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  Mitochondrial Biogenesis - Larimichthys crocea (large yellow croaker)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 7095394 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 7095382 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 7095388 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 7095390 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 7095389 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 7095391 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 7095392 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 7095393 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 7095383 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 7095384 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 7095387 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 7095385 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 7095386 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 104918751 polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 104938062 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 104919289 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 104920142 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 104935438 mtif2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 104925693 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3 D 104931967 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 104930339 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 104939347 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 104931317 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 104927571 mterf1; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 109137999 transcription termination factor 2, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein D 104935268 mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 104919202 mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 104924554 mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 104920557 guf1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 104931573 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 104934213 pop4; ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 104939134 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 104938343 rpp30; ribonuclease P protein subunit p30 isoform X1 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 104932934 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 104940672 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 104926952 uncharacterized protein LOC104926952 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 104939958 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 104923048 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 104932669 rpp40; ribonuclease P protein subunit p40 isoform X3 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 104922559 trmt10c; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 104928358 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 104928658 kiaa0391; mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 104920714 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 104920713 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 104929844 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 104921178 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 104935143 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 104935345 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 104938315 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 104922562 afg1l; AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 104929403 AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 104924518 atp23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 104920180 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 104930071 lactb2; endoribonuclease LACTB2 isoform X1 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 109141357 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 104931197 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 104931565 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 104930032 mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 104929962 mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 104934621 mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 109137352 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 104923443 eral1; GTPase Era, mitochondrial isoform X1 K03595 era; GTPase D 104921010 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 104920437 yars; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 104924022 lars; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 104937907 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 104935389 dars2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 104937015 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 104937430 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 104921900 rars; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 109139479 rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 104923335 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 104917966 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X5 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 104937262 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 104928819 mtpap; poly(A) RNA polymerase, mitochondrial isoform X2 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 104940303 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 104924261 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 104936077 noa1; nitric oxide-associated protein 1 isoform X1 K19832 NOA1; nitric oxide-associated protein 1 D 104923038 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 104920947 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 104933322 mitochondrial RNA pseudouridine synthase rpusd4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 109138804 rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 104927156 ngrn; neugrin K23496 NGRN; neugrin D 104931325 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 104934535 fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 104920300 ciiih12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor D 104929396 rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 104923464 G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1 D 104919247 mettl15; probable methyltransferase-like protein 15 isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 104919955 cvih12orf10; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 104924775 cxxivh6orf203; uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 104925275 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 104932973 polg2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2 D 104930198 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 104939374 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 104918288 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 104928476 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3] D 104920949 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 104935987 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 109141625 atad3a; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 104931333 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 104919827 dnaja2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 104935148 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 104929842 mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 109136624 mitochondrial Rho GTPase 1-A isoform X3 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 104928941 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 104935111 heat shock cognate 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 104932369 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 104926754 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 104938643 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 104934863 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein D 104922857 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein D 104936639 aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 104928053 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 104927345 tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 104929928 mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40 D 104929495 tomm70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 104918900 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 104918199 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 104927318 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 104922048 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 109139297 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 104933257 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 104927303 samm50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family D 104937573 sorting and assembly machinery component 50 homolog A isoform X1 K07277 SAM50; outer membrane protein insertion porin family C Porin D 104931727 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 104930544 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 104930678 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 104921660 voltage-dependent anion-selective channel protein 2 isoform X2 K15041 VDAC3; voltage-dependent anion channel protein 3 D 104934930 voltage-dependent anion-selective channel protein 2 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 104921208 mtx3; metaxin-3 isoform X2 K17776 MTX; metaxin D 104927095 mtx2; metaxin-2 K17776 MTX; metaxin D 104937266 uncharacterized protein LOC104937266 isoform X1 K17776 MTX; metaxin D 104923449 myo19; unconventional myosin-XIX K25838 MYO19; myosin XIX D 104936560 mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 104939563 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 104927688 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 104923816 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 104940595 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 104925366 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 104920235 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 104938929 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 109142966 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 104936675 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 104928002 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 104935409 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 D 104918748 micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 104923711 chchd3; MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 104940685 proline-rich extensin-like protein EPR1 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 104936024 MICOS complex subunit mic25a isoform X5 K17564 CHCHD6; MICOS complex subunit MIC25 D 104919266 MICOS complex subunit mic25a isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 104936204 MICOS complex subunit MIC26 K24625 APOO; MICOS complex subunit MIC26 D 104934077 apoo; MICOS complex subunit MIC26 isoform X1 K24625 APOO; MICOS complex subunit MIC26 D 104925176 MICOS complex subunit MIC27-like isoform X1 