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Mitochondrial Biogenesis - Glossina fuscipes (tsetse fly)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 119633644 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 119638748 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
D 119644158 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 119634559 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 119638040 translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 119635646 uncharacterized protein LOC119635646 K02520 infC; translation initiation factor IF-3
D 119633437 elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 119636170 elongation factor Tu K02358 tuf; elongation factor Tu
D 119633822 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 119639427 LOW QUALITY PROTEIN: ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 119632096 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 119635377 transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 119634777 translation factor waclaw, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 119642166 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 119642299 uncharacterized protein LOC119642299 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 119632136 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 119638687 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 119641862 ribonuclease P protein subunit p30 isoform X1 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 119639918 ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 119641192 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 119636938 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 119638479 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 119633685 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 119631992 uncharacterized protein LOC119631992 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 119632098 uncharacterized protein LOC119632098 K17658 TEFM; transcription elongation factor, mitochondrial
D 119645259 pentatricopeptide repeat-containing protein 1, mitochondrial isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 119641596 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 (small subunit ribosomal protein S39)
D 119645253 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 119638616 putative ATPase N2B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 119633697 mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 119639245 LOW QUALITY PROTEIN: mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 119644132 LOW QUALITY PROTEIN: mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 119644141 LOW QUALITY PROTEIN: mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 119635071 ATP-dependent RNA helicase SUV3 homolog, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 119640513 beta-lactamase-like protein 2 homolog K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 119631595 ADP,ATP carrier protein K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 119631607 ADP,ATP carrier protein 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 119638890 mitoferrin K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 119637897 mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 119636399 GTPase Era, mitochondrial K03595 era; GTPase
D 119631972 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 119644361 tyrosine--tRNA ligase, mitochondrial-like isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 119644367 tyrosine--tRNA ligase, mitochondrial-like isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 119633639 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 119645364 probable leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 119633380 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 119631737 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 119638614 probable arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 119639270 arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 119634693 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial isoform X1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 119641997 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 119640629 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 119636566 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 119637632 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 119641956 mitochondrial GTPase 1 isoform X1 K19828 MTG1; mitochondrial GTPase 1
D 119636462 nitric oxide-associated protein 1 isoform X1 K19832 NOA1; nitric oxide-associated protein 1
D 119633077 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 119643038 uncharacterized protein LOC119643038 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 119643072 uncharacterized protein LOC119643072 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 119635495 RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 119642768 uncharacterized protein LOC119642768 K23496 NGRN; neugrin
D 119636011 mitochondrial mRNA pseudouridine synthase Trub2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 119642397 FAST kinase domain-containing protein 1, mitochondrial K27754 FASTKD1; FAST kinase domain-containing protein 1
D 119640739 FAST kinase domain-containing protein 4 K27756 TBRG4; FAST kinase domain-containing protein 4
D 119640136 FAST kinase domain-containing protein 5, mitochondrial isoform X1 K27757 FASTKD5; FAST kinase domain-containing protein 5
D 119638743 probable peptide chain release factor C12orf65, mitochondrial K23498 COXPD7; peptide chain release factor
D 119638840 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 119641058 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 119639380 MYG1 protein K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 119641738 mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 119632953 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 119640628 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
C Mitochondrial DNA maintenance factors
D 119632967 endonuclease G, mitochondrial-like K01173 ENDOG; endonuclease G, mitochondrial
D 119637070 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 119633940 twinkle protein, mitochondrial K17680 TWNK; twinkle mtDNA helicase [EC:5.6.2.3]
D 119634074 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 119638700 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 119642707 ATPase family AAA domain-containing protein 3A homolog K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 119635298 dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 119641564 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 119632518 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119641924 heat shock 70 kDa protein cognate 2-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119641976 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119641999 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119642057 LOW QUALITY PROTEIN: heat shock 70 kDa protein cognate 4-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119642058 LOW QUALITY PROTEIN: heat shock 70 kDa protein cognate 4-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 119637822 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 119641319 mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 119631846 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 119632804 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 119632316 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 119636876 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 119638096 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 119643188 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 119633106 mitochondrial import receptor subunit TOM70 isoform X1 K17768 TOM70; mitochondrial import receptor subunit TOM70
C TOB/SAM complex
D 119639695 LOW QUALITY PROTEIN: SAM50-like protein CG7639 K07277 SAM50; outer membrane protein insertion porin family
C MIM complex
C Porin
D 119633841 voltage-dependent anion-selective channel K15040 VDAC2; voltage-dependent anion channel protein 2
C Other outer membrane factor
D 119631913 metaxin-2 isoform X1 K17776 MTX; metaxin
D 119635274 metaxin-2-like K17776 MTX; metaxin
D 119642771 metaxin-1 homolog isoform X1 K17776 MTX; metaxin
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 119637202 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 119635651 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 119638971 mitochondrial import inner membrane translocase subunit Tim10B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 119644199 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 119635419 mitochondrial import inner membrane translocase subunit Tim13-like K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
