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Mitochondrial Biogenesis - Octopus bimaculoides (California two-spot octopus)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 27205972 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 106869121 LOW QUALITY PROTEIN: NADH-ubiquinone oxidoreductase chain 2-like K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 27205956 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 27205954 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 27205965 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 27205966 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 27205963 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 27205970 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 27205969 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 27205957 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 27205958 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 27205977 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 27205960 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 27205961 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 106880721 DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 106873366 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
D 106879671 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 106868064 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 106877158 uncharacterized protein LOC106877158 isoform X1 K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 106870599 translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 106877722 translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 106883783 elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 106870016 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 106878110 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 106880155 ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 106876646 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 106877460 transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 106867342 uncharacterized protein LOC106867342 K15031 MTERF; mitochondrial transcription termination factor family protein
D 106871983 translation factor Guf1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 106870598 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 106882309 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 106877138 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 106884283 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 106869399 ribonuclease P protein subunit p20 isoform X1 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 106877581 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 106874933 ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 106879601 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 106870550 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 106873924 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 106884315 pentatricopeptide repeat-containing protein 1, mitochondrial isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 106882152 pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 106868930 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 106869403 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 106874543 AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 106869202 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 106877494 ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 106875199 endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 106870577 uncharacterized protein LOC106870577 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 106875980 mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 106873318 uncharacterized protein LOC106873318 isoform X1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 106871545 GTPase Era, mitochondrial K03595 era; GTPase
D 106868681 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 106882089 tyrosine--tRNA ligase, mitochondrial isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 106871282 leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 106875567 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 106878711 aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 106879482 glycine--tRNA ligase isoform X1 K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 106871987 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 106881690 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 106879571 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial isoform X1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 106867553 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 106868694 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 106872676 poly(A) RNA polymerase, mitochondrial isoform X2 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 106882813 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 106873742 mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 106868619 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 106881478 5-methylcytosine rRNA methyltransferase NSUN4 isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 106873813 uncharacterized protein LOC106873813 isoform X1 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 106876835 RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 106880138 uncharacterized protein LOC106880138 K23496 NGRN; neugrin
D 106877505 pseudouridylate synthase TRUB2, mitochondrial K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 106882541 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 106871759 probable methyltransferase-like protein 15 homolog isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 106873298 MYG1 exonuclease isoform X1 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 106867641 mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 106877835 LOW QUALITY PROTEIN: DNA polymerase subunit gamma-1-like K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 106868952 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 106883065 DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 106867925 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 106869494 uncharacterized protein LOC106869494 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 106882273 twinkle mtDNA helicase isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 106872404 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 106871876 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 106876122 uncharacterized protein LOC106876122 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 106870645 ATP-dependent DNA helicase PIF4-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 106874392 uncharacterized protein LOC106874392 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 106870915 uncharacterized protein LOC106870915 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 106872477 uncharacterized protein LOC106872477 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 106876227 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 106878421 ATPase family AAA domain-containing protein 3-B K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 106872678 dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 106871508 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 106878391 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 106879627 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 106881232 LOW QUALITY PROTEIN: heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 106873940 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 106867879 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 106867870 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 106871540 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 106877834 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
C TOB/SAM complex
