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Mitochondrial Biogenesis - Polyodon spathula (Mississippi paddlefish)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 805407 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 805405 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 805403 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 805402 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 805413 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 805414 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 805404 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 805406 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 805409 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 805412 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 805408 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 805410 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 805411 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 121301453 polrmt; DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 121325960 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 121322187 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 121315380 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 121317656 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 121317283 mtif2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 121302874 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 121308965 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 121307320 elongation factor Tu, mitochondrial-like K02358 tuf; elongation factor Tu
D 121307321 elongation factor Tu, mitochondrial-like K02358 tuf; elongation factor Tu
D 121307322 elongation factor Tu, mitochondrial-like K02358 tuf; elongation factor Tu
D 121326674 elongation factor G, mitochondrial-like isoform X1 K02355 fusA; elongation factor G
D 121323178 elongation factor G, mitochondrial-like K02355 fusA; elongation factor G
D 121313460 ribosome-releasing factor 2, mitochondrial-like isoform X1 K02355 fusA; elongation factor G
D 121315015 transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 121318402 mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 121313225 mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 121326414 mterf4; transcription termination factor 4, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 121324189 guf1; translation factor Guf1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 121314951 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 121295975 ribonuclease P protein subunit p29-like K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 121299877 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 121325895 ribonuclease P protein subunit p30-like K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 121321501 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 121306594 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 121299364 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 121314657 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 121312987 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 121313184 ribonuclease P protein subunit p38-like K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 121314524 rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 121320844 tRNA methyltransferase 10 homolog C-like K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 121328097 tRNA methyltransferase 10 homolog C-like isoform X1 K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 121305366 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 121330159 mitochondrial ribonuclease P catalytic subunit-like K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 121300562 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 121307627 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 121300890 ptcd1; pentatricopeptide repeat-containing protein 1, mitochondrial isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 121319290 LOW QUALITY PROTEIN: pentatricopeptide repeat-containing protein 2, mitochondrial-like K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 121305578 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 121325719 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 121312818 dhx30; ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 121298100 ubiquinol-cytochrome-c reductase complex assembly factor 1-like K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 121319466 ubiquinol-cytochrome-c reductase complex assembly factor 1-like isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 121317416 afg1la; AFG1 like ATPase a isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 121318111 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 121319991 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 121326056 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 121313403 lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 121295429 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 121297608 ADP/ATP translocase 1-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 121320453 ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 121320702 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 121327991 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 121328224 ADP/ATP translocase 4-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 121318842 ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 121325674 mitoferrin-2-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 121321787 slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 121302435 mitoferrin-1-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 121303132 mitoferrin-1-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 121313609 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 isoform X1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 121308436 eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 121308363 yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 121318527 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 121297606 leucine--tRNA ligase, cytoplasmic-like K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 121312900 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 121324629 leucine--tRNA ligase, cytoplasmic-like K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 121326718 dars2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 121309791 glycine--tRNA ligase-like K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 121314026 gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 121317605 rars2; probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 121324634 rars1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 121316289 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 121321419 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 121297185 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial-like K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 121300282 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial-like isoform X1 K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 121311588 poly(A) RNA polymerase, mitochondrial-like K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 121314103 poly(A) RNA polymerase, mitochondrial-like isoform X1 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 121298258 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 121321806 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 121294882 noa1; nitric oxide-associated protein 1 isoform X1 K19832 NOA1; nitric oxide-associated protein 1
