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  Mitochondrial Biogenesis - Ictalurus punctatus (channel catfish)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 804880 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 804883 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 804878 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 804882 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 804881 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 804879 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 804886 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 804887 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 804884 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 804875 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 804885 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 804876 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 804877 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 108271309 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 108274334 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 108269828 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 108269873 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 108264715 translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2 D 108260173 translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3 D 108271604 elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 108272996 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 108280774 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 108260278 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 108264424 transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 108274823 transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 108257236 transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 108280825 mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 108268617 translation factor Guf1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 108256656 ribonucleases P/MRP protein subunit POP1 isoform X1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 108259280 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 100528538 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 108274261 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 100528550 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 108264191 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 124625957 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 108256513 ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 108280187 ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 108258702 tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 100528090 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 108269878 prorp; mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 108276074 putative protein MSS51 homolog, mitochondrial isoform X2 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 108263122 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 108273257 transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 108262201 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 108261958 pentatricopeptide repeat-containing protein 1, mitochondrial-like K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 128629228 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 108260266 pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 108268969 pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 108267787 ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 108272058 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 108269919 afg1la; AFG1 like ATPase a K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 108280045 mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 108263364 ATP-dependent RNA helicase SUPV3L1, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 108280430 endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 108260169 si:dkey-251i10.1; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 108260845 ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 108266970 slc25a6; ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 108273102 ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 100528860 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 108263424 mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 108265398 mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 108263520 mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 108260407 GTPase Era, mitochondrial K03595 era; GTPase D 108274440 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 108257421 yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 108270607 probable leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 108278975 lars1b; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 108267777 aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 108256644 gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 108255105 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 108279246 rars1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 108269694 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 108260654 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 108255592 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial isoform X1 K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 108274186 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 108254968 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 100528095 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 108273942 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 108258895 tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 108280832 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 100528698 rpusd4; pseudouridylate synthase RPUSD4, mitochondrial K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 108260110 RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein D 108265436 neugrin isoform X1 K23496 NGRN; neugrin D 108271730 mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 108258353 FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 108256002 mtrfr; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor D 108270400 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 108255698 G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1 D 108259596 probable methyltransferase-like protein 15 isoform X2 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 108255223 myg1; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 108263382 mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 108275148 DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 108273112 DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2 D 108260893 DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 108264877 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 108261149 mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 108271400 nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial D 108273940 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3] D 108280831 ATP-dependent DNA helicase PIF1 isoform X1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 108280094 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 108254699 atad3; ATPase family AAA domain containing 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 100528072 cf125; uncharacterized protein c6orf125 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 108264052 dnaja2b; dnaJ homolog subfamily A member 2b K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 108259613 dnaja2a; dnaJ homolog subfamily A member 2a K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 108271848 mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 108272928 rhot1b; mitochondrial Rho GTPase 1b K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 108257070 rhot1a; mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 108277187 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 108259092 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100305036 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 108277936 hspa8b; heat shock protein family A (Hsp70) member 8b K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 108277666 hsc70; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 108276297 ada; adenosine deaminase K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 108259095 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 108262339 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 128629166 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 128629167 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 108263254 aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein D 108268564 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein D 108277465 aryl-hydrocarbon-interacting protein-like 1 isoform X2 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 