ORTHOLOGY: K00597
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Entry
K00597 KO
Symbol
MTRR
Name
methionine synthase reductase [EC:
1.16.1.8
]
Pathway
map04980
Cobalamin transport and metabolism
Disease
H00183
Homocystinuria
H00262
Neural tube defects, folate-sensitive
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09150 Organismal Systems
09154 Digestive system
04980 Cobalamin transport and metabolism
K00597 MTRR; methionine synthase reductase
Enzymes [BR:
ko01000
]
1. Oxidoreductases
1.16 Oxidizing metal ions
1.16.1 With NAD+ or NADP+ as acceptor
1.16.1.8 [methionine synthase] reductase
K00597 MTRR; methionine synthase reductase
BRITE hierarchy
Other DBs
GO:
0030586
Genes
HSA:
4552
(MTRR)
PTR:
461717
(MTRR)
PPS:
100990677
(MTRR)
GGO:
101138335
(MTRR)
PON:
100174319
(MTRR)
PPYG:
129036480
(MTRR)
NLE:
100605425
(MTRR)
HMH:
116457012
(MTRR)
SSYN:
129464956
(MTRR)
MCC:
100430789
(MTRR)
MCF:
101925754
(MTRR)
MTHB:
126956057
MNI:
105489477
(MTRR)
CSAB:
103214983
(MTRR)
CATY:
105585969
(MTRR)
PANU:
101008135
(MTRR)
TGE:
112626561
(MTRR)
MLEU:
105535659
(MTRR)
RRO:
104674086
(MTRR)
RBB:
108536959
(MTRR)
TFN:
117064737
(MTRR)
PTEH:
111546734
(MTRR)
CANG:
105510966
(MTRR)
CJC:
100389974
(MTRR)
SBQ:
101042701
(MTRR)
CIMI:
108281389
(MTRR)
ANAN:
105732982
(MTRR)
CSYR:
103274646
(MTRR)
MMUR:
105885839
(MTRR)
LCAT:
123648029
(MTRR)
PCOQ:
105813261
105821319
(MTRR)
OGA:
100940712
(MTRR)
MMU:
210009
(Mtrr)
MCAL:
110307972
(Mtrr)
MPAH:
110329102
(Mtrr)
RNO:
290947
(Mtrr)
MCOC:
116083549
(Mtrr)
ANU:
117724003
(Mtrr)
MUN:
110550967
(Mtrr)
CGE:
100773236
(Mtrr)
MAUA:
101837109
(Mtrr)
PROB:
127220709
(Mtrr)
PLEU:
114696124
(Mtrr)
MORG:
121433733
(Mtrr)
MFOT:
126503181
AAMP:
119809960
(Mtrr)
NGI:
103735353
(Mtrr)
HGL:
101720530
(Mtrr)
CPOC:
100732821
(Mtrr)
CCAN:
109688199
(Mtrr)
DORD:
105983780
(Mtrr)
DSP:
122120995
(Mtrr)
PLOP:
125367698
(Mtrr)
NCAR:
124986755
MMMA:
107146369
(Mtrr)
OCU:
100350605
TUP:
102491380
(MTRR)
GVR:
103597915
(MTRR)
CFA:
478623
(MTRR)
CLUD:
112662624
(MTRR)
VVP:
112934268
(MTRR)
VLG:
121477419
(MTRR)
NPO:
129498612
(MTRR)
AML:
100484655
(MTRR)
UMR:
103662251
(MTRR)
UAH:
113260809
(MTRR)
UAR:
123791267
(MTRR)
ELK:
111153446
LLV:
125099992
MPUF:
101674005
(MTRR)
MNP:
132028202
(MTRR)
MLK:
131831572
(MTRR)
NVS:
122896012
(MTRR)
ORO:
101366274
(MTRR)
EJU:
114223671
(MTRR)
ZCA:
113929503
(MTRR)
MLX:
118006296
(MTRR)
NSU:
110591583
(MTRR)
LWW:
102749796
FCA:
101098359
(MTRR)
PYU:
121042463
(MTRR)
PCOO:
112861128
(MTRR)
PBG:
122495505
(MTRR)
PVIV:
125167884
(MTRR)
LRUF:
124522602
PTG:
102949230
(MTRR)
PPAD:
109267828
(MTRR)
PUC:
125934724
AJU:
106971266
HHV:
120225094
(MTRR)
BTA:
507991
(MTRR)
BOM:
102272980
(MTRR)
BIU:
109574962
