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Mitochondrial Biogenesis - Gigantopelta aegis (peltospirid snail)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 121390668 DNA-directed RNA polymerase, mitochondrial-like isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 121378914 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 121375186 dimethyladenosine transferase 1, mitochondrial-like K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 121371052 dimethyladenosine transferase 2, mitochondrial-like K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 121371615 translation initiation factor IF-2, mitochondrial-like K02519 infB; translation initiation factor IF-2
D 121375712 translation initiation factor IF-3-like K02520 infC; translation initiation factor IF-3
D 121387459 elongation factor Ts, mitochondrial-like isoform X1 K02357 tsf; elongation factor Ts
D 121369161 elongation factor Tu, mitochondrial-like K02358 tuf; elongation factor Tu
D 121377011 elongation factor Tu, mitochondrial-like K02358 tuf; elongation factor Tu
D 121370510 ribosome-releasing factor 2, mitochondrial-like K02355 fusA; elongation factor G
D 121388471 elongation factor G, mitochondrial-like K02355 fusA; elongation factor G
D 121376819 transcription termination factor 3, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 121386406 transcription termination factor 4, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 121376037 translation factor Guf1, mitochondrial-like isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 121375166 LOW QUALITY PROTEIN: ribonucleases P/MRP protein subunit POP1-like K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 121389381 ribonuclease P protein subunit p29-like K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 121380795 ribonuclease P/MRP protein subunit POP5-like isoform X1 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 121383375 ribonuclease P protein subunit p30-like K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 121370203 ribonuclease P protein subunit p20-like K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 121380821 ribonuclease P protein subunit p25-like protein isoform X1 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 121375405 ribonuclease P protein subunit p38-like K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 121388724 ribonuclease P protein subunit p40-like isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 121367609 tRNA methyltransferase 10 homolog C-like K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 121367959 3-hydroxyacyl-CoA dehydrogenase type-2-like K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 121370409 mitochondrial ribonuclease P catalytic subunit-like isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 121378985 transcription elongation factor, mitochondrial-like K17658 TEFM; transcription elongation factor, mitochondrial
D 121378751 pentatricopeptide repeat-containing protein 1, mitochondrial-like K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 121382973 protein PTCD3 homolog, mitochondrial-like K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 121377245 ubiquinol-cytochrome-c reductase complex assembly factor 1-like K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 121371893 AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 121391138 LOW QUALITY PROTEIN: AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 121367892 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 121392516 LOW QUALITY PROTEIN: mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 121383217 ATP-dependent RNA helicase SUPV3L1, mitochondrial-like K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 121376750 endoribonuclease LACTB2-like K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 121392475 LOW QUALITY PROTEIN: endoribonuclease LACTB2-like K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 121375693 ADP,ATP carrier protein 3, mitochondrial-like isoform X1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 121378779 ADP,ATP carrier protein 3, mitochondrial-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 121382780 mitoferrin-2-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 121387660 uncharacterized protein LOC121387660 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 121368356 GTPase Era, mitochondrial-like K03595 era; GTPase
D 121379250 tyrosine--tRNA ligase, mitochondrial-like K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 121375132 leucine--tRNA ligase, cytoplasmic-like K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 121388790 probable leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 121384786 aspartate--tRNA ligase, mitochondrial-like isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 121381190 glycine--tRNA ligase-like K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 121374268 arginine--tRNA ligase, cytoplasmic-like K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 121388661 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 121391409 LOW QUALITY PROTEIN: arginine--tRNA ligase, cytoplasmic-like K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 121372617 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial-like K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 121376154 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial-like isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 121368216 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial-like K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 121380621 2',5'-phosphodiesterase 12-like K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 121380928 mitochondrial ribosome-associated GTPase 1-like K19828 MTG1; mitochondrial GTPase 1
