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Mitochondrial Biogenesis - Meriones unguiculatus (Mongolian gerbil)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 18129817 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 18129806 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 18129811 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 18129813 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 18129812 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 18129814 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 18129815 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 18129816 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 18129805 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 18129807 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 18129810 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 18129808 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 18129809 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 110551343 Polrmt; LOW QUALITY PROTEIN: DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 110540629 Tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 110541650 LOW QUALITY PROTEIN: transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 110555674 Tfb1m; dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 110539879 Tfb2m; dimethyladenosine transferase 2, mitochondrial isoform X1 K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 110557355 Mtif2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 110561239 Tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 110547938 Tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 110550016 Gfm2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 110562740 Gfm1; elongation factor G, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 110561961 Mterf2; LOW QUALITY PROTEIN: transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 110557234 Mterf1; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 110545734 Mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 110561771 Mterf3; transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 110543481 Guf1; translation factor GUF1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 110563426 Pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 110545713 Pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 110545571 Pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 110545287 Rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 110556780 Pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 110547134 Rpp25l; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 110558540 Rpp25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 110564301 Rpp38; ribonuclease P protein subunit p38 isoform X1 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 110557792 Rpp40; ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 110563325 Trmt10c; tRNA methyltransferase 10 homolog C isoform X1 K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 110540816 Hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 110559678 Prorp; mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 110551987 Mss51; putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 110545081 Tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 110552630 Ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 110564153 Ptcd3; small ribosomal subunit protein mS39 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 110565833 Dhx30; ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 110550542 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 110555703 Afg1l; AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 110561207 Atp23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 110565124 ATP-dependent RNA helicase SUPV3L1, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 110565721 Lactb2; endoribonuclease LACTB2 isoform X1 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 110556812 Slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 110566446 Slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 110566972 Slc25a31; ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 110552972 Slc25a28; mitoferrin-2 isoform X2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 110554940 Slc25a37; mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 110551299 Malsu1; mitochondrial assembly of ribosomal large subunit protein 1 isoform X1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 110544971 Eral1; GTPase Era, mitochondrial isoform X1 K03595 era; GTPase
D 110548612 Yars1; tyrosine--tRNA ligase, cytoplasmic isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 110562068 Yars2; tyrosine--tRNA ligase, mitochondrial isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 110556794 Lars1; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 110554138 Lars2; leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 110565002 Dars2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 110555087 Gars1; glycine--tRNA ligase isoform X1 K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 110551852 Rars2; probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 110545412 Rars1; arginine--tRNA ligase, cytoplasmic isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 110548284 Qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial isoform X2 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 110557868 Gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 110558398 Mtpap; poly(A) RNA polymerase, mitochondrial isoform X1 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 110560199 Pde12; 2',5'-phosphodiesterase 12 isoform X1 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 110563314 Mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 110560332 Noa1; nitric oxide-associated protein 1 isoform X1 K19832 NOA1; nitric oxide-associated protein 1
D 110541427 Nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 110563061 Nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 110548949 Rpusd3; mitochondrial mRNA pseudouridine synthase RPUSD3 isoform X1 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 110555277 Rpusd4; pseudouridylate synthase RPUSD4, mitochondrial K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 110554208 Rcc1l; RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 110553397 Ngrn; neugrin K23496 NGRN; neugrin
D 110552312 Trub2; pseudouridylate synthase TRUB2, mitochondrial isoform X1 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 110566904 Fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 110558048 Mtrfr; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 110552867 Rmnd1; required for meiotic nuclear division protein 1 homolog isoform X2 K23499 RMND1; required for meiotic nuclear division protein 1
D 110541832 Grsf1; G-rich sequence factor 1 isoform X1 K24984 GRSF1; G-rich sequence factor 1
