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Mitochondrial Biogenesis - Trichechus manatus latirostris (Florida manatee)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 101358497 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 101347051 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
D 101344996 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 101351757 dimethyladenosine transferase 2, mitochondrial isoform X1 K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 101361726 translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 101347112 translation initiation factor IF-3, mitochondrial isoform X2 K02520 infC; translation initiation factor IF-3
D 101354272 elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts
D 101358877 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 101355530 elongation factor G, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 101361340 ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 101347152 transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 101349991 transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 101352239 transcription termination factor 1, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 101359601 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 101361568 translation factor GUF1, mitochondrial isoform X2 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 101356696 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 101349090 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 101362036 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 101353745 LOW QUALITY PROTEIN: ribonuclease P protein subunit p30-like K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 101359681 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 101345830 ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 101359001 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 101361085 ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 101360589 ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 101359583 ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 101351331 tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 101360197 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 101355865 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 101353838 LOW QUALITY PROTEIN: putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 101343541 transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 101340899 pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 101343992 pentatricopeptide repeat domain-containing protein 3, mitochondrial isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 101345925 putative ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 101352172 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 101354492 AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 101353497 mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 101359057 ATP-dependent RNA helicase SUPV3L1, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 101356532 endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 101341492 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 101350620 ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 101351885 ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 101354695 ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 101341344 mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 101360543 mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 101352116 mitochondrial assembly of ribosomal large subunit protein 1 isoform X1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 101355727 GTPase Era, mitochondrial isoform X2 K03595 era; GTPase
D 101353721 tyrosine--tRNA ligase, mitochondrial isoform X2 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 101354739 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 101349569 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 101361135 probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 101343239 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 101349544 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 101346960 probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 101359429 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 101349939 LOW QUALITY PROTEIN: glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 101346581 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X2 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 101340462 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial isoform X2 K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 101343377 poly(A) RNA polymerase, mitochondrial isoform X1 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 101360451 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 101340542 mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 101345227 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 101340883 tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 101349268 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 101347548 mitochondrial mRNA pseudouridine synthase RPUSD3 isoform X2 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 101344041 mitochondrial RNA pseudouridine synthase RPUSD4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 101343352 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 101352428 neugrin K23496 NGRN; neugrin
D 101342746 LOW QUALITY PROTEIN: mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 101350384 FAST kinase domain-containing protein 1, mitochondrial K27754 FASTKD1; FAST kinase domain-containing protein 1
D 101344635 FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 101360072 FAST kinase domain-containing protein 3, mitochondrial isoform X2 K27755 FASTKD3; FAST kinase domain-containing protein 3
D 101349836 protein TBRG4 isoform X1 K27756 TBRG4; FAST kinase domain-containing protein 4
D 101344485 FAST kinase domain-containing protein 5, mitochondrial K27757 FASTKD5; FAST kinase domain-containing protein 5
D 101353263 probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor
D 101351971 required for meiotic nuclear division protein 1 homolog isoform X2 K23499 RMND1; required for meiotic nuclear division protein 1
D 101361539 LOW QUALITY PROTEIN: G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1
D 111821819 G-rich sequence factor 1-like K24984 GRSF1; G-rich sequence factor 1
D 101351549 probable methyltransferase-like protein 15 isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 101350881 UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 101352253 uncharacterized protein C6orf203 homolog isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 101348996 DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 101351927 DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2
