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Mitochondrial Biogenesis - Macaca thibetana thibetana (Pere David's macaque)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 126947324 NADH-ubiquinone oxidoreductase chain 5-like K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 126942933 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 126962161 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
D 126952350 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 126943347 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 126934147 translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 126940749 translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 126930383 EEF1A lysine methyltransferase 3 isoform X1 K02357 tsf; elongation factor Ts
D 126944446 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 126948272 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 126956510 ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 126931484 transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 126932820 transcription termination factor 4, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 126949913 transcription termination factor 1, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 126960827 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 126955243 translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 126961139 ribonucleases P/MRP protein subunit POP1 isoform X1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 126943627 ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 126930702 ribonuclease P/MRP protein subunit POP5 isoform X1 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 126963419 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 126950427 ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 126937428 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 126960022 ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 126962857 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 126962397 ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 126951965 ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 126947862 tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 126946552 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 126959162 mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 126962431 putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 126938994 transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 126950459 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 126956543 pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 126933398 pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 126948630 ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 126964261 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 126953629 AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 126930410 mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 126963160 ATP-dependent RNA helicase SUPV3L1, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 126961473 endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 126946121 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 126946856 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 126947143 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 126955617 ADP/ATP translocase 4 isoform X1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 126955724 ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 126960559 mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 126963396 mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 126950026 mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 126938734 GTPase Era, mitochondrial K03595 era; GTPase
D 126931687 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 126957418 tyrosine--tRNA ligase, cytoplasmic isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 126948557 leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 126956769 leucine--tRNA ligase, cytoplasmic isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 126941010 aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 126950070 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 126952925 probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 126957132 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 126952299 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 126955229 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 126930704 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 126963357 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 126948803 2',5'-phosphodiesterase 12 isoform X1 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 126963301 mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 126955059 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 126947880 tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 126947720 mitochondrial mRNA pseudouridine synthase RPUSD3 isoform X1 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 126934862 pseudouridylate synthase RPUSD4, mitochondrial K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 126950365 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 126937051 neugrin-like K23496 NGRN; neugrin
D 126958923 neugrin K23496 NGRN; neugrin
D 126937031 pseudouridylate synthase TRUB2, mitochondrial isoform X1 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 126932008 FAST kinase domain-containing protein 1, mitochondrial isoform X1 K27754 FASTKD1; FAST kinase domain-containing protein 1
D 126932932 FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 126956058 FAST kinase domain-containing protein 3, mitochondrial K27755 FASTKD3; FAST kinase domain-containing protein 3
D 126950162 FAST kinase domain-containing protein 4 isoform X1 K27756 TBRG4; FAST kinase domain-containing protein 4
D 126929393 FAST kinase domain-containing protein 5, mitochondrial K27757 FASTKD5; FAST kinase domain-containing protein 5
D 126930701 mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 126952373 required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 126955132 G-rich sequence factor 1 isoform X1 K24984 GRSF1; G-rich sequence factor 1
D 126934662 12S rRNA N4-methylcytidine (m4C) methyltransferase isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 126931164 MYG1 exonuclease K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 126936836 mitochondrial transcription rescue factor 1-like K26186 MTRES1; mitochondrial transcription rescue factor 1
D 126951696 mitochondrial transcription rescue factor 1-like K26186 MTRES1; mitochondrial transcription rescue factor 1
D 126952313 mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 126958901 DNA polymerase subunit gamma-1 isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 126938350 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 126955292 DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 126937048 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 126929189 mitochondrial genome maintenance exonuclease 1 isoform X1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 126947576 nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial
D 126963068 twinkle mtDNA helicase isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 126958013 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 126949657 single-stranded DNA-binding protein, mitochondrial isoform X1 K03111 ssb; single-strand DNA-binding protein
D 126939042 LOW QUALITY PROTEIN: ATPase family AAA domain-containing protein 3C-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 126951593 LOW QUALITY PROTEIN: ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 126963043 ATPase family AAA domain-containing protein 3C-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 126939909 C16H17orf80; uncharacterized protein C17orf80 homolog isoform X1 K27759 MTNAP1; mitochondrial nucleoid-associated protein 1
D 126951613 GTPase IMAP family member 5 K27758 GIMAP1_3_5; GTPase IMAP family member 1/3/5
D 126951616 GTPase IMAP family member 1 K27758 GIMAP1_3_5; GTPase IMAP family member 1/3/5
