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Mitochondrial Biogenesis - Mustela lutreola (European mink)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 131838643 LOW QUALITY PROTEIN: NADH-ubiquinone oxidoreductase chain 5-like K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 131838648 NADH-ubiquinone oxidoreductase chain 6-like K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 131823150 POLRMT; DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 131828949 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 131833435 TFB1M; dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 131814295 TFB2M; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 131840137 MTIF2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 131814094 MTIF3; translation initiation factor IF-3, mitochondrial isoform X1 K02520 infC; translation initiation factor IF-3
D 131838532 TSFM; elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts
D 131819439 TUFM; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 131824937 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 131832354 GFM2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 131839380 MTERF2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 131829361 MTERF1; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 131826576 MTERF3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 131827254 MTERF4; transcription termination factor 4, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 131824427 GUF1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 131826563 POP1; ribonucleases P/MRP protein subunit POP1 isoform X1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 131818780 ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 131810889 POP5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 131828666 RPP30; ribonuclease P protein subunit p30 isoform X1 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 131819756 POP7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 131812343 RPP25L; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 131835768 RPP25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 131838253 RPP38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 131834483 RPP40; ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 131825185 TRMT10C; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 131822124 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 isoform X1 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 131836463 PRORP; mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 131828830 MSS51; putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 131816487 TEFM; transcription elongation factor, mitochondrial isoform X1 K17658 TEFM; transcription elongation factor, mitochondrial
D 131819929 PTCD1; pentatricopeptide repeat-containing protein 1, mitochondrial isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 131832333 PTCD2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 131840401 PTCD3; small ribosomal subunit protein mS39 isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 131823878 DHX30; ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 131807761 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 131833538 AFG1L; AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 131838534 ATP23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 131828886 SUPV3L1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 131826724 LACTB2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 131820320 SLC25A4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 131828020 SLC25A31; ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 131821117 SLC25A5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 131821316 SLC25A6; ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 131833988 SLC25A37; mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 131828560 SLC25A28; mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 131829503 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 131816489 ERAL1; GTPase Era, mitochondrial isoform X1 K03595 era; GTPase
D 131838890 YARS2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 131810320 YARS1; tyrosine--tRNA ligase, cytoplasmic isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 131823833 LARS2; leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 131832209 LARS1; leucine--tRNA ligase, cytoplasmic isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 131814656 DARS2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 131829575 GARS1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 131833619 RARS2; probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 131831885 RARS1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 131833555 QRSL1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial isoform X1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 131832468 GATB; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 131811811 GATC; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 131838104 MTPAP; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 131824059 PDE12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 131830491 MTG1; mitochondrial ribosome-associated GTPase 1 isoform X1 K19828 MTG1; mitochondrial GTPase 1
D 131823733 NOA1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 131825225 NSUN3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 131809695 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 131824201 RPUSD3; mitochondrial mRNA pseudouridine synthase RPUSD3 isoform X1 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 131838361 RPUSD4; pseudouridylate synthase RPUSD4, mitochondrial isoform X1 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 131819555 RCC1L; RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 131835592 NGRN; neugrin K23496 NGRN; neugrin
D 131812384 TRUB2; pseudouridylate synthase TRUB2, mitochondrial isoform X1 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 131827528 FASTKD2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 131810880 MTRFR; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 131833455 RMND1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 131823363 GRSF1; G-rich sequence factor 1 isoform X1 K24984 GRSF1; G-rich sequence factor 1
D 131810761 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 131838698 MYG1; MYG1 exonuclease K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 131825685 MYG1 exonuclease-like K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 131833550 MTRES1; mitochondrial transcription rescue factor 1 isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 131835617 POLG; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 131816458 POLG2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2
D 131820363 PRIMPOL; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 131813022 ENDOG; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 131808150 MGME1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 131824360 EXOG; nuclease EXOG, mitochondrial isoform X1 K15050 EXOG; nuclease EXOG, mitochondrial
