingtin
D 113590816 esrra; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 113585935 esrrb; LOW QUALITY PROTEIN: steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta
D 113588499 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 113580121 estrogen-related receptor gamma-like isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 113584464 nuclear receptor-interacting protein 1-like K17965 NRIP1; nuclear receptor-interacting protein 1
D 113586323 nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 113589709 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 113570222 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 113591724 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 113567518 sirt1; NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 113570569 serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 113585823 uxt; protein UXT K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 113576230 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 113580052 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 113582798 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 isoform X1 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 113590555 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 isoform X1 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 113579675 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 113572709 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 113571678 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 113577631 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 isoform X1 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 113581832 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 113589349 acad9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 113576675 nubpl; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 113580716 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 113589229 rtn4ip1; reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 113590734 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 113569870 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 113577203 mitochondrial chaperone BCS1 isoform X1 K08900 BCS1; mitochondrial chaperone BCS1
D 113590311 ttc19; tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 113576748 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 113574253 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 113576022 ubiquinol-cytochrome-c reductase complex assembly factor 2 isoform X1 K17682 MNF1; mitochondrial nucleoid factor 1
D 113576267 ubiquinol-cytochrome-c reductase complex assembly factor 3-like K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 113586581 cunh16orf91; protein CCSMST1 isoform X1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 113569974 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 113586447 cunh12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 113587781 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 113574440 cmc1; COX assembly mitochondrial protein homolog isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1
D 113570811 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 113584244 cytochrome c oxidase assembly factor 1 homolog isoform X1 K18173 COA1; cytochrome c oxidase assembly factor 1
D 113574308 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 113582993 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 113591091 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 113575815 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 113591626 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 113568188 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 113579426 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 113583735 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 113590660 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 113574733 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 113587744 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 113587940 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 113591436 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 113587690 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 113567772 mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 113581859 pet100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 113581479 pet117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 113573509 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 113570219 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 113577889 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 113585504 protein SCO2 homolog, mitochondrial-like K23755 SCO2; protein SCO2
D 113576837 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 113578353 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 113584109 apopt1; apoptogenic protein 1, mitochondrial isoform X1 K23506 APOPT1; apoptogenic protein 1
D 113587781 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 113569974 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 113574454 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 113574527 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 113591508 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 113578061 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 113572957 6.8 kDa mitochondrial proteolipid-like K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 113574601 atp5md; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 113578499 mitofusin-1-like K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 113578194 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 113570429 opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 113589585 opa3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein
D 113573331 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 113588545 parl; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 113580268 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 113578802 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 113589910 bax; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 113579723 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 113578149 LOW QUALITY PROTEIN: dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 113583641 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 113579803 mitochondrial fission 1 protein-like K17969 FIS1; mitochondrial fission 1 protein
D 113584103 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 113584791 sumo2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 113574650 small ubiquitin-related modifier 3-like isoform X1 K12160 SUMO; small ubiquitin-related modifier
D 113567680 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 113582774 small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier
D 113575635 endophilin-B1-like K11248 SH3GLB1; endophilin-B1
D 113591231 endophilin-B1-like isoform X1 K11248 SH3GLB1; endophilin-B1
D 113588911 mtch2; mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier
D 113582153 mitochondrial fission factor-like isoform X1 K22076 MFF; mitochondrial fission factor
D 113581582 mff; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor
D 113591661 mitochondrial fission factor homolog A-like isoform X1 K22076 MFF; mitochondrial fission factor
D 113584468 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 113578598 gdap1l1; LOW QUALITY PROTEIN: ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 113589802 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 113569798 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 113580906 mitochondrial dynamics protein MID51-like K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 113583728 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 113590046 miga2; mitoguardin 2 K27289 MIGA; mitoguardin
