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  Mitochondrial Biogenesis - Leucoraja erinacea (little skate)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 11452178 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 11452179 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 11452185 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 11452187 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 11452186 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 11452188 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 11452176 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 11452177 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 11452180 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 11452181 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 11452184 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 11452182 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 11452183 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 129711321 polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 129704242 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 129694728 dimethyladenosine transferase 1, mitochondrial-like K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 129699849 LOW QUALITY PROTEIN: dimethyladenosine transferase 1, mitochondrial-like K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 129699465 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 129699778 mtif2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 129698065 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3 D 129714731 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 129695304 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 129703699 gfm1; elongation factor G, mitochondrial isoform X1 K02355 fusA; elongation factor G D 129709505 transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 129696168 mterf3; transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 129703474 mterf4; transcription termination factor 4, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 129697990 guf1; translation factor Guf1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 129696440 pop1; ribonucleases P/MRP protein subunit POP1 isoform X1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 129704995 pop4; ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 129709131 pop5; ribonuclease P/MRP protein subunit POP5 isoform X1 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 129703889 rpp30; ribonuclease P protein subunit p30 isoform X1 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 129695150 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 129695341 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 129713620 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 129709383 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 129695534 ube2r2; ubiquitin-conjugating enzyme E2 R2 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] D 129696607 uncharacterized protein LOC129696607 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] D 129697443 uncharacterized protein LOC129697443 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] D 129699607 uncharacterized protein LOC129699607 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] D 129700305 uncharacterized protein LOC129700305 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] D 129708172 rpp40; ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 129702897 tRNA methyltransferase 10 homolog C-like K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 129700229 prorp; mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 129706999 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 129708464 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 129706681 ptcd1; LOW QUALITY PROTEIN: pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 129695328 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 129705816 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 129714875 dhx30; ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 129707587 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 129696857 afg1lb; lactation elevated protein 1 homolog B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 129706400 atp23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 129704287 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 129696494 lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 129695241 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 129702317 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 129704457 ADP/ATP translocase 4-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 129713223 mitoferrin-1-like isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 129704124 mitoferrin-1-like isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 129694306 mitochondrial assembly of ribosomal large subunit protein 1-like K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 129712626 mitochondrial assembly of ribosomal large subunit protein 1-like K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 129710596 eral1; GTPase Era, mitochondrial K03595 era; GTPase D 129706152 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 129709772 yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 129701859 lars1b; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 129711233 lars2; probable leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 129701047 dars2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 129705705 gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 129701851 rars1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 129697459 rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 129696905 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial isoform X1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 129703980 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 129709126 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 129715123 mtpap; poly(A) RNA polymerase, mitochondrial isoform X1 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 129704460 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 129712871 mtg1; LOW QUALITY PROTEIN: mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 129695583 nitric oxide-associated protein 1-like K19832 NOA1; nitric oxide-associated protein 1 D 129702671 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 129700829 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 129704793 mitochondrial mRNA pseudouridine synthase RPUSD3-like isoform X1 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 129694651 pseudouridylate synthase RPUSD4, mitochondrial-like K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 129710646 rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 129713509 ngrn; neugrin K23496 NGRN; neugrin D 129712188 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 129698945 fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 129709246 mtrfr; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor D 129699338 rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 129702301 G-rich sequence factor 1-like K24984 GRSF1; G-rich sequence factor 1 D 129705561 mettl15; LOW QUALITY PROTEIN: probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 129696903 mtres1; mitochondrial transcription rescue factor 1 isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 129712504 polg; LOW QUALITY PROTEIN: DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 129708177 polg2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 D 129695245 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 129712068 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 129699525 mgme1; mitochondrial genome maintenance exonuclease 1 isoform X1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 129704101 twnk; twinkle protein, mitochondrial isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3] D 129700821 pif1; ATP-dependent DNA helicase