D 131828534 TWNK; twinkle mtDNA helicase isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 131835924 PIF1; ATP-dependent DNA helicase PIF1 isoform X1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 131829860 SSBP1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 131808826 ATPase family AAA domain-containing protein 3 isoform X1 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 131834232 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 131818228 DNAJA2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 131807583 TOMM34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 131815748 RHOT1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 131837691 HSPA8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 131833881 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 131834338 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 131834339 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 131834340 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 131832001 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 131816580 AIP; AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein
D 131816648 AIPL1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 131814325 TOMM40L; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 131818109 TOMM40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 131825197 TOMM70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 131839484 TOMM22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 131818203 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 131836620 TOMM20L; TOMM20-like protein 1 isoform X1 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 131813642 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 131813646 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 131813648 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 131813654 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 131813656 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 131829057 TOMM20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 131832218 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 131829494 TOMM7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 131833961 TOMM6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 131812450 TOMM5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 131839594 SAMM50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 131836545 voltage-dependent anion-selective channel protein 1-like K05862 VDAC1; voltage-dependent anion channel protein 1
D 131832037 VDAC1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 131828797 VDAC2; LOW QUALITY PROTEIN: voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 131820455 VDAC3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
D 131832988 voltage-dependent anion-selective channel protein 3-like K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 131827053 MTX2; metaxin-2 isoform X1 K17776 MTX; metaxin
D 131814946 MTX1; metaxin-1 isoform X1 K17776 MTX; metaxin
D 131832401 MTX3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 131816086 MYO19; unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX
D 131821725 ARMCX2; armadillo repeat-containing X-linked protein 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2
D 131821523 ARMCX3; armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3
D 131821013 ARMCX6; LOW QUALITY PROTEIN: protein ARMCX6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6
D 131814333 mitochondrial amidoxime-reducing component 1 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 131814334 MTARC2; mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 131836623 TIMM9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 131835380 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 131812784 TIMM10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 131808616 TIMM10B; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 131835943 TIMM8B; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 131821272 TIMM8A; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 131823249 TIMM13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 131824265 CHCHD4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 131819899 GFER; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 131809317 MICOS10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 131840400 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 131823355 MICOS13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 131829783 CHCHD3; MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 131824314 CHCHD6; MICOS complex subunit MIC25 isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 131821569 APOO; MICOS complex subunit MIC26 isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 131825137 MICOS complex subunit MIC26-like K24625 APOO; MICOS complex subunit MIC26
D 131825617 MICOS complex subunit MIC26-like K24625 APOO; MICOS complex subunit MIC26
D 131836134 MICOS complex subunit MIC27-like K24626 APOOL; MICOS complex subunit MIC27
D 131821243 APOOL; MICOS complex subunit MIC27 isoform X1 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 131809317 MICOS10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 131840400 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 131816019 TIMM22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 131828709 TIMM23B; mitochondrial import inner membrane translocase subunit Tim23B K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 131814790 TIMM17A; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 131822171 TIMM17B; mitochondrial import inner membrane translocase subunit Tim17-B isoform X1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 131809536 mitochondrial import inner membrane translocase subunit Tim17-A-like K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 131811772 TIMM21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 131818292 TIMM50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 131828840 MCU; calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial
D 131828844 MICU1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 131813935 MICU2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 131829371 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial isoform X1 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 131839560 SMDT1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 131834710 MCUR1; mitochondrial calcium uniporter regulator 1 isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 131827143 LETM1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 131810896 IMMP1L; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 131829632 IMMP2L; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 131839896 TMEM126A; transmembrane protein 126A isoform X1 K18157 TMEM126A; transmembrane protein 126A
D 131814604 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A
D 131822188 MPC1L; mitochondrial pyruvate carrier 1-like protein K22138 MPC1; mitochondrial pyruvate carrier 1
