ICD-11 International Classification of Diseases

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 01 Certain infectious or parasitic diseases
 
 02 Neoplasms
 
 03 Diseases of the blood or blood-forming organs
   Anaemias or other erythrocyte disorders
     Nutritional or metabolic anaemias
     Haemolytic anaemias
       Congenital haemolytic anaemia
         3A10  Hereditary haemolytic anaemia
           3A10.0  Haemolytic anaemias due to hexose monophosphate shunt or glutathione metabolism anomalies
             3A10.00  Haemolytic anaemia due to glucose-6-phosphate dehydrogenase deficiency
             3A10.0Y  Other specified haemolytic anaemias due to hexose monophosphate shunt or glutathione metabolism anomalies
             3A10.0Z  Haemolytic anaemias due to hexose monophosphate shunt or glutathione metabolism anomalies, unspecified
           3A10.1  Haemolytic anaemia due to adenosine deaminase excess
           3A10.2  Hereditary elliptocytosis
           3A10.3  Familial pseudohyperkalaemia
           3A10.Y  Other specified hereditary haemolytic anaemia
           3A10.Z  Hereditary haemolytic anaemia, unspecified
         3A1Y  Other specified congenital haemolytic anaemia
       Acquired haemolytic anaemia
       3A4Z  Haemolytic anaemias, unspecified
     3A50  Thalassaemias
     3A51  Sickle cell disorders or other haemoglobinopathies
     Pure red cell aplasia
     3A70  Aplastic anaemia
     3A71  Anaemia due to chronic disease
     3A72  Sideroblastic anaemia
     3A73  Congenital dyserythropoietic anaemia
     Polycythaemia
     3A90  Anaemia due to acute disease
     3A91  Congenital methaemoglobinaemia
     3A92  Hereditary methaemoglobinaemia
     3A93  Acquired methaemoglobinaemia
     3A94  Acute posthaemorrhagic anaemia
     3A9Y  Other specified anaemias or erythrocyte disorders
     3A9Z  Anaemias or other erythrocyte disorders, unspecified
   Coagulation defects, purpura or other haemorrhagic or related conditions
   Diseases of spleen
   3C0Y  Other specified diseases of the blood or blood-forming organs
   3C0Z  Diseases of the blood or blood-forming organs, unspecified
 
 04 Diseases of the immune system
   Primary immunodeficiencies
   4A20  Acquired immunodeficiencies
   Nonorgan specific systemic autoimmune disorders
   Autoinflammatory disorders
   Allergic or hypersensitivity conditions
   Immune system disorders involving white cell lineages
     4B00  Disorders of neutrophil number
     4B01  Disorders of neutrophil function
       4B01.0  Constitutional disorders of neutrophil function
         4B01.00  Disorders of neutrophil adhesion
         4B01.01  Disorders of neutrophil chemotaxis
         4B01.02  Disorders of neutrophil granule formation or release
         4B01.03  Disorders of neutrophil oxidative metabolism
         4B01.0Y  Other specified constitutional disorders of neutrophil function
         4B01.0Z  Constitutional disorders of neutrophil function, unspecified
       4B01.1  Acquired disorders of neutrophil function
       4B01.Z  Disorders of neutrophil function, unspecified
     4B02  Eosinopenia
     4B03  Eosinophilia
     4B04  Disorders with decreased monocyte counts
     4B05  Disorders with increased monocyte counts
     4B06  Acquired lymphopenia
     4B07  Acquired lymphocytosis
     4B0Y  Other specified immune system disorders involving white cell lineages
     4B0Z  Immune system disorders involving white cell lineages, unspecified
   Certain disorders involving the immune system
   4B40  Diseases of thymus
   4B4Y  Other specified diseases of the immune system
   4B4Z  Diseases of the immune system, unspecified
 
