KEGG    Network variation - beta-Oxidation in mitochondria
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ENTRYnt06020
Namebeta-Oxidation in mitochondria
CategoryPathway view; Lipid/glycolipid metabolism
Pathwayhsa00071 Fatty acid degradation
Modulehsa_M00086 beta-Oxidation, acyl-CoA synthesis
hsa_M00087 beta-Oxidation
DiseaseH00525 Disorders of mitochondrial fatty-acid oxidation
Display drug-target relation   disease type
N00812   
    CDSP
 
N00814   
    CACT deficiency
 
N00765   
    CPT I deficiency
    CPT II deficiency
 
N00804   
    MCAD deficiency
    VLCAD deficiency
    SCAD deficiency
    ECHS1 deficiency
    HADH deficiency
    LCHAD deficiency
    LCKAT deficiency

CDSPH01589Systemic primary carnitine deficiency
CACT deficiencyH01983Carnitine-acylcarnitine translocase deficiency
CPT I deficiencyH01981Carnitine palmitoyltransferase I deficiency
CPT II deficiencyH01982Carnitine palmitoyltransferase II deficiency
MCAD deficiencyH00488MCAD deficiency
VLCAD deficiencyH00392VLCAD deficiency
SCAD deficiencyH01980SCAD deficiency
HADH deficiencyH013643-Hydroxyacyl-CoA dehydrogenase deficiency
LCHAD deficiencyH00489LCHAD deficiency
LCKAT deficiencyH01352Mitochondrial trifunctional protein deficiency