KEGG ORTHOLOGY: K08900

ORTHOLOGY: K08900

Entry

K08900                      KO

Symbol

BCS1

Name

mitochondrial chaperone BCS1

Disease

H00820

Bjornstad syndrome

H01354

Leigh syndrome

H02007

GRACILE syndrome

H02086

Mitochondrial complex III deficiency

Brite

KEGG Orthology (KO) [BR:ko00001]
09180 Brite Hierarchies
  09182 Protein families: genetic information processing
   03029 Mitochondrial biogenesis
    K08900  BCS1; mitochondrial chaperone BCS1
Mitochondrial biogenesis [BR:ko03029]
Mitochondrial quality control factors
  Mitochondrial respiratory chain complex assembly factors
   Complex-III assembly factors
    K08900  BCS1; mitochondrial chaperone BCS1

Genes

HSA:	617(BCS1L)

PTR:	459946(BCS1L)

PPS:

GGO:

PON:

NLE:

HMH:

MCC:	699690(BCS1L)

MCF:

102123539

MTHB:

126933002

MNI:

105481221

CSAB:

103217874(BCS1L)

CATY:

PANU:

TGE:

MLEU:

RRO:

RBB:

TFN:

PTEH:

CANG:

CJC:

SBQ:

CIMI:

CSYR:

MMUR:

LCAT:

PCOQ:

OGA:

MMU:	66821(Bcs1l)

MCAL:

110304618

MPAH:

110321210

RNO:	301514(Bcs1l)

MCOC:

ANU:

MUN:

CGE:

MAUA:

PROB:

PLEU:

MORG:

MFOT:

AAMP:

NGI:

HGL:

CPOC:

CCAN:

DORD:

DSP:

PLOP:

NCAR:

MMMA:

OCU:

OPI:

TUP:

GVR:

CFA:	478911(BCS1L)

CLUD:

VVP:

VLG:

NPO:

AML:

UMR:

UAH:

UAR:

ELK:

LLV:

MPUF:

MNP:

MLK:

NVS:

ORO:

EJU:

ZCA:

MLX:

NSU:

LWW:

FCA:	101090709(BCS1L)

PYU:

PCOO:

PBG:

PVIV:

LRUF:

PTG:

PPAD:

PUC:

AJU:

HHV:

BTA:	539713(BCS1L)

BOM:

BIU:

BBUB:

BBIS:

CHX:

OAS:

BTAX:

ODA:

CCAD:

MBEZ:

SSC:	100626589(BCS1L)

CFR:

CBAI:

CDK:

VPC:

BACU:

BMUS:

LVE:	103072648 103081436

OOR:

DLE:

PCAD:

PSIU:

NASI:

ECB:	100055811(BCS1L)

EPZ:

EAI:

MYB:

MYD:

MMYO:

MLF:

PKL:

EFUS:

MNA:

DRO:

SHON:

AJM:

PDIC:

PHAS:

MMF:

PPAM:

HAI:

RFQ:

PALE:

PGIG:

PVP:

RAY:

MJV:

TOD:

SARA:

SETR:

LAV:

TMU:

ETF:

DNM:

MDO:	100011174(BCS1L)

GAS:

SHR:

AFZ:

PCW:

OAA:

GGA:	424212(BCS1L)

PCOC:

MGP:

CJO:

TPAI:

LMUT:

NMEL:

APLA:

ACYG:

CATA:

AFUL:

TGU:

LSR:

SCAN:

PMOA:

OTC:

PRUF:

GFR:

FAB:

OMA:

PHI:

PMAJ:

CCAE:

CCW:

CBRC:

ETL:

ZAB:

ACHL:

SVG:

MMEA:

HRT:

FPG:

FCH:

CLV:

EGZ:

NNI:

PCRI:

PLET:

EHS:

PCAO:

ACUN:

TALA:

PADL:

AFOR:

ACHC:

HALD:

HLE:

AGEN:

GCL:

CCRI:

CSTI:

CMAC:

MUI:

BREG:

FGA:

GSTE:

LDI:

MNB:

OHA:

NNT:

SHAB:

DPUB:

PGUU:

ACAR:

CPEA:

AVIT:

CVF:

RTD:

CUCA:

TEO:

BRHI:

AAM:

AROW:

NPD:

TGT:

DNE:

SCAM:

ASN:

AMJ:	102570697(BCS1L)

CPOO:

GGN:

PSS:

CMY:

CCAY:

DCC:

CPIC:

TST:

CABI:

MRV:

ACS:

ASAO:

PVT:

SUND:

PBI:

PMUR:

CTIG:

TSR:

PGUT:

PTEX:

NSS:

VKO:

PMUA:

PRAF:

ZVI:

HCG:

GJA:

STOW:

EMC:

XLA:	380366(bcs1l.L)

XTR:	549619(bcs1l)

NPR:

RTEM:

BBUF:

BGAR:

MUO:

GSH:

DRE:	394157(bcs1l)

SRX:	107714219 107741911

SANH:

107673730

SGH:

107555925

CCAR:

109064884 109088803 109088815

CAUA:

CGIB:

PTET:

LROH:

OMC:

PPRM:

RKG:

MAMB:

CIDE:

MASI:

TROS:

TDW:

MANU:

IPU:

IFU:

PHYP:

SMEO:

TFD:

TVC:

AMEX:

CMAO:

EEE:

CHAR:

TRU:

TFS:

TNG:	GSTEN00029106G001

LCO:

104936008

NCC:	104955626 104955697

TBEN:

CGOB:

PGEO:

GACU:

EMAC:

ELY:

EFO:

PLEP:

SLUC:

ECRA:

ESP:

PFLV:

GAT:

PPUG:

AFB:

CLUM:

PSWI:

MSAM:

SCHU:

CUD:

ALAT:

MZE:

ONL:

OAU:

OLA:

OML:

CSAI:

XMA:

XCO:

XHE:

PRET:

PFOR:

PLAI:

PMEI:

GAF:

PPRL:

CVG:

CTUL:

GMU:

NFU:

KMR:

ALIM:

NWH:

AOCE:

MCEP:

CSEM:

POV:

SSEN:

HHIP:

HSP:

SMAU:

LCF:

SDU:

SLAL:

XGL:

HCQ:

SSCV:

SBIA:

PEE:

PTAO:

BPEC:

MALB:

BSPL:

SJO:

SASA:

106581856(BCS1)

STRU:

OTW:

OMY:

OGO:

ONE:

OKI:

OKE:

SALