+D #

  Mitochondrial Biogenesis - Maylandia zebra (zebra mbuna)

% ! AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 26037634 APK84_gp13; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 26037637 APK84_gp12; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 26037646 APK84_gp06; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 26037625 APK84_gp04; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 26037647 APK84_gp05; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 26037650 APK84_gp03; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 26037626 APK84_gp02; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 26037651 APK84_gp01; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 26037642 APK84_gp11; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 26037644 APK84_gp10; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 26037622 APK84_gp07; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 26037645 APK84_gp09; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 26037621 APK84_gp08; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 101481838 polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 101484483 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 101487512 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 101477317 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 101473025 mtif2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2 D 101466886 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3 D 101481611 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 101487069 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 101484645 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 101481737 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 101467557 transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 101474947 transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 101487631 mterf1; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 101466224 mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 101481499 transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 101467024 guf1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 101473147 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 101486265 pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 101473550 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 101470266 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 101486199 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 112432574 ribonuclease P protein subunit p20-like K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 101479391 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 101467860 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 101470544 ribonuclease P protein subunit p25-like K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 112435077 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 101467203 ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 106674462 ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 101481437 rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 101479672 trmt10c; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 101486814 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 101483589 kiaa0391; mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 101480763 putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 101480077 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 101485408 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 101465823 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 101469825 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 101486156 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 101482281 dhx30; putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 101471699 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 101482778 afg1l; AFG1-like ATPase isoform X3 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 101485853 AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 101483685 atp23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 101465023 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 101483051 lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 101464643 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 106676295 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 101482797 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 101478476 mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 101473886 mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 101487766 slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 101480829 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 101473548 eral1; GTPase Era, mitochondrial isoform X1 K03595 era; GTPase D 101468331 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 101470094 yars; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 101487309 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 101478855 lars; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 101482570 LOW QUALITY PROTEIN: aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 112436477 aspartate--tRNA ligase, mitochondrial-like K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 101472906 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 101473206 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 101472042 rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 101485191 rars; arginine--tRNA ligase, cytoplasmic isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 101479385 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 101486870 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 101484106 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial isoform X1 K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 101483945 mtpap; poly(A) RNA polymerase, mitochondrial isoform X1 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 101465253 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 112433379 LOW QUALITY PROTEIN: 2',5'-phosphodiesterase 12-like K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 101483691 mtg1; mitochondrial ribosome-associated GTPase 1 isoform X1 K19828 MTG1; mitochondrial GTPase 1 D 101473103 noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 101475305 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 101472316 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 101484748 mitochondrial RNA pseudouridine synthase rpusd4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 101483473 rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 101485641 ngrn; neugrin K23496 NGRN; neugrin D 101485993 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 101482037 fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 101483154 lg12h12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial isoform X1 K23498 COXPD7; peptide chain release factor D 101469779 rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 101486519 grsf1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1 D 101485863 mettl15; probable methyltransferase-like protein 15 isoform X2 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 101481242 lg5h12orf10; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 101478881 lg19h6orf203; uncharacterized protein C6orf203 homolog isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 101487408 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 101470248 polg2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 D 101482310 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 101465942 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 101464723 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 101483101 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3] D 101472623 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 112432313 ATP-dependent DNA helicase PIF1-like isoform X1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 112432424 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 112432426 ATP-dependent DNA helicase PIF1-like isoform X1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 112430723 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 112432709 ATP-dependent DNA helicase PIF1-like isoform X1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 112434772 ATP-dependent DNA helicase PIF1-like isoform X1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 112434360 uncharacterized protein LOC112434360 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 112436586 uncharacterized protein LOC112436586 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 112436009 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 112433706 uncharacterized protein LOC112433706 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 101481042 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 101467751 atad3a; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 101478664 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 101481877 dnaja2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 101465466 dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 101484221 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 101484650 mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 