D 121328137 tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial-like isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 121326428 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 121329299 mitochondrial mRNA pseudouridine synthase RPUSD3-like K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 121306875 rpusd4; mitochondrial RNA pseudouridine synthase rpusd4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 121308459 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 121305086 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 121299994 neugrin-like K23496 NGRN; neugrin
D 121306724 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 isoform X1 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 121322127 FAST kinase domain-containing protein 2, mitochondrial-like K18190 FASTKD2; FAST kinase domain-containing protein 2
D 121322599 FAST kinase domain-containing protein 2, mitochondrial-like K18190 FASTKD2; FAST kinase domain-containing protein 2
D 121296770 mtrfr; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor
D 121315844 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 121316961 required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 121300160 G-rich sequence factor 1-like K24984 GRSF1; G-rich sequence factor 1
D 121317349 grsf1; G-rich sequence factor 1 isoform X1 K24984 GRSF1; G-rich sequence factor 1
D 121295098 mettl15; probable methyltransferase-like protein 15 isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 121307139 MYG1 exonuclease-like K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 121316292 mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 121304422 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 121296213 polg2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 121297508 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 121306737 LOW QUALITY PROTEIN: endonuclease G, mitochondrial-like K01173 ENDOG; endonuclease G, mitochondrial
D 121316376 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 121314043 nuclease EXOG, mitochondrial-like K15050 EXOG; nuclease EXOG, mitochondrial
D 121325695 twinkle protein, mitochondrial-like K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 121321621 twinkle protein, mitochondrial-like K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 121330763 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 121318519 single-stranded DNA-binding protein, mitochondrial-like isoform X1 K03111 ssb; single-strand DNA-binding protein
D 121319579 single-stranded DNA-binding protein, mitochondrial-like isoform X1 K03111 ssb; single-strand DNA-binding protein
D 121328699 atad3; ATPase family AAA domain containing 3 isoform X1 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 121310453 ATPase family AAA domain-containing protein 3-A-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 121300224 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 121296453 dnaJ homolog subfamily A member 2-like K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 121326026 dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 121297861 mitochondrial import receptor subunit TOM34-like K17766 TOM34; mitochondrial import receptor subunit TOM34
D 121319474 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 121295750 mitochondrial Rho GTPase 1-like isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 121296300 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 121298079 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121298099 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121298556 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121309497 heat shock cognate 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121303974 heat shock cognate 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121319201 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121319202 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121319203 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121319204 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121319206 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 121307193 AH receptor-interacting protein-like K17767 AIP; AH receptor-interacting protein
D 121302110 AH receptor-interacting protein-like K17767 AIP; AH receptor-interacting protein
D 121308694 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 121317876 uncharacterized protein LOC121317876 K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 121298778 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 121304001 si:dkey-71l1.1; mitochondrial import receptor subunit TOM40B isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 121304241 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 121320530 mitochondrial import receptor subunit TOM70-like isoform X1 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 121327800 mitochondrial import receptor subunit TOM70-like isoform X1 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 121309352 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 121316083 tomm20b; mitochondrial import receptor subunit TOM20 homolog B K17770 TOM20; mitochondrial import receptor subunit TOM20
D 121317208 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 121313604 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 121304697 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 121319458 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 121318468 sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 121297542 voltage-dependent anion-selective channel protein 1-like K05862 VDAC1; voltage-dependent anion channel protein 1
D 121324665 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 121325888 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2