 05 Endocrine, nutritional or metabolic diseases
   Endocrine diseases
   Nutritional disorders
   Metabolic disorders
     Inborn errors of metabolism
       5C50  Inborn errors of amino acid or other organic acid metabolism
         5C50.0  Phenylketonuria
         5C50.1  Disorders of tyrosine metabolism
           5C50.10  Alkaptonuria
           5C50.11  Tyrosinaemia type 1
           5C50.12  Tyrosinaemia type 2
           5C50.1Y  Other specified disorders of tyrosine metabolism
           5C50.1Z  Disorders of tyrosine metabolism, unspecified
         5C50.2  Disorders of histidine metabolism
           5C50.20  Histidinaemia
           5C50.21  Urocanic aciduria
           5C50.2Y  Other specified disorders of histidine metabolism
           5C50.2Z  Disorders of histidine metabolism, unspecified
         5C50.3  Disorders of tryptophan metabolism
         5C50.4  Disorders of lysine or hydroxylysine metabolism
         5C50.5  Disorders of the gamma-glutamyl cycle
         5C50.6  Disorders of serine metabolism
         5C50.7  Disorders of glycine metabolism
           5C50.70  Glycine encephalopathy
           5C50.71  Sarcosinaemia
           5C50.7Y  Other specified disorders of glycine metabolism
           5C50.7Z  Disorders of glycine metabolism, unspecified
         5C50.8  Disorders of proline or hydroxyproline metabolism
         5C50.9  Disorders of ornithine metabolism
         5C50.A  Disorders of urea cycle metabolism
           5C50.A0  Argininosuccinic aciduria
           5C50.A1  Carbamoylphosphate synthetase deficiency
           5C50.A2  Argininaemia
           5C50.A3  Citrullinaemia
           5C50.AY  Other specified disorders of urea cycle metabolism
           5C50.AZ  Disorders of urea cycle metabolism, unspecified
         5C50.B  Disorders of methionine cycle or sulphur amino acid metabolism
         5C50.C  Disorders of beta or omega amino acid metabolism
         5C50.D  Disorders of branched-chain amino acid metabolism
           5C50.D0  Maple-syrup-urine disease
           5C50.DY  Other specified disorders of branched-chain amino acid metabolism
           5C50.DZ  Disorders of branched-chain amino acid metabolism, unspecified
         5C50.E  Organic aciduria
         5C50.F  Disorders of peptide metabolism
           5C50.F0  Prolidase deficiency
           5C50.F1  Carnosinaemia
           5C50.F2  Homocarnosinosis
           5C50.FY  Other specified disorders of peptide metabolism
           5C50.FZ  Disorders of peptide metabolism, unspecified
         5C50.G  Trimethylaminuria
         5C50.Y  Other specified inborn errors of amino acid or other organic acid metabolism
         5C50.Z  Inborn errors of amino acid or other organic acid metabolism, unspecified
       5C51  Inborn errors of carbohydrate metabolism
         5C51.0  Disorders of the pentose phosphate pathway
         5C51.1  Disorders of glycerol metabolism
         5C51.2  Disorders of glyoxylate metabolism
           5C51.20  Primary hyperoxaluria type 1
           5C51.2Y  Other specified disorders of glyoxylate metabolism
           5C51.2Z  Disorders of glyoxylate metabolism, unspecified
         5C51.3  Glycogen storage disease
         5C51.4  Disorders of galactose metabolism
           5C51.40  Galactose-1-phosphate uridyltransferase deficiency
           5C51.41  Galactokinase deficiency
           5C51.42  Glucose or galactose intolerance of newborn
           5C51.4Y  Other specified disorders of galactose metabolism
           5C51.4Z  Disorders of galactose metabolism, unspecified
         5C51.5  Disorders of fructose metabolism
           5C51.50  Hereditary fructose intolerance
           5C51.5Y  Other specified disorders of fructose metabolism
           5C51.5Z  Disorders of fructose metabolism, unspecified
         5C51.Y  Other specified inborn errors of carbohydrate metabolism
         5C51.Z  Inborn errors of carbohydrate metabolism, unspecified
       5C52  Inborn errors of lipid metabolism