PIF1 isoform X1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 129710255 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 129711522 atad3; ATPase family AAA domain containing 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 129708666 ubiquinol-cytochrome-c reductase complex assembly factor 2 isoform X1 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 129705007 dnaja2a; dnaJ homolog subfamily A member 2a K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 129707354 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 129708149 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 129695204 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 129695205 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 129695206 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 129695207 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 129695208 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 129695210 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 129700076 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 129712322 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 129712323 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 129710017 LOW QUALITY PROTEIN: AH receptor-interacting protein-like K17767 AIP; AH receptor-interacting protein D 129710842 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 129708546 mitochondrial import receptor subunit TOM40B-like isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 129702920 tomm70a; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 129696985 tomm20a; translocase of outer mitochondrial membrane 20 K17770 TOM20; mitochondrial import receptor subunit TOM20 D 129700210 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 129707939 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 129712682 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 129695605 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 129706169 sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family C Porin D 129701805 voltage-dependent anion-selective channel protein 1-like K05862 VDAC1; voltage-dependent anion channel protein 1 D 129712859 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 129713388 vdac3; voltage-dependent anion-selective channel protein 3 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 129694952 mtx3; metaxin-3 K17776 MTX; metaxin D 129698713 mtx2; metaxin-2 isoform X1 K17776 MTX; metaxin D 129710812 unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX D 129699752 marc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 129700211 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 129698349 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B isoform X1 K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 129704077 timm8a; LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 129716373 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 129711011 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 129704653 mitochondrial intermembrane space import and assembly protein 40-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 129706707 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 129711514 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 129705923 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 D 129711366 micos13; MICOS complex subunit MIC13 isoform X1 K24624 MICOS13; MICOS complex subunit MIC13 D 129707921 chchd3a; coiled-coil-helix-coiled-coil-helix domain containing 3a K17563 CHCHD3; MICOS complex subunit MIC19 D 129704687 MICOS complex subunit mic25a-like K17564 CHCHD6; MICOS complex subunit MIC25 D 129702770 MICOS complex subunit MIC26-like K24625 APOO; MICOS complex subunit MIC26 D 129702004 MICOS complex subunit MIC27-like isoform X1 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 129711514 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 129705923 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 129710499 timm22; LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 129713032 mitochondrial import inner membrane translocase subunit Tim23-like K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 129708681 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 129696744 timm21; mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 129714239 timm50; LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 129712941 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 129712940 micu1; calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial D 129698095 micu2; calcium uptake protein 2, mitochondrial isoform X1 K22828 MICU2; calcium uptake protein 2, mitochondrial D 129697128 calcium uniporter protein, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 129702676 LOW QUALITY PROTEIN: calcium uniporter regulatory subunit MCUb, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 129713768 smdt1b; single-pass membrane protein with aspartate-rich tail 1b K22830 SMDT1; essential MCU regulator, mitochondrial D 129708360 mcur1; mitochondrial calcium uniporter regulator 1 isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 129708270 letm1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 129705625 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 129706053 immp2l; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 129698231 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 129699274 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 129702726 mpc2b; mitochondrial pyruvate carrier 2b K22139 MPC2; mitochondrial pyruvate carrier 2 B Matrix C MMC/PAM proteins D 129711020 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 129701449 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 129701659 grpE protein homolog 2, mitochondrial-like isoform X1 K03687 GRPE; molecular chaperone GrpE D 129702857 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 129703206 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 C Other matrix factors D 129712087 pmpca; mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 129707806 pmpcb; mitochondrial-processing peptidase subunit beta isoform X1 K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 129698087 mitochondrial intermediate peptidase-like isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 129698663 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 129698665 hspe1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 129706893 dnaja3a; dnaJ heat shock protein family (Hsp40) member A3a isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 129704851 tamm41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 129712101 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 129710638 poldip2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 129698910 cyclic AMP-responsive element-binding protein 1-like isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 129695304 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 129703699 gfm1; elongation factor G, mitochondrial isoform X1 K02355 fusA; elongation factor G D 129694994 LOW QUALITY PROTEIN: transcription factor Sp1-like K04684 SP1; transcription factor Sp1 D 129700557 yy1a; transcriptional repressor protein YY1a K09201 YY; transcription factor YY D 129694531 gabpb2b; GA-binding protein subunit beta-2b K09454 GABPB; GA-binding protein transcription factor, beta D 129712680 gabpb1; GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 129704242 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 129707907 nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1 D 129698710 nfe2l2a; nuclear factor erythroid 2-related factor 2a isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 129705136 mt2; metallothionein-2 K14739 MT1_2; metallothionein 1/2 D 129697797 metallothionein-1-like K14739 MT1_2; metallothionein 1/2 C Coactivators D 129698870 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 129711090 CREB-regulated transcription coactivator 1-like isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 