D 110541087 Mettl15; 12S rRNA N4-methylcytidine (m4C) methyltransferase isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 110552336 Myg1; MYG1 exonuclease K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 110548286 Mtres1; mitochondrial transcription rescue factor 1 isoform X2 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 110554401 Polg; DNA polymerase subunit gamma-1 isoform X2 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 110547024 Polg2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 110556805 Primpol; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 110554893 Endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 110548487 Mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 110555056 Exog; nuclease EXOG, mitochondrial isoform X1 K15050 EXOG; nuclease EXOG, mitochondrial
D 110556111 Twnk; twinkle mtDNA helicase isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 110552697 Pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 110564073 Ssbp1; single-stranded DNA-binding protein, mitochondrial isoform X1 K03111 ssb; single-strand DNA-binding protein
D 110560050 ATPase family AAA domain-containing protein 3 isoform X1 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 110543758 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 110552991 Dnaja2; dnaJ homolog subfamily A member 2 isoform X1 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 110548226 Tomm34; mitochondrial import receptor subunit TOM34 isoform X2 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 110545096 Rhot1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 110560143 Hspa1l; heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110560130 heat shock 70 kDa protein 1A K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110552032 Hspa8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110554439 Hspa6; LOW QUALITY PROTEIN: heat shock 70 kDa protein 6 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110551233 Aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 110560347 Aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 110554449 Tomm40l; mitochondrial import receptor subunit TOM40B isoform X4 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 110551534 Tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 110565043 Tomm70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 110557811 Tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 110551823 Tomm20l; TOMM20-like protein 1 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 110554853 Tomm20; mitochondrial import receptor subunit TOM20 homolog isoform X2 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 132653050 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 110566804 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 110564142 Tomm7; mitochondrial import receptor subunit TOM7 homolog isoform X2 K17771 TOM7; mitochondrial import receptor subunit TOM7
D 110550231 Tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 110558833 Tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 110545028 Samm50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 110549632 Vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 110548867 Vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 110556618 Vdac3; voltage-dependent anion-selective channel protein 3 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 110556594 Mtx2; metaxin-2 isoform X1 K17776 MTX; metaxin
D 110558835 Mtx1; metaxin-1 K17776 MTX; metaxin
D 110561300 Mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 110555251 Myo19; unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX
D 110563881 Armcx1; armadillo repeat-containing X-linked protein 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1
D 110563886 Armcx2; armadillo repeat-containing X-linked protein 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2
D 110563887 Armcx3; armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3
D 110563885 Armcx6; protein ARMCX6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6
D 110547931 Mtarc2; mitochondrial amidoxime reducing component 2 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 110547929 Mtarc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 110551822 Timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 110551970 Timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 110559579 Timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 110541657 Timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 110562011 Timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 110555609 Timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 110541943 myelin transcription factor 1-like protein K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 110549247 Chchd4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 110553005 Gfer; FAD-linked sulfhydryl oxidase ALR isoform X1 K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 110544991 Micos10; MICOS complex subunit MIC10 isoform X2 K17784 MICOS10; MICOS complex subunit MIC10
D 110564152 Immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 110546271 Micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 110558128 Chchd3; MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 110554298 Chchd6; MICOS complex subunit MIC25 isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 110563656 MICOS complex subunit Mic26 K24625 APOO; MICOS complex subunit MIC26
D 110543212 Apoo; MICOS complex subunit MIC26 isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 110542802 Apool; MICOS complex subunit MIC27 isoform X2 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 110544991 Micos10; MICOS complex subunit MIC10 isoform X2 K17784 MICOS10; MICOS complex subunit MIC10
D 110564152 Immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 110548497 Timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 110551272 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 110548431 Timm17a; mitochondrial import inner membrane translocase subunit Tim17-A isoform X1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 110561988 Timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 110540861 Timm21; mitochondrial import inner membrane translocase subunit Tim21 isoform X1 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 110564732 Timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 110557989 Mcu; calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial
D 110557988 Micu1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 110549751 Micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 110553232 Mcub; calcium uniporter regulatory subunit MCUb, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 110554105 Smdt1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 110544342 Mcur1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 110557294 Letm1; mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 110540482 mitochondrial proton/calcium exchanger protein-like K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 110560797 Immp1l; mitochondrial inner membrane protease subunit 1 isoform X1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 110556904 Immp2l; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 110552601 Tmem126a; transmembrane protein 126A isoform X2 K18157 TMEM126A; transmembrane protein 126A
