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  Mitochondrial Biogenesis - Tachysurus fulvidraco (yellow catfish)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I C Mitochondrial respiratory chain complex III C Cytochrome c oxidase C F-type ATPase B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 113657756 polrmt; DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 113649389 tfam; transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 113649341 tfb1m; dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 113638538 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 113660171 mtif2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2 D 113650893 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3 D 113651652 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 113650548 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 113634612 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 113663350 gfm2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G D 113640679 mterf4; transcription termination factor 4, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 113652295 mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 113656392 transcription termination factor 1b, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 113661398 mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 113635788 guf1; translation factor Guf1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 113662376 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 113651438 pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 113663935 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 113662566 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 113654687 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 113650804 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 113651672 rpp25l; ribonuclease P protein subunit p25-like protein isoform X2 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 113658714 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 113653728 rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 113648669 trmt10c; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 113642024 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 isoform X1 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 113635364 prorp; mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 113649780 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 113649782 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 113656878 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 113640599 ptcd1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 113656688 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 113647725 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial isoform X2 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 113662249 dhx30; ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 113643096 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 113643372 afg1lb; lactation elevated protein 1 homolog B isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 113659838 afg1la; AFG1 like ATPase a isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 113647275 atp23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 113661052 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 113637323 lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 113634424 ADP/ATP translocase 2-like isoform X1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 113635425 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 113636107 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 113650877 si:dkey-251i10.1; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 113654404 slc25a6; ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 113639851 slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 113646480 slc25a37; mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 113648020 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 113634189 eral1; GTPase Era, mitochondrial K03595 era; GTPase D 113639140 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 113661672 yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 113644762 lars2; probable leucine--tRNA ligase, mitochondrial isoform X2 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 113647552 lars1b; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 113634120 dars2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 113660963 gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 113653909 rars1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 113661166 rars2; probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 113641427 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 113649931 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 113638646 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial-like K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 113639255 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial-like K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 113662602 poly(A) RNA polymerase, mitochondrial isoform X1 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 113656477 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 113660965 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 113637504 noa1; LOW QUALITY PROTEIN: nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 113652323 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 113650159 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 113661857 rpusd4; mitochondrial RNA pseudouridine synthase rpusd4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 113663407 rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 113655913 ngrn; neugrin isoform X1 K23496 NGRN; neugrin D 113642767 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 113654276 fastkd1; FAST kinase domain-containing protein 1, mitochondrial isoform X1 K27754 FASTKD1; FAST kinase domain-containing protein 1 D 113661920 fastkd2; FAST kinase domain-containing protein 2, mitochondrial isoform X1 K18190 FASTKD2; FAST kinase domain-containing protein 2 D 113657377 fastkd3; FAST kinase domain-containing protein 3, mitochondrial K27755 FASTKD3; FAST kinase domain-containing protein 3 D 113659202 tbrg4; FAST kinase domain-containing protein 4 K27756 TBRG4; FAST kinase domain-containing protein 4 D 113636524 FAST kinase domain-containing protein 5, mitochondrial K27757 FASTKD5; FAST kinase domain-containing protein 5 D 113648150 mtrfr; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor D 113659763 rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 113637647 grsf1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1 D 113636811 mettl15; probable methyltransferase-like protein 15 isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 113655070 myg1; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 113655766 mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 113660106 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 113634525 polg2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2 D 113635527 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 113634267 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 113644927 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 113644186 nuclease EXOG, mitochondrial isoform X1 K15050 EXOG; nuclease EXOG, mitochondrial D 113638887 twnk; twinkle protein, mitochondrial isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3] D 113650158 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 113645890 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 125140755 atad3; ATPase