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Mitochondrial Biogenesis - Hydra vulgaris (swiftwater hydra)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 6904241 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 6904228 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 6904242 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 6904238 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 6904239 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 6904230 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 6904236 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 6904240 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 6904237 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 6904233 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 6904224 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 100201150 DNA-directed RNA polymerase, mitochondrial-like K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 100199740 HMG box-containing protein 5 K11830 TFAM; transcription factor A, mitochondrial
D 100201215 dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 100214574 translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 100202023 elongation factor Tu K02358 tuf; elongation factor Tu
D 100210106 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 100215429 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 100202384 translation factor GUF1 homolog, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 100200523 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 100205391 ribonuclease P protein subunit p29-like K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 100210147 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 100210676 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 100199633 mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 100210577 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 101239296 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 100198494 AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 100214622 AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 100210240 mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 100212802 endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 105843221 ADP,ATP carrier protein 3, mitochondrial K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 100198773 mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 100203338 GTPase Era, mitochondrial K03595 era; GTPase
D 100204641 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 100211075 leucine--tRNA ligase, cytoplasmic-like K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 100210444 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 100214624 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 100204657 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 101239907 mitochondrial ribosome-associated GTPase 1 isoform X1 K19828 MTG1; mitochondrial GTPase 1
D 100199504 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 100206182 mitochondrial RNA pseudouridine synthase RPUSD4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 100204383 mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 105843932 uncharacterized protein LOC105843932 K23499 RMND1; required for meiotic nuclear division protein 1
D 100215306 MYG1 exonuclease isoform X1 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 100211228 DNA polymerase subunit gamma-1-like K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 100207697 DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 100206816 nuclease EXOG, mitochondrial-like K15050 EXOG; nuclease EXOG, mitochondrial
D 100209293 twinkle mtDNA helicase K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 100203838 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 100206110 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 100214489 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 100200293 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 100208430 ATPase family AAA domain-containing protein 3-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 100200583 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 100207557 mitochondrial Rho GTPase 1-A-like K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 100202286 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 100203304 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 105844776 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124807918 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124807919 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124807971 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124807972 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124816626 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124816818 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 100201756 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 100202953 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 100213621 mitochondrial import receptor subunit TOM22 homolog isoform X1 K17769 TOM22; mitochondrial import receptor subunit TOM22
D 100199772 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 100204386 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
C TOB/SAM complex
C Porin
D 100207044 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
C ERMES complex
C Other outer membrane factor
D 101241678 metaxin-1 isoform X1 K17776 MTX; metaxin
D 100203408 mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 100209469 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
C TIM8/13 complex
D 101241048 mitochondrial import inner membrane translocase subunit Tim13-B K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 100203461 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 100205059 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 100200802 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 100206504 MICOS complex subunit MIC19 K17563 CHCHD3; MICOS complex subunit MIC19
D 100213200 uncharacterized protein LOC100213200 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 100200802 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 100204116 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 100212978 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 100204864 mitochondrial import inner membrane translocase subunit Tim17-A isoform X1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 100200458 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 100214829 mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 100206887 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 100200728 calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial
C Other inner membrane factors
D 100199336 mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 100207849 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 100211733 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 101238598 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 100201845 mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 100215990 OCIA domain-containing protein 1 K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 100212434 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 100201403 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 100199526 grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 100211445 dnaJ homolog subfamily C member 15 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 105845113 mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
D 100212861 presequence translocated-associated motor subunit pam17, mitochondrial K17806 PAM17; mitochondrial import inner membrane translocase subunit TIM23
C Other matrix factors
D 100207790 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 100203118 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 100209426 heat shock protein 60A K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 100205882 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 100211135 dnaJ homolog subfamily A member 3, mitochondrial isoform X2 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 100209883 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 101235461 uncharacterized protein LOC101235461 isoform X1 K17808 ZIM17; mitochondrial protein import protein ZIM17
D 100205916 persulfide dioxygenase ETHE1 homolog, mitochondrial-like K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 100211012 polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 100200223 cyclic AMP-responsive element-binding protein K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 100210106 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 101234786 uncharacterized protein LOC101234786 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 100199740 HMG box-containing protein 5 K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 100204750 DNA-binding protein P3A2 isoform X2 K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 101240388 CREB-regulated transcription coactivator 3 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 100203474 histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 100211782 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 100212947 iron-sulfur cluster assembly scaffold protein IscU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 100211504 frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1]
D 100206921 ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 100200068 NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 100201403 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 101239636 iron-sulfur cluster co-chaperone protein HscB-like K04082 hscB; molecular chaperone HscB