D 131833374 MPC1; mitochondrial pyruvate carrier 1 isoform X1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 131815296 MPC2; mitochondrial pyruvate carrier 2 isoform X1 K22139 MPC2; mitochondrial pyruvate carrier 2
D 131811533 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 131823424 TIMM44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 131832100 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 131826569 GRPEL1; grpE protein homolog 1, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE
D 131814568 LOW QUALITY PROTEIN: grpE protein homolog 1, mitochondrial-like K03687 GRPE; molecular chaperone GrpE
D 131831749 GRPEL2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 131824832 DNAJC19; mitochondrial import inner membrane translocase subunit TIM14 isoform X1 K09539 DNAJC19; DnaJ homolog subfamily C member 19
C Other matrix factors
D 131812058 PMPCA; mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 131829280 PMPCB; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 131813543 MIPEP; mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 131833857 LOW QUALITY PROTEIN: 60 kDa heat shock protein, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 131827612 HSPD1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 131819935 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 131808458 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 131819308 DNAJA3; dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 131824230 TAMM41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 131813193 DNLZ; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 131817855 ETHE1; persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 131815599 POLDIP2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 131827517 CREB1; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 131824937 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 131832354 GFM2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 131838694 SP1; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 131836984 YY1; transcriptional repressor protein YY1 K09201 YY; transcription factor YY
D 131821140 YY2; transcription factor YY2 K09201 YY; transcription factor YY
D 131836274 GABPB1; GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 131810338 GABPB2; GA-binding protein subunit beta-2 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 131828949 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 131829755 NRF1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 131827050 NFE2L2; nuclear factor erythroid 2-related factor 2 isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 131838098 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 131818505 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 131818555 metallothionein-1 K14739 MT1_2; metallothionein 1/2
D 131833860 metallothionein-1-like K14739 MT1_2; metallothionein 1/2
D 131824082 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 131817991 metallothionein-1-like K14739 MT1_2; metallothionein 1/2
D 131817622 uncharacterized protein LOC131817622 K14740 MT3; metallothionein 3
D 131818554 MT4; metallothionein-4 K14741 MT4; metallothionein 4
C Coactivators
D 131825299 PPARGC1A; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 131831755 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 131828509 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 131823782 CRTC1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 131839523 EP300; histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 131819828 CREBBP; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 131807749 NFS1; cysteine desulfurase K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 131811474 ISCU; iron-sulfur cluster assembly enzyme ISCU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 131812359 iron-sulfur cluster assembly enzyme ISCU-like K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 131834486 LYRM4; LYR motif-containing protein 4 isoform X1 K22069 LYRM4; LYR motif-containing protein 4
D 131812392 FXN; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 131835558 FDX1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 131823514 FDX2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 131816440 FDXR; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 131832100 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 131811320 HSCB; iron-sulfur cluster co-chaperone protein HscB isoform X1 K04082 hscB; molecular chaperone HscB
D 131832103 SIL1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 131836954 GLRX5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 131812827 ISCA1; iron-sulfur cluster assembly 1 homolog, mitochondrial isoform X1 K22063 ISCA1; iron-sulfur cluster assembly 1
D 131836875 ISCA2; iron-sulfur cluster assembly 2 homolog, mitochondrial isoform X1 K22072 ISCA2; iron-sulfur cluster assembly 2
D 131832721 IBA57; putative transferase CAF17, mitochondrial isoform X1 K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 131840248 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 131824599 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 131809453 BOLA1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 131840317 BOLA3; bolA-like protein 3 isoform X1 K22075 BOLA3; BolA-like protein 3
D 131828530 SFXN3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 131831934 SFXN1; sideroflexin-1 isoform X1 K23500 SFXN1_3; sideroflexin-1/3
D 131828500 SFXN2; sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2
D 131830629 SFXN4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4
D 131840293 SFXN5; sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 131816881 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 131839669 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 131817459 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
D 131838283 DHTKD1; 2-oxoadipate dehydrogenase complex component E1 isoform X1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 131833581 FBXL4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 131820835 HCFC1; host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1
D 131839346 HCFC2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2
D 131826799 HTT; huntingtin isoform X1 K04533 HD; huntingtin
D 131814664 ESRRA; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 131836845 ESRRB; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 131814309 ESRRG; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 131825259 NRIP1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 131808931 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 131831692 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 131823353 LONP1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 131828905 SIRT1; NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 131833420 SERAC1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 131820862 UXT; protein UXT K26537 UXT; protein UXT