D 110544867 Mpc1l; mitochondrial pyruvate carrier 1-like protein K22138 MPC1; mitochondrial pyruvate carrier 1
D 110564991 Mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 110545171 Mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 110558685 Chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 110558461 Hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 110546701 Grpel2; grpE protein homolog 2, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE
D 110544365 Grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 110556576 Dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 110551670 mitochondrial import inner membrane translocase subunit TIM14-like K09539 DNAJC19; DnaJ homolog subfamily C member 19
C Other matrix factors
D 110550824 Pmpca; mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 110554809 Pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 110556381 Mipep; mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 110551641 Hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 110556053 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 110545976 Dnaja3; dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 110558515 Tamm41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 110550865 Dnlz; DNL-type zinc finger protein isoform X1 K17808 ZIM17; mitochondrial protein import protein ZIM17
D 110539763 Ethe1; persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 110550124 Poldip2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 110551437 Creb1; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 110550016 Gfm2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 110562740 Gfm1; elongation factor G, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 110552322 Sp1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1
D 110542533 Yy2; transcription factor YY2 isoform X1 K09201 YY; transcription factor YY
D 110551781 Yy1; transcriptional repressor protein YY1 K09201 YY; transcription factor YY
D 110551942 Gabpb1; GA-binding protein subunit beta-1 isoform X3 K09454 GABPB; GA-binding protein transcription factor, beta
D 110560793 Gabpb2; GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta
D 110540629 Tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 110541650 LOW QUALITY PROTEIN: transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 110550985 Nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 110562029 Nfe2l2; nuclear factor erythroid 2-related factor 2 isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 110561155 metallothionein-2-like K14739 MT1_2; metallothionein 1/2
D 110561159 metallothionein-2 isoform X1 K14739 MT1_2; metallothionein 1/2
D 110561160 metallothionein-1 K14739 MT1_2; metallothionein 1/2
D 110561161 metallothionein-2-like K14739 MT1_2; metallothionein 1/2
D 110546206 metallothionein-1-like K14739 MT1_2; metallothionein 1/2
D 132656833 metallothionein-1-like K14739 MT1_2; metallothionein 1/2
D 132656834 metallothionein-1 K14739 MT1_2; metallothionein 1/2
D 132656835 metallothionein-1-like K14739 MT1_2; metallothionein 1/2
D 110551617 metallothionein-1-like K14739 MT1_2; metallothionein 1/2
D 110564653 metallothionein-1-like K14739 MT1_2; metallothionein 1/2
D 110561158 metallothionein-4 K14741 MT4; metallothionein 4
C Coactivators
D 110548956 Ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 110546693 Ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 110556355 Pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 110549173 Crtc1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 110554089 Ep300; histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 110545943 Crebbp; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 110550565 Nfs1; cysteine desulfurase isoform X1 K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 110553853 Iscu; iron-sulfur cluster assembly enzyme ISCU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 110557794 Lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 110555635 Fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 110550931 Fdx1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 110555763 Fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 110547618 Fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 110558461 Hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 110553153 Hscb; iron-sulfur cluster co-chaperone protein HscB isoform X1 K04082 hscB; molecular chaperone HscB
D 110554087 Sil1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 110554373 Glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 110554889 Isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial isoform X1 K22063 ISCA1; iron-sulfur cluster assembly 1
D 110546951 Isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 110552191 Iba57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 110563679 Nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 110556674 Bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 110566858 Bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 110554069 Sfxn1; sideroflexin-1 isoform X3 K23500 SFXN1_3; sideroflexin-1/3
D 110556177 Sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 110556593 Sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2
D 110562374 Sfxn4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4
D 110547191 Sfxn5; sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 110546982 Cpt1a; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 110549670 Cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 110546839 Cpt1c; LOW QUALITY PROTEIN: carnitine O-palmitoyltransferase 1, brain isoform K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
D 110560545 Dhtkd1; 2-oxoadipate dehydrogenase complex component E1 isoform X2 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 110564260 Fbxl4; F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 110542609 host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1
D 132649838 host cell factor 1-like isoform X1 K14966 HCFC1; host cell factor 1
D 132650048 host cell factor 1-like isoform X1 K14966 HCFC1; host cell factor 1
D 132651444 host cell factor 1-like isoform X1 K14966 HCFC1; host cell factor 1
D 110550775 Hcfc2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2
D 110552401 Htt; huntingtin isoform X1 K04533 HD; huntingtin
D 110551586 Esrra; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 110558478 Esrrb; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 110559353 Esrrg; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 110556316 Nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 110556367 Prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 110563129 Prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 110546250 Lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 110554873 Sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 110547880 Serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 110553689 protein UXT K26537 UXT; protein UXT