D 119637511 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 119640827 mitochondrial intermembrane space import and assembly protein 40-B K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 119642275 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 119634869 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 119632581 MICOS complex subunit MIC13 homolog QIL1 K24624 MICOS13; MICOS complex subunit MIC13
D 119634975 uncharacterized protein LOC119634975 K17563 CHCHD3; MICOS complex subunit MIC19
D 119641491 MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 119634869 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 119634573 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 119633672 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 119640801 mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 119633710 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 119641481 mitochondrial import inner membrane translocase subunit TIM50-C-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 119632234 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 119633283 calcium uptake protein 1 homolog, mitochondrial-like isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 119636411 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
C Other inner membrane factors
D 119633487 mitochondrial proton/calcium exchanger protein K17800 LETM1; mitochondrial proton/calcium exchanger protein
D 119643367 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 119636918 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 119632308 uncharacterized protein LOC119632308 K18157 TMEM126A; transmembrane protein 126A
D 119641823 mitochondrial pyruvate carrier 1-like K22138 MPC1; mitochondrial pyruvate carrier 1
D 119641828 mitochondrial pyruvate carrier 1-like K22138 MPC1; mitochondrial pyruvate carrier 1
D 119639117 mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 119636073 OCIA domain-containing protein 1 K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 119638824 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 119635959 LOW QUALITY PROTEIN: heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 119636616 grpE protein homolog, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 119632120 mitochondrial import inner membrane translocase subunit TIM14 isoform X1 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 119639655 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 119636897 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 119634931 mitochondrial-processing peptidase subunit beta-like K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 119638736 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 119638621 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 119638636 heat shock protein 60A K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 119642924 heat shock protein 60A-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 119631500 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 119634112 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 119636184 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 119643596 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 119635979 protein tumorous imaginal discs, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 119638738 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 119633707 uncharacterized protein LOC119633707 K17808 ZIM17; mitochondrial protein import protein ZIM17
D 119644267 DNL-type zinc finger protein-like K17808 ZIM17; mitochondrial protein import protein ZIM17
D 119636809 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 119642772 polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 119644812 cyclic AMP response element-binding protein B isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 119633822 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 119639427 LOW QUALITY PROTEIN: ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 119632256 polycomb protein PHO K09201 YY; transcription factor YY
D 119643757 polycomb protein PHO isoform X1 K09201 YY; transcription factor YY
D 119645351 probable serine/threonine-protein kinase DDB_G0286465 K09454 GABPB; GA-binding protein transcription factor, beta
D 119638748 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 119644678 DNA-binding protein Ewg isoform X1 K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 119633572 histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 119640374 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 119639526 LOW QUALITY PROTEIN: iron-sulfur cluster assembly scaffold protein IscU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 119634139 protein bcn92 K22069 LYRM4; LYR motif-containing protein 4
D 119637383 frataxin homolog, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 119632108 adrenodoxin-like protein 2, mitochondrial isoform X1 K22070 FDX1; ferredoxin-1, mitochondrial
D 119632027 adrenodoxin-like protein 1, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 119641541 NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 119635959 LOW QUALITY PROTEIN: heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 119645125 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 119639525 nucleotide exchange factor Sil1 K14001 SIL1; nucleotide exchange factor SIL1
D 119633497 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 119637107 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 119641480 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 119634691 putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 119637360 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 119634808 bolA-like protein DDB_G0274169 K22066 BOLA1; BolA-like protein 1
D 119636784 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 119638891 sideroflexin-1-3 K23500 SFXN1_3; sideroflexin-1/3
D 119632690 sideroflexin-2 K23501 SFXN2; sideroflexin-2
C Other regulator of mitochondrial biogenesis
D 119638648 LOW QUALITY PROTEIN: carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 119634454 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 119637343 F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 119632420 host cell factor-like isoform X1 K14966 HCFC1; host cell factor 1
D 119643653 host cell factor isoform X1 K14966 HCFC1; host cell factor 1
D 119634383 uncharacterized protein LOC119634383 isoform X1 K04533 HD; huntingtin
D 119643303 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 119645384 lon protease homolog, mitochondrial isoform X1 K08675 LONP1; ATP-dependent Lon protease [EC:3.4.21.53]
D 119635485 NAD-dependent histone deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 119635252 protein SERAC1 K23504 SERAC1; protein SERAC1
D 119638449 uncharacterized protein LOC119638449 isoform X1 K23504 SERAC1; protein SERAC1
D 119639985 protein UXT K26537 UXT; protein UXT
D 119632926 transport and Golgi organization protein 2 isoform X1 K28098 TANGO2; transport and Golgi organization protein 2
D 119634535 putative uncharacterized protein DDB_G0271606 isoform X1 K28271 C2ORF69; mitochondrial protein C2orf69
D 119641574 uncharacterized protein LOC119641574 K28528 ATOS; protein Atossa
D 119633365 probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7]
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 119634674 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 119633188 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 119640240 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 119640112 protein NDUFAF4 homolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 119636373 arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 119637794 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 homolog isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 119642783 protein arginine methyltransferase NDUFAF7 homolog, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 119635769 uncharacterized protein LOC119635769 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 119634835 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 119643497 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 119633836 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 119633387 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 119634717 RPII140-upstream gene protein isoform X1 K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 119641371 succinate dehydrogenase assembly factor 2-B, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 119642971 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 119633439 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 119639194 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 119645253 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
