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Mitochondrial Biogenesis - Pieris rapae (cabbage white)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 11030472 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 11030477 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 11030483 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 11030473 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 11030476 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 11030474 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 11030475 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 11030471 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
D 110996672 LOW QUALITY PROTEIN: cytochrome b-like K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 11030478 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 11030479 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 11030482 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 11030480 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 11030481 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 111003703 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 110995435 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 110995046 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 110997484 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 111000861 translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 110996559 translation initiation factor IF-3, mitochondrial-like K02520 infC; translation initiation factor IF-3
D 111002409 elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts
D 110999451 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 111003303 elongation factor Tu K02358 tuf; elongation factor Tu
D 110994197 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 111003940 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 111003144 transcription termination factor 5, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 110999440 transcription termination factor 5, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 111002234 transcription termination factor, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 110998646 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 110996615 translation factor GUF1 homolog, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 111003755 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 110998348 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 110996857 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 110995199 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 110994532 ribonuclease P protein subunit p20-like isoform X1 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 110996489 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 110997669 ribonuclease P protein subunit p40-like K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 110994388 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 111000559 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 110993036 3-hydroxyacyl-CoA dehydrogenase type-2 isoform X1 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 110992969 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 110992616 uncharacterized protein LOC110992616 K17658 TEFM; transcription elongation factor, mitochondrial
D 111003106 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 110991519 pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 110995079 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 111003296 ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 110996443 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 110994661 putative ATPase N2B isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 110995578 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 110994499 ATP-dependent RNA helicase SUV3 homolog, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 110994204 beta-lactamase-like protein 2 homolog K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 111001811 ADP,ATP carrier protein K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 110999236 ADP,ATP carrier protein-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 110994128 mitoferrin isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 110993556 uncharacterized protein LOC110993556 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 110996842 GTPase Era, mitochondrial K03595 era; GTPase
D 110996667 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 111004211 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 111001213 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 111003239 probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 110991956 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 110991891 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 111001406 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 111003680 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 110991570 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 110991513 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 110991924 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 110998662 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 111001297 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 110991840 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 110995453 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 110993673 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 111004259 uncharacterized protein LOC111004259 K23496 NGRN; neugrin
D 110991842 mitochondrial mRNA pseudouridine synthase Trub2 isoform X1 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 111003942 uncharacterized protein LOC111003942 isoform X1 K18190 FASTKD2; FAST kinase domain-containing protein 2
D 110996882 mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 111002937 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 111000873 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 110997321 MYG1 exonuclease K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 110998891 mitochondrial transcription rescue factor 1 isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 110999849 DNA polymerase subunit gamma-1, mitochondrial isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 110996618 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
C Mitochondrial DNA maintenance factors
D 111000640 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 110995087 mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 111001188 mitochondrial DNA helicase isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 110999185 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 110997018 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 110995236 ATPase family AAA domain-containing protein 3A homolog K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 111002233 dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 110992726 mitochondrial Rho GTPase isoform X3 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 110993516 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110995687 heat shock protein 68 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 111003529 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 111004097 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 111004285 heat shock protein 68 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110994558 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 111003863 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 111001165 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 110996128 uncharacterized protein LOC110996128 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 111002727 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 110994537 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 110997767 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
C TOB/SAM complex