D 121392835 LOW QUALITY PROTEIN: mitochondrial ribosome-associated GTPase 1-like K19828 MTG1; mitochondrial GTPase 1
D 121384473 nitric oxide-associated protein 1-like K19832 NOA1; nitric oxide-associated protein 1
D 121372155 5-methylcytosine rRNA methyltransferase NSUN4-like K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 121377517 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 121377263 uncharacterized protein LOC121377263 K23496 NGRN; neugrin
D 121384397 mitochondrial mRNA pseudouridine synthase Trub2-like K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 121388703 FAST kinase domain-containing protein 1, mitochondrial-like K27754 FASTKD1; FAST kinase domain-containing protein 1
D 121385327 FAST kinase domain-containing protein 3, mitochondrial-like K27755 FASTKD3; FAST kinase domain-containing protein 3
D 121385582 FAST kinase domain-containing protein 4-like K27756 TBRG4; FAST kinase domain-containing protein 4
D 121377739 FAST kinase domain-containing protein 5, mitochondrial-like isoform X1 K27757 FASTKD5; FAST kinase domain-containing protein 5
D 121386771 uncharacterized protein LOC121386771 isoform X1 K27757 FASTKD5; FAST kinase domain-containing protein 5
D 121368452 probable peptide chain release factor C12orf65, mitochondrial isoform X1 K23498 COXPD7; peptide chain release factor
D 121369337 required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 121372244 12S rRNA N4-methylcytidine methyltransferase-like K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 121381067 MYG1 exonuclease-like K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 121370697 uncharacterized protein LOC121370697 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 121380688 LOW QUALITY PROTEIN: DNA polymerase subunit gamma-1-like K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 121378540 DNA polymerase subunit gamma-2, mitochondrial-like K02333 POLG2; DNA polymerase gamma 2
D 121379111 DNA-directed primase/polymerase protein-like K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 121383391 endonuclease G, mitochondrial-like K01173 ENDOG; endonuclease G, mitochondrial
D 121370598 uncharacterized protein LOC121370598 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 121382225 nuclease EXOG, mitochondrial-like isoform X1 K15050 EXOG; nuclease EXOG, mitochondrial
D 121390797 twinkle protein, mitochondrial-like K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 121376159 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 121381205 single-stranded DNA-binding protein, mitochondrial-like K03111 ssb; single-strand DNA-binding protein
D 121389769 LOW QUALITY PROTEIN: ATPase family AAA domain-containing protein 3-B-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 121374763 ubiquinol-cytochrome-c reductase complex assembly factor 2-like K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 121387987 dnaJ homolog subfamily A member 2-like K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 121378285 mitochondrial Rho GTPase 1-like isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 121374185 heat shock protein 70 A1-like isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121374307 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121374308 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121374339 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121384593 heat shock protein 70 A1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121385207 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121385431 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121391748 AH receptor-interacting protein-like K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 121371229 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 121378716 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 121386341 mitochondrial import receptor subunit TOM40 homolog 1-like K11518 TOM40; mitochondrial import receptor subunit TOM40
D 121386482 mitochondrial import receptor subunit TOM70-like K17768 TOM70; mitochondrial import receptor subunit TOM70
C TOB/SAM complex
D 121381120 sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 121380260 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2
C ERMES complex
C Other outer membrane factor
D 121378738 metaxin-1-like K17776 MTX; metaxin
D 121385170 metaxin-2-like isoform X1 K17776 MTX; metaxin
D 121368440 unconventional myosin-XIX-like isoform X1 K25838 MYO19; myosin XIX
D 121370098 uncharacterized protein LOC121370098 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 121371507 mitochondrial amidoxime reducing component 2-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 121371963 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 121375269 mitochondrial import inner membrane translocase subunit Tim9-like K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 121370974 mitochondrial import inner membrane translocase subunit Tim13-like K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 121390779 mitochondrial intermembrane space import and assembly protein 40-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 121379383 FAD-linked sulfhydryl oxidase ALR-like K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 121390130 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 121382779 MICOS complex subunit MIC60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 121373379 MICOS complex subunit MIC13-like K24624 MICOS13; MICOS complex subunit MIC13
D 121369266 MICOS complex subunit MIC19-like K17563 CHCHD3; MICOS complex subunit MIC19
D 121376979 MICOS complex subunit MIC27-like K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 121390130 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 121382779 MICOS complex subunit MIC60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 121368341 mitochondrial import inner membrane translocase subunit Tim22-like K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 121378491 mitochondrial import inner membrane translocase subunit Tim23-like K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 121367787 mitochondrial import inner membrane translocase subunit Tim17-A-like K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 121388933 mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 121370905 mitochondrial import inner membrane translocase subunit TIM50-C-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 121378481 calcium uniporter protein, mitochondrial-like K20858 MCU; calcium uniporter protein, mitochondrial
D 121379423 calcium uptake protein 1, mitochondrial-like isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 121388677 mitochondrial calcium uniporter regulator 1-like isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 121382684 mitochondrial proton/calcium exchanger protein-like isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 121380689 mitochondrial inner membrane protease subunit 1-like K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 121392508 mitochondrial inner membrane protease subunit 1-like K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 121367777 mitochondrial inner membrane protease subunit 2-like isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 121366477 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A
D 121371914 mitochondrial pyruvate carrier 1-like K22138 MPC1; mitochondrial pyruvate carrier 1
D 121370818 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
D 121374334 OCIA domain-containing protein 1-like K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 121387330 mitochondrial import inner membrane translocase subunit TIM44-like K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 121382841 stress-70 protein, mitochondrial-like K04043 dnaK; molecular chaperone DnaK
D 121383157 grpE protein homolog 1, mitochondrial-like K03687 GRPE; molecular chaperone GrpE
D 121369516 mitochondrial import inner membrane translocase subunit TIM14-like K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 121376077 mitochondrial import inner membrane translocase subunit Tim16-like isoform X1 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 121383929 mitochondrial-processing peptidase subunit alpha-like K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 121367938 mitochondrial-processing peptidase subunit beta-like K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 121372889 mitochondrial intermediate peptidase-like K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 121380527 heat shock protein 60A-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 121380528 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 121375243 protein tumorous imaginal discs, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 121366353 LOW QUALITY PROTEIN: phosphatidate cytidylyltransferase, mitochondrial-like K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 121371632 phosphatidate cytidylyltransferase, mitochondrial-like K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 121383220 uncharacterized protein LOC121383220 K17808 ZIM17; mitochondrial protein import protein ZIM17
D 121386223 persulfide dioxygenase ETHE1, mitochondrial-like K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 121367880 polymerase delta-interacting protein 2-like K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 121370510 ribosome-releasing factor 2, mitochondrial-like K02355 fusA; elongation factor G
D 121388471 elongation factor G, mitochondrial-like K02355 fusA; elongation factor G
D 121370635 transcriptional repressor protein YY1-like isoform X1 K09201 YY; transcription factor YY
D 121373237 GA-binding protein subunit beta-1-like isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 121378914 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 121369229 DNA-binding protein P3A2-like K11831 NRF1; nuclear respiratory factor 1
D 121369298 DNA-binding protein P3A2-like K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 121379786 CREB-regulated transcription coactivator 1-like isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 121375784 CREB-binding protein-like isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 121388361 cysteine desulfurase, mitochondrial-like K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 121391158 LOW QUALITY PROTEIN: cysteine desulfurase, mitochondrial-like K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 121370624 iron-sulfur cluster assembly scaffold protein IscU-like K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 121388990 LYR motif-containing protein 4-like K22069 LYRM4; LYR motif-containing protein 4
D 121377651 frataxin, mitochondrial-like K19054 FXN; frataxin [EC:1.16.3.1]