         5C52.0  Inborn errors of fatty acid oxidation or ketone body metabolism
           5C52.00  Disorders of carnitine transport or the carnitine cycle
           5C52.01  Disorders of mitochondrial fatty acid oxidation
           5C52.02  Disorders of ketone body metabolism
           5C52.03  Sjögren-Larsson syndrome
           5C52.0Y  Other specified inborn errors of fatty acid oxidation or ketone body metabolism
           5C52.0Z  Inborn errors of fatty acid oxidation or ketone body metabolism, unspecified
         5C52.1  Inborn errors of sterol metabolism
           5C52.10  Disorders of cholesterol synthesis
           5C52.11  Bile acid synthesis defect with cholestasis
           5C52.1Y  Other specified inborn errors of sterol metabolism
           5C52.1Z  Inborn errors of sterol metabolism, unspecified
         5C52.2  Neutral lipid storage disease
         5C52.Y  Other specified inborn errors of lipid metabolism
         5C52.Z  Inborn errors of lipid metabolism, unspecified
       5C53  Inborn errors of energy metabolism
         5C53.0  Disorders of pyruvate metabolism
           5C53.00  Pyruvate kinase deficiency
           5C53.01  Lactate dehydrogenase deficiency
           5C53.02  Pyruvate dehydrogenase complex deficiency
           5C53.03  Pyruvate carboxylase deficiency
           5C53.0Y  Other specified disorders of pyruvate metabolism
           5C53.0Z  Disorders of pyruvate metabolism, unspecified
         5C53.1  Disorders of the citric acid cycle
         5C53.2  Disorders of mitochondrial oxidative phosphorylation
         5C53.3  Disorders of mitochondrial membrane transport
         5C53.4  Disorders of creatine metabolism
         5C53.Y  Other specified inborn errors of energy metabolism
         5C53.Z  Inborn errors of energy metabolism, unspecified
       5C54  Inborn errors of glycosylation or other specified protein modification
       5C55  Inborn errors of purine, pyrimidine or nucleotide metabolism
         5C55.0  Disorders of purine metabolism
           5C55.00  Xanthinuria
           5C55.01  Lesch-Nyhan syndrome
           5C55.0Y  Other specified disorders of purine metabolism
           5C55.0Z  Disorders of purine metabolism, unspecified
         5C55.1  Disorders of pyrimidine metabolism
         5C55.2  Disorders of nucleotide metabolism
         5C55.Y  Other specified inborn errors of purine, pyrimidine or nucleotide metabolism
         5C55.Z  Inborn errors of purine, pyrimidine or nucleotide metabolism, unspecified
       5C56  Lysosomal diseases
         5C56.0  Sphingolipidosis
         5C56.1  Neuronal ceroid lipofuscinosis
         5C56.2  Glycoproteinosis
         5C56.3  Mucopolysaccharidosis
         5C56.4  Disorders of sialic acid metabolism
         5C56.Y  Other specified lysosomal diseases
         5C56.Z  Lysosomal diseases, unspecified
       5C57  Peroxisomal diseases
       5C58  Inborn errors of porphyrin or heme metabolism
         5C58.0  Disorders of bilirubin metabolism or excretion
           5C58.00  Crigler-Najjar syndrome
           5C58.01  Gilbert syndrome
           5C58.02  Dubin-Johnson syndrome
           5C58.03  Progressive familial intrahepatic cholestasis
           5C58.04  Benign recurrent intrahepatic cholestasis
           5C58.0Y  Other specified disorders of bilirubin metabolism or excretion
           5C58.0Z  Disorders of bilirubin metabolism or excretion, unspecified
         5C58.1  Porphyrias
         5C58.Y  Other specified inborn errors of porphyrin or heme metabolism
         5C58.Z  Inborn errors of porphyrin or heme metabolism, unspecified
       5C59  Inborn errors of neurotransmitter metabolism
         5C59.0  Disorders of biogenic amine metabolism
           5C59.00  Disorders of catecholamine synthesis
           5C59.01  Disorders of pterin metabolism
           5C59.0Y  Other specified disorders of biogenic amine metabolism
           5C59.0Z  Disorders of biogenic amine metabolism, unspecified