129713867 ep300b; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 129706899 CREB-binding protein-like isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 129707321 nfs1; cysteine desulfurase, mitochondrial isoform X1 K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 129709356 iscu; iron-sulfur cluster assembly enzyme ISCU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 129708183 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 129695517 fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 129698119 fdx1; adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial D 129702063 fdx1b; ferredoxin 1b K22071 FDX2; ferredoxin-2, mitochondrial D 129714347 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 129708384 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 129701449 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 129711152 hscb; LOW QUALITY PROTEIN: iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB D 129701450 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1 D 129700087 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 129695731 iron-sulfur cluster assembly 1 homolog, mitochondrial-like K22063 ISCA1; iron-sulfur cluster assembly 1 D 129711035 iron-sulfur cluster assembly 1 homolog, mitochondrial-like K22063 ISCA1; iron-sulfur cluster assembly 1 D 129700004 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 129714187 iba57; putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 129713001 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 129713274 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 129715203 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 129705322 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 129701655 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 129704099 sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 129704113 sfxn2; sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2 D 129704074 sfxn4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4 D 129694297 LOW QUALITY PROTEIN: sideroflexin-5-like K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 129713966 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 129705915 LOW QUALITY PROTEIN: carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 129707957 dhtkd1; 2-oxoadipate dehydrogenase complex component E1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 129697379 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 129704671 LOW QUALITY PROTEIN: host cell factor 1-like K14966 HCFC1; host cell factor 1 D 129706372 host cell factor 2-like K27390 HCFC2; host cell factor 2 D 129695389 htt; huntingtin isoform X1 K04533 HD; huntingtin D 129699718 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 129703060 nrip1a; LOW QUALITY PROTEIN: nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 129695268 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 129700987 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 129711025 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 129704215 sirt1; LOW QUALITY PROTEIN: NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 129699574 serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 129700499 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 129696709 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 isoform X1 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 129704640 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 129697373 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 129699268 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 129696162 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 129699596 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 129708313 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 129702893 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 129704828 acad9; LOW QUALITY PROTEIN: complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 129700292 nubpl; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning D 129712443 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 129696906 rtn4ip1; reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 129707347 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 129714226 sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 129705791 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 129696403 ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 129695678 lyrm7; complex III assembly factor LYRM7 isoform X1 K18170 LYRM7; complex III assembly factor LYRM7 D 129707587 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 129708666 ubiquinol-cytochrome-c reductase complex assembly factor 2 isoform X1 K17682 MNF1; mitochondrial nucleoid factor 1 D 129706780 ubiquinol-cytochrome-c reductase complex assembly factor 4 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 129704887 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 129706371 ubiquinol-cytochrome-c reductase complex assembly factor 6 isoform X1 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 129706084 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 129712153 cmc1; COX assembly mitochondrial protein homolog isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1 D 129705344 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 129710103 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1 D 129710272 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 129715976 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 129697860 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 129699452 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 129700921 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 129708102 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 129702118 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 129708399 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14 D 129714676 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14 D 129704143 LOW QUALITY PROTEIN: cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 129700380 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 129702544 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 129703528 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18 D 129706960 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 129699461 cytochrome c oxidase assembly protein COX20, mitochondrial isoform X1 K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 129706999 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 129714384 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 129699530 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 129712102 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 129708128 protein SCO1 homolog, mitochondrial-like isoform X1 K07152 SCO1; protein SCO1 D 129707836 protein SCO2 homolog, mitochondrial isoform X1 K23755 SCO2; protein SCO2 D 129710235 translational activator of cytochrome c oxidase 1-like isoform X1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 129699647 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 129700271 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1 D 129706084 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 129704887 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 129694177 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 129700822 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 129705505 ATP synthase mitochondrial F1 complex assembly factor 2-like K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 129706842 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 129696514 tmem70; transmembrane protein 70, mitochondrial isoform X1 K17966 TMEM70; transmembrane protein 70, mitochondrial D 129704185 atp5md; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 129703637 mitofusin-1-like K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 129711562 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 129703619 opa1; LOW QUALITY