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 104936675 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 104928002 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 104935409 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 104923452 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 104923421 timm23; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 104924465 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 104932133 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B isoform X2 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 104921201 timm21; mitochondrial import inner membrane translocase subunit Tim21 isoform X1 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 104930613 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 104918533 mcu; calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial D 104918492 micu1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 104931678 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 104927261 calcium uniporter protein, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 104938259 calcium uniporter regulatory subunit MCUb, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 104926652 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 104938955 smdt1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 104929013 mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 104926794 letm1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 104921644 letm2; LETM1 domain-containing protein LETM2, mitochondrial isoform X2 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 104927774 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 104927034 immp2l; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 104922714 transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 104920184 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 104930896 mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 104931755 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 104920979 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 104920239 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 104921512 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 104928268 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 104923497 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 C Other matrix factors D 104923662 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 104923758 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 104921133 mipep; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 104932518 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 104936735 dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 104925697 dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 104919335 tamm41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 104924500 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 104930280 ethe1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 104920873 poldip2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 104928338 cyclic AMP-responsive element-binding protein 1 isoform X2 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 104923591 cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 104939347 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 104931317 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 104919961 sp1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1 D 104921572 transcriptional repressor protein YY1 K09201 YY; transcription factor YY D 104919809 transcriptional repressor protein YY1 isoform X1 K09201 YY; transcription factor YY D 104932806 GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta D 104936840 gabpb2; GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta D 104938062 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 109138584 nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1 D 104932150 nfe2; transcription factor NF-E2 45 kDa subunit K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 104924427 nfe2l2; nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 C Coactivators D 104921321 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X9 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 104931910 ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 104922275 peroxisome proliferator-activated receptor gamma coactivator-related protein 1-like K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 104924280 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 104921003 CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 104920414 crtc1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 104932063 histone acetyltransferase p300 isoform X5 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 104925373 CREB-binding protein isoform X4 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 104925726 CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 104918882 histone acetyltransferase p300 isoform X3 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 104933300 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 104934686 uncharacterized protein LOC104934686 K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 104937683 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 104935845 lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 104937870 fxn; frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1] D 104925329 fdx1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 104926665 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 104924915 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 104921512 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 104923673 hscb; iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB D 104934871 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1 D 109139567 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 104922992 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 104921369 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 104917691 iba57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 104930157 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 104930649 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 104934033 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 104930093 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 104930226 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 104938452 sfxn1; sideroflexin-1 isoform X2 K23500 SFXN1_3; sideroflexin-1/3 D 104933896 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2 D 104921871 sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4 D 104936094 sfxn5; sideroflexin-5 K23503 SFXN5; sideroflexin-5 D 104927920 sideroflexin-5 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 104920470 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 104922940 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 104935904 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 104940473 cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 104940683 dhtkd1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 104939270 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 104935477 host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1 D 104939450 hcfc1; host cell factor 1 K14966 HCFC1; host cell factor 1 D 104930603 hcfc2; host cell factor 2 K27390 HCFC2; host cell factor 2 D 104921948 htt; huntingtin isoform X10 K04533 HD; huntingtin D 104926321 steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha D 104921347 esrrb; steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta D 104922425 steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 104930080 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 104933525 estrogen-related receptor gamma isoform X4 K08554 NR3B3; estrogen-related receptor gamma D 104925618 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 104930330 nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 104924922 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 104919125 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 104927279 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 104921892 sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 104931013 serac1; protein SERAC1 K23504 SERAC1; protein SERAC1 D 104937402 uxt; protein UXT K26537 UXT; protein UXT B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 104935563 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 104922957 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 104933311 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 104932429 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 104938382 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 104936482 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 104934226 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 109139135 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 104928748 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 104921962 acad9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 104924819 nubpl; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning D 104919186 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 104923336 rtn4ip1; reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 104926747 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial C Complex-II assembly factors D 104936531 sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 104919222 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial isoform X2 K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 104936008 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 104928428 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 104938315 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 104931333 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 104926066 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 104923270 cxvih16orf91; protein CCSMST1 isoform X1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 104935384 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 104937570 cxivh12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 104933640 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 104924531 cmc1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 104927607 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 109141052 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1 D 104928469 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 104932213 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 104929447 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 104932328 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 104922640 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 104926003 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 104934339 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 104938902 cytochrome c oxidase assembly protein COX11, mitochondrial isoform X1 K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 104928375 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14 D 104929856 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 104929781 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 104921485 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 104938307 