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Mitochondrial Biogenesis - Notothenia coriiceps (black rockcod)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 10752035 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 10752023 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 10752029 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 10752031 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 10752030 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 10752032 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 10752034 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 10752033 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 10752024 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 10752025 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 10752028 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 10752026 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 10752027 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 104950622 polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
D 104951345 DNA-directed RNA polymerase, mitochondrial-like K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 104950813 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 104950249 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 104959803 dimethyladenosine transferase 2, mitochondrial-like K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
D 104966711 dimethyladenosine transferase 2, mitochondrial-like K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 104943666 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 104966836 tsfm; elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts
D 104942719 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 104957410 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 104967825 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 104942276 transcription termination factor 2, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 104947045 mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 104953788 transcription termination factor 2, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 104962949 mterf1; transcription termination factor 1, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 104966187 mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 104964599 guf1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 104958668 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 104960843 ribonuclease P protein subunit p29-like K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 104955529 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 104946301 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 104942708 rpp25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 104953496 uncharacterized protein LOC104953496 isoform X1 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 104953506 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 104959142 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 104958915 trmt10c; mitochondrial ribonuclease P protein 1 K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 104961420 kiaa0391; mitochondrial ribonuclease P protein 3 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 104964198 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 104964199 LOW QUALITY PROTEIN: putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 104947977 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 104956587 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 104941155 dhx30; putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 104966137 lace1; lactation elevated protein 1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 104954159 xrcc6bp1; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 104944967 ATP-dependent RNA helicase SUPV3L1, mitochondrial-like K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 104947575 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 104941834 ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 104949645 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 104958400 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 104941292 mitoferrin-1-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 104955139 slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 104962798 mitoferrin-2-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 104948721 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 104963927 eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 104952722 yars; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 104955519 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 104940929 lars; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 104965350 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 104942946 gars; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 104963184 rars; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 104967315 rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 104942762 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 104963070 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 104942800 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial isoform X1 K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 104953910 mtpap; poly(A) RNA polymerase, mitochondrial isoform X1 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 104959239 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 104961334 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 104951597 putative methyltransferase NSUN3 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 104951605 uncharacterized protein LOC104951605 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 104954312 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 104948999 rpusd4; RNA pseudouridylate synthase domain-containing protein 4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 104964283 Williams-Beuren syndrome chromosomal region 16 protein-like K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 104942232 ngrn; neugrin K23496 NGRN; neugrin
D 104955538 trub2; probable tRNA pseudouridine synthase 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 104948283 fastkd1; FAST kinase domain-containing protein 1 K27754 FASTKD1; FAST kinase domain-containing protein 1
D 104945504 FAST kinase domain-containing protein 2-like K18190 FASTKD2; FAST kinase domain-containing protein 2
D 104949655 LOW QUALITY PROTEIN: FAST kinase domain-containing protein 3-like K27755 FASTKD3; FAST kinase domain-containing protein 3
D 104951161 tbrg4; protein TBRG4 K27756 TBRG4; FAST kinase domain-containing protein 4
D 104947501 fastkd5; FAST kinase domain-containing protein 5 K27757 FASTKD5; FAST kinase domain-containing protein 5
D 104962307 probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor
D 104964454 mettl15; probable methyltransferase-like protein 15 isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 104967291 UPF0160 protein MYG1, mitochondrial-like K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 104958608 uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 104944014 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 104944579 polg2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2