108272662 tomm40l; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40 D 108259972 si:dkey-71l1.1; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40 D 108272680 tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 108272087 tomm70a; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 108273994 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 100528246 tomm20b; mitochondrial import receptor subunit TOM20 homolog B K17770 TOM20; mitochondrial import receptor subunit TOM20 D 108257495 mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 108272056 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 100528948 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 108269286 samm50; sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family D 108280132 samm50l; sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family C Porin D 108263545 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 108273854 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 100528960 zgc:56235; voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 108272909 mtx1b; metaxin-1b isoform X2 K17776 MTX; metaxin D 108267565 mtx1a; metaxin-1a isoform X1 K17776 MTX; metaxin D 100528665 mtx2; metaxin-2 K17776 MTX; metaxin D 108255991 metaxin-3 isoform X1 K17776 MTX; metaxin D 108260099 unconventional myosin-XIX K25838 MYO19; myosin XIX D 100528866 marc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 108269753 mitochondrial import inner membrane translocase subunit Tim9 isoform X1 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 100528406 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 108277351 mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 108269132 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 108260428 mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 108270874 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 108254934 chchd4a; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 108257358 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 100528896 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 108268968 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 108271266 micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 108275053 chchd3b; coiled-coil-helix-coiled-coil-helix domain containing 3b isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 100528260 chchd3a; coiled-coil-helix-coiled-coil-helix domain containing 3a K17563 CHCHD3; MICOS complex subunit MIC19 D 108272181 chchd6b; coiled-coil-helix-coiled-coil-helix domain containing 6b K17564 CHCHD6; MICOS complex subunit MIC25 D 108260191 apooa; apolipoprotein O, a isoform X1 K24625 APOO; MICOS complex subunit MIC26 D 108256572 apoob; apolipoprotein O, b isoform X2 K24625 APOO; MICOS complex subunit MIC26 D 108259903 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27 D 108269120 MICOS complex subunit MIC27 isoform X1 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 100528896 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 108268968 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 108260075 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 108263229 timm23b; mitochondrial import inner membrane translocase subunit Tim23B isoform X1 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 108274050 timm23a; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 108265669 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 108255216 mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 108256094 mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 108277495 mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 108263040 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 108263039 calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial D 108260281 calcium uptake protein 2, mitochondrial isoform X1 K22828 MICU2; calcium uptake protein 2, mitochondrial D 108262961 calcium uniporter protein, mitochondrial isoform X3 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 108272514 smdt1b; single-pass membrane protein with aspartate-rich tail 1b K22830 SMDT1; essential MCU regulator, mitochondrial D 108268156 mcur1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 108263603 mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 100528950 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 108268701 mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 100529013 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 100528655 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 108266934 mpc2b; mitochondrial pyruvate carrier 2b K22139 MPC2; mitochondrial pyruvate carrier 2 D 108258922 mpc2a; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 108279156 coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 108271037 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 108269129 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 108278944 grpel2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 108268322 grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 108271133 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 100528747 pam16; mitochondrial import inner membrane translocase subunit tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 108255664 mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 108275141 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 108277681 mipepa; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 108266280 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 100528879 hspe1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 108259422 dnaja3b; dnaJ heat shock protein family (Hsp40) member A3b K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 108276514 dnaja3a; dnaJ heat shock protein family (Hsp40) member A3a K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 100528503 tamm41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 108279180 DNL-type zinc finger protein isoform X1 K17808 ZIM17; mitochondrial protein import protein ZIM17 D 108278065 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 108260229 polymerase delta-interacting protein 2 isoform X2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 108258958 creb1a; cyclic AMP-responsive element-binding protein 1a K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 108267006 creb1b; cyclic AMP-responsive element-binding protein 1b K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 108280774 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 108260278 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 108254785 transcription factor Sp1 K04684 SP1; transcription factor Sp1 D 108258103 yy1b; transcriptional repressor protein YY1b isoform X1 K09201 YY; transcription factor YY D 100304682 yy1a; transcriptional repressor protein YY1a K09201 YY; transcription factor YY D 108257329 gabpb2a; GA-binding protein subunit beta-2a K09454 GABPB; GA-binding protein transcription factor, beta D 108264493 GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 108274334 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 108279827 nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1 D 108266577 nfe2l2a; nuclear factor erythroid 2-related factor 2a K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 100304478 mt2; metallothionein K14739 MT1_2; metallothionein 1/2 C Coactivators D 108267918 peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X5 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 108268932 ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 108263826 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 108270890 si:dkey-93h22.8; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 108271387 crtc1b; CREB-regulated transcription coactivator 1b isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 108279275 crebbpb; CREB binding protein b isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 108273944 ep300a; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 108272975 ep300b; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 108259383 crebbpa; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 108255141 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 108255833 iron-sulfur cluster assembly enzyme ISCU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 100528078 lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 108265194 frataxin, mitochondrial-like K19054 FXN; frataxin [EC:1.16.3.1] D 108265371 frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 108259004 fdx1; adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial D 108259761 fdx1b; ferredoxin 1b K22070 FDX1; ferredoxin-1, mitochondrial D 108272318 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 108273819 NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X6 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 108269129 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 