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Mitochondrial Biogenesis - Triplophysa rosa
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 14048448 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 14048436 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 14048442 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 14048444 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 14048443 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 14048445 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 130568784 LOW QUALITY PROTEIN: NADH-ubiquinone oxidoreductase chain 5-like K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 14048446 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 14048447 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 14048437 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 14048438 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 14048441 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 14048439 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 14048440 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 130548449 polrmt; DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 130569637 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 130559897 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 130560335 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 130556287 mtif2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 130550883 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 130556896 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 130548578 elongation factor Tu 2-like K02358 tuf; elongation factor Tu
D 130548580 elongation factor Tu 2-like K02358 tuf; elongation factor Tu
D 130561556 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 130567077 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 130548579 elongation factor G-like K02355 fusA; elongation factor G
D 130550345 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 130566899 transcription termination factor 1a, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 130562884 mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 130555052 mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 130566586 mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 130563954 guf1; translation factor Guf1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
D 130548326 elongation factor 4-like K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 130557820 pop1; ribonucleases P/MRP protein subunit POP1 isoform X1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 130559327 pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 130568389 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 130569190 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 130558728 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 130552096 rpp25a; ribonuclease P protein subunit p25a K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 130558080 rpp25l; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 130562384 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 130558521 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 130554558 rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 130552991 trmt10c; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 130544981 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 130560434 prorp; mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 130546713 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 130546717 mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 130556716 tefm; transcription elongation factor, mitochondrial isoform X1 K17658 TEFM; transcription elongation factor, mitochondrial
D 130553012 ptcd1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 130565986 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 130564152 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 130554344 dhx30; ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 130557109 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 130566055 afg1lb; lactation elevated protein 1 homolog B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 130560240 afg1la; AFG1 like ATPase a K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 130547982 atp23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 130559033 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 130554069 lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 130563952 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 130553598 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 130548443 ADP/ATP translocase 3-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 130555988 slc25a6; ADP/ATP translocase 3 isoform X1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 130550173 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 130558977 slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 130568435 slc25a37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 130557657 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 130568470 eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 130551572 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 130566999 yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 130557810 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 130570333 lars1b; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 130548567 leucine--tRNA ligase-like K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 130554893 dars2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 130547391 gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 130570072 rars1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 130566250 rars2; probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 130560298 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 130553107 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 130548569 aspartyl/glutamyl-tRNA(Asn/Gln) amidotransferase subunit B-like K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 130548791 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 130569529 mtpap; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 130570944 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 130558988 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 130563625 noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 130552386 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 130554939 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 130571147 rpusd4; pseudouridylate synthase RPUSD4, mitochondrial K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 130568115 rcc1l; RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 130568026 ngrn; neugrin K23496 NGRN; neugrin
D 130556942 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 130552511 fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 130568876 mtrfr; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 130560580 rmnd1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 130568491 grsf1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1
D 130552831 mettl15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 130570990 myg1; UPF0160 protein MYG1, mitochondrial isoform X1 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 130559268 mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 130551895 polg; DNA polymerase subunit gamma-1 isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 130557154 polg2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2