D 126951622 GTPase IMAP family member 1-like K27758 GIMAP1_3_5; GTPase IMAP family member 1/3/5
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 126944417 dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 126963848 mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 126938978 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 126934789 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126943192 LOW QUALITY PROTEIN: heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126953203 heat shock 70 kDa protein 1B K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126953204 LOW QUALITY PROTEIN: heat shock 70 kDa protein 1A-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126953205 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126935390 AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein
D 126939722 aryl-hydrocarbon-interacting protein-like 1 isoform X1 K17767 AIP; AH receptor-interacting protein
D 126945427 fetal and adult testis-expressed transcript protein K28235 FATE1; fetal and adult testis-expressed transcript protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 126936379 mitochondrial import receptor subunit TOM40B isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 126956696 LOW QUALITY PROTEIN: mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 126949297 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 126946136 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 126962825 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 126962960 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 126963772 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 126942590 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 126959924 TOMM20-like protein 1 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 126960108 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 126950036 mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 126929324 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 126938369 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 126943518 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 126947843 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 126953820 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 126954340 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 126957060 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 126935285 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
D 126935722 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
D 126938106 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
D 126952548 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 126963628 sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 126956005 voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 126962446 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 126960768 voltage-dependent anion-selective channel protein 3 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 126932700 metaxin-2 isoform X1 K17776 MTX; metaxin
D 126934083 LOW QUALITY PROTEIN: metaxin-1 K17776 MTX; metaxin
D 126957606 metaxin-3 isoform X1 K17776 MTX; metaxin
D 126939327 LOW QUALITY PROTEIN: unconventional myosin-XIX K25838 MYO19; myosin XIX
D 126946003 armadillo repeat-containing X-linked protein 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1
D 126945990 armadillo repeat-containing X-linked protein 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2
D 126946012 armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3
D 126946019 protein ARMCX6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6
D 126937657 mitochondrial amidoxime-reducing component 1 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 126937671 mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 126940823 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 126959925 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 126936190 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 126935234 mitochondrial import inner membrane translocase subunit Tim10 B isoform X1 K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 126935814 mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 126937462 mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 126942876 mitochondrial import inner membrane translocase subunit Tim8 B-like K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 126946064 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 126953448 mitochondrial import inner membrane translocase subunit Tim8 A-like K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 126942868 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 126946353 mitochondrial intermembrane space import and assembly protein 40-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 126949177 mitochondrial intermembrane space import and assembly protein 40 isoform X1 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 126944747 FAD-linked sulfhydryl oxidase ALR isoform X1 K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 126938328 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 126956635 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 126933386 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 126942850 MICOS complex subunit MIC13 isoform X1 K24624 MICOS13; MICOS complex subunit MIC13
D 126938095 LOW QUALITY PROTEIN: MICOS complex subunit MIC19-like K17563 CHCHD3; MICOS complex subunit MIC19
D 126949711 MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 126952135 MICOS complex subunit MIC19-like K17563 CHCHD3; MICOS complex subunit MIC19
D 126952214 MICOS complex subunit MIC19-like K17563 CHCHD3; MICOS complex subunit MIC19
D 126949139 MICOS complex subunit MIC25 isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 126946727 MICOS complex subunit MIC26 isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 126946275 MICOS complex subunit MIC27-like K24626 APOOL; MICOS complex subunit MIC27
D 126946279 MICOS complex subunit MIC27 isoform X1 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 126938328 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 126956635 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 126933386 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 126938885 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 126963224 mitochondrial import inner membrane translocase subunit Tim23 isoform X1 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 126939368 mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 126945651 mitochondrial import inner membrane translocase subunit Tim17-B isoform X1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 126941535 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 126942035 LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
D 126944979 mitochondrial import inner membrane translocase subunit TIM50-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 126962518 calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial
D 126962146 LOW QUALITY PROTEIN: calcium uptake protein 1, mitochondrial-like K22827 MICU1; calcium uptake protein 1, mitochondrial
D 126962512 calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 126940527 calcium uptake protein 2, mitochondrial isoform X1 K22828 MICU2; calcium uptake protein 2, mitochondrial
D 126954938 calcium uniporter regulatory subunit MCUb, mitochondrial isoform X1 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 126963676 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 126953718 mitochondrial calcium uniporter regulator 1 isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 126955562 mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 126936357 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 126949828 mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 126934928 transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 126957993 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A
D 126946894 LOW QUALITY PROTEIN: mitochondrial pyruvate carrier 1-like protein K22138 MPC1; mitochondrial pyruvate carrier 1
