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Mitochondrial Biogenesis - Rhinopithecus bieti (black snub-nosed monkey)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 10549380 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 10549368 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 10549374 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 10549376 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 10549375 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 10549377 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 10549378 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 10549379 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 10549369 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 10549370 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 10549373 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 10549371 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 10549372 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 108537883 POLRMT; DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 108540737 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 108520437 LOW QUALITY PROTEIN: transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 108542148 TFB1M; dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 108532482 TFB2M; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 108512925 MTIF3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 108524404 elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts
D 108519904 LOW QUALITY PROTEIN: elongation factor Tu, mitochondrial-like K02358 tuf; elongation factor Tu
D 108523669 TUFM; LOW QUALITY PROTEIN: elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 108541107 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 108541143 GFM2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 108539512 MTERF2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 108544029 MTERF1; transcription termination factor 1, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 108521086 MTERF4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 108531702 MTERF3; transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 108515165 GUF1; LOW QUALITY PROTEIN: translation factor GUF1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 108531715 POP1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 108530607 POP4; ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 108529653 POP5; ribonuclease P/MRP protein subunit POP5 isoform X1 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 108544920 RPP30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 108538196 POP7; ribonuclease P protein subunit p20 isoform X1 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 108542162 RPP25L; ribonuclease P protein subunit p25-like protein isoform X1 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 108531484 RPP25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 108530969 RPP38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 108514274 RPP40; ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 108527951 TRMT10C; mitochondrial ribonuclease P protein 1 K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 108520302 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 108519586 KIAA0391; mitochondrial ribonuclease P protein 3 isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 108516855 MSS51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 108541399 TEFM; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 108538142 PTCD1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 108541152 PTCD2; LOW QUALITY PROTEIN: pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 108518116 PTCD3; pentatricopeptide repeat domain-containing protein 3, mitochondrial isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 108517637 DHX30; putative ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 108538505 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 108533815 LACE1; LOW QUALITY PROTEIN: lactation elevated protein 1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 108524408 ATP23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 108531509 ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 108530077 LACTB2; beta-lactamase-like protein 2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 108515615 ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 108529787 ADP/ATP translocase 3-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 108520942 SLC25A6; ADP/ATP translocase 3 isoform X1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 108535888 LOW QUALITY PROTEIN: calcium-binding mitochondrial carrier SAL1-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 108538574 SLC25A31; ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 108518758 ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 108512004 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 108537890 SLC25A37; mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 108534970 SLC25A28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 108529779 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 108517279 ERAL1; GTPase Era, mitochondrial K03595 era; GTPase
D 108537228 YARS; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 108538533 YARS2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 108513758 LARS2; probable leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 108529648 LARS; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 108526273 DARS2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 108533231 GARS; LOW QUALITY PROTEIN: glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 108522369 RARS2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 108513602 RARS; LOW QUALITY PROTEIN: arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 108533693 QRSL1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 108529053 GATB; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 108529659 GATC; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 108528091 MTPAP; LOW QUALITY PROTEIN: poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 108543590 PDE12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 108543376 MTG1; mitochondrial ribosome-associated GTPase 1 isoform X1 K19828 MTG1; mitochondrial GTPase 1
D 108513478 NOA1; nitric oxide-associated protein 1 isoform X1 K19832 NOA1; nitric oxide-associated protein 1
D 108517288 NSUN3; putative methyltransferase NSUN3 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 108535598 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 108534813 RPUSD3; RNA pseudouridylate synthase domain-containing protein 3 isoform X1 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 108542310 RPUSD4; RNA pseudouridylate synthase domain-containing protein 4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 108513919 RCC1L; Williams-Beuren syndrome chromosomal region 16 protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 108521401 NGRN; neugrin K23496 NGRN; neugrin
D 108512784 TRUB2; probable tRNA pseudouridine synthase 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 108543440 FASTKD2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 108540816 CUNH12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor
D 108539133 RMND1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 108534043 GRSF1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1
D 108516990 LOW QUALITY PROTEIN: probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 108521593 CUNH12orf10; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 108533699 CUNH6orf203; uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 108540902 POLG; DNA polymerase subunit gamma-1 isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 108536252 POLG2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 108515614 PRIMPOL; LOW QUALITY PROTEIN: DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 108512788 ENDOG; LOW QUALITY PROTEIN: endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 108544409 MGME1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 108513783 EXOG; nuclease EXOG, mitochondrial isoform X1 K15050 EXOG; nuclease EXOG, mitochondrial
D 108515144 CUNH10orf2; twinkle protein, mitochondrial isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 108537544 PIF1; ATP-dependent DNA helicase PIF1 isoform X1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 108541548 SSBP1; single-stranded DNA-binding protein, mitochondrial isoform X1 K03111 ssb; single-strand DNA-binding protein
D 108536045 ATAD3A; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 108515785 LOW QUALITY PROTEIN: ATPase family AAA domain-containing protein 3C-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 108520194 ATPase family AAA domain-containing protein 3C-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 108523195 ATPase family AAA domain-containing protein 3C-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 108516256 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 108534777 DNAJA2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 108533370 TOMM34; mitochondrial import receptor subunit TOM34 isoform X1 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 108541403 RHOT1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 108520227 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 108520228 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 108531954 HSPA8; LOW QUALITY PROTEIN: heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 108528791 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 108542584 HSPA6; LOW QUALITY PROTEIN: heat shock 70 kDa protein 6 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 108514347 AIPL1; aryl-hydrocarbon-interacting protein-like 1 isoform X1 K17767 AIP; AH receptor-interacting protein
D 108518685 AIP; AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 108521188 TOMM40L; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 108531118 TOMM40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 108542075 TOMM70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 108525623 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 108530497 TOMM22; mitochondrial import receptor subunit TOM22 homolog isoform X1 K17769 TOM22; mitochondrial import receptor subunit TOM22
D 108522209 TOMM20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 108529717 TOMM20L; TOMM20-like protein 1 isoform X1 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 108529328 TOMM7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 108533506 TOMM6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 108543046 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
D 108516202 TOMM5; LOW QUALITY PROTEIN: mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 108514005 SAMM50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 108529563 VDAC1; voltage-dependent anion-selective channel protein 1 isoform X1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 108529513 VDAC2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 108540717 VDAC3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 108526836 LOW QUALITY PROTEIN: metaxin-1-like K17776 MTX; metaxin
D 108527144 MTX2; metaxin-2 K17776 MTX; metaxin
D 108528907 MTX3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 108524874 LOW QUALITY PROTEIN: metaxin-1-like K17776 MTX; metaxin
D 108526288 MYO19; LOW QUALITY PROTEIN: unconventional myosin-XIX K25838 MYO19; myosin XIX
D 108517308 ARMCX1; armadillo repeat-containing X-linked protein 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1
D 108526605 ARMCX2; armadillo repeat-containing X-linked protein 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2
D 108526603 ARMCX3; armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3
D 108526602 ARMCX6; protein ARMCX6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6
D 108528267 MARC1; mitochondrial amidoxime-reducing component 1 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 108528269 MARC2; mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 108529720 TIMM9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 108514863 TIMM10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 108543242 TIMM10B; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 108544994 TIMM8A; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 108527892 mitochondrial import inner membrane translocase subunit Tim8 B-like K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 108524011 mitochondrial import inner membrane translocase subunit Tim8 A-like K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 108518155 mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 108531450 TIMM13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
