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Mitochondrial Biogenesis - Pectinophora gossypiella (pink bollworm)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 73956692 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 73956675 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 73956682 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 73956689 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 73956667 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 73956688 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 73956691 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 73956669 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 73956678 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 73956679 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 73956663 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 73956681 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 73956662 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 126373944 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 126373872 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 126372786 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 126374945 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 126374859 translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 126366334 translation initiation factor IF-3, mitochondrial-like K02520 infC; translation initiation factor IF-3
D 126381932 elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts
D 126377362 elongation factor Tu-like K02358 tuf; elongation factor Tu
D 126367800 elongation factor Tu K02358 tuf; elongation factor Tu
D 126370200 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 126375251 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 126381827 transcription termination factor 5, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 126381861 transcription termination factor 5, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 126382377 transcription termination factor, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 126366448 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 126368882 translation factor GUF1 homolog, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 126372297 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 126375940 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 126367865 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 126369431 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 126371846 ribonuclease P protein subunit p20-like isoform X1 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 126367885 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 126371297 uncharacterized protein LOC126371297 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 126376405 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 126379862 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 126380374 3-hydroxyacyl-CoA dehydrogenase type-2-like K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 126373023 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 126372515 uncharacterized protein LOC126372515 isoform X1 K17658 TEFM; transcription elongation factor, mitochondrial
D 126372854 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 126374389 pentatricopeptide repeat-containing protein 2, mitochondrial-like K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 126366390 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 126377327 ATP-dependent RNA helicase DHX30-like isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 126369707 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 126366740 putative ATPase N2B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 126367840 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 126366358 ATP-dependent RNA helicase SUV3 homolog, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 126370839 beta-lactamase-like protein 2 homolog K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 126378959 ADP,ATP carrier protein K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 126380201 ADP,ATP carrier protein 1-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 126375783 ADP,ATP carrier protein 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 126376922 mitoferrin K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 126373572 uncharacterized protein LOC126373572 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 126367172 GTPase Era, mitochondrial K03595 era; GTPase
D 126368922 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 126370966 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 126377573 leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 126382339 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 126380171 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 126373963 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 126366245 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 126377083 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 126374621 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 126368997 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 126373302 poly(A) RNA polymerase, mitochondrial-like K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 126369041 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 126375298 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 126382210 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 126373811 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 126378449 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 126370976 uncharacterized protein LOC126370976 K23496 NGRN; neugrin
D 126382236 pseudouridylate synthase TRUB2, mitochondrial K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 126367244 mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 126376269 required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 126374899 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 126380357 MYG1 exonuclease K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 126370309 mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 126375638 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
C Mitochondrial DNA maintenance factors
D 126376670 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 126373333 uncharacterized protein LOC126373333 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 126382027 mitochondrial DNA helicase K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 126373561 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 126366093 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 126379800 ATPase family AAA domain-containing protein 3A homolog K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 126382347 dnaJ homolog subfamily A member 2-like K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 126367902 mitochondrial Rho GTPase K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 126377727 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126377845 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126369380 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126379432 heat shock protein 70 B2-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126370368 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126372121 heat shock protein 68-like isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126375871 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126367034 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 126371840 AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 126377896 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 126375591 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 126368133 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 126371844 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 126378205 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
C TOB/SAM complex
D 126379211 sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 126373672 voltage-dependent anion-selective channel-like isoform X1 K15040 VDAC2; voltage-dependent anion channel protein 2
C ERMES complex
C Other outer membrane factor
D 126378497 metaxin-2 isoform X1 K17776 MTX; metaxin
D 126370709 metaxin-1 isoform X1 K17776 MTX; metaxin
D 126374798 mitochondrial amidoxime-reducing component 1 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 126373241 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 126378221 mitochondrial import inner membrane translocase subunit Tim10 isoform X1 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
C TIM8/13 complex
D 126366143 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 126381756 mitochondrial import inner membrane translocase subunit Tim13-like K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 126374889 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 126372818 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 126379737 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 126367404 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 126377030 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 126369449 MICOS complex subunit MIC13 homolog QIL1-like isoform X1 K24624 MICOS13; MICOS complex subunit MIC13
D 126382149 uncharacterized protein LOC126382149 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 126379737 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 126367404 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 126377030 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 126375941 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 126376706 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 126370316 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 126369856 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 126371040 mitochondrial import inner membrane translocase subunit TIM50-C-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 126367061 calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial
D 126366834 calcium uptake protein 1 homolog, mitochondrial-like isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 126371850 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
C Other inner membrane factors
D 126371455 mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 126382418 mitochondrial inner membrane protease subunit 1 isoform X1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 126376318 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 126368229 uncharacterized protein LOC126368229 K18157 TMEM126A; transmembrane protein 126A
D 126370327 mitochondrial pyruvate carrier 1 isoform X1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 126380393 mitochondrial pyruvate carrier 2-like isoform X1 K22139 MPC2; mitochondrial pyruvate carrier 2
D 126374894 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
D 126372257 coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial-like K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
D 126372258 coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial-like K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 126373326 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 126378850 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 126378977 grpE protein homolog, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE
D 126381921 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 126380396 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 126381764 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 126380107 cytochrome b-c1 complex subunit 1, mitochondrial-like K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 126372179 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 126378193 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 126373802 heat shock protein 60A-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 126375071 63 kDa chaperonin, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 126372894 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 126375671 protein tumorous imaginal discs, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 126381897 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 126371352 DNL-type zinc finger protein-like K17808 ZIM17; mitochondrial protein import protein ZIM17