D 126953778 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 126932543 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
D 126941736 mitochondrial pyruvate carrier 2 isoform X1 K22139 MPC2; mitochondrial pyruvate carrier 2
D 126958710 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
D 126929541 coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
D 126954570 OCIA domain-containing protein 1 isoform X1 K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 126942644 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 126957308 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 126950313 grpE protein homolog 1, mitochondrial-like K03687 GRPE; molecular chaperone GrpE
D 126953502 LOW QUALITY PROTEIN: grpE protein homolog 2, mitochondrial-like K03687 GRPE; molecular chaperone GrpE
D 126955518 grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 126956797 grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 126948394 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 126944779 mitochondrial import inner membrane translocase subunit TIM16 isoform X1 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 126936963 mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 126949870 mitochondrial-processing peptidase subunit beta isoform X1 K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 126940868 mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 126932138 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 126955185 60 kDa heat shock protein, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 126930963 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 126931750 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 126931780 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 126932153 10 kDa heat shock protein, mitochondrial isoform X1 K04078 groES; chaperonin GroES
D 126933466 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 126939473 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 126941266 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 126946804 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 126963361 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 126944651 dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 126949062 phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 126937098 DNL-type zinc finger protein isoform X1 K17808 ZIM17; mitochondrial protein import protein ZIM17
D 126942982 persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 126938731 polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
#
AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 126933094 cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 126948272 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 126956510 ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 126931105 transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1
D 126945250 transcription factor YY2 K09201 YY; transcription factor YY
D 126958435 transcriptional repressor protein YY1 K09201 YY; transcription factor YY
D 126931736 GA-binding protein subunit beta-2 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 126958701 GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 126962161 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 126949761 nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 126932076 nuclear factor erythroid 2-related factor 2 isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 126929773 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 126934831 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 126943908 metallothionein-1E K14739 MT1_2; metallothionein 1/2
D 126943913 metallothionein-1X K14739 MT1_2; metallothionein 1/2
D 126943914 metallothionein-2-like K14739 MT1_2; metallothionein 1/2
D 126943915 metallothionein-1F K14739 MT1_2; metallothionein 1/2
D 126943916 metallothionein-2-like K14739 MT1_2; metallothionein 1/2
D 126943917 metallothionein-1F-like K14739 MT1_2; metallothionein 1/2
D 126943918 metallothionein-1A-like K14739 MT1_2; metallothionein 1/2
D 126943920 metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 126943921 metallothionein-2-like K14739 MT1_2; metallothionein 1/2
D 126943922 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 126943923 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 126943924 metallothionein-1L K14739 MT1_2; metallothionein 1/2
D 126943925 metallothionein-1B-like K14739 MT1_2; metallothionein 1/2
D 126943927 metallothionein-1A-like K14739 MT1_2; metallothionein 1/2
D 126943928 metallothionein-1G-like isoform X1 K14739 MT1_2; metallothionein 1/2
D 126943930 metallothionein-1-like K14739 MT1_2; metallothionein 1/2
D 126943910 metallothionein-3 K14740 MT3; metallothionein 3
D 126943912 metallothionein-4 K14741 MT4; metallothionein 4
C Coactivators
D 126954797 peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 126956583 peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 126962739 peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 126942212 CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 126944569 CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 126963565 histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 126964229 cysteine desulfurase, mitochondrial isoform X1 K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 126931508 iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 126930713 LYR motif-containing protein 4-like K22069 LYRM4; LYR motif-containing protein 4
D 126953921 LYR motif-containing protein 4 isoform X1 K22069 LYRM4; LYR motif-containing protein 4
D 126937649 frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1]
D 126935803 adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 126942819 ferredoxin-2, mitochondrial isoform X1 K22071 FDX2; ferredoxin-2, mitochondrial
D 126939201 NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 126957308 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 126963982 iron-sulfur cluster co-chaperone protein HscB isoform X1 K04082 hscB; molecular chaperone HscB
D 126957317 nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 126959698 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 126937501 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 126959576 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 126936019 putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 126934064 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 126932585 bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 126934094 bolA-like protein 3 isoform X1 K22075 BOLA3; BolA-like protein 3
D 126956350 sideroflexin-1 isoform X1 K23500 SFXN1_3; sideroflexin-1/3
D 126963080 sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 126962758 sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2
D 126962674 sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4
D 126934053 sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 126935951 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 126929429 carnitine O-palmitoyltransferase 1, muscle isoform isoform X1 K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 126943095 carnitine O-palmitoyltransferase 1, brain isoform isoform X1 K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
D 126962360 2-oxoadipate dehydrogenase complex component E1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 126952177 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 126945453 host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1
D 126930898 host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2
D 126955552 huntingtin isoform X1 K04533 HD; huntingtin
D 126935585 steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 126959536 steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 126948514 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 126949667 nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 126932625 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 126956450 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 126942484 lon protease homolog, mitochondrial isoform X1 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 126962950 NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 126952294 protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 126945624 protein UXT K26537 UXT; protein UXT
