KEGG   ENZYME: 1.14.11.18
Entry
EC 1.14.11.18               Enzyme                                 
Name
phytanoyl-CoA dioxygenase;
phytanoyl-CoA hydroxylase
Class
Oxidoreductases;
Acting on paired donors, with incorporation or reduction of molecular oxygen;
With 2-oxoglutarate as one donor, and incorporation of one atom of oxygen into each donor
Sysname
phytanoyl-CoA, 2-oxoglutarate:oxygen oxidoreductase (2-hydroxylating)
Reaction(IUBMB)
phytanoyl-CoA + 2-oxoglutarate + O2 = 2-hydroxyphytanoyl-CoA + succinate + CO2 [RN:R05722]
Reaction(KEGG)
R05722
Substrate
phytanoyl-CoA [CPD:C02060];
2-oxoglutarate [CPD:C00026];
O2 [CPD:C00007]
Product
2-hydroxyphytanoyl-CoA [CPD:C07343];
succinate [CPD:C00042];
CO2 [CPD:C00011]
Comment
Part of the peroxisomal phytanic acid alpha-oxidation pathway. Requires Fe2+ and ascorbate.
History
EC 1.14.11.18 created 2000
Orthology
K00477  phytanoyl-CoA hydroxylase
Genes
HSA5264(PHYH)
PTR450310(PHYH)
PPS100983012(PHYH)
GGO109025269(PHYH)
PON100444487(PHYH)
MCC695915(PHYH)
MCF102126599(PHYH)
CSAB103237904(PHYH)
CATY105583866(PHYH)
PANU100462930(PHYH)
TGE112631952(PHYH)
RRO104664458(PHYH)
RBB108531286(PHYH)
TFN117081977(PHYH)
PTEH111550024(PHYH)
CJC100394030(PHYH)
SBQ101043326(PHYH)
CSYR103271604(PHYH)
MMUR105871998(PHYH)
OGA100963396(PHYH)
MMU16922(Phyh)
MCAL110310225(Phyh)
MPAH110333915(Phyh)
RNO114209(Phyh)
MCOC116082272(Phyh)
MUN110552358(Phyh)
CGE100774732(Phyh)
PLEU114708537(Phyh)
NGI103749079(Phyh)
HGL101717354(Phyh) 106007539
CPOC100721980(Phyh)
CCAN109690084(Phyh)
DORD105984435(Phyh)
DSP122113177(Phyh)
NCAR124961617 124962141
OCU100338511 100339259 100339756 100344175 100344679 100345653(PHYHD1) 100356864
OPI101522852(PHYH)
TUP102475212(PHYH)
CFA478000
VVP112912718 112933299(PHYH)
VLG121497417(PHYH) 121498121
AML100467763(PHYH) 100470234
UMR103664176(PHYH) 103682385
UAR123786156(PHYH) 123786332 123789992 123789993
ELK111155514
LLV125106044 125106045
MPUF101676398 101676988(PHYH) 101690963
ORO101386900(PHYH)
EJU114203621 114203622 114210443
ZCA113922491(PHYH) 113932647
MLX118021573(PHYH)
FCA101098238(PHYH)
PYU121014803(PHYH)
PBG122472302(PHYH)
PTG102957487(PHYH) 102969046(PHYHD1)
PPAD109273714(PHYH)
AJU106971027(PHYH)
HHV120236938(PHYH)
BTA100300115 281400(PHYH)
BOM102270224 102286749(PHYH)
BIU109567956(PHYH)
BBUB102397235(PHYH) 102397569
CHX102179212(PHYH)
OAS101107212(PHYH)
ODA120859242 120859889 120869305(PHYH)
CCAD122448246 122448315(PHYH)
SSC100134962(PHYH)
CFR102511029(PHYH)
CBAI105072463(PHYH)
CDK105100655(PHYH)
VPC102527327(PHYH)
BACU103000323(PHYH)
LVE103088031(PHYH)
OOR101276116(PHYH)
DLE111178076(PHYH)
PCAD102988147(PHYH)
PSIU116749469(PHYH)
ECB100056651 100069176
EPZ103567243(PHYH) 103567246
EAI106840463(PHYH) 106840471
MYB102244663(PHYH)
MYD102753013(PHYH)
MMYO118677505(PHYH)
MLF102418211(PHYH)
MNA107530239(PHYH)
PKL118727183(PHYH)
HAI109393810(PHYH)
DRO112322870(PHYH)
SHON119000810(PHYH)
AJM119048014(PHYH)
PDIC114492390(PHYH)
PHAS123831285(PHYH)
MMF118634453(PHYH)
RFQ117019131(PHYH)
PALE102894373(PHYH)
PGIG120614609(PHYH)
PVP105291696(PHYH)
RAY107504844(PHYH)
MJV108385274(PHYH)
TOD119244695(PHYH)
SARA101550062(PHYH)
LAV100677071(PHYH)
TMU101340562
DNM101417217(PHYH)
MDO100014074(PHYH)
