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  Mitochondrial Biogenesis - Pterocles gutturalis (yellow-throated sandgrouse)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I C Mitochondrial respiratory chain complex III C Cytochrome c oxidase C F-type ATPase B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 104470495 POLRMT; LOW QUALITY PROTEIN: DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 104457740 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 104461031 TFB1M; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 104458020 MTIF2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 104460133 MTIF3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3 D 104471155 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 104471454 GFM2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 104458763 MTERF3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 104460595 MTERF2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 104458248 GUF1; translation factor GUF1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 104469511 POP1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 104459351 POP4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 104459241 RPP30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 104464957 RPP25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 104466409 RPP25L; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 104469701 RPP38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 104464367 RPP40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 104460440 TRMT10C; mitochondrial ribonuclease P protein 1 K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 104460485 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 104464861 mitochondrial ribonuclease P protein 3-like K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 104458552 PTCD1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 104469042 PTCD2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 104458341 PTCD3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 104469053 DHX30; LOW QUALITY PROTEIN: putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 104472322 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 104469465 LACE1; lactation elevated protein 1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 104467601 SUPV3L1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 104459253 LACTB2; beta-lactamase-like protein 2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 104463451 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 104470004 ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 104460762 mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 104461510 LOW QUALITY PROTEIN: mitoferrin-1-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 104468036 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 104458801 ERAL1; GTPase Era, mitochondrial K03595 era; GTPase D 104471623 YARS; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 104460986 LARS2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 104470003 LARS; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 104462425 DARS2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 104458287 GARS; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 104458086 RARS2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 104469461 RARS; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 104468278 QRSL1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 104468157 GATB; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 104457871 GATC; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 104465543 MTPAP; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 104458527 PDE12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 104463932 MTG1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 104470157 NOA1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 104458259 NSUN3; putative methyltransferase NSUN3 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 104465689 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 104463017 RPUSD4; RNA pseudouridylate synthase domain-containing protein 4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 104462694 WBSCR16; Williams-Beuren syndrome chromosomal region 16 protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 104459902 TRUB2; probable tRNA pseudouridine synthase 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 104462065 FASTKD1; FAST kinase domain-containing protein 1 K27754 FASTKD1; FAST kinase domain-containing protein 1 D 104467857 FAST kinase domain-containing protein 2-like K18190 FASTKD2; FAST kinase domain-containing protein 2 D 104459533 FASTKD3; FAST kinase domain-containing protein 3 K27755 FASTKD3; FAST kinase domain-containing protein 3 D 104467655 TBRG4; LOW QUALITY PROTEIN: protein TBRG4 K27756 TBRG4; FAST kinase domain-containing protein 4 D 104460273 FASTKD5; FAST kinase domain-containing protein 5 K27757 FASTKD5; FAST kinase domain-containing protein 5 D 104465718 probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor D 104460967 RMND1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 104469293 GRSF1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1 D 104467408 METTL15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 104471494 uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 104469070 LOW QUALITY PROTEIN: DNA polymerase subunit gamma-1-like K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 104458025 POLG2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 D 104468680 PRIMPOL; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 104467166 ENDOG; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 104458090 MGME1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 104460667 LOW QUALITY PROTEIN: twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3] D 104466752 PIF1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 104465357 SSBP1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 104472444 ATAD3A; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 104467563 LOW QUALITY PROTEIN: ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 104465928 DNAJA2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 104465766 