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  Mitochondrial Biogenesis - Python bivittatus (Burmese python)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D YP_008083599 NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D YP_008083600 NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D YP_008083606 NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D YP_008083608 NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D YP_008083607 NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D YP_008083609 NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D YP_008083610 NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D YP_008083611 cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D YP_008083601 cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D YP_008083602 cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D YP_008083605 cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D YP_008083604 ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 103054213 POLRMT; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 103061663 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 103066012 TFB1M; dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 103052100 TFB2M; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 103058469 MTIF2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 103065125 MTIF3; translation initiation factor IF-3, mitochondrial isoform X2 K02520 infC; translation initiation factor IF-3 D 103065379 TSFM; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 103053505 TUFM; elongation factor Tu, mitochondrial isoform X1 K02358 tuf; elongation factor Tu D 103057655 GFM2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G D 103059751 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 103054587 MTERF2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 103064761 MTERF4; transcription termination factor 4, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 103067848 MTERF3; transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 103055798 GUF1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 103065063 POP1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 103059328 POP4; ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 103058808 POP5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 103050789 RPP30; ribonuclease P protein subunit p30 isoform X1 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 103055212 RPP25L; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 103053934 RPP25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 103066119 RPP38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 103064000 RPP40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 103052754 TRMT10C; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 103051793 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 103058244 mitochondrial ribonuclease P catalytic subunit-like K17655 MRPP3; mitochondrial ribonuclease P protein 3 D 103058176 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 103062011 MSS51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 103064276 TEFM; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 103068000 PTCD1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 103062437 PTCD2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 103067878 PTCD3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 103054531 DHX30; putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 103065509 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 103051561 AFG1L; AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 103067642 ATP23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 103060369 SUPV3L1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 103058011 LACTB2; endoribonuclease LACTB2 isoform X2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 103067374 SLC25A4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 103061653 ADP/ATP translocase 4-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 103056684 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 103063191 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 103058219 SLC25A37; mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 103057092 SLC25A28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 107326558 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 103063762 ERAL1; GTPase Era, mitochondrial K03595 era; GTPase D 103058690 YARS2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 103060659 YARS; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 103068067 LARS2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 103067098 LARS; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 103061428 DARS2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 103062113 GARS; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 103066590 RARS; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 103052711 RARS2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 103064757 QRSL1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 103052059 GATB; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 103062824 GATC; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 103064114 MTPAP; poly(A) RNA polymerase, mitochondrial isoform X2 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 103061339 PDE12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 103060792 MTG1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 103056312 NOA1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 103055195 NSUN3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 103048761 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 103055119 RPUSD3; mitochondrial mRNA pseudouridine synthase RPUSD3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 103063588 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 103057009 RCC1L; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 103056559 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 isoform X1 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 103060759 FASTKD1; FAST kinase domain-containing protein 1, mitochondrial K27754 FASTKD1; FAST kinase domain-containing protein 1 D 103051828 FASTKD2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 103050586 FASTKD3; FAST kinase domain-containing protein 3, mitochondrial isoform X1 K27755 FASTKD3; FAST kinase domain-containing protein 3 D 103064701 TBRG4; FAST kinase domain-containing protein 4 K27756 TBRG4; FAST kinase domain-containing protein 4 D 103065902 FASTKD5; FAST kinase domain-containing protein 5, mitochondrial K27757 FASTKD5; FAST kinase domain-containing protein 5 D 103056487 CUNH12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial isoform X1 K23498 COXPD7; peptide chain release factor D 103067859 RMND1; required for meiotic nuclear division protein 1 homolog isoform X2 K23499 RMND1; required for meiotic nuclear division protein 1 D 103050749 GRSF1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1 D 103067413 METTL15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 103054066 CUNH12orf10; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 103064992 CUNH6orf203; uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 103062476 POLG; DNA polymerase subunit gamma-1 isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 103051819 POLG2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 D 103049953 PRIMPOL; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 103059989 ENDOG; LOW QUALITY PROTEIN: endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 103063730 MGME1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 103066994 EXOG; nuclease EXOG, mitochondrial isoform X1 K15050 EXOG; nuclease EXOG, mitochondrial D 103053121 TWNK; twinkle protein, mitochondrial isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3] D 103065091 PIF1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 103055480 SSBP1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 