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  Mitochondrial Biogenesis - Papilio machaon (common yellow swallowtail)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 106711773 LOW QUALITY PROTEIN: NADH-ubiquinone oxidoreductase chain 1-like K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 13080339 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 106711768 LOW QUALITY PROTEIN: NADH-ubiquinone oxidoreductase chain 2-like K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 13080340 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 13080346 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 106711772 LOW QUALITY PROTEIN: NADH-ubiquinone oxidoreductase chain 4-like K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 13080348 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 13080349 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 13080347 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 13080337 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 13080338 cytB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 13080341 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 13080342 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 13080345 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 13080343 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 106711769 LOW QUALITY PROTEIN: ATP synthase subunit a-like K02126 ATPeF0A; F-type H+-transporting ATPase subunit a D 13080344 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 106720903 LOW QUALITY PROTEIN: DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 106710233 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 106718968 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 106721532 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 106707924 translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 106708769 uncharacterized protein LOC106708769 K02520 infC; translation initiation factor IF-3 D 106713759 elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts D 106720014 elongation factor Tu-like K02358 tuf; elongation factor Tu D 106720186 elongation factor Tu K02358 tuf; elongation factor Tu D 106708661 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 106714207 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 106710835 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 106712231 uncharacterized protein LOC106712231 K15031 MTERF; mitochondrial transcription termination factor family protein D 106712435 uncharacterized protein LOC106712435 K15031 MTERF; mitochondrial transcription termination factor family protein D 106714385 uncharacterized protein LOC106714385 isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 106718082 translation factor GUF1 homolog, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 106719115 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 106713657 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 106720275 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 106720602 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 106717863 ribonuclease P protein subunit p20 isoform X1 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 106710779 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 106709729 uncharacterized protein LOC106709729 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 106717632 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 106719897 3-hydroxyacyl-CoA dehydrogenase type-2 isoform X1 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 106721132 3-hydroxyacyl-CoA dehydrogenase type-2-like K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 106719884 mitochondrial ribonuclease P protein 3 K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 106710453 transcription elongation factor, mitochondrial isoform X1 K17658 TEFM; transcription elongation factor, mitochondrial D 106713801 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 106716629 pentatricopeptide repeat-containing protein 2, mitochondrial-like K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 106713513 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 106719069 putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 106719032 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 106714827 putative ATPase N2B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 106720257 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 106707746 LOW QUALITY PROTEIN: ATP-dependent RNA helicase SUV3 homolog, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 106714232 beta-lactamase-like protein 2 homolog K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 106713248 ADP,ATP carrier protein K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 106717268 ADP,ATP carrier protein-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 106713987 mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 106714197 uncharacterized protein LOC106714197 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 106716636 GTPase Era, mitochondrial K03595 era; GTPase D 106716366 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 106718206 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 106708976 probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 106710632 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 106714732 uncharacterized protein LOC106714732 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 106711841 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 106715673 probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 106720936 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 106716230 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 106716713 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 106718127 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 106708386 poly(A) RNA polymerase, mitochondrial-like K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 106710713 2',5'-phosphodiesterase 12 isoform X1 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 106708738 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 106708481 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 106711311 5-methylcytosine rRNA methyltransferase NSUN4-like K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 106716031 Williams-Beuren syndrome chromosomal region 16 protein-like K23495 RCC1L; RCC1-like G exchanging factor-like protein D 106712510 uncharacterized protein LOC106712510 K23496 NGRN; neugrin D 106708347 probable tRNA pseudouridine synthase 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 106708687 uncharacterized protein LOC106708687 K18190 FASTKD2; FAST kinase domain-containing protein 2 D 106709276 FAST kinase domain-containing protein 3-like K27755 FASTKD3; FAST kinase domain-containing protein 3 D 106711831 protein TBRG4 K27756 TBRG4; FAST kinase domain-containing protein 4 D 106708583 FAST kinase domain-containing protein 5 K27757 FASTKD5; FAST kinase domain-containing protein 5 D 106720263 probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor D 106713568 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 106721121 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 106707929 LOW QUALITY PROTEIN: probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 106707719 UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 106718172 uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 106719735 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 106718126 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 C Mitochondrial DNA maintenance factors D 106718728 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 106708450 mitochondrial genome maintenance exonuclease 1-like K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 106712430 twinkle protein, mitochondrial K17680 TWNK; twinkle mtDNA helicase [EC:5.6.2.3] D 106720961 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 106708541 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 106717063 ATPase family AAA domain-containing protein 3-B K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 106714373 dnaJ homolog subfamily A member 2-like K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 106720175 LOW QUALITY PROTEIN: mitochondrial Rho GTPase K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 106708062 LOW QUALITY PROTEIN: heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 106712862 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 106713054 