D 130553443 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 130556249 endonuclease G, mitochondrial-like K01173 ENDOG; endonuclease G, mitochondrial
D 130568251 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 130559077 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 130547100 nuclease EXOG, mitochondrial-like isoform X1 K15050 EXOG; nuclease EXOG, mitochondrial
D 130569211 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 130554539 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 130547891 ssbp1; single-stranded DNA-binding protein, mitochondrial isoform X1 K03111 ssb; single-strand DNA-binding protein
D 130549122 atad3; ATPase family AAA domain containing 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 130556391 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 130561440 dnaja2a; dnaJ homolog subfamily A member 2a K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 130562443 dnaja2b; dnaJ homolog subfamily A member 2b K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 130556550 tomm34; LOW QUALITY PROTEIN: mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 130561765 rhot1a; mitochondrial Rho GTPase 1-A K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 130564541 hspa8b; heat shock protein family A (Hsp70) member 8b K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 130564576 hsc70; heat shock cognate 71 kDa protein isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 130545754 hspa8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 130561280 hsp70.3; heat shock cognate 70-kd protein, tandem duplicate 3 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 130561288 heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 130567829 hspa1b; LOW QUALITY PROTEIN: heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 130563771 LOW QUALITY PROTEIN: uncharacterized protein LOC130563771 K17767 AIP; AH receptor-interacting protein
D 130553131 aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
D 130565297 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 130557939 tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 130567265 tomm40l; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 130567964 si:dkey-71l1.1; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 130556802 tomm70a; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 130569047 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 130559225 tomm20a; translocase of outer mitochondrial membrane 20 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 130571205 tomm20b; mitochondrial import receptor subunit TOM20 homolog B K17770 TOM20; mitochondrial import receptor subunit TOM20
D 130567231 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 130556392 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
C TOB/SAM complex
D 130551820 samm50; sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family
D 130547536 samm50l; sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 130570444 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 130569321 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2
D 130558783 vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 130546471 zgc:56235; voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3
D 130567730 vdac3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 130558411 mtx1a; metaxin-1a K17776 MTX; metaxin
D 130556459 mtx2; metaxin-2 K17776 MTX; metaxin
D 130550323 unconventional myosin-XIX K25838 MYO19; myosin XIX
D 130560728 marc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 130560538 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 130553279 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 130546156 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 130546248 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 130563450 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 130548723 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 130563983 mitochondrial intermembrane space import and assembly protein 40-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 130571692 chchd4a; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 130561426 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 130545207 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 130564050 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 130548870 micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 130547840 chchd3a; coiled-coil-helix-coiled-coil-helix domain containing 3a isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 130545440 chchd6a; MICOS complex subunit mic25a isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 130557026 chchd6b; coiled-coil-helix-coiled-coil-helix domain containing 6b isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25
D 130547168 apoob; apolipoprotein O, b K24625 APOO; MICOS complex subunit MIC26
D 130551401 apooa; apolipoprotein O, a isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 130548393 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 130545207 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 130564050 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 130569124 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 130559257 timm23b; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 130568751 timm23a; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 130571181 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 130567984 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 130547301 timm21; mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 130564633 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 130559170 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 130559169 micu1; calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial
D 130565743 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 130552370 smdt1b; single-pass membrane protein with aspartate-rich tail 1b K22830 SMDT1; essential MCU regulator, mitochondrial
D 130556157 mcur1; mitochondrial calcium uniporter regulator 1 isoform X1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 130558951 letm1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 130571124 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 130552194 immp2l; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 130545967 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 130559665 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 130552861 mpc2a; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 130555623 mpc2b; mitochondrial pyruvate carrier 2b K22139 MPC2; mitochondrial pyruvate carrier 2
D 130570346 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 130548760 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 130548571 chaperone protein DnaK-like K04043 dnaK; molecular chaperone DnaK
