| Entry |
|
| Symbol |
ECHS1
|
| Name |
|
| Pathway |
| map00280 | Valine, leucine and isoleucine degradation |
| map01110 | Biosynthesis of secondary metabolites |
| map01120 | Microbial metabolism in diverse environments |
|
| Module |
| M00013 | Malonate semialdehyde pathway, propanoyl-CoA => acetyl-CoA |
| M00032 | Lysine degradation, lysine => saccharopine => acetoacetyl-CoA |
| M00085 | Fatty acid elongation in mitochondria |
|
| Reaction |
| R02685 | (3S)-3-hydroxyacyl-CoA hydro-lyase |
| R03026 | (S)-3-hydroxybutanoyl-CoA hydro-lyase |
| R03045 | 3-hydroxypropionyl-CoA hydro-lyase |
| R04137 | 3-hydroxyisovaleryl-CoA hydro-lyase |
| R04170 | (S)-3-hydroxydodecanoyl-CoA hydro-lyase |
| R04204 | (2S,3S)-3-hydroxy-2-methylbutanoyl-CoA hydro-liase |
| R04224 | (S)-3-hydroxyisobutyryl-CoA hydro-lyase |
| R04738 | (S)-3-hydroxyhexadecanoyl-CoA hydro-lyase |
| R04740 | (S)-3-hydroxytetradecanoyl-CoA hydro-lyase |
| R04744 | (S)-hydroxydecanoyl-CoA hydro-lyase |
| R04746 | (S)-hydroxyoctanoyl-CoA hydro-lyase |
| R04749 | (S)-hydroxyhexanoyl-CoA hydro-lyase |
| R06942 | (3S)-3-hydroxyacyl-CoA hydro-lyase |
|
| Disease |
| H00525 | Disorders of mitochondrial fatty-acid oxidation |
|
| Brite |
KEGG Orthology (KO) [BR:ko00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
K07511 ECHS1; enoyl-CoA hydratase
00650 Butanoate metabolism
K07511 ECHS1; enoyl-CoA hydratase
09103 Lipid metabolism
00062 Fatty acid elongation
K07511 ECHS1; enoyl-CoA hydratase
00071 Fatty acid degradation
K07511 ECHS1; enoyl-CoA hydratase
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
K07511 ECHS1; enoyl-CoA hydratase
00310 Lysine degradation
K07511 ECHS1; enoyl-CoA hydratase
00380 Tryptophan metabolism
K07511 ECHS1; enoyl-CoA hydratase
09106 Metabolism of other amino acids
00410 beta-Alanine metabolism
K07511 ECHS1; enoyl-CoA hydratase
09111 Xenobiotics biodegradation and metabolism
00627 Aminobenzoate degradation
K07511 ECHS1; enoyl-CoA hydratase
00930 Caprolactam degradation
K07511 ECHS1; enoyl-CoA hydratase
Enzymes [BR:ko01000]
4. Lyases
4.2 Carbon-oxygen lyases
4.2.1 Hydro-lyases
4.2.1.17 enoyl-CoA hydratase
K07511 ECHS1; enoyl-CoA hydratase
|
| Other DBs |
|
| Genes |
» show all
|
| Reference |
|
| Authors |
Janssen U, Davis EM, Le Beau MM, Stoffel W |
| Title |
Human mitochondrial enoyl-CoA hydratase gene (ECHS1): structural organization and assignment to chromosome 10q26.2-q26.3. |
| Journal |
|
| Sequence |
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| LinkDB |
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