D 126373358 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 126367579 uncharacterized protein LOC126367579 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 126376158 polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 126367692 cyclic AMP response element-binding protein B isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 126370200 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 126375251 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 126379226 transcriptional repressor protein YY1-like K09201 YY; transcription factor YY
D 126369396 poly [ADP-ribose] polymerase tankyrase-2 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 126373872 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 126378336 DNA-binding protein Ewg isoform X1 K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 126374364 CREB-regulated transcription coactivator 3-like isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 126366183 histone acetyltransferase p300-like isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 126368994 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 126371548 iron-sulfur cluster assembly scaffold protein IscU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 126378560 LYR motif-containing protein 4-like K22069 LYRM4; LYR motif-containing protein 4
D 126378561 LYR motif-containing protein 4-like K22069 LYRM4; LYR motif-containing protein 4
D 126369721 frataxin homolog, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1]
D 126379004 adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial
D 126378204 adrenodoxin-like protein 1, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 126375110 NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 126378850 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 126376312 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 126373230 uncharacterized monothiol glutaredoxin ycf64-like K07390 grxD; monothiol glutaredoxin
D 126366866 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 126373596 uncharacterized protein LOC126373596 K22072 ISCA2; iron-sulfur cluster assembly 2
D 126374090 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 126369728 bolA-like protein DDB_G0274169 K22066 BOLA1; BolA-like protein 1
D 126373238 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 126377155 sideroflexin-1-3-like isoform X1 K23500 SFXN1_3; sideroflexin-1/3
D 126377159 sideroflexin-1-3-like K23500 SFXN1_3; sideroflexin-1/3
D 126371506 sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2
C Other regulator of mitochondrial biogenesis
D 126380507 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 126370209 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 126371899 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 126375461 host cell factor 1 K14966 HCFC1; host cell factor 1
D 126376153 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 126370846 lon protease homolog, mitochondrial isoform X1 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 126380774 protein SERAC1-like K23504 SERAC1; protein SERAC1
D 126375142 protein UXT homolog K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 126368985 uncharacterized protein LOC126368985 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 126374803 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 126379063 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 126379271 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 126376697 protein NDUFAF4 homolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 126379242 arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 126369693 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 126375423 protein arginine methyltransferase NDUFAF7 homolog, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 126378224 uncharacterized protein LOC126378224 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 126368726 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 126380691 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 126382327 FAD-dependent oxidoreductase domain-containing protein 1-like K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 126376573 reticulon-4-interacting protein 1, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 126372704 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 126366843 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 126366347 succinate dehydrogenase assembly factor 2-B, mitochondrial-like K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 126381832 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 126374405 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 126369731 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 126369707 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 126368758 uncharacterized protein LOC126368758 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 126367611 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 126367612 protein brawnin K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
C Complex-IV assembly factors
D 126370891 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 126373598 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 126372829 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 126379029 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 126371375 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 126367343 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 126372808 cytochrome c oxidase assembly protein COX11, mitochondrial isoform X1 K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 126371277 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 126370933 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 126371811 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 126371820 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 126368099 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 126369594 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 126370974 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 126380049 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 126368087 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 126378085 leucine-rich PPR motif-containing protein, mitochondrial-like K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 126368365 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 126367611 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 126372555 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 126370410 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 126368779 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 126368979 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 126381073 uncharacterized protein LOC126381073 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 126367312 transmembrane GTPase Marf K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 126378050 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 126374951 optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 126372083 TP53-regulated inhibitor of apoptosis 1-like K17968 TRIAP1; TRIAP1/MDM35 family protein
D 126381839 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 126366038 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 126369174 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 126371559 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 126372796 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier
D 126382284 transport and Golgi organization protein 11 K22076 MFF; mitochondrial fission factor
D 126372633 ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 126380947 uncharacterized protein LOC126380947 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 126372802 mitochondrial cardiolipin hydrolase-like K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 126372806 mitochondrial cardiolipin hydrolase-like K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 126377001 mitoguardin isoform X1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 126368943 actin-5C K05692 ACTB_G1; actin beta/gamma 1
D 126368944 actin, cytoplasmic A3a K05692 ACTB_G1; actin beta/gamma 1
D 126373024 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 126375988 phagocyte signaling-impaired protein K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 126366518 protein l(2)37Cc K17080 PHB1; prohibitin 1
D 126373346 prohibitin-2 K17081 PHB2; prohibitin 2
D 126375427 prohibitin-2-like K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 126366038 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 126378328 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
C Morphogenesis factors
D 126366205 sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 126367902 mitochondrial Rho GTPase K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 126377030 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 126376323 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 126379176 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 126374700 E3 ubiquitin-protein ligase Nedd-4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 126367043 protein misato K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 126375148 autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 126368516 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 126368844 cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 126375026 cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 126381929 autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 126378124 beclin-1-like protein K08334 BECN; beclin
D 126370954 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 126372712 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 126380773 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 126368234 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 126369283 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12
D 126370058 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 126369244 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 126366640 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 126368650 protein CLEC16A homolog isoform X1 K19513 CLEC16A; protein CLEC16A
D 126381839 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
C Parkin-independent mechanism factors
D 126377366 autophagy-related protein 13 homolog K08331 ATG13; autophagy-related protein 13
D 126380784 autophagy-related protein 13 homolog K08331 ATG13; autophagy-related protein 13
D 126371863 serine/threonine-protein kinase ULK1 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 126370812 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 126377726 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG
D 126379877 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 126368793 E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 126377865 FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 126376153 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 126379886 uncharacterized protein LOC126379886 K10435 MAP1LC; microtubule-associated protein 1 light chain
D 126367701 tectonin beta-propeller repeat-containing protein isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 126371835 bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 126372446 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024