D 131810386 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 131836137 NDUFAF1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 131832269 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 131823916 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 isoform X1 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 131833587 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 131808118 NDUFAF5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 131826585 NDUFAF6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 131840523 NDUFAF7; protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 131839918 TMEM126B; LOW QUALITY PROTEIN: complex I assembly factor TMEM126B, mitochondrial K18165 TMEM126B; complex I assembly factor TMEM126B
D 131823562 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 131824276 ACAD9; complex I assembly factor ACAD9, mitochondrial isoform X1 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 131836436 NUBPL; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 131838347 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 131837244 reticulon-4-interacting protein 1, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 131833556 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 131825090 TIMMDC1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 131817759 SDHAF1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 131813616 SDHAF2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 131827453 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 131816859 TTC19; tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 131832005 LYRM7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 131807761 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 131834232 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 131814066 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 131819715 ubiquinol-cytochrome-c reductase complex assembly factor 4 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 131824023 ubiquinol-cytochrome-c reductase complex assembly factor 5 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 131839358 ubiquinol-cytochrome-c reductase complex assembly factor 6 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 131831670 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 131824465 CMC1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 131817979 CMC2; COX assembly mitochondrial protein 2 homolog isoform X1 K18172 CMC2; COX assembly mitochondrial protein 2
D 131815802 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 131807553 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 131808579 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 131829071 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 131809767 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 131815781 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 131816775 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 131838782 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 131828558 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 131836747 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 131825084 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 131823284 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18
D 131819095 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 131815043 cytochrome c oxidase assembly protein COX20, mitochondrial isoform X1 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 131828830 MSS51; putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 131823446 protein PET100 homolog, mitochondrial isoform X1 K18186 PET100; protein PET100, animal type
D 131808155 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 131836347 OXA1L; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 131812930 surfeit locus protein 1 isoform X1 K14998 SURF1; surfeit locus 1 family protein
D 131815588 protein SCO1 homolog, mitochondrial isoform X1 K07152 SCO1; protein SCO1
D 131839668 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 131815545 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 131808531 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 131837036 cytochrome c oxidase assembly factor 8 isoform X1 K23506 APOPT1; apoptogenic protein 1
D 131820672 cytochrome c oxidase assembly factor 8-like K23506 APOPT1; apoptogenic protein 1
D 131831670 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 131824023 ubiquinol-cytochrome-c reductase complex assembly factor 5 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 131814233 TMEM223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 131810367 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 131817092 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 131826699 TMEM70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 131837039 ATP5MJ; ATP synthase subunit ATP5MJ, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 131820556 LOW QUALITY PROTEIN: ATP synthase subunit ATP5MJ, mitochondrial-like K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 131828063 ATP synthase subunit ATP5MJ, mitochondrial-like K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 131815947 ATP synthase subunit ATP5MJ, mitochondrial-like K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 131840560 ATP synthase membrane subunit K, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 131828483 ATP5MK; ATP synthase membrane subunit K, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 131824845 MFN1; mitofusin-1 isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 131809290 MFN2; mitofusin-2 isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 131824716 OPA1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 131818797 OPA3; optic atrophy 3 protein isoform X1 K23166 OPA3; optic atrophy 3 protein
D 131811814 TRIAP1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 131824812 PARL; presenilin-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 131834235 BAK1; bcl-2 homologous antagonist/killer isoform X1 K14021 BAK; Bcl-2 homologous antagonist/killer
D 131817775 BAX; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 131838889 DNM1L; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 131819149 FIS1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 131827564 SUMO1; small ubiquitin-related modifier 1 isoform X1 K12160 SUMO; small ubiquitin-related modifier
D 131821633 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier
D 131829146 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 131816199 SUMO2; small ubiquitin-related modifier 2 isoform X1 K12160 SUMO; small ubiquitin-related modifier
D 131832395 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 131825141 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 131825468 SUMO3; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 131808823 SH3GLB1; endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1
D 131833898 MTCH1; mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier
D 131812599 MTCH2; mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier
D 131827374 MFF; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor
D 131826694 GDAP1; ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 131807595 GDAP1L1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 131815996 VAT1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 131839498 MIEF1; mitochondrial dynamics protein MIEF1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 131815670 MIEF2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 131816843 PLD6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 131812463 MIGA2; mitoguardin 2 K27289 MIGA; mitoguardin
D 131809010 MIGA1; mitoguardin 1 isoform X1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 131820100 ACTB; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 131816144 ACTG1; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 131808178 NAA20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 131811575 NAA25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 131816360 PHB1; prohibitin 1 K17080 PHB1; prohibitin 1
D 131838478 PHB2; prohibitin-2 isoform X1 K17081 PHB2; prohibitin 2
D 131836603 KTN1; kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 131838889 DNM1L; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 131836298 MYO5C; unconventional myosin-Vc isoform X1 K10357 MYO5; myosin V
D 131836301 MYO5A; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
D 131810870 MYO5B; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 131822235 XIAP; E3 ubiquitin-protein ligase XIAP isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 131811910 DIABLO; diablo IAP-binding mitochondrial protein isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 131820313 SNX25; sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 131815748 RHOT1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 131840400 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 131811765 MTFP1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 131815218 DAP3; small ribosomal subunit protein mS29 isoform X1 K17408 DAP3; small subunit ribosomal protein S29
D 131835843 NEDD4; E3 ubiquitin-protein ligase NEDD4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 131826506 OXR1; oxidation resistance protein 1 isoform X1 K25437 OXR1; oxidation resistance protein 1
D 131814823 MSTO1; protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 131836963 ATG2B; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 131815013 ATG2A; autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 131828077 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 131832326 LOW QUALITY PROTEIN: ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 131825135 ATG3; ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 131827238 ATG4B; LOW QUALITY PROTEIN: cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 131820790 ATG4A; cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 131823524 ATG4D; cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 131809260 ATG4C; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 131833557 ATG5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 131815214 BECN2; beclin-2 K08334 BECN; beclin
D 131816325 BECN1; beclin-1 isoform X1 K08334 BECN; beclin
D 131824226 ATG7; ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 131839055 GABARAPL1; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 131818699 GABARAPL2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 131815738 GABARAP; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 131827426 ATG9A; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 131829937 ATG9B; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 131832422 ATG10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 131832603 ATG12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 131836601 ATG14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 131827318 ATG16L1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 131807753 ATG16L2; protein Atg16l2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 131819416 WIPI2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
D 131816133 WIPI1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 131833389 PRKN; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31]
D 131838605 RNF41; E3 ubiquitin-protein ligase NRDP1 isoform X1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 131819781 CLEC16A; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 131810414 PINK1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 131824812 PARL; presenilin-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 131832651 SQSTM1; sequestosome-1 K14381 SQSTM1; sequestosome 1
D 131829551 TAX1BP1; tax1-binding protein 1 isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 131831115 ANXA2R; LOW QUALITY PROTEIN: annexin-2 receptor K21347 TAX1BP1; Tax1-binding protein 1
D 131815783 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 131812046 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 131812082 ATG13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 131811225 ULK1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 131817041 serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 131826840 RB1CC1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 131837003 HSP90AA1; heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 131834029 HSP90AB1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 131827404 LOW QUALITY PROTEIN: heat shock protein HSP 90-alpha-like K04079 HSP90A; molecular chaperone HtpG
D 131832553 LOW QUALITY PROTEIN: heat shock protein HSP 90-alpha-like K04079 HSP90A; molecular chaperone HtpG
D 131823519 CDC37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 131820095 SMURF1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 131816965 SMURF2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 131834386 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 131833082 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 131833248 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 131821577 FUNDC1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 131808931 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 131831692 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 131818770 MAP1LC3B; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 131814292 MAP1LC3C; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 131807814 MAP1LC3A; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 131816812 NBR1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 131819732 TECPR1; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 131836907 ZFYVE1; zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 131817100 COASY; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 131839467 PLA2G6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 131818781 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 131818782 protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN
D 131818783 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 131818327 C16H19orf12; protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN
D 131820878 FUNDC2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024