(MTRR)
BBUB:
102411193
(MTRR)
BBIS:
105001005
(MTRR)
CHX:
102171193
(MTRR)
OAS:
101123409
(MTRR)
BTAX:
128066100
(MTRR)
ODA:
120879371
(MTRR)
CCAD:
122454368
(MTRR)
MBEZ:
129553374
(MTRR)
SSC:
100516580
(MTRR)
CFR:
102511463
(MTRR)
CBAI:
105081237
(MTRR)
CDK:
105094043
(MTRR)
VPC:
102539936
(MTRR)
BACU:
103019188
(MTRR)
BMUS:
118892397
(MTRR)
LVE:
103085843
(MTRR)
OOR:
101285453
(MTRR)
DLE:
111178558
(MTRR)
PCAD:
102990472
(MTRR)
PSIU:
116751336
(MTRR)
NASI:
112404523
(MTRR)
ECB:
100071310
(MTRR)
EPZ:
103540506
(MTRR)
EAI:
106823000
(MTRR)
MYB:
102241177
(MTRR)
MYD:
102763596
(MTRR)
MMYO:
118656738
(MTRR)
MLF:
102430988
(MTRR)
MDT:
132233657
(MTRR)
PKL:
118703331
(MTRR)
EFUS:
103305100
(MTRR)
MNA:
107540559
(MTRR)
DRO:
112321035
(MTRR)
SHON:
118998677
(MTRR)
AJM:
119049315
(MTRR)
PDIC:
114498869
(MTRR)
PHAS:
123824930
(MTRR)
MMF:
118642804
(MTRR)
PPAM:
129074540
(MTRR)
RFQ:
117024848
(MTRR)
PALE:
102892778
(MTRR)
PGIG:
120586285
(MTRR)
PVP:
105299590
(MTRR)
RAY:
107502702
(MTRR)
MJV:
108384628
(MTRR)
TOD:
119260625
(MTRR)
SARA:
101558683
(MTRR)
SETR:
126000778
(MTRR)
LAV:
100654114
(MTRR)
TMU:
101359820
ETF:
101644091
(MTRR)
DNM:
101425735
(MTRR)
101428450
101442305
MDO:
100013254
(MTRR)
GAS:
123231587
(MTRR)
SHR:
100923220
(MTRR)
AFZ:
127543618
PCW:
110220385
(MTRR)
TVP:
118850609
(MTRR)
OAA:
100089744
(MTRR)
GGA:
428502
(MTRR)
PCOC:
116226344
(MTRR)
MGP:
100540427
(MTRR)
CJO:
107309523
(MTRR)
TPAI:
128091008
(MTRR)
LMUT:
125691018
(MTRR)
NMEL:
110393327
(MTRR)
APLA:
101802959
(MTRR)
ACYG:
106036580
(MTRR)
CATA:
118250991
(MTRR)
TGU:
100228556
(MTRR)
LSR:
110479512
(MTRR)
SCAN:
103822476
(MTRR)
PMOA:
120504886
(MTRR)
OTC:
121339731
(MTRR)
PRUF:
121358093
(MTRR)
GFR:
102038689
(MTRR)
FAB:
101807366
(MTRR)
OMA:
130249406
(MTRR)
PHI:
102113343
(MTRR)
PMAJ:
107200311
(MTRR)
CCAE:
111925671
(MTRR)
CCW:
104685872
(MTRR)
CBRC:
103618767
(MTRR)
ETL:
114055131
(MTRR)
ZAB:
102073177
(MTRR)
ZLE:
135444211
(MTRR)
ACHL:
103811102
(MTRR)
SVG:
106850753
(MTRR)
MMEA:
130576261
(MTRR)
HRT:
120749197
(MTRR)
SATI:
136365912
(MTRR)
FPG:
101910301
(MTRR)
FCH:
102047448
(MTRR)
CCRI:
104158620
(MTRR)
NNT:
104399477
(MTRR)
SHAB:
115608717
(MTRR)
ACUN:
113476799
(MTRR)
TALA:
104361405
(MTRR)
ACHC:
115352899
(MTRR)
HALD:
104325095
(MTRR)
HLE:
104834255
(MTRR)
AGEN:
126048602
GCL:
127013551
CSTI:
104549738
(MTRR)
LDI:
104347081
(MTRR)
MNB:
103769290
(MTRR)
DPUB:
104299268
(MTRR)
AVIT:
104267393
(MTRR)
BRHI:
104499171
(MTRR)
EGZ:
104126205
(MTRR)
NNI:
104018869
(MTRR)
PCRI:
104028347
(MTRR)
PCAO:
104040068
104044877
PADL:
103915149
(MTRR)
AFOR:
103898434
(MTRR)
FGA:
104074282
(MTRR)
GSTE:
104255238
(MTRR)
CLV:
102096989
(MTRR)
MUI:
104539545
(MTRR)
PGUU:
104463218
(MTRR)
PLET:
104613825
(MTRR)
EHS:
104502728
(MTRR)
CMAC:
104485556
CUCA:
104067541
(MTRR)
TEO:
104372610
(MTRR)
BREG:
104641988
(MTRR)
OHA:
104333156
(MTRR)
ACAR:
104527875
(MTRR)
CPEA:
104398259
(MTRR)
CVF:
104285329
(MTRR)
RTD:
128906288
(MTRR)
AAM:
106492684
(MTRR)
AROW:
112974047
(MTRR)
NPD:
112955282
(MTRR)
TGT:
104570113
(MTRR)
DNE:
112982725
(MTRR)
SCAM:
104137821
(MTRR)
ASN:
102383326
(MTRR)
AMJ:
102561574
(MTRR)
CPOO:
109314303
(MTRR)
GGN:
109300378
(MTRR)
PSS:
102457990
(MTRR)
CMY:
102929534
(MTRR)
CCAY:
125631994
(MTRR)
CPIC:
101951331
(MTRR)
TST:
117872759
(MTRR)
CABI:
116828362
(MTRR)
MRV:
120397426
(MTRR)
ACS:
100563923
(mtrr)
ASAO:
132774203
(MTRR)
PVT:
110089599
(MTRR)
SUND:
121929530
(MTRR)
PBI:
103055371
(MTRR)
PMUR:
107297701
(MTRR)
CTIG:
120301703
(MTRR)
PGUT:
117662381
(MTRR)
APRI:
131195506
(MTRR)
PTEX:
113436534
(MTRR)
NSS:
113415192
(MTRR)
VKO:
123029692
(MTRR)
PMUA:
114601218
(MTRR)
PRAF:
128418088
(MTRR)
ZVI:
118077646
(MTRR)
HCG:
128322474
(MTRR)
GJA:
107108830
(MTRR)
STOW:
125443447
(MTRR)
EMC:
129333378
(MTRR)
XLA:
108719055
(mtrr.L)
XTR:
733716
(mtrr)
NPR:
108802102
(MTRR)
RTEM:
120941649
(MTRR)
BBUF:
121001007
(MTRR)
BGAR:
122937714
(MTRR)
MUO:
115471629
(MTRR)
GSH:
117353594
(MTRR)
DRE:
560667
(mtrr)
SRX:
107727200
107741721
SANH:
107686717
(mtrr)
107695375
SGH:
107549192
107595114
(mtrr)
CCAR:
109049376
109070639
CAUA:
113042285
(mtrr)
113066006
CGIB:
127946451
128013383
PTET:
122330005
(mtrr)
LROH:
127156073
(mtrr)
OMC:
131532970
(mtrr)
PPRM:
120475933
(mtrr)
RKG:
130087657
(mtrr)
MAMB:
125258479
(mtrr)
CIDE:
127506272
CERY:
137014360
(mtrr)
MASI:
127432104
TROS:
130547352
(mtrr)
TDW:
130413571
(mtrr)
MANU:
129426642
(mtrr)
IPU:
108256395
IFU:
128600017
(mtrr)
PHYP:
113541137
(mtrr)
SMEO:
124375585
(mtrr)
TFD:
113660435
(mtrr)
TVC:
132840456
(mtrr)
TRN:
134301080
(mtrr)
AMEX:
103046907
(mtrr)
CMAO:
118798578
(mtrr)
EEE:
113588751
(mtrr)
CHAR:
105890298
TRU:
101070210
(mtrr)
TFS:
130513394
(mtrr)
TNG:
GSTEN00015528G001
LCO:
104921714
(mtrr)
NCC:
104954888
(mtrr)
TBEN:
117484139
(mtrr)
CGOB:
115025297
(mtrr)
PGEO:
117465808
(mtrr)
EMAC:
134883718
(mtrr)
ELY:
117264346
(mtrr)
EFO:
125881776
(mtrr)
PLEP:
121960422
(mtrr)
SLUC:
116037854
(mtrr)
ECRA:
117937681
(mtrr)
ESP:
116672097
(mtrr)
PFLV:
114549124
(mtrr)
GAT:
120811570
(mtrr)
PPUG:
119198462
(mtrr)
AFB:
129110569
(mtrr)
CLUM:
117749553
(mtrr)
PSWI:
130205937
(mtrr)
MSAM:
119908963
(mtrr)
119916723
SCHU:
122866850
(mtrr)
CUD:
121527283
(mtrr)
ALAT:
119008643
(mtrr)
ASTR:
137614198
(mtrr)
MZE:
101481719
(mtrr)
ONL:
100709326
(mtrr)
OAU:
116328322
(mtrr)
OLA:
101167253
(mtrr)
OML:
112151255
(mtrr)
CSAI:
133423279
(mtrr)
XMA:
102232227
(mtrr)
XCO:
114136999
(mtrr)
XHE:
116711923
(mtrr)
PRET:
103482452
(mtrr)
PFOR:
103135214
(mtrr)
PLAI:
106945836
(mtrr)
PMEI:
106915713
(mtrr)
GAF:
122823890
(mtrr)
PPRL:
129364709
(mtrr)
CVG:
107096083
(mtrr)
CTUL:
119786007
(mtrr)
GMU:
124857865
(mtrr)
NFU:
107382941
(mtrr)
KMR:
108243160
(mtrr)
ALIM:
106513500
(mtrr)
NWH:
119426553
(mtrr)
AOCE:
111581030
(mtrr)
MCEP:
124995404
(mtrR)
CSEM:
103377015
(mtrr)
POV:
109629723
(mtrr)
SSEN:
122768035
(mtrr)
HHIP:
117753534
(mtrr)
HSP:
118098418
(mtrr)
PPLT:
128426083
(mtrr)
SMAU:
118291125
(mtrr)
LCF:
108902055
SDU:
111237220
(mtrr)
SLAL:
111662991
(mtrr)
XGL:
120789616
(mtrr)
HCQ:
109511817
(mtrr)
SSCV:
125985662
(mtrr)
SBIA:
133492524
(mtrr)
PEE:
133396651
(mtrr)
PTAO:
133470071
(mtrr)
BPEC:
110160921
(mtrr)
MALB:
109965535
(mtrr)
BSPL:
114853480
(mtrr)
SJO:
128382742
(mtrr)
SASA:
106578438
106590608
STRU:
115152674
115195377
OTW:
112227637
112234917
OMY:
110489568
110535451
(mtrr)
OGO:
123991222
(mtrr)
124039468
ONE:
115105024
115119947
OKI:
109899196
109909942
OKE:
118361646
118381360
SALP:
111972954
112069456
SNH:
120028000
120050923
CCLU:
121549907
121569343
(mtrr)
ELS:
105019455
(mtrr)
SFM:
108935528
(mtrr)
PKI:
111849508
(mtrr)
AANG:
118226350
(mtrr)
LOC:
102683394
(mtrr)
PSPA:
121312733
121314194
ARUT:
117400543
117435804
117972350
PSEX:
120530158
(mtrr)
LCM:
102351804
(MTRR)
CMK:
103186339
(mtrr)
RTP:
109935699
(mtrr)
CPLA:
122549854
(mtrr)
HOC:
132816054
(mtrr)
LERI:
129713735
(mtrr)
PMRN:
116940837
(MTRR)
LRJ:
133344596
(MTRR)
BFO:
118403551
BBEL:
109475814
CIN:
100182690
SCLV:
120333702
SPU:
581957
LPIC:
129257126
APLC:
110975926
ARUN:
117288471
AJC:
117100775
SKO:
100371498
DME:
Dmel_CG14882
(CG14882)
DER:
6553357
DSE:
6616881
DSI:
Dsimw501_GD19100
(Dsim_GD19100)
DYA:
Dyak_GE24396
DSR:
110177283
DPO:
4802548
DPE:
6592026
DMN:
108155099
DWI:
6651662
DGR:
6563834
DMO:
Dmoj_GI22554
DAZ:
108608773
DNV:
108653072
DHE:
111604956
CCAT:
101460713
BOD:
106621643
BDR:
105227060
RZE:
108359714
AOQ:
129235633
TDA:
119681733
MDE:
101896273
SCAC:
106081791
LCQ:
111676765
LSQ:
119605785
GFS:
119639594
ECOE:
129938463
CLON:
129612987
AGA:
1281330
5667537
ACOZ:
120947327
120950664
AARA:
120894669
120906299
AMER:
121589425
121603667
ASTE:
118507709
118507710
AFUN:
125765621
125766171
AMOU:
128297364
128299583
AALI:
118468823
118468824
AAG:
110678628
110678731
5578477
5578478
AALB:
109401790
109406154
109406159
ASUA:
134226328
134226501
CQU:
CpipJ_CPIJ006043
CpipJ_CPIJ006044
CPII:
120414000
120414020
CNS:
116339537
BCOO:
119077885
TCA:
655238
DPA:
109546268
SOY:
115888852
AGRG:
126733869
ATD:
109594433
CSET:
123319121
AGB:
108911566
NVL:
108558885
APLN:
108736342
PPYR:
116166330
116166874
OTU:
111428153
BMOR:
101743356
BMAN:
114248178
MSEX:
115441099
DPL:
KGM_203279
BANY:
112058113
MJU:
123870173
NIQ:
126772355
VCD:
124543954
MCIX:
123658646
PMAC:
106717667
PPOT:
106105687
PXU:
106121932
ZCE:
119833735
CCRC:
123696597
LSIN:
126974450
AAGE:
121733516
HAW:
110376093
HZE:
124633976
TNL:
113505823
SLIU:
111357378
OFU:
114362733
ATRA:
106137350
GMW:
113509748
PXY:
105386469
PGW:
126371270
LGLY:
125229619
CCRN:
123297254
CLEC:
106670593
HHAL:
106681556
PHU:
Phum_PHUM317650
TPAL:
117647078
ZNE:
110830537
CSEC:
111869859
IEL:
124166861
FCD:
110845930
DPX:
DAPPUDRAFT_308706
DMK:
116922820
DPZ:
124341060
PVM:
113810127
PJA:
122265754
PCHN:
125040353
PMOO:
119575084
HAME:
121863726
PCLA:
123755462
CQD:
128691779
PTRU:
123511512
ESN:
127008217
MNZ:
135213547
MRJ:
136825422
HAZT:
108673187
EAF:
111698950
LSM:
121126949
DSV:
119446402
RSAN:
119389554
VDE:
111252907
VJA:
111273928
TUT:
107363566
DPTE:
113789801
DFR:
124499097
CSCU:
111614502
CVS:
136975553
PTEP:
107450790
ABRU:
129969209
UDV:
129234243
SDM:
118194194
LPOL:
106474232
CEL:
CELE_C01G6.6
(mtrr-1)
CBR:
CBG_00882
(Cbr-mtrr-1)
CRQ:
GCK72_004711
BMY:
BM_BM1887
(Bma-mtrr-1)
LOA:
LOAG_00690
TSP:
Tsp_01287
HRO:
HELRODRAFT_192212
LGI:
LOTGIDRAFT_225295
PVUL:
126821848
PCAN:
112556068
BGT:
106065660
GAE:
121385605
HRF:
124113360
HRJ:
124281376
HASI:
137298889
CRG:
105333103
CANU:
128178419
CVN:
111130109
OED:
125651723
MYI:
110450395
PMAX:
117318294
MMER:
123561042
RPHI:
132746759
DPOL:
127831755
127831822
MAEA:
128236250
OBI:
106882104
OSN:
115221088
LJP:
135464449
LAK:
106162590
106162591
SMM:
Smp_034220
SHX:
MS3_00006893
OVI:
T265_02681
EGL:
EGR_00462
LLON:
135497568
NVE:
5511985
EPA:
110247156
ATEN:
116300168
ADF:
107342874
AMIL:
114954870
PDAM:
113682435
SPIS:
111320968
DGT:
114526309
XEN:
124445181
HMG:
100207049
HSY:
130622767
RES:
135682074
TAD:
TRIADDRAFT_21300
AQU:
100635303
GSL:
Gasu_27190
CCP:
CHC_T00009055001
ECU:
ECU09_1710
EIN:
Eint_091730
EHE:
EHEL_091730
ERO:
EROM_091710
NCE:
NCER_101456
RIE:
OCT59_001954
MBR:
MONBRDRAFT_34058
SRE:
PTSG_06101
DDI:
DDB_G0267824
DDB_G0286763
DPP:
DICPUDRAFT_16710
DICPUDRAFT_43883
DFA:
DFA_03150
DFA_03353
ACAN:
ACA1_167060
PIF:
PITG_06954
PITG_20722
PSOJ:
PHYSODRAFT_359519
SPAR:
SPRG_03729
GTT:
GUITHDRAFT_108699
NGR:
NAEGRDRAFT_59563
(FM177)
» show all
Taxonomy
UniProt
Reference
PMID:
9501215
Authors
Leclerc D, Wilson A, Dumas R, Gafuik C, Song D, Watkins D, Heng HH, Rommens JM, Scherer SW, Rosenblatt DS, Gravel RA
Title
Cloning and mapping of a cDNA for methionine synthase reductase, a flavoprotein defective in patients with homocystinuria.
Journal
Proc Natl Acad Sci U S A 95:3059-64 (1998)
DOI:
10.1073/pnas.95.6.3059
Sequence
[hsa:
4552
]
LinkDB
All DBs
DBGET
integrated database retrieval system