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  Mitochondrial Biogenesis - Myotis brandtii (Brandt's bat)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 20964692 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 20964693 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 20964699 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 20964701 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 20964700 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 20964702 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 20964703 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 20964704 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 20964694 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 20964695 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 20964698 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 20964696 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 20964697 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 102253884 POLRMT; RNA polymerase mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 102254389 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 102257017 TFB1M; transcription factor B1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 102239264 TFB2M; transcription factor B2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 102240612 MTIF2; mitochondrial translational initiation factor 2 K02519 infB; translation initiation factor IF-2 D 102258462 MTIF3; mitochondrial translational initiation factor 3 K02520 infC; translation initiation factor IF-3 D 102264073 TSFM; Ts translation elongation factor, mitochondrial K02357 tsf; elongation factor Ts D 102239400 TUFM; Tu translation elongation factor, mitochondrial K02358 tuf; elongation factor Tu D 102259642 GFM2; G elongation factor mitochondrial 2 K02355 fusA; elongation factor G D 102249908 GFM1; G elongation factor mitochondrial 1 K02355 fusA; elongation factor G D 102262113 MTERF1; mitochondrial transcription termination factor 1 K15031 MTERF; mitochondrial transcription termination factor family protein D 106723552 MTERF2; mitochondrial transcription termination factor 2 K15031 MTERF; mitochondrial transcription termination factor family protein D 102242690 MTERF4; mitochondrial transcription termination factor 4 K15031 MTERF; mitochondrial transcription termination factor family protein D 102252736 MTERF3; mitochondrial transcription termination factor 3 K15031 MTERF; mitochondrial transcription termination factor family protein D 102260232 GUF1; GUF1 homolog, GTPase K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 102252642 POP1; POP1 homolog, ribonuclease P/MRP subunit K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 102250285 POP4; POP4 homolog, ribonuclease P/MRP subunit K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 102252378 POP5; POP5 homolog, ribonuclease P/MRP subunit K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 102262415 RPP30; ribonuclease P/MRP subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 102242894 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 102258568 POP7; POP7 homolog, ribonuclease P/MRP subunit K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 102259088 RPP25; ribonuclease P/MRP subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 102256549 RPP25L; ribonuclease P/MRP subunit p25 like K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 102259156 RPP38; ribonuclease P/MRP subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 102250939 RPP40; ribonuclease P/MRP subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 102257770 TRMT10C; tRNA methyltransferase 10C, mitochondrial RNase P subunit K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 102241897 3-hydroxyacyl-CoA dehydrogenase type-2-like K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 102248031 KIAA0391 ortholog K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 102252470 MSS51; MSS51 mitochondrial translational activator K17656 MSS51; mitochondrial splicing suppressor protein 51 D 102255824 TEFM; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 102242474 PTCD1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 102251753 PTCD2; pentatricopeptide repeat domain 2 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 102243543 PTCD3; pentatricopeptide repeat domain 3 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 102239697 DHX30; DExH-box helicase 30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 102239259 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 102256070 LACE1; lactation elevated 1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 102240675 ATP23; ATP23 metallopeptidase and ATP synthase assembly factor homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 102242907 SUPV3L1; Suv3 like RNA helicase K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 102239197 LACTB2; lactamase beta 2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 102255058 SLC25A4; solute carrier family 25 member 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 102239133 SLC25A31; solute carrier family 25 member 