TOMM34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 104471976 RHOT1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 104470036 HSPA8; heat shock cognate 71 kDa protein isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 104467954 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein D 104467092 FATE1; fetal and adult testis-expressed transcript protein K28235 FATE1; fetal and adult testis-expressed transcript protein B Outer membrane C Transporter outer membrane (TOM) complex D 104459988 TOMM20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 104458520 TOMM70A; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 C TOB/SAM complex D 104458562 SAMM50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family C Porin D 104469646 VDAC1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 104459891 VDAC2; voltage-dependent anion-selective channel protein 2 isoform X1 K15040 VDAC2; voltage-dependent anion channel protein 2 D 104460026 VDAC3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 104462129 MTX2; metaxin-2 K17776 MTX; metaxin D 104465694 MTX3; metaxin-3 K17776 MTX; metaxin D 104458066 MYO19; unconventional myosin-XIX K25838 MYO19; myosin XIX D 104463847 mitochondrial amidoxime reducing component 2-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 104460418 TIMM9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 C TIM8/13 complex C Mitochondrial intermembrane space assembly (MIA) complex D 104471868 CHCHD4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 104470136 GFER; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 104460304 MINOS1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 104458849 IMMT; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 D 104459062 protein QIL1 K24624 MICOS13; MICOS complex subunit MIC13 D 104468313 CHCHD6; MICOS complex subunit MIC25 K17564 CHCHD6; MICOS complex subunit MIC25 D 104462722 APOO; apolipoprotein O K24625 APOO; MICOS complex subunit MIC26 C MICOS complex (yeast) D 104460304 MINOS1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 104458849 IMMT; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex C TIM23 complex D 104465795 TIMM23; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 104471729 TIMM17A; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 104457603 TIMM21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 C Mitochondrial calcium uniporter complex D 104470097 MCU; LOW QUALITY PROTEIN: calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 104465853 MICU1; calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial D 104460998 MICU2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 104469642 CCDC109B; mitochondrial calcium uniporter regulatory subunit MCUb K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 104460910 SMDT1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 104470018 MCUR1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 104464528 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 104464252 IMMP1L; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 104458645 TMEM126A; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 104460123 MPC1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 104466859 MPC2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 104468140 OCIAD1; OCIA domain-containing protein 1 K28215 OCIAD1; OCIA domain-containing protein 1 B Matrix C MMC/PAM proteins D 104457575 TIMM44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 104459684 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 104459565 GRPEL2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 104460111 GRPEL1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 104462757 DNAJC19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 104461060 PAM16; mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 104458566 PMPCA; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 104458723 PMPCB; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 104458679 HSPD1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 104460517 HSPE1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 104458746 DNAJA3; dnaJ homolog subfamily A member 3, mitochondrial K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 104465295 TAMM41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 104466289 DNLZ; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 104464793 POLDIP2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 104469777 CREB1; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 104471155 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 104471454 GFM2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 104465949 LOW QUALITY PROTEIN: transcription factor Sp1-like K04684 SP1; transcription factor Sp1 D 104458002 GABPB2; GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta D 104468476 GA-binding protein subunit beta-1 K09454 GABPB; GA-binding protein transcription factor, beta D 104457740 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 104466123 NRF1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1 D 104467713 NFE2L2; nuclear factor erythroid 2-related factor 2 isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 C Coactivators D 104464933 PPARGC1A; peroxisome proliferator-activated receptor gamma coactivator 1-alpha K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 104459209 CRTC1; CREB-regulated transcription coactivator 1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 104458372 CREBBP; CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 104470743 EP300; histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 104465910 NFS1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 104458423 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 104460584 LYRM4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 104458733 FXN; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 104460096 adrenodoxin-like K22071 FDX2; ferredoxin-2, mitochondrial D 104466846 FDXR; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 104459684 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 104465986 HSCB; iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB D 104471394 SIL1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1 