D 108532131 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 108544862 CHCHD4; mitochondrial intermembrane space import and assembly protein 40 isoform X1 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 108519412 GFER; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 108515271 MINOS1; MICOS complex subunit MIC10 isoform X1 K17784 MICOS10; MICOS complex subunit MIC10
D 108518118 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 108512099 CUNH19orf70; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 108537534 CHCHD3; MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 108528201 CHCHD6; MICOS complex subunit MIC25 isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 108544220 MICOS complex subunit MIC26-like K24625 APOO; MICOS complex subunit MIC26
D 108516921 MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 108515271 MINOS1; MICOS complex subunit MIC10 isoform X1 K17784 MICOS10; MICOS complex subunit MIC10
D 108518118 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
C TIM23 complex
D 108520452 TIMM23; LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 108513101 mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 108540596 LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit Tim17-B-like K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 108545057 TIMM17A; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 108520420 mitochondrial import inner membrane translocase subunit Tim17-B-like K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 108525056 TIMM21; LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 108539081 TIMM50; LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 108516879 MCU; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 108516892 MICU1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 108538287 MICU2; calcium uptake protein 2, mitochondrial isoform X1 K22828 MICU2; calcium uptake protein 2, mitochondrial
D 108541014 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial isoform X1 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 108543565 SMDT1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 108541610 MCUR1; mitochondrial calcium uniporter regulator 1 isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 108532287 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 108537967 IMMP1L; LOW QUALITY PROTEIN: mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 108533771 IMMP2L; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 108514585 TMEM126A; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 108535822 MPC1L; mitochondrial pyruvate carrier 1-like protein K22138 MPC1; mitochondrial pyruvate carrier 1
D 108527971 MPC1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 108526737 MPC2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 108534846 mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 108540429 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 108534519 TIMM44; mitochondrial import inner membrane translocase subunit TIM44 isoform X1 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 108541693 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 108532065 GRPEL2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 108516086 GRPEL1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 108532761 DNAJC19; mitochondrial import inner membrane translocase subunit TIM14 isoform X1 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 108538298 PAM16; mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 108542881 PMPCA; mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 108515653 PMPCB; mitochondrial-processing peptidase subunit beta isoform X1 K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 108531177 MIPEP; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 108527810 HSPD1; LOW QUALITY PROTEIN: 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 108525048 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 108535226 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 108527833 HSPE1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 108538295 DNAJA3; dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 108519329 TAMM41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 108542904 DNLZ; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 108538048 ETHE1; persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 108539952 POLDIP2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
#
AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 108540349 CREB1; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 108541107 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 108541143 GFM2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 108521535 SP1; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 108525337 transcriptional repressor protein YY1-like K09201 YY; transcription factor YY
D 108531648 YY2; transcription factor YY2 K09201 YY; transcription factor YY
D 108542287 YY1; LOW QUALITY PROTEIN: transcriptional repressor protein YY1 K09201 YY; transcription factor YY
D 108544832 GABPB1; GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 108533248 GABPB2; GA-binding protein subunit beta-2 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 108540737 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 108520437 LOW QUALITY PROTEIN: transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 108531576 NRF1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1
D 108527136 NFE2L2; LOW QUALITY PROTEIN: nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 108522302 metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 108533846 MT2A; metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 108533848 metallothionein-1E K14739 MT1_2; metallothionein 1/2
D 108533849 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 108533851 metallothionein-1F-like isoform X1 K14739 MT1_2; metallothionein 1/2
D 108533852 metallothionein-1-like K14739 MT1_2; metallothionein 1/2
D 108533853 metallothionein-1F-like K14739 MT1_2; metallothionein 1/2
D 108533854 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 108533855 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 108533857 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2
D 108533858 metallothionein-1L-like isoform X1 K14739 MT1_2; metallothionein 1/2
