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Mitochondrial Biogenesis - Lingula anatina
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D C2G87_mgp06 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D C2G87_mgp12 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D C2G87_mgp05 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D C2G87_mgp03 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D C2G87_mgp11 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D C2G87_mgp04 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D C2G87_mgp10 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D C2G87_mgp01 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D C2G87_mgp13 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D C2G87_mgp02 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 106161215 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
D 106177706 DNA-directed RNA polymerase, mitochondrial-like K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 106176950 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 106177014 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 106151358 mitochondrial dimethyladenosine transferase 1-like K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 106181777 mitochondrial dimethyladenosine transferase 1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 106161836 uncharacterized protein LOC106161836 K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 106168248 translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 106171905 elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 106153650 uncharacterized protein LOC106153650 K02358 tuf; elongation factor Tu
D 106153750 uncharacterized protein LOC106153750 isoform X1 K02358 tuf; elongation factor Tu
D 106165922 ribosome-releasing factor 2, mitochondrial-like K02355 fusA; elongation factor G
D 106167130 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 106176301 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 106153612 uncharacterized protein LOC106153612 K15031 MTERF; mitochondrial transcription termination factor family protein
D 106174735 translation factor Guf1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 106151689 ribonucleases P/MRP protein subunit POP1-like K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 106151694 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 106173710 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 112042424 ribonuclease P protein subunit p29-like K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 106153751 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 106160804 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 106150585 ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 106164802 ribonuclease P protein subunit p20-like isoform X1 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 106159443 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 106166726 ribonuclease P protein subunit p38-like K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 106168171 ribonuclease P protein subunit p40-like K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
D 106179352 ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 106174142 tRNA methyltransferase 10 homolog B K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 106166979 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 106178562 uncharacterized protein LOC106178562 isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 106158916 pentatricopeptide repeat-containing protein 1, mitochondrial-like K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 106150469 pentatricopeptide repeat-containing protein 3, mitochondrial-like isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 106180701 pentatricopeptide repeat-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 106167249 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 106175853 ubiquinol-cytochrome-c reductase complex assembly factor 1-like K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 106175895 AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 106178256 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 106180936 ATP-dependent RNA helicase SUPV3L1, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 106161440 endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 106153250 ADP,ATP carrier protein 3, mitochondrial K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 106156755 ADP,ATP carrier protein 1, mitochondrial K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 106156756 ADP,ATP carrier protein 3, mitochondrial-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 106174504 ADP,ATP carrier protein isoform X1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 106175352 ADP,ATP carrier protein 3, mitochondrial-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 106177089 ADP,ATP carrier protein ER-ANT1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 106159051 mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 112042383 mitoferrin-2-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 106156776 uncharacterized protein LOC106156776 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 106154341 GTPase Era, mitochondrial K03595 era; GTPase
D 106152550 tyrosine--tRNA ligase, cytoplasmic-like K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 106152557 tyrosine--tRNA ligase, cytoplasmic-like K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 106153505 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 106171814 tyrosine--tRNA ligase, mitochondrial-like K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 106156387 probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 106157677 leucine--tRNA ligase, cytoplasmic isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 106165790 probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 106169165 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 106158877 glycine--tRNA ligase-like isoform X1 K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 106173664 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 106158504 arginine--tRNA ligase, cytoplasmic-like K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 106159702 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 106162319 arginine--tRNA ligase, cytoplasmic isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 106168690 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 106178502 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 106181052 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 106160217 poly(A) RNA polymerase, mitochondrial-like K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 106182028 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 106153657 mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 106170317 nitric oxide-associated protein 1-like K19832 NOA1; nitric oxide-associated protein 1
D 106180869 nitric oxide-associated protein 1-like K19832 NOA1; nitric oxide-associated protein 1