PROTEIN: dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 129714111 opa3; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein D 129709127 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 129703537 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 129706538 bcl-2 homologous antagonist/killer-like K14021 BAK; Bcl-2 homologous antagonist/killer D 129708611 bcl-2 homologous antagonist/killer-like K14021 BAK; Bcl-2 homologous antagonist/killer D 129705596 zgc:153993; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 129713845 apoptosis regulator BAX-like isoform X1 K02159 BAX; apoptosis regulator BAX D 129706151 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 129694118 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 129710385 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 129707058 small ubiquitin-related modifier 3-like isoform X1 K12160 SUMO; small ubiquitin-related modifier D 129708356 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 129700721 endophilin-B1-like isoform X1 K11248 SH3GLB1; endophilin-B1 D 129705922 mtch2; mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier D 129702208 mitochondrial fission factor-like K22076 MFF; mitochondrial fission factor D 129703286 mffa; mitochondrial fission factor homolog B isoform X1 K22076 MFF; mitochondrial fission factor D 129696517 gdap1; ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 129707482 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 129710287 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 129713922 mief1; mitochondrial dynamics protein MID51 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 129706854 pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 129712074 miga2; mitoguardin 2 isoform X1 K27289 MIGA; mitoguardin D 129700710 miga1; mitoguardin 1 isoform X1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 129696389 actin, non-muscle 6.2-like K05692 ACTB_G1; actin beta/gamma 1 D 129696393 actin, non-muscle 6.2-like isoform X1 K05692 ACTB_G1; actin beta/gamma 1 D 129696398 actin, non-muscle 6.2-like K05692 ACTB_G1; actin beta/gamma 1 D 129696400 actin, non-muscle 6.2-like K05692 ACTB_G1; actin beta/gamma 1 D 129696402 actin, non-muscle 6.2-like K05692 ACTB_G1; actin beta/gamma 1 D 129706670 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 129708303 actin, cytoplasmic type 5 K05692 ACTB_G1; actin beta/gamma 1 D 129694224 actin-2-like K05692 ACTB_G1; actin beta/gamma 1 D 129699322 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 129709151 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 129710373 phb; prohibitin K17080 PHB1; prohibitin 1 D 129700186 ktn1; kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 129706151 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 129712060 myo5b; unconventional myosin-Vb K10357 MYO5; myosin V D 129712575 LOW QUALITY PROTEIN: unconventional myosin-Va-like K10357 MYO5; myosin V D 129712576 unconventional myosin-Vc-like isoform X1 K10357 MYO5; myosin V D 129702043 E3 ubiquitin-protein ligase XIAP-like isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 129709389 diablo IAP-binding mitochondrial protein-like K10522 DIABLO; diablo C Morphogenesis factors D 129695238 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25 D 129708149 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 129705923 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 D 129709440 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 129694480 28S ribosomal protein S29, mitochondrial-like K17408 DAP3; small subunit ribosomal protein S29 D 129715785 28S ribosomal protein S29, mitochondrial-like K17408 DAP3; small subunit ribosomal protein S29 D 129712649 E3 ubiquitin-protein ligase NEDD4-like isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 129696081 oxidation resistance protein 1-like isoform X1 K25437 OXR1; oxidation resistance protein 1 D 129709896 si:ch211-15d5.11; nuclear receptor coactivator 7 K25437 OXR1; oxidation resistance protein 1 B Mitophagy factors C Autophagy-related proteins D 129700083 autophagy-related protein 2 homolog B-like isoform X1 K17906 ATG2; autophagy-related protein 2 D 129702721 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 129702354 atg4a; cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 129703461 atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 129701106 atg4c; cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 129714537 atg4da; cysteine protease atg4da K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 129696909 atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5 D 129710269 becn1; beclin-1 K08334 BECN; beclin D 129704853 atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 129705422 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 129696101 atg9b; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9 D 129693618 LOW QUALITY PROTEIN: autophagy-related protein 9A-like K17907 ATG9; autophagy-related protein 9 D 129695929 atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 129715772 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12 D 129700187 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 129703548 autophagy-related protein 16-1-like isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 129715979 autophagy-related protein 16-1-like K17890 ATG16L1; autophagy-related protein 16-1 D 129706655 wipi2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 D 129708278 wipi1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 129697417 uncharacterized protein LOC129697417 isoform X1 K08332 VAC8; vacuolar protein 8 C Parkin-dependent mechanism factors D 129699537 prkn; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31] D 129714742 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 129707029 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 129711510 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 129703537 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 129701581 sqstm1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1 D 129710113 tax1-binding protein 1 homolog B-like isoform X1 K21347 TAX1BP1; Tax1-binding protein 1 D 129711904 tax1bp1b; tax1-binding protein 1 homolog B isoform X1 K21347 TAX1BP1; Tax1-binding protein 1 D 129705862 activating molecule in BECN1-regulated autophagy protein 1-like isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 129705861 atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13 D 129710559 ulk2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 129696304 rb1cc1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 129697595 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 129700542 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG D 129714423 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 129706662 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 129708174 smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 129713308 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 129702714 fundc1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 129695268 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 129700987 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 129705464 map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 129699440 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 129707283 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 129715088 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 129710290 nbr1a; NBR1 autophagy cargo receptor a isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 129706929 tecpr1a; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 129700495 zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 129710051 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 129713941 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 129704973 protein C19orf12 homolog K23168 MPAN; protein MPAN D 129702198 fundc2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024