family AAA domain containing 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 113642829 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 113638994 si:dkey-21c1.4; uncharacterized protein si:dkey-21c1.4 K27759 MTNAP1; mitochondrial nucleoid-associated protein 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 113657286 dnaja2b; dnaJ homolog subfamily A member 2b K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 113660630 dnaja2a; dnaJ homolog subfamily A member 2a K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 113643095 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 113643995 rhot1a; mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 113656857 rhot1b; mitochondrial Rho GTPase 1b K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 113643689 hsc70; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 113645341 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 113645389 hspa8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 113652206 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 113652235 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 113652236 heat shock 70 kDa protein-like isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 113660461 hspa8b; heat shock protein family A (Hsp70) member 8b K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 125138828 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 125138829 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 113635873 aryl-hydrocarbon-interacting protein-like 1 isoform X1 K17767 AIP; AH receptor-interacting protein D 113642570 aipl1; aryl-hydrocarbon-interacting protein-like 1 isoform X2 K17767 AIP; AH receptor-interacting protein D 113649314 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein D 113662414 mitochondrial fission factor-like isoform X1 K28235 FATE1; fetal and adult testis-expressed transcript protein B Outer membrane C Transporter outer membrane (TOM) complex D 113641216 tomm40l; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40 D 113647461 tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 113663412 si:dkey-71l1.1; mitochondrial import receptor subunit TOM40B isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 113642949 tomm70a; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 113637079 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 113653254 tomm20b; mitochondrial import receptor subunit TOM20 homolog B K17770 TOM20; mitochondrial import receptor subunit TOM20 D 113661641 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 113642832 tomm6; mitochondrial import receptor subunit TOM6 homolog isoform X1 K17772 TOM6; mitochondrial import receptor subunit TOM6 D 113652951 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 113635598 samm50; sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family D 113645753 samm50l; sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family C Porin D 113634812 voltage-dependent anion-selective channel protein 2-like isoform X1 K15040 VDAC2; voltage-dependent anion channel protein 2 D 113639914 vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 113638373 voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3 D 113638426 voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 113637727 mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin D 113644828 mtx1a; metaxin-1a isoform X1 K17776 MTX; metaxin D 113651015 mtx2; metaxin-2 K17776 MTX; metaxin D 113662760 mtx1b; metaxin-1b isoform X1 K17776 MTX; metaxin D 113634137 unconventional myosin-XIX K25838 MYO19; myosin XIX D 113659839 marc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 113659683 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 113642370 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 113644353 timm10b; LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 113635601 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A isoform X1 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 113655078 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 113650450 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 113648558 chchd4a; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 113644010 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 113648825 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 113658222 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 113647724 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 113657948 micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 113656662 chchd3a; coiled-coil-helix-coiled-coil-helix domain containing 3a isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 113659865 chchd3b; coiled-coil-helix-coiled-coil-helix domain containing 3b isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 113643089 chchd6b; coiled-coil-helix-coiled-coil-helix domain containing 6b isoform X2 K17564 CHCHD6; MICOS complex subunit MIC25 D 113646849 apooa; apolipoprotein O, a isoform X2 K24625 APOO; MICOS complex subunit MIC26 D 113661387 apoob; apolipoprotein O, b isoform X1 K24625 APOO; MICOS complex subunit MIC26 D 113662872 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 113648825 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 113658222 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 113647724 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 113655068 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 113638894 timm23a; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 113644971 timm23b; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 113655198 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 113656102 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B isoform X1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 113662383 timm21; mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 113661238 timm50; mitochondrial import inner membrane translocase subunit TIM50 isoform X1 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 113655422 mcu; calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial D 113655420 micu1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 113662932 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 113642423 calcium uniporter protein, mitochondrial-like K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 113661806 essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial D 113663575 smdt1b; single-pass membrane protein with aspartate-rich tail 1b K22830 SMDT1; essential MCU regulator, mitochondrial D 113657351 mcur1; mitochondrial calcium uniporter regulator 1 isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 113644987 letm1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 113646208 immp1l; mitochondrial inner membrane protease subunit 1 isoform X1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 113636157 immp2l; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 113645237 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 113660639 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 113649039 mpc2a; mitochondrial pyruvate carrier 2 isoform X1 K22139 MPC2; mitochondrial pyruvate carrier 2 D 113654194 mpc2b; mitochondrial pyruvate carrier 2b K22139 MPC2; mitochondrial pyruvate carrier 2 D 113663965 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 D 113648197 OCIA domain-containing protein 1-like isoform X1 K28215 OCIAD1; OCIA domain-containing protein 1 B Matrix C MMC/PAM proteins D 113651032 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 113635826 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 113638209 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 