D 121321982 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 121302158 voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3
D 121303215 voltage-dependent anion-selective channel protein 2-like isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 121322454 metaxin-2-like isoform X1 K17776 MTX; metaxin
D 121309945 metaxin-1-like K17776 MTX; metaxin
D 121323674 metaxin-2-like K17776 MTX; metaxin
D 121305038 metaxin-3-like isoform X1 K17776 MTX; metaxin
D 121313765 metaxin-3-like isoform X1 K17776 MTX; metaxin
D 121308440 unconventional myosin-XIX K25838 MYO19; myosin XIX
D 121315953 marc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 121329480 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 121323916 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 121302281 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 121303874 mitochondrial import inner membrane translocase subunit Tim10 B-like K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
D 121304855 mitochondrial import inner membrane translocase subunit Tim10 B-like K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 121295420 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 121309417 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 121318805 mitochondrial import inner membrane translocase subunit Tim8 A-like K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 121300942 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
D 121301126 mitochondrial import inner membrane translocase subunit Tim13-like K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 121298117 mitochondrial intermembrane space import and assembly protein 40-A-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 121328741 mitochondrial intermembrane space import and assembly protein 40-A-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 121300898 FAD-linked sulfhydryl oxidase ALR-like K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
D 121330870 FAD-linked sulfhydryl oxidase ALR-like K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 121328411 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 121329108 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 121325736 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 121331025 MICOS complex subunit MIC60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 121300664 MICOS complex subunit MIC13-like K24624 MICOS13; MICOS complex subunit MIC13
D 121309575 MICOS complex subunit MIC13-like isoform X1 K24624 MICOS13; MICOS complex subunit MIC13
D 121318239 chchd3a; coiled-coil-helix-coiled-coil-helix domain containing 3a isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 121319874 MICOS complex subunit MIC19-like K17563 CHCHD3; MICOS complex subunit MIC19
D 121298287 MICOS complex subunit mic25-a-like isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 121329358 MICOS complex subunit mic25a-like isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 121302697 apooa; apolipoprotein O, a isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 121295795 MICOS complex subunit MIC27-like K24626 APOOL; MICOS complex subunit MIC27
D 121318783 apool; MICOS complex subunit MIC27 isoform X1 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 121328411 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 121329108 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 121325736 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 121331025 MICOS complex subunit MIC60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 121305046 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 121326228 mitochondrial import inner membrane translocase subunit Tim23-like isoform X1 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 121308004 mitochondrial import inner membrane translocase subunit Tim23 isoform X1 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 121299904 mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 121300048 mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 121328273 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B isoform X1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 121307779 mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 121314191 mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 121303780 mitochondrial import inner membrane translocase subunit TIM50-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
D 121304949 mitochondrial import inner membrane translocase subunit TIM50-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 121325929 calcium uniporter protein, mitochondrial-like isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial
D 121321760 calcium uniporter protein, mitochondrial-like K20858 MCU; calcium uniporter protein, mitochondrial
D 121325642 calcium uptake protein 1, mitochondrial-like isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 121321761 calcium uptake protein 1, mitochondrial-like isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 121302933 micu2; calcium uptake protein 2, mitochondrial isoform X1 K22828 MICU2; calcium uptake protein 2, mitochondrial
D 121294957 calcium uniporter protein, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 121323187 calcium uniporter protein, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 121306195 smdt1b; single-pass membrane protein with aspartate-rich tail 1b K22830 SMDT1; essential MCU regulator, mitochondrial
D 121314597 mitochondrial calcium uniporter regulator 1-like K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 121330879 mitochondrial proton/calcium exchanger protein-like isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 121325527 mitochondrial proton/calcium exchanger protein-like isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 121294293 mitochondrial inner membrane protease subunit 1-like isoform X1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 121329604 mitochondrial inner membrane protease subunit 1-like K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 121319963 immp2l; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 121320374 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 121315765 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 121320579 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
D 121328177 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
D 121296787 coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial-like isoform X1 K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