D 108533860 metallothionein-like K14739 MT1_2; metallothionein 1/2
D 108533861 metallothionein-1X K14739 MT1_2; metallothionein 1/2
D 108533921 MT3; metallothionein-3 K14740 MT3; metallothionein 3
D 108533925 MT4; metallothionein-4 K14741 MT4; metallothionein 4
C Coactivators
D 108526071 PPARGC1A; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 108532052 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 108515139 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 108515626 CRTC1; LOW QUALITY PROTEIN: CREB-regulated transcription coactivator 1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 108538320 CREBBP; LOW QUALITY PROTEIN: CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 108528445 EP300; LOW QUALITY PROTEIN: histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 108538490 NFS1; cysteine desulfurase, mitochondrial isoform X1 K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 108534397 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 108537026 LYRM4; LYR motif-containing protein 4 isoform X1 K22069 LYRM4; LYR motif-containing protein 4
D 108530269 FXN; frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1]
D 108536467 FDX1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 108517814 FDX1L; adrenodoxin-like protein, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 108537405 FDXR; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 108541693 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 108517556 HSCB; iron-sulfur cluster co-chaperone protein HscB, mitochondrial isoform X1 K04082 hscB; molecular chaperone HscB
D 108541686 SIL1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 108535001 LOW QUALITY PROTEIN: glutaredoxin-related protein 5, mitochondrial-like K07390 grxD; monothiol glutaredoxin
D 108544358 iron-sulfur cluster assembly 1 homolog, mitochondrial-like isoform X1 K22063 ISCA1; iron-sulfur cluster assembly 1
D 108520510 ISCA1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 108534911 ISCA2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 108536796 IBA57; putative transferase CAF17, mitochondrial isoform X1 K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 108513111 LOW QUALITY PROTEIN: NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 108516325 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 108533286 BOLA1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 108517131 BOLA3; bolA-like protein 3 isoform X1 K22075 BOLA3; BolA-like protein 3
D 108515118 SFXN3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 108523471 SFXN1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 108515084 SFXN2; sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2
D 108513854 SFXN4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4
D 108532567 SFXN5; sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 108538087 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 108539398 carnitine O-palmitoyltransferase 1, muscle isoform-like K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 108535821 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform isoform X1 K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
D 108538522 DHTKD1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 108540691 FBXL4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 108535066 HCFC1; host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1
D 108544246 HCFC2; host cell factor 2 K27390 HCFC2; host cell factor 2
D 108522748 HTT; huntingtin isoform X1 K04533 HD; huntingtin
D 108542761 ESRRA; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 108534943 ESRRB; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 108528287 ESRRG; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 108515498 NRIP1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 108544746 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108532936 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108512096 LONP1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 108514897 SIRT1; LOW QUALITY PROTEIN: NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 108540552 SERAC1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 108530926 UXT; protein UXT K26537 UXT; protein UXT
D 108516795 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 isoform X1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 108544343 NDUFAF1; complex I intermediate-associated protein 30, mitochondrial isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 108515469 NDUFAF2; LOW QUALITY PROTEIN: mimitin, mitochondrial K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 108527009 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 isoform X1 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 108538595 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 108527878 NDUFAF5; LOW QUALITY PROTEIN: NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 108539881 NDUFAF6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 108520880 NDUFAF7; NADH dehydrogenase [ubiquinone] complex I, assembly factor 7 isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 108534128 NDUFAF8; uncharacterized protein C17orf89 homolog isoform X1 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 108514592 TMEM126B; complex I assembly factor TMEM126B, mitochondrial isoform X1 K18165 TMEM126B; complex I assembly factor TMEM126B
D 108527911 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 108537519 ACAD9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 108544686 NUBPL; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 108542309 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 108533694 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 108531840 TIMMDC1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 108513061 SDHAF1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 108533613 SDHAF2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 108518458 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 108522163 TTC19; tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 108524252 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 108512574 complex III assembly factor LYRM7-like isoform X1 K18170 LYRM7; complex III assembly factor LYRM7