D 100207222 nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 100212558 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 100201724 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 100205979 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 105843432 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 100208943 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 100200883 bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 100209632 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 100212840 sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2
D 100206719 sideroflexin-5 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 100206022 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 100212546 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 100204465 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial isoform X1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 100204514 host cell factor 2 K14966 HCFC1; host cell factor 1
D 101237115 huntingtin K04533 HD; huntingtin
D 101238049 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 100213990 lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 100210841 NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 100203890 protein SERAC1 K23504 SERAC1; protein SERAC1
D 100209830 protein UXT homolog K26537 UXT; protein UXT
D 100197503 ES1 protein homolog, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 100212946 transport and Golgi organization protein 2 homolog K28098 TANGO2; transport and Golgi organization protein 2
D 100199411 mitochondrial protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69
D 100207864 protein FAM214A K28528 ATOS; protein Atossa
D 100197156 probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7]
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 100201539 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 101239048 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 isoform X1 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 100207857 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 100210831 arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 100202861 protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 100198387 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 100205616 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 100202827 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 100201008 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 100203452 succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 100204808 tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 100211491 mitochondrial zinc maintenance protein 1, mitochondrial-like K18170 LYRM7; complex III assembly factor LYRM7
D 101239296 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 100200583 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
C Complex-IV assembly factors
D 101239643 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 100201700 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 101240379 cytochrome c oxidase assembly factor 5 isoform X2 K18178 COA5; cytochrome c oxidase assembly factor 5
D 100208691 protoheme IX farnesyltransferase, mitochondrial isoform X1 K02257 COX10; heme o synthase [EC:2.5.1.141]
D 105844949 cytochrome c oxidase assembly protein COX11, mitochondrial isoform X1 K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 100207442 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 100201939 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 100211968 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 100213538 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 100198802 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 100204646 probable transcriptional regulatory protein Nther_1800 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 100211364 transmembrane protein 223 isoform X1 K27342 TMEM223; transmembrane protein 223
D 124813410 HIG1 domain family member 1A, mitochondrial-like K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 100203263 HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial
C Complex-V assembly factors
D 100197798 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 101241264 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 101237803 uncharacterized protein LOC101237803 K17966 TMEM70; transmembrane protein 70, mitochondrial
B Mitochondrial dynamics
C Fission and Fusion factors
D 100205666 mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 100207782 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 100213638 optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 100197728 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 100208613 bcl-2 homologous antagonist/killer-like K14021 BAK; Bcl-2 homologous antagonist/killer
D 100212122 uncharacterized protein LOC100212122 K14021 BAK; Bcl-2 homologous antagonist/killer
D 100199542 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 100202650 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 100203138 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 100203439 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 100215691 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 100200342 mitochondrial fission 1 protein isoform X3 K17969 FIS1; mitochondrial fission 1 protein
D 100209666 small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 101235331 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier
D 100209424 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
C Actin cytoskeleton organization
D 100202036 actin, non-muscle 6.2 K05692 ACTB_G1; actin beta/gamma 1
D 100206987 actin, non-muscle 6.2-like K05692 ACTB_G1; actin beta/gamma 1
D 100209935 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 100212478 N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 100202865 prohibitin 1 K17080 PHB1; prohibitin 1
D 100209842 prohibitin-2-like K17081 PHB2; prohibitin 2
D 100214520 prohibitin-2-like K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 100215691 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 100205824 unconventional myosin-Va K10357 MYO5; myosin V
C Morphogenesis factors
D 101239002 sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 100207557 mitochondrial Rho GTPase 1-A-like K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 100200802 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 100204145 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 100208619 E3 ubiquitin-protein ligase NEDD4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 100208133 protein misato homolog 1 K27320 MSTO1; protein misato
D 100204307 PRELI domain-containing protein 1, mitochondrial K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 101239803 PRELI domain containing protein 3A K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 100213404 autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 100200108 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 100207318 cysteine protease atg4da isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 100210994 cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 100214492 autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 100205250 beclin-1 K08334 BECN; beclin
D 100201900 ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 100198377 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 100215460 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 100207320 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 100214812 ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 100211206 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12
D 100211848 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 100198344 WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 101237967 E3 ubiquitin-protein ligase parkin-like isoform X1 K04556 PARK2; parkin [EC:2.3.2.31]
D 100212713 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 101236092 protein CLEC16A-like K19513 CLEC16A; protein CLEC16A
D 100197728 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 100211305 sequestosome-1 K14381 SQSTM1; sequestosome 1
D 100199635 activating molecule in BECN1-regulated autophagy protein 1B K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 105846112 autophagy-related protein 13 homolog K08331 ATG13; autophagy-related protein 13
D 100212126 serine/threonine-protein kinase unc-51 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 101240051 RB1-inducible coiled-coil protein 1-like isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 100199389 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 101235897 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 100214820 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 100213637 E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
C Other mitophagy factors
D 101238049 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 100204686 microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 101237722 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 100206706 protein PF3D7_1417600 K17987 NBR1; next to BRCA1 gene 1 protein
D 100209515 tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 100207485 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 100209839 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 100198066 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 100206457 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 105845105 protein C19orf12 homolog K23168 MPAN; protein MPAN
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025