GAS123248484(PHYH)
SHR100927877(PHYH)
PCW110217370(PHYH)
OAA100085334(PHYH)
GGA426601(PHYH)
PCOC116225440(PHYH)
MGP100550784(PHYH)
CJO107318471(PHYH)
NMEL110392271(PHYH)
APLA101791044(PHYH)
ACYG106046211(PHYH)
AFUL116502048(PHYH)
TGU100231512(PHYH)
LSR110470932(PHYH)
SCAN103813563(PHYH)
PMOA120512502(PHYH)
OTC121340578(PHYH)
PRUF121362347(PHYH)
GFR102031343(PHYH)
FAB101813875(PHYH)
PHI102100009(PHYH)
PMAJ107204956(PHYH)
CCAE111923112(PHYH)
CCW104694497(PHYH)
ETL114066630(PHYH)
ZAB102071594(PHYH)
FPG101915232(PHYH)
FCH102060134(PHYH)
CLV102085518(PHYH)
EGZ104135766 104135767
NNI104014617(PHYH)
ACUN113491184(PHYH)
TALA104366565(PHYH) 116959932
PADL103915010 103915028
ACHC115341154 115342279
AAM106485478(PHYH)
AROW112978126(PHYH)
NPD112942375(PHYH)
DNE112994805(PHYH)
ASN102372139(PHYH)
AMJ102572271(PHYH)
CPOO109315799(PHYH)
GGN109292212(PHYH)
PSS102463722(PHYH)
CMY102945710(PHYH)
CPIC101936756(PHYH)
TST117874669(PHYH)
CABI116835457
MRV120395198(PHYH)
ACS100560714 100560911(phyh)
PVT110081229(PHYH)
SUND121931681(PHYH)
PBI103068159(PHYH)
PMUR107295057(PHYH)
TSR106549083(PHYH)
VKO123020004(PHYH)
PMUA114605031 114605888
ZVI118091093 118091319(PHYH)
GJA107118480(PHYH)
STOW125435031(PHYH)
XLA108711219(phyh.L) 446332(phyh.S)
XTR100379998(phyh)
NPR108784804(PHYH)
RTEM120931709(PHYH)
BBUF120983419 120983444 120983453 120983478
BGAR122925395 122927827 122927828 122927829
DRE550521(phyh)
SRX107726059 107743808
SANH107658861
SGH107584013(phyh)
CCAR109066471(phyh)
CAUA113058696(phyh)
PPRM120476744(phyh)
MAMB125245230(phyh)
IPU108280036(phyh)
PHYP113532310(phyh)
SMEO124401850(phyh)
TFD113645677(phyh)
AMEX103026834(phyh)
EEE113591541(phyh)
TRU101069626(phyh)
TNGGSTEN00013261G001
LCO104930594(phyh)
NCC104961091(phyh)
CGOB115028103(phyh)
ELY117248916(phyh)
PLEP121961369(phyh)
SLUC116054611(phyh)
ECRA117938645(phyh)
PFLV114550318(phyh)
GAT120816940(phyh)
PPUG119210075(phyh)
MSAM119909721 119917890(phyh)
CUD121505750(phyh)
ALAT119032313(phyh)
MZE101468356(phyh)
ONL100690874(phyh)
OAU116317031(phyh)
OLA101162091(phyh)
OML112139792(phyh)
XMA102223740(phyh)
XCO114161055(phyh)
XHE116736815(phyh)
PRET103459683(phyh)
PFOR103151536(phyh)
PLAI106962254(phyh)
PMEI106908868(phyh)
GAF122826738(phyh)
CVG107096226(phyh)
CTUL119794476(phyh)
GMU124882945(phyh)
NFU107381937(phyh)
KMR108249286(phyh)
ALIM106530528(phyh)
NWH119428450(phyh)
AOCE111564974(phyh)
CSEM103383104(phyh)
POV109632674(phyh)
SSEN122767283(phyh)
HHIP117757548(phyh)
LCF108874301(phyh)
SDU111225044(phyh)
SLAL111667343(phyh)
XGL120803372(phyh)
HCQ109528844(phyh)
BPEC110161769(phyh)
MALB109960989(phyh)
BSPL114861367(phyh)
SASA100195182(pahx)
OTW112214927 112216927
OMY110490340
OGO123994573
ONE115106260 115133722
SALP112072726(phyh)
SNH120032169(phyh)
ELS105007489(phyh)
SFM108926656(phyh)
PKI111840258(phyh)
AANG118218715(phyh)
LOC102690477(phyh)
PSPA121319842(phyh)
ARUT117415108(phyh)
LCM102366940(PHYH)
CMK103190516(phyh)
RTP109928309(phyh)
BFO118409211 118415139 118415141 118420793
BBEL109477446 109477447 109484574
CIN100176685 100180098
SCLV120327023 120337900 120339602 120339603
SPU115919089 579037
APLC110989925
SKO100367262 100374284 100378442
AME410288
ACER107996052
ALAB122715493
BIM100749150
BBIF117211615
BVK117235005