31 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 102256951 SLC25A5; solute carrier family 25 member 5 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 102256266 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 102246203 ADP/ATP translocase 3-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 102251112 SLC25A37; solute carrier family 25 member 37 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 102261663 SLC25A28; solute carrier family 25 member 28 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 102257727 MALSU1; mitochondrial assembly of ribosomal large subunit 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 102239239 ERAL1; Era like 12S mitochondrial rRNA chaperone 1 K03595 era; GTPase D 102251301 GTPase Era, mitochondrial-like K03595 era; GTPase D 102240828 YARS2; tyrosyl-tRNA synthetase 2 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 102247490 YARS; tyrosyl-tRNA synthetase K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 102243263 LARS; leucyl-tRNA synthetase K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 102250091 LARS2; leucyl-tRNA synthetase 2, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 102239503 DARS2; aspartyl-tRNA synthetase 2, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 102257680 GARS; glycyl-tRNA synthetase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 102263222 RARS; arginyl-tRNA synthetase K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 102247984 RARS2; arginyl-tRNA synthetase 2, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 102259481 QRSL1; glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 102250441 GATB; glutamyl-tRNA amidotransferase subunit B K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 102248063 MTPAP; mitochondrial poly(A) polymerase K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 102241344 PDE12; phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 102259752 MTG1; mitochondrial ribosome associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 102241377 NOA1; nitric oxide associated 1 K19832 NOA1; nitric oxide-associated protein 1 D 102256853 NSUN3; NOP2/Sun RNA methyltransferase family member 3 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 102253681 NSUN4; NOP2/Sun RNA methyltransferase family member 4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 102239926 RPUSD3; RNA pseudouridylate synthase domain containing 3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 102252794 RPUSD4; RNA pseudouridylate synthase domain containing 4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 102256835 RCC1L; RCC1 like K23495 RCC1L; RCC1-like G exchanging factor-like protein D 102240673 NGRN; neugrin, neurite outgrowth associated K23496 NGRN; neugrin D 102243080 neugrin-like K23496 NGRN; neugrin D 102254545 TRUB2; TruB pseudouridine synthase family member 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 102249056 FASTKD2; FAST kinase domains 2 K18190 FASTKD2; FAST kinase domain-containing protein 2 D 102263842 chromosome unknown open reading frame, human C12orf65 K23498 COXPD7; peptide chain release factor D 102254087 RMND1; required for meiotic nuclear division 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 102243697 GRSF1; G-rich RNA sequence binding factor 1 K24984 GRSF1; G-rich sequence factor 1 D 102246560 METTL15; methyltransferase like 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 102257816 chromosome unknown open reading frame, human C12orf10 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 102257487 chromosome unknown open reading frame, human C6orf203 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 102246846 POLG; DNA polymerase gamma, catalytic subunit K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 102255340 POLG2; DNA polymerase gamma 2, accessory subunit K02333 POLG2; DNA polymerase gamma 2 D 102257591 PRIMPOL; primase and DNA directed polymerase K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 102261142 ENDOG; endonuclease G K01173 ENDOG; endonuclease G, mitochondrial D 102242505 MGME1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 102261043 EXOG; exo/endonuclease G K15050 EXOG; nuclease EXOG, mitochondrial D 102254481 TWNK; twinkle mtDNA helicase K17680 PEO1; twinkle protein [EC:5.6.2.3] D 102263269 PIF1; PIF1 5'-to-3' DNA helicase K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 102250720 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 102252510 SSBP1; single stranded DNA binding protein 1 K03111 ssb; single-strand DNA-binding protein D 102259418 ATPase family AAA domain-containing protein 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 102240975 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 102248789 DNAJA2; DnaJ heat shock protein family (Hsp40) member A2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 102249835 TOMM34; translocase of outer mitochondrial membrane 34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 102241689 RHOT1; ras homolog family member T1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 102238827 HSPA1A; heat shock protein