113649037 grpel2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 113650416 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 isoform X2 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 113639587 pam16; mitochondrial import inner membrane translocase subunit tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 113637602 pmpca; mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 113654037 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 113643509 mipepa; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 113655473 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 113655448 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 113655474 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 113664046 10 kDa heat shock protein, mitochondrial-like isoform X1 K04078 groES; chaperonin GroES D 125138371 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 125141542 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 113639548 dnaja3a; dnaJ heat shock protein family (Hsp40) member A3a K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 113657045 dnaja3b; dnaJ heat shock protein family (Hsp40) member A3b isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 113639112 tamm41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 113633895 dnlz; DNL-type zinc finger protein isoform X1 K17808 ZIM17; mitochondrial protein import protein ZIM17 D 113650733 ethe1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 113634165 poldip2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 113641047 creb1b; cyclic AMP-responsive element-binding protein 1b K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 113653982 creb1a; cyclic AMP-responsive element-binding protein 1a isoform X3 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 113634612 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 113663350 gfm2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G D 113643964 sp1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1 D 113644356 yy1b; transcriptional repressor protein YY1b isoform X1 K09201 YY; transcription factor YY D 113659649 yy1a; transcriptional repressor protein YY1a K09201 YY; transcription factor YY D 113638753 gabpb1; GA-binding protein subunit beta-1 isoform X4 K09454 GABPB; GA-binding protein transcription factor, beta D 113662963 gabpb2a; GA-binding protein subunit beta-2a K09454 GABPB; GA-binding protein transcription factor, beta D 125140163 GA-binding protein subunit beta-2-like K09454 GABPB; GA-binding protein transcription factor, beta D 113649389 tfam; transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 113663747 nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1 D 113654253 nfe2l2a; nuclear factor erythroid 2-related factor 2a K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 125146193 mt2; metallothionein-2 K14739 MT1_2; metallothionein 1/2 C Coactivators D 113657521 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X5 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 113635862 ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 113645045 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 113657700 crtc1b; CREB-regulated transcription coactivator 1b isoform X2 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 113637131 ep300a; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 113639600 crebbpb; CREB binding protein b isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 113640116 ep300b; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 113657009 crebbpa; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 113643115 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 113638370 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 113644408 LYR motif-containing protein 4 isoform X2 K22069 LYRM4; LYR motif-containing protein 4 D 113634318 fxn; frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1] D 113637781 fdx1b; ferredoxin 1b K22070 FDX1; ferredoxin-1, mitochondrial D 113648970 fdx1; adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial D 113634508 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 113634073 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 113635826 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 113653239 hscb; iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB D 113635940 sil1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1 D 113647980 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 113642321 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 113659396 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 113657107 iba57; putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 113639868 zgc:110319; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 113645623 nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 113649824 bola1; bolA-like protein 1 isoform X1 K22066 BOLA1; BolA-like protein 1 D 113646643 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 113639734 sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 113654921 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 113639009 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2 D 113660994 sfxn4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4 D 113635967 sfxn5b; sideroflexin-5b K23503 SFXN5; sideroflexin-5 D 113639915 sfxn5a; LOW QUALITY PROTEIN: sideroflexin-5a K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 113636660 cpt1aa; carnitine palmitoyltransferase 1Aa (liver) isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 113648527 cpt1a2b; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 113652098 carnitine O-palmitoyltransferase 1, liver isoform isoform X2 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 113652632 cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 113659891 cpt1ab; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 113653931 dhtkd1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 113640423 fbxl4; F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 113645575 hcfc1b; host cell factor 1b isoform X1 K14966 HCFC1; host cell factor 1 D 113645769 hcfc2; host cell factor 2 K27390 HCFC2; host cell factor 2 D 113642389 htt; huntingtin isoform X1 K04533 HD; huntingtin D 113646904 esrra; steroid hormone receptor ERR1 isoform X2 K08552 NR3B1; estrogen-related receptor alpha D 113659310 esrrb; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 113638824 esrrd; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma D 113651029 esrrga; estrogen-related receptor gamma a isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 113658629 estrogen-related receptor gamma-like K08554 NR3B3; estrogen-related receptor gamma D 113645173 nrip1a; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 113650290 nrip1b; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 113655142 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 113658709 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 113650940 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 113655350 sirt1; NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 113650519 serac1; protein SERAC1 K23504 SERAC1; protein SERAC1 D 113645845 uxt; protein UXT isoform X1 K26537 UXT; protein UXT D 113635674 si:ch211-153b23.5; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 113639739 gatd3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial isoform X1 K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial D 113638912 tango2; transport and Golgi organization protein 2 homolog isoform X1 K28098 TANGO2; transport and Golgi organization protein 2 D 113646243 