D 121372609 adrenodoxin-like protein 2, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 121376548 adrenodoxin-like protein 1, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 121392706 adrenodoxin-like protein 1, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 121379228 NADPH:adrenodoxin oxidoreductase, mitochondrial-like K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 121392794 LOW QUALITY PROTEIN: NADPH:adrenodoxin oxidoreductase, mitochondrial-like K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 121382841 stress-70 protein, mitochondrial-like K04043 dnaK; molecular chaperone DnaK
D 121377487 iron-sulfur cluster co-chaperone protein HscB-like K04082 hscB; molecular chaperone HscB
D 121384125 LOW QUALITY PROTEIN: nucleotide exchange factor SIL1-like K14001 SIL1; nucleotide exchange factor SIL1
D 121380622 glutaredoxin-related protein 5, mitochondrial-like K07390 grxD; monothiol glutaredoxin
D 121375202 iron-sulfur cluster assembly 1 homolog, mitochondrial-like K22063 ISCA1; iron-sulfur cluster assembly 1
D 121369666 iron-sulfur cluster assembly 2 homolog, mitochondrial-like K22072 ISCA2; iron-sulfur cluster assembly 2
D 121370418 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 121378450 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 121379426 DNA-binding transcriptional regulator BolA-like isoform X1 K22066 BOLA1; BolA-like protein 1
D 121388324 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 121384205 sideroflexin-1-like K23500 SFXN1_3; sideroflexin-1/3
D 121382826 sideroflexin-2-like K23501 SFXN2; sideroflexin-2
D 121384710 sideroflexin-5-like isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 121370983 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 121372730 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 121392756 LOW QUALITY PROTEIN: probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 121381283 F-box/LRR-repeat protein 4-like K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 121369156 host cell factor 1-like isoform X1 K14966 HCFC1; host cell factor 1
D 121382843 huntingtin-like isoform X1 K04533 HD; huntingtin
D 121384497 nuclear hormone receptor FTZ-F1 beta-like K08553 NR3B2; estrogen-related receptor beta
D 121370372 steroid hormone receptor ERR2-like isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 121376464 5'-AMP-activated protein kinase catalytic subunit alpha-2-like K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 121384968 lon protease homolog, mitochondrial-like K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 121379090 NAD-dependent protein deacetylase sirtuin-1-like isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 121383884 protein SERAC1-like K23504 SERAC1; protein SERAC1
D 121368210 protein UXT-like K26537 UXT; protein UXT
D 121372069 transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2
D 121380882 UPF0565 protein C2orf69 homolog isoform X1 K28271 C2ORF69; mitochondrial protein C2orf69
D 121373831 protein FAM214A-like K28528 ATOS; protein Atossa
D 121379172 probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7]
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 121371438 complex I intermediate-associated protein 30, mitochondrial-like K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 121374003 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2-like K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 121369032 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3-like isoform X1 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 121371835 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 121370073 arginine-hydroxylase NDUFAF5, mitochondrial-like K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 121391448 LOW QUALITY PROTEIN: arginine-hydroxylase NDUFAF5, mitochondrial-like K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 121388988 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6-like isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 121372336 protein arginine methyltransferase NDUFAF7, mitochondrial-like isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 121380044 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial-like isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 121367866 complex I assembly factor ACAD9, mitochondrial-like isoform X1 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 121387768 iron-sulfur protein NUBPL-like isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 121391645 LOW QUALITY PROTEIN: iron-sulfur protein NUBPL-like K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 121391647 iron-sulfur protein NUBPL-like K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 121382660 FAD-dependent oxidoreductase domain-containing protein 1-like K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 121370724 reticulon-4-interacting protein 1, mitochondrial-like isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 121366269 uncharacterized protein LOC121366269 isoform X1 K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
C Complex-III assembly factors
D 121372159 mitochondrial chaperone BCS1-like K08900 BCS1; mitochondrial chaperone BCS1
D 121383393 tetratricopeptide repeat protein 19, mitochondrial-like K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 121376462 complex III assembly factor LYRM7-like isoform X1 K18170 LYRM7; complex III assembly factor LYRM7
D 121377245 ubiquinol-cytochrome-c reductase complex assembly factor 1-like K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 121374763 ubiquinol-cytochrome-c reductase complex assembly factor 2-like K17682 MNF1; mitochondrial nucleoid factor 1