103061973 ATAD3A; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 103068094 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 103060541 uncharacterized protein C17orf80 homolog isoform X1 K27759 MTNAP1; mitochondrial nucleoid-associated protein 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 103065350 DNAJA2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 103055290 TOMM34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 103064754 RHOT1; mitochondrial Rho GTPase 1 isoform X2 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 103059585 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 103051671 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 103051650 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 103051884 heat shock 70 kDa protein II K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 103054024 AIP; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein D 112541400 uncharacterized protein LOC112541400 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 103064112 TOMM40L; mitochondrial import receptor subunit TOM40B isoform X2 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 103048438 TOMM40; mitochondrial import receptor subunit TOM40 homolog isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 103052357 TOMM70; LOW QUALITY PROTEIN: mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 103051687 TOMM22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 103058122 TOMM20L; TOMM20-like protein 1 K17770 TOM20; mitochondrial import receptor subunit TOM20 D 103068077 TOMM20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 103066697 TOMM7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 103049914 TOMM6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 103058582 TOMM5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 103063309 SAMM50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family C Porin D 103048389 VDAC1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 103049275 VDAC2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 103050712 VDAC3; voltage-dependent anion-selective channel protein 3 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 103058120 MTX3; metaxin-3 isoform X1 K17776 MTX; metaxin D 103054644 MTX2; metaxin-2 K17776 MTX; metaxin D 103049671 MTX1; metaxin-1 K17776 MTX; metaxin D 103051298 MYO19; unconventional myosin-XIX K25838 MYO19; myosin XIX D 103060551 LOW QUALITY PROTEIN: mitochondrial amidoxime reducing component 2-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] D 103060310 MARC2; mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 103055186 TIMM9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 103067214 TIMM10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 C TIM8/13 complex D 103050854 TIMM8B; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 103068017 TIMM8A; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 C Mitochondrial intermembrane space assembly (MIA) complex D 103057511 CHCHD4; mitochondrial intermembrane space import and assembly protein 40 isoform X2 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 103053400 GFER; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 103064322 MINOS1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 103058018 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 103052867 CUNH19orf70; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 103067102 CHCHD3; MICOS complex subunit MIC19 K17563 CHCHD3; MICOS complex subunit MIC19 D 103058313 CHCHD6; MICOS complex subunit MIC25 K17564 CHCHD6; MICOS complex subunit MIC25 D 103065257 APOO; MICOS complex subunit MIC26 K24625 APOO; MICOS complex subunit MIC26 D 103056641 APOOL; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 103064322 MINOS1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 103058018 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 103064370 TIMM22; mitochondrial import inner membrane translocase subunit Tim22 isoform X2 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 103060564 TIMM23; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 103062274 TIMM17B; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 103066836 TIMM17A; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 103052317 TIMM21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 103049732 TIMM50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 103059552 MCU; calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial D 103050705 calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial D 103068005 MICU2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 103055553 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 103056020 calcium uniporter regulatory subunit MCUb, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 103051413 SMDT1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 103058064 MCUR1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 103055850 mitochondrial proton/calcium exchanger protein-like K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 103067621 LETM2; LETM1 domain-containing protein LETM2, mitochondrial isoform X2 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 103059339 IMMP1L; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 112540454 IMMP2L; LOW QUALITY PROTEIN: mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 103059184 TMEM126A; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 103062423 MPC1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 103056010 MPC2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 103054698 coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial-like isoform X1 K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 103055476 TIMM44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 103053418 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 103057243 GRPEL2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 103060533 GRPEL1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 103062853 DNAJC19; mitochondrial import inner membrane translocase subunit TIM14 isoform X2 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 107326306 PAM16; mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 103049874 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 103054883 PMPCB; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 103051948 MIPEP; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 103059132 HSPD1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 103059365 HSPE1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 103056495 DNAJA3; dnaJ homolog subfamily A member 3, mitochondrial K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 103067711 TAMM41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 103056756 DNLZ; DNL-type zinc finger protein isoform X1 K17808 ZIM17; mitochondrial protein import protein ZIM17 D 103054622 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 103060336 POLDIP2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 103058702 CREB1; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 103057655 GFM2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G D 103059751 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 103052107 SP1; transcription factor Sp1 K04684 SP1; transcription factor Sp1 D 103057825 YY1; transcriptional repressor protein YY1 isoform X1 K09201 YY; transcription factor YY D 103062781 GABPB1; GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 103054529 GABPB2; GA-binding protein subunit beta-2 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 103061663 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 103067118 nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1 D 103062856 NFE2L2; nuclear factor erythroid 2-related factor 2 isoform X2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 C Coactivators D 103050560 PPARGC1A; peroxisome proliferator-activated receptor gamma coactivator 1-alpha K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 