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  Mitochondrial Biogenesis - Ischnura elegans (blue-tailed damselfly)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I C Mitochondrial respiratory chain complex III C Cytochrome c oxidase C F-type ATPase B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 124164098 DNA-directed RNA polymerase, mitochondrial-like K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] D 124171687 DNA-directed RNA polymerase, mitochondrial-like isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 124170942 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172149 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172152 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172246 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172291 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172299 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial D 124172337 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172630 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124163558 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 124167847 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 124168074 translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 124161843 translation initiation factor IF-3 K02520 infC; translation initiation factor IF-3 D 124169756 elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts D 124166544 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 124169813 elongation factor Tu K02358 tuf; elongation factor Tu D 124167729 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 124167843 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 124157975 transcription termination factor 4, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein D 124166617 transcription termination factor 5, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 124167589 transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 124168073 transcription termination factor, mitochondrial-like isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 124168279 transcription termination factor, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein D 124162883 translation factor GUF1 homolog, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 124154052 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 124156508 ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 124168185 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 124155492 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 124163617 ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 124159052 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 124169579 ribonuclease P protein subunit p40-like K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 124159381 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 124162942 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 124154432 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 124169742 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 124169393 pentatricopeptide repeat-containing protein 2, mitochondrial-like K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 124155739 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 124164347 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 124161550 putative ATPase N2B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 124157865 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 124153617 ATP-dependent RNA helicase SUV3 homolog, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 124167514 endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 124159500 ADP,ATP carrier protein 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 124169187 ADP,ATP carrier protein-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 124154238 mitoferrin-1-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 124155898 mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 124156376 GTPase Era, mitochondrial K03595 era; GTPase D 124160993 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 124169797 tyrosine--tRNA ligase, mitochondrial isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 124156541 probable leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 124159515 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 124169216 aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 124163203 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 124162021 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 124165483 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 124160996 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 124159143 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 124165126 poly(A) RNA polymerase, mitochondrial-like K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 124166135 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 124168640 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 124156115 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 124170780 5-methylcytosine rRNA methyltransferase NSUN4 isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 124166386 mitochondrial mRNA pseudouridine synthase RPUSD3-like K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 124154294 RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein D 124166852 uncharacterized protein LOC124166852 isoform X1 K23496 NGRN; neugrin D 124165060 mitochondrial mRNA pseudouridine synthase Trub2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 124161946 FAST kinase domain-containing protein 1, mitochondrial isoform X1 K27754 FASTKD1; FAST kinase domain-containing protein 1 D 124163276 FAST kinase domain-containing protein 3, mitochondrial-like K27755 FASTKD3; FAST kinase domain-containing protein 3 D 124162849 uncharacterized protein LOC124162849 K27757 FASTKD5; FAST kinase domain-containing protein 5 D 124159436 mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor D 124156581 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 124168242 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 124170559 MYG1 protein C27H6.8 isoform X1 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 124169517 mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 124159101 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 124168174 DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2 D 124155455 DNA-directed primase/polymerase protein-like K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 124165436 endonuclease G, mitochondrial isoform X1 K01173 ENDOG; endonuclease G, mitochondrial D 124154740 mitochondrial genome maintenance exonuclease 1-like K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 124158634 mitochondrial DNA helicase K17680 PEO1; twinkle protein [EC:5.6.2.3] D 124164268 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 124161878 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 124163656 ATPase family AAA domain-containing protein 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 124168243 ubiquinol-cytochrome-c reductase complex assembly factor 2 isoform X1 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 124155493 dnaJ homolog subfamily A member 2-like K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 124165385 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 124159201 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 124158973 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 124166564 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 124166846 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 124169080 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 124154683 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 124157168 mitochondrial import receptor subunit TOM70 isoform X1 K17768 TOM70; mitochondrial import receptor subunit TOM70 C TOB/SAM complex D 124153336 sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family C Porin D 124153478 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2 D 124163024 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2 D 124171898 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2 C ERMES complex C Other outer membrane factor D 124165779 metaxin-2-like K17776 MTX; metaxin D 124166518 metaxin-1 K17776 MTX; metaxin D 124157812 mitochondrial amidoxime reducing component 2-like isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] D 124162608 mitochondrial amidoxime reducing component 2-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 