D 130551223 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 130570324 grpel2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 130556395 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 130549281 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 130561881 pam16; mitochondrial import inner membrane translocase subunit tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 130547060 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 130547801 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 130564894 mipepa; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 130545990 mipepb; mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 130556057 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 130549149 chaperonin GroEL-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 130555548 hspe1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 130560988 dnaja3a; dnaJ heat shock protein family (Hsp40) member A3a K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 130548803 dnaja3b; dnaJ heat shock protein family (Hsp40) member A3b isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 130571185 tamm41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 130570134 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 130558541 ethe1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 130564568 poldip2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
D 130550462 polymerase delta-interacting protein 2-like K17809 POLDIP2; polymerase delta-interacting protein 2
#
AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 130552390 creb1a; cyclic AMP-responsive element-binding protein 1a isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 130555518 creb1b; cyclic AMP-responsive element-binding protein 1b K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 130567077 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 130548579 elongation factor G-like K02355 fusA; elongation factor G
D 130550345 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 130549521 sp1; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 130565633 yy1b; transcriptional repressor protein YY1b K09201 YY; transcription factor YY
D 130560225 yy1a; transcriptional repressor protein YY1a K09201 YY; transcription factor YY
D 130558417 gabpb2b; GA-binding protein subunit beta-2b K09454 GABPB; GA-binding protein transcription factor, beta
D 130567017 gabpb2a; GA-binding protein subunit beta-2a K09454 GABPB; GA-binding protein transcription factor, beta
D 130562615 gabpb1; GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 130569637 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 130547839 nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 130555472 nfe2l2a; nuclear factor erythroid 2-related factor 2a K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 130555222 mtbl; metallothionein-B-like K14739 MT1_2; metallothionein 1/2
D 130562722 metallothionein K14739 MT1_2; metallothionein 1/2
D 130562723 metallothionein K14739 MT1_2; metallothionein 1/2
D 130562724 metallothionein K14739 MT1_2; metallothionein 1/2
C Coactivators
D 130554932 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 130563645 ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 130559623 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 130571585 crtc1b; CREB-regulated transcription coactivator 1b isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 130554388 crtc1a; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 130548380 crebbpa; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 130561858 crebbpb; CREB binding protein b isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 130562285 ep300b; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 130568762 ep300a; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 130571085 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 130551009 cysteine desulfurase-like K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 130569574 iscu; iron-sulfur cluster assembly enzyme ISCU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 130570089 iscub; iron-sulfur cluster assembly enzyme b K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 130554560 lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 130547392 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 130568123 fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 130563931 fdx1b; ferredoxin 1b K22070 FDX1; ferredoxin-1, mitochondrial
D 130555297 fdx1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 130556843 fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 130569446 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 130548571 chaperone protein DnaK-like K04043 dnaK; molecular chaperone DnaK
D 130551223 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 130571652 hscb; iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 130563486 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 130565611 glutaredoxin-related protein 5, mitochondrial isoform X1 K07390 grxD; monothiol glutaredoxin
D 130565612 glutaredoxin-related protein 5, mitochondrial isoform X1 K07390 grxD; monothiol glutaredoxin
D 130569310 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial isoform X1 K22063 ISCA1; iron-sulfur cluster assembly 1
D 130560022 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 130554583 iba57; putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 130559590 zgc:110319; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 130568056 nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 130558794 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 130563711 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 130559191 sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 130569055 sfxn2; sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2
D 130559749 sfxn4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4
D 130563851 sfxn5b; sideroflexin-5b K23503 SFXN5; sideroflexin-5
D 130559627 sfxn5a; sideroflexin-5a K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 130551539 cpt1ab; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 130551648 cpt1aa; carnitine palmitoyltransferase 1Aa (liver) isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 130546818 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 130561431 cpt1a2b; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 130562617 cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 130551686 dhtkd1; 2-oxoadipate dehydrogenase complex component E1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 130558180 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 130570863 hcfc1a; LOW QUALITY PROTEIN: host cell factor 1a K14966 HCFC1; host cell factor 1
D 130568077 hcfc1b; host cell factor 1b K14966 HCFC1; host cell factor 1
D 130547532 hcfc2; host cell factor 2 K27390 HCFC2; host cell factor 2
D 130552696 htt; huntingtin isoform X1 K04533 HD; huntingtin
D 130569902 esrra; steroid hormone receptor ERR1 isoform X1 K08552 NR3B1; estrogen-related receptor alpha
D 130560096 esrrb; LOW QUALITY PROTEIN: steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta
D 130565935 esrrgb; estrogen-related receptor gamma b K08554 NR3B3; estrogen-related receptor gamma
D 130560644 esrrga; estrogen-related receptor gamma a isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 130563003 esrrd; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma
D 130565045 nrip1a; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 130546267 nrip1b; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 130565660 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 130566724 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 130548410 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 130548563 lon protease-like K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 130558770 sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 130566274 serac1; protein SERAC1 K23504 SERAC1; protein SERAC1