BVAN117153236
BTER100648165
BPYO122568974
CCAL108625169
OBB114882774
MGEN117223180
NMEA116430568
CGIG122395221 122398422
SOC105204439 105206848 105207428 113005027
MPHA105837351 105839891
AEC105143947 105145740 105153832
ACEP105620509 105624165 105624404
PBAR105430195 105433604 105433940
VEM105558527 105565031 105569056
HST105180958 105181940 105182333
DQU106745938 106746344 106749745
CFO105248435 105252851 105256842
FEX115232836 115237023 115239582 115243840
LHU105678173 105679847 105680092
PGC109854617 109855790 109858383
OBO105281653 105285398 105288037
PCF106789157 106789559
PFUC122515141 122524191
VPS122634177 122635938
NVI100118569 100120956
CSOL105359733 105360218
TPRE106650117 106659374 106660435
MDL103568478 103572359 103575757
CGLO123260068 123265763
FAS105266761 105271908
DAM107041549 107044454
AGIF122849073
CCIN107263505 107268778
TCA658138 659158
DPA109532917 109533967
SOY115889004
ATD109595821
CSET123319217
AGB108909319
LDC111502701 111502703 111512626
NVL108562900 108563537 108565240 108569762
APLN108735674 108740747
PPYR116178945 116179329
OTU111416644 111416667 111421954 111424645
BMOR101739774 105842603 692832
BMAN114249838 114249845 114251834
MSEX115445497 115448817 115448822 115448824 119191265
DPLKGM_202988 KGM_214703 KGM_214829 KGM_214830
BANY112047756
PMAC106707936 106710560
PPOT106103279 106110452
PXU106116060 106119995
PRAP110993805 111003851
ZCE119828660 119828712 119828787 119835716 119836789
HAW110370902 110372496 110382397 110382401
TNL113492453 113502910
SLIU111356654 111363519 111364744 111364832
OFU114350014 114360137 114360138 114360145 114360256 114361993
PXY105381299 105387671 105387692 105387694 105389198 105389742 105392830 105396210
API100159854 100165994 100167257
DNX107163652 107163656 107164790
AGS114128458 114128644
RMD113552876 113553779 113553970
DCI103520915
CLEC106664376 106669420 106669446
HHAL106683056
NLU111043214 111046214
PHUPhum_PHUM274820
FOC113206131 113206926 113210888
ZNE110833304
CSEC111864324
FCD110843001 110853006
DPXDAPPUDRAFT_188919 DAPPUDRAFT_316382 DAPPUDRAFT_321740
DMK116916757 116920964 116921193
PVM113805335 113811729
PJA122250184 122261686
PCHN125026347 125047277
HAME121860504 121862768 121875779
PCLA123756830 123758616
PTRU123507799 123515219
HAZT108671571 108673006
EAF111700402 111706778
ISCIscW_ISCW007193 IscW_ISCW007194
DSV119466002 119466287
RSAN119406265 119406970
RMP119163333 119163463
VDE111249841 111250620
VJA111259895 111268644
TUT107366181 107366879
DPTE113798508
DFR124500431
PTEP107455720
SDM118183906
CELCELE_ZK550.5(ZK550.5) CELE_ZK550.6(ZK550.6)
CBRCBG_00368 CBG_00370
NAINECAME_13565
HROHELRODRAFT_185000
LGILOTGIDRAFT_202643
PCAN112571426
BGT106061655
GAE121367987 121392166
HRF124113145 124121584 124121599 124121625
HRJ124282920 124291902 124291911
CRG105338069
MYI110464938
PMAX117331491
MMER123528791 123543461
OBI106874674
OSN115216346
LAK106170645 106174551
NVE5513549 5520472
EPA110242906 110254831
ATEN116308777
ADF107343439
AMIL114959929
PDAM113685168
SPIS111323781
DGT114521576 114531924
HMG100210387
AQU100640946 105313390 105316730
ATHAT2G01490(PAHX)
ALY9311143
CRB17886344
CSAT104710076 104789908
EUSEUTSA_v10000985mg
BRP103854067
BNA106388861 106416809 106427988