D 121299540 coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial-like K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 121301045 mitochondrial import inner membrane translocase subunit TIM44-like K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 121301477 mitochondrial import inner membrane translocase subunit TIM44-like K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 121297014 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 121324105 stress-70 protein, mitochondrial-like K04043 dnaK; molecular chaperone DnaK
D 121297372 grpE protein homolog 2, mitochondrial-like K03687 GRPE; molecular chaperone GrpE
D 121330273 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 121324830 grpE protein homolog 1, mitochondrial-like isoform X1 K03687 GRPE; molecular chaperone GrpE
D 121324951 grpE protein homolog 2, mitochondrial-like isoform X1 K03687 GRPE; molecular chaperone GrpE
D 121326767 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 121323173 mitochondrial import inner membrane translocase subunit TIM14-like K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 121301017 mitochondrial import inner membrane translocase subunit TIM16-like K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
D 121331091 mitochondrial import inner membrane translocase subunit TIM16-like isoform X1 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 121306697 mitochondrial-processing peptidase subunit alpha-like K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 121309784 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 121318370 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 121319730 mitochondrial-processing peptidase subunit beta-like K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 121302843 mipepa; mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 121322395 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 121323151 60 kDa heat shock protein, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 121301509 dnaJ homolog subfamily A member 3, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 121301646 dnaJ homolog subfamily A member 3, mitochondrial-like K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 121328356 tamm41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 121309758 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 121298709 persulfide dioxygenase ETHE1, mitochondrial-like K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 121304407 persulfide dioxygenase ETHE1, mitochondrial-like K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 121308605 poldip2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
#
AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 121322469 cyclic AMP-responsive element-binding protein 1-like isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 121323571 cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 121326674 elongation factor G, mitochondrial-like isoform X1 K02355 fusA; elongation factor G
D 121323178 elongation factor G, mitochondrial-like K02355 fusA; elongation factor G
D 121313460 ribosome-releasing factor 2, mitochondrial-like isoform X1 K02355 fusA; elongation factor G
D 121308931 sp1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1
D 121329800 transcriptional repressor protein YY1-like isoform X1 K09201 YY; transcription factor YY
D 121324272 transcriptional repressor protein YY1-like isoform X1 K09201 YY; transcription factor YY
D 121294458 GA-binding protein subunit beta-1-like isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 121299344 GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 121307014 GA-binding protein subunit beta-1-like K09454 GABPB; GA-binding protein transcription factor, beta
D 121325960 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 121322187 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 121318159 nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 121319947 nuclear respiratory factor 1-like isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 121322197 nuclear factor erythroid 2-related factor 2-like K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 121323407 nuclear factor erythroid 2-related factor 2-like K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
C Coactivators
D 121329761 peroxisome proliferator-activated receptor gamma coactivator 1-alpha-like isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 121324292 peroxisome proliferator-activated receptor gamma coactivator 1-alpha-like isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 121297292 peroxisome proliferator-activated receptor gamma coactivator 1-beta-like K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 121324455 peroxisome proliferator-activated receptor gamma coactivator 1-beta-like K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 121325771 peroxisome proliferator-activated receptor gamma coactivator-related protein 1-like isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 121321683 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 121300940 CREB-regulated transcription coactivator 1-like isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 121301448 CREB-regulated transcription coactivator 1-like isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 121300700 CREB-binding protein-like isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 121301211 CREB-binding protein-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 121331048 CREB-binding protein-like isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 121306077 LOW QUALITY PROTEIN: histone acetyltransferase p300-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 121307860 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 121297024 iron-sulfur cluster assembly scaffold protein IscU-like K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 121299660 iron-sulfur cluster assembly scaffold protein IscU-like K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 121314522 LYR motif-containing protein 4 isoform X1 K22069 LYRM4; LYR motif-containing protein 4
D 121314885 fxn; frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1]
D 121295318 adrenodoxin-like K22070 FDX1; ferredoxin-1, mitochondrial
D 121328101 fdx1; adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial
D 121309149 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 121295694 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 121297014 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 121324105 stress-70 protein, mitochondrial-like K04043 dnaK; molecular chaperone DnaK