108255983 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB D 108268829 nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1 D 108258029 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 108255919 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 108270216 iron-sulfur cluster assembly 2 homolog, mitochondrial isoform X1 K22072 ISCA2; iron-sulfur cluster assembly 2 D 108267895 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 108263312 zgc:110319; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 108265347 nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 108256193 bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 108271399 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 108263463 sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 108275306 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 108274066 sideroflexin-2 K23501 SFXN2; sideroflexin-2 D 108263167 sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4 D 108262907 sfxn5a; sideroflexin-5a K23503 SFXN5; sideroflexin-5 D 108269334 sfxn5b; sideroflexin-5b K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 108269775 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 108264444 carnitine O-palmitoyltransferase 1, muscle isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 108259197 cpt1aa; carnitine palmitoyltransferase 1Aa (liver) isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 108275128 cpt1ab; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 108280342 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 108275231 2-oxoadipate dehydrogenase complex component E1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 108280900 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 108265652 hcfc1b; host cell factor 1b isoform X1 K14966 HCFC1; host cell factor 1 D 108279775 host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2 D 108263566 huntingtin isoform X1 K04533 HD; huntingtin D 108278770 steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha D 108269441 steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 108257748 esrrgb; estrogen-related receptor gamma b K08554 NR3B3; estrogen-related receptor gamma D 108270480 esrrga; estrogen-related receptor gamma a isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 108263916 esrrd; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma D 108278217 nrip1a; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 108277259 nrip1b; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 108260283 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 108258037 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 100304917 lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 108261052 NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 108257770 protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 108265647 protein UXT isoform X2 K26537 UXT; protein UXT B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 108262986 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 100529027 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 108254711 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 108258626 arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 108272529 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 108258052 protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 108273794 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 108267587 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 108254954 complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 108270385 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 108276862 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 108269695 reticulon-4-interacting protein 1 homolog, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 100528463 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 108271018 succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 108266488 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 108267676 tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 108276560 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 108272058 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 100528072 cf125; uncharacterized protein c6orf125 K17682 MNF1; mitochondrial nucleoid factor 1 D 108276903 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 108270539 protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 108276133 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 108269361 protein brawnin K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 108279635 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 108256239 COX assembly mitochondrial protein homolog isoform X2 K18171 CMC1; COX assembly mitochondrial protein 1 D 124626610 COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 108267121 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1 D 108274181 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 108276751 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 100528793 cb064; uncharacterized protein c2orf64-like protein K18178 COA5; cytochrome c oxidase assembly factor 5 D 108280096 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 108258110 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 108274223 protoheme IX farnesyltransferase, mitochondrial isoform X1 K02257 COX10; heme o synthase [EC:2.5.1.141] D 108273989 cytochrome c oxidase assembly protein COX11, mitochondrial isoform X1 K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 108255111 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14 D 108260879 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9] D 108263232 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 108266537 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 108278588 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18 D 108273447 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 108263832 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 108276074 putative protein MSS51 homolog, mitochondrial isoform X2 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 108263122 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 108257119 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 124626412 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 108267792 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 100528075 surf1; surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 108258077 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 108274471 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 128634963 protein SCO2 homolog, mitochondrial-like K23755 SCO2; protein SCO2 D 108273850 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 108263541 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 108263202 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1 D 108279635 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 108276133 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 C Complex-V assembly factors D 100528934 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 108274357 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 108280504 transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 108257849 atp5mj; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid D 100528788 atp5md; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 108270971 mfn1b; mitofusin-1b isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 108265739 mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 108271989 dynamin-like 120 kDa protein, mitochondrial isoform X5 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 108264292 optic atrophy 3 protein homolog isoform X1 K23166 OPA3; optic atrophy 3 protein D 100528976 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 108277433 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 108270970 zgc:153993; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 100528667 baxa; BCL2 associated X, apoptosis regulator a K02159 BAX; apoptosis regulator BAX D 108274750 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 108259599 baxb; BCL2 associated X, apoptosis regulator b isoform X1 K02159 BAX; apoptosis regulator BAX D 128629193 apoptosis regulator BAX-like isoform X1 K02159 BAX; apoptosis regulator BAX D 128629195 apoptosis regulator BAX-like isoform X1 K02159 BAX; apoptosis regulator BAX D 128629196 apoptosis regulator BAX-like isoform X1 K02159 BAX; apoptosis regulator BAX D 128629197 apoptosis regulator BAX-like isoform X1 K02159 BAX; apoptosis regulator BAX D 108265374 si:dkey-32e23.4; dynamin-1-like protein isoform X2 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 108269241 dynamin-1-like protein isoform X2 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 108267635 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 100528483 sumo2a; small ubiquitin like modifier 2a K12160 