D 101354049 DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 101356375 LOW QUALITY PROTEIN: endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 101359969 mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 101344631 nuclease EXOG, mitochondrial isoform X2 K15050 EXOG; nuclease EXOG, mitochondrial
D 101344344 twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 101349694 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 101345050 single-stranded DNA-binding protein, mitochondrial isoform X1 K03111 ssb; single-strand DNA-binding protein
D 101361636 ATPase family AAA domain-containing protein 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 101354640 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 101359183 uncharacterized protein C17orf80 homolog isoform X1 K27759 MTNAP1; mitochondrial nucleoid-associated protein 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 101350368 dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 101351822 mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 101343809 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 101348660 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 101348919 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 101351001 heat shock 70 kDa protein 6 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 101354728 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 101356536 LOW QUALITY PROTEIN: heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 101356837 LOW QUALITY PROTEIN: heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 101357110 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 101343025 AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein
D 101350297 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 101358554 fetal and adult testis-expressed transcript protein K28235 FATE1; fetal and adult testis-expressed transcript protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 101355332 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
D 101350467 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 111820787 mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 101340880 TOMM20-like protein 1 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 101359699 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 101342154 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 101347642 mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 101354474 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 101341330 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
C TOB/SAM complex
D 101345216 sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 101351096 voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 101346677 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 101351954 voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 101353138 metaxin-3 isoform X1 K17776 MTX; metaxin
D 101354472 metaxin-1 K17776 MTX; metaxin
D 101357626 metaxin-2 isoform X1 K17776 MTX; metaxin
D 101347342 unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX
D 101356126 armadillo repeat-containing X-linked protein 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1
D 101355185 armadillo repeat-containing X-linked protein 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2
D 101355435 armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3
D 101355869 protein ARMCX6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6
D 101345107 mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 101341134 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 105756245 mitochondrial import inner membrane translocase subunit Tim9-like isoform X1 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 101358636 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 101347971 mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 101347775 mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 101357127 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 101348607 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 101350102 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 101348668 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 101352018 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 101343733 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 101352119 MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 101359216 MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 101352932 MICOS complex subunit MIC25 K17564 CHCHD6; MICOS complex subunit MIC25
D 101356655 MICOS complex subunit MIC26 K24625 APOO; MICOS complex subunit MIC26
D 101350140 MICOS complex subunit MIC27 isoform X1 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 101352018 MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 101343733 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 101343948 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 101347039 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 101342665 mitochondrial import inner membrane translocase subunit Tim17-A isoform X2 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 101347253 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 101353951 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 101361396 mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 101357576 calcium uptake protein 1, mitochondrial isoform X2 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 101343914 calcium uptake protein 2, mitochondrial isoform X1 K22828 MICU2; calcium uptake protein 2, mitochondrial
D 101347511 calcium uniporter regulatory subunit MCUb, mitochondrial isoform X1 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 101341085 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 101351353 mitochondrial calcium uniporter regulator 1 isoform X2 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 101340742 mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 101354046 mitochondrial inner membrane protease subunit 1 isoform X1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 101349216 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 101361965 transmembrane protein 126A isoform X1 K18157 TMEM126A; transmembrane protein 126A
D 101340869 mitochondrial pyruvate carrier 1 isoform X1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 101353053 mitochondrial pyruvate carrier 1-like protein K22138 MPC1; mitochondrial pyruvate carrier 1
D 105756740 mitochondrial pyruvate carrier-like protein K22138 MPC1; mitochondrial pyruvate carrier 1
D 101356660 mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 101353073 OCIA domain-containing protein 1 isoform X3 K28215 OCIAD1; OCIA domain-containing protein 1
B Matrix
C MMC/PAM proteins