D 121297604 hscb; iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 121308020 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 121329573 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 121324993 glutaredoxin-related protein 5, mitochondrial-like K07390 grxD; monothiol glutaredoxin
D 121299464 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 121300532 iron-sulfur cluster assembly 1 homolog, mitochondrial-like isoform X1 K22063 ISCA1; iron-sulfur cluster assembly 1
D 121301335 iron-sulfur cluster assembly 1 homolog, mitochondrial-like isoform X1 K22063 ISCA1; iron-sulfur cluster assembly 1
D 121324930 iron-sulfur cluster assembly 2 homolog, mitochondrial-like K22072 ISCA2; iron-sulfur cluster assembly 2
D 121312847 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 121314289 LOW QUALITY PROTEIN: putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 121326303 zgc:110319; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 121302443 nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 121303046 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 121309846 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 121296608 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 121326041 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 121297538 sideroflexin-1-like K23500 SFXN1_3; sideroflexin-1/3
D 121321499 sideroflexin-1-like isoform X1 K23500 SFXN1_3; sideroflexin-1/3
D 121324737 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 121325175 sideroflexin-3-like isoform X1 K23500 SFXN1_3; sideroflexin-1/3
D 121326010 sideroflexin-2-like isoform X1 K23501 SFXN2; sideroflexin-2
D 121322018 sideroflexin-2-like K23501 SFXN2; sideroflexin-2
D 121321495 sfxn4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4
D 121307125 sideroflexin-5-like isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 121294487 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 121318209 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 121329718 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 121305881 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 121319925 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 121318271 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 121316243 LOW QUALITY PROTEIN: F-box/LRR-repeat protein 4-like K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 121317370 F-box/LRR-repeat protein 4-like K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 121328966 host cell factor 1-like K14966 HCFC1; host cell factor 1
D 121305497 LOW QUALITY PROTEIN: host cell factor 1-like K14966 HCFC1; host cell factor 1
D 121318476 host cell factor 2-like K27390 HCFC2; host cell factor 2
D 121319622 host cell factor 2-like K27390 HCFC2; host cell factor 2
D 121330443 huntingtin-like isoform X1 K04533 HD; huntingtin
D 121325047 htt; huntingtin isoform X1 K04533 HD; huntingtin
D 121306335 esrra; LOW QUALITY PROTEIN: steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 121329494 steroid hormone receptor ERR2-like K08553 NR3B2; estrogen-related receptor beta
D 121324004 steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 121315974 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 121317106 esrrga; estrogen-related receptor gamma a isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 121303761 estrogen-related receptor gamma-like K08554 NR3B3; estrogen-related receptor gamma
D 121304870 esrrd; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma
D 121302672 nuclear receptor-interacting protein 1-like K17965 NRIP1; nuclear receptor-interacting protein 1
D 121299544 5'-AMP-activated protein kinase catalytic subunit alpha-1-like K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 121326929 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 121318564 5'-AMP-activated protein kinase catalytic subunit alpha-1-like K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 121331275 5'-AMP-activated protein kinase catalytic subunit alpha-2-like K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 121301396 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 121326144 NAD-dependent protein deacetylase sirtuin-1-like K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 121321631 NAD-dependent protein deacetylase sirtuin-1-like K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 121316968 serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 121305469 uxt; protein UXT isoform X1 K26537 UXT; protein UXT
D 121328143 protein UXT-like K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 121324235 complex I intermediate-associated protein 30, mitochondrial-like isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 121300787 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2-like isoform X1 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 121318106 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2-like K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 121298344 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 121315462 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 121316103 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 121314965 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 121317639 protein arginine methyltransferase NDUFAF7, mitochondrial-like K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 121307625 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 121308000 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial-like K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 121309150 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial-like K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 121298150 acad9; complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 121330063 iron-sulfur protein NUBPL-like isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 121309526 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 121316290 rtn4ip1; reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 121321080 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 121303782 sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 121294697 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 121323327 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 121314395 ttc19; tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 121302235 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 121298100 ubiquinol-cytochrome-c reductase complex assembly factor 1-like K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 121319466 ubiquinol-cytochrome-c reductase complex assembly factor 1-like isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 121300224 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 121306368 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 121329116 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 121318479 c7h12orf73; protein BRAWNIN K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 121318507 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 121319592 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 121314720 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 121312918 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 121296612 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 121314564 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 121301926 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 121321144 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 121320504 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 121318506 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 121327259 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 121295775 protoheme IX farnesyltransferase, mitochondrial-like K02257 COX10; heme o synthase [EC:2.5.1.141]