         5C59.1  Disorders of gamma aminobutyric acid metabolism
         5C59.2  Disorders of pyridoxine metabolism
         5C59.Y  Other specified inborn errors of neurotransmitter metabolism
         5C59.Z  Inborn errors of neurotransmitter metabolism, unspecified
       5C5A  Alpha-1-antitrypsin deficiency
       5C5Y  Other specified inborn errors of metabolism
       5C5Z  Inborn errors of metabolism, unspecified
     Disorders of metabolite absorption or transport
       5C60  Disorders of amino acid absorption or transport
       5C61  Disorders of carbohydrate absorption or transport
       5C62  Disorders of lipid absorption or transport
       5C63  Disorders of vitamin or non-protein cofactor absorption or transport
         5C63.0  Disorders of cobalamin metabolism or transport
         5C63.1  Disorders of folate metabolism or transport
         5C63.2  Disorders of vitamin D metabolism or transport
           5C63.20  Hypocalcaemic vitamin D dependent rickets
           5C63.21  Hypocalcaemic vitamin D resistant rickets
           5C63.22  Hypophosphataemic rickets
           5C63.2Y  Other specified disorders of vitamin D metabolism or transport
           5C63.2Z  Disorders of vitamin D metabolism or transport, unspecified
         5C63.Y  Other specified disorders of vitamin or non-protein cofactor absorption or transport
         5C63.Z  Disorders of vitamin or non-protein cofactor absorption or transport, unspecified
       5C64  Disorders of mineral absorption or transport
         5C64.0  Disorders of copper metabolism
           5C64.00  Wilson disease
           5C64.0Y  Other specified disorders of copper metabolism
           5C64.0Z  Disorders of copper metabolism, unspecified
         5C64.1  Disorders of iron metabolism
           5C64.10  Iron overload diseases
           5C64.1Y  Other specified disorders of iron metabolism
           5C64.1Z  Disorders of iron metabolism, unspecified
         5C64.2  Disorders of zinc metabolism
           5C64.20  Acrodermatitis enteropathica
           5C64.21  Zinc deficiency syndromes
           5C64.2Y  Other specified disorders of zinc metabolism
           5C64.2Z  Disorders of zinc metabolism, unspecified
         5C64.3  Disorders of phosphorus metabolism or phosphatases
         5C64.4  Disorders of magnesium metabolism
           5C64.40  Hypermagnesaemia
           5C64.41  Hypomagnesaemia
           5C64.4Z  Disorders of magnesium metabolism, unspecified
         5C64.5  Disorders of calcium metabolism
         5C64.6  Disorders of sodium metabolism
         5C64.7  Disorders of chloride metabolism
         5C64.Y  Disorders of other specified mineral absorption and transport
         5C64.Z  Disorders of mineral absorption or transport, unspecified
       5C6Y  Other specified disorders of metabolite absorption or transport
       5C6Z  Disorders of metabolite absorption or transport, unspecified
     Disorders of fluid, electrolyte or acid-base balance
     Disorders of lipoprotein metabolism or certain specified lipidaemias
       5C80  Hyperlipoproteinaemia
       5C81  Hypolipoproteinaemia
       5C8Y  Other specified disorders of lipoprotein metabolism or lipidaemias
       5C8Z  Unspecified disorders of lipoprotein metabolism or lipidaemias
     5C90  Metabolic or transporter liver disease
       5C90.0  Liver diseases due to urea cycle defects
       5C90.1  Liver diseases due to disorders of porphyrin or bilirubin metabolism or transport
       5C90.2  Liver diseases due to disorders of amino acid metabolism
       5C90.3  Liver disease due to disorders of lysosomal storage
       5C90.4  Liver diseases due to mitochondrial disorders
       5C90.5  Liver diseases due to disorders of mineral metabolism
       5C90.Y  Other specified metabolic or transporter liver disease
       5C90.Z  Metabolic or transporter liver disease, unspecified
     Other metabolic disorders
     5D2Z  Metabolic disorders, unspecified
   Postprocedural endocrine or metabolic disorders
 