c6h2orf69; mitochondrial protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69 B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 113656067 ndufaf1; complex I intermediate-associated protein 30, mitochondrial isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 113634293 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 isoform X1 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 113637018 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 isoform X1 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 113647311 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 isoform X1 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 113663577 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 113644739 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X2 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 113648261 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 113638917 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 isoform X2 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 113657405 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 113641312 acad9; complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 113659817 nubpl; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 113650285 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 113641429 rtn4ip1; reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 113648690 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 113646182 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial isoform X2 K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 113654494 mitochondrial chaperone BCS1 isoform X1 K08900 BCS1; mitochondrial chaperone BCS1 D 113657639 ttc19; tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 113639257 lyrm7; complex III assembly factor LYRM7 isoform X1 K18170 LYRM7; complex III assembly factor LYRM7 D 113643096 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 113642829 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 113650249 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 113663720 c3h16orf91; protein CCSMST1 isoform X1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 113658262 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 113636111 c17h12orf73; protein BRAWNIN K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 113651564 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 113650072 cmc1; COX assembly mitochondrial protein homolog isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1 D 113647884 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 113644062 cytochrome c oxidase assembly factor 1 homolog isoform X1 K18173 COA1; cytochrome c oxidase assembly factor 1 D 113653619 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 113637769 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 113654619 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 113645497 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 113648077 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 113651618 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 113638969 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 113639062 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14 D 113655462 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 113648354 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 113654425 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 113637506 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18 D 113662680 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 113655337 cytochrome c oxidase assembly protein COX20, mitochondrial isoform X1 K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 113649780 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 113649782 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 113648096 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 113657077 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 113635163 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 113655149 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 113638108 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 113654025 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 113650594 translational activator of cytochrome c oxidase 1 isoform X1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 113644952 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial isoform X1 K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 113639823 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1 D 113651564 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 113658262 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 113649936 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 D 113636598 higd1a; HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 113639048 HIG1 domain family member 1C-like K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial D 113637447 higd2a; HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial C Complex-V assembly factors D 113657858 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 113637162 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 113640373 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 113644210 atp5mj; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid D 113649048 atp5md; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 113653683 mfn1b; mitofusin-1b isoform X1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 113656019 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 113653676 opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 113635642 opa3; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein D 113638420 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 113637829 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 113646760 zgc:153993; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 113652242 baxa; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX D 113636017 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 113646489 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 113635177 fis1; mitochondrial fission 1 protein isoform X1 K17969 FIS1; mitochondrial fission 1 protein D 113650456 sumo2b; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 113651165 sumo3a; small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier D 113651314 sumo1; small ubiquitin-related modifier 1 isoform X1 K12160 SUMO; small ubiquitin-related modifier D 113658691 sumo2a; small ubiquitin like modifier 2a K12160 SUMO; small ubiquitin-related modifier D 113638496 sh3glb1b; endophilin-B1b isoform X3 K11248 SH3GLB1; endophilin-B1 D 113647510 sh3glb1a; endophilin-B1a K11248 SH3GLB1; endophilin-B1 D 113634236 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 113648361 mffa; mitochondrial fission factor homolog B isoform X1 K22076 MFF; mitochondrial fission factor D 113650085 mffb; mitochondrial fission factor homolog A isoform X1 K22076 MFF; mitochondrial fission factor D 113641969 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 113657776 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 113638063 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 113640124 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 113640551 mief2; mitochondrial dynamics protein MID49 isoform X2 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 113648865 pld6; mitochondrial cardiolipin hydrolase isoform X1 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 113644055 miga1; mitoguardin 1 K27289 MIGA; mitoguardin D 113663997 miga2; mitoguardin 2 isoform X1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 