D 101347677 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 101361110 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 101342616 grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 101345137 grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 101343887 mitochondrial import inner membrane translocase subunit TIM14 isoform X1 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 105756299 mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 101360803 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 101361162 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 101348130 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 101358584 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 101346470 dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 101355735 phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 101350106 DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 101349750 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 101361124 polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 101356881 cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 101355530 elongation factor G, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 101361340 ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G
D 101349790 transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 101349288 transcriptional repressor protein YY1 isoform X1 K09201 YY; transcription factor YY
D 101354446 transcription factor YY2 K09201 YY; transcription factor YY
D 101346878 GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta
D 101358433 GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 101347051 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 101348371 nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 101356462 nuclear factor erythroid 2-related factor 2 isoform X2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 101355071 metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 101355325 metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 101355582 metallothionein-2-like isoform X2 K14739 MT1_2; metallothionein 1/2
D 101355838 metallothionein-1E K14739 MT1_2; metallothionein 1/2
D 101356098 metallothionein-3 K14740 MT3; metallothionein 3
D 111819625 metallothionein-4 K14741 MT4; metallothionein 4
C Coactivators
D 101340445 peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 101340394 peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 101351390 peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 101348456 CREB-regulated transcription coactivator 1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 101344282 CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 101349614 histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 101349857 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 101353822 iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 105756859 LYR motif-containing protein 4 isoform X2 K22069 LYRM4; LYR motif-containing protein 4
D 101347335 frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 101358151 ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 101340285 NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 101361110 stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 101354716 iron-sulfur cluster co-chaperone protein HscB, mitochondrial isoform X1 K04082 hscB; molecular chaperone HscB
D 101361880 nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1
D 101345709 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 101344395 iron-sulfur cluster assembly 1 homolog, mitochondrial isoform X2 K22063 ISCA1; iron-sulfur cluster assembly 1
D 101353112 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 101346423 putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 101340774 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 101356934 bolA-like protein 1 isoform X2 K22066 BOLA1; BolA-like protein 1
D 101349921 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 111820117 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 101345169 sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 101349000 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 101355310 sideroflexin-2 K23501 SFXN2; sideroflexin-2
D 101350292 sideroflexin-4 K23502 SFXN4; sideroflexin-4
D 101354043 sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 101360516 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 101354017 carnitine O-palmitoyltransferase 1, muscle isoform isoform X1 K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 101347610 carnitine O-palmitoyltransferase 1, brain isoform isoform X1 K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
D 101351336 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 101345695 F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 101342908 host cell factor 1 K14966 HCFC1; host cell factor 1
D 101342583 host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2
D 101360779 huntingtin K04533 HD; huntingtin
D 101350739 steroid hormone receptor ERR1 isoform X1 K08552 NR3B1; estrogen-related receptor alpha
D 101358720 steroid hormone receptor ERR2 isoform X2 K08553 NR3B2; estrogen-related receptor beta
D 101348592 estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 101355578 nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 101346784 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 101360368 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 101354513 lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 101342951 NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 101346440 protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 101352789 protein UXT isoform X1 K26537 UXT; protein UXT
D 101344410 PGC-1 and ERR-induced regulator in muscle protein 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
D 101346330 ES1 protein homolog, mitochondrial K27835 GATD3; glutamine amidotransferase-like class 1 domain-containing protein 3, mitochondrial
D 101347059 transport and Golgi organization protein 2 homolog isoform X4 K28098 TANGO2; transport and Golgi organization protein 2
D 101361439 UPF0565 protein C2orf69 homolog K28271 C2ORF69; mitochondrial protein C2orf69
D 101354177 protein FAM214A isoform X1 K28528 ATOS; protein Atossa
D 101355170 protein FAM214B K28528 ATOS; protein Atossa
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 101353065 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 111820203 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 101353094 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 isoform X2 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 101347650 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 101349023 LOW QUALITY PROTEIN: arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 101360901 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 101341878 protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 101344620 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 101354365 complex I assembly factor TMEM126B, mitochondrial K18165 TMEM126B; complex I assembly factor TMEM126B