SUMO; small ubiquitin-related modifier D 108272860 sumo2b; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 108273059 sumo3a; small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier D 108273359 small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 108280317 sh3glb1b; endophilin-B1b isoform X1 K11248 SH3GLB1; endophilin-B1 D 108265118 sh3glb1a; endophilin-B1a K11248 SH3GLB1; endophilin-B1 D 100528187 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 108278744 mitochondrial fission factor-like isoform X1 K22076 MFF; mitochondrial fission factor D 108278285 mffa; mitochondrial fission factor homolog B isoform X1 K22076 MFF; mitochondrial fission factor D 108280720 mffb; mitochondrial fission factor homolog A isoform X1 K22076 MFF; mitochondrial fission factor D 108256098 ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 108276258 ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 108279890 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 108258856 mief2; mitochondrial dynamics protein MID49 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 108272995 mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 108258502 mitochondrial cardiolipin hydrolase isoform X1 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 108279161 mitoguardin 2 K27289 MIGA; mitoguardin D 108267591 LOW QUALITY PROTEIN: mitoguardin 1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 108258691 actb1; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 100526698 actb2; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 108258191 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 108276932 N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 108260386 prohibitin K17080 PHB1; prohibitin 1 D 108280866 phb2a; prohibitin-2a K17081 PHB2; prohibitin 2 D 108270116 kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 108265374 si:dkey-32e23.4; dynamin-1-like protein isoform X2 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 108269241 dynamin-1-like protein isoform X2 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 108275443 myo5ab; unconventional myosin-Va K10357 MYO5; myosin V D 108264474 myo5aa; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V D 108270951 si:dkey-110c1.10; unconventional myosin-Vb K10357 MYO5; myosin V D 108275348 unconventional myosin-Vc K10357 MYO5; myosin V D 108279397 unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V D 108269205 xiap; E3 ubiquitin-protein ligase XIAP isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 108269206 E3 ubiquitin-protein ligase XIAP isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 108279085 diablob; diablo, IAP-binding mitochondrial protein b K10522 DIABLO; diablo D 108278350 diabloa; diablo, IAP-binding mitochondrial protein a K10522 DIABLO; diablo C Morphogenesis factors D 108268616 sorting nexin-25 K17887 SNX25; sorting nexin-25 D 108272928 rhot1b; mitochondrial Rho GTPase 1b K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 108257070 rhot1a; mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 108268968 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 108260378 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 100529017 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 124627078 E3 ubiquitin-protein ligase NEDD4-like isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 108256331 oxr1a; oxidation resistance protein 1a isoform X1 K25437 OXR1; oxidation resistance protein 1 D 108274805 protein misato homolog 1 K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 108269093 autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 108270328 autophagy-related protein 2 homolog B isoform X4 K17906 ATG2; autophagy-related protein 2 D 100528116 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 108272127 cysteine protease ATG4C isoform X2 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 108258540 atg4da; cysteine protease atg4da K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 108272027 cysteine protease ATG4B isoform X3 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 108272831 cysteine protease atg4da isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 108278677 cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 108280573 autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 128634440 beclin-1 isoform X1 K08334 BECN; beclin D 108255112 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 108260203 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 108268088 gabarapb; GABA(A) receptor-associated protein b K08341 GABARAP; GABA(A) receptor-associated protein D 108268593 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 108266696 zgc:92606; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 108264054 atg9b; autophagy-related protein 9B isoform X2 K17907 ATG9; autophagy-related protein 9 D 100304775 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 124629002 ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 108266987 ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12 D 108270077 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 108277711 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 108277834 protein Atg16l2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2 D 108259373 WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 108256943 WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 108263700 prkn; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31] D 108276236 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 108276814 protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 108275846 serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 108277433 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 108268580 sequestosome-1 K14381 SQSTM1; sequestosome 1 D 108257015 tax1bp1a; tax1-binding protein 1 homolog A K21347 TAX1BP1; Tax1-binding protein 1 D 108267440 tax1bp1b; tax1-binding protein 1 homolog B isoform X1 K21347 TAX1BP1; Tax1-binding protein 1 D 108274126 calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 108274968 ambra1b; activating molecule in BECN1-regulated autophagy protein 1B isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 108259341 autophagy-related protein 13 isoform X3 K08331 ATG13; autophagy-related protein 13 D 108279004 ulk1b; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 108265551 ulk1a; serine/threonine-protein kinase ULK1a isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 108277484 serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 108264415 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 108257811 hsp90aa1.2; heat shock protein 90, alpha (cytosolic), class A member 1, tandem duplicate 2 K04079 HSP90A; molecular chaperone HtpG D 108257813 hsp90aa1.1; heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG D 100526716 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 108258780 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 108273115 E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 108257367 E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 108254810 smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 108277095 bnip3lb; BCL2 interacting protein 3 like b isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 108265827 bnip3la; BCL2 interacting protein 3 like a K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 108266973 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 108260283 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 108258037 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 108269044 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 108270579 microtubule-associated proteins 1A/1B light chain 3C isoform X1 K10435 MAP1LC; microtubule-associated protein 1 light chain D 100529034 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 108268898 map1lc3cl; microtubule-associated proteins 1A/1B light chain 3C isoform X2 K10435 MAP1LC; microtubule-associated protein 1 light chain D 108276620 nbr1b; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 108273956 nbr1a; NBR1 autophagy cargo receptor a isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 108273961 tecpr1a; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 108276900 tecpr1b; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 108278225 si:ch211-11n16.2; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 108257578 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 108264103 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 108259399 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 100528775 zgc:112052; protein C19orf12 homolog K23168 MPAN; protein MPAN D 108259285 protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN D 108259286 protein C19orf12 homolog K23168 MPAN; protein MPAN D 108279134 FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024