D 106874119 sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 106877054 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
C ERMES complex
C Other outer membrane factor
D 106878396 metaxin-2 K17776 MTX; metaxin
D 106881544 metaxin-1 K17776 MTX; metaxin
D 106874221 unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX
D 106872172 mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 106878841 mitochondrial import inner membrane translocase subunit Tim10-B K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
C TIM8/13 complex
D 106884399 mitochondrial import inner membrane translocase subunit Tim13-B K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 106869192 mitochondrial intermembrane space import and assembly protein 40-B K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 106884309 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 106870128 MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10
D 106871626 MICOS complex subunit Mic60 K17785 IMMT; MICOS complex subunit MIC60
D 106874425 MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 106868566 neurofilament heavy polypeptide K17563 CHCHD3; MICOS complex subunit MIC19
D 106874679 MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 106870128 MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10
D 106871626 MICOS complex subunit Mic60 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 106881380 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 106868705 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 106869166 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 106878442 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 106873759 mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 106867904 calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial
D 106869687 calcium uptake protein 1, mitochondrial isoform X2 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 106879101 coiled-coil domain-containing protein 90B, mitochondrial K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 106868837 mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 106874002 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 106873715 transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 106871809 mitochondrial pyruvate carrier 1-like protein isoform X2 K22138 MPC1; mitochondrial pyruvate carrier 1
D 106870757 mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
B Matrix
C MMC/PAM proteins
D 106884504 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 106873137 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 106870469 grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 106874709 mitochondrial import inner membrane translocase subunit TIM14 isoform X1 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 128246981 mitochondrial import inner membrane translocase subunit Tim16-like K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 106881124 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 106879606 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 106879897 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 106868146 heat shock protein 60A K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 106868108 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 106876069 dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 106881807 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 106877800 DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 106871303 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 106872074 polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 106881849 cAMP-responsive element modulator isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 106878110 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 106880155 ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 106877161 transcriptional repressor protein YY1 isoform X1 K09201 YY; transcription factor YY
D 106873792 GA-binding protein subunit beta-1 K09454 GABPB; GA-binding protein transcription factor, beta
D 106873366 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
D 106879671 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 106877210 DNA-binding protein P3A2 isoform X1 K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 106884229 putative uncharacterized protein DDB_G0277255 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 106881030 CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 106876257 CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 106879590 cysteine desulfurase K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 128250636 iron-sulfur cluster assembly scaffold protein IscU-like K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 106880225 LYR motif-containing protein 4-like K22069 LYRM4; LYR motif-containing protein 4
D 106877921 frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1]
D 106868688 adrenodoxin isoform X1 K22070 FDX1; ferredoxin-1, mitochondrial
D 106869397 adrenodoxin-like protein 1, mitochondrial isoform X2 K22071 FDX2; ferredoxin-2, mitochondrial
D 106882139 NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 106873137 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 106884380 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 106881520 nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 106883097 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 106881059 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 106878612 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 106875785 putative transferase CAF17 homolog, mitochondrial isoform X1 K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 106879262 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 106880095 DNA-binding transcriptional regulator BolA K22066 BOLA1; BolA-like protein 1
D 106871621 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 106868929 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 106868689 sideroflexin-2 isoform X2 K23501 SFXN2; sideroflexin-2
D 106874271 sideroflexin-5 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 106870396 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 106881816 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 106874001 2-oxoadipate dehydrogenase complex component E1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 106871283 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 106873592 host cell factor 2 K14966 HCFC1; host cell factor 1
D 106883334 huntingtin K04533 HD; huntingtin
D 106883388 steroid hormone receptor ERR1 isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 106875312 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 106872622 lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 106881695 NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 106876845 protein SERAC1 K23504 SERAC1; protein SERAC1
D 106880301 protein UXT K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 106881200 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 106874923 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 106879602 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 106882715 uncharacterized protein LOC106882715 isoform X1 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 106869034 arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 106880143 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 106879174 protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 106874086 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 106883527 complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 106880906 iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 106869409 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 106879620 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 106875155 complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 106870174 succinate dehydrogenase assembly factor 2, mitochondrial isoform X2 K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 106871007 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 106879250 tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 106883077 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 106869403 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 106881790 uncharacterized protein LOC106881790 isoform X1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 106876313 uncharacterized protein LOC106876313 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