 06 Mental, behavioural or neurodevelopmental disorders
 
 07 Sleep-wake disorders
 
 08 Diseases of the nervous system
 
 09 Diseases of the visual system
 
 10 Diseases of the ear or mastoid process
 
 11 Diseases of the circulatory system
 
 12 Diseases of the respiratory system
   Upper respiratory tract disorders
   Certain lower respiratory tract diseases
   Lung infections
   Lung diseases due to external agents
   Respiratory diseases principally affecting the lung interstitium
     CB00  Acute respiratory distress syndrome
     CB01  Pulmonary oedema
     CB02  Pulmonary eosinophilia
     CB03  Idiopathic interstitial pneumonitis
     CB04  Primary interstitial lung diseases specific to infancy or childhood
       CB04.0  Diffuse pulmonary developmental disorders
       CB04.1  Pulmonary lymphatic dysplasia syndromes
       CB04.2  Disorders of surfactant metabolism
       CB04.3  Alveolar or peri-alveolar conditions
       CB04.4  Pulmonary capillaritis
       CB04.5  Brain-lung-thyroid syndrome
       CB04.6  Chronic pneumonitis of infancy
       CB04.7  Neuroendocrine cell hyperplasia of infancy
       CB04.Y  Other specified primary interstitial lung diseases specific to infancy or childhood
       CB04.Z  Primary interstitial lung diseases specific to infancy or childhood, unspecified
     CB05  Interstitial lung diseases associated with systemic diseases
     CB06  Pulmonary alveolar microlithiasis
     CB07  Lymphangioleiomyomatosis
     CB0Y  Other specified respiratory diseases principally affecting the lung interstitium
     CB0Z  Respiratory diseases principally affecting the lung interstitium, unspecified
   Pleural, diaphragm or mediastinal disorders
   CB40  Certain diseases of the respiratory system
   CB41  Respiratory failure
   Postprocedural disorders of the respiratory system
   CB7Z  Diseases of the respiratory system, unspecified
 
 13 Diseases of the digestive system
 
 14 Diseases of the skin
   Certain skin disorders attributable to infection or infestation
   Inflammatory dermatoses
   Metabolic and nutritional disorders affecting the skin
     EB90  Dermatoses resulting from disturbed metabolic processes
       EB90.0  Diabetic skin lesions
       EB90.1  Cutaneous mucinosis
       EB90.2  Cutaneous and subcutaneous xanthomata
         EB90.20  Plane xanthoma
         EB90.21  Tuberous xanthoma
         EB90.22  Eruptive xanthoma
         EB90.23  Tendinous xanthoma
         EB90.24  Xanthoma due to specified disorder of lipid metabolism
         EB90.2Z  Cutaneous and subcutaneous xanthomata of unspecified type
       EB90.3  Porphyria or pseudoporphyria affecting the skin
       EB90.4  Calcification of skin or subcutaneous tissue
     EB9Y  Other specified metabolic and nutritional disorders affecting the skin
   Genetic and developmental disorders affecting the skin
   Sensory and psychological disorders affecting the skin
   Skin disorders involving specific cutaneous structures
   Skin disorders involving certain specific body regions
   Skin disorders associated with pregnancy, the neonatal period and infancy
   Adverse cutaneous reactions to medication
   Skin disorders provoked by external factors
   Benign proliferations, neoplasms and cysts of the skin
   Disorders of the skin of uncertain or unpredictable malignant potential
   Cutaneous markers of internal disorders
   Postprocedural disorders of the skin
   EM0Y  Other specified diseases of the skin
   EM0Z  Skin disease of unspecified nature
 
