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Mitochondrial Biogenesis - Osmia lignaria (orchard mason bee)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 117611526 NADH-ubiquinone oxidoreductase chain 5-like K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 117611525 LOW QUALITY PROTEIN: cytochrome b-like K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 117611527 LOW QUALITY PROTEIN: cytochrome c oxidase subunit 1-like K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 117611528 LOW QUALITY PROTEIN: cytochrome c oxidase subunit 2-like K02261 COX2; cytochrome c oxidase subunit 2
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 117605842 DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 117610752 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 117610683 mitochondrial dimethyladenosine transferase 1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 117609951 dimethyladenosine transferase 2, mitochondrial-like isoform X1 K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 117603146 translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 117605100 translation initiation factor IF-3-like K02520 infC; translation initiation factor IF-3
D 117601855 elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 117602392 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 117604131 elongation factor Tu, mitochondrial-like K02358 tuf; elongation factor Tu
D 117600968 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 117602970 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 117602509 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 117610347 transcription termination factor 5, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 117601820 translation factor GUF1 homolog, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 117608697 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 117604990 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 117610015 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 117603109 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 117609231 ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 117605381 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 117607999 uncharacterized protein LOC117607999 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 117606929 ribonuclease P protein subunit p40-like K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 117607216 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 117607659 3-hydroxyacyl-CoA dehydrogenase type-2-like K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 117609087 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 117606179 mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 117608336 uncharacterized protein LOC117608336 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 117602942 uncharacterized protein LOC117602942 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 117608712 uncharacterized protein LOC117608712 K17658 TEFM; transcription elongation factor, mitochondrial
D 117606950 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 117603802 protein PTCD3 homolog, mitochondrial isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 117606136 ATP-dependent RNA helicase DHX30-like K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 117609564 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 117607024 putative ATPase N2B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 117600441 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 117607924 ATP-dependent RNA helicase SUV3 homolog, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 117602187 endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 117602538 ADP,ATP carrier protein-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 117602649 ADP/ATP translocase 4-like isoform X1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 117602842 ADP,ATP carrier protein 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 117607927 mitoferrin-1-like isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 117601824 mitochondrial assembly of ribosomal large subunit protein 1 isoform X1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 117605503 GTPase Era, mitochondrial K03595 era; GTPase
D 117606437 tyrosine--tRNA ligase, mitochondrial isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 117604434 tyrosine--tRNA ligase, cytoplasmic isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 117609343 probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 117604733 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 117606232 aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 117605742 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 117608320 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 117604809 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 117608875 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 117606559 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 117609585 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 117607675 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 117604906 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 117607310 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 117608040 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 117601130 mitochondrial RNA pseudouridine synthase rpusd4-like K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 117610269 RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 117610220 uncharacterized protein LOC117610220 K23496 NGRN; neugrin
D 117605287 LOW QUALITY PROTEIN: mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 117603028 uncharacterized protein LOC117603028 K18190 FASTKD2; FAST kinase domain-containing protein 2
D 117602413 probable peptide chain release factor C12orf65, mitochondrial K23498 COXPD7; peptide chain release factor
D 117603014 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 117606702 UPF0160 protein MYG1, mitochondrial isoform X1 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 117601348 uncharacterized protein LOC117601348 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 117612062 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 117606551 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
C Mitochondrial DNA maintenance factors
D 117605120 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 117603682 twinkle protein, mitochondrial isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 117603252 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 117611067 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 117611360 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 117609488 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 117607312 ATPase family AAA domain-containing protein 3A homolog K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 117601908 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 117608186 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 117602627 heat shock 70 kDa protein cognate 4-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 117603907 heat shock 70 kDa protein cognate 4-like isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
B Outer membrane
C Transporter outer membrane (TOM) complex
D 117607049 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 117601259 mitochondrial import receptor subunit TOM40 homolog 1-like K11518 TOM40; mitochondrial import receptor subunit TOM40
D 117611597 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 117602792 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 117600511 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
C TOB/SAM complex
D 117607395 sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 117605915 voltage-dependent anion-selective channel protein 2-like K05862 VDAC1; voltage-dependent anion channel protein 1
D 117609096 voltage-dependent anion-selective channel-like K15040 VDAC2; voltage-dependent anion channel protein 2
C ERMES complex
C Other outer membrane factor
D 117609609 metaxin-2-like isoform X1 K17776 MTX; metaxin
D 117610341 metaxin-1 isoform X1 K17776 MTX; metaxin