BOE106322865
RSZ108806162 108824279
THJ104823806
CPAP110813412
CIT102611341
CICCICLE_v10016178mg
PVY116144817
MINC123212890
TCC18609786
GRA105785702
GHI107939631 121213926
GAB108465541
DZI111287785 111318050
EGR104416398
GMX100788875 100790934
GSJ114402264 114419759
PVUPHAVU_002G095700g
VRA106766985
VAR108342114
VUN114176452
CCAJ109787702
APRC113858617
MTRMTR_4g084560
CAM101493765
LJALj4g3v0643880.1(Lj4g3v0643880.1) Lj4g3v0643880.2(Lj4g3v0643880.2)
ADU107484164
AIP107639257
AHF112741998
LANG109341393
FVE101302927
RCN112196835
PPER18792103
PMUM103341606
PAVI110764569
PDUL117636634
MDM103402584 103414220
PXB103931873 103943015
ZJU107429322
MNT21405717
CSV101218922
CMO103502875
BHJ120081638
MCHA111019644 111022332
CMAX111493063
CMOS111458811
CPEP111780472
RCU8258202
JCU105634069
HBR110663207
MESC110602183
POP7462233
PEU105122143
PALZ118030744
JRE108994097
QSU112025483 112031350
QLO115972416
TWL120007781
VVI100254163
VRI117924907
SLY101249915
SPEN107018501
SOT102599620
CANN107847498
NTA107795467 107814469
NSY104233686
NTO104094447
NAU109235191
INI109163311
ITR116015244
SIND105156242
OEU111378219 111403211
EGT105966065
SSPL121749572 121751336
HAN110920919
ECAD122596427
LSV111890392
CCAV112523544
DCR108206333
CSIN114261772 114273132
BVG104883814
SOE110785673
CQI110699920
NNU104609962
MING122076488
TSS122646055
PSOM113275529 113282083
NCOL116245035 116259651
OSA4333863 4339087
DOSAOs03t0708100-01(Os03g0708100) Os05t0473900-01(Os05g0473900)
OBR102710110
BDI100833021
ATS109780746
TDC119286920 119294788
TAES123087133 123090828 123095838
SBI8063400
ZMA100273407 103637754 103640918 103650819
SITA101769463 101770133
SVS117838816 117838817
PVIR120650038 120650040 120654008 120690913 120698518
PHAI112877271
PDA103721394
EGU105041302
MUS103986850
DCT110109674
PEQ110025823
AOF109850190
ATR18421937
SMOSELMODRAFT_102227 SELMODRAFT_141696 SELMODRAFT_416220 SELMODRAFT_440351
PPP112283401 112284342
CRECHLRE_16g673281v5
VCNVOLCADRAFT_81992
MNGMNEG_0138
CSLCOCSUDRAFT_28352 COCSUDRAFT_37381
CVRCHLNCDRAFT_140522
APROF751_0106
OLUOSTLU_35257
OTAOT_ostta07g03630
BPGBathy04g03930
MISMICPUN_86550 MICPUN_98894
MPPMICPUCDRAFT_57426 MICPUCDRAFT_5760
GSLGasu_32140
CCPCHC_T00003462001
PPAPAS_FragB_0025
DHADEHA2A02398g
PICPICST_43511
PGUPGUG_01587
SPAASPAPADRAFT_54079
LELLELG_04064
CALCAALFM_CR09190CA(CaO19.7316)
CTPCTRG_05907
COTCORT_0G01410
CDUCD36_34570
CTENCANTEDRAFT_115405
YLIYALI0A10010g
CLUCLUG_02206
CLUSA9F13_02g00979
CAURCJI97_004938
SLBAWJ20_4390
BNNFOA43_004763
BBRXBRETT_001638
OPAHPODL_02274
NCRNCU04228
NTENEUTE1DRAFT56595(NEUTE1DRAFT_56595)
SMPSMAC_04372
CTHRCTHT_0062300
MGRMGG_06880
PPEIPpBr36_07354
TMNUCRPA7_5184
FVRFVEG_16045
FOXFOXG_15789 FOXG_18742
NHENECHADRAFT_77029 NECHADRAFT_85877 NECHADRAFT_94695 NECHADRAFT_96363
MAWMAC_00527 MAC_01127
MAJMAA_07281
PLJVFPFJ_06225 VFPFJ_09407 VFPFJ_11236
VALVDBG_02781
CFJCFIO01_00732 CFIO01_01688 CFIO01_01963
CHIGCH63R_07972 CH63R_08833
ELAUCREL1_4246 UCREL1_4661
PFYPFICI_02180 PFICI_05392 PFICI_14010 PFICI_14715
MBEMBM_07890
PSCOLY89DRAFT_632472 LY89DRAFT_735074 LY89DRAFT_783003
GLZGLAREA_00540
ANIAN1262.2 AN4647.2
AFMAFUA_1G10170
NFINFIA_015480 NFIA_034200
AORAO090011000425 AO090038000416 AO090038000507