D 121379178 uncharacterized protein LOC121379178 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
C Complex-IV assembly factors
D 121376920 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 121389436 COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 121387409 uncharacterized protein LOC121387409 K18173 COA1; cytochrome c oxidase assembly factor 1
D 121385197 cytochrome c oxidase assembly factor 3, mitochondrial-like K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 121371664 cytochrome c oxidase assembly factor 4 homolog, mitochondrial-like K18177 COA4; cytochrome c oxidase assembly factor 4
D 121375908 cytochrome c oxidase assembly factor 5-like K18178 COA5; cytochrome c oxidase assembly factor 5
D 121369635 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 121375500 cytochrome c oxidase assembly factor 7B-like K18180 COA7; cytochrome c oxidase assembly factor 7
D 121378401 protoheme IX farnesyltransferase, mitochondrial-like K02257 COX10; heme o synthase [EC:2.5.1.141]
D 121378414 cytochrome c oxidase assembly protein COX11, mitochondrial-like K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 121391178 LOW QUALITY PROTEIN: cytochrome c oxidase assembly protein COX11, mitochondrial-like K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 121383112 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 121371633 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial-like isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 121378228 cytochrome c oxidase assembly protein COX18, mitochondrial-like K17797 COX18; mitochondrial inner membrane protein COX18
D 121378594 cytochrome c oxidase assembly protein COX19-like K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 121375106 protein PET100 homolog, mitochondrial-like K18186 PET100; protein PET100, animal type
D 121388817 mitochondrial inner membrane protein OXA1L-like K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 121383101 surfeit locus protein 1-like K14998 SURF1; surfeit locus 1 family protein
D 121390727 protein SCO1 homolog, mitochondrial-like K07152 SCO1; protein SCO1
D 121381000 probable transcriptional regulatory protein Cagg_2594 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 121370354 leucine-rich PPR motif-containing protein, mitochondrial-like K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 121371172 COA8 family protein CBG23705, mitochondrial-like K23506 APOPT1; apoptogenic protein 1
D 121372373 transmembrane protein 223-like K27342 TMEM223; transmembrane protein 223
D 121382671 HIG1 domain family member 2A, mitochondrial-like K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial
C Complex-V assembly factors
D 121379155 ATP synthase mitochondrial F1 complex assembly factor 2-like K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 121388449 transmembrane protein 70 homolog, mitochondrial-like K17966 TMEM70; transmembrane protein 70, mitochondrial
D 121388537 uncharacterized protein LOC121388537 K17966 TMEM70; transmembrane protein 70, mitochondrial
B Mitochondrial dynamics
C Fission and Fusion factors
D 121390185 mitofusin-2-like isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 121390117 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 121372087 putative OPA3-like protein CG13603 K23166 OPA3; optic atrophy 3 protein
D 121368218 TP53-regulated inhibitor of apoptosis 1-like K17968 TRIAP1; TRIAP1/MDM35 family protein
D 121369620 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 121372114 bcl-2 homologous antagonist/killer-like K14021 BAK; Bcl-2 homologous antagonist/killer
D 121380597 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 121386736 uncharacterized protein LOC121386736 K02159 BAX; apoptosis regulator BAX
D 121369417 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 121373447 mitochondrial fission 1 protein-like K17969 FIS1; mitochondrial fission 1 protein
D 121375150 small ubiquitin-related modifier 2-A-like K12160 SUMO; small ubiquitin-related modifier
D 121384153 endophilin-B1-like isoform X1 K11248 SH3GLB1; endophilin-B1
D 121369873 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier
D 121377217 uncharacterized protein LOC121377217 isoform X1 K22076 MFF; mitochondrial fission factor
D 121388165 ganglioside-induced differentiation-associated protein 1-like isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 121388473 ganglioside-induced differentiation-associated protein 1-like K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 121388793 ganglioside-induced differentiation-associated protein 1-like K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 121389425 ganglioside-induced differentiation-associated protein 1-like K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 121379209 mitochondrial cardiolipin hydrolase-like K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 121383181 mitoguardin-like K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 121373886 actin, cytoplasmic-like K05692 ACTB_G1; actin beta/gamma 1
D 121374109 actin-5 K05692 ACTB_G1; actin beta/gamma 1
D 121374110 actin, cytoplasmic K05692 ACTB_G1; actin beta/gamma 1
D 121374111 LOW QUALITY PROTEIN: actin-like K05692 ACTB_G1; actin beta/gamma 1
D 121374286 actin, cytoplasmic 3-like K05692 ACTB_G1; actin beta/gamma 1
D 121376475 actin, adductor muscle-like isoform X1 K05692 ACTB_G1; actin beta/gamma 1
D 121384432 actin, adductor muscle K05692 ACTB_G1; actin beta/gamma 1