D 117602570 unconventional myosin-XIX-like isoform X1 K25838 MYO19; myosin XIX
D 117604732 mitochondrial amidoxime-reducing component 1-like isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 117612033 mitochondrial amidoxime reducing component 2 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 117605983 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 117601158 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 117605171 mitochondrial import inner membrane translocase subunit Tim10 B isoform X1 K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 117611671 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 117607416 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 117609988 mitochondrial intermembrane space import and assembly protein 40-A K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 117604621 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 117602276 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 117604063 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 117602280 trichohyalin isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 117607738 MICOS complex subunit MIC13-like isoform X1 K24624 MICOS13; MICOS complex subunit MIC13
D 117610621 MICOS complex subunit MIC25 K17563 CHCHD3; MICOS complex subunit MIC19
D 117605554 MICOS complex subunit MIC27 isoform X1 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 117602276 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 117604063 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 117602280 trichohyalin isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 117605720 mitochondrial import inner membrane translocase subunit Tim22 isoform X1 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 117607628 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 117605655 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 117602069 mitochondrial import inner membrane translocase subunit Tim17-A-like K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 117602887 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 117600754 mitochondrial import inner membrane translocase subunit TIM50-C-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 117605956 calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial
D 117606503 calcium uptake protein 1 homolog, mitochondrial-like isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 117602690 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
C Other inner membrane factors
D 117601163 mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 117600587 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 117607249 transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 117607652 mitochondrial pyruvate carrier 1-like K22138 MPC1; mitochondrial pyruvate carrier 1
D 117601752 mitochondrial pyruvate carrier 1-like K22138 MPC1; mitochondrial pyruvate carrier 1
D 117608596 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
D 117612037 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
B Matrix
C MMC/PAM proteins
D 117610216 mitochondrial import inner membrane translocase subunit TIM44 isoform X1 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 117610553 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 117602739 mitochondrial import inner membrane translocase subunit TIM14 isoform X1 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 117610381 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 117605431 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 117601169 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 117608011 mitochondrial-processing peptidase subunit beta-like K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 117606049 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 117607379 heat shock protein 60A-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 117607302 10 kDa heat shock protein, mitochondrial-like isoform X1 K04078 groES; chaperonin GroES
D 117607304 10 kDa heat shock protein, mitochondrial-like isoform X1 K04078 groES; chaperonin GroES
D 117602438 protein tumorous imaginal discs, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 117608683 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 117603951 uncharacterized protein C24H6.02c-like K17808 ZIM17; mitochondrial protein import protein ZIM17
D 117600200 uncharacterized protein LOC117600200 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 117608498 persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 117601990 polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 117605323 cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 117600968 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 117602970 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 117607487 transcriptional repressor protein YY1-like isoform X1 K09201 YY; transcription factor YY
D 117609266 GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 117610752 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 117610027 DNA-binding protein P3A2 isoform X1 K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 117609725 NK-tumor recognition protein isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 117600341 CREB-regulated transcription coactivator 1-like isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 117608258 histone lysine acetyltransferase CREBBP isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 117603222 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 117610755 iron-sulfur cluster assembly scaffold protein IscU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 117607724 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 117601774 frataxin homolog, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 117610335 adrenodoxin-like protein 2, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 117600056 adrenodoxin-like protein 1, mitochondrial isoform X1 K22071 FDX2; ferredoxin-2, mitochondrial
D 117610553 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 117600712 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 117600920 nucleotide exchange factor Sil1 K14001 SIL1; nucleotide exchange factor SIL1
D 117602048 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 117610442 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 117603767 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 117602673 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 117604171 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 117601878 bolA-like protein DDB_G0274169 isoform X1 K22066 BOLA1; BolA-like protein 1
D 117600374 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 117603708 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 117603893 sideroflexin-2 K23501 SFXN2; sideroflexin-2
C Other regulator of mitochondrial biogenesis
D 117607987 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 117606919 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial isoform X1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 117607207 F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 117600234 host cell factor isoform X1 K14966 HCFC1; host cell factor 1
D 117604819 huntingtin K04533 HD; huntingtin
D 117611743 lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 117607607 NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 117605056 protein SERAC1-like K23504 SERAC1; protein SERAC1