D 101347508 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 101343652 acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 101346222 iron-sulfur protein NUBPL isoform X2 K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 101355532 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 101351742 reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 101351049 complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 101344430 succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 101348286 succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 101346481 mitochondrial chaperone BCS1 isoform X1 K08900 BCS1; mitochondrial chaperone BCS1
D 101346908 tetratricopeptide repeat protein 19, mitochondrial isoform X2 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 111822076 complex III assembly factor LYRM7 isoform X1 K18170 LYRM7; complex III assembly factor LYRM7
D 101352172 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 101354640 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 101349046 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 101352443 protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 101348721 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 101360310 uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 101352451 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1
D 105756619 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 101355957 COX assembly mitochondrial protein homolog isoform X2 K18171 CMC1; COX assembly mitochondrial protein 1
D 101344127 COX assembly mitochondrial protein 2 homolog isoform X2 K18172 CMC2; COX assembly mitochondrial protein 2
D 101358867 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 101352336 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 101355283 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 101341125 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 101348249 cytochrome c oxidase assembly factor 6 homolog isoform X1 K18179 COA6; cytochrome c oxidase assembly factor 6
D 101357021 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 101348940 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 101355500 LOW QUALITY PROTEIN: protoheme IX farnesyltransferase, mitochondrial-like K02257 COX10; heme o synthase [EC:2.5.1.141]
D 101346394 cytochrome c oxidase assembly protein COX11, mitochondrial isoform X1 K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 101360280 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 101361313 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 105755970 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 101350126 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 101359911 LOW QUALITY PROTEIN: mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18
D 101343374 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 101354255 cytochrome c oxidase protein 20 homolog isoform X2 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 101353838 LOW QUALITY PROTEIN: putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 101345290 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 101359714 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 101346280 mitochondrial inner membrane protein OXA1L isoform X2 K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 101355232 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 101351231 protein SCO1 homolog, mitochondrial isoform X1 K07152 SCO1; protein SCO1
D 101348874 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 101355947 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 101356513 leucine-rich PPR motif-containing protein, mitochondrial isoform X1 K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 111820641 apoptogenic protein 1, mitochondrial isoform X1 K23506 APOPT1; apoptogenic protein 1
D 101352451 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1
D 105756619 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 101348721 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 101348032 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
D 101355908 HIG1 domain family member 1A, mitochondrial K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 111822770 HIG1 domain family member 1C K28216 HIGD1A_C; HIG1 domain family member 1A/C, mitochondrial
D 101358122 HIG1 domain family member 2A, mitochondrial K28217 HIGD2A; HIG1 domain family member 2A, mitochondrial
C Complex-V assembly factors
D 101347232 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 101351868 ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 101358301 transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 101359195 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 105756637 LOW QUALITY PROTEIN: 6.8 kDa mitochondrial proteolipid-like K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 111822409 up-regulated during skeletal muscle growth protein 5 isoform X1 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 101348530 mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 101360670 mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 101361254 LOW QUALITY PROTEIN: dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 101342180 optic atrophy 3 protein-like K23166 OPA3; optic atrophy 3 protein
D 101355882 optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 101358239 TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 101341669 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 101341201 bcl-2 homologous antagonist/killer K14021 BAK; Bcl-2 homologous antagonist/killer
D 101356564 apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 101353980 dynamin-1-like protein isoform X3 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 101349993 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 101342274 small ubiquitin-related modifier 3 isoform X2 K12160 SUMO; small ubiquitin-related modifier
D 101344762 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 101347507 small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 101353551 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 101359450 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 101359469 LOW QUALITY PROTEIN: small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 105756334 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 101356130 endophilin-B1 isoform X2 K11248 SH3GLB1; endophilin-B1
D 101343263 mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier
D 101356340 mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier
D 101354291 mitochondrial fission factor isoform X5 K22076 MFF; mitochondrial fission factor
D 101355154 ganglioside-induced differentiation-associated protein 1-like 1 isoform X2 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 101357539 ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 101357268 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 101340645 mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 101345100 mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 101341416 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 101358925 mitoguardin 2 K27289 MIGA; mitoguardin