D 104951051 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 104963445 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 104950658 twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 104945614 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 104946467 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 104949019 atad3a; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 104959049 uncharacterized protein LOC104959049 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 104948859 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 104946515 uncharacterized protein YMR317W-like K27759 MTNAP1; mitochondrial nucleoid-associated protein 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 104957469 dnaja2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 104947980 rhot1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 104960765 mitochondrial Rho GTPase 1-A-like K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 104942238 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 104944608 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 104945953 hspa6; heat shock 70 kDa protein 6 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 104954997 hspa8; heat shock cognate 71 kDa protein isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 104961379 heat shock cognate 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 104943191 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 104955323 aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
D 104958010 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 104958011 protein TANC1-like K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 104952061 tomm20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 104950540 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 104954105 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 104963749 tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 104964651 mitochondrial import receptor subunit TOM40B-like K11518 TOM40; mitochondrial import receptor subunit TOM40
C TOB/SAM complex
D 104948416 sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
D 104948868 samm50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 104960858 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 104943447 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2
D 104949930 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 104948043 voltage-dependent anion-selective channel protein 2-like isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
D 104956686 vdac3; voltage-dependent anion-selective channel protein 3 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 104953146 mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 104942854 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 104946436 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 104952261 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 104942624 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 104964528 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 104954440 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 104949936 mitochondrial intermembrane space import and assembly protein 40-B-like isoform X1 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 104952072 mitochondrial intermembrane space import and assembly protein 40-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 104956837 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 104942779 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 104966044 minos1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 104964520 protein QIL1 K24624 MICOS13; MICOS complex subunit MIC13
D 104962453 MICOS complex subunit MIC19-like K17563 CHCHD3; MICOS complex subunit MIC19
D 104964142 proline-rich extensin-like protein EPR1 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 104942275 MICOS complex subunit mic25a-like K17564 CHCHD6; MICOS complex subunit MIC25
D 104959440 chchd6; MICOS complex subunit MIC25 K17564 CHCHD6; MICOS complex subunit MIC25
D 104948614 apolipoprotein O-like K24625 APOO; MICOS complex subunit MIC26
D 104960625 apoo; apolipoprotein O isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 104955299 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 104942779 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 104966044 minos1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
C TIM22 complex
D 104942047 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 104946511 timm23; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 104952112 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 104961559 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 104953978 timm21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
C Mitochondrial calcium uniporter complex
D 104952219 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 104957294 calcium uptake protein 1, mitochondrial-like K22827 MICU1; calcium uptake protein 1, mitochondrial
D 104943497 calcium uptake protein 2, mitochondrial-like K22828 MICU2; calcium uptake protein 2, mitochondrial
D 104954472 calcium uptake protein 2, mitochondrial-like K22828 MICU2; calcium uptake protein 2, mitochondrial
D 104941007 calcium uniporter protein, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 104964052 smdt1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 104943226 mitochondrial calcium uniporter regulator 1-like K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 104955635 LETM1 and EF-hand domain-containing protein 1, mitochondrial-like isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 104967082 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 104965697 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A
D 104951162 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 104951949 mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 104956720 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
D 104959919 ociad1; OCIA domain-containing protein 1 K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 104944842 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 104949086 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 104967667 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 104960157 mitochondrial import inner membrane translocase subunit TIM16-like isoform X1 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 104958595 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 104960160 dnaja3; dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 104946833 tamm41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 104941965 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 104950320 ethe1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 104961482 poldip2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 104950718 cyclic AMP-responsive element-binding protein 1-like K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 104957759 cyclic AMP-responsive element-binding protein 1-like isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 104957410 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 104967825 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 104962038 transcription factor Sp1-like K04684 SP1; transcription factor Sp1
D 104960360 transcriptional repressor protein YY1-like K09201 YY; transcription factor YY
D 104960657 transcriptional repressor protein YY1-like isoform X1 K09201 YY; transcription factor YY
D 104950813 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 104953415 nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 104952544 nfe2; transcription factor NF-E2 45 kDa subunit isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 104965531 nfe2l2; nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
C Coactivators
D 104953595 peroxisome proliferator-activated receptor gamma coactivator 1-alpha-like isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 104967499 peroxisome proliferator-activated receptor gamma coactivator 1-beta-like K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 104955385 peroxisome proliferator-activated receptor gamma coactivator-related protein 1-like K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 104963202 peroxisome proliferator-activated receptor gamma coactivator-related protein 1-like isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 104959362 crtc1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 104959378 CREB-regulated transcription coactivator 1-like K15309 CRTC1; CREB-regulated transcription coactivator 1