D 110996187 sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 111001634 voltage-dependent anion-selective channel K15040 VDAC2; voltage-dependent anion channel protein 2
C ERMES complex
C Other outer membrane factor
D 111003591 metaxin-1 isoform X1 K17776 MTX; metaxin
D 110993060 mitochondrial amidoxime reducing component 2-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 110993080 mitochondrial amidoxime reducing component 2 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 110995907 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 111004025 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
C TIM8/13 complex
D 110996241 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 111001343 mitochondrial import inner membrane translocase subunit Tim13-like K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 111003866 mitochondrial intermembrane space import and assembly protein 40-B K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 110995403 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 110994717 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 110998776 MICOS complex subunit Mic60-like K17785 IMMT; MICOS complex subunit MIC60
D 110998942 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 110994961 uncharacterized protein LOC110994961 K17563 CHCHD3; MICOS complex subunit MIC19
D 110994807 uncharacterized protein LOC110994807 K17563 CHCHD3; MICOS complex subunit MIC19
D 110991748 uncharacterized protein LOC110991748 K17564 CHCHD6; MICOS complex subunit MIC25
D 110992323 uncharacterized protein LOC110992323 isoform X1 K24626 APOOL; MICOS complex subunit MIC27
D 111003338 uncharacterized protein LOC111003338 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 110994717 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 110998776 MICOS complex subunit Mic60-like K17785 IMMT; MICOS complex subunit MIC60
D 110998942 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 111002075 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 110996784 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 111001583 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 110998088 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 111003523 mitochondrial import inner membrane translocase subunit TIM50-C K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 110997730 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 110998368 calcium uptake protein 1 homolog, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 110994574 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
C Other inner membrane factors
D 111001955 mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 111001215 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 110997072 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 111003652 uncharacterized protein LOC111003652 K18157 TMEM126A; transmembrane protein 126A
D 111001577 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 111000423 mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
B Matrix
C MMC/PAM proteins
D 110991908 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 110992825 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 110993704 grpE protein homolog, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 110997123 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 110993023 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 110993774 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 110993118 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 111003330 mitochondrial-processing peptidase subunit beta-like K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 111003331 mitochondrial-processing peptidase subunit beta-like K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 111001867 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 110993743 heat shock protein 60A K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 110994055 63 kDa chaperonin, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 111003075 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 110997053 protein tumorous imaginal discs, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 110998485 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 110993245 DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 110999564 uncharacterized protein LOC110999564 isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 110995493 persulfide dioxygenase ETHE1, mitochondrial isoform X2 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 110991485 polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 110992742 cyclic AMP response element-binding protein B isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 110994197 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 111003940 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 110997486 transcriptional repressor protein YY1 isoform X1 K09201 YY; transcription factor YY
D 111001841 poly [ADP-ribose] polymerase tankyrase isoform X2 K09454 GABPB; GA-binding protein transcription factor, beta
D 110995435 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 110993665 DNA-binding protein P3A2 isoform X1 K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 111002869 uncharacterized protein LOC111002869 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 110991527 CREB-regulated transcription coactivator 3 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 111001410 CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 110999099 cysteine desulfurase, mitochondrial isoform X1 K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 110992578 iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 111004167 frataxin homolog, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 111003778 adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial
D 110997945 adrenodoxin-like protein 1, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 110993775 LOW QUALITY PROTEIN: NADPH:adrenodoxin oxidoreductase, mitochondrial-like K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 110992825 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 110993217 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 111004141 uncharacterized monothiol glutaredoxin ycf64-like K07390 grxD; monothiol glutaredoxin
D 111002262 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 111000334 iron-sulfur assembly protein IscA-like 2, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 110993094 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 110995037 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 110996969 putative bolA-like protein K11H12.1 K22066 BOLA1; BolA-like protein 1
D 110999164 sideroflexin-1-3 isoform X2 K23500 SFXN1_3; sideroflexin-1/3
D 110999728 sideroflexin-2 K23501 SFXN2; sideroflexin-2
C Other regulator of mitochondrial biogenesis
D 110999281 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 110995686 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 110999221 F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 111002994 host cell factor 1 K14966 HCFC1; host cell factor 1
D 110998919 huntingtin K04533 HD; huntingtin
D 110991484 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 111003238 lon protease homolog, mitochondrial isoform X1 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 111000753 protein SERAC1 K23504 SERAC1; protein SERAC1
D 110995914 uncharacterized protein LOC110995914 K23504 SERAC1; protein SERAC1