D 108538505 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 108516256 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 108533577 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 108519425 CUNH16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 108522331 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 108544253 CUNH12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 108539194 CUNH7orf73; uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1
D 108537200 uncharacterized protein C7orf73 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 108527296 CMC1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 108539490 CMC2; LOW QUALITY PROTEIN: COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 108544018 cytochrome c oxidase assembly factor 1 homolog isoform X1 K18173 COA1; cytochrome c oxidase assembly factor 1
D 108526774 cytochrome c oxidase assembly factor 3 homolog, mitochondrial isoform X1 K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 108537835 LOW QUALITY PROTEIN: cytochrome c oxidase assembly factor 3 homolog, mitochondrial-like K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 108537641 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 108526108 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 108529488 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 108518980 cytochrome c oxidase assembly factor 6 homolog isoform X1 K18179 COA6; cytochrome c oxidase assembly factor 6
D 108531235 cytochrome c oxidase assembly factor 7 isoform X1 K18180 COA7; cytochrome c oxidase assembly factor 7
D 108542393 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 108515738 cytochrome c oxidase assembly protein COX11, mitochondrial isoform X1 K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 108543925 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 108535008 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 108536198 LOW QUALITY PROTEIN: cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 108541849 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 108523443 mitochondrial inner membrane protein COX18 isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18
D 108542320 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 108528552 cytochrome c oxidase protein 20 homolog isoform X1 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 108516855 MSS51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 108534540 PET100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 108544415 PET117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 108523577 OXA1L; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 108513405 SURF1; surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 108520320 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 108539417 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 108536282 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 108522501 LRPPRC; LOW QUALITY PROTEIN: leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 108514967 APOPT1; LOW QUALITY PROTEIN: apoptogenic protein 1, mitochondrial K23506 APOPT1; apoptogenic protein 1
D 108519333 apoptogenic protein 1, mitochondrial K23506 APOPT1; apoptogenic protein 1
D 108539194 CUNH7orf73; uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1
D 108537200 uncharacterized protein C7orf73 K27319 STMP1; short transmembrane mitochondrial protein 1
D 108522331 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 108533566 TMEM223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 108535623 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 108544484 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 108515046 TMEM70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 108523159 LOW QUALITY PROTEIN: 6.8 kDa mitochondrial proteolipid-like K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 108520183 LOW QUALITY PROTEIN: 6.8 kDa mitochondrial proteolipid-like K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 108521891 CUNH14orf2; 6.8 kDa mitochondrial proteolipid isoform X1 K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 108515126 USMG5; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 108531558 up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 108532919 MFN1; LOW QUALITY PROTEIN: mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 108539352 MFN2; mitofusin-2 isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 108530499 OPA1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 108531095 OPA3; optic atrophy 3 protein isoform X1 K23166 OPA3; optic atrophy 3 protein
D 108529660 TRIAP1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 108521059 PARL; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 108516259 BAK1; bcl-2 homologous antagonist/killer K14021 BAK; Bcl-2 homologous antagonist/killer
D 108523624 BAX; apoptosis regulator BAX isoform X1 K02159 BAX; apoptosis regulator BAX
D 108538193 DNM1L; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 108518935 FIS1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 108526127 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 108536674 SUMO4; small ubiquitin-related modifier 4 K12160 SUMO; small ubiquitin-related modifier
D 108537442 SUMO2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 108539833 SUMO3; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 108530986 small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 108514499 SH3GLB1; endophilin-B1 K11248 SH3GLB1; endophilin-B1
D 108528343 MTCH1; mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier
D 108524656 MTCH2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 108538740 MFF; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor
D 108538023 GDAP1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 108533385 GDAP1L1; ganglioside-induced differentiation-associated protein 1-like 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 108526783 VAT1; synaptic vesicle membrane protein VAT-1 homolog isoform X1 K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 108516630 MIEF2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 108520462 MIEF1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 108544474 PLD6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 108533034 MIGA1; mitoguardin-1 K27289 MIGA; mitoguardin
