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Mitochondrial Biogenesis - Ictalurus furcatus (blue catfish)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 26118477 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 26118480 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 26118489 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 26118468 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 26118490 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 26118493 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 26118470 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 26118494 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 26118485 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 26118487 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 26118465 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 26118488 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 26118464 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 128613598 polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 128616550 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 128612306 tfb1m; dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 128612929 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 128606524 mtif2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 128603692 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 128614799 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 128615579 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 128603537 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 128624011 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 128606610 mterf2; transcription termination factor 2, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 128618637 transcription termination factor 1, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 128624510 mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 128611205 guf1; translation factor Guf1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 128599724 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 128602948 pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 128607346 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 128616983 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 128610201 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 128599721 rpp25l; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 128607186 rpp25b; ribonuclease P protein subunit p25b K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 128599444 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 128623854 rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 128601920 trmt10c; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 128619628 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 128612719 prorp; mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 128615620 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 128615635 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 128615806 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 128602381 ptcd1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 128603700 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 128611149 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 128610395 dhx30; ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 128614986 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 128612682 afg1la; AFG1 like ATPase a K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 128623626 atp23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 128605929 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 128624205 lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 128603577 si:dkey-251i10.1; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 128604196 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 128608764 slc25a6; ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 128611181 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 128616143 ADP/ATP translocase 1-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 128605611 slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 128607450 slc25a37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 128615864 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 128603779 eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 128600241 yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 128618198 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 128613218 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 128622375 lars1b; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 128599888 gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 128622022 rars1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 128612711 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 128604131 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 128598919 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 128616617 mtpap; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 128625129 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 128605898 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 128624197 noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 128602332 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 128624488 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 128625138 rpusd4; pseudouridylate synthase RPUSD4, mitochondrial K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 128603495 rcc1l; RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 128607912 ngrn; neugrin K23496 NGRN; neugrin
D 128614913 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 128609000 fastkd1; FAST kinase domain-containing protein 1, mitochondrial K27754 FASTKD1; FAST kinase domain-containing protein 1
D 128601773 fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 128609875 fastkd3; FAST kinase domain-containing protein 3, mitochondrial K27755 FASTKD3; FAST kinase domain-containing protein 3
D 128599499 tbrg4; FAST kinase domain-containing protein 4 K27756 TBRG4; FAST kinase domain-containing protein 4
D 128603384 FAST kinase domain-containing protein 5, mitochondrial K27757 FASTKD5; FAST kinase domain-containing protein 5
D 128598949 mtrfr; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 128613233 rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 128625684 grsf1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1
D 128602739 mettl15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 128624893 myg1; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 128605099 mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 128618273 polg; DNA polymerase subunit gamma-1 isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 128616127 polg2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2
D 128604137 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 128608118 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 128605340 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 128614022 nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial
D 128616513 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 128624383 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 128623124 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 128614904 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 128617383 si:dkey-21c1.4; uncharacterized protein si:dkey-21c1.4 K27759 MTNAP1; mitochondrial nucleoid-associated protein 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 128602703 dnaja2a; dnaJ homolog subfamily A member 2a K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 128606372 dnaja2b; dnaJ homolog subfamily A member 2b K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 128615069 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 128600324 rhot1a; mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 128615992 rhot1b; mitochondrial Rho GTPase 1b isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 128602025 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 128602031 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 128602036 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 128620237 hspa8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 128621106 hspa8b; heat shock protein family A (Hsp70) member 8b K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 128621142 hsc70; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 128606137 aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
D 128611126 aryl-hydrocarbon-interacting protein-like 1 isoform X1 K17767 AIP; AH receptor-interacting protein
D 128621340 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 128621981 mitochondrial fission factor-like isoform X1 K28235 FATE1; fetal and adult testis-expressed transcript protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 128612074 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