D 110994340 protein UXT homolog K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 110998806 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 110995849 uncharacterized protein LOC110995849 isoform X2 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 111003871 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 110996198 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 110995971 protein NDUFAF4 homolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 110998227 arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 111000350 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 110996840 protein arginine methyltransferase NDUFAF7 homolog, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 110999029 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 110991799 iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 110999096 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 111003255 reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 110994104 reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 111002138 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 110992861 succinate dehydrogenase assembly factor 2-A, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 111003140 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 110991496 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 111002055 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 110996443 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 123689346 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 111002592 uncharacterized protein LOC111002592 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
C Complex-IV assembly factors
D 111003505 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 111004334 COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 110995047 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 123690351 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 110993361 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 110991333 cytochrome c oxidase assembly factor 6 homolog isoform X3 K18179 COA6; cytochrome c oxidase assembly factor 6
D 110995146 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7
D 110995663 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 110995391 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 110997693 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 111003619 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 110995099 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 111000302 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 110993996 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 110996947 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 123689575 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 110998802 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 111000349 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 111001097 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 110996772 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 111003856 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 111000193 COA8 family protein CG14806, mitochondrial K23506 APOPT1; apoptogenic protein 1
D 123689346 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 110992660 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 110999497 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 110998076 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 111004213 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
B Mitochondrial dynamics
C Fission and Fusion factors
D 111000195 transmembrane GTPase Marf K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 110994964 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 110997468 putative OPA3-like protein CG13603 K23166 OPA3; optic atrophy 3 protein
D 111001905 TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 111001695 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 110992552 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 110997816 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 110992608 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 111003065 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier
D 110995500 transport and Golgi organization protein 11 K22076 MFF; mitochondrial fission factor
D 110992111 ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 111003055 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 110995060 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 110999149 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 110995822 uncharacterized protein LOC110995822 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 111002164 mitoguardin K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 110993588 actin, cytoplasmic A3a K05692 ACTB_G1; actin beta/gamma 1
D 110993589 actin-5C K05692 ACTB_G1; actin beta/gamma 1
D 110992936 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 110993277 phagocyte signaling-impaired protein K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 110994195 protein l(2)37Cc K17080 PHB1; prohibitin 1
D 110997791 prohibitin-2 K17081 PHB2; prohibitin 2
D 110994985 prohibitin-2-like K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 110992552 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 110992647 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
C Morphogenesis factors
D 110992886 sorting nexin-25 isoform X3 K17887 SNX25; sorting nexin-25
D 110992726 mitochondrial Rho GTPase isoform X3 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 110998776 MICOS complex subunit Mic60-like K17785 IMMT; MICOS complex subunit MIC60
D 110998942 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 110996577 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 110994953 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 111000167 E3 ubiquitin-protein ligase Nedd-4 isoform X2 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 110998042 protein misato K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 110997534 autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 110997815 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 110994234 cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 110997456 cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 111004243 autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 110997779 beclin-1-like protein K08334 BECN; beclin
D 111004437 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 110992141 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 110997371 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 111003695 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 111002829 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12
D 110991308 beclin 1-associated autophagy-related key regulator isoform X1 K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 110995297 autophagy-related protein 16 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 110997974 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 110998395 E3 ubiquitin-protein ligase NRDP1 isoform X1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 110996228 protein CLEC16A homolog isoform X1 K19513 CLEC16A; protein CLEC16A
D 111001695 presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 110994780 sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1
D 111000340 uncharacterized protein LOC111000340 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 110999590 autophagy-related protein 13 homolog K08331 ATG13; autophagy-related protein 13
D 110995139 serine/threonine-protein kinase unc-51 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 110998751 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 111004307 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG
D 110995382 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 111002814 E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 111003271 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 110991484 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 110993027 uncharacterized protein LOC110993027 isoform X1 K10435 MAP1LC; microtubule-associated protein 1 light chain
D 110992684 tectonin beta-propeller repeat-containing protein K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 110997005 bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 111003749 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024