D 104460945 GLRX5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 104470507 ISCA1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 104463924 ISCA2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 104460237 IBA57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 104471413 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 104458689 SFXN1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 104462608 sideroflexin-1-like K23500 SFXN1_3; sideroflexin-1/3 D 104461761 sideroflexin-5 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 104469317 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 104458330 DHTKD1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 104465440 FBXL4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 104459592 HCFC2; host cell factor 2 K27390 HCFC2; host cell factor 2 D 104464991 HTT; huntingtin K04533 HD; huntingtin D 104462325 ESRRB; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 104467035 ESRRG; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 104464193 NRIP1; LOW QUALITY PROTEIN: nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 104459056 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 104465814 PRKAA2; LOW QUALITY PROTEIN: 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 104466131 LONP1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 104468886 SIRT1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 104464113 SERAC1; protein SERAC1 K23504 SERAC1; protein SERAC1 D 104464845 ES1 protein homolog, mitochondrial-like K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 104470785 ES1 protein homolog, mitochondrial-like K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 104462865 TANGO2; transport and Golgi organization protein 2 homolog K28098 TANGO2; transport and Golgi organization protein 2 D 104470381 UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69 D 104467093 FAM214B; protein FAM214B K28528 ATOS; protein Atossa D 104469628 FAM214A; protein FAM214A K28528 ATOS; protein Atossa D 104462005 DDX47; probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7] B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 104460895 NDUFAF1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 104459627 NDUFAF2; mimitin, mitochondrial K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 104459711 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 104467535 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 104458162 NDUFAF6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 104458093 NDUFAF7; NADH dehydrogenase [ubiquinone] complex I, assembly factor 7 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 104467515 ACAD9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 104470463 NUBPL; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 104463535 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 104463003 TIMMDC1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors C Complex-III assembly factors D 104470543 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 104459430 TTC19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 104459637 LYRM7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 104472322 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 104467563 LOW QUALITY PROTEIN: ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 104457470 uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 104468672 uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 104457418 CMC2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 104470698 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1 D 104464334 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 104470222 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 104471837 protoheme IX farnesyltransferase, mitochondrial-like K02257 COX10; heme o synthase [EC:2.5.1.141] D 104459617 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 104458861 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9] D 104468531 mitochondrial inner membrane protein COX18-like K17797 COX18; mitochondrial inner membrane protein COX18 D 104459652 cytochrome c oxidase protein 20 homolog K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 104467800 PET117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 104458465 SURF1; surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 104461168 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 104463857 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 104466402 APOPT1; LOW QUALITY PROTEIN: apoptogenic protein 1, mitochondrial K23506 APOPT1; apoptogenic protein 1 D 104468672 uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1 D 104458239 HIG1 domain family member 1A, mitochondrial-like K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial C Complex-V assembly factors D 104471136 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 104461182 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 104467917 TMEM70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 104464673 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid D 104457461 USMG5; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 104458345 MFN1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 104461842 MFN2; mitofusin-2 isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 104469412 OPA1; dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 104459699 PARL; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 104463478 LOW QUALITY PROTEIN: bcl-2 homologous antagonist/killer-like K14021 BAK; Bcl-2 homologous antagonist/killer D 104464309 DNM1L; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 104460257 SUMO2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 104463453 SUMO1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 104463384 SH3GLB1; endophilin-B1 K11248 SH3GLB1; endophilin-B1 D 104459251 MTCH1; mitochondrial carrier homolog 1 K17885 MTCH; mitochondrial carrier D 104463995 MFF; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor D 104459690 ganglioside-induced differentiation-associated protein 1-like K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 104464559 ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 104469018 