ANGANI_1_304074(An08g01970) ANI_1_634114(An13g01600)
AFVAFLA_008894 AFLA_008993
ALUCAKAW2_11689A AKAW2_20056S AKAW2_30790S
ACHEACHE_30863S ACHE_80137A
APUUAPUU_50473A APUU_51617S APUU_70935S
PCSPc16g04850 Pc22g16220
TMFPMAA_046770
TRGTRUGW13939_01351 TRUGW13939_09277 TRUGW13939_10076
CIMCIMG_05604
CPWCPC735_067270
PBLPAAG_03366
PBNPADG_12125(PADG_06459)
AJEHCAG_08861
BGHBDBG_05156
PNOSNOG_01644
PTEPTT_04385 PTT_18664
BZECOCCADRAFT_25846 COCCADRAFT_26771
BSCCOCSADRAFT_175888 COCSADRAFT_98957
BORCOCMIDRAFT_39162 COCMIDRAFT_95850
AALTCC77DRAFT_1017820 CC77DRAFT_1023029
ZTRMYCGRDRAFT_65666
PFJMYCFIDRAFT_46045
FFUCLAFUR5_07557 CLAFUR5_11875
BCOMBAUCODRAFT_290267 BAUCODRAFT_434805
NPAUCRNP2_183 UCRNP2_2578 UCRNP2_403 UCRNP2_727
CNGCNAG_04101
TASAA1Q1_01035 A1Q1_02921
HIRHETIRDRAFT_440598
CCICC1G_03299
WSEWALSEDRAFT_33062
WICJ056_000767
SREPTSG_04949
DDIDDB_G0278961
DPPDICPUDRAFT_74901 DICPUDRAFT_96115
DFADFA_07379 DFA_08694
ACANACA1_105970 ACA1_277850
PTMGSPATT00006130001 GSPATT00014604001 GSPATT00022358001
SMINv1.2.010013.t1(symbB.v1.2.010013.t1)
FCYFRACYDRAFT_160634
AAFAURANDRAFT_19085 AURANDRAFT_25217 AURANDRAFT_35045
PIFPITG_12813
PSOJPHYSODRAFT_561797
SPARSPRG_01670
GTTGUITHDRAFT_74806
NGRNAEGRDRAFT_59944
BRBEH207_01915
LGULG3211_0379
VNIVIBNI_A0779
SBKSHEWBE_4252
PATPatl_1683
AMCMADE_1020325
AMAAamad1_20160
AMADI636_19295
AMAII635_20150
AMBAMBAS45_04990
GAGGlaag_2649
GNIGNIT_3616
GPSC427_2654 C427_3964
PMESFX988_00949
CEBB0D95_04365
CEKD0B88_12815
CEGD0C16_04405 D0C16_11620
SDESde_3060
MARQMARGE09_P2530
ALGAQULUS_20020
ASIPAQUSIP_22490
LPNlpg2694(legD1)
LPHLPV_3040
LPOLPO_2975
LPULPE509_00331
LPMLP6_2726(legD1)
LPFlpl2621
LPPlpp2748
LPCLPC_0442
LPAlpa_03931
LPElp12_2687
LFALFA_0371
LHALHA_2568(Phyhd)
LJRNCTC11533_01617
LWASAMEA4504053_3193
LSSNCTC12082_01815
TMCLMI_2425(Phyhd)
WOCBA177_15485
GAIIMCC3135_08210(ectD_1)
TTCFOKN1_2351
HCHHCH_03217
HAHEENC22_16120
MMEMarme_0221
MPCMar181_3384
MPRIMP3633_3646
MARDIBG28_20120
MFOIJSY38_08400
RFOREIFOR_00118
LLPGH975_11510
SALNSALB1_1200
TSNW908_04680
THINCRN91_05775
IODEJO50_01645
IFLC1H71_01950
DEEHQN60_01370
CHIZHQ393_10585
CFONHZU75_04705
RSORSp0209
RSLRPSI07_mp0152
RSNRSPO_m00196
RSMCMR15_mp10177
RSEF504_3648
RSYRSUY_35430
RPIRpic_3916
RPFRpic12D_4030
RPJN234_21775
RMNTK49_19970
RINACS15_5635
RPUCDC45_18650
RSGJK151_04995
REHH16_B0166(h16_B0166)
CNCCNE_2c01510
CUHBJN34_20850
REUReut_B5568
RMERmet_3627
CTIRALTA_B0176
CBWRR42_s3209
CGDCR3_4468
CCUPBKK81_21015
CUPBKK80_20865
CUUBKK79_26080
CPAUEHF44_22485
COXE0W60_06870
BMABMA3264
BMVBMASAVP1_A2927
BMLBMA10229_A2162
BMNBMA10247_3421
BMALDM55_466
BMAEDM78_2737
BMAQDM76_447
BMAIDM57_1919
BMAFDM51_2859
BMAZBM44_3096
BMABBM45_367
BPSBPSL0213
BPMBURPS1710b_0397
BPLBURPS1106A_0213
BPDBURPS668_0201
BPRGBP346_A0115
BPSEBDL_1776
BPSMBBQ_3217
BPSUBBN_3339
BPSDBBX_166
BPZBP1026B_I3300
BPQBPC006_I0199
BPKBBK_1255
BPSHDR55_876
BPSABBU_1929
BPSOX996_497
BUTX994_2487
BTEBTH_I0176
BTQBTQ_201
BTJBTJ_2284
BTZBTL_199
BTDBTI_3544
BTVBTHA_256
BTHEBTN_1193
BTHMBTRA_400
BTHADR62_1368
BTHLBG87_363
BOKDM82_3400
BOCBG90_1418
BUUWS70_16570
BSAVWS86_18180
BVIBcep1808_3164
BVEAK36_837
BURBcep18194_A6429
BCNBcen_2465
BCHBcen2424_3079
BCMBcenmc03_3097
BCJBCAL0511
BCENDM39_3173