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18 D 104939492 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 104937564 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 104920714 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 104920713 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 104918569 pet100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 104927613 oxa1l; mitochondrial inner membrane protein OXA1L isoform X2 K03217 yidC; YidC/Oxa1 family membrane protein insertase D 104939083 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 104933981 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 104938688 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 104935466 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 104928438 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 104938945 apopt1; apoptogenic protein 1, mitochondrial isoform X1 K23506 APOPT1; apoptogenic protein 1 D 104933640 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 104935384 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 104918653 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 104928365 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 104918941 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 104938021 tmem70; transmembrane protein 70, mitochondrial isoform X1 K17966 TMEM70; transmembrane protein 70, mitochondrial D 109140234 atp5mpl; 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid D 104921612 atp5md; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 104931950 mfn1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 104938095 mitofusin-1 isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 104932314 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 104923503 opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 104934299 opa3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein D 104936117 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 104933382 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 104936814 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 104933823 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 104923927 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 104927165 apoptosis regulator BAX isoform X2 K02159 BAX; apoptosis regulator BAX D 104931148 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 104940665 dynamin-1-like protein isoform X2 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 104933661 dynamin-1-like protein isoform X2 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 104927605 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 104929816 sumo2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 104931601 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 104937204 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 109141157 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 104938460 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 104918170 endophilin-B1 K11248 SH3GLB1; endophilin-B1 D 104935276 mtch1; mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier D 104933820 mtch2; mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier D 104920900 mitochondrial fission factor homolog A K22076 MFF; mitochondrial fission factor D 104936020 mff; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor D 104921273 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 104939289 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 104926253 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 104930974 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 104921182 mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 104924099 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 104926673 pld6; mitochondrial cardiolipin hydrolase isoform X1 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 104924482 miga2; mitoguardin 2 isoform X1 K27289 MIGA; mitoguardin D 104927477 miga1; mitoguardin 1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 104921174 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 104932075 actb; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 104928531 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 104934935 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 104926273 phb; prohibitin K17080 PHB1; prohibitin 1 D 104934317 phb2; prohibitin-2 K17081 PHB2; prohibitin 2 D 104921423 ktn1; kinectin isoform X2 K17975 KTN1; kinectin C Retention of mitochondria D 104931148 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 104940665 dynamin-1-like protein isoform X2 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 104933661 dynamin-1-like protein isoform X2 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 104921041 unconventional myosin-Vb-like K10357 MYO5; myosin V D 104932823 myo5c; unconventional myosin-Vc isoform X1 K10357 MYO5; myosin V D 104926382 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V D 104936392 myo5b; unconventional myosin-Vb K10357 MYO5; myosin V D 104938662 xiap; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 104940059 diablo homolog, mitochondrial isoform X1 K10522 DIABLO; diablo D 104919845 diablo homolog, mitochondrial isoform X1 K10522 DIABLO; diablo C Morphogenesis factors D 104935337 snx25; sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25 D 104929842 mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 109136624 mitochondrial Rho GTPase 1-A isoform X3 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 104935409 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 D 104924930 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 104934665 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 104930381 nedd4; E3 ubiquitin-protein ligase NEDD4 isoform X2 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 104926268 oxr1; oxidation resistance protein 1 isoform X2 K25437 OXR1; oxidation resistance protein 1 D 104937363 msto1; protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 104921371 atg2b; autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2 D 104925536 atg2a; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 104936450 atg3; ubiquitin-like-conjugating enzyme ATG3 isoform X3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 104926020 atg4b; cysteine protease ATG4B isoform X3 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 104932225 cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 104919028 atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 104926657 atg4d; cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 109138725 atg5; autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 104930972 becn1; beclin-1 K08334 BECN; beclin D 104919333 atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 104929025 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 104937788 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 104923964 gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 104933813 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 104917680 autophagy-related protein 9A isoform X1 K17907 ATG9; autophagy-related protein 9 D 104935281 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 109142683 atg10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 104929801 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12 D 104936576 atg14; beclin 1-associated autophagy-related key regulator isoform X1 K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 104932701 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 104929725 WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 104932088 wipi2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 104923262 wipi1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18 D 104938730 vacuolar protein 8-like K08332 VAC8; vacuolar protein 8 C Parkin-dependent mechanism factors D 104934697 prkn; LOW QUALITY PROTEIN: E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31] D 104919909 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 104917642 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 104937209 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 104933382 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 104936814 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 104938308 sqstm1; sequestosome-1 K14381 SQSTM1; sequestosome 1 D 104940563 tax1-binding protein 1 homolog A K21347 TAX1BP1; Tax1-binding protein 1 D 104927760 tax1bp1; tax1-binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1 D 104933436 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 104936096 activating molecule in BECN1-regulated autophagy protein 1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 104917973 atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13 D 104933467 serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 104920108 serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 104930671 ulk2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 104917671 rb1cc1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 104924694 heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG D 104924933 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 109136649 heat shock protein HSP 90-alpha isoform X1 K04079 HSP90A; molecular chaperone HtpG D 104936186 hsp90 co-chaperone Cdc37-like isoform X1 K09554 CDC37; cell division cycle protein 37 D 104918675 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 104929439 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 104932078 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 104933556 E3 ubiquitin-protein ligase SMURF2 isoform X2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 109142371 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 104923609 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 104937845 FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1 D 104934714 fundc1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 104924922 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 104919125 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 104938582 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 104936809 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A isoform X1 K10435 MAP1LC; microtubule-associated protein 1 light chain D 104927321 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 104934093 microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 109141895 next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 104928988 next to BRCA1 gene 1 protein-like isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 104918870 tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 104918049 tecpr1; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 104927205 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 104921328 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 104929770 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 104932149 coasy; bifunctional coenzyme A synthase isoform X2 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 104925446 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 104921432 cviiih19orf12; protein C19orf12 homolog K23168 MPAN; protein MPAN D 104923721 protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024