124153378 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 124156623 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 C TIM8/13 complex D 124162376 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 124160619 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 124167713 mitochondrial intermembrane space import and assembly protein 40-B K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 124165811 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 124158541 MICOS complex subunit Mic10-like isoform X1 K17784 MICOS10; MICOS complex subunit MIC10 D 124154324 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 124160605 MICOS complex subunit MIC19 K17563 CHCHD3; MICOS complex subunit MIC19 D 124160928 MICOS complex subunit MIC26 isoform X1 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 124158541 MICOS complex subunit Mic10-like isoform X1 K17784 MICOS10; MICOS complex subunit MIC10 D 124154324 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 124155089 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 124160630 mitochondrial import inner membrane translocase subunit Tim23 isoform X1 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 124158713 mitochondrial import inner membrane translocase subunit Tim17-B-like K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 124155581 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 124168235 mitochondrial import inner membrane translocase subunit TIM50-C-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 124160142 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 124161128 calcium uptake protein 1 homolog, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 124164904 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial C Other inner membrane factors D 124156298 mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 124162089 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 124163882 uncharacterized protein LOC124163882 K18157 TMEM126A; transmembrane protein 126A D 124161203 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 124169808 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2 D 124159497 OCIA domain-containing protein 1 K28215 OCIAD1; OCIA domain-containing protein 1 B Matrix C MMC/PAM proteins D 124154715 mitochondrial import inner membrane translocase subunit TIM44 isoform X1 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 124156262 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 124155367 grpE protein homolog 1, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE D 124160757 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 124164079 mitochondrial import inner membrane translocase subunit Tim16-like K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 124169097 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 124166623 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 124153771 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 124164385 heat shock protein 60A K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 124164388 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 124161842 protein tumorous imaginal discs, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 124160217 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 124153804 persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 124155447 polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 124167729 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 124167843 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 124153410 transcriptional repressor protein YY1-like K09201 YY; transcription factor YY D 124172741 GA-binding protein subunit beta-1-like isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 124170942 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172149 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172152 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172246 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172291 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172299 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial D 124172337 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 124172630 transcription factor A, mitochondrial-like isoform X1 K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 124157905 DNA-binding protein P3A2-like isoform X1 K11831 NRF1; nuclear respiratory factor 1 C Coactivators D 124162015 histone acetyltransferase p300-like isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 124169684 cysteine desulfurase, mitochondrial-like K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 124169360 iron-sulfur cluster assembly scaffold protein IscU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 124155903 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 124160465 frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 124169469 adrenodoxin-like protein 2, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 124169450 adrenodoxin-like protein 1, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 124173542 NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 124156262 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 124165733 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB D 124153587 nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1 D 124154706 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 124167363 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 124168285 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 124168501 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 124168898 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 124160082 putative bolA-like protein K11H12.1 isoform X1 K22066 BOLA1; BolA-like protein 1 D 124155008 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 124154741 sideroflexin-1 isoform X1 K23500 SFXN1_3; sideroflexin-1/3 D 124155720 sideroflexin-2 K23501 SFXN2; sideroflexin-2 C Other regulator of mitochondrial biogenesis D 124159045 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 124172124 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 124167760 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 124158471 F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 124171767 host cell factor-like isoform X1 K14966 HCFC1; host cell factor 1 D 124153929 huntingtin isoform X1 K04533 HD; huntingtin D 124171888 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 124163093 lon protease homolog, mitochondrial isoform X1 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 124160811 NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 124155889 protein SERAC1 K23504 SERAC1; protein SERAC1 D 124155891 uncharacterized protein LOC124155891 K23504 SERAC1; protein SERAC1 D 124153891 protein UXT homolog K26537 UXT; protein UXT D 124156008 glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 124155974 transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2 D 124164571 uncharacterized protein LOC124164571 isoform X1 K28271 C2ORF69; mitochondrial protein C2orf69 D 124165983 uncharacterized protein LOC124165983 K28528 ATOS; protein Atossa D 124160214 probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7] B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 124168194 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 124168877 uncharacterized protein LOC124168877 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 124168206 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 124153741 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 124171850 protein NDUFAF4 homolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 124154008 arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 124155439 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 124157557 protein arginine methyltransferase NDUFAF7 homolog, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 124160438 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 124168943 complex I assembly factor ACAD9, mitochondrial-like isoform X1 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 124169788 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 124165516 FAD-dependent oxidoreductase domain-containing protein 1-like K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 124155372 reticulon-4-interacting protein 1 homolog, mitochondrial-like isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 124160997 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 