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Mitochondrial Biogenesis - Lynx rufus (bobcat)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 124527653 DNA-directed RNA polymerase, mitochondrial-like isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 124506826 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
D 124528885 mitochondrial dimethyladenosine transferase 1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 124510284 dimethyladenosine transferase 2, mitochondrial-like K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 124503649 translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 124511150 translation initiation factor IF-3, mitochondrial-like K02520 infC; translation initiation factor IF-3
D 124502062 elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 124518018 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 124518137 ribosome-releasing factor 2, mitochondrial-like K02355 fusA; elongation factor G
D 124526375 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 124524328 transcription termination factor 1, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 124501414 transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 124516241 transcription termination factor 4, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 124519040 transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 124520864 translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 124519070 ribonucleases P/MRP protein subunit POP1-like K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 124511278 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 124518414 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 124506987 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 124519200 ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 124501472 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 124508401 ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 124502473 ribonuclease P protein subunit p38-like K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 124528878 ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 124526831 tRNA methyltransferase 10 homolog C-like K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 124522283 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 124508910 mitochondrial ribonuclease P catalytic subunit-like K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 124513273 transcription elongation factor, mitochondrial-like isoform X1 K17658 TEFM; transcription elongation factor, mitochondrial
D 124519243 LOW QUALITY PROTEIN: pentatricopeptide repeat-containing protein 1, mitochondrial-like K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 124509690 pentatricopeptide repeat-containing protein 2, mitochondrial-like K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 124503550 pentatricopeptide repeat domain-containing protein 3, mitochondrial-like isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 124524000 ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 124503804 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 124528662 AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 124502080 mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 124506864 ATP-dependent RNA helicase SUPV3L1, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 124507707 endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 124517976 LOW QUALITY PROTEIN: ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 124513873 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 124520964 ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 124520991 ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 124509313 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 124520654 mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 124507049 mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 124523960 mitochondrial assembly of ribosomal large subunit protein 1-like K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 124513180 GTPase Era, mitochondrial isoform X1 K03595 era; GTPase
D 124514568 tyrosine--tRNA ligase, cytoplasmic isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 124502331 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 124517189 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 124524207 leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 124510210 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 124524322 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 124520463 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 124528350 probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 124528754 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 124520743 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 124518228 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial-like K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 124501409 poly(A) RNA polymerase, mitochondrial-like K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 124524326 2',5'-phosphodiesterase 12 isoform X1 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 124507262 mitochondrial ribosome-associated GTPase 1 isoform X1 K19828 MTG1; mitochondrial GTPase 1
D 124520175 nitric oxide-associated protein 1-like isoform X1 K19832 NOA1; nitric oxide-associated protein 1
D 124527062 tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 124516246 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 124523180 mitochondrial mRNA pseudouridine synthase RPUSD3-like K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 124505672 mitochondrial RNA pseudouridine synthase RPUSD4-like K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 124519276 RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 124517241 neugrin-like K23496 NGRN; neugrin
D 124504707 LOW QUALITY PROTEIN: mitochondrial mRNA pseudouridine synthase TRUB2-like K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 124516356 FAST kinase domain-containing protein 2, mitochondrial-like K18190 FASTKD2; FAST kinase domain-containing protein 2
D 124518544 mitochondrial translation release factor in rescue-like K23498 COXPD7; peptide chain release factor
D 124528294 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 124520113 G-rich sequence factor 1 isoform X1 K24984 GRSF1; G-rich sequence factor 1
D 124505830 12S rRNA N4-methylcytidine methyltransferase K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 124501441 MYG1 exonuclease K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 124528236 mitochondrial transcription rescue factor 1-like K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 124517249 DNA polymerase subunit gamma-1 isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 124513520 DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2
D 124520431 DNA-directed primase/polymerase protein-like isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 124504908 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 124503436 mitochondrial genome maintenance exonuclease 1-like K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 124526304 nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial
D 124507071 twinkle mtDNA helicase K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 124508501 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 124524497 single-stranded DNA-binding protein, mitochondrial isoform X1 K03111 ssb; single-strand DNA-binding protein
D 124514974 ATPase family AAA domain-containing protein 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 124528061 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 124511288 dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 124503564 mitochondrial import receptor subunit TOM34-like K17766 TOM34; mitochondrial import receptor subunit TOM34
D 124513062 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 124505172 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124526648 LOW QUALITY PROTEIN: heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124520272 LOW QUALITY PROTEIN: heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124527622 LOW QUALITY PROTEIN: heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124528066 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124528067 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124528068 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124504733 AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein
D 124519608 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 124511037 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 124521827 mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 124526445 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 124527209 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 124501360 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 124518656 mitochondrial import receptor subunit TOM20 homolog isoform X1 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 124512150 LOW QUALITY PROTEIN: TOMM20-like protein 1 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 124524836 mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 124528837 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 124520825 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
D 124501991 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 124501701 sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 124505439 LOW QUALITY PROTEIN: voltage-dependent anion-selective channel protein 1-like K05862 VDAC1; voltage-dependent anion channel protein 1
D 124515603 voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 124506927 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 124520533 voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 124518448 metaxin-3 K17776 MTX; metaxin
D 124521753 uncharacterized protein LOC124521753 isoform X1 K17776 MTX; metaxin
D 124515915 metaxin-2 K17776 MTX; metaxin
D 124513133 unconventional myosin-XIX-like isoform X1 K25838 MYO19; myosin XIX
D 124509137 armadillo repeat-containing X-linked protein 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1
D 124509138 armadillo repeat-containing X-linked protein 2-like K26188 ARMCX2; armadillo repeat-containing X-linked protein 2
D 124509586 armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3
D 124509584 protein ARMCX6-like K26190 ARMCX6; armadillo repeat-containing X-linked protein 6
D 124509936 mitochondrial amidoxime-reducing component 1-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 124510376 mitochondrial amidoxime reducing component 2-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 124524672 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 124512151 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 124527149 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 124506225 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 124505458 mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 124504883 mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 124509579 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 124523691 mitochondrial import inner membrane translocase subunit Tim13 isoform X1 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 124524742 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 124514015 mitochondrial intermembrane space import and assembly protein 40-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 124529116 mitochondrial intermembrane space import and assembly protein 40-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 124525514 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 124528523 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 124515573 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 124503335 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 124524746 MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 124523852 MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 124524817 MICOS complex subunit MIC25-like isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 124519625 LOW QUALITY PROTEIN: MICOS complex subunit MIC26-like K24625 APOO; MICOS complex subunit MIC26
D 124509419 MICOS complex subunit MIC26 isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 124509564 MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 124528523 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 124515573 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 124503335 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 124512993 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 124506960 mitochondrial import inner membrane translocase subunit Tim23 isoform X1 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 124510026 mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 124509519 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 124517134 mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 124511129 mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 124506896 calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial
D 124506893 calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 124510958 calcium uptake protein 2, mitochondrial-like K22828 MICU2; calcium uptake protein 2, mitochondrial
D 124520245 LOW QUALITY PROTEIN: calcium uniporter regulatory subunit MCUb, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 124502208 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 124528343 mitochondrial calcium uniporter regulator 1-like isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 124522627 mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 124505191 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 124523071 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 124517657 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A
D 124505431 transmembrane protein 126A isoform X1 K18157 TMEM126A; transmembrane protein 126A
D 124526729 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A
D 124521999 mitochondrial pyruvate carrier 1 isoform X1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 124509687 mitochondrial pyruvate carrier-like protein K22138 MPC1; mitochondrial pyruvate carrier 1
D 124510249 mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 124519839 coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial isoform X1 K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 124524597 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 124516194 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 124520101 grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 124521561 grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 124504107 mitochondrial import inner membrane translocase subunit TIM14-like K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 124526064 mitochondrial import inner membrane translocase subunit TIM14 isoform X1 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 124517989 mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 124522378 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 124523518 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 124510979 mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 124510280 60 kDa heat shock protein, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 124514784 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 124504806 LOW QUALITY PROTEIN: 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 124517939 dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 124524860 phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 124522358 DNL-type zinc finger protein-like K17808 ZIM17; mitochondrial protein import protein ZIM17
D 124511063 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 124513031 polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 124516566 cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 124518137 ribosome-releasing factor 2, mitochondrial-like K02355 fusA; elongation factor G
D 124526375 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 124502539 transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1
D 124512524 transcriptional repressor protein YY1 K09201 YY; transcription factor YY
D 124508596 GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 124516365 GA-binding protein subunit beta-2 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 124506826 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 124525019 nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 124514555 nuclear factor erythroid 2-related factor 2 isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 124511835 metallothionein-1 K14739 MT1_2; metallothionein 1/2
D 124511836 metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 124511837 metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 124511898 metallothionein-4 K14741 MT4; metallothionein 4
C Coactivators
D 124520204 peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 124510143 peroxisome proliferator-activated receptor gamma coactivator 1-beta-like K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 124507086 peroxisome proliferator-activated receptor gamma coactivator-related protein 1-like isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 124524056 CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 124517735 CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 124501617 histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 124504056 cysteine desulfurase, mitochondrial isoform X1 K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 124518254 iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 124528724 LYR motif-containing protein 4 isoform X1 K22069 LYRM4; LYR motif-containing protein 4