D 106180876 nitric oxide-associated protein 1-like K19832 NOA1; nitric oxide-associated protein 1
D 106176479 5-methylcytosine rRNA methyltransferase NSUN4 isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 106178265 mitochondrial mRNA pseudouridine synthase Rpusd3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 106176752 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 106168553 uncharacterized protein LOC106168553 K23496 NGRN; neugrin
D 106179521 mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 106175121 FAST kinase domain-containing protein 4 K27756 TBRG4; FAST kinase domain-containing protein 4
D 106169663 required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 106155169 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 106151161 UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 106161085 uncharacterized protein C6orf203 homolog isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1
D 106178693 uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 106162019 DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 106162337 DNA polymerase subunit gamma-1 isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 106163603 DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2
D 106162662 uncharacterized protein LOC106162662 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
D 106166308 DNA-directed primase/polymerase protein-like K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 106171507 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 106173506 endonuclease G, mitochondrial-like K01173 ENDOG; endonuclease G, mitochondrial
D 106176279 mitochondrial genome maintenance exonuclease 1 isoform X1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 106151390 nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial
D 106156672 twinkle protein, mitochondrial-like K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 106171970 twinkle protein, mitochondrial-like K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 106167512 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 106161542 ATPase family AAA domain-containing protein 3-A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 106157834 dnaJ homolog subfamily A member 2 isoform X1 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 106161848 mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 106152011 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 106153171 heat shock 70 kDa protein 1B-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 106161608 heat shock cognate 71 kDa protein isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 106166564 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 106174133 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 106181032 heat shock 70 kDa protein 1B-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 106181034 heat shock 70 kDa protein 1B-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 106157846 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 106165369 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 106178377 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 106156765 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 106180423 mitochondrial import receptor subunit TOM40 homolog 2-like K11518 TOM40; mitochondrial import receptor subunit TOM40
D 106151075 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 106170274 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
C TOB/SAM complex
D 106159164 sorting and assembly machinery component 50 homolog B-like K07277 SAM50; outer membrane protein insertion porin family
D 106180752 sorting and assembly machinery component 50 homolog B-like K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 106167163 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
C ERMES complex
C Other outer membrane factor
D 106155001 metaxin-2-like K17776 MTX; metaxin
D 106155419 metaxin-1 isoform X1 K17776 MTX; metaxin
D 106169346 metaxin-2 isoform X1 K17776 MTX; metaxin
D 106169583 mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 106169584 mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 106171794 mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 106178218 mitochondrial amidoxime reducing component 2-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 106171750 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 106165822 mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
D 106180342 mitochondrial import inner membrane translocase subunit Tim10 B isoform X1 K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 106158462 mitochondrial import inner membrane translocase subunit Tim13-B K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 106170894 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 106175969 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 106163975 MICOS complex subunit MIC60-1 K17785 IMMT; MICOS complex subunit MIC60
D 106173248 uncharacterized protein LOC106173248 isoform X1 K24624 MICOS13; MICOS complex subunit MIC13
D 106151641 MICOS complex subunit mic25a isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 106162509 uncharacterized protein LOC106162509 K24626 APOOL; MICOS complex subunit MIC27
D 106181501 uncharacterized protein LOC106181501 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 106175969 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 106163975 MICOS complex subunit MIC60-1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 106181073 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 106180818 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 106157736 mitochondrial import inner membrane translocase subunit Tim17-B-like K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 106160158 mitochondrial import inner membrane translocase subunit Tim17-B-like K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 106153336 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 106161298 mitochondrial import inner membrane translocase subunit TIM50-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
D 106161330 mitochondrial import inner membrane translocase subunit TIM50-like isoform X1 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 106163237 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 106170764 calcium uniporter protein, mitochondrial-like K20858 MCU; calcium uniporter protein, mitochondrial
D 106173734 calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 106175068 mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 106169780 LETM1 domain-containing protein LETM2, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 106159663 mitochondrial inner membrane protease subunit 1-like isoform X1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 106179929 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 106169284 uncharacterized protein LOC106169284 K18157 TMEM126A; transmembrane protein 126A
D 106155471 mitochondrial pyruvate carrier 1 isoform X1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 106163433 mitochondrial pyruvate carrier 1-like K22138 MPC1; mitochondrial pyruvate carrier 1