D 121296381 protoheme IX farnesyltransferase, mitochondrial-like isoform X1 K02257 COX10; heme o synthase [EC:2.5.1.141]
D 121295866 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 121296263 cytochrome c oxidase assembly protein COX11, mitochondrial-like K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 121308832 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 121321791 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 121323880 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 121320750 cytochrome c oxidase copper chaperone-like isoform X1 K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 121328123 cytochrome c oxidase copper chaperone-like isoform X1 K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 121294906 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 121300628 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 121316554 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 121300562 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 121304614 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 121315259 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 121307316 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 121309725 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 121296481 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 121319815 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 121302020 translational activator of cytochrome c oxidase 1-like K18189 TACO1; translational activator of cytochrome c oxidase 1
D 121309187 translational activator of cytochrome c oxidase 1-like K18189 TACO1; translational activator of cytochrome c oxidase 1
D 121316352 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 121316622 LOW QUALITY PROTEIN: leucine-rich PPR motif-containing protein, mitochondrial-like K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 121329594 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1
D 121318507 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 121319592 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1
D 121329116 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 121310090 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 121330924 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 121300822 ATP synthase mitochondrial F1 complex assembly factor 2-like K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 121313411 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 121329650 atp5mj; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 121325740 ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 121321730 ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 121326730 mitofusin-1-like K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 121322887 mitofusin-1-like isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 121328735 mitofusin-2 isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 121328846 mitofusin-2-like isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 121327040 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 121322844 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 121303855 opa3; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 121297186 TP53-regulated inhibitor of apoptosis 1-like K17968 TRIAP1; TRIAP1/MDM35 family protein
D 121300283 TP53-regulated inhibitor of apoptosis 1-like K17968 TRIAP1; TRIAP1/MDM35 family protein
D 121323068 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 121299910 bcl-2 homologous antagonist/killer-like K14021 BAK; Bcl-2 homologous antagonist/killer
D 121304731 bcl-2 homologous antagonist/killer-like K14021 BAK; Bcl-2 homologous antagonist/killer
D 121294441 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 121329741 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 121318603 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 121319544 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 121306589 mitochondrial fission 1 protein-like K17969 FIS1; mitochondrial fission 1 protein
D 121305588 mitochondrial fission 1 protein-like K17969 FIS1; mitochondrial fission 1 protein
D 121296447 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 121307533 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 121322075 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 121322110 small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 121323170 small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 121323632 sumo3b; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 121326875 endophilin-B1-like isoform X1 K11248 SH3GLB1; endophilin-B1
D 121331090 endophilin-B1-like isoform X1 K11248 SH3GLB1; endophilin-B1
D 121299545 mitochondrial carrier homolog 1-like K17885 MTCH; mitochondrial carrier
D 121300019 mitochondrial carrier homolog 1-like K17885 MTCH; mitochondrial carrier
D 121307639 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier
D 121329603 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier
D 121327304 mitochondrial fission factor-like isoform X1 K22076 MFF; mitochondrial fission factor
D 121323598 mitochondrial fission factor-like isoform X1 K22076 MFF; mitochondrial fission factor
D 121318749 mitochondrial fission factor-like isoform X1 K22076 MFF; mitochondrial fission factor
