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  Mitochondrial Biogenesis - Pseudopodoces humilis (Tibetan ground-tit)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 9481005 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 9480993 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 9480999 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 9481001 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 9481000 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 9481002 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 9481004 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 9481003 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 9480994 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 9480995 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 9480998 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 9480996 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 9480997 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 102099359 POLRMT; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 102100514 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 102111132 TFB1M; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 102107494 TFB2M; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 102105068 MTIF2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 102106964 MTIF3; translation initiation factor IF-3, mitochondrial isoform X1 K02520 infC; translation initiation factor IF-3 D 102103035 TSFM; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 102109826 GFM2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 102106378 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 102114611 MTERF2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 102110874 MTERF3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 102112260 MTERF4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 102103113 GUF1; translation factor GUF1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 102109281 POP1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 102113383 POP4; ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 102111269 POP5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 102103788 RPP30; ribonuclease P protein subunit p30 isoform X1 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 102100829 POP7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 102112056 RPP25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 102109983 RPP25L; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 102110066 RPP38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 102110399 RPP40; ribonuclease P protein subunit p40 isoform X2 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 102102501 TRMT10C; mitochondrial ribonuclease P protein 1 K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 102108549 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 102102366 KIAA0391; mitochondrial ribonuclease P protein 3 K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 102112807 MSS51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 102108576 PTCD1; pentatricopeptide repeat-containing protein 1, mitochondrial isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 102109469 PTCD2; LOW QUALITY PROTEIN: pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 102113662 PTCD3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 102113340 DHX30; putative ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 102099365 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 102111808 LACE1; lactation elevated protein 1 isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 102108982 XRCC6BP1; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 102099108 SUPV3L1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 102111500 LACTB2; beta-lactamase-like protein 2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 102105225 SLC25A4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 102112843 SLC25A6; ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 102110337 SLC25A5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 102102038 SLC25A37; mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 102111330 SLC25A28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 102111866 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 106628322 ERAL1; GTPase Era, mitochondrial K03595 era; GTPase D 102100686 YARS; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 102109789 YARS2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 102106050 LARS; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 102108435 LARS2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 102109314 DARS2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 102109974 GARS; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 102109474 RARS; arginine--tRNA ligase, cytoplasmic isoform X2 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 102103591 RARS2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 102113420 QRSL1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 102102548 GATB; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 102109963 GATC; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 102103118 MTPAP; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 102101089 PDE12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 102109985 MTG1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 102111294 NOA1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 102113187 NSUN3; putative methyltransferase NSUN3 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 102111630 NSUN4; LOW QUALITY PROTEIN: 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 102109595 RPUSD3; RNA pseudouridylate synthase domain-containing protein 3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 102113077 RPUSD4; RNA pseudouridylate synthase domain-containing protein 4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 102104221 WBSCR16; Williams-Beuren syndrome chromosomal region 16 protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 102104955 TRUB2; probable tRNA pseudouridine synthase 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 102105974 FASTKD1; FAST kinase domain-containing protein 1 K27754 FASTKD1; FAST kinase domain-containing protein 1 D 102109464 FASTKD2; FAST kinase domain-containing protein 2 K18190 FASTKD2; FAST kinase domain-containing protein 2 D 102113529 FASTKD3; LOW QUALITY PROTEIN: FAST kinase domain-containing protein 3 K27755 FASTKD3; FAST kinase domain-containing protein 3 D 102102161 TBRG4; protein TBRG4 K27756 TBRG4; FAST kinase domain-containing protein 4 D 102105845 FASTKD5; FAST kinase domain-containing protein 5 K27757 FASTKD5; FAST kinase domain-containing protein 5 D 102110082 probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor D 102108314 RMND1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1 D 102110542 GRSF1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1 D 102106137 METTL15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 102112327 UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 102113610 uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 102114280 POLG; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 102102762 POLG2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 D 102104503 PRIMPOL; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 102109074 ENDOG; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 102100668 MGME1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 102107188 EXOG; nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial D 102102487 twinkle protein, mitochondrial isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3] D 102101766 PIF1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 102099107 ATAD3A; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 102109680 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 106628579 uncharacterized protein C17orf80 homolog K27759 MTNAP1; mitochondrial nucleoid-associated protein 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 102111585 DNAJA2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 102099631 TOMM34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 102104887 RHOT1; mitochondrial Rho GTPase 1 isoform X2 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 102108461 HSPA8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 102110652 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein D 102100622 AIP; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 102104243 TOMM40L; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40 D 102101255 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 102101402 TOMM70A; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 102113134 TOMM22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 102113853 TOMM20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 102110950 TOMM7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 102106888 TOMM6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 102114073 TOMM5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 102101863 SAMM50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family C Porin D 102099691 VDAC1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 102102486 VDAC2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 102100744 VDAC3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 102107941 MTX2; metaxin-2 K17776 MTX; metaxin D 102113518 MTX3; metaxin-3 isoform X2 K17776 MTX; metaxin D 102111604 MTX1; metaxin-1 K17776 MTX; metaxin D 102105371 MYO19; unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX D 102099267 mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 102105382 TIMM9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 102108100 TIMM10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 102104344 TIMM10B; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 102110595 TIMM8A; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 102099360 TIMM13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 102108388 CHCHD4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 102102749 GFER; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 102101847 MINOS1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 102100707 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 102104180 MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 102105150 CHCHD3; MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 102109773 CHCHD6; MICOS complex subunit MIC25 isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 102099791 APOO; MICOS complex subunit MIC26 K24625 APOO; MICOS complex subunit MIC26 D 102112303 APOOL; MICOS complex subunit MIC27 isoform X2 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 102101847 MINOS1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 102100707 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 102108153 TIMM22; mitochondrial import inner membrane translocase subunit Tim22 isoform X2 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 102109948 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 102105825 TIMM17A; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 102111061 TIMM21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 102099551 TIMM50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 102100271 MCU; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 102113344 MICU1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 102111370 MICU2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 102110877 CCDC109B; calcium uniporter regulatory subunit MCUb, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 102107907 SMDT1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 102101165 MCUR1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 102113726 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 102104542 LETM2; LETM1 domain-containing protein LETM2, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 102103087 IMMP1L; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 102103782 IMMP2L; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 102101934 transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 102103382 MPC1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 102099880 MPC2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 102105558 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 102101194 TIMM44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 102104007 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 102099576 GRPEL2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 102106970 GRPEL1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 102112118 DNAJC19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 102102938 PAM16; mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 102113640 PMPCA; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 102109431 PMPCB; mitochondrial-processing peptidase subunit beta isoform X2 K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 102104433 MIPEP; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 102107942 HSPD1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 102113925 DNAJA3; dnaJ homolog subfamily A member 3, mitochondrial K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 102104732 TAMM41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 102108645 DNLZ; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 106628866 ETHE1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 102114738 POLDIP2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 102101211 CREB1; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 102109826 GFM2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 102106378 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 102112711 SP1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1 D 102114222 YY1; transcriptional repressor protein YY1 K09201 YY; transcription factor YY D 102106863 GABPB1; GA-binding protein subunit beta-1 K09454 GABPB; GA-binding protein transcription factor, beta D 102100514 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 102107997 NRF1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1 D 102108440 NFE2L2; nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 C Coactivators D 102112718 PPARGC1A; peroxisome proliferator-activated receptor gamma coactivator 1-alpha K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 102104036 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 102099208 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 102107013 CRTC1; CREB-regulated transcription coactivator 1 isoform X2 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 102103796 CREBBP; CREB-binding protein isoform X2 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 102103022 EP300; histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 102101247 NFS1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 102104283 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 102110207 LYRM4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 102104392 FXN; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 