103049893 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 103057705 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 103067163 CRTC1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 103059972 EP300; histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 103064490 CREBBP; CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 103066871 NFS1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 103054013 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 103048025 LYRM4; LYR motif-containing protein 4 isoform X3 K22069 LYRM4; LYR motif-containing protein 4 D 103050170 FXN; frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1] D 103056000 FDX1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 103065333 FDX2; ferredoxin-2, mitochondrial isoform X2 K22071 FDX2; ferredoxin-2, mitochondrial D 103068267 adrenodoxin, mitochondrial-like K22071 FDX2; ferredoxin-2, mitochondrial D 103051603 FDXR; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 103053418 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 103050867 SIL1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1 D 103049713 GLRX5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 103065894 ISCA1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 103057621 ISCA2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 103056127 IBA57; putative transferase CAF17, mitochondrial isoform X1 K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 103058711 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 103052216 BOLA3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 103052270 SFXN3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 103065822 SFXN1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 103062598 SFXN2; sideroflexin-2 isoform X2 K23501 SFXN2; sideroflexin-2 D 103064524 SFXN4; sideroflexin-4 K23502 SFXN4; sideroflexin-4 D 103057596 SFXN5; sideroflexin-5 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 103057982 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 103062048 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 103049945 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform isoform X1 K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21] D 103051773 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 103066009 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 103066182 FBXL4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 103067504 HCFC1; host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1 D 103059522 HCFC2; host cell factor 2 K27390 HCFC2; host cell factor 2 D 103059334 HTT; huntingtin K04533 HD; huntingtin D 103065659 ESRRA; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha D 103048909 ESRRB; steroid hormone receptor ERR2 isoform X3 K08553 NR3B2; estrogen-related receptor beta D 103067887 ESRRG; estrogen-related receptor gamma isoform X2 K08554 NR3B3; estrogen-related receptor gamma D 103062928 NRIP1; nuclear receptor-interacting protein 1 isoform X2 K17965 NRIP1; nuclear receptor-interacting protein 1 D 103064935 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 103057294 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 103066216 LONP1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 103054603 SIRT1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 103052548 SERAC1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 103050543 UXT; protein UXT isoform X2 K26537 UXT; protein UXT D 103057223 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 103049349 NDUFAF1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 103051613 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 103060224 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 103050948 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 103053118 NDUFAF5; arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 103055040 NDUFAF6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X2 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 103066000 NDUFAF7; protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 112540488 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 103061494 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 103066766 ACAD9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 103064849 NUBPL; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning D 103065443 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 103064344 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 103059495 TIMMDC1; complex I assembly factor TIMMDC1, mitochondrial isoform X1 K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 103055249 SDHAF2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 103059046 mitochondrial chaperone BCS1 isoform X1 K08900 BCS1; mitochondrial chaperone BCS1 D 103050480 TTC19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 103059521 LYRM7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 103065509 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 103068094 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 103057669 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 103057934 CUNH12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 103054810 STMP1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 103049434 CMC1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 103055352 CMC2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 103049715 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1 D 103058615 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 103059659 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 103065231 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 103051655 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 103051861 protoheme IX farnesyltransferase, mitochondrial isoform X1 K02257 COX10; heme o synthase [EC:2.5.1.141] D 103048849 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 103049170 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14 D 103054482 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 103056079 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 103061780 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 103053913 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18 D 103061241 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 103048928 cytochrome c oxidase assembly protein COX20, mitochondrial isoform X1 K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 103062011 MSS51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 103051796 PET100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 103055756 PET117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 103063363 OXA1L; mitochondrial inner membrane protein OXA1L isoform X1 K03217 yidC; YidC/Oxa1 family membrane protein insertase D 103061075 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 103062681 protein SCO1 homolog, mitochondrial isoform X2 K07152 SCO1; protein SCO1 D 103052652 protein SCO2 homolog, mitochondrial-like K23755 SCO2; protein SCO2 D 103060671 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 103051090 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 107326031 APOPT1; apoptogenic protein 1, mitochondrial K23506 APOPT1; apoptogenic protein 1 D 103054810 STMP1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 103057669 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 103064965 TMEM223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 103051904 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 103065547 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 103064873 TMEM70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 103068058 transmembrane protein 70, mitochondrial-like K17966 TMEM70; transmembrane protein 70, mitochondrial D 103048134 ATP5MD; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 103049224 MFN1; mitofusin-1 isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 103066015 MFN2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 