D 104960178 crebbp; CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 104967661 histone acetyltransferase p300-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 104961367 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 104946819 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 104958920 iron-sulfur cluster assembly enzyme ISCU, mitochondrial-like K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 104950501 adrenodoxin-like protein, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 104962498 hscb; iron-sulfur cluster co-chaperone protein HscB, mitochondrial isoform X1 K04082 hscB; molecular chaperone HscB
D 104959897 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 104949306 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 104960610 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 104960907 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 104941059 iba57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 104946244 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 104957615 nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 104944105 bola1; bolA-like protein 1 isoform X1 K22066 BOLA1; BolA-like protein 1
D 104962985 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 104943165 sideroflexin-1-like K23500 SFXN1_3; sideroflexin-1/3
D 104947754 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 104961779 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2
D 104954175 sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4
D 104949072 sideroflexin-5-like K23503 SFXN5; sideroflexin-5
D 104956967 sfxn5; sideroflexin-5 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 104941360 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 104948946 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 104950780 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 104940829 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 104953823 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 104945730 hcfc1; host cell factor 1 K14966 HCFC1; host cell factor 1
D 104946235 hcfc2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2
D 104946108 huntingtin-like K04533 HD; huntingtin
D 104957962 esrra; steroid hormone receptor ERR1 isoform X1 K08552 NR3B1; estrogen-related receptor alpha
D 104943723 esrrb; steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta
D 104964431 steroid hormone receptor ERR2-like K08553 NR3B2; estrogen-related receptor beta
D 104964076 esrrg; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 104944207 nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 104959371 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 104959556 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 104964612 sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 104962360 serac1; protein SERAC1 K23504 SERAC1; protein SERAC1
D 104962497 uxt; protein UXT K26537 UXT; protein UXT
D 104958623 ES1 protein homolog, mitochondrial-like K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 104961732 ES1 protein, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 104943813 UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69
D 104950423 fam214b; protein FAM214B K28528 ATOS; protein Atossa
D 104953689 fam214a; protein FAM214A isoform X1 K28528 ATOS; protein Atossa
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 104949282 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 104942932 ndufaf2; mimitin, mitochondrial K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 104949005 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 104958892 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 104959710 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5-like K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 104944809 uncharacterized protein C17orf89 homolog K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 104961654 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 104942759 rtn4ip1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 104963850 reticulon-4-interacting protein 1 homolog, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 104961759 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 104955604 sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 104962080 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 104955626 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 104955697 LOW QUALITY PROTEIN: mitochondrial chaperone BCS1-like K08900 BCS1; mitochondrial chaperone BCS1
D 104954339 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 104948859 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 104946340 protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 104956316 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 104948409 uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 104960038 uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 104943545 cmc1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 104949420 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 104956093 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 104959956 cytochrome c oxidase assembly factor 3 homolog, mitochondrial-like isoform X1 K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 104946938 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 104966797 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 104943477 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 104945052 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 104944645 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 104967285 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 104955150 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 104951593 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 104940857 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 104964198 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 104964199 LOW QUALITY PROTEIN: putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 104952494 pet100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 104963905 LOW QUALITY PROTEIN: mitochondrial inner membrane protein OXA1L-like K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 104965749 mitochondrial inner membrane protein OXA1L-like K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 104948927 surfeit locus protein 1-like K14998 SURF1; surfeit locus 1 family protein
D 104954622 surfeit locus protein 1-like K14998 SURF1; surfeit locus 1 family protein
D 104946671 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 104959058 protein SCO2 homolog, mitochondrial-like K23755 SCO2; protein SCO2
D 104946772 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 104960038 uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1
D 104956316 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 104956038 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
D 104959739 HIG1 domain family member 2A-like K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial
C Complex-V assembly factors
D 104949059 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 104949932 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 104942505 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 104947669 usmg5; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 104947676 mitofusin-1-like K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 104941303 dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 104960645 opa3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein
D 104951470 parl; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 104944891 LOW QUALITY PROTEIN: apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 104946810 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 104960035 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 104964463 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 104964901 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 104944100 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 104945654 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 104946064 sumo2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 104947988 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 104958714 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 104955778 endophilin-B1-like K11248 SH3GLB1; endophilin-B1
D 104950233 mff; mitochondrial fission factor K22076 MFF; mitochondrial fission factor
D 104959813 mitochondrial fission factor homolog A-like K22076 MFF; mitochondrial fission factor
D 104961080 ganglioside-induced differentiation-associated protein 1-like K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 104949140 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 104967612 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 104951181 mitochondrial dynamics protein MID51-like K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 104951312 mitochondrial dynamics protein MID51-like K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 104967902 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 104950518 pld6; mitochondrial cardiolipin hydrolase isoform X1 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
C Actin cytoskeleton organization
D 104951171 actb; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 104965067 actin, cytoplasmic 3-like K05692 ACTB_G1; actin beta/gamma 1
D 104948046 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 104949138 phb; prohibitin K17080 PHB1; prohibitin 1
D 104948176 ktn1; kinectin K17975 KTN1; kinectin
C Retention of mitochondria
D 104946810 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 104960035 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 104964463 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 104940954 unconventional myosin-Va-like K10357 MYO5; myosin V
D 104946315 unconventional myosin-Va-like K10357 MYO5; myosin V
D 104960106 myo5a; unconventional myosin-Va K10357 MYO5; myosin V
D 104960108 myo5c; unconventional myosin-Vc isoform X1 K10357 MYO5; myosin V
D 104951294 diablo; diablo homolog, mitochondrial K10522 DIABLO; diablo
D 104952394 diablo homolog, mitochondrial-like K10522 DIABLO; diablo
C Morphogenesis factors
D 104947980 rhot1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 104960765 mitochondrial Rho GTPase 1-A-like K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 104956442 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 104958847 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 104966441 nedd4; E3 ubiquitin-protein ligase NEDD4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 104964947 LOW QUALITY PROTEIN: oxidation resistance protein 1-like K25437 OXR1; oxidation resistance protein 1
D 104951173 PRELI domain-containing protein 1, mitochondrial-like K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 104967511 prelid1; PRELI domain-containing protein 1, mitochondrial K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 104941487 protein slowmo homolog 2-like K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
D 104961551 protein slowmo homolog 2-like K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 104956023 autophagy-related protein 2 homolog A-like isoform X1 K17906 ATG2; autophagy-related protein 2
D 104960911 atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 104964301 autophagy-related protein 2 homolog A-like K17906 ATG2; autophagy-related protein 2
D 104964161 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 104958087 atg4b; cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 104962122 atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 104964056 atg4d; cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 104967609 becn1; beclin-1 K08334 BECN; beclin
D 104954607 atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 104945426 gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 104950885 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 104960404 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 104963252 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 104958712 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 104963896 atg9b; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 104952848 atg10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 104960423 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 104944332 autophagy-related protein 16-2-like K20868 ATG16L2; autophagy-related protein 16-2
D 104944192 WD repeat domain phosphoinositide-interacting protein 1-like K17908 WIPI1_2; autophagy-related protein 18
D 104956914 wipi2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 104963460 wipi1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 104941775 clec16a; protein CLEC16A K19513 CLEC16A; protein CLEC16A
D 104951470 parl; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 104941142 tax1-binding protein 1 homolog A-like K21347 TAX1BP1; Tax1-binding protein 1
D 104949894 tax1-binding protein 1 homolog B-like isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 104945460 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
C Parkin-independent mechanism factors
D 104948990 atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 104943547 serine/threonine-protein kinase ULK1-like isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 104961519 ulk1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 104954052 serine/threonine-protein kinase ULK2-like K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 104955960 rb1cc1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 104950058 hsp90ab1; LOW QUALITY PROTEIN: heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 104962005 heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG
D 104962225 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 104950892 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 104955482 hsp90 co-chaperone Cdc37-like K09554 CDC37; cell division cycle protein 37
D 104947293 smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 104956912 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 104947651 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 104961739 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 104954636 fundc1; FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 104959371 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 104959556 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 104942685 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 104950457 LOW QUALITY PROTEIN: microtubule-associated proteins 1A/1B light chain 3B-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 104964015 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 104945914 next to BRCA1 gene 1 protein-like K17987 NBR1; next to BRCA1 gene 1 protein
D 104960564 next to BRCA1 gene 1 protein-like K17987 NBR1; next to BRCA1 gene 1 protein
D 104946079 tectonin beta-propeller repeat-containing protein 1-like isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 104944716 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 104945225 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 104954711 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 104943459 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 104949268 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 104957830 protein C19orf12 homolog K23168 MPAN; protein MPAN
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025