D 124528273 frataxin, mitochondrial-like K19054 FXN; frataxin [EC:1.16.3.1]
D 124505737 adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial
D 124523660 ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 124513440 NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 124516194 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 124518367 iron-sulfur cluster co-chaperone protein HscB-like isoform X1 K04082 hscB; molecular chaperone HscB
D 124516206 nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 124512541 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 124529127 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 124512308 iron-sulfur cluster assembly 2 homolog, mitochondrial isoform X1 K22072 ISCA2; iron-sulfur cluster assembly 2
D 124514319 putative transferase CAF17, mitochondrial isoform X1 K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 124504265 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 124514740 bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 124503417 bolA-like protein 3 isoform X1 K22075 BOLA3; BolA-like protein 3
D 124520230 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 124507073 sideroflexin-3 isoform X1 K23500 SFXN1_3; sideroflexin-1/3
D 124507103 sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2
D 124507180 sideroflexin-4-like K23502 SFXN4; sideroflexin-4
D 124504195 sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 124504618 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 124502379 carnitine O-palmitoyltransferase 1, muscle isoform isoform X1 K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 124510897 carnitine O-palmitoyltransferase 1, brain isoform K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
D 124501743 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial isoform X1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 124527927 F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 124525826 host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1
D 124501078 host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2
D 124522605 huntingtin K04533 HD; huntingtin
D 124505142 steroid hormone receptor ERR1 isoform X1 K08552 NR3B1; estrogen-related receptor alpha
D 124512424 steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 124510380 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 124526615 nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 124521983 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 124515130 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 124523873 lon protease homolog, mitochondrial isoform X1 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 124506847 NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 124528890 protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 124509495 protein UXT K26537 UXT; protein UXT
D 124516269 PGC-1 and ERR-induced regulator in muscle protein 1-like isoform X1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 124508691 complex I intermediate-associated protein 30, mitochondrial-like isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 124517525 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2-like K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 124522916 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 isoform X1 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 124528580 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 124504212 arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 124518958 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 124503408 protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 124522590 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8-like K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 124505855 complex I assembly factor TMEM126B, mitochondrial-like isoform X1 K18165 TMEM126B; complex I assembly factor TMEM126B
D 124524471 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial-like K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 124523895 complex I assembly factor ACAD9, mitochondrial isoform X1 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 124508889 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 124505832 FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 124527931 reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 124526385 complex I assembly factor TIMMDC1, mitochondrial-like K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 124511201 succinate dehydrogenase assembly factor 1, mitochondrial-like K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 124505585 succinate dehydrogenase assembly factor 2, mitochondrial isoform X1 K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 124515383 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 124519630 tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 124515375 complex III assembly factor LYRM7 isoform X1 K18170 LYRM7; complex III assembly factor LYRM7
D 124503804 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 124528061 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 124505575 ubiquinol-cytochrome-c reductase complex assembly factor 3-like K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 124525505 protein CCSMST1-like K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 124524985 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 124502106 protein BRAWNIN K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 124524145 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 124526033 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 124511514 COX assembly mitochondrial protein 2 homolog isoform X1 K18172 CMC2; COX assembly mitochondrial protein 2
D 124513804 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 124523388 LOW QUALITY PROTEIN: cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 124522079 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 124506493 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 124504209 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 124518727 cytochrome c oxidase assembly factor 6 homolog isoform X1 K18179 COA6; cytochrome c oxidase assembly factor 6
D 124515369 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 124519571 protoheme IX farnesyltransferase, mitochondrial-like K02257 COX10; heme o synthase [EC:2.5.1.141]
D 124513215 cytochrome c oxidase assembly protein COX11, mitochondrial-like K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 124502171 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 124507052 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 124512070 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 124526798 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 124520547 cytochrome c oxidase assembly protein COX18, mitochondrial-like isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18
D 124519260 cytochrome c oxidase assembly protein COX19 isoform X1 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 124510278 cytochrome c oxidase assembly protein COX20, mitochondrial-like isoform X1 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 124524635 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 124503600 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 124508804 mitochondrial inner membrane protein OXA1L isoform X1 K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 124522427 surfeit locus protein 1 isoform X1 K14998 SURF1; surfeit locus 1 family protein
D 124519605 protein SCO1 homolog, mitochondrial-like K07152 SCO1; protein SCO1
D 124501287 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 124513546 translational activator of cytochrome c oxidase 1-like K18189 TACO1; translational activator of cytochrome c oxidase 1
D 124503629 leucine-rich PPR motif-containing protein, mitochondrial-like K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 124512487 cytochrome c oxidase assembly factor 8-like K23506 APOPT1; apoptogenic protein 1
D 124524145 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 124524985 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 124504761 transmembrane protein 223-like K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 124515493 ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 124519544 ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 124507725 transmembrane protein 70, mitochondrial-like K17966 TMEM70; transmembrane protein 70, mitochondrial