D 121297814 ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 121313414 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 121319237 ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 121301859 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 121324326 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 121301139 mitochondrial dynamics protein MID49-like isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 121301555 mitochondrial dynamics protein MID49-like K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 121306143 mief1; mitochondrial dynamics protein MID51 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 121306148 mitochondrial dynamics protein MID51-like K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 121310199 pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 121309739 miga2; mitoguardin 2 isoform X1 K27289 MIGA; mitoguardin
D 121326992 mitoguardin 1-like K27289 MIGA; mitoguardin
D 121331215 mitoguardin 1-like isoform X1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 121300962 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 121295310 actin, cytoplasmic type 5 K05692 ACTB_G1; actin beta/gamma 1
D 121296069 actin, cytoplasmic type 5 K05692 ACTB_G1; actin beta/gamma 1
D 121294181 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 121315420 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 121317625 N-alpha-acetyltransferase 20 isoform X1 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 121297036 uncharacterized protein LOC121297036 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
D 121300242 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
D 121307761 N-alpha-acetyltransferase 25, NatB auxiliary subunit-like K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 121301937 phb; prohibitin isoform X1 K17080 PHB1; prohibitin 1
D 121324554 prohibitin isoform X1 K17080 PHB1; prohibitin 1
D 121327131 prohibitin-2-like K17081 PHB2; prohibitin 2
D 121323406 prohibitin-2-like K17081 PHB2; prohibitin 2
D 121329783 kinectin-like isoform X1 K17975 KTN1; kinectin
D 121324144 kinectin-like isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 121318603 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 121319544 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 121294510 unconventional myosin-Va-like isoform X1 K10357 MYO5; myosin V
D 121300934 si:dkey-110c1.10; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 121299021 unconventional myosin-Va-like isoform X1 K10357 MYO5; myosin V
D 121299278 unconventional myosin-Vc-like isoform X1 K10357 MYO5; myosin V
D 121294300 unconventional myosin-Vc-like K10357 MYO5; myosin V
D 121317735 myo5b; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 121295567 E3 ubiquitin-protein ligase XIAP-like K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 121318906 E3 ubiquitin-protein ligase XIAP-like K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 121320434 diablo homolog, mitochondrial-like isoform X1 K10522 DIABLO; diablo
D 121327611 diablo homolog, mitochondrial-like isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 121297615 sorting nexin-25-like isoform X1 K17887 SNX25; sorting nexin-25
D 121320432 sorting nexin-25-like isoform X1 K17887 SNX25; sorting nexin-25
D 121295750 mitochondrial Rho GTPase 1-like isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 121296300 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 121325736 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 121331025 MICOS complex subunit MIC60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 121297033 mitochondrial fission process protein 1-like K17981 MTFP1; mitochondrial fission process protein 1
D 121300143 mitochondrial fission process protein 1-like K17981 MTFP1; mitochondrial fission process protein 1
D 121319819 plexin-C1-like K17981 MTFP1; mitochondrial fission process protein 1
D 121306892 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 121294702 E3 ubiquitin-protein ligase NEDD4-like isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 121299165 E3 ubiquitin-protein ligase NEDD4-like isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 121313265 oxr1a; oxidation resistance protein 1a isoform X1 K25437 OXR1; oxidation resistance protein 1
D 121314919 oxidation resistance protein 1-like isoform X1 K25437 OXR1; oxidation resistance protein 1
D 121309937 msto1; protein misato homolog 1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 121306285 atg2a; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 121329559 autophagy-related protein 2 homolog B-like isoform X1 K17906 ATG2; autophagy-related protein 2
D 121324195 autophagy-related protein 2 homolog B-like isoform X1 K17906 ATG2; autophagy-related protein 2
D 121320587 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 121328082 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 121295527 cysteine protease ATG4A-like isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 121327119 atg4c; cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 121327269 cysteine protease ATG4B-like isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 121309158 atg4da; cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 121323221 atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 121318665 cysteine protease ATG4A-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 121331264 cysteine protease ATG4C-like isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 121316273 autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 121317400 autophagy protein 5-like K08339 ATG5; autophagy-related protein 5
D 121301920 becn1; beclin-1 K08334 BECN; beclin
D 121329014 atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 121296099 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 121296133 gamma-aminobutyric acid receptor-associated protein-like K08341 GABARAP; GABA(A) receptor-associated protein
D 121296515 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 121306598 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 121326012 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 121305680 gamma-aminobutyric acid receptor-associated protein-like K08341 GABARAP; GABA(A) receptor-associated protein
D 121325389 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 121325390 gamma-aminobutyric acid receptor-associated protein-like K08341 GABARAP; GABA(A) receptor-associated protein
D 121322077 autophagy-related protein 9A-like isoform X1 K17907 ATG9; autophagy-related protein 9
D 121322842 autophagy-related protein 9A-like isoform X1 K17907 ATG9; autophagy-related protein 9
D 121312833 atg9b; autophagy-related protein 9B isoform X1 K17907 ATG9; autophagy-related protein 9
D 121314318 autophagy-related protein 9A-like isoform X1 K17907 ATG9; autophagy-related protein 9
D 121312859 atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 121302342 atg12; ubiquitin-like protein ATG12 isoform X1 K08336 ATG12; ubiquitin-like protein ATG12