D 108512827 MIGA2; mitoguardin-2 isoform X1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 108534125 ACTG1; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 108538237 ACTB; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 108536493 NAA20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 108512115 NAA25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 108541432 LOW QUALITY PROTEIN: prohibitin-like K17080 PHB1; prohibitin 1
D 108534534 prohibitin-like K17080 PHB1; prohibitin 1
D 108516483 PHB; prohibitin K17080 PHB1; prohibitin 1
D 108542027 PHB2; prohibitin-2 K17081 PHB2; prohibitin 2
D 108530672 KTN1; LOW QUALITY PROTEIN: kinectin K17975 KTN1; kinectin
C Retention of mitochondria
D 108538193 DNM1L; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 108538118 MYO5A; LOW QUALITY PROTEIN: unconventional myosin-Va K10357 MYO5; myosin V
D 108538177 MYO5C; unconventional myosin-Vc K10357 MYO5; myosin V
D 108539751 MYO5B; LOW QUALITY PROTEIN: unconventional myosin-Vb K10357 MYO5; myosin V
D 108541060 DIABLO; diablo homolog, mitochondrial isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 108515619 sorting nexin-25-like isoform X1 K17887 SNX25; sorting nexin-25
D 108522423 sorting nexin-25 K17887 SNX25; sorting nexin-25
D 108541403 RHOT1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 108518118 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 108517582 MTFP1; mitochondrial fission process protein 1 isoform X1 K17981 MTFP1; mitochondrial fission process protein 1
D 108524500 DAP3; LOW QUALITY PROTEIN: 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 108535312 NEDD4; E3 ubiquitin-protein ligase NEDD4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 108537578 oxidation resistance protein 1-like K25437 OXR1; oxidation resistance protein 1
D 108526853 MSTO1; protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 108519131 ATG2B; LOW QUALITY PROTEIN: autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2
D 108543000 ATG2A; autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 108519505 ATG3; ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 108532903 ATG4C; LOW QUALITY PROTEIN: cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 108534855 ATG4A; cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 108539978 ATG4D; cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 108528709 ATG4B; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 108533692 ATG5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 108526772 BECN1; beclin-1 isoform X1 K08334 BECN; beclin
D 108512516 BECN2; beclin-2 K08334 BECN; beclin
D 108519325 ATG7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 108514304 GABARAP; gamma-aminobutyric acid receptor-associated protein isoform X1 K08341 GABARAP; GABA(A) receptor-associated protein
D 108527415 GABARAPL2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 108545090 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 108542138 GABARAPL1; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 108517211 gamma-aminobutyric acid receptor-associated protein-like 3 K08341 GABARAP; GABA(A) receptor-associated protein
D 108518416 ATG9A; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 108532526 ATG9B; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 108542268 ATG10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 108540013 ATG12; LOW QUALITY PROTEIN: ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 108530670 ATG14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 108520100 ATG16L1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 108543745 ATG16L2; autophagy-related protein 16-2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 108530419 WIPI2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 108523042 WIPI1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 108527984 PARK2; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31]
D 108516011 RNF41; E3 ubiquitin-protein ligase NRDP1 isoform X1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 108541218 CLEC16A; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 108515300 PINK1; serine/threonine-protein kinase PINK1, mitochondrial isoform X1 K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 108521059 PARL; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 108523366 SQSTM1; sequestosome-1 K14381 SQSTM1; sequestosome 1
D 108535457 TAX1BP1; tax1-binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1
D 108516482 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
C Parkin-independent mechanism factors
D 108521955 ATG13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 108527503 ULK1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 108521945 ULK2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 108540897 serine/threonine-protein kinase ULK2-like K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 108526927 RB1CC1; LOW QUALITY PROTEIN: RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 108542298 HSP90AA1; LOW QUALITY PROTEIN: heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 108533442 HSP90AB1; LOW QUALITY PROTEIN: heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 108537061 LOW QUALITY PROTEIN: heat shock protein HSP 90-alpha-like K04079 HSP90A; molecular chaperone HtpG
D 108517810 CDC37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 108523576 SMURF1; E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 108536248 SMURF2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 108537689 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 108527458 FUNDC1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
D 108529105 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 108544746 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108532936 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108520768 MAP1LC3B; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 108512512 MAP1LC3C; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 108533773 MAP1LC3A; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 108526766 NBR1; next to BRCA1 gene 1 protein K17987 NBR1; next to BRCA1 gene 1 protein
D 108521682 TECPR1; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 108536212 ZFYVE1; zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 108518329 COASY; bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 108521470 PLA2G6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 108530609 CUNH19orf12; protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN
D 108530675 FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024