+D
#
Mitochondrial Biogenesis - Vanessa cardui (painted lady)
%
!
AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 124536753 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 124536742 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 124536317 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 124538602 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 124538308 translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 124544088 uncharacterized protein LOC124544088 K02520 infC; translation initiation factor IF-3
D 124531292 elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts
D 124533490 elongation factor Tu K02358 tuf; elongation factor Tu
D 124539413 elongation factor Tu-like K02358 tuf; elongation factor Tu
D 124538494 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 124531116 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 124541151 transcription termination factor 5, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 124542093 transcription termination factor 5, mitochondrial-like isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 124530818 transcription termination factor, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 124530945 transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 124529972 translation factor GUF1 homolog, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 124536537 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 124533017 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 124533546 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 124532307 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 124534375 ribonuclease P protein subunit p20-like isoform X1 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 124533687 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 124543571 uncharacterized protein LOC124543571 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 124532166 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 124532176 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 124543010 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 124538772 3-hydroxyacyl-CoA dehydrogenase type-2-like K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 124535685 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 124536467 uncharacterized protein LOC124536467 K17658 TEFM; transcription elongation factor, mitochondrial
D 124536068 pentatricopeptide repeat-containing protein 1, mitochondrial isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 124537198 pentatricopeptide repeat-containing protein 2, mitochondrial-like K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 124544341 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 124539177 ATP-dependent RNA helicase DHX30-like K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 124532306 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 124530523 putative ATPase N2B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 124533563 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 124544278 ATP-dependent RNA helicase SUV3 homolog, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 124530837 beta-lactamase-like protein 2 homolog K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 124543123 ADP,ATP carrier protein-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 124541411 ADP,ATP carrier protein K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 124539590 mitoferrin K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 124530985 uncharacterized protein LOC124530985 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 124530361 GTPase Era, mitochondrial K03595 era; GTPase
D 124530067 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 124534681 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 124544511 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 124530637 leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 124530216 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 124536244 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 124536880 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 124544364 probable arginine--tRNA ligase, mitochondrial isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 124539842 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 124537312 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 124535869 poly(A) RNA polymerase, mitochondrial-like K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 124531193 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 124538333 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 124537789 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 124530497 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 124534833 uncharacterized protein LOC124534833 K23496 NGRN; neugrin
D 124539312 mitochondrial mRNA pseudouridine synthase Trub2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 124533069 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 124538463 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 124538913 MYG1 exonuclease K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 124535125 mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 124537921 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
C Mitochondrial DNA maintenance factors
D 124540307 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 124535585 mitochondrial genome maintenance exonuclease 1-like K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 124542411 mitochondrial DNA helicase K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 124536869 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
D 124542534 uncharacterized protein LOC124542534 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 124544046 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 124543256 ATPase family AAA domain-containing protein 3A homolog K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
#
AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 124530817 dnaJ homolog subfamily A member 2-like K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 124533350 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 124542362 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124532508 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124532918 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124535242 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124540462 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124540465 major heat shock 70 kDa protein Ba-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124540467 major heat shock 70 kDa protein Ba-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124540473 major heat shock 70 kDa protein Ba-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124540509 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 124534481 aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 124532037 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 124540466 mitochondrial import receptor subunit TOM40 homolog 1-like K11518 TOM40; mitochondrial import receptor subunit TOM40
D 124531648 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 124534416 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 124540789 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
C TOB/SAM complex
D 124541995 sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 124536783 voltage-dependent anion-selective channel-like K15040 VDAC2; voltage-dependent anion channel protein 2
C ERMES complex
C Other outer membrane factor
D 124534779 metaxin-1 K17776 MTX; metaxin
D 124538554 uncharacterized protein LOC124538554 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 124535632 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 124540635 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