D 110543350 Uxt; protein UXT isoform X1 K26537 UXT; protein UXT
D 110560362 Perm1; PGC-1 and ERR-induced regulator in muscle protein 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 110550580 Ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 110546134 Ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 isoform X3 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 110565359 Ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 110561199 Ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 110551771 Ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 110554800 Ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 110564191 Ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 110548852 Ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 110552590 Tmem126b; complex I assembly factor TMEM126B, mitochondrial K18165 TMEM126B; complex I assembly factor TMEM126B
D 110552482 Ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 110546353 Acad9; complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 110562434 Nubpl; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 110555284 Foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 110548285 Rtn4ip1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 110555389 Timmdc1; complex I assembly factor TIMMDC1, mitochondrial isoform X1 K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 110551681 Sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 110548097 Sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial isoform X1 K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 110566690 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 110549786 Ttc19; tetratricopeptide repeat protein 19, mitochondrial isoform X2 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 110547211 Lyrm7; complex III assembly factor LYRM7 isoform X2 K18170 LYRM7; complex III assembly factor LYRM7
D 110550542 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 110543758 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 110557447 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 110548707 ubiquinol-cytochrome-c reductase complex assembly factor 4 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 110547566 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 110563928 ubiquinol-cytochrome-c reductase complex assembly factor 6 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 110558574 Stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 110541350 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 110555508 Cmc1; COX assembly mitochondrial protein homolog isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1
D 110549597 Cmc2; COX assembly mitochondrial protein 2 homolog isoform X3 K18172 CMC2; COX assembly mitochondrial protein 2
D 110543487 COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 110550892 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 110542538 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 110545445 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 110555227 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 110563488 cytochrome c oxidase assembly factor 7 isoform X1 K18180 COA7; cytochrome c oxidase assembly factor 7
D 110556789 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 110559651 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 110549610 cytochrome c oxidase assembly protein COX14-like K18181 COX14; cytochrome c oxidase assembly factor 14
D 110547421 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 110561227 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 110552967 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 110542091 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 110555386 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 110541225 cytochrome c oxidase copper chaperone-like K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 110566849 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18
D 110550687 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 110552492 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 110551987 Mss51; putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 110542360 LOW QUALITY PROTEIN: protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 132650559 protein PET100 homolog, mitochondrial isoform X1 K18186 PET100; protein PET100, animal type
D 110548489 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 110550053 Oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 110557508 surfeit locus protein 1 isoform X1 K14998 SURF1; surfeit locus 1 family protein
D 110552778 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 110549664 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 110547023 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 110558053 Lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 110560175 cytochrome c oxidase assembly factor 8 isoform X4 K23506 APOPT1; apoptogenic protein 1
D 110558574 Stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 110547566 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 110557458 Tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 110562621 Atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 110550009 Atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 isoform X2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 110557612 Tmem70; transmembrane protein 70, mitochondrial isoform X1 K17966 TMEM70; transmembrane protein 70, mitochondrial
D 110560170 Atp5mj; ATP synthase subunit ATP5MJ, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 110555657 ATP synthase subunit ATP5MJ, mitochondrial-like K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 110556708 Atp5mk; ATP synthase membrane subunit K, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 110556261 Mfn1; mitofusin-1 isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 110555747 Mfn2; mitofusin-2 isoform X2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 110566493 Opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 110551484 optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 110551509 optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein
D 110549386 Parl; presenilin-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 110543676 Bak1; bcl-2 homologous antagonist/killer isoform X1 K14021 BAK; Bcl-2 homologous antagonist/killer
D 110560658 Bax; apoptosis regulator BAX isoform X1 K02159 BAX; apoptosis regulator BAX
D 110562067 Dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 110566261 Fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 110559101 Sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 110547753 Sumo2; small ubiquitin-related modifier 2 isoform X1 K12160 SUMO; small ubiquitin-related modifier
D 110545109 Sumo3; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 110557576 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier
D 110562973 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier
D 132652422 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 110561561 Sh3glb1; endophilin-B1 isoform X5 K11248 SH3GLB1; endophilin-B1
D 110546565 Mtch1; mitochondrial carrier homolog 1 isoform X2 K17885 MTCH; mitochondrial carrier
D 110550740 Mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 110547497 Mff; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor
D 110548238 Gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 110561509 Gdap1; ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 110550887 Vat1; synaptic vesicle membrane protein VAT-1 homolog isoform X1 K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 110549978 Mief2; mitochondrial dynamics protein MID49 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 110564635 Mief1; mitochondrial dynamics protein MIEF1 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 110550008 Pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 110556278 Miga2; mitoguardin 2 isoform X1 K27289 MIGA; mitoguardin
D 110556062 Miga1; mitoguardin 1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 110548804 Actg1; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 110558188 Actb; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 110564759 Naa20; N-alpha-acetyltransferase 20 isoform X1 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 110546378 Naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 110540742 prohibitin 1-like K17080 PHB1; prohibitin 1
D 110551208 Phb1; prohibitin 1 K17080 PHB1; prohibitin 1
D 110548606 Phb2; prohibitin-2 K17081 PHB2; prohibitin 2
D 110556876 Ktn1; kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 110562067 Dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 110545475 Myo5a; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
D 110545476 Myo5c; unconventional myosin-Vc isoform X1 K10357 MYO5; myosin V
D 110550726 Myo5b; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 110542115 Xiap; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 110545348 Diablo; diablo IAP-binding mitochondrial protein isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 110556803 Snx25; sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 110545096 Rhot1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 110564152 Immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 110557721 Mtfp1; mitochondrial fission process protein 1 isoform X1 K17981 MTFP1; mitochondrial fission process protein 1
D 110548962 Dap3; small ribosomal subunit protein mS29 K17408 DAP3; small subunit ribosomal protein S29
D 110549134 Nedd4; E3 ubiquitin-protein ligase NEDD4 isoform X4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 110541692 Oxr1; oxidation resistance protein 1 isoform X10 K25437 OXR1; oxidation resistance protein 1
D 110548979 Msto1; protein misato homolog 1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 110555930 Atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 110549310 Atg2a; autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 110539637 Atg3; ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 110545728 Atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 110555767 Atg4d; cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 110559906 Atg4c; cysteine protease ATG4C isoform X3 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 110564781 Atg4a; cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 110546899 Atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 110550890 Becn1; beclin-1 K08334 BECN; beclin
D 110564121 Becn2; beclin-2 K08334 BECN; beclin
D 110558517 Atg7; ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 110559712 Gabarapl1; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 110555154 Gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 110554748 Gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 110548318 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 110562553 Atg9b; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 110566892 Atg9a; autophagy-related protein 9A isoform X1 K17907 ATG9; autophagy-related protein 9
D 110540607 Atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 110563216 Atg12; ubiquitin-like protein ATG12 isoform X1 K08336 ATG12; ubiquitin-like protein ATG12
D 110556880 Atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 110552949 Atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 110550794 Atg16l2; protein Atg16l2 isoform X2 K20868 ATG16L2; autophagy-related protein 16-2
D 110540721 Wipi2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 110560038 Wipi1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 110554861 Prkn; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31]
D 110559397 Rnf41; E3 ubiquitin-protein ligase NRDP1 isoform X1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 110555265 Clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 110544995 Pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 110549386 Parl; presenilin-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 110557385 Sqstm1; sequestosome-1 K14381 SQSTM1; sequestosome 1
D 110546144 Tax1bp1; tax1-binding protein 1 isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 110553416 Calcoco2; calcium-binding and coiled-coil domain-containing protein 2 isoform X3 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 110549887 Ambra1; activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 110549872 Atg13; autophagy-related protein 13 isoform X7 K08331 ATG13; autophagy-related protein 13
D 110553155 Ulk1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 110549788 Ulk2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 110557748 Rb1cc1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 110555839 Hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 110553235 Hsp90aa1; heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 110555779 Cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 110547040 Smurf2; E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 110555644 Smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X3 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 110559325 Bnip3l; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 110540073 Fundc1; FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 110556367 Prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 110563129 Prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 110550561 Map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 110545211 Map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 110550918 Nbr1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 110539309 Tecpr1; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 110558642 Zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 110550914 Coasy; bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 110566433 Pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 110545711 C14H19orf12; protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN
D 110543781 Fundc2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
D 110552051 FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024