D 121329825 beclin 1-associated autophagy-related key regulator-like K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 121325048 beclin 1-associated autophagy-related key regulator-like K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 121326659 autophagy-related protein 16-1-like isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 121323000 autophagy-related protein 16-1-like isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 121320366 protein Atg16l2-like isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 121320608 protein Atg16l2-like isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 121295530 wipi1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 121307557 WD repeat domain phosphoinositide-interacting protein 1-like isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 121301405 WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
D 121330846 WD repeat domain phosphoinositide-interacting protein 2-like isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 121315872 vacuolar protein 8-like K08332 VAC8; vacuolar protein 8
C Parkin-dependent mechanism factors
D 121316301 prkn; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31]
D 121308812 rnf41; E3 ubiquitin-protein ligase NRDP1 isoform X1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 121300845 protein CLEC16A-like isoform X1 K19513 CLEC16A; protein CLEC16A
D 121330816 protein CLEC16A-like isoform X1 K19513 CLEC16A; protein CLEC16A
D 121329075 serine/threonine-protein kinase PINK1, mitochondrial-like K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 121329247 serine/threonine-protein kinase PINK1, mitochondrial-like K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 121323068 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 121297301 sqstm1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1
D 121324864 sequestosome-1-like K14381 SQSTM1; sequestosome 1
D 121315115 tax1bp1b; tax1-binding protein 1 homolog B K21347 TAX1BP1; Tax1-binding protein 1
D 121313638 tax1-binding protein 1 homolog B-like isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 121302022 calcium-binding and coiled-coil domain-containing protein 2-like isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 121324289 calcium-binding and coiled-coil domain-containing protein 2-like K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 121294603 activating molecule in BECN1-regulated autophagy protein 1-like isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
D 121330411 activating molecule in BECN1-regulated autophagy protein 1-like isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 121295107 autophagy-related protein 13-like isoform X1 K08331 ATG13; autophagy-related protein 13
D 121330019 autophagy-related protein 13-like isoform X1 K08331 ATG13; autophagy-related protein 13
D 121297148 serine/threonine-protein kinase ULK1-like isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 121307708 serine/threonine-protein kinase ULK1-like K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 121300031 serine/threonine-protein kinase ULK1-like K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 121308596 ulk2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 121313433 RB1-inducible coiled-coil protein 1-like K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 121314374 rb1cc1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 121315981 heat shock protein HSP 90-beta isoform X1 K04079 HSP90A; molecular chaperone HtpG
D 121317110 heat shock protein HSP 90-beta-like K04079 HSP90A; molecular chaperone HtpG
D 121329610 heat shock protein HSP 90-alpha 1-like K04079 HSP90A; molecular chaperone HtpG
D 121324147 heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG
D 121324184 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 121309137 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 121300858 LOW QUALITY PROTEIN: E3 ubiquitin-protein ligase SMURF1-like K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 121295547 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 121296358 E3 ubiquitin-protein ligase SMURF2-like isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 121330930 E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 121302311 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 121303234 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 121320591 fundc1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
D 121327561 FUN14 domain-containing protein 1-like isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 121299544 5'-AMP-activated protein kinase catalytic subunit alpha-1-like K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 121326929 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 121318564 5'-AMP-activated protein kinase catalytic subunit alpha-1-like K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 121331275 5'-AMP-activated protein kinase catalytic subunit alpha-2-like K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 121296354 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 121297854 microtubule-associated proteins 1A/1B light chain 3A-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 121325938 microtubule-associated proteins 1A/1B light chain 3B isoform X1 K10435 MAP1LC; microtubule-associated protein 1 light chain
D 121315306 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 121316557 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 121319430 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 121301911 nbr1b; next to BRCA1 gene 1 protein K17987 NBR1; next to BRCA1 gene 1 protein
D 121324454 nbr1a; NBR1 autophagy cargo receptor a isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 121300442 tecpr1a; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 121331159 tectonin beta-propeller repeat-containing protein 1-like K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 121303813 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 121330198 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 121324529 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 121304987 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 121302015 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 121306129 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 121296344 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 121325243 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 121295602 FUN14 domain-containing protein 1-like isoform X1 K24308 FUNDC2; FUN14 domain-containing protein 2
D 121318644 FUN14 domain-containing protein 1-like K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024