D 106176363 mitochondrial pyruvate carrier 4 isoform X1 K22139 MPC2; mitochondrial pyruvate carrier 2
B Matrix
C MMC/PAM proteins
D 106158059 mitochondrial import inner membrane translocase subunit TIM44-like K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 106168522 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 106176543 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 106169732 grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 106174693 grpE protein homolog 1, mitochondrial-like K03687 GRPE; molecular chaperone GrpE
D 106176425 mitochondrial import inner membrane translocase subunit TIM14-like isoform X1 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 106176426 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 106150552 mitochondrial import inner membrane translocase subunit Tim16-like K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
D 106170057 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 106179910 mitochondrial-processing peptidase subunit alpha-like K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 106180529 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 106167002 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 106152488 mitochondrial intermediate peptidase-like K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 106164240 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 106151387 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 106151388 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 106155414 protein tumorous imaginal discs, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 106176706 protein tumorous imaginal discs, mitochondrial-like K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 106181993 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 106178602 DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 106154017 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 106160274 persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 106160912 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 106166234 polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
D 106172113 polymerase delta-interacting protein 2-like K17809 POLDIP2; polymerase delta-interacting protein 2
D 106172114 polymerase delta-interacting protein 2-like K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 106157277 cAMP-responsive element modulator isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 106165922 ribosome-releasing factor 2, mitochondrial-like K02355 fusA; elongation factor G
D 106167130 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 106176301 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 106161829 transcriptional repressor protein YY1 isoform X1 K09201 YY; transcription factor YY
D 106170792 GA-binding protein subunit beta-1-like K09454 GABPB; GA-binding protein transcription factor, beta
D 106176950 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 106177014 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 106176786 nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 106162653 CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 106170324 LOW QUALITY PROTEIN: CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 106169204 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 106174078 cysteine desulfurase, mitochondrial-like K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 106169203 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 106174083 LYR motif-containing protein 4-like K22069 LYRM4; LYR motif-containing protein 4
D 106163079 frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 106164829 frataxin, mitochondrial-like K19054 FXN; frataxin [EC:1.16.3.1]
D 106153996 adrenodoxin-like K22070 FDX1; ferredoxin-1, mitochondrial
D 106151869 adrenodoxin-like protein, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 106177774 NADPH:adrenodoxin oxidoreductase, mitochondrial-like K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 106176543 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 106177280 iron-sulfur cluster co-chaperone protein HscB, mitochondrial-like K04082 hscB; molecular chaperone HscB
D 106158493 nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 106155975 glutaredoxin-related protein 5, mitochondrial-like K07390 grxD; monothiol glutaredoxin
D 106155985 glutaredoxin-related protein 5, mitochondrial-like K07390 grxD; monothiol glutaredoxin
D 106155792 iron-sulfur cluster assembly 1 homolog, mitochondrial-like K22063 ISCA1; iron-sulfur cluster assembly 1
D 106173310 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 106168670 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 106181116 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 106160420 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 106180922 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 106176914 bolA-like protein DDB_G0274169 K22066 BOLA1; BolA-like protein 1
D 106155260 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 106180933 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 106163954 sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2
D 106170561 sideroflexin-5 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 106159033 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 106164942 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 106167245 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 106173274 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 106179926 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 106179945 carnitine O-palmitoyltransferase 1, muscle isoform isoform X1 K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 106169636 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 106176283 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 106178702 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 106165253 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 106180476 host cell factor 2 isoform X1 K14966 HCFC1; host cell factor 1
D 106165242 huntingtin K04533 HD; huntingtin
D 106170076 steroid hormone receptor ERR2 K08554 NR3B3; estrogen-related receptor gamma
D 106153756 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 106171922 serine/threonine-protein kinase AtPK2/AtPK19 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 106174398 NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 106158528 protein SERAC1-like K23504 SERAC1; protein SERAC1
D 106178647 protein UXT-like K26537 UXT; protein UXT
D 106159760 ES1 protein homolog, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 106164517 ES1 protein homolog, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 106176778 transport and Golgi organization 2 homolog K28098 TANGO2; transport and Golgi organization protein 2
D 106163733 UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69
D 106164972 protein FAM214A-like K28528 ATOS; protein Atossa