102100397 FDX1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 102103405 FDX1L; adrenodoxin-like protein, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 102102760 adrenodoxin-like K22071 FDX2; ferredoxin-2, mitochondrial D 102103074 FDXR; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 102104007 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 102110705 HSCB; iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB D 102108661 nucleotide exchange factor SIL1-like K14001 SIL1; nucleotide exchange factor SIL1 D 102109744 SIL1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1 D 102102485 GLRX5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 102100001 ISCA1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 102105419 ISCA2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 102112691 IBA57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 102107813 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 102104240 BOLA1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 102105032 BOLA3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 102102305 SFXN3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 102112062 SFXN1; sideroflexin-1 isoform X1 K23500 SFXN1_3; sideroflexin-1/3 D 102103968 SFXN2; sideroflexin-2 K23501 SFXN2; sideroflexin-2 D 102102488 SFXN4; sideroflexin-4 isoform X2 K23502 SFXN4; sideroflexin-4 D 102104919 SFXN5; sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 102103127 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 102105403 carnitine O-palmitoyltransferase 1, muscle isoform-like K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21] D 102106815 DHTKD1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 102109580 FBXL4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 102111184 host cell factor 1 K14966 HCFC1; host cell factor 1 D 102111652 HCFC2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2 D 102109876 HTT; huntingtin K04533 HD; huntingtin D 102101080 ESRRB; steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta D 102099760 ESRRG; estrogen-related receptor gamma isoform X5 K08554 NR3B3; estrogen-related receptor gamma D 102104705 NRIP1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 102111333 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 102111653 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 102101980 SIRT1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 102112660 SERAC1; protein SERAC1 K23504 SERAC1; protein SERAC1 D 102102723 UXT; protein UXT isoform X2 K26537 UXT; protein UXT D 102109444 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 D 102101042 ES1 protein homolog, mitochondrial-like K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 102100398 ES1 protein homolog, mitochondrial-like K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 102105440 ES1 protein homolog, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 102104091 NDUFAF1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 102109148 NDUFAF2; mimitin, mitochondrial isoform X1 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 102109039 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 102112251 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 102100402 NDUFAF6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 102110034 NDUFAF7; NADH dehydrogenase [ubiquinone] complex I, assembly factor 7 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 106628580 uncharacterized protein C17orf89 homolog K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 102107277 ZNF653; zinc finger protein 653 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 102112394 ACAD9; acyl-CoA dehydrogenase family member 9, mitochondrial isoform X1 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 102102556 NUBPL; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning D 102111951 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 102113234 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 102100239 TIMMDC1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 102103329 SDHAF2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 102100470 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 102106994 TTC19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 102108105 LYRM7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 102099365 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 102109680 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 106628976 ubiquinol-cytochrome-c reductase complex assembly factor 3-like K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 106628179 protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 102110077 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 106628411 uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 102102954 uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 102112101 CMC1; COX assembly mitochondrial protein homolog isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1 D 102104717 CMC2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 102114391 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1 D 102104123 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 102111081 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 102101997 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 102114531 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 102105059 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 102101672 protoheme IX farnesyltransferase, mitochondrial isoform X1 K02257 COX10; heme o synthase [EC:2.5.1.141] D 102101229 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 102106077 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14 D 102110959 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 102113117 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 102105801 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 102110733 mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18 D 102100724 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 102111478 cytochrome c oxidase protein 20 homolog K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 102112807 MSS51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 102101810 PET100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 102101029 PET117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 106628932 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 102109913 SURF1; surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 102102039 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 102112713 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 102108368 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 102103308 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 102110128 APOPT1; apoptogenic protein 1, mitochondrial isoform X1 K23506 APOPT1; apoptogenic protein 1 D 102102954 uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1 D 102110077 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 106627987 TMEM223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 102114474 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 102112485 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 102102982 TMEM70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 102106608 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid D 102103054 USMG5; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 102114490 MFN1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 102110409 MFN2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 102100616 