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 106720294 heat shock 70 kDa protein cognate 4 isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 106717842 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 106708011 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 106717870 LOW QUALITY PROTEIN: uncharacterized protein LOC106717870 K17769 TOM22; mitochondrial import receptor subunit TOM22 D 106711273 mitochondrial import receptor subunit TOM40 homolog 1-like K11518 TOM40; mitochondrial import receptor subunit TOM40 D 106713240 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 106717623 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 106709473 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 C TOB/SAM complex D 106708352 sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family C MIM complex C Porin D 106721007 voltage-dependent anion-selective channel-like K15040 VDAC2; voltage-dependent anion channel protein 2 C Other outer membrane factor D 106711524 metaxin-1 isoform X1 K17776 MTX; metaxin D 106721537 mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 106711138 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 106708028 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 C TIM8/13 complex D 106715691 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 106719261 mitochondrial import inner membrane translocase subunit Tim13-like K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 106707897 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 106718937 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 106715474 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10 D 106720717 MICOS complex subunit MIC13 homolog K24624 MICOS13; MICOS complex subunit MIC13 D 106713903 uncharacterized protein LOC106713903 K17563 CHCHD3; MICOS complex subunit MIC19 D 106707870 uncharacterized protein LOC106707870 K24626 APOOL; MICOS complex subunit MIC27 D 106715199 uncharacterized protein LOC106715199 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 106715474 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10 C TIM22 complex D 106713042 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 106707594 mitochondrial import inner membrane translocase subunit Tim23-like K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 106715081 mitochondrial import inner membrane translocase subunit Tim23-like K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 106711716 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 106719849 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 106711378 mitochondrial import inner membrane translocase subunit TIM50-C-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 106709064 LOW QUALITY PROTEIN: calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial D 106714748 calcium uptake protein 1 homolog, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial D 106717916 protein EMRE homolog, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial C Other inner membrane factors D 106708662 LETM1 and EF-hand domain-containing protein 1, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 106710598 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 106712996 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 106715959 uncharacterized protein LOC106715959 K18157 TMEM126A; transmembrane protein 126A D 106711717 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 106707712 mitochondrial pyruvate carrier 2-like isoform X1 K22139 MPC2; mitochondrial pyruvate carrier 2 D 106715907 OCIA domain-containing protein 1-like K28215 OCIAD1; OCIA domain-containing protein 1 B Matrix C MMC/PAM proteins D 106708399 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 106708131 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 106707389 grpE protein homolog, mitochondrial-like K03687 GRPE; molecular chaperone GrpE D 106710188 grpE protein homolog, mitochondrial-like K03687 GRPE; molecular chaperone GrpE D 106712417 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 106721138 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 106720444 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 106715885 cytochrome b-c1 complex subunit 1, mitochondrial-like K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 106716875 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 106715991 mitochondrial intermediate peptidase-like K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 106713144 60 kDa heat shock protein, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 106721555 63 kDa chaperonin, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 106713771 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 106720821 protein tumorous imaginal discs, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 106712448 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 106717682 DNL-type zinc finger protein-like K17808 ZIM17; mitochondrial protein import protein ZIM17 D 106713947 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 106711087 LOW QUALITY PROTEIN: polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 106710823 cyclic AMP response element-binding protein B isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 106708661 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 106714207 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 106721253 transcriptional repressor protein YY1-like K09201 YY; transcription factor YY D 106721263 GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta D 106710233 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 106716071 DNA-binding protein Ewg K11831 NRF1; nuclear respiratory factor 1 C Coactivators D 106713670 titin K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 106716501 CREB-regulated transcription coactivator 3-like K15309 CRTC1; CREB-regulated transcription coactivator 1 D 106715652 histone acetyltransferase p300-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 106719862 probable cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 106708747 iron-sulfur cluster assembly scaffold protein IscU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 106715265 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 106720241 frataxin homolog, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 106709620 adrenodoxin-like protein, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 106720445 NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 106708131 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 106714590 iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB D 106711177 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 106714947 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 106720994 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 106721526 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 106709774 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 106720281 bolA-like protein DDB_G0274169 K22066 BOLA1; BolA-like protein 1 D 106710099 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 106720490 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 106708600 sideroflexin-2-like K23501 SFXN2; sideroflexin-2 D 106716153 sideroflexin-2 K23501 SFXN2; sideroflexin-2 C Other regulator of mitochondrial biogenesis D 106720032 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 106712864 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 106710048 LOW QUALITY PROTEIN: F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 106713898 uncharacterized protein LOC106713898 K04533 HD; huntingtin D 106711118 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 106709369 uncharacterized protein LOC106709369 K23504 SERAC1; protein SERAC1 D 106717052 protein SERAC1 K23504 SERAC1; protein SERAC1 D 106714583 transport and Golgi organization protein 2 isoform X1 K28098 TANGO2; transport and Golgi organization protein 2 D 106711821 UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69 D 106715563 uncharacterized protein LOC106715563 K28528 ATOS; protein Atossa D 106719305 probable ATP-dependent RNA helicase DDX47 K14777 DDX47; ATP-dependent RNA helicase DDX47/RRP3 [EC:5.6.2.7] B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 106710809 uncharacterized protein C9E9.15-like isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 106721577 complex I intermediate-associated protein 30, mitochondrial isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 106709282 mimitin, mitochondrial K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 