D 106155602 probable ATP-dependent RNA helicase DDX47 isoform X1 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7]
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 106176657 complex I intermediate-associated protein 30, mitochondrial isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 106163574 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 isoform X1 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 106162088 uncharacterized protein LOC106162088 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 106155688 arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 106160539 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 106161316 protein arginine methyltransferase NDUFAF7, mitochondrial-like K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 106166612 protein arginine methyltransferase NDUFAF7, mitochondrial-like K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 106172072 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8-like K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 106151637 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 106166781 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 106151905 acyl-CoA dehydrogenase family member 9, mitochondrial-like K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 106151925 acyl-CoA dehydrogenase family member 9, mitochondrial-like K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 106166209 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 106167931 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 106168722 reticulon-4-interacting protein 1 homolog, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 106172560 uncharacterized protein LOC106172560 K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 106166528 succinate dehydrogenase assembly factor 2, mitochondrial-like K18168 SDHAF2; succinate dehydrogenase assembly factor 2
D 106170854 succinate dehydrogenase assembly factor 2, mitochondrial isoform X1 K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 106166292 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 106167955 tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 106172370 complex III assembly factor LYRM7 isoform X1 K18170 LYRM7; complex III assembly factor LYRM7
D 106167249 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 106175853 ubiquinol-cytochrome-c reductase complex assembly factor 1-like K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
C Complex-IV assembly factors
D 106151738 uncharacterized protein LOC106151738 K18171 CMC1; COX assembly mitochondrial protein 1
D 106155972 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 106170431 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 106171161 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 106160816 protoheme IX farnesyltransferase, mitochondrial-like K02257 COX10; heme o synthase [EC:2.5.1.141]
D 106161487 uncharacterized protein LOC106161487 K02257 COX10; heme o synthase [EC:2.5.1.141]
D 106180846 cytochrome c oxidase assembly protein COX11, mitochondrial isoform X1 K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 106173078 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 106173096 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 106176895 mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18
D 106157783 uncharacterized protein LOC106157783 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 106164232 uncharacterized protein LOC106164232 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 106175730 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 106180213 LOW QUALITY PROTEIN: mitochondrial inner membrane protein OXA1L-like K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 106178607 surfeit locus protein 1 isoform X1 K14998 SURF1; surfeit locus 1 family protein
D 106171597 protein sco1-like isoform X1 K07152 SCO1; protein SCO1
D 106152750 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 106162835 protein SCO2 homolog, mitochondrial-like K23755 SCO2; protein SCO2
D 106168387 protein SCO2 homolog, mitochondrial-like K23755 SCO2; protein SCO2
D 106157690 uncharacterized protein LOC106157690 isoform X1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 106173960 APOPT family protein CBG23705, mitochondrial K23506 APOPT1; apoptogenic protein 1
C Complex-V assembly factors
D 106152001 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 106153718 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 106179336 uncharacterized protein LOC106179336 isoform X1 K17966 TMEM70; transmembrane protein 70, mitochondrial
D 106179339 uncharacterized protein LOC106179339 K17966 TMEM70; transmembrane protein 70, mitochondrial
D 112041318 transmembrane protein 70 homolog, mitochondrial-like K17966 TMEM70; transmembrane protein 70, mitochondrial
B Mitochondrial dynamics
C Fission and Fusion factors
D 106176815 mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 106178351 mitofusin-2-like isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 106157245 dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 106166138 optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 106160562 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 106156464 bcl-2 homologous antagonist/killer-like K14021 BAK; Bcl-2 homologous antagonist/killer
D 106181879 bcl-2 homologous antagonist/killer-like K14021 BAK; Bcl-2 homologous antagonist/killer
D 106168833 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 106165591 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 106180478 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 106151594 mitochondrial fission 1 protein-like K17969 FIS1; mitochondrial fission 1 protein
D 106151595 mitochondrial fission 1 protein-like K17969 FIS1; mitochondrial fission 1 protein
D 106157563 small ubiquitin-related modifier K12160 SUMO; small ubiquitin-related modifier
D 106166223 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 106162333 endophilin-B1-like K11248 SH3GLB1; endophilin-B1
D 106166222 endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1
D 106170602 mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 106158126 mitochondrial fission factor homolog B-like K22076 MFF; mitochondrial fission factor
D 106162352 mitochondrial fission factor K22076 MFF; mitochondrial fission factor
D 106151533 ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 106162244 ganglioside-induced differentiation-associated protein 1-like K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 106162246 ganglioside-induced differentiation-associated protein 1-like K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 106175245 ganglioside-induced differentiation-associated protein 1-like K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 106175274 ganglioside-induced differentiation-associated protein 1-like K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 106181391 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 106177620 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 106174999 mitoguardin isoform X1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 106155868 actin, adductor muscle K05692 ACTB_G1; actin beta/gamma 1