D 101361143 mitoguardin 1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 101344372 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 101358156 actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 101356305 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 101349123 N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 101359367 prohibitin K17080 PHB1; prohibitin 1
D 101358352 prohibitin-2 isoform X1 K17081 PHB2; prohibitin 2
D 101347730 kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 101353980 dynamin-1-like protein isoform X3 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 101350067 unconventional myosin-Vb K10357 MYO5; myosin V
D 101352711 unconventional myosin-Vc K10357 MYO5; myosin V
D 101352971 unconventional myosin-Va isoform X2 K10357 MYO5; myosin V
D 101346318 E3 ubiquitin-protein ligase XIAP isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 101356250 diablo homolog, mitochondrial isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 101355207 sorting nexin-25 isoform X2 K17887 SNX25; sorting nexin-25
D 101343809 mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 101343733 MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 101357636 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 101348135 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29
D 101345961 E3 ubiquitin-protein ligase NEDD4 isoform X2 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 101344518 oxidation resistance protein 1 isoform X2 K25437 OXR1; oxidation resistance protein 1
D 101353703 protein misato homolog 1 K27320 MSTO1; protein misato
D 101342904 PRELI domain-containing protein 1, mitochondrial isoform X4 K27964 PRELID1; PRELI domain-containing protein 1, mitochondrial
D 101354961 PRELI domain-containing protein 2 K27965 PRELID2; PRELI domain-containing protein 2 mitochondrial
D 101345177 PRELI domain containing protein 3A K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
D 101347389 PRELI domain containing protein 3B K27966 PRELID3; PRELI domain-containing protein 3, mitochondrial
B Mitophagy factors
C Autophagy-related proteins
D 101345997 autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 101355263 autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2
D 101357622 ubiquitin-like-conjugating enzyme ATG3 isoform X2 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 101343995 cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 101349296 cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 101351272 cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 101355699 cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 101351212 autophagy protein 5 isoform X3 K08339 ATG5; autophagy-related protein 5
D 101349952 LOW QUALITY PROTEIN: beclin-2 K08334 BECN; beclin
D 101359690 beclin-1 isoform X1 K08334 BECN; beclin
D 105756546 ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 101346525 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 101347875 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 101359453 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 101346894 autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 101349796 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 101350547 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 101348349 ubiquitin-like protein ATG12 isoform X2 K08336 ATG12; ubiquitin-like protein ATG12
D 101359341 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 101350174 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 101352468 autophagy-related protein 16-2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 101345874 WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 101359379 WD repeat domain phosphoinositide-interacting protein 2 isoform X2 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 101340669 E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 101351602 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 101355595 protein CLEC16A isoform X2 K19513 CLEC16A; protein CLEC16A
D 101344541 serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 101341669 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 101351010 sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1
D 101345115 tax1-binding protein 1 isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 101357321 LOW QUALITY PROTEIN: tax1-binding protein 1 homolog K21347 TAX1BP1; Tax1-binding protein 1
D 101361776 calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 101345407 activating molecule in BECN1-regulated autophagy protein 1 isoform X2 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 101346435 autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 101357581 serine/threonine-protein kinase ULK1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 101345383 serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 101351891 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 101341605 heat shock protein HSP 90-alpha-like isoform X1 K04079 HSP90A; molecular chaperone HtpG
D 101343785 heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 101348117 LOW QUALITY PROTEIN: heat shock protein HSP 90-alpha-like K04079 HSP90A; molecular chaperone HtpG
D 101349955 heat shock protein HSP 90-alpha isoform X1 K04079 HSP90A; molecular chaperone HtpG
D 101357378 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 101351406 E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 101351693 E3 ubiquitin-protein ligase SMURF1 isoform X2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 101352994 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X2 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 101359811 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 101346784 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 101360368 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 101351409 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 101351672 microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 101353236 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 101356277 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 101356355 next to BRCA1 gene 1 protein K17987 NBR1; next to BRCA1 gene 1 protein
D 101346925 tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 101346283 zinc finger FYVE domain-containing protein 1 isoform X2 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 101353624 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 101345872 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 101348405 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 101359951 FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: September 5, 2025