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ENTRY	nt06020
Name	beta-Oxidation in mitochondria
Category	Pathway view; Lipid/glycolipid metabolism
Pathway	hsa00071 Fatty acid degradation
Module	hsa_M00086 beta-Oxidation, acyl-CoA synthesis hsa_M00087 beta-Oxidation
Disease	H00525 Disorders of mitochondrial fatty-acid oxidation
Display	drug-target relation   disease type

N00812    Carnitine(blood) − SLC22A5 → Carnitine     CDSP     SLC22A5*   N00814    Palmitoylcarnitine.. − SLC25A20 → Palmitoylcarnitine..     CACT deficiency     SLC25A20*   N00765    Palmitate − (ACSL,ACSBG) ⇉ CPT1A/B/C ⇉ CPT2 → Palmitoyl-CoA     CPT I deficiency         CPT1A*     CPT II deficiency             CPT2*   N00804    Acyl-CoA(n) − (ACADM,ACADL,ACADV.. ⇉ ((ECHS1+HADH),HADH.. ⇉ (ACAA2,HADHB,ACAT1.. → Acyl-CoA(n-2)     MCAD deficiency     ACADM*     VLCAD deficiency     ACADVL*     SCAD deficiency     ACADS*     ECHS1 deficiency         ECHS1*     HADH deficiency         HADH*     LCHAD deficiency         HADHA*     LCKAT deficiency             HADHB*

		Disease name	Disease category
CDSP	H01589	Systemic primary carnitine deficiency	Inherited metabolic disorder
CACT deficiency	H01983	Carnitine-acylcarnitine translocase deficiency	Inherited metabolic disorder
CPT I deficiency	H01981	Carnitine palmitoyltransferase I deficiency	Inherited metabolic disorder, Mitochondrial disease
CPT II deficiency	H01982	Carnitine palmitoyltransferase II deficiency	Inherited metabolic disorder, Mitochondrial disease
MCAD deficiency	H00488	MCAD deficiency	Inherited metabolic disorder, Mitochondrial disease
VLCAD deficiency	H00392	Very long-chain acyl-CoA dehydrogenase deficiency	Inherited metabolic disorder, Mitochondrial disease
SCAD deficiency	H01980	SCAD deficiency	Inherited metabolic disorder, Mitochondrial disease
ECHS1 deficiency	H00525	Disorders of mitochondrial fatty-acid oxidation	Inherited metabolic disorder
HADH deficiency	H01364	3-Hydroxyacyl-CoA dehydrogenase deficiency	Inherited metabolic disorder, Mitochondrial disease
LCHAD deficiency	H00489	LCHAD deficiency	Inherited metabolic disorder, Mitochondrial disease
LCKAT deficiency	H01352	Mitochondrial trifunctional protein deficiency	Inherited metabolic disorder, Mitochondrial disease