BCEWDM40_682
BCEOI35_3155
BAMBamb_3127
BACBamMC406_2990
BMJBMULJ_00156(phyH)
BMUBmul_3076
BMKDM80_1842
BMULNP80_3204
BCTGEM_0362
BCEDDM42_1931
BCEPAPZ15_03305
BDLAK34_30
BPYRABD05_05440
BCONNL30_28495
BUBBW23_1806 BW23_5476
BDFWI26_14910
BLATWK25_14950
BTEIWS51_25750
BSEMWJ12_15430
BPSLWS57_34195
BMECWJ16_15615
BSTGWT74_16225
BSTLBBJ41_13195
BANNJFN94_15730
BGLbglu_1g33660
BGUKS03_827
BUGBC1001_0095
BGFBC1003_0117
BGDbgla_1g37850
BGOBM43_1302
BYIBYI23_A027220
BUKMYA_2840
BUEBRPE67_ACDS27720
BULBW21_30
BUQAC233_00710
BGPBGL_1c35520
BPLAbpln_1g34490
BUDAQ610_17770
BUMAXG89_06245
BURKDM992_04440
BXEBxe_A4369
BXBDR64_2045
BPHBphy_0080
BGEBC1002_0070
BPXBUPH_04000
BPYBphyt_0353
BUZAYM40_00520
BFNOI25_1342
BCAIK788_0003461
PSPWBJG93_12190
PARABTO02_01390
PARBCJU94_04745 CJU94_24745
PHSC2L64_00385
PTERC2L65_00385
PGPCUJ91_00830
PCJCUJ87_00570
PTSCUJ90_00510
PCAFDSC91_005518
PMEGFNZ07_14080
PTROG5S35_00360
PGISI6I06_10915
PACPFAZ97_00385
PACSFAZ98_00340
PEWKZJ38_00535
PDIOPDMSB3_0151
BRHRBRH_00766
PPKU875_12475
PPNODA70_04875
PPNMLV28_01385
PRBX636_22220
PPULRO07_20330
PSPUNA29_16880
PAPISG18_19445
PVEUC34_11550
POXMB84_15945
PTXABW99_07770
PFGAB870_21925
PNRAT302_21785
PANDDRB87_10600
PFIBPI93_016120 PI93_021440
MCYSMCB1EB_2187
CABASBC2_00880
BUOBRPE64_ACDS28410
CARIFNU76_01975
VTRMYVALT_G_00230
VLAGKR41_00009(ectD)
BPEBP3605
BPCBPTD_3551
BPERBN118_0499
BPETB1917_3617
BPEUQ425_38430
BPARBN117_0435
BPABPP0438
BBHBN112_2973
BBRBB0440
BBMBN115_0427
BBXBBS798_0436
BPTBpet4505
BAVBAV0329
BHZACR54_00390
BTRMSAMEA390648701575(thpD_1)
BBROBAU06_11915
BFZBAU07_14795
BPDZBBN53_18975
BOHAKI39_11075
BGMCAL15_21750
AXYAXYL_05883
AXONH44784_027221
AXNAX27061_5583
AXXERS451415_05606
ADTAPT56_25745
AISBUW96_28585
ASWCVS48_09465
ACHRC2U31_01795
ACHBDVB37_25310
ADYHLG70_24210
PIGEGT29_03835
RHGEXZ61_16505
HYNF9K07_08280
HARHEAR3315
MMSmma_3549
JAGGJA_1036(PHYHD1)
JABVN23_09465
JAZYQ44_03660
JALBZG29_23875
JSVCNX70_24305
JASFJQ89_13540
JLVG3257_24570
HSEHsero_3965
HSZACP92_19795
HHTF506_01635
HRBHrubri_3911
HEEhmeg3_04070
HHFE2K99_20630
HFRG5S34_21520
CFUCFU_0471
CARELT85_0462
CPRACPter91_0551
MNRACZ75_24115
MASWAM586_23470
MASSCR152_13590
MASZC9I28_23825
MTIMDIR46_24060
MASYDPH57_25475
MALIEYF70_03490
MUMFCL38_15140
MFLAGO485_10595
MPLIE1742_10905
MANCIV454_02035
DUGHH213_05375
UPVEJN92_11615
UPIEJG51_014215
GLCJQN73_10245
UPLDSM104440_00186
ANTArnit_2688
ASUIASUIS_2277
AVPAVENP_2690
ADZADFLV_2625
ALKALEK_2989
ALPLPB137_12080
AHSAHALO_2307
AMYTAMYT_2364
AMARAMRN_2399
ACAAACAN_2400
AMOLAMOL_2378
APAIAPAC_2207
HBVABIV_0315
HEBRAEBR_2595
AANAAANAER_2555
PACOAACT_2608
ARCABLL_2506
NSANitsa_0663
SUNSUN_0232
SLHYH65_09870
SINUIMZ28_09630
MXAMXAN_3973
MSDMYSTI_03943
MYMA176_002933 A176_002951
MFBMFUL124B02_21440
CCXCOCOR_03955 COCOR_03959
MFULILAB_27970
MMASMYMAC_003884
SURSTAUR_1565 STAUR_4442
AGEAA314_04582 AA314_05809
AVMJQX13_20915 JQX13_43030
MBDMEBOL_007569
CFUSCYFUS_005421 CYFUS_008936
SCUSCE1572_33750
CCROCMC5_064810
PAUUE8A73_026020
SAMYDB32_001333
LLUAKJ09_03390
MRMA7982_07308 A7982_07418
RENEF513_02840
DEIC4375_13405
BRND1F64_03075
PSFPSE_1045
SIWGH266_16920
RUAD1823_06580
RUTFIU92_10680
RDERD1_0676 RD1_1757
RLIRLO149_c029630 RLO149_c038650
RPONG3256_01660