D 106159426 actin, adductor muscle K05692 ACTB_G1; actin beta/gamma 1
D 106161464 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 106164072 actin, adductor muscle-like K05692 ACTB_G1; actin beta/gamma 1
D 106167998 actin, cytoplasmic isoform X1 K05692 ACTB_G1; actin beta/gamma 1
D 106171767 actin-1 K05692 ACTB_G1; actin beta/gamma 1
D 106173866 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 106158851 N-alpha-acetyltransferase 20-like K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 106165390 N-alpha-acetyltransferase 20-like K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 106163674 N-alpha-acetyltransferase 25, NatB auxiliary subunit-like K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 106161687 prohibitin K17080 PHB1; prohibitin 1
D 106174917 prohibitin-2 K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 106165591 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 106180478 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 106153177 unconventional myosin-Va-like K10357 MYO5; myosin V
D 106174567 unconventional myosin-Va-like K10357 MYO5; myosin V
D 106161698 baculoviral IAP repeat-containing protein 7-A-like K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 106150651 diablo homolog, mitochondrial-like K10522 DIABLO; diablo
D 106164021 diablo homolog, mitochondrial K10522 DIABLO; diablo
C Morphogenesis factors
D 106159911 sorting nexin-25 K17887 SNX25; sorting nexin-25
D 106167807 sorting nexin-25-like K17887 SNX25; sorting nexin-25
D 106161848 mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 106163975 MICOS complex subunit MIC60-1 K17785 IMMT; MICOS complex subunit MIC60
D 106151100 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 106158475 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 106154247 E3 ubiquitin-protein ligase NEDD4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 106152832 protein misato homolog 1 K27320 MSTO1; protein misato
D 106170378 PRELI domain containing protein 3B K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 106155585 autophagy-related protein 2 homolog B-like K17906 ATG2; autophagy-related protein 2
D 106177197 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 106160314 cysteine protease ATG4A-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 106163133 cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 106180057 uncharacterized protein LOC106180057 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 106154920 autophagy protein 5-like K08339 ATG5; autophagy-related protein 5
D 106154921 autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 106171888 beclin-1 K08334 BECN; beclin
D 106171903 beclin-1-like K08334 BECN; beclin
D 106162377 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 106164368 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 106154602 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 106160890 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 106178447 autophagy-related protein 8 K08341 GABARAP; GABA(A) receptor-associated protein
D 106178512 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 106166078 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 106171792 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 106166458 ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 106165540 ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 106157036 beclin 1-associated autophagy-related key regulator isoform X1 K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 106177754 beclin 1-associated autophagy-related key regulator-like K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 106155851 autophagy-related protein 16-like K17890 ATG16L1; autophagy-related protein 16-1
D 106177136 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 106172375 WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
D 106165290 vacuolar protein 8 K08332 VAC8; vacuolar protein 8
D 106171738 vacuolar protein 8-like K08332 VAC8; vacuolar protein 8
C Parkin-dependent mechanism factors
D 106166390 E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31]
D 106173254 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 106173257 E3 ubiquitin-protein ligase NRDP1-like K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 106154552 protein CLEC16A K19513 CLEC16A; protein CLEC16A
D 106175425 serine/threonine-protein kinase PINK1, mitochondrial isoform X1 K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 106160562 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 106158993 sequestosome-1-like K14381 SQSTM1; sequestosome 1
D 106166208 sequestosome-1 K14381 SQSTM1; sequestosome 1
D 112042683 uncharacterized protein LOC112042683 K14381 SQSTM1; sequestosome 1
D 106162507 uncharacterized protein LOC106162507 K21347 TAX1BP1; Tax1-binding protein 1
D 106163814 tax1-binding protein 1 homolog K21347 TAX1BP1; Tax1-binding protein 1
D 106175544 tax1-binding protein 1 homolog B-like K21347 TAX1BP1; Tax1-binding protein 1
D 106164451 activating molecule in BECN1-regulated autophagy protein 1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 106158979 autophagy-related protein 13 K08331 ATG13; autophagy-related protein 13
D 106158387 serine/threonine-protein kinase 4 homolog B-like K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 106153722 serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 106156501 uncharacterized protein LOC106156501 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 106165638 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 106172755 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG
D 106152595 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 106161242 E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 106177109 E3 ubiquitin-protein ligase SMURF2-like isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 106150955 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 106153756 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 106171922 serine/threonine-protein kinase AtPK2/AtPK19 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 106154233 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 106156530 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 106156668 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 106154225 tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 106156546 tectonin beta-propeller repeat-containing protein 1-like isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 106159835 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 106152114 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 106175711 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 106177994 protein C19orf12 homolog K23168 MPAN; protein MPAN
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#
#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025