family A (Hsp70) member 1A K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 102239444 HSPA1L; heat shock protein family A (Hsp70) member 1 like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 102256875 HSPA8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 102253077 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein D 106723812 AH receptor-interacting protein-like K17767 AIP; AH receptor-interacting protein D 102258478 AIPL1; aryl hydrocarbon receptor interacting protein like 1 K17767 AIP; AH receptor-interacting protein D 102252765 AH receptor-interacting protein-like K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 102246504 TOMM40L; translocase of outer mitochondrial membrane 40 like K11518 TOM40; mitochondrial import receptor subunit TOM40 D 102247210 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 102239472 TOMM40; translocase of outer mitochondrial membrane 40 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 102251671 TOMM70; translocase of outer mitochondrial membrane 70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 102255973 TOMM22; translocase of outer mitochondrial membrane 22 K17769 TOM22; mitochondrial import receptor subunit TOM22 D 102251846 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 102253304 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 102261141 TOMM20; translocase of outer mitochondrial membrane 20 K17770 TOM20; mitochondrial import receptor subunit TOM20 D 102245175 TOMM20L; translocase of outer mitochondrial membrane 20 like K17770 TOM20; mitochondrial import receptor subunit TOM20 D 102243076 TOMM7; translocase of outer mitochondrial membrane 7 K17771 TOM7; mitochondrial import receptor subunit TOM7 D 102239012 TOMM6; translocase of outer mitochondrial membrane 6 K17772 TOM6; mitochondrial import receptor subunit TOM6 D 102254378 TOMM5; translocase of outer mitochondrial membrane 5 K17773 TOM5; mitochondrial import receptor subunit TOM5 D 102257801 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 102245969 SAMM50; SAMM50 sorting and assembly machinery component K07277 SAM50; outer membrane protein insertion porin family C Porin D 102249622 VDAC1; voltage dependent anion channel 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 102245606 VDAC2; voltage dependent anion channel 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 102263138 VDAC3; voltage dependent anion channel 3 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 102254298 MTX1; metaxin 1 K17776 MTX; metaxin D 102243674 MTX2; metaxin 2 K17776 MTX; metaxin D 102249270 MTX3; metaxin 3 K17776 MTX; metaxin D 102249770 MYO19; myosin XIX K25838 MYO19; myosin XIX D 102246762 ARMCX1; armadillo repeat containing, X-linked 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1 D 102245027 ARMCX2; armadillo repeat containing, X-linked 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2 D 102246451 ARMCX3; armadillo repeat containing, X-linked 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3 D 102245721 ARMCX6; armadillo repeat containing, X-linked 6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6 D 102248583 MARC2; mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] D 102255137 MARC1; mitochondrial amidoxime reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 102244083 TIMM9; translocase of inner mitochondrial membrane 9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 106724673 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 102248926 TIMM10; translocase of inner mitochondrial membrane 10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 102247832 TIMM10B; translocase of inner mitochondrial membrane 10B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 102257846 TIMM8B; translocase of inner mitochondrial membrane 8 homolog B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 102261059 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 102246458 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 102254308 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 C Mitochondrial intermembrane space assembly (MIA) complex D 102246137 CHCHD4; coiled-coil-helix-coiled-coil-helix domain containing 4 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 102260593 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 102262999 GFER; growth factor, augmenter of liver regeneration K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 102245682 MINOS1; mitochondrial inner membrane organizing system 1 K17784 MICOS10; MICOS complex subunit MIC10 D 102244317 IMMT; inner membrane mitochondrial protein K17785 IMMT; MICOS complex subunit MIC60 D 102246932 chromosome unknown open reading frame, human C19orf70 K24624 MICOS13; MICOS complex subunit MIC13 D 102254718 CHCHD3; coiled-coil-helix-coiled-coil-helix domain containing 3 K17563 CHCHD3; MICOS complex subunit MIC19 D 102249925 CHCHD6; coiled-coil-helix-coiled-coil-helix domain containing 6 K17564 CHCHD6; MICOS complex subunit MIC25 D 102259175 APOO; apolipoprotein O K24625 APOO; MICOS complex subunit MIC26 D 102247245 APOOL; apolipoprotein O like K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 