D 117603135 protein UXT homolog K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 117602875 complex I intermediate-associated protein 30, mitochondrial isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 117610404 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 117608972 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 117601272 protein NDUFAF4 homolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 117609318 arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 117604350 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 117608391 protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 117610317 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 117601463 complex I assembly factor ACAD9, mitochondrial-like isoform X1 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 117610749 iron-sulfur protein NUBPL-like isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 117609465 FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 117606148 reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 117604897 reticulon-4-interacting protein 1 homolog, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 117608966 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 117610259 succinate dehydrogenase assembly factor 2, mitochondrial-like K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 117606860 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 117608678 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 117609564 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 117611421 uncharacterized protein LOC117611421 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 117611431 uncharacterized protein LOC117611431 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 117603994 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 117603995 uncharacterized protein LOC117603995 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 117605612 uncharacterized protein LOC117605612 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 117605384 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 117608566 uncharacterized protein LOC117608566 K18173 COA1; cytochrome c oxidase assembly factor 1
D 117610690 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 117602790 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 117607882 cytochrome c oxidase assembly factor 7 homolog isoform X1 K18180 COA7; cytochrome c oxidase assembly factor 7
D 117601910 protoheme IX farnesyltransferase, mitochondrial isoform X1 K02257 COX10; heme o synthase [EC:2.5.1.141]
D 117606266 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 117604106 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 117611827 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 117609516 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 117601746 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 117608300 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 117607350 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 117608336 uncharacterized protein LOC117608336 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 117602942 uncharacterized protein LOC117602942 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 117601969 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 117611853 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 117606564 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 117603283 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 117602353 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1
D 117605612 uncharacterized protein LOC117605612 K27319 STMP1; short transmembrane mitochondrial protein 1
D 117603994 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 117605776 transmembrane protein 223 isoform X1 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 117607222 ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 117608691 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 117605118 uncharacterized protein LOC117605118 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 117602340 transmembrane GTPase Marf K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 117606668 dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 117609940 putative OPA3-like protein CG13603 K23166 OPA3; optic atrophy 3 protein
D 117603163 TP53-regulated inhibitor of apoptosis 1-like isoform X1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 117611852 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 117601034 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 117608198 mitochondrial fission 1 protein isoform X1 K17969 FIS1; mitochondrial fission 1 protein
D 117607983 small ubiquitin-related modifier-like K12160 SUMO; small ubiquitin-related modifier
D 117601354 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 117604556 endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1
D 117603058 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier
D 117608647 transport and Golgi organization protein 11 K22076 MFF; mitochondrial fission factor
D 117604616 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 117608103 mitoguardin K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 117601604 actin-5C K05692 ACTB_G1; actin beta/gamma 1
D 117608578 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 117608267 N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 117603284 protein l(2)37Cc K17080 PHB1; prohibitin 1
D 117604330 prohibitin-2 K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 117601034 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 117603170 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
C Morphogenesis factors
D 117602269 sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 117601908 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 117604063 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 117602280 trichohyalin isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 117611995 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 117612079 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29
D 117601005 E3 ubiquitin-protein ligase Nedd-4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 117601152 protein misato K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 117609942 autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2
D 117600767 ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 117602062 cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 117611823 cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 117605261 autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 117602700 beclin-1-like protein isoform X1 K08334 BECN; beclin
D 117606680 ubiquitin-like modifier-activating enzyme atg7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 117609603 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 117606480 autophagy-related protein 9A isoform X1 K17907 ATG9; autophagy-related protein 9
D 117602166 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 117607447 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12
D 117610079 beclin 1-associated autophagy-related key regulator isoform X1 K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 117606126 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 117604690 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 117609528 E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 117603211 E3 ubiquitin-protein ligase NRDP1 isoform X1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 117604424 protein CLEC16A homolog isoform X1 K19513 CLEC16A; protein CLEC16A
D 117606587 serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 117611852 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 117612078 sequestosome-1 K14381 SQSTM1; sequestosome 1
C Parkin-independent mechanism factors
D 117606885 autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 117608121 serine/threonine-protein kinase unc-51 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 117602500 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 117601204 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG
D 117609470 heat shock protein 83-like K04079 HSP90A; molecular chaperone HtpG
D 117600528 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 117601834 E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 117605944 uncharacterized protein LOC117605944 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 117612055 microtubule-associated proteins 1A/1B light chain 3A-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 117605176 tectonin beta-propeller repeat-containing protein isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 117602005 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 117607876 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 117604607 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 117604343 protein C19orf12 homolog K23168 MPAN; protein MPAN
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024