ROMEI983_05065
AHTANTHELSMS3_02345
OCDFHY55_05205
MARUFIU81_13455
MALUKU6B_17250
PALXGQA70_18270
PTPRCA23_c09800
SALOEF888_07710
PGVSL003B_3683
CACTHZ995_12065
HDHG5B40_08380
NOGGKE62_15095
SMAZLH19_20290
SPHQBWQ93_03375
SPAPH3Z74_08855
PALGHFP57_06685
SANDH3309_16070 H3309_16075
ERKCD351_08300
SHUMSTHU_43390
SVCSTVA_42120
AZMDM194_27660
AZZDEW08_29980
NCBC0V82_17015
SKTIGS68_11525
SMUCJL100_013250
SROEJL101_012615
HTQFRZ44_03520
DVNHQ394_14385
APBSAR116_0278 SAR116_1546
BMXBMS_1155
SBFJCM31447_01720
MEKUHUW50_07160 HUW50_23165 HUW50_23745
PJDPjdr2_0510 Pjdr2_1911 Pjdr2_2976 Pjdr2_5210
GYMGYMC10_2713 GYMC10_2738 GYMC10_3361
PMSKNP414_01728 KNP414_01778 KNP414_02396
PMQPM3016_2025 PM3016_2656
PMWB2K_10555 B2K_10760 B2K_13455
PBJVN24_19045
POWIJ21_29340 IJ21_30680 IJ21_38500 IJ21_44820 IJ21_45380
PSWUSY83_04060 SY83_07030 SY83_19975 SY83_21005 SY83_21030 SY83_22010
PIBBBD41_00725 BBD41_27265
PVOPVOR_16319
PLWD5F53_13475 D5F53_16095 D5F53_16180
PPSCEHS13_05125 EHS13_05855 EHS13_06370 EHS13_06625 EHS13_09575 EHS13_10435 EHS13_14545 EHS13_21085 EHS13_26990 EHS13_27845 EHS13_29605
PALBEJC50_00445 EJC50_08270 EJC50_09060 EJC50_09320 EJC50_09595 EJC50_12405 EJC50_13740 EJC50_23770 EJC50_24265 EJC50_24640 EJC50_27225 EJC50_28970
PCHIPC41400_06475 PC41400_06480 PC41400_06580
PBKBack11_04190 Back11_20610 Back11_33370 Back11_54590 Back11_61480
PRZGZH47_06330 GZH47_09410 GZH47_09625 GZH47_13820 GZH47_15480 GZH47_20260 GZH47_21305 GZH47_22370 GZH47_26040 GZH47_27055 GZH47_31200
PLYCGXP70_01565 GXP70_06785 GXP70_07000 GXP70_09925 GXP70_20600 GXP70_21210 GXP70_21600 GXP70_22570 GXP70_24080 GXP70_26375 GXP70_26430
PCELHUB94_12575
COHEAV92_03330 EAV92_03840 EAV92_10735
COHNKCTCHS21_09760
NOZDMB37_03595
NODFOH10_16520
NAHF5544_10560 F5544_12730
SCBSCAB_21421 SCAB_8921
SMALSMALA_8372
SSOII1A49_45600
SDVBN159_1064
SALSSLNWT_0971
SLDT261_3458
STRCAA958_31980
SCXAS200_01265 AS200_06335
SRWTUE45_04035(ptlH)
SGSAVL59_17470
STSIA4E84_37725
SCADDN051_06070
SLSSLINC_7713
SNWBBN63_01675
SPUNBFF78_03910 BFF78_11290
SGVB1H19_03015
SFKKY5_8084c
SGEDWG14_00950
SRJSRO_0724
SDXC4B68_03260
SQZFQU76_30320
SCYAEJ357_03275
SKACP970_39720 CP970_43420
SHAWCEB94_37855
SFYGFH48_05290
SAQUEJC51_00445 EJC51_41420 EJC51_47100
SGFHEP81_00706
SPHVF9278_43280
SPACB1H29_00685 B1H29_36375
SCHACP983_03095
SCOECP976_39105
STUIGCM10017668_04560
SCHFIPT68_33105
SFEUIM697_20565
SROIIAG44_36815
SMAOCAG99_24045
SLFJEQ17_42650
BCVBcav_0067 Bcav_2128
BFABfae_28650 Bfae_29130
BRXBH708_11055 BH708_11510
BGGCFK41_01795 CFK41_02070
BSAUDWV08_12220
BRRC1N80_04370
LMOIVV02_25835
MPHMLP_16240
MIKFOE78_00575 FOE78_08940 FOE78_11905 FOE78_17155 FOE78_21020
MICGGJV80_01725 GJV80_02290 GJV80_08340 GJV80_19260
KFLKfla_2368 Kfla_5005 Kfla_5893
KQIF1D05_07350 F1D05_14035 F1D05_31800
NOABKM31_03910 BKM31_25625
NOWGBF35_34315
NGNLCN96_38150
FREFranean1_6323
FRIFraEuI1c_3443
FALFRAAL2554
AABA4R43_02015
PDXPsed_1312
KPHYAOZ06_22560
ACTIUA75_16685
MCRAID554_09985
PLABC6361_23965
PLATC6W10_35820
ATLAthai_10850
SNASnas_3392 Snas_5543
RUBGBA63_13195 GBA63_13235
AYMYM304_11130
ATQGH723_13585
AQZKSP35_10880
IAMHC251_14800
AMRAM1_0372
KOVK9N68_28050
PSEUPse7367_1629
PSERABRG53_2048
THEUHPC62_13360
MICMic7113_3608
AFLOHEQ12_13280