102245682 MINOS1; mitochondrial inner membrane organizing system 1 K17784 MICOS10; MICOS complex subunit MIC10 D 102244317 IMMT; inner membrane mitochondrial protein K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 102262123 TIMM22; translocase of inner mitochondrial membrane 22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 102253561 TIMM23; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 102245911 TIMM17A; translocase of inner mitochondrial membrane 17 homolog A (yeast) K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 102262425 TIMM17B; translocase of inner mitochondrial membrane 17 homolog B (yeast) K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 102249666 mitochondrial import inner membrane translocase subunit Tim17-B-like K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 102244308 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 102240902 TIMM21; translocase of inner mitochondrial membrane 21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 102243184 TIMM50; translocase of inner mitochondrial membrane 50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 102238865 MCU; mitochondrial calcium uniporter K20858 MCU; calcium uniporter protein, mitochondrial D 102257186 MICU1; mitochondrial calcium uptake 1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 102262441 MICU2; mitochondrial calcium uptake 2 K22828 MICU2; calcium uptake protein 2, mitochondrial D 102239521 MCUB; mitochondrial calcium uniporter dominant negative beta subunit K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 102258578 SMDT1; single-pass membrane protein with aspartate rich tail 1 K22830 SMDT1; essential MCU regulator, mitochondrial D 102243684 MCUR1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 102241844 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 102241874 IMMP1L; inner mitochondrial membrane peptidase subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 102257835 IMMP2L; inner mitochondrial membrane peptidase subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 102250423 TMEM126A; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 102262335 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 102258633 mitochondrial pyruvate carrier 1-like K22138 MPC1; mitochondrial pyruvate carrier 1 D 102238702 MPC1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 102257469 MPC2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 102243091 CHCHD10; coiled-coil-helix-coiled-coil-helix domain containing 10 K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 102248837 TIMM44; translocase of inner mitochondrial membrane 44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 102259869 HSPA9; heat shock protein family A (Hsp70) member 9 K04043 dnaK; molecular chaperone DnaK D 102258706 GRPEL1; GrpE like 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 102252410 GRPEL2; GrpE like 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 102240374 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 102248480 DNAJC19; DnaJ heat shock protein family (Hsp40) member C19 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 102255198 PAM16; presequence translocase associated motor 16 homolog K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 D 102259736 mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 102257476 PMPCA; peptidase, mitochondrial processing alpha subunit K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 102252866 PMPCB; peptidase, mitochondrial processing beta subunit K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 102251949 MIPEP; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 102253603 HSPD1; heat shock protein family D (Hsp60) member 1 K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 102255440 60 kDa heat shock protein, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 102255701 TAMM41; TAM41 mitochondrial translocator assembly and maintenance homolog K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 102256755 DNLZ; DNL-type zinc finger K17808 ZIM17; mitochondrial protein import protein ZIM17 D 102243740 ETHE1; ETHE1, persulfide dioxygenase K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 102252522 POLDIP2; DNA polymerase delta interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 102246867 CREB1; cAMP responsive element binding protein 1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 102259642 GFM2; G elongation factor mitochondrial 2 K02355 fusA; elongation factor G D 102249908 GFM1; G elongation factor mitochondrial 1 K02355 fusA; elongation factor G D 102256096 SP1; Sp1 transcription factor K04684 SP1; transcription factor Sp1 D 102253101 YY2; YY2 transcription factor K09201 YY; transcription factor YY D 102250968 YY1; YY1 transcription factor K09201 YY; transcription factor YY D 102258774 GABPB2; GA binding protein transcription factor beta subunit 2 K09454 GABPB; GA-binding protein transcription factor, beta D 102257687 GABPB1; GA binding protein transcription factor beta subunit 1 K09454 GABPB; GA-binding protein transcription factor, beta D 102254389 