D 124512481 ATP synthase subunit ATP5MJ, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 124513331 ATP synthase subunit ATP5MJ, mitochondrial-like K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 124527136 ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 124506007 ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 124520691 ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 124507118 ATP synthase membrane subunit K, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 124515857 ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 124502897 ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 124527016 mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 124514778 mitofusin-2 isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 124525914 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 124511016 optic atrophy 3 protein-like K23166 OPA3; optic atrophy 3 protein
D 124511717 optic atrophy 3 protein-like K23166 OPA3; optic atrophy 3 protein
D 124518230 TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 124526371 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 124528274 bcl-2 homologous antagonist/killer K14021 BAK; Bcl-2 homologous antagonist/killer
D 124510927 apoptosis regulator BAX isoform X1 K02159 BAX; apoptosis regulator BAX
D 124502329 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 124519148 mitochondrial fission 1 protein isoform X1 K17969 FIS1; mitochondrial fission 1 protein
D 124525006 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier
D 124526546 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 124512876 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 124519943 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier
D 124527229 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 124513429 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 124514026 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 124521019 small ubiquitin-related modifier 2-like isoform X1 K12160 SUMO; small ubiquitin-related modifier
D 124515681 small ubiquitin-related modifier 1 isoform X1 K12160 SUMO; small ubiquitin-related modifier
D 124516214 endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1
D 124505269 mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier
D 124528324 mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier
D 124514731 mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor
D 124507427 ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 124502944 ganglioside-induced differentiation-associated protein 1-like 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 124522103 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 124519622 mitochondrial dynamics protein MID49-like isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 124501349 mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 124519492 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 124515599 mitoguardin 1 K27289 MIGA; mitoguardin
D 124504964 mitoguardin 2 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 124519153 actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 124522513 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 124503326 N-alpha-acetyltransferase 20 isoform X1 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 124518301 N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 124513252 prohibitin 1 isoform X1 K17080 PHB1; prohibitin 1
D 124502107 prohibitin-2 isoform X1 K17081 PHB2; prohibitin 2
D 124512165 kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 124502329 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 124508239 unconventional myosin-Vc K10357 MYO5; myosin V
D 124508579 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
D 124517035 unconventional myosin-Vb K10357 MYO5; myosin V
D 124513901 E3 ubiquitin-protein ligase XIAP isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 124518140 diablo IAP-binding mitochondrial protein K10522 DIABLO; diablo
C Morphogenesis factors
D 124520754 sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 124513062 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 124503335 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 124518316 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 124521677 28S ribosomal protein S29, mitochondrial-like isoform X1 K17408 DAP3; small subunit ribosomal protein S29
D 124508566 E3 ubiquitin-protein ligase NEDD4-like isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 124519062 oxidation resistance protein 1 isoform X1 K25437 OXR1; oxidation resistance protein 1
D 124521681 protein misato homolog 1-like K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 124504821 autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 124512539 autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 124527092 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 124513997 cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 124514856 cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 124516031 cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 124523317 cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 124528571 autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 124522135 beclin-1 isoform X1 K08334 BECN; beclin
D 124509901 beclin-2-like K08334 BECN; beclin
D 124524150 ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 124511498 gamma-aminobutyric acid receptor-associated protein-like 2 isoform X1 K08341 GABARAP; GABA(A) receptor-associated protein
D 124519445 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 124501727 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 124524466 autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 124516492 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 124518634 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 124515075 ubiquitin-like protein ATG12 isoform X1 K08336 ATG12; ubiquitin-like protein ATG12
D 124512167 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 124516639 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 124506402 protein Atg16l2-like isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 124519163 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 124513492 WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 124528391 E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 124501445 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 124518086 protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 124514764 serine/threonine-protein kinase PINK1, mitochondrial-like K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 124526371 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 124514696 sequestosome-1 K14381 SQSTM1; sequestosome 1
D 124524708 tax1-binding protein 1 homolog isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 124513268 calcium-binding and coiled-coil domain-containing protein 2-like isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 124506277 activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 124504650 autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 124527799 serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 124519653 serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 124507640 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 124512510 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 124528527 heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 124526507 LOW QUALITY PROTEIN: hsp90 co-chaperone Cdc37-like K09554 CDC37; cell division cycle protein 37
D 124524103 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 124519102 E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 124513516 E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 124520165 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 124509469 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 124521983 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 124515130 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 124517357 microtubule-associated proteins 1A/1B light chain 3B-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 124503829 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 124511562 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 124509804 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 124509809 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 124522153 next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 124519129 tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 124512057 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 124522113 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 124501042 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 124511906 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 124527631 FUN14 domain-containing protein 2-like K24308 FUNDC2; FUN14 domain-containing protein 2
D 124502955 FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024