101469002 mitochondrial Rho GTPase 1-A isoform X3 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 101464789 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 101484458 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 101486419 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 101481563 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 101480703 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 101472616 uncharacterized protein LOC101472616 isoform X1 K17767 AIP; AH receptor-interacting protein D 101477549 aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein D 101483837 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 101485670 mitochondrial import receptor subunit TOM40B isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 101472306 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 101464782 tomm40; mitochondrial import receptor subunit TOM40 homolog isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 101475867 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 101479464 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 101484224 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 112433043 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 101470981 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 101467967 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 101485315 samm50; sorting and assembly machinery component 50 homolog isoform X1 K07277 SAM50; outer membrane protein insertion porin family D 101485700 sorting and assembly machinery component 50 homolog B isoform X1 K07277 SAM50; outer membrane protein insertion porin family C Porin D 101468605 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 101464912 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 101472641 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 101479017 voltage-dependent anion-selective channel protein 2 isoform X2 K15041 VDAC3; voltage-dependent anion channel protein 3 D 101473099 voltage-dependent anion-selective channel protein 2 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 101478972 mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin D 101478845 metaxin-1 K17776 MTX; metaxin D 101476330 mtx2; metaxin-2 K17776 MTX; metaxin D 101476256 myo19; unconventional myosin-XIX K25838 MYO19; myosin XIX D 101468829 mitochondrial amidoxime-reducing component 1 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 101471163 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101474652 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 112431274 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 112436570 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101464162 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 101478112 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 101470446 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 101469050 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 101471833 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 101465716 mitochondrial intermembrane space import and assembly protein 40-B K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 101467661 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 112434290 mitochondrial intermembrane space import and assembly protein 40-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 101484136 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 101464687 MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10 D 101470279 MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10 D 101468341 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 101487367 MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 101466629 mucin-2 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 101476516 chchd3; MICOS complex subunit MIC19 isoform X5 K17563 CHCHD3; MICOS complex subunit MIC19 D 101477813 MICOS complex subunit mic25-a isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 101472905 chchd6; MICOS complex subunit MIC25 isoform X2 K17564 CHCHD6; MICOS complex subunit MIC25 D 101478976 MICOS complex subunit MIC26 K24625 APOO; MICOS complex subunit MIC26 D 101467887 MICOS complex subunit MIC26 isoform X1 K24625 APOO; MICOS complex subunit MIC26 D 101486644 MICOS complex subunit MIC27 isoform X1 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 101464687 MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10 D 101470279 MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10 D 101468341 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 101468310 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 101487855 timm23; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 101466320 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 101472023 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 101483066 timm21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 101473467 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 101477384 mcu; calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial D 101478319 micu1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 101476169 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 112429990 mcub; calcium uniporter regulatory subunit MCUb, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 101488016 calcium uniporter protein, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 101478003 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 101478718 smdt1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 101486379 mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 101475753 letm1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 101479874 letm2; LETM1 domain-containing protein LETM2, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 101485770 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 112429868 mitochondrial inner membrane protease subunit 2-like K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 101469636 immp2l; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 101475926 transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 101487785 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 101472046 mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 101482224 coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 101473596 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 101464271 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 101484508 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 101482082 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 101485205 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 C Other matrix factors D 101474814 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 101472648 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 101479497 mipep; mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 101471832 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 101486573 dnaJ homolog subfamily A member 3, mitochondrial K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 101478521 dnaJ homolog subfamily A member 3, mitochondrial isoform X2 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 101485428 tamm41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 101486688 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 101473226 persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 101473515 persulfide dioxygenase ETHE1, mitochondrial-like K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 101473809 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 101471182 poldip2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 101465790 cyclic AMP-responsive element-binding protein 1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 101472017 creb1; cyclic AMP-responsive element-binding protein 1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 101484645 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 101481737 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 101477446 sp1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1 D 101481694 transcriptional repressor protein YY1 K09201 YY; transcription factor YY D 101483827 transcriptional repressor protein YY1 isoform X1 K09201 YY; transcription factor YY D 101472419 gabpb2; GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta D 101484483 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 101475731 nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1 D 101473441 nfe2; transcription factor NF-E2 45 kDa subunit isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 101467713 nfe2l2; nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 101479115 metallothionein K14739 MT1_2; metallothionein 1/2 D 112435134 metallothionein K14739 MT1_2; metallothionein 1/2 C Coactivators D 101480402 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X7 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 101476034 peroxisome proliferator-activated receptor gamma coactivator 1-alpha K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 101471689 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 101480327 peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 101470904 crtc1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 101481701 