C Complex-IV assembly factors
D 106876952 COX assembly mitochondrial protein homolog isoform X2 K18171 CMC1; COX assembly mitochondrial protein 1
D 106880465 COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 106876657 uncharacterized protein LOC106876657 K18173 COA1; cytochrome c oxidase assembly factor 1
D 106879633 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 106870429 cytochrome c oxidase assembly factor 5 isoform X1 K18178 COA5; cytochrome c oxidase assembly factor 5
D 106878900 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 106884326 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7
D 106868845 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 106869477 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 106876136 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 128246978 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial-like K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 106874135 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 106884001 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 106879748 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 106877053 mitochondrial inner membrane protein OXA1L isoform X2 K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 106867658 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 106874182 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 106869964 probable transcriptional regulatory protein PERMA_0079 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 106869892 cytochrome c oxidase assembly factor 8 isoform X1 K23506 APOPT1; apoptogenic protein 1
D 106875736 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 106876012 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 106873864 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 106868190 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
B Mitochondrial dynamics
C Fission and Fusion factors
D 106881618 mitofusin-2 isoform X2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 106875919 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 106875290 optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 106874295 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 106868686 uncharacterized protein LOC106868686 isoform X1 K14021 BAK; Bcl-2 homologous antagonist/killer
D 106869728 apoptosis regulator BAX isoform X2 K02159 BAX; apoptosis regulator BAX
D 106867941 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 106875394 mitochondrial fission 1 protein isoform X2 K17969 FIS1; mitochondrial fission 1 protein
D 106884298 small ubiquitin-related modifier 3-like isoform X1 K12160 SUMO; small ubiquitin-related modifier
D 106879481 small ubiquitin-related modifier K12160 SUMO; small ubiquitin-related modifier
D 106869469 endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1
D 106875547 mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 106876950 mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor
D 106881764 ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 106874083 uncharacterized protein LOC106874083 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 106874085 uncharacterized protein LOC106874085 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 106868429 mitoguardin K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 106870394 actin, adductor muscle K05692 ACTB_G1; actin beta/gamma 1
D 106875747 actin, adductor muscle K05692 ACTB_G1; actin beta/gamma 1
D 106879182 actin, cytoplasmic 2 isoform X1 K05692 ACTB_G1; actin beta/gamma 1
D 106882825 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 106869073 N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 106875850 prohibitin 1 isoform X1 K17080 PHB1; prohibitin 1
D 106870041 prohibitin-2 K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 106867941 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 106873192 LOW QUALITY PROTEIN: unconventional myosin-Va K10357 MYO5; myosin V
D 106883317 uncharacterized protein LOC106883317 isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 106871910 sorting nexin-25 K17887 SNX25; sorting nexin-25
D 106871508 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 106871626 MICOS complex subunit Mic60 K17785 IMMT; MICOS complex subunit MIC60
D 106869574 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 106884486 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 106873354 E3 ubiquitin-protein ligase NEDD4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 106872830 protein misato homolog 1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 106870186 autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2
D 106877727 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 106877415 cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 106876337 autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 106883798 beclin-1 K08334 BECN; beclin
D 106880300 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 106873160 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 106874365 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 106871037 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 106874580 ubiquitin-like-conjugating enzyme ATG10 isoform X2 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 106871637 ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 106883707 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 106883708 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 106882625 autophagy-related protein 16 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 106875830 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 106879720 uncharacterized protein LOC106879720 K08332 VAC8; vacuolar protein 8
C Parkin-dependent mechanism factors
D 106872239 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 106883998 protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 106876772 serine/threonine-protein kinase Pink1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 106874295 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 106873472 sequestosome-1 K14381 SQSTM1; sequestosome 1
D 106880483 tax1-binding protein 1 homolog K21347 TAX1BP1; Tax1-binding protein 1
C Parkin-independent mechanism factors
D 106871588 autophagy-related protein 13 K08331 ATG13; autophagy-related protein 13
D 106876056 serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 106874584 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 106882217 heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 106870674 hsp90 co-chaperone Cdc37 isoform X1 K09554 CDC37; cell division cycle protein 37
D 106869353 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 106876509 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
D 106877865 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 106875312 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 106882390 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 106877484 next to BRCA1 gene 1 protein K17987 NBR1; next to BRCA1 gene 1 protein
D 106875269 tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 106879851 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 106882755 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 106870832 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 106867269 protein C19orf12 homolog K23168 MPAN; protein MPAN
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024