D 128614905 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 128600638 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 128614207 tomm20b; mitochondrial import receptor subunit TOM20 homolog B K17770 TOM20; mitochondrial import receptor subunit TOM20
D 128616888 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 128603185 si:dkey-71l1.1; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 128606052 tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 128616168 tomm40l; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 128614694 tomm70a; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
C TOB/SAM complex
D 128611603 samm50; sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family
D 128623649 samm50l; sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 128605539 vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 128616863 voltage-dependent anion-selective channel protein 2-like isoform X1 K15040 VDAC2; voltage-dependent anion channel protein 2
D 128620496 zgc:56235; voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 128609678 mtx1a; metaxin-1a isoform X1 K17776 MTX; metaxin
D 128616096 mtx1b; metaxin-1b isoform X1 K17776 MTX; metaxin
D 128616160 mtx2; metaxin-2 K17776 MTX; metaxin
D 128625710 mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 128603519 unconventional myosin-XIX K25838 MYO19; myosin XIX
D 128613065 marc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 128612660 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 128605992 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 128620769 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 128603380 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 128611689 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A isoform X1 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 128613578 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 128625241 chchd4a; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 128600377 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 128619372 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 128611148 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 128613718 micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 128617827 chchd3b; coiled-coil-helix-coiled-coil-helix domain containing 3b K17563 CHCHD3; MICOS complex subunit MIC19
D 128622994 chchd3a; coiled-coil-helix-coiled-coil-helix domain containing 3a isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 128614646 chchd6b; coiled-coil-helix-coiled-coil-helix domain containing 6b K17564 CHCHD6; MICOS complex subunit MIC25
D 128599954 apoob; apolipoprotein O, b isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 128603832 apooa; apolipoprotein O, a isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 128603512 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
D 128611056 MICOS complex subunit MIC27-like K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 128619372 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 128611148 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 128603573 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 128605052 timm23b; mitochondrial import inner membrane translocase subunit Tim23B K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 128616570 timm23a; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 128607469 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 128625166 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 128600013 timm21; mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 128621355 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 128605240 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 128605238 micu1; calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial
D 128603553 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 128606019 calcium uniporter protein, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 128616025 smdt1b; single-pass membrane protein with aspartate-rich tail 1b K22830 SMDT1; essential MCU regulator, mitochondrial
D 128609616 mcur1; mitochondrial calcium uniporter regulator 1 isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 128605480 letm1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 128613619 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 128611590 immp2l; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 128620249 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 128604142 mpc1; LOW QUALITY PROTEIN: mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 128608793 mpc2b; mitochondrial pyruvate carrier 2b K22139 MPC2; mitochondrial pyruvate carrier 2
D 128621950 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
D 128604244 OCIA domain-containing protein 1-like K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 128614103 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 128611103 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 128610520 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 128622507 grpel2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 128613559 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
C Other matrix factors
D 128625667 pmpca; mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 128617940 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 128621209 mipepa; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 128609224 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 128603010 dnaja3b; dnaJ heat shock protein family (Hsp40) member A3b K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 128625037 dnaja3a; dnaJ heat shock protein family (Hsp40) member A3a isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 128625378 tamm41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 128622652 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 128603405 poldip2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 128602106 creb1a; cyclic AMP-responsive element-binding protein 1a K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 128608729 creb1b; cyclic AMP-responsive element-binding protein 1b K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 128603537 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 128624011 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 128624771 sp1; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 128601038 yy1b; transcriptional repressor protein YY1b isoform X1 K09201 YY; transcription factor YY
D 128613177 yy1a; transcriptional repressor protein YY1a K09201 YY; transcription factor YY
D 128600451 gabpb2a; GA-binding protein subunit beta-2a K09454 GABPB; GA-binding protein transcription factor, beta
D 128607137 gabpb1; GA-binding protein subunit beta-1 K09454 GABPB; GA-binding protein transcription factor, beta
D 128616550 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 128623605 nrf1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1
D 128608898 nfe2l2a; nuclear factor erythroid 2-related factor 2a K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 128606668 mt2; metallothionein-2 K14739 MT1_2; metallothionein 1/2
C Coactivators
D 128609997 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 128611482 ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 128605459 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 128613405 crtc1b; CREB-regulated transcription coactivator 1b isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 128603019 crebbpa; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 128615555 ep300b; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 128616552 ep300a; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 128624929 crebbpb; CREB binding protein b isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 128625215 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 128599217 iscu; iron-sulfur cluster assembly enzyme ISCU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 128614625 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 128608106 frataxin, mitochondrial-like K19054 FXN; frataxin [EC:1.16.3.1]
D 128608280 frataxin, mitochondrial-like K19054 FXN; frataxin [EC:1.16.3.1]
D 128602213 adrenodoxin-like K22070 FDX1; ferredoxin-1, mitochondrial
D 128616258 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 128616604 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 128611103 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 128599210 hscb; iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 128611787 sil1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 128601192 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 128599131 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial isoform X1 K22063 ISCA1; iron-sulfur cluster assembly 1