C TIM8/13 complex
D 124544178 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 124531250 mitochondrial import inner membrane translocase subunit Tim13-like K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 124538515 mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 124536145 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 124538775 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 124539622 MICOS complex subunit Mic60-like K17785 IMMT; MICOS complex subunit MIC60
D 124539722 MICOS complex subunit Mic60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 124532278 MICOS complex subunit MIC13 homolog QIL1 K24624 MICOS13; MICOS complex subunit MIC13
D 124530402 uncharacterized protein LOC124530402 K17563 CHCHD3; MICOS complex subunit MIC19
D 124539415 uncharacterized protein LOC124539415 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 124538775 MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 124539622 MICOS complex subunit Mic60-like K17785 IMMT; MICOS complex subunit MIC60
D 124539722 MICOS complex subunit Mic60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 124532882 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 124539965 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 124535251 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 124530889 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 124534599 mitochondrial import inner membrane translocase subunit TIM50-C-like isoform X1 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 124530237 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 124530286 calcium uptake protein 1 homolog, mitochondrial-like isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 124534447 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
C Other inner membrane factors
D 124543536 mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 124544142 mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 124532961 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 124531897 uncharacterized protein LOC124531897 K18157 TMEM126A; transmembrane protein 126A
D 124535292 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 124538766 mitochondrial pyruvate carrier 2-like isoform X1 K22139 MPC2; mitochondrial pyruvate carrier 2
B Matrix
C MMC/PAM proteins
D 124535862 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 124541772 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 124541688 grpE protein homolog, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 124538091 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 124538929 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 124540055 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 124543228 cytochrome b-c1 complex subunit 1, mitochondrial-like K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 124543437 cytochrome b-c1 complex subunit 1, mitochondrial-like K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 124534880 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 124544309 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 124536759 heat shock protein 60A-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 124538444 63 kDa chaperonin, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 124536210 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES
D 124537885 protein tumorous imaginal discs, mitochondrial-like isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 124536611 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 124543579 DNL-type zinc finger protein-like K17808 ZIM17; mitochondrial protein import protein ZIM17
D 124535520 persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 124532706 polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
#
AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 124533891 cyclic AMP response element-binding protein B isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 124538494 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 124531116 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 124541973 transcriptional repressor protein YY1-like isoform X1 K09201 YY; transcription factor YY
D 124532291 neurogenic locus notch homolog protein 4 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 124536742 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 124531527 DNA-binding protein P3A2 isoform X1 K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 124537200 CREB-regulated transcription coactivator 3 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 124544026 histone lysine acetyltransferase CREBBP isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 124531037 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 124543820 iron-sulfur cluster assembly scaffold protein IscU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 124541095 LYR motif-containing protein 4B K22069 LYRM4; LYR motif-containing protein 4
D 124532493 frataxin homolog, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 124541730 adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial
D 124540709 adrenodoxin-like protein 1, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 124537035 LOW QUALITY PROTEIN: NADPH:adrenodoxin oxidoreductase, mitochondrial-like K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 124541772 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 124532866 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 124535759 uncharacterized monothiol glutaredoxin ycf64-like K07390 grxD; monothiol glutaredoxin
D 124530305 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 124536878 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 124538294 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 124536747 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 124532526 bolA-like protein DDB_G0274169 isoform X1 K22066 BOLA1; BolA-like protein 1
D 124535635 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 124539889 sideroflexin-1-3 K23500 SFXN1_3; sideroflexin-1/3
D 124543797 sideroflexin-2 K23501 SFXN2; sideroflexin-2
C Other regulator of mitochondrial biogenesis
D 124542906 carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 124535210 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 124534424 F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 124537785 host cell factor 1-like K14966 HCFC1; host cell factor 1
D 124532704 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 124534572 lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 124543016 protein SERAC1 K23504 SERAC1; protein SERAC1
D 124538474 protein UXT homolog K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 124538478 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 124530796 uncharacterized protein LOC124530796 isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 124543995 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 124542010 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 124540176 protein NDUFAF4 homolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 124541903 arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 124531071 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 124538005 protein arginine methyltransferase NDUFAF7 homolog, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 124540636 uncharacterized protein LOC124540636 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 124529865 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 124542599 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 124530825 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 124540174 reticulon-4-interacting protein 1, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 124536493 reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 124530293 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 124544070 succinate dehydrogenase assembly factor 2-A, mitochondrial-like K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 124541534 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 124537156 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 124532369 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 124532306 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 124529750 uncharacterized protein LOC124529750 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 124533499 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 124533500 protein brawnin K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