D 126951664 PGC-1 and ERR-induced regulator in muscle protein 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
D 126950645 glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial isoform X1 K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 126929680 transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2
D 126932144 C12H2orf69; mitochondrial protein C2orf69 homolog K28271
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 126959858 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 126956997 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 126948744 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 126952172 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 126958709 LOW QUALITY PROTEIN: NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 126961807 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 126929386 arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 126960829 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 126933553 protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 126939142 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 isoform X1 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 126934925 complex I assembly factor TMEM126B, mitochondrial isoform X1 K18165 TMEM126B; complex I assembly factor TMEM126B
D 126942654 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 126949118 complex I assembly factor ACAD9, mitochondrial isoform X1 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 126959382 iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 126934855 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 126952305 reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 126947749 complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 126942123 succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 126935529 succinate dehydrogenase assembly factor 2, mitochondrial isoform X1 K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 126933002 mitochondrial chaperone BCS1 isoform X1 K08900 BCS1; mitochondrial chaperone BCS1
D 126938807 tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 126956027 complex III assembly factor LYRM7 isoform X1 K18170 LYRM7; complex III assembly factor LYRM7
D 126964261 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 126935534 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 126944777 C20H16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 126947620 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 126930917 C11H12orf73; protein BRAWNIN K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 126932206 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1
D 126939823 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1
D 126949698 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 126934828 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 126948104 COX assembly mitochondrial protein homolog isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1
D 126943987 COX assembly mitochondrial protein 2 homolog isoform X1 K18172 CMC2; COX assembly mitochondrial protein 2
D 126950193 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 126929767 cytochrome c oxidase assembly factor 3 homolog, mitochondrial-like K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 126938609 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 126942183 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 126957537 cytochrome c oxidase assembly factor 3 homolog, mitochondrial-like K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 126935281 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 126934347 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 126942581 cytochrome c oxidase assembly factor 6 homolog isoform X1 K18179 COA6; cytochrome c oxidase assembly factor 6
D 126962460 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 126939902 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 126939410 cytochrome c oxidase assembly protein COX11, mitochondrial isoform X1 K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 126931026 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 126963392 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 126958789 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 126949250 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 126954637 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18
D 126950585 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 126932400 LOW QUALITY PROTEIN: cytochrome c oxidase assembly protein COX20, mitochondrial-like K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 126951220 cytochrome c oxidase assembly protein COX20, mitochondrial isoform X1 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 126962431 putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 126942879 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 126929204 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 126958278 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 126937047 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 126939739 protein SCO1 homolog, mitochondrial isoform X1 K07152 SCO1; protein SCO1
D 126947182 protein SCO1 homolog, mitochondrial-like K07152 SCO1; protein SCO1
D 126929439 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 126939554 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 126934136 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 126959427 cytochrome c oxidase assembly factor 8 isoform X1 K23506 APOPT1; apoptogenic protein 1
D 126932206 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1
D 126939823 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1
D 126949698 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 126947620 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 126935518 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
D 126931070 HIG1 domain family member 1C K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 126948544 HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 126956390 HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial
C Complex-V assembly factors
D 126961469 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 126938812 ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 126961697 transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 126931341 ATP synthase subunit ATP5MJ, mitochondrial-like K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 126936305 LOW QUALITY PROTEIN: ATP synthase subunit ATP5MJ, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 126959435 ATP synthase subunit ATP5MJ, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 126963052 ATP synthase membrane subunit K, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 126947558 mitofusin-1 isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 126953005 mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 126947951 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 126943506 optic atrophy 3 protein isoform X1 K23166 OPA3; optic atrophy 3 protein
D 126930716 TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 126948415 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 126952802 bcl-2 homologous antagonist/killer K14021 BAK; Bcl-2 homologous antagonist/killer
D 126943600 apoptosis regulator BAX isoform X1 K02159 BAX; apoptosis regulator BAX
D 126931686 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 126950424 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 126929852 small ubiquitin-related modifier 5 K12160 SUMO; small ubiquitin-related modifier
D 126931729 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier
D 126932188 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier
D 126932205 small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 126939283 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 126950661 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 126955629 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 126956124 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier
D 126956393 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 126957367 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier
D 126959013 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 126961052 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 126961325 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 126944457 endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1
D 126936389 mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier
D 126943904 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier
D 126952772 mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier
D 126932961 mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor
D 126961695 ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 126963836 ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 126938508 synaptic vesicle membrane protein VAT-1 homolog isoform X1 K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 126939078 mitochondrial dynamics protein MID49 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 126963726 mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 126938824 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 126936932 mitoguardin 2 K27289 MIGA; mitoguardin
D 126963297 mitoguardin 1 isoform X1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 126932601 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 126939111 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 126950494 actin, cytoplasmic 1 isoform X1 K05692 ACTB_G1; actin beta/gamma 1
D 126963560 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 126931433 N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 126935988 prohibitin 1-like K17080 PHB1; prohibitin 1
D 126939885 prohibitin 1 K17080 PHB1; prohibitin 1
D 126943981 prohibitin 1-like K17080 PHB1; prohibitin 1
D 126950057 prohibitin 1-like K17080 PHB1; prohibitin 1
D 126930471 prohibitin-2 K17081 PHB2; prohibitin 2
D 126959685 LOW QUALITY PROTEIN: prohibitin-2-like K17081 PHB2; prohibitin 2
D 126959328 kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 126931686 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 126941304 unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 126959030 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
D 126959031 unconventional myosin-Vc isoform X1 K10357 MYO5; myosin V
D 126946702 E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 126930665 diablo IAP-binding mitochondrial protein isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 126955716 sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 126938978 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 126933386 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 126963950 mitochondrial fission process protein 1 isoform X1 K17981 MTFP1; mitochondrial fission process protein 1
D 126934198 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29
D 126959964 E3 ubiquitin-protein ligase NEDD4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 126961648 oxidation resistance protein 1 isoform X1 K25437 OXR1; oxidation resistance protein 1
D 126933665 protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato
D 126956371 PRELI domain-containing protein 1, mitochondrial K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 126956798 PRELI domain-containing protein 2 K27965 PRELID2; PRELI domain-containing protein 2 mitochondrial
D 126929355 PRELI domain containing protein 3B K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
D 126941228 PRELI domain containing protein 3A K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 126935549 autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 126959628 autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 126947802 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 126932790 cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 126933917 cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 126942632 cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 126946616 cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 126952311 autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 126938472 beclin-1 isoform X1 K08334 BECN; beclin
D 126942963 beclin-2 K08334 BECN; beclin
D 126949053 ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 126930013 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 126934131 gamma-aminobutyric acid receptor-associated protein-like K08341 GABARAP; GABA(A) receptor-associated protein
D 126939812 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 126943775 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 126932984 autophagy-related protein 9A isoform X1 K17907 ATG9; autophagy-related protein 9
D 126951643 autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 126957617 ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 126956258 ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 126959336 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 126932569 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 126935045 protein Atg16l2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 126938352 WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 126950483 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 126953705 E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31]
D 126931218 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 126944595 protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 126955100 serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 126948415 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 126956915 sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1
D 126950048 tax1-binding protein 1 isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 126939871 calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 126935738 activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 126935748 autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 126930540 serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 126939023 serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 126961411 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 126952392 heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 126955457 LOW QUALITY PROTEIN: heat shock protein HSP 90-alpha-like K04079 HSP90A; molecular chaperone HtpG
D 126958418 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 126938337 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 126950454 E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 126961828 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 126945657 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
D 126956379 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 126932625 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 126956450 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 126938294 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 126942985 microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 126944350 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 126964325 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 126938421 next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 126950449 tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 126959500 zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 126938456 bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 126963704 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 126943628 C19H19orf12; protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN
D 126934165 FUN14 domain-containing protein 2-like K24308 FUNDC2; FUN14 domain-containing protein 2
D 126945493 FUN14 domain-containing protein 2 isoform X1 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: April 30, 2025