D 130568101 uxt; protein UXT K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 130559078 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 130567814 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 130548759 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 130550322 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 isoform X1 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 130553284 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 130558515 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 130565450 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 130568928 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 130554306 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 130571698 acad9; complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 130560162 nubpl; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 130546028 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 130559973 rtn4ip1; reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 130546094 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 130557526 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 130556085 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 130555002 ttc19; tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 130550305 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 130557109 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 130556391 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 130545989 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 130545449 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 130552134 ubiquinol-cytochrome-c reductase complex assembly factor 6 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 130548033 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 130557736 cmc1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 130562503 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 130554772 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 130561510 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 130568919 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 130546611 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 130555285 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 130547894 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 130565991 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 130568869 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 130569260 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 130548813 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 130559576 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 130559579 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 130559049 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 130555876 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 130563629 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 130569264 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 130559453 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 130546713 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 130546717 mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 130561711 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 130549009 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 130549654 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 130566753 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 130561309 protein SCO1 homolog, mitochondrial isoform X1 K07152 SCO1; protein SCO1
D 130547758 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 130569261 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 130559358 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 130558782 cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1
D 130548033 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 130545449 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 130569831 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 130549087 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 130569306 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 130554693 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 130566074 atp5mj; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 130552842 atp5md; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 130553450 ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 130571322 mfn1b; mitofusin-1b K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 130554732 mfn1a; LOW QUALITY PROTEIN: mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 130550713 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 130556684 opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 130562831 opa3; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 130545861 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 130564592 parlb; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 130554542 parla; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 130554222 zgc:153993; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 130561428 baxa; BCL2 associated X, apoptosis regulator a K02159 BAX; apoptosis regulator BAX
D 130561915 apoptosis regulator BAX-like isoform X1 K02159 BAX; apoptosis regulator BAX
D 130551672 dnm1l; LOW QUALITY PROTEIN: dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 130568000 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 130559784 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 130551415 mitochondrial fission 1 protein-like K17969 FIS1; mitochondrial fission 1 protein
D 130555730 sumo3b; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 130561178 sumo2b; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 130556740 sumo3a; small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier
D 130556795 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 130554462 sh3glb1b; endophilin-B1b isoform X1 K11248 SH3GLB1; endophilin-B1
D 130547360 sh3glb1a; endophilin-B1a K11248 SH3GLB1; endophilin-B1
D 130550177 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 130564416 mffa; mitochondrial fission factor homolog B isoform X1 K22076 MFF; mitochondrial fission factor
D 130570196 mitochondrial fission factor-like isoform X1 K22076 MFF; mitochondrial fission factor
D 130554866 mffb; mitochondrial fission factor homolog A isoform X1 K22076 MFF; mitochondrial fission factor
D 130545444 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 130547014 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 130562017 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 130552783 mief2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 130561700 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 130553480 pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 130570091 miga2; mitoguardin 2 K27289 MIGA; mitoguardin
D 130554002 miga1; mitoguardin 1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 130553659 actb1; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 130562249 actb2; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 130565871 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 130545756 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 130562039 phb; prohibitin isoform X1 K17080 PHB1; prohibitin 1