124168696 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 124162638 succinate dehydrogenase assembly factor 2, mitochondrial-like K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 124160872 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 124165612 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 124159556 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 124164347 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 124168243 ubiquinol-cytochrome-c reductase complex assembly factor 2 isoform X1 K17682 MNF1; mitochondrial nucleoid factor 1 D 124162053 uncharacterized protein LOC124162053 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 124167716 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 C Complex-IV assembly factors D 124164200 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 124166016 uncharacterized protein LOC124166016 K18173 COA1; cytochrome c oxidase assembly factor 1 D 124163559 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 124154170 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 124154493 cytochrome c oxidase assembly factor 6 homolog isoform X1 K18179 COA6; cytochrome c oxidase assembly factor 6 D 124166875 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7 D 124168814 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 124165611 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 124155578 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 124166990 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 124165238 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 124168019 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18 D 124168804 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 124157961 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 124169354 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 124159001 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 124157261 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 124163301 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 124157829 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 124157749 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 124159103 COA8 family protein CG14806, mitochondrial K23506 APOPT1; apoptogenic protein 1 D 124167716 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 124163482 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 D 124161255 HIG1 domain family member 1C-like isoform X1 K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 124159165 HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial C Complex-V assembly factors D 124170610 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 124168228 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 124159009 transmembrane protein 70 homolog, mitochondrial isoform X1 K17966 TMEM70; transmembrane protein 70, mitochondrial D 124165817 ATP synthase membrane subunit K, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 124159099 transmembrane GTPase Marf isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 124163480 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 124167970 putative OPA3-like protein CG13603 isoform X1 K23166 OPA3; optic atrophy 3 protein D 124158932 TP53-regulated inhibitor of apoptosis 1-like K17968 TRIAP1; TRIAP1/MDM35 family protein D 124161543 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 124170636 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 124167810 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 124158501 small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier D 124158781 small ubiquitin-related modifier-like K12160 SUMO; small ubiquitin-related modifier D 124171739 small ubiquitin-related modifier-like K12160 SUMO; small ubiquitin-related modifier D 124171859 small ubiquitin-related modifier 4-like K12160 SUMO; small ubiquitin-related modifier D 124166128 endophilin-B2 isoform X1 K11248 SH3GLB1; endophilin-B1 D 124158450 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier D 124160641 transport and Golgi organization protein 11 K22076 MFF; mitochondrial fission factor D 124164038 ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 124165565 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 124164919 mitoguardin K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 124163247 actin-5C-like K05692 ACTB_G1; actin beta/gamma 1 D 124163453 actin-5C-like K05692 ACTB_G1; actin beta/gamma 1 D 124171710 actin-5C K05692 ACTB_G1; actin beta/gamma 1 D 124171878 actin, muscle K05692 ACTB_G1; actin beta/gamma 1 D 124154495 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 124155815 N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 124156572 protein l(2)37Cc K17080 PHB1; prohibitin 1 D 124157689 prohibitin-2 K17081 PHB2; prohibitin 2 C Retention of mitochondria D 124170636 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 124169801 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V C Morphogenesis factors D 124161861 sorting nexin-25 K17887 SNX25; sorting nexin-25 D 124165385 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 124154324 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 124155381 mitochondrial fission process protein 1 isoform X1 K17981 MTFP1; mitochondrial fission process protein 1 D 124169589 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 124166094 E3 ubiquitin-protein ligase Nedd-4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 124169438 protein misato homolog 1 K27320 MSTO1; protein misato D 124155364 protein preli-like K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial D 124156328 protein slowmo isoform X1 K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial B Mitophagy factors C Autophagy-related proteins D 124167906 autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2 D 124167950 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 124168118 cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 124171033 cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 124169255 autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 124167766 beclin-1-like protein K08334 BECN; beclin D 124172868 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 124157863 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 124164580 autophagy-related protein 9A isoform X1 K17907 ATG9; autophagy-related protein 9 D 124158635 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 124162006 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12 D 124167780 beclin 1-associated autophagy-related key regulator isoform X1 K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 124164363 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 124159725 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 124160138 E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31] D 124162989 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 124159146 protein CLEC16A homolog isoform X1 K19513 CLEC16A; protein CLEC16A D 124161543 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 124169050 tax1-binding protein 1 homolog B-like K21347 TAX1BP1; Tax1-binding protein 1 C Parkin-independent mechanism factors D 124158947 autophagy-related protein 13 homolog isoform X1 K08331 ATG13; autophagy-related protein 13 D 124158678 serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 124165084 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 124158499 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG D 124168413 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 124159667 E3 ubiquitin-protein ligase SMURF1-like isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 124154050 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 124171888 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 124169184 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 124171002 microtubule-associated proteins 1A/1B light chain 3B-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 124161467 tectonin beta-propeller repeat-containing protein K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 124154427 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 124161923 bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 124157327 85/88 kDa calcium-independent phospholipase A2-like K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 124161489 uncharacterized protein LOC124161489 K23168 MPAN; protein MPAN ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025