KBSEPA93_13550
TTRTter_1946
DEZDKM44_00895
CCZCCALI_01094 CCALI_01282 CCALI_01760 CCALI_01825 CCALI_02204 CCALI_02303 CCALI_02835
FGIOP10G_0526 OP10G_0989 OP10G_1123 OP10G_3472
NPYNPRO_22300
PNLPNK_1871
OLEK0B96_07085 K0B96_12960
LCREPla8534_34060(ptlH_2)
AAGGETAA8_14190
AMUCPan181_31000(ptlH)
PNDPla175_38870 Pla175_38880
PLMPlim_1638
PEHSpb1_24900(ptlH)
PBSPlabr_2051
PLSVT03_10780 VT03_23410(ptlH_2)
FMRFuma_02735 Fuma_05232(ptlH_2) Fuma_06198(ptlH_3)
GMRGmarT_08890(ptlH_2)
GIMF1728_09860 F1728_13305
GPNPan110_09590
MRIMal4_23720
SDYNMal52_54880 Mal52_61010(ptlH_3)
PLONPla110_33350 Pla110_40360
PHMPSMK_06950 PSMK_07800 PSMK_08800 PSMK_08900
CHITFW415_13135
CFILMYF79_21605
NSONIASO_15075
FLASY85_14135
FGGFSB75_00085
AGIFSB73_20315 FSB73_21145
PSEGD3H65_09780
PHEPhep_1576 Phep_3118
PGSCPT03_04890
SHTKO02_06690
SPHEGFH32_14750
MGKFSB76_10285
MRUBDEO27_002365
MMABHQ865_23575
MGIKGO620_002255
CAMUCA2015_0106
SLISlin_4809
SMONAWR27_23320
SPIRCWM47_26950
SPIKEXU85_31110
DFEDfer_1903 Dfer_2103 Dfer_2295
RUNDR864_16510
RUPDTQ70_20640
FAEFAES_0746 FAES_2385
HMTMTP16_02840
FGLEM308_17760
FSDLXD69_15570
FBCFB2170_03640
AALGAREALGSMS7_01695
EMARD1013_00920
FBEFF125_04150
HALJG9465_16230
NMONmlp_3445
HMUHmuk_0567
HALZE5139_05985
HALLLC1Hm_3101(phyH)
HAZPGBQ70_05980
HAEhalTADL_1133
 » show all
Reference
1  [PMID:9565335]
  Authors
Jansen GA, Mihalik SJ, Watkins PA, Jakobs C, Moser HW, Wanders RJ.
  Title
Characterization of phytanoyl-Coenzyme A hydroxylase in human liver and activity measurements in patients with peroxisomal disorders.
  Journal
Clin Chim Acta 271:203-11 (1998)
DOI:10.1016/S0009-8981(97)00259-3
Reference
2  [PMID:8954107]
  Authors
Jansen GA, Mihalik SJ, Watkins PA, Moser HW, Jakobs C, Denis S, Wanders RJ.
  Title
Phytanoyl-CoA hydroxylase is present in human liver, located in peroxisomes, and deficient in Zellweger syndrome: direct, unequivocal evidence for the new, revised pathway of phytanic acid alpha-oxidation in humans.
  Journal
Biochem Biophys Res Commun 229:205-10 (1996)
DOI:10.1006/bbrc.1996.1781
Reference
3  [PMID:9326940]
  Authors
Jansen GA, Ofman R, Ferdinandusse S, Ijlst L, Muijsers AO, Skjeldal OH, Stokke O, Jakobs C, Besley GT, Wraith JE, Wanders RJ.
  Title
Refsum disease is caused by mutations in the phytanoyl-CoA hydroxylase gene.
  Journal
Nat Genet 17:190-3 (1997)
DOI:10.1038/ng1097-190
  Sequence
[rno:114209]
Reference
4  [PMID:7556205]
  Authors
Mihalik SJ, Rainville AM, Watkins PA.
  Title
Phytanic acid alpha-oxidation in rat liver peroxisomes. Production of alpha-hydroxyphytanoyl-CoA and formate is enhanced by dioxygenase cofactors.
  Journal
Eur J Biochem 232:545-51 (1995)
DOI:10.1111/j.1432-1033.1995.545zz.x
Reference
5  [PMID:9326939]
  Authors
Mihalik SJ, Morrell JC, Kim D, Sacksteder KA, Watkins PA, Gould SJ.
  Title
Identification of PAHX, a Refsum disease gene.
  Journal
Nat Genet 17:185-9 (1997)
DOI:10.1038/ng1097-185
  Sequence
[hsa:5264] [mmu:16922]
Other DBs
ExplorEnz - The Enzyme Database: 1.14.11.18
IUBMB Enzyme Nomenclature: 1.14.11.18
ExPASy - ENZYME nomenclature database: 1.14.11.18
BRENDA, the Enzyme Database: 1.14.11.18
CAS: 185402-46-4
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