D 130554966 phb2a; prohibitin-2a K17081 PHB2; prohibitin 2
D 130556787 phb2b; prohibitin-2b K17081 PHB2; prohibitin 2
D 130560030 ktn1; kinectin K17975 KTN1; kinectin
C Retention of mitochondria
D 130551672 dnm1l; LOW QUALITY PROTEIN: dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 130568000 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 130551678 myo5ab; unconventional myosin-Va K10357 MYO5; myosin V
D 130551775 myo5c; unconventional myosin-Vc K10357 MYO5; myosin V
D 130570234 myo5b; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 130548383 si:dkey-110c1.10; unconventional myosin-Vb K10357 MYO5; myosin V
D 130562432 myo5aa; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
D 130563400 xiap; E3 ubiquitin-protein ligase XIAP isoform X1 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 130570316 diablob; diablo, IAP-binding mitochondrial protein b K10522 DIABLO; diablo
D 130564957 diabloa; diablo, IAP-binding mitochondrial protein a isoform X1 K10522 DIABLO; diablo
C Morphogenesis factors
D 130563432 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25
D 130561765 rhot1a; mitochondrial Rho GTPase 1-A K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 130564050 immt; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 130550123 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 130563309 nedd4a; E3 ubiquitin-protein ligase NEDD4-like K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 130567044 oxr1b; oxidation resistance protein 1b isoform X1 K25437 OXR1; oxidation resistance protein 1
D 130557518 oxr1a; oxidation resistance protein 1a isoform X1 K25437 OXR1; oxidation resistance protein 1
D 130567006 msto1; protein misato homolog 1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 130559993 atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 130563433 atg2a; autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 130557162 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 130570683 atg4a; cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 130553612 atg4da; cysteine protease atg4da K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 130561120 cysteine protease atg4da-like isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 130549486 atg4b; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 130557118 atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 130557647 atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 130569631 becn1; beclin-1 isoform X1 K08334 BECN; beclin
D 130571482 atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 130551702 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 130558493 zgc:92606; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 130570738 gabarapa; GABA(A) receptor-associated protein a K08341 GABARAP; GABA(A) receptor-associated protein
D 130554869 gabarapb; GABA(A) receptor-associated protein b K08341 GABARAP; GABA(A) receptor-associated protein
D 130546763 atg9b; autophagy-related protein 9B isoform X1 K17907 ATG9; autophagy-related protein 9
D 130557206 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 130546286 atg10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 130558220 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 130560210 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 130564587 atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 130564508 protein Atg16l2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 130561544 wipi2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 130562191 wipi1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
D 130568987 LOW QUALITY PROTEIN: WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 130559188 prkn; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31]
D 130572065 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 130561231 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 130545131 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 130564592 parlb; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 130554542 parla; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 130564073 sqstm1; sequestosome-1 K14381 SQSTM1; sequestosome 1
D 130566822 tax1bp1a; tax1-binding protein 1 homolog A isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 130557472 tax1bp1b; tax1-binding protein 1 homolog B isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 130568964 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 130551955 ambra1b; activating molecule in BECN1-regulated autophagy protein 1B K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 130552929 atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 130570139 ulk1b; serine/threonine-protein kinase ULK1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 130568645 ulk1a; serine/threonine-protein kinase ULK1a K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 130564398 ulk2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 130547000 rb1cc1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 130553029 heat shock protein HSP 90-alpha-like K04079 HSP90A; molecular chaperone HtpG
D 130553400 heat shock protein HSP 90-alpha 1-like K04079 HSP90A; molecular chaperone HtpG
D 130565403 hsp90aa1.2; heat shock protein 90, alpha (cytosolic), class A member 1, tandem duplicate 2 K04079 HSP90A; molecular chaperone HtpG
D 130565885 hsp90aa1.1; heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG
D 130566398 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 130552473 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 130561707 smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 130561792 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 130546340 bnip3lb; BCL2 interacting protein 3 like b K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 130567974 bnip3la; BCL2 interacting protein 3 like a K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 130556158 fundc1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
D 130556252 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 130565660 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 130566724 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 130551757 map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 130563957 map1lc3cl; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 130571355 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 130571366 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 130569423 nbr1a; NBR1 autophagy cargo receptor a isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 130561752 nbr1b; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 130561026 tecpr1b; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 130550238 tecpr1a; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 130565237 si:ch211-11n16.2; zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 130565834 zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 130546960 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 130549101 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 130559335 si:ch211-260e23.7; protein C19orf12 homolog K23168 MPAN; protein MPAN
D 130548768 zgc:101715; protein C19orf12 homolog-like K23168 MPAN; protein MPAN
D 130556902 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 130563101 zgc:112052; protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN
D 130570538 fundc2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024