C Complex-IV assembly factors
D 119635312 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 119638798 COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 119635747 uncharacterized protein LOC119635747 K18173 COA1; cytochrome c oxidase assembly factor 1
D 119644159 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 119636401 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 119636656 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 119637153 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 119641795 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7
D 119633460 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 119645309 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 119641208 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 119641840 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 119641814 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 119631841 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 119641205 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 119641989 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 119631992 uncharacterized protein LOC119631992 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 119636233 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 119635357 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 119631633 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 119631744 SURF1-like protein K14998 SURF1; surfeit locus 1 family protein
D 119632776 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 119633620 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 119643491 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 119640446 COA8 family protein CG14806, mitochondrial K23506 APOPT1; apoptogenic protein 1
D 119636494 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
D 119638494 HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 119640050 HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial
C Complex-V assembly factors
D 119635003 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 119633795 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 119638849 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 119642353 ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 119636300 transmembrane GTPase Marf-like K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 119639349 transmembrane GTPase Marf isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 119635950 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 119634976 putative OPA3-like protein CG13603 K23166 OPA3; optic atrophy 3 protein
D 119634988 putative OPA3-like protein CG13603 K23166 OPA3; optic atrophy 3 protein
D 119638257 TP53-regulated inhibitor of apoptosis 1-like K17968 TRIAP1; TRIAP1/MDM35 family protein
D 119636632 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 119633687 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 119640606 mitochondrial fission 1 protein isoform X1 K17969 FIS1; mitochondrial fission 1 protein
D 119640237 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 119641855 endophilin-B1 K11248 SH3GLB1; endophilin-B1
D 119631710 mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier
D 119636769 transport and Golgi organization protein 11 isoform X1 K22076 MFF; mitochondrial fission factor
D 119631352 ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 119631984 mitochondrial cardiolipin hydrolase-like isoform X1 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 119633681 mitochondrial cardiolipin hydrolase-like K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 119641847 mitochondrial cardiolipin hydrolase-like K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 119643766 mitoguardin K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 119631241 actin-5C K05692 ACTB_G1; actin beta/gamma 1
D 119634396 actin-87E K05692 ACTB_G1; actin beta/gamma 1
D 119636123 actin-57B K05692 ACTB_G1; actin beta/gamma 1
D 119639662 actin, indirect flight muscle K05692 ACTB_G1; actin beta/gamma 1
D 119644028 actin-85C-like K05692 ACTB_G1; actin beta/gamma 1
D 119639893 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 119639428 phagocyte signaling-impaired protein K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 119632930 protein l(2)37Cc K17080 PHB1; prohibitin 1
D 119635695 prohibitin-2 isoform X1 K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 119633687 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 119636288 unconventional myosin-Va K10357 MYO5; myosin V
C Morphogenesis factors
D 119637571 sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 119641564 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 119634869 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 119633308 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 119641569 uncharacterized protein LOC119641569 K29121 MISO1; mitochondrial inner membrane subdomain organizer 1
D 119637340 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 119645362 E3 ubiquitin-protein ligase Nedd-4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 119637504 protein misato isoform X1 K27320 MSTO1; protein misato
D 119636742 protein preli-like K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 119644354 protein slowmo-like K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
D 119644356 protein slowmo-like K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
D 119633767 TM2 domain-containing protein almondex K28688 TM2D3; TM2 domain-containing protein 3
B Mitophagy factors
C Autophagy-related proteins
D 119639226 autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2
D 119631425 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 119633262 cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 119635025 cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 119644626 autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 119641980 beclin-1-like protein K08334 BECN; beclin
D 119642209 ubiquitin-like modifier-activating enzyme atg7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 119636169 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 119641898 gamma-aminobutyric acid receptor-associated protein-like K08341 GABARAP; GABA(A) receptor-associated protein
D 119644784 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 119641272 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 119631733 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12
D 119635026 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 119641991 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 119633802 WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
D 119637782 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 119640411 E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 119632181 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 119638502 protein CLEC16A homolog isoform X1 K19513 CLEC16A; protein CLEC16A
D 119636632 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
C Parkin-independent mechanism factors
D 119638780 autophagy-related protein 13 homolog K08331 ATG13; autophagy-related protein 13
D 119632695 serine/threonine-protein kinase unc-51 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 119639152 RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 119633304 heat shock protein 83-like K04079 HSP90A; molecular chaperone HtpG
D 119644345 heat shock protein 83-like K04079 HSP90A; molecular chaperone HtpG
D 119644351 heat shock protein 83-like K04079 HSP90A; molecular chaperone HtpG
D 119645375 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG
D 119645149 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 119633491 E3 ubiquitin-protein ligase Smurf1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 119633913 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 119643303 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 119631742 tectonin beta-propeller repeat-containing protein K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 119643550 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 119631834 bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 119631277 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 119634531 protein C19orf12 homolog K23168 MPAN; protein MPAN
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: July 24, 2026