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 102250936 NRF1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1 D 102244372 NFE2L2; nuclear factor, erythroid 2 like 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 102261648 metallothionein-2A K14739 MT1_2; metallothionein 1/2 D 102245932 metallothionein-2B-like K14739 MT1_2; metallothionein 1/2 D 102251925 metallothionein-2-like K14739 MT1_2; metallothionein 1/2 D 102250329 metallothionein-1E K14739 MT1_2; metallothionein 1/2 D 102262771 MT4; metallothionein 4 K14741 MT4; metallothionein 4 C Coactivators D 102250163 PPARGC1A; PPARG coactivator 1 alpha K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 102240543 PPARGC1B; PPARG coactivator 1 beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 102243681 PPRC1; peroxisome proliferator-activated receptor gamma, coactivator-related 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 102250141 CRTC1; CREB regulated transcription coactivator 1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 102249541 CREBBP; CREB binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 102260716 EP300; E1A binding protein p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 102262132 NFS1; NFS1, cysteine desulfurase K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 102241966 ISCU; iron-sulfur cluster assembly enzyme K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 102251420 LYRM4; LYR motif containing 4 K22069 LYRM4; LYR motif-containing protein 4 D 102242757 FXN; frataxin K19054 FXN; frataxin [EC:1.16.3.1] D 102248506 FDX1; ferredoxin 1 K22070 FDX1; ferredoxin-1, mitochondrial D 102242614 FDX1L; ferredoxin 1 like K22071 FDX2; ferredoxin-2, mitochondrial D 102263706 FDXR; ferredoxin reductase K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 102259869 HSPA9; heat shock protein family A (Hsp70) member 9 K04043 dnaK; molecular chaperone DnaK D 102251228 HSCB; HscB mitochondrial iron-sulfur cluster cochaperone K04082 hscB; molecular chaperone HscB D 102261850 SIL1; SIL1 nucleotide exchange factor K14001 SIL1; nucleotide exchange factor SIL1 D 102258429 ISCA1; iron-sulfur cluster assembly 1 K22063 ISCA1; iron-sulfur cluster assembly 1 D 102251290 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 102251584 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 102244955 IBA57; IBA57 homolog, iron-sulfur cluster assembly K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 102255995 NFU1; NFU1 iron-sulfur cluster scaffold K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 102246953 BOLA1; bolA family member 1 K22066 BOLA1; BolA-like protein 1 D 102256597 BOLA3; bolA family member 3 K22075 BOLA3; BolA-like protein 3 D 102249181 SFXN1; sideroflexin 1 K23500 SFXN1_3; sideroflexin-1/3 D 102257839 sideroflexin-3-like K23500 SFXN1_3; sideroflexin-1/3 D 102258759 SFXN3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 102260944 SFXN2; sideroflexin 2 K23501 SFXN2; sideroflexin-2 D 102246895 SFXN4; sideroflexin 4 K23502 SFXN4; sideroflexin-4 D 102241549 SFXN5; sideroflexin 5 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 102261269 CPT1A; carnitine palmitoyltransferase 1A K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 102252400 CPT1B; carnitine palmitoyltransferase 1B K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21] D 102242927 CPT1C; carnitine palmitoyltransferase 1C K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21] D 102255818 DHTKD1; dehydrogenase E1 and transketolase domain containing 1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 102240939 FBXL4; F-box and leucine rich repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 102258702 HCFC1; host cell factor C1 K14966 HCFC1; host cell factor 1 D 102252557 HCFC2; host cell factor C2 K27390 HCFC2; host cell factor 2 D 102250928 HTT; huntingtin K04533 HD; huntingtin D 102240102 ESRRA; estrogen related receptor alpha K08552 NR3B1; estrogen-related receptor alpha D 102258175 ESRRB; estrogen related receptor beta K08553 NR3B2; estrogen-related receptor beta D 102253341 ESRRG; estrogen related receptor gamma K08554 NR3B3; estrogen-related receptor gamma D 102257068 NRIP1; nuclear receptor interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 102241697 PRKAA2; protein kinase AMP-activated catalytic subunit alpha 2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 102248668 PRKAA1; protein kinase AMP-activated catalytic subunit alpha 1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 102247241 LONP1; lon peptidase 1, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 102240165 SIRT1; sirtuin 1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 102260524 SERAC1; serine active site containing 1 K23504 SERAC1; protein SERAC1 D 102240241 UXT; ubiquitously expressed prefoldin like chaperone K26537 UXT; protein UXT D 102261793 PERM1; PPARGC1 and ESRR induced regulator, muscle 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 102261537 NDUFAF1; NADH:ubiquinone oxidoreductase complex assembly factor 1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 102252631 NDUFAF2; NADH:ubiquinone oxidoreductase