 15 Diseases of the musculoskeletal system or connective tissue
 
 16 Diseases of the genitourinary system
 
 17 Conditions related to sexual health
 
 18 Pregnancy, childbirth or the puerperium
 
 19 Certain conditions originating in the perinatal period
   Fetus or newborn affected by maternal factors or by complications of pregnancy, labour or delivery
   Disorders of newborn related to length of gestation or fetal growth
   Birth injury
   Infections of the fetus or newborn
   Haemorrhagic or haematological disorders of fetus or newborn
   Neurological disorders specific to the perinatal or neonatal period
   Respiratory disorders specific to the perinatal or neonatal period
   Cardiovascular disorders present in the perinatal or neonatal period
   Transitory endocrine or metabolic disorders specific to fetus or newborn
     KB60  Transitory disorders of carbohydrate metabolism specific to fetus or newborn
       KB60.0  Syndrome of infant of mother with gestational diabetes
       KB60.1  Syndrome of infant of a diabetic mother, type 1 or 2, nongestational, insulin dependent
       KB60.2  Neonatal diabetes mellitus
       KB60.3  Neonatal hyperglycaemia
       KB60.4  Neonatal hypoglycaemia
       KB60.Y  Other specified transitory disorders of carbohydrate metabolism specific to fetus or newborn
       KB60.Z  Transitory disorders of carbohydrate metabolism specific to fetus or newborn, unspecified
     KB61  Transitory neonatal disorders of calcium or magnesium metabolism
       KB61.0  Neonatal hypomagnesaemia
       KB61.1  Neonatal tetany without calcium or magnesium deficiency
       KB61.2  Neonatal hypocalcaemia
       KB61.3  Neonatal osteopenia
       KB61.Y  Other specified transitory neonatal disorders of calcium or magnesium metabolism
       KB61.Z  Transitory neonatal disorders of calcium or magnesium metabolism, unspecified
     KB62  Transitory neonatal disorders of thyroid function
     KB63  Certain specified transitory neonatal electrolyte or metabolic disturbances
     KB64  Transitory neonatal hypoparathyroidism
     KB6Z  Transitory endocrine or metabolic disorders specific to fetus or newborn, unspecified
   Digestive system disorders of fetus or newborn
   Genitourinary system disorders specific to the perinatal or neonatal period
   Disorders involving the integument of fetus or newborn
   Disturbances of temperature regulation of newborn
   Certain disorders originating in the perinatal period
   KD5Z  Conditions originating in the perinatal or neonatal period, unspecified
 
 20 Developmental anomalies
   Structural developmental anomalies primarily affecting one body system
   Multiple developmental anomalies or syndromes
     LD20  Syndromes with central nervous system anomalies as a major feature
     LD21  Syndromes with eye anomalies as a major feature
     LD22  Syndromes with dental anomalies as a major feature
     LD23  Syndromes with vascular anomalies as a major feature
     LD24  Syndromes with skeletal anomalies as a major feature
     LD25  Syndromes with face or limb anomalies as a major feature
     LD26  Syndromes with limb anomalies as a major feature
     LD27  Syndromes with skin or mucosal anomalies as a major feature
     LD28  Syndromes with connective tissue involvement as a major feature
     LD29  Syndromes with obesity as a major feature
     LD2A  Malformative disorders of sex development
       LD2A.0  Ovotesticular disorder of sex development
       LD2A.1  46,XY gonadal dysgenesis
       LD2A.2  Testicular agenesis
       LD2A.3  46,XY disorder of sex development due to a defect in testosterone metabolism
       LD2A.4  46,XY disorder of sex development due to androgen resistance
       LD2A.Y  Other specified malformative disorders of sex development
       LD2A.Z  Malformative disorders of sex development, unspecified
     LD2B  Syndromes with premature ageing appearance as a major feature
     LD2C  Overgrowth syndromes
     LD2D  Phakomatoses or hamartoneoplastic syndromes
     LD2E  Syndromes with structural anomalies due to inborn errors of metabolism
     LD2F  Syndromes with multiple structural anomalies, without predominant body system involvement
     LD2G  Conjoined twins
     LD2H  Syndromic genetic deafness
     LD2Y  Other specified multiple developmental anomalies or syndromes
     LD2Z  Multiple developmental anomalies or syndromes, unspecified
   Chromosomal anomalies, excluding gene mutations
   LD90  Conditions with disorders of intellectual development as a relevant clinical feature
   LD9Y  Other specified developmental anomalies
   LD9Z  Developmental anomalies, unspecified
 
 21 Symptoms, signs or clinical findings, not elsewhere classified
 
 22 Injury, poisoning or certain other consequences of external causes
 
 23 External causes of morbidity or mortality
 
 24 Factors influencing health status or contact with health services
 
 25 Codes for special purposes
 
 26 Supplementary Chapter Traditional Medicine Conditions
 
 27 Supplementary section for functioning assessment

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Last updated: January 28, 2025
ICD-11 by World Health Organization, Version 02/2024