CREB-regulated transcription coactivator 1 isoform X3 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 101467023 CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 101478121 ep300; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 101468013 histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 101476833 crebbp; CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 101486290 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 101464286 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 105941477 lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 101472359 frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 106676935 fxn; frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1] D 101475946 fdx1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 101472993 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 101468891 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 101484508 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 101468265 hscb; iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB D 101475354 sil1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1 D 101468752 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 101477625 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 101487789 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 101474449 iba57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 101465714 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 101480388 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 101469705 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 101480921 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 101477275 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 101487885 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 101481069 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2 D 101470441 sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4 D 101471447 sideroflexin-5 K23503 SFXN5; sideroflexin-5 D 101484418 sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 101469965 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 101464009 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 101480171 carnitine O-palmitoyltransferase 1, liver isoform isoform X2 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 101481455 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 101480158 dhtkd1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 101476076 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 101486868 host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1 D 101464951 host cell factor 1 K14966 HCFC1; host cell factor 1 D 101487331 hcfc2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2 D 101475773 htt; huntingtin isoform X1 K04533 HD; huntingtin D 101469665 steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha D 101473368 esrrb; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 101467647 steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta D 101466090 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 101469694 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 101481777 estrogen-related receptor gamma isoform X2 K08554 NR3B3; estrogen-related receptor gamma D 101477588 nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 101487955 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 101471464 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 101475120 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 101480414 sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 101478266 protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 112435998 serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 101480845 uxt; protein UXT isoform X1 K26537 UXT; protein UXT B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 101477219 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 101473311 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 isoform X1 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 101486849 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 101475604 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 101488053 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 101480965 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 101483922 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 101486917 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 101475842 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 101463753 acad9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 101477955 nubpl; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 101486981 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 101473489 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 101483249 rtn4ip1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 101485168 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 101475131 sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 101474815 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 101465291 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 101473505 ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 101468362 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 101471699 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 101478664 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 101477766 ubiquinol-cytochrome-c reductase complex assembly factor 3 isoform X1 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 101465304 lg8h16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 101467755 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 101484285 lg7h12orf73; uncharacterized protein C12orf73 homolog isoform X1 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 101471897 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 101476094 cmc1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 101476565 cmc2; COX assembly mitochondrial protein 2 homolog isoform X1 K18172 CMC2; COX assembly mitochondrial protein 2 D 101473316 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1 D 101475535 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 101480893 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 112432507 cytochrome c oxidase assembly factor 3 homolog, mitochondrial-like K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 101479994 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 101469650 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 101475621 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 101474772 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 101472949 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 101465124 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 101478185 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14 D 101470230 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 105941112 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 101487158 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 101469218 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18 D 101473140 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 101485366 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 101480763 putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 101480077 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 101484897 pet100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 105940473 pet117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 101473064 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 101467366 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 101482735 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 101485020 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 101483192 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 101467257 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 101463841 apopt1; apoptogenic protein 1, mitochondrial isoform X1 K23506 APOPT1; apoptogenic protein 1 D 101471897 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 101467755 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 101468704 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 101476798 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 101475881 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 101470817 tmem70; transmembrane protein 70, mitochondrial isoform X2 K17966 TMEM70; transmembrane protein 70, mitochondrial D 111500345 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid D 101471412 atp5md; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 101466797 mitofusin-1 isoform X4 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 101484571 mfn1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 101476877 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 101474999 opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 101472855 opa3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein D 101487980 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 101471225 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 101469142 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 101484052 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 101475737 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 101468197 