103064614 OPA1; dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 103049164 OPA3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein D 103063059 TRIAP1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 103052191 PARL; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 103053500 BAK1; bcl-2 homologous antagonist/killer K14021 BAK; Bcl-2 homologous antagonist/killer D 103067636 apoptosis regulator BAX-like isoform X2 K02159 BAX; apoptosis regulator BAX D 103058396 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX D 103052507 dynamin-1-like protein isoform X2 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 103058290 DNM1L; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 103051196 FIS1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 103053873 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 103060254 SUMO2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 103061565 SUMO1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 103064674 SH3GLB1; endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1 D 103050688 MTCH1; mitochondrial carrier homolog 1 isoform X2 K17885 MTCH; mitochondrial carrier D 103053787 MTCH2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 103053734 MFF; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor D 103064653 FATE1; fetal and adult testis-expressed transcript protein isoform X1 K22076 MFF; mitochondrial fission factor D 103053618 GDAP1; ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 103056586 GDAP1L1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 103057025 VAT1; synaptic vesicle membrane protein VAT-1 homolog isoform X1 K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 103055494 MIEF1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 103061338 MIEF2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 103055400 PLD6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 103050618 MIGA1; mitoguardin 1 K27289 MIGA; mitoguardin D 103060186 MIGA2; mitoguardin 2 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 103063147 ACTG1; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 103050159 ACTL8; actin-like protein 8 K05692 ACTB_G1; actin beta/gamma 1 D 103060469 N-alpha-acetyltransferase 20 isoform X2 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 103051114 NAA25; N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 103054418 PHB; prohibitin K17080 PHB1; prohibitin 1 D 103065688 PHB2; prohibitin-2 K17081 PHB2; prohibitin 2 D 103056536 KTN1; kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 103052507 dynamin-1-like protein isoform X2 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 103058290 DNM1L; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 103053038 MYO5A; unconventional myosin-Va isoform X2 K10357 MYO5; myosin V D 103053748 MYO5C; unconventional myosin-Vc isoform X2 K10357 MYO5; myosin V D 103049653 MYO5B; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V D 103053668 XIAP; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 103059888 DIABLO; diablo homolog, mitochondrial K10522 DIABLO; diablo C Morphogenesis factors D 103066740 SNX25; sorting nexin-25 isoform X3 K17887 SNX25; sorting nexin-25 D 103064754 RHOT1; mitochondrial Rho GTPase 1 isoform X2 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 103058018 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 103053721 MTFP1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 103059683 DAP3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 103055395 OXR1; oxidation resistance protein 1 isoform X1 K25437 OXR1; oxidation resistance protein 1 D 103061133 MSTO1; protein misato homolog 1 K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 103059711 autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 103052314 ATG2B; autophagy-related protein 2 homolog B isoform X2 K17906 ATG2; autophagy-related protein 2 D 103063297 ATG2A; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 103062867 ATG3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 103053271 ATG4C; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 103059663 ATG4D; cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 103056317 ATG4A; cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 103062489 cysteine protease ATG4B-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 103063575 ATG5; autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 103048087 BECN1; beclin-1 K08334 BECN; beclin D 103054015 ATG7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 103057849 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 103061483 GABARAPL2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 103051384 ATG9A; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 103054704 autophagy-related protein 9A-like K17907 ATG9; autophagy-related protein 9 D 103053383 ATG10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 103056278 ATG12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12 D 103056236 ATG14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 103048124 ATG16L1; autophagy-related protein 16-1 K17890 ATG16L1; autophagy-related protein 16-1 D 103057870 WIPI1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 103065993 WIPI2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 D 103052643 LOW QUALITY PROTEIN: vacuolar protein 8-like K08332 VAC8; vacuolar protein 8 C Parkin-dependent mechanism factors D 103051791 E3 ubiquitin-protein ligase parkin-like K04556 PARK2; parkin [EC:2.3.2.31] D 103063491 RNF41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 103066773 CLEC16A; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 103059482 PINK1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 103052191 PARL; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 103067573 SQSTM1; sequestosome-1 K14381 SQSTM1; sequestosome 1 D 103058727 TAX1BP1; tax1-binding protein 1 isoform X1 K21347 TAX1BP1; Tax1-binding protein 1 D 103061031 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 103063553 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 isoform X2 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 103064179 ATG13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13 D 103056702 ULK1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 103061964 ULK2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 103061220 RB1CC1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 103062969 HSP90AA1; heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG D 103060535 HSP90AB1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 103050472 CDC37; hsp90 co-chaperone Cdc37 isoform X1 K09554 CDC37; cell division cycle protein 37 D 103052692 SMURF2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 103049498 SMURF1; E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 103049324 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X3 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 103053395 FUNDC1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 103064935 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 103057294 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 103047970 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 103062914 MAP1LC3B; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 103049191 MAP1LC3C; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 103063212 MAP1LC3A; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 103067963 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 103055597 NBR1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 103064434 TECPR1; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 103053211 ZFYVE1; zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 103048219 COASY; bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 103058056 CUNH19orf12; protein C19orf12 homolog isoform X4 K23168 MPAN; protein MPAN D 103055925 FUNDC2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: August 9, 2024