complex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 102241739 NDUFAF3; NADH:ubiquinone oxidoreductase complex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 102242367 NDUFAF4; NADH:ubiquinone oxidoreductase complex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 102261542 NDUFAF5; NADH:ubiquinone oxidoreductase complex assembly factor 5 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 102250587 NDUFAF6; NADH:ubiquinone oxidoreductase complex assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 102250820 NDUFAF7; NADH:ubiquinone oxidoreductase complex assembly factor 7 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 102251021 TMEM126B; transmembrane protein 126B K18165 TMEM126B; complex I assembly factor TMEM126B D 102238837 ECSIT; ECSIT signalling integrator K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 102245314 ACAD9; acyl-CoA dehydrogenase family member 9 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 102251570 NUBPL; nucleotide binding protein like K03593 mrp; ATP-binding protein involved in chromosome partitioning D 102252026 FOXRED1; FAD dependent oxidoreductase domain containing 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 102258891 RTN4IP1; reticulon 4 interacting protein 1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 102244850 TIMMDC1; translocase of inner mitochondrial membrane domain containing 1 K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 102260419 SDHAF2; succinate dehydrogenase complex assembly factor 2 K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 102254268 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 102248942 TTC19; tetratricopeptide repeat domain 19 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 102264119 LYRM7; LYR motif containing 7 K18170 LYRM7; complex III assembly factor LYRM7 D 102239259 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 102240975 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 102254036 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 102253189 chromosome unknown open reading frame, human C16orf91 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 102248703 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 106725931 chromosome unknown open reading frame, human C12orf73 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 102245279 uncharacterized protein C7orf73-like K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 102244765 CMC1; C-X9-C motif containing 1 K18171 CMC1; COX assembly mitochondrial protein 1 D 102240300 CMC2; C-X9-C motif containing 2 K18172 CMC2; COX assembly mitochondrial protein 2 D 102263861 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1 D 102259145 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 102246748 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 102258501 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 102247667 SELRC1; cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 102261324 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 102248842 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 102256430 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14 D 102263800 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 102243001 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 102247674 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 102239568 mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18 D 102246284 cytochrome c oxidase protein 20 homolog K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 102252470 MSS51; MSS51 mitochondrial translational activator K17656 MSS51; mitochondrial splicing suppressor protein 51 D 102254868 PET100; PET100 homolog K18186 PET100; protein PET100, animal type D 102240505 OXA1L; OXA1L, mitochondrial inner membrane protein K03217 yidC; YidC/Oxa1 family membrane protein insertase D 102241246 SURF1; surfeit 1 K14998 SURF1; surfeit locus 1 family protein D 102248571 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 102254190 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 102245867 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 102256776 LRPPRC; leucine rich pentatricopeptide repeat containing K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 102252816 APOPT1; apoptogenic 1, mitochondrial K23506 APOPT1; apoptogenic protein 1 D 102245279 uncharacterized protein C7orf73-like K27319 STMP1; short transmembrane mitochondrial protein 1 D 102248703 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 C Complex-V assembly factors D 102260176 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 102238682 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 102255587 TMEM70; transmembrane protein 70 K17966 TMEM70; transmembrane protein 70, mitochondrial D 102250381 transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 102241387 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid D 102247969 chromosome unknown open reading frame, human C14orf2 K18193 MP68; 6.8 kDa mitochondrial proteolipid D 102257243 USMG5; up-regulated during skeletal muscle growth 5 homolog (mouse) K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 