106708315 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 106718693 protein NDUFAF4 homolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 106715611 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 106719941 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 106719347 NADH dehydrogenase [ubiquinone] complex I, assembly factor 7 homolog K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 106708031 uncharacterized protein LOC106708031 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 106718050 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 106709410 LOW QUALITY PROTEIN: acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 106711978 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 106714383 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 106718958 reticulon-4-interacting protein 1, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 106714745 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 106708776 succinate dehydrogenase assembly factor 2-B, mitochondrial-like K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 106712330 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 106716630 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 106720651 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 106719032 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 106718161 uncharacterized protein LOC106718161 isoform X1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 106710777 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 106710778 uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 C Complex-IV assembly factors D 106721017 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 106715430 COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 106718969 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 106710510 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 106709719 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 106711413 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 106718449 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 106718939 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 106709728 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 106712513 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 106717802 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 106714927 cytochrome c oxidase protein 20 homolog K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 106720721 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 106718009 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 106719916 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 106714038 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 106719506 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 106719000 APOPT family protein CG14806, mitochondrial K23506 APOPT1; apoptogenic protein 1 D 106710777 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 106710448 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 D 106712339 HIG1 domain family member 1A, mitochondrial-like K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 106712374 HIG1 domain family member 1C K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 106714227 HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial C Complex-V assembly factors D 106709741 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 106713293 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 106718147 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 106719695 up-regulated during skeletal muscle growth protein 5-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 106718413 LOW QUALITY PROTEIN: transmembrane GTPase Marf-like K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 106711036 dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 106721561 optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein D 106710592 TP53-regulated inhibitor of apoptosis 1-like K17968 TRIAP1; TRIAP1/MDM35 family protein D 106712334 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 106708523 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 106719270 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 106708686 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 106713730 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier D 106712324 transport and Golgi organization protein 11 K22076 MFF; mitochondrial fission factor D 106719147 ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 106718905 mitochondrial cardiolipin hydrolase-like K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 106719660 mitochondrial cardiolipin hydrolase-like K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 106713321 protein FAM73B K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 106710491 actin, muscle K05692 ACTB_G1; actin beta/gamma 1 D 106720055 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 106713014 phagocyte signaling-impaired protein K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 106714272 protein l(2)37Cc K17080 PHB1; prohibitin 1 D 106708400 prohibitin-2 K17081 PHB2; prohibitin 2 C Retention of mitochondria D 106708523 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 106709467 LOW QUALITY PROTEIN: unconventional myosin-Va-like K10357 MYO5; myosin V C Morphogenesis factors D 106707776 sorting nexin-25 K17887 SNX25; sorting nexin-25 D 106720175 LOW QUALITY PROTEIN: mitochondrial Rho GTPase K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 106712998 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 106713919 28S ribosomal protein S29, mitochondrial-like K17408 DAP3; small subunit ribosomal protein S29 D 106716462 E3 ubiquitin-protein ligase Nedd-4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 106716740 protein misato K27320 MSTO1; protein misato D 106710690 protein slowmo K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial D 106716644 TM2 domain-containing protein almondex K28688 TM2D3; TM2 domain-containing protein 3 B Mitophagy factors C Autophagy-related proteins D 106721483 autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 106707434 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 106719269 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 106714236 cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 106721501 cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 106719613 autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 106708496 beclin-1-like protein K08334 BECN; beclin D 106716350 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 106719220 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 106717092 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 106715960 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 106713781 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12 D 106712756 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 106718699 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 106713720 WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 106714813 E3 ubiquitin-protein ligase NRDP1 isoform X1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 106717476 protein CLEC16A K19513 CLEC16A; protein CLEC16A D 106712334 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 106714365 protein ref(2)P-like isoform X1 K14381 SQSTM1; sequestosome 1 D 106719780 uncharacterized protein LOC106719780 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 106717124 autophagy-related protein 13 homolog K08331 ATG13; autophagy-related protein 13 D 106721720 autophagy-related protein 13 homolog K08331 ATG13; autophagy-related protein 13 D 106717803 LOW QUALITY PROTEIN: serine/threonine-protein kinase unc-51 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 106714274 RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 106708061 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG D 106715422 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 106717545 E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 106709013 FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 106711118 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 106715426 uncharacterized protein LOC106715426 K10435 MAP1LC; microtubule-associated protein 1 light chain D 106709085 tectonin beta-propeller repeat-containing protein K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 106717784 bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 106718320 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: December 5, 2025