bax; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 112432380 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX D 101474618 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101468757 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101471206 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101476176 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 101472185 small ubiquitin-related modifier 3 isoform X2 K12160 SUMO; small ubiquitin-related modifier D 101479826 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 101485310 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 101474245 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 101486041 small ubiquitin-related modifier 2 isoform X1 K12160 SUMO; small ubiquitin-related modifier D 112434737 sumo2; small ubiquitin-related modifier 2 isoform X1 K12160 SUMO; small ubiquitin-related modifier D 101480068 endophilin-B1 K11248 SH3GLB1; endophilin-B1 D 101479506 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 101480751 mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier D 101470740 mff; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor D 101485256 mitochondrial fission factor homolog A isoform X1 K22076 MFF; mitochondrial fission factor D 101472669 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 101487237 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 101469385 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 101484103 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 101466858 mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 101475075 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 101465713 pld6; mitochondrial cardiolipin hydrolase isoform X1 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 101465073 miga2; mitoguardin 2 K27289 MIGA; mitoguardin D 101477958 miga1; mitoguardin 1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 101487522 actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 101470738 actb; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 101464190 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 101487996 actin, cytoplasmic 2-like K05692 ACTB_G1; actin beta/gamma 1 D 101476622 actin, cytoplasmic D 101478243 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 101477999 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 101469653 phb; prohibitin K17080 PHB1; prohibitin 1 D 101478560 prohibitin-2 K17081 PHB2; prohibitin 2 D 101465856 prohibitin-2 isoform X1 K17081 PHB2; prohibitin 2 D 101477886 ktn1; kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 101474618 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101468757 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101471206 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101466683 unconventional myosin-Va K10357 MYO5; myosin V D 101480822 myo5a; unconventional myosin-Va isoform X4 K10357 MYO5; myosin V D 101472368 myo5b; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V D 101482435 unconventional myosin-Vb K10357 MYO5; myosin V D 101466400 myo5c; unconventional myosin-Vc K10357 MYO5; myosin V D 101472383 E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 101485833 diablo homolog, mitochondrial isoform X1 K10522 DIABLO; diablo D 101486140 diablo; diablo homolog, mitochondrial K10522 DIABLO; diablo C Morphogenesis factors D 101484824 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25 D 101484650 mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 101469002 mitochondrial Rho GTPase 1-A isoform X3 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 101468341 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 101473059 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 101471132 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 101487985 nedd4; E3 ubiquitin-protein ligase NEDD4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 101469515 oxr1; oxidation resistance protein 1 isoform X1 K25437 OXR1; oxidation resistance protein 1 D 101468764 msto1; protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 101465525 atg2a; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 101487020 atg2b; autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2 D 101473950 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 101483721 cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 101476006 atg4d; cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 101479434 atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 101482235 atg4b; cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 101480416 atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5 D 101470672 becn1; beclin-1 K08334 BECN; beclin D 101484318 atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 101473761 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 101471919 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 101483169 gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 101467473 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 112435145 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 101470365 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 101471315 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 101467642 atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 101486009 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12 D 101466786 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 101485162 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 105941231 autophagy-related protein 16-2 isoform X2 K20868 ATG16L2; autophagy-related protein 16-2 D 101465687 wipi1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 101471896 wipi2; WD repeat domain phosphoinositide-interacting protein 2 isoform X4 K17908 WIPI1_2; autophagy-related protein 18 D 101473644 vacuolar protein 8 K08332 VAC8; vacuolar protein 8 C Parkin-dependent mechanism factors D 101482320 prkn; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31] D 101486347 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 101464342 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 101472469 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 101471225 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 101469142 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 101468330 sqstm1; sequestosome-1 K14381 SQSTM1; sequestosome 1 D 101486558 tax1-binding protein 1 homolog B K21347 TAX1BP1; Tax1-binding protein 1 D 101466606 tax1-binding protein 1 homolog B K21347 TAX1BP1; Tax1-binding protein 1 D 101476941 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 101473599 ambra1; activating molecule in BECN1-regulated autophagy protein 1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 101468081 atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13 D 101472768 serine/threonine-protein kinase ULK1 isoform X2 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 101471730 serine/threonine-protein kinase ULK2 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 101479468 ulk2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 101466197 rb1cc1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 101474541 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG D 101475013 heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG D 101486975 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 101474459 hsp90 co-chaperone Cdc37 isoform X1 K09554 CDC37; cell division cycle protein 37 D 101468002 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 101469682 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 101467626 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 101471598 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 101477054 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 101471601 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 101477832 fundc1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 D 101471568 FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 101487955 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 101471464 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 101486259 map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 101482496 microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 101473350 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 101467126 microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 101468295 next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 101479164 nbr1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 101479260 tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 101479564 tecpr1; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 101468258 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 101481481 zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 101481978 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 101470739 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 101485355 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 101480916 protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN D 101483913 protein C19orf12 K23168 MPAN; protein MPAN D 101485699 protein C19orf12 homolog K23168 MPAN; protein MPAN ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024