VAT1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 104463208 MIEF2; LOW QUALITY PROTEIN: mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 104465363 MIEF1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 104462461 PLD6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 104463404 FAM73B; protein FAM73B K27289 MIGA; mitoguardin D 104471910 FAM73A; protein FAM73A K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 104459850 actin, cytoplasmic 2-like K05692 ACTB_G1; actin beta/gamma 1 D 104460713 actin, cytoplasmic type 5 isoform X1 K05692 ACTB_G1; actin beta/gamma 1 D 104469616 LOW QUALITY PROTEIN: actin, cytoplasmic 1-like K05692 ACTB_G1; actin beta/gamma 1 D 104458186 NAA25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 104459847 PHB; prohibitin K17080 PHB1; prohibitin 1 D 104459885 PHB2; prohibitin-2 K17081 PHB2; prohibitin 2 D 104469202 KTN1; LOW QUALITY PROTEIN: kinectin K17975 KTN1; kinectin C Retention of mitochondria D 104464309 DNM1L; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 104462745 MYO5C; unconventional myosin-Vc K10357 MYO5; myosin V D 104463431 LOW QUALITY PROTEIN: unconventional myosin-Va-like K10357 MYO5; myosin V D 104468931 XIAP; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 104465750 DIABLO; LOW QUALITY PROTEIN: diablo homolog, mitochondrial K10522 DIABLO; diablo C Morphogenesis factors D 104469284 SNX25; sorting nexin-25 K17887 SNX25; sorting nexin-25 D 104471976 RHOT1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 104458849 IMMT; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 D 104458611 DAP3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 104471532 LOW QUALITY PROTEIN: E3 ubiquitin-protein ligase NEDD4-like K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 104466421 oxidation resistance protein 1-like K25437 OXR1; oxidation resistance protein 1 D 104470464 oxidation resistance protein 1-like K25437 OXR1; oxidation resistance protein 1 D 104457829 MSTO1; protein misato homolog 1 K27320 MSTO1; protein misato D 104459994 PRELID1; PRELI domain-containing protein 1, mitochondrial K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial D 104463609 PRELID2; PRELI domain-containing protein 2 K27965 PRELID2; PRELI domain-containing protein 2 mitochondrial D 104457760 protein slowmo homolog 1-like K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial D 104472373 SLMO2; LOW QUALITY PROTEIN: protein slowmo homolog 2 K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial B Mitophagy factors C Autophagy-related proteins D 104463695 LOW QUALITY PROTEIN: autophagy-related protein 2 homolog B-like K17906 ATG2; autophagy-related protein 2 D 104464507 ATG3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 104458740 ATG4B; cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 104467937 ATG4A; cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 104470030 ATG4C; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 104468250 ATG5; autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 104459494 BECN1; beclin-1 K08334 BECN; beclin D 104457825 ATG7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 104465292 GABARAPL2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 104471860 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 104461487 ATG9A; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 104465906 ATG14; LOW QUALITY PROTEIN: beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 104458392 ATG16L1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 104458822 WIPI2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 D 104461496 WIPI1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18 D 104465113 LOW QUALITY PROTEIN: vacuolar protein 8-like K08332 VAC8; vacuolar protein 8 C Parkin-dependent mechanism factors D 104461264 RNF41; LOW QUALITY PROTEIN: E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 104458203 CLEC16A; protein CLEC16A K19513 CLEC16A; protein CLEC16A D 104458928 PINK1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 104459699 PARL; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 104462667 SQSTM1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1 D 104457880 tax1-binding protein 1 homolog K21347 TAX1BP1; Tax1-binding protein 1 D 104460894 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 104467176 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 104465304 ATG13; autophagy-related protein 13 K08331 ATG13; autophagy-related protein 13 D 104467444 LOW QUALITY PROTEIN: serine/threonine-protein kinase ULK1-like K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 104462215 ULK2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 104471756 RB1CC1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 104459046 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG D 104460864 HSP90AB1; LOW QUALITY PROTEIN: heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 104458592 SMURF2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 104461629 SMURF1; E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 104467306 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 104460320 FUNDC1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 104459056 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 104465814 PRKAA2; LOW QUALITY PROTEIN: 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 104464148 MAP1LC3B; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 104467262 MAP1LC3C; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 104468405 MAP1LC3A; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 104471574 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain D 104461133 NBR1; next to BRCA1 gene 1 protein K17987 NBR1; next to BRCA1 gene 1 protein D 104470043 TECPR1; LOW QUALITY PROTEIN: tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 104470959 ZFYVE1; zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 104461622 PLA2G6; 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 104457432 protein C19orf12 homolog K23168 MPAN; protein MPAN D 104463469 protein C19orf12 homolog K23168 MPAN; protein MPAN D 104466548 FUN14 domain-containing protein 2-like K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025