D 113570142 miga1; mitoguardin 1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 113580904 actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 113585569 actb; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 113571717 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 113591670 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 113580240 phb; prohibitin K17080 PHB1; prohibitin 1
D 113579540 prohibitin-2-like K17081 PHB2; prohibitin 2
D 113591766 prohibitin-2-like K17081 PHB2; prohibitin 2
D 113583307 ktn1; LOW QUALITY PROTEIN: kinectin K17975 KTN1; kinectin
C Retention of mitochondria
D 113579723 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 113578149 LOW QUALITY PROTEIN: dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 113588945 unconventional myosin-Vb-like K10357 MYO5; myosin V
D 113568348 unconventional myosin-Va-like K10357 MYO5; myosin V
D 113575206 myo5b; unconventional myosin-Vb K10357 MYO5; myosin V
D 113584501 myo5c; unconventional myosin-Vc K10357 MYO5; myosin V
D 113584514 unconventional myosin-Va-like K10357 MYO5; myosin V
D 113581375 xiap; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 113573455 diablo; diablo homolog, mitochondrial K10522 DIABLO; diablo
D 113587637 diablo homolog, mitochondrial-like K10522 DIABLO; diablo
C Morphogenesis factors
D 113581751 snx25; sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 113584944 mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 113578848 mitochondrial Rho GTPase 1-A-like isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 113576546 immt; LOW QUALITY PROTEIN: MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
D 113588083 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 113570602 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 113584271 nedd4; E3 ubiquitin-protein ligase NEDD4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 113577070 oxr1; LOW QUALITY PROTEIN: oxidation resistance protein 1 K25437 OXR1; oxidation resistance protein 1
D 113583856 msto1; protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 113581573 atg2a; autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 113583311 atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 113579636 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 113579678 cysteine protease ATG4D-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 113568380 cysteine protease ATG4D-like isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 113575927 atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 113587813 atg4c; cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 113582865 atg4a; cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 113581711 atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 113576843 becn1; beclin-1 K08334 BECN; beclin
D 113583792 ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 113568339 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 113580805 gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 113570205 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 113570646 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 113582756 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 113583780 autophagy-related protein 9A-like isoform X1 K17907 ATG9; autophagy-related protein 9
D 113590885 atg10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 113570704 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 113579336 atg14; beclin 1-associated autophagy-related key regulator isoform X1 K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 113588544 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 113574671 autophagy-related protein 16-2-like isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 113580266 wipi1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 113589656 wipi2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 113572720 prkn; LOW QUALITY PROTEIN: E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 113587252 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 113572843 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 113570339 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 113588545 parl; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 113584814 sqstm1; sequestosome-1 K14381 SQSTM1; sequestosome 1
D 113571160 tax1-binding protein 1 homolog B-like K21347 TAX1BP1; Tax1-binding protein 1
D 113580413 tax1-binding protein 1 homolog A-like isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 113574823 calcium-binding and coiled-coil domain-containing protein 2-like K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 113584511 ambra1; LOW QUALITY PROTEIN: activating molecule in BECN1-regulated autophagy protein 1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 113585615 atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 113584871 serine/threonine-protein kinase ULK1-like isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 113573444 ulk1; serine/threonine-protein kinase ULK1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 113569687 ulk2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 113581641 rb1cc1; LOW QUALITY PROTEIN: RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 113569657 heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG
D 113569531 heat shock protein HSP 90-alpha isoform X1 K04079 HSP90A; molecular chaperone HtpG
D 113580649 hsp90ab1; heat shock protein HSP 90-beta isoform X1 K04079 HSP90A; molecular chaperone HtpG
D 113585196 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 113570666 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 113583267 smurf2; LOW QUALITY PROTEIN: E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 113575189 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 113587413 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 113571004 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 113582594 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1
D 113574352 fundc1; FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 113589709 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 113570222 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 113589347 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 113586510 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 113585311 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 113590009 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 113574863 nbr1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 113580871 next to BRCA1 gene 1 protein-like isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 113569883 tectonin beta-propeller repeat-containing protein 1-like isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 113579465 tecpr1; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 113582033 zinc finger FYVE domain-containing protein 1-like isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 113570180 zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 113583783 coasy; bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 113585736 pla2g6; 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 113577198 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 113591785 cunh19orf12; protein C19orf12 homolog K23168 MPAN; protein MPAN
D 113583181 fundc2; FUN14 domain-containing protein 2 isoform X1 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024