113640465 actb1; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 113643994 actb2; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 113648254 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 113638395 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 113638143 phb; prohibitin K17080 PHB1; prohibitin 1 D 113650155 phb2a; prohibitin-2a K17081 PHB2; prohibitin 2 D 113659399 ktn1; kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 113636017 dnm1l; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 113646489 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 113634950 myo5b; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V D 113653962 myo5ab; unconventional myosin-Va K10357 MYO5; myosin V D 113653963 myo5c; unconventional myosin-Vc K10357 MYO5; myosin V D 113657886 si:dkey-110c1.10; unconventional myosin-Vb isoform X3 K10357 MYO5; myosin V D 113658630 myo5aa; unconventional myosin-Va K10357 MYO5; myosin V D 113636052 E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 113636897 diabloa; diablo, IAP-binding mitochondrial protein a K10522 DIABLO; diablo D 113638557 diablob; diablo, IAP-binding mitochondrial protein b K10522 DIABLO; diablo C Morphogenesis factors D 113635975 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25 D 113643995 rhot1a; mitochondrial Rho GTPase 1-A isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 113656857 rhot1b; mitochondrial Rho GTPase 1b K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 113647724 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 113640994 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 113644202 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 113658857 oxr1a; oxidation resistance protein 1a isoform X1 K25437 OXR1; oxidation resistance protein 1 D 113634018 msto1; protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato D 113647829 prelid1a; PRELI domain containing 1a K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial D 113652987 prelid1b; PRELI domain containing 1b K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial D 113643248 prelid3b; PRELI domain containing protein 3B isoform X1 K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial B Mitophagy factors C Autophagy-related proteins D 113635667 atg2a; autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2 D 113659393 atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2 D 113643154 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 113643151 atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 113643186 atg4c; cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 113647572 atg4a; cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 113650448 cysteine protease atg4da-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 113663600 atg4da; cysteine protease atg4da K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 113640334 atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5 D 113639065 atg7; ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 113643585 zgc:92606; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 113651928 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 113657426 gabarapb; GABA(A) receptor-associated protein b K08341 GABARAP; GABA(A) receptor-associated protein D 113663947 gabarapa; GABA(A) receptor-associated protein a K08341 GABARAP; GABA(A) receptor-associated protein D 113651237 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 113659055 atg9b; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9 D 113638321 atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 113644141 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12 D 113659436 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 113637875 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 113643625 protein Atg16l2 K20868 ATG16L2; autophagy-related protein 16-2 D 113650735 wipi2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 113663521 wipi1; WD repeat domain phosphoinositide-interacting protein 1 isoform X3 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 113644945 prkn; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31] D 113635255 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 113649206 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 113641891 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 113637829 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 113647769 sqstm1; sequestosome-1 K14381 SQSTM1; sequestosome 1 D 113641590 tax1bp1a; tax1-binding protein 1 homolog A isoform X1 K21347 TAX1BP1; Tax1-binding protein 1 D 113644157 tax1bp1b; tax1-binding protein 1 homolog B isoform X2 K21347 TAX1BP1; Tax1-binding protein 1 D 113637140 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 113653942 ambra1b; activating molecule in BECN1-regulated autophagy protein 1B isoform X2 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 113634220 atg13; autophagy-related protein 13 isoform X2 K08331 ATG13; autophagy-related protein 13 D 113653827 ulk1a; serine/threonine-protein kinase ULK1a isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 113661753 ulk1b; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 113661219 ulk2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 113659060 rb1cc1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 113655582 hsp90aa1.2; heat shock protein 90, alpha (cytosolic), class A member 1, tandem duplicate 2 K04079 HSP90A; molecular chaperone HtpG D 113655583 hsp90aa1.1; heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG D 113655692 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 113636958 hsp90 co-chaperone Cdc37 isoform X1 K09554 CDC37; cell division cycle protein 37 D 113637226 hsp90 co-chaperone Cdc37-like isoform X1 K09554 CDC37; cell division cycle protein 37 D 113634456 E3 ubiquitin-protein ligase SMURF2-like isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 113639683 smurf2; E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 113660597 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 113652936 bnip3lb; BCL2 interacting protein 3 like b K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 113656195 bnip3la; BCL2 interacting protein 3 like a isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 113654522 fundc1; FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 113655142 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 113658709 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 113636045 map1lc3cl; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 113639121 map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 113641294 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 113652480 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 113637198 nbr1a; NBR1 autophagy cargo receptor a isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 113663919 nbr1b; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 113637174 tecpr1a; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 113638066 tecpr1b; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 113648369 si:ch211-11n16.2; zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 113658053 zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 113659050 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 113656988 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 113651439 protein C19orf12 homolog K23168 MPAN; protein MPAN D 113652761 zgc:112052; protein C19orf12 homolog K23168 MPAN; protein MPAN D 113647562 fundc2; FUN14 domain-containing protein 2 isoform X1 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: April 30, 2025