D 128612312 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 128610589 iba57; putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 128605529 zgc:110319; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 128607425 nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 128599516 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 128613720 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 128605519 sfxn3; sideroflexin-3 isoform X1 K23500 SFXN1_3; sideroflexin-1/3
D 128618055 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 128616833 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2
D 128605880 sfxn4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4
D 128605497 sfxn5a; sideroflexin-5a K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 128602749 cpt1aa; carnitine palmitoyltransferase 1Aa (liver) K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 128604112 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 128604388 cpt1a2b; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 128606947 cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 128618082 cpt1ab; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 128617891 dhtkd1; 2-oxoadipate dehydrogenase complex component E1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 128624182 fbxl4; F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 128608187 hcfc1b; host cell factor 1b isoform X1 K14966 HCFC1; host cell factor 1
D 128623445 hcfc2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2
D 128605996 htt; huntingtin isoform X1 K04533 HD; huntingtin
D 128622868 esrra; steroid hormone receptor ERR1 isoform X1 K08552 NR3B1; estrogen-related receptor alpha
D 128612645 esrrb; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 128606879 esrrd; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 128612186 esrrga; estrogen-related receptor gamma a K08554 NR3B3; estrogen-related receptor gamma
D 128619015 esrrgb; estrogen-related receptor gamma b isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 128620386 nrip1b; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 128621143 nrip1a; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 128601100 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 128603610 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 128613478 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 128605330 sirt1; NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 128600986 serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 128608164 uxt; protein UXT K26537 UXT; protein UXT
D 128608834 zgc:162944; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 128609210 gatd3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 128611232 si:ch211-153b23.5; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 128599094 tango2; transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2
D 128608584 c6h2orf69; mitochondrial protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69
D 128607102 atosa; atos homolog protein A isoform X1 K28528 ATOS; protein Atossa
D 128625444 atos homolog protein B K28528 ATOS; protein Atossa
D 128615576 ddx47; probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7]
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 128605122 ndufaf1; complex I intermediate-associated protein 30, mitochondrial isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 128608085 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 isoform X1 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 128624841 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 128617842 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 128602345 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 128613392 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 128601420 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 128617391 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 128609926 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 128624807 acad9; complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 128612830 nubpl; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 128620173 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 128612712 rtn4ip1; reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 128602158 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 128613764 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 128609027 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 128609565 ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 128620856 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 128614986 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 128614904 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 128620611 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 128605343 protein ccsmst1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 128619771 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 128611611 protein brawnin K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 128623712 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 128606402 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 128609680 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 128616681 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 128620357 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 128609115 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 128623523 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 128601147 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 128617149 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 128617012 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 128625036 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 128604434 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 128609386 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 128624204 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 128617043 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 128605304 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 128615620 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 128615635 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 128600835 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 128602683 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 128610112 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 128603416 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 128600245 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 128618406 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 128617467 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 128605054 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 128605564 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1
D 128623712 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 128619771 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 128622580 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
D 128610609 higd1a; HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 128624890 HIG1 domain family member 1C K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 128623953 higd2a; HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial
C Complex-V assembly factors
D 128613987 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 128616905 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 128624352 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 128601463 atp5mj; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 128601812 atp5md; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 128613357 mfn1b; mitofusin-1b isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 128607555 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 128614586 opa1; dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 128606496 opa3; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 128620726 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 128621283 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 128602137 apoptosis regulator BAX-like isoform X1 K02159 BAX; apoptosis regulator BAX
D 128602505 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 128602514 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 128614261 zgc:153993; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 128607431 si:dkey-32e23.4; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 128611576 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 128610098 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 128615347 sumo2b; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 128615830 sumo3a; small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier
D 128615945 sumo2a; small ubiquitin like modifier 2a K12160 SUMO; small ubiquitin-related modifier
D 128616180 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 128606043 sh3glb1a; endophilin-B1a K11248 SH3GLB1; endophilin-B1
D 128623926 sh3glb1b; endophilin-B1b isoform X1 K11248 SH3GLB1; endophilin-B1
D 128602921 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 128621322 mffa; mitochondrial fission factor homolog B isoform X1 K22076 MFF; mitochondrial fission factor
D 128624194 mffb; mitochondrial fission factor homolog A isoform X1 K22076 MFF; mitochondrial fission factor
D 128599813 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 128619532 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 128601314 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 128601800 mief2; mitochondrial dynamics protein MID49 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 128615575 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 128602522 pld6; mitochondrial cardiolipin hydrolase isoform X1 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 128609712 miga1; LOW QUALITY PROTEIN: mitoguardin 1 K27289 MIGA; mitoguardin
D 128622147 miga2; mitoguardin 2 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 128600219 actb2; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 128601766 actb1; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 128601439 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 128601558 N-alpha-acetyltransferase 20-like K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 128620167 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 128601435 phb; prohibitin K17080 PHB1; prohibitin 1
D 128624323 phb2a; prohibitin-2a K17081 PHB2; prohibitin 2
D 128612409 ktn1; kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 128607431 si:dkey-32e23.4; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 128611576 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 128607116 myo5aa; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
D 128613925 si:dkey-110c1.10; unconventional myosin-Va K10357 MYO5; myosin V
D 128618271 myo5ab; unconventional myosin-Va K10357 MYO5; myosin V
D 128618680 myo5c; unconventional myosin-Vc K10357 MYO5; myosin V
D 128622432 myo5b; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 128611436 xiap; E3 ubiquitin-protein ligase XIAP isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 128611437 E3 ubiquitin-protein ligase XIAP isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 128621360 diabloa; diablo, IAP-binding mitochondrial protein a K10522 DIABLO; diablo
D 128622322 diablob; diablo, IAP-binding mitochondrial protein b K10522 DIABLO; diablo
C Morphogenesis factors
D 128611204 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25
D 128600324 rhot1a; mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 128615992 rhot1b; mitochondrial Rho GTPase 1b isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 128611148 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 128603702 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 128608771 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 128607091 nedd4a; E3 ubiquitin-protein ligase NEDD4-like isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 128599565 oxr1a; oxidation resistance protein 1a isoform X1 K25437 OXR1; oxidation resistance protein 1
D 128618707 msto1; protein misato homolog 1 K27320 MSTO1; protein misato
D 128611352 prelid1a; PRELI domain containing 1a K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 128618899 prelid1b; PRELI domain containing 1b isoform X1 K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 128615487 prelid3b; PRELI domain containing protein 3B K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 128611184 atg2a; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 128612741 atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 128615358 atg3; ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 128602076 atg4da; cysteine protease atg4da K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 128614519 atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 128614957 atg4c; cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 128615776 cysteine protease atg4da-like isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 128622071 atg4a; cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 128623988 atg5; autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 128617527 becn1; beclin-1 K08334 BECN; beclin
D 128625375 atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 128608162 zgc:92606; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 128610010 gabarapb; GABA(A) receptor-associated protein b K08341 GABARAP; GABA(A) receptor-associated protein
D 128611114 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 128600364 atg9b; autophagy-related protein 9B isoform X1 K17907 ATG9; autophagy-related protein 9
D 128615828 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 128620225 atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 128608654 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 128612674 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 128621205 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 128620931 protein Atg16l2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 128600273 wipi2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
D 128602676 wipi1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 128605392 prkn; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31]
D 128619346 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 128624508 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 128619217 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 128621283 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 128611050 sqstm1; sequestosome-1 K14381 SQSTM1; sequestosome 1
D 128600419 tax1bp1a; tax1-binding protein 1 homolog A isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 128609262 tax1bp1b; tax1-binding protein 1 homolog B isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 128617556 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 128617889 ambra1b; activating molecule in BECN1-regulated autophagy protein 1B K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 128602791 atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 128607389 ulk1a; serine/threonine-protein kinase ULK1a isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 128622170 ulk1b; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 128621163 ulk2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 128599924 rb1cc1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 128601060 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 128601306 hsp90aa1.2; heat shock protein 90, alpha (cytosolic), class A member 1, tandem duplicate 2 K04079 HSP90A; molecular chaperone HtpG
D 128601307 hsp90aa1.1; heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG
D 128602286 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 128599138 smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 128600269 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 128615504 E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 128607768 bnip3la; BCL2 interacting protein 3 like a K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 128619986 bnip3lb; BCL2 interacting protein 3 like b K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 128620116 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 128608783 fundc1; FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 128601100 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 128603610 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 128611117 map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 128614220 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 128624808 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 128603612 nbr1b; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 128616969 nbr1a; NBR1 autophagy cargo receptor a isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 128600339 tecpr1b; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 128617064 tecpr1a; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 128600921 zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 128621567 si:ch211-11n16.2; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 128601151 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 128602898 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 128603067 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 128603147 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 128606559 zgc:112052; protein C19orf12 homolog K23168 MPAN; protein MPAN
D 128622539 fundc2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025