C Complex-IV assembly factors
D 124536650 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 124536318 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 124541609 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 124543492 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 124535533 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 124539313 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7
D 124533474 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 124536147 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 124543769 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 124534558 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 124534495 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 124532126 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 124532418 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 124534794 mitochondrial inner membrane protein OXA1L-like K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 124542994 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 124531758 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 124544416 leucine-rich PPR motif-containing protein, mitochondrial-like K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 124531663 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 124533776 COA8 family protein CBG23705, mitochondrial K23506 APOPT1; apoptogenic protein 1
D 124533499 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 124536191 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 124535004 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 124531270 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 124529735 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 124539931 ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 124533929 transmembrane GTPase Marf K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 124540692 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 124538223 optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 124530897 putative OPA3-like protein CG13603 K23166 OPA3; optic atrophy 3 protein
D 124534089 TP53-regulated inhibitor of apoptosis 1-like K17968 TRIAP1; TRIAP1/MDM35 family protein
D 124537998 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 124544057 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 124531065 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 124543534 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 124536183 mitochondrial carrier homolog 2-like K17885 MTCH; mitochondrial carrier
D 124540753 transport and Golgi organization protein 11 K22076 MFF; mitochondrial fission factor
D 124536158 ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 124536548 mitochondrial cardiolipin hydrolase-like K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 124542327 uncharacterized protein LOC124542327 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 124536359 mitochondrial cardiolipin hydrolase-like K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 124530782 mitoguardin K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 124529615 actin-5C K05692 ACTB_G1; actin beta/gamma 1
D 124529616 actin, cytoplasmic A3a K05692 ACTB_G1; actin beta/gamma 1
D 124535686 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 124532693 phagocyte signaling-impaired protein K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 124531099 protein l(2)37Cc K17080 PHB1; prohibitin 1
D 124535730 prohibitin-2 K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 124544057 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 124541016 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
C Morphogenesis factors
D 124544292 sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25
D 124533350 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 124539622 MICOS complex subunit Mic60-like K17785 IMMT; MICOS complex subunit MIC60
D 124539722 MICOS complex subunit Mic60-like isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 124532710 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 124529611 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 124537626 E3 ubiquitin-protein ligase Nedd-4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 124530270 protein misato K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 124538661 autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 124531029 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 124538283 cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 124530801 cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 124537180 autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 124540793 beclin-1-like protein K08334 BECN; beclin
D 124534650 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 124536079 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 124542926 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 124532081 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 124529730 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12
D 124531262 beclin 1-associated autophagy-related key regulator isoform X1 K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 124535454 autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 124529593 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 124530533 E3 ubiquitin-protein ligase NRDP1 isoform X1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 124529743 protein CLEC16A homolog K19513 CLEC16A; protein CLEC16A
D 124537998 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 124530829 activating molecule in BECN1-regulated autophagy protein 1-like K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 124542970 autophagy-related protein 13 homolog K08331 ATG13; autophagy-related protein 13
D 124539271 autophagy-related protein 13 homolog isoform X1 K08331 ATG13; autophagy-related protein 13
D 124534380 serine/threonine-protein kinase unc-51 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 124530833 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 124540508 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG
D 124538879 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 124529723 E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 124531586 FUN14 domain-containing protein 1A-like isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
D 124540260 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 124532704 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 124538741 uncharacterized protein LOC124538741 K10435 MAP1LC; microtubule-associated protein 1 light chain
D 124533521 tectonin beta-propeller repeat-containing protein isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 124534296 bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 124536510 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
!
#
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024