102264006 MFN1; mitofusin 1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 102246147 MFN2; mitofusin 2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 102258927 OPA1; OPA1, mitochondrial dynamin like GTPase K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 102246614 OPA3; OPA3, outer mitochondrial membrane lipid metabolism regulator K23166 OPA3; optic atrophy 3 protein D 102253668 TRIAP1; TP53 regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 102246769 PARL; presenilin associated rhomboid like K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 102240268 BAK1; BCL2 antagonist/killer 1 K14021 BAK; Bcl-2 homologous antagonist/killer D 106723573 BAX; BCL2 associated X, apoptosis regulator K02159 BAX; apoptosis regulator BAX D 102240524 DNM1L; dynamin 1 like K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 102239873 FIS1; fission, mitochondrial 1 K17969 FIS1; mitochondrial fission 1 protein D 102249840 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 102253849 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 102244024 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 102245400 SUMO2; small ubiquitin-like modifier 2 K12160 SUMO; small ubiquitin-related modifier D 102248434 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 102252734 SUMO3; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 102261545 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 102251166 SUMO1; small ubiquitin-like modifier 1 K12160 SUMO; small ubiquitin-related modifier D 102252038 small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 102238601 uncharacterized LOC102238601 K12160 SUMO; small ubiquitin-related modifier D 102257225 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 102250917 SH3GLB1; SH3 domain containing GRB2 like endophilin B1 K11248 SH3GLB1; endophilin-B1 D 102263531 MTCH1; mitochondrial carrier 1 K17885 MTCH; mitochondrial carrier D 102239095 MTCH2; mitochondrial carrier 2 K17885 MTCH; mitochondrial carrier D 102249705 MFF; mitochondrial fission factor K22076 MFF; mitochondrial fission factor D 102241557 GDAP1L1; ganglioside induced differentiation associated protein 1 like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 102246122 GDAP1; ganglioside induced differentiation associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 102252712 VAT1; vesicle amine transport 1 K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 102239100 MIEF1; mitochondrial elongation factor 1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 102239708 MIEF2; mitochondrial elongation factor 2 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 102255306 MIGA1; mitoguardin 1 K27289 MIGA; mitoguardin D 102244581 MIGA2; mitoguardin 2 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 102263592 ACTG1; actin gamma 1 K05692 ACTB_G1; actin beta/gamma 1 D 102251030 actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 102256245 ACTB; actin beta K05692 ACTB_G1; actin beta/gamma 1 D 102261767 NAA20; N(alpha)-acetyltransferase 20, NatB catalytic subunit K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 102253319 NAA25; N(alpha)-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 102254784 PHB; prohibitin K17080 PHB1; prohibitin 1 D 102256518 PHB2; prohibitin 2 K17081 PHB2; prohibitin 2 D 102242327 KTN1; kinectin 1 K17975 KTN1; kinectin C Retention of mitochondria D 102240524 DNM1L; dynamin 1 like K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 102254879 MYO5B; myosin VB K10357 MYO5; myosin V D 102242127 MYO5A; myosin VA K10357 MYO5; myosin V D 102242423 MYO5C; myosin VC K10357 MYO5; myosin V D 102246972 XIAP; X-linked inhibitor of apoptosis K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 102257435 DIABLO; diablo IAP-binding mitochondrial protein K10522 DIABLO; diablo C Morphogenesis factors D 102251993 SNX25; sorting nexin 25 K17887 SNX25; sorting nexin-25 D 102241689 RHOT1; ras homolog family member T1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 102244317 IMMT; inner membrane mitochondrial protein K17785 IMMT; MICOS complex subunit MIC60 D 102260918 MTFP1; mitochondrial fission process 1 K17981 MTFP1; mitochondrial fission process protein 1 D 102256093 DAP3; death associated protein 3 K17408 DAP3; small subunit ribosomal protein S29 D 102259863 NEDD4; neural precursor cell expressed, developmentally down-regulated 4, E3 ubiquitin protein ligase K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 102251579 OXR1; oxidation resistance 1 K25437 OXR1; oxidation resistance protein 1 D 102257199 MSTO1; misato 1, mitochondrial distribution and morphology regulator K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 102243916 ATG2A; autophagy related 2A K17906 ATG2; autophagy-related protein 2 D 102249037 ATG2B; autophagy related 2B K17906 ATG2; autophagy-related protein 2 D 102254797 ATG3; autophagy related 3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 102257295 ATG4A; autophagy related 4A cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 102251065 ATG4C; autophagy related 4C cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 