![]() |
ENTRY | nt06020 |
Name | beta-Oxidation in mitochondria |
Category | Pathway view; Lipid/glycolipid metabolism |
Pathway | hsa00071 Fatty acid degradation |
Module | hsa_M00086 beta-Oxidation, acyl-CoA synthesis hsa_M00087 beta-Oxidation |
Disease | H00525 Disorders of mitochondrial fatty-acid oxidation |
Display | drug-target relation disease type |
|
CDSP | H01589 | Systemic primary carnitine deficiency |
CACT deficiency | H01983 | Carnitine-acylcarnitine translocase deficiency |
CPT I deficiency | H01981 | Carnitine palmitoyltransferase I deficiency |
CPT II deficiency | H01982 | Carnitine palmitoyltransferase II deficiency |
MCAD deficiency | H00488 | MCAD deficiency |
VLCAD deficiency | H00392 | VLCAD deficiency |
SCAD deficiency | H01980 | SCAD deficiency |
HADH deficiency | H01364 | 3-Hydroxyacyl-CoA dehydrogenase deficiency |
LCHAD deficiency | H00489 | LCHAD deficiency |
LCKAT deficiency | H01352 | Mitochondrial trifunctional protein deficiency |