D 121370127 N-alpha-acetyltransferase 20-like K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 121367909 N-alpha-acetyltransferase 25, NatB auxiliary subunit-like K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 121382913 prohibitin-like K17080 PHB1; prohibitin 1
D 121390737 prohibitin-2-like K17081 PHB2; prohibitin 2
D 121392106 LOW QUALITY PROTEIN: prohibitin-2-like K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 121369417 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 121373473 unconventional myosin-Vb-like K10357 MYO5; myosin V
D 121374247 baculoviral IAP repeat-containing protein 2-like K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 121381272 uncharacterized protein LOC121381272 isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 121374140 sorting nexin-25-like isoform X1 K17887 SNX25; sorting nexin-25
D 121378285 mitochondrial Rho GTPase 1-like isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 121382779 MICOS complex subunit MIC60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 121368283 mitochondrial fission process protein 1-like K17981 MTFP1; mitochondrial fission process protein 1
D 121386440 28S ribosomal protein S29, mitochondrial-like K17408 DAP3; small subunit ribosomal protein S29
D 121382175 E3 ubiquitin-protein ligase NEDD4-like isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 121377198 protein misato homolog 1-like K27320 MSTO1; protein misato
D 121384194 PRELI domain-containing protein 1, mitochondrial-like K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 121387994 PRELI domain containing protein 3B-like K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 121371346 autophagy-related protein 2 homolog A-like isoform X1 K17906 ATG2; autophagy-related protein 2
D 121373303 ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 121367475 cysteine protease ATG4B-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 121376004 cysteine protease ATG4C-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 121392555 LOW QUALITY PROTEIN: cysteine protease ATG4D-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 121369628 autophagy protein 5-like K08339 ATG5; autophagy-related protein 5
D 121387527 beclin-1-like isoform X1 K08334 BECN; beclin
D 121369155 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 121388257 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 121390515 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 121381095 autophagy-related protein 9A-like K17907 ATG9; autophagy-related protein 9
D 121375866 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 121378723 ubiquitin-like protein ATG12 isoform X1 K08336 ATG12; ubiquitin-like protein ATG12
D 121370262 beclin 1-associated autophagy-related key regulator-like K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 121369195 autophagy-related protein 16-1-like K17890 ATG16L1; autophagy-related protein 16-1
D 121379366 WD repeat domain phosphoinositide-interacting protein 2-like isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 121377589 vacuolar protein 8-like K08332 VAC8; vacuolar protein 8
C Parkin-dependent mechanism factors
D 121370189 E3 ubiquitin-protein ligase parkin-like K04556 PARK2; parkin [EC:2.3.2.31]
D 121387540 E3 ubiquitin-protein ligase NRDP1-like K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 121378764 protein CLEC16A-like K19513 CLEC16A; protein CLEC16A
D 121369620 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 121374896 sequestosome-1-like K14381 SQSTM1; sequestosome 1
D 121374981 sequestosome-1-like K14381 SQSTM1; sequestosome 1
D 121385670 tax1-binding protein 1 homolog K21347 TAX1BP1; Tax1-binding protein 1
D 121372499 activating molecule in BECN1-regulated autophagy protein 1-like K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 121373893 autophagy-related protein 13-like K08331 ATG13; autophagy-related protein 13
D 121369141 serine/threonine-protein kinase unc-51-like K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 121374347 RB1-inducible coiled-coil protein 1-like isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 121370895 heat shock protein HSP 90-beta-like K04079 HSP90A; molecular chaperone HtpG
D 121370681 hsp90 co-chaperone Cdc37-like K09554 CDC37; cell division cycle protein 37
D 121378547 E3 ubiquitin-protein ligase SMURF2-like K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 121374704 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1
D 121374730 FUN14 domain-containing protein 1A-like K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 121376464 5'-AMP-activated protein kinase catalytic subunit alpha-2-like K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 121372744 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 121382329 microtubule-associated proteins 1A/1B light chain 3A-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 121387682 next to BRCA1 gene 1 protein-like K17987 NBR1; next to BRCA1 gene 1 protein
D 121379063 tectonin beta-propeller repeat-containing protein 1-like isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 121371232 zinc finger FYVE domain-containing protein 1-like isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 121388360 bifunctional coenzyme A synthase-like K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 121378657 85/88 kDa calcium-independent phospholipase A2-like K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 121379264 85/88 kDa calcium-independent phospholipase A2-like isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025