102261824 ATG4B; autophagy related 4B cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 102254452 ATG4D; autophagy related 4D cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 102259790 ATG5; autophagy related 5 K08339 ATG5; autophagy-related protein 5 D 102256414 BECN1; beclin 1 K08334 BECN; beclin D 102244808 beclin-2 K08334 BECN; beclin D 102253655 beclin-2-like K08334 BECN; beclin D 102256212 ATG7; autophagy related 7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 102262056 GABARAPL1; GABA type A receptor associated protein like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 102259347 GABARAP; GABA type A receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 102255361 GABARAPL2; GABA type A receptor associated protein like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 102258966 ATG9B; autophagy related 9B K17907 ATG9; autophagy-related protein 9 D 102259677 ATG9A; autophagy related 9A K17907 ATG9; autophagy-related protein 9 D 102254728 ATG10; autophagy related 10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 102240569 ATG12; autophagy related 12 K08336 ATG12; ubiquitin-like protein ATG12 D 102249790 ATG14; autophagy related 14 K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 102240090 ATG16L1; autophagy related 16 like 1 K17890 ATG16L1; autophagy-related protein 16-1 D 102247547 ATG16L2; autophagy related 16 like 2 K20868 ATG16L2; autophagy-related protein 16-2 D 102255438 WIPI2; WD repeat domain, phosphoinositide interacting 2 K17908 WIPI1_2; autophagy-related protein 18 D 102260137 WIPI1; WD repeat domain, phosphoinositide interacting 1 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 102255484 PARK2; parkin RBR E3 ubiquitin protein ligase K04556 PARK2; parkin [EC:2.3.2.31] D 102262114 RNF41; ring finger protein 41 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 102240844 CLEC16A; C-type lectin domain family 16 member A K19513 CLEC16A; protein CLEC16A D 102242404 PINK1; PTEN induced putative kinase 1 K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 102246769 PARL; presenilin associated rhomboid like K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 102258898 SQSTM1; sequestosome 1 K14381 SQSTM1; sequestosome 1 D 102241825 TAX1BP1; Tax1 binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1 D 102249732 CALCOCO2; calcium binding and coiled-coil domain 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 102248838 AMBRA1; autophagy and beclin 1 regulator 1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 102250643 ATG13; autophagy related 13 K08331 ATG13; autophagy-related protein 13 D 102240341 ULK1; unc-51 like autophagy activating kinase 1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 102260328 ULK2; unc-51 like autophagy activating kinase 2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 102257294 RB1CC1; RB1 inducible coiled-coil 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 102263971 HSP90AA1; heat shock protein 90 alpha family class A member 1 K04079 HSP90A; molecular chaperone HtpG D 102261247 HSP90AB1; heat shock protein 90 alpha family class B member 1 K04079 HSP90A; molecular chaperone HtpG D 102246274 CDC37; cell division cycle 37 K09554 CDC37; cell division cycle protein 37 D 102262993 SMURF1; SMAD specific E3 ubiquitin protein ligase 1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 102256642 SMURF2; SMAD specific E3 ubiquitin protein ligase 2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 102241134 BNIP3L; BCL2 interacting protein 3 like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 102264042 FUNDC1; FUN14 domain containing 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 102241697 PRKAA2; protein kinase AMP-activated catalytic subunit alpha 2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 102248668 PRKAA1; protein kinase AMP-activated catalytic subunit alpha 1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 102242319 MAP1LC3A; microtubule associated protein 1 light chain 3 alpha K10435 MAP1LC; microtubule-associated protein 1 light chain D 102247349 microtubule-associated proteins 1A/1B light chain 3B-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 102250858 NBR1; NBR1, autophagy cargo receptor K17987 NBR1; next to BRCA1 gene 1 protein D 102255133 TECPR1; tectonin beta-propeller repeat containing 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 102249921 ZFYVE1; zinc finger FYVE-type containing 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 102261991 COASY; Coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 102258983 PLA2G6; phospholipase A2 group VI K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 102244432 protein C19orf12 homolog K23168 MPAN; protein MPAN D 102243469 protein C19orf12 homolog K23168 MPAN; protein MPAN D 102254988 protein C19orf12 homolog K23168 MPAN; protein MPAN D 102255595 protein C19orf12 homolog K23168 MPAN; protein MPAN D 102256684 FUNDC2; FUN14 domain containing 2 K24308 FUNDC2; FUN14 domain-containing protein 2 D 102254802 FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024