OPA1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 102104976 OPA3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein D 102110144 TRIAP1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 102108104 PARL; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 102107798 BAK1; bcl-2 homologous antagonist/killer K14021 BAK; Bcl-2 homologous antagonist/killer D 102106020 BAX; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 102101789 DNM1L; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 102100075 SUMO2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 102102837 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 102102483 SUMO1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 102109588 SH3GLB1; endophilin-B1 isoform X2 K11248 SH3GLB1; endophilin-B1 D 102111598 MTCH1; mitochondrial carrier homolog 1 K17885 MTCH; mitochondrial carrier D 102101729 MTCH2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 102105630 MFF; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor D 102108276 FATE1; fetal and adult testis-expressed transcript protein K22076 MFF; mitochondrial fission factor D 102108307 GDAP1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 102109062 GDAP1L1; ganglioside-induced differentiation-associated protein 1-like 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 102102842 VAT1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 102100495 MIEF1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 102113743 MIEF2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 102107420 PLD6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 102110786 FAM73B; protein FAM73B isoform X2 K27289 MIGA; mitoguardin D 102100291 FAM73A; protein FAM73A K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 102110255 actin, cytoplasmic type 5 K05692 ACTB_G1; actin beta/gamma 1 D 102111224 ACTG1; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 102106742 ACTB; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 102111367 NAA20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 102103372 NAA25; N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 102101058 PHB; prohibitin K17080 PHB1; prohibitin 1 D 102109900 PHB2; prohibitin-2 K17081 PHB2; prohibitin 2 D 102107910 KTN1; kinectin isoform X8 K17975 KTN1; kinectin C Retention of mitochondria D 102101789 DNM1L; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 102099388 MYO5A; unconventional myosin-Va K10357 MYO5; myosin V D 102099569 MYO5C; unconventional myosin-Vc K10357 MYO5; myosin V D 102104960 MYO5B; unconventional myosin-Vb K10357 MYO5; myosin V D 102101552 XIAP; E3 ubiquitin-protein ligase XIAP isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 102099764 DIABLO; diablo homolog, mitochondrial isoform X1 K10522 DIABLO; diablo C Morphogenesis factors D 102105601 SNX25; sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25 D 102104887 RHOT1; mitochondrial Rho GTPase 1 isoform X2 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 102100707 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 102099630 MTFP1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 102112836 DAP3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 102112350 NEDD4; E3 ubiquitin-protein ligase NEDD4 isoform X2 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 102103531 OXR1; oxidation resistance protein 1 isoform X1 K25437 OXR1; oxidation resistance protein 1 D 102110476 MSTO1; protein misato homolog 1 K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 102101582 ATG2B; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2 D 102113186 ATG3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 102099386 ATG4C; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 102105263 ATG4B; cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 102103393 ATG4A; cysteine protease ATG4A isoform X2 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 102107576 cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 102112721 ATG5; autophagy protein 5 isoform X3 K08339 ATG5; autophagy-related protein 5 D 102104305 BECN1; beclin-1 K08334 BECN; beclin D 102107634 ATG7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 102107990 GABARAPL2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 102114705 GABARAPL1; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 102114461 GABARAP; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 102103232 ATG9A; autophagy-related protein 9A isoform X1 K17907 ATG9; autophagy-related protein 9 D 102101055 ATG9B; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9 D 102100875 ATG10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 102110914 ATG12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12 D 102108281 ATG14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 102099836 ATG16L1; autophagy-related protein 16-1 isoform X2 K17890 ATG16L1; autophagy-related protein 16-1 D 102106867 WIPI2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 102114741 WIPI1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 102104443 vacuolar protein 8-like K08332 VAC8; vacuolar protein 8 C Parkin-dependent mechanism factors D 102105199 PARK2; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31] D 102099300 RNF41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 102114661 CLEC16A; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 102103989 PINK1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 102108104 PARL; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 102110080 SQSTM1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1 D 102102181 TAX1BP1; tax1-binding protein 1 isoform X1 K21347 TAX1BP1; Tax1-binding protein 1 D 102099944 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 102099326 ATG13; autophagy-related protein 13 isoform X6 K08331 ATG13; autophagy-related protein 13 D 102112005 ULK1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 102103867 ULK2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 102107096 RB1CC1; RB1-inducible coiled-coil protein 1 isoform X2 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 102112171 HSP90AA1; heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG D 102099720 HSP90AB1; LOW QUALITY PROTEIN: heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 102110871 CDC37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 102107051 SMURF1; E3 ubiquitin-protein ligase SMURF1 isoform X4 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 102102573 SMURF2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 102107510 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 102104525 FUNDC1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 102111333 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 102111653 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 102109519 MAP1LC3C; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 102100510 MAP1LC3A; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 102114441 MAP1LC3B; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 102105885 NBR1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 102113561 TECPR1; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 102110767 ZFYVE1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 102100635 COASY; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 102111464 PLA2G6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 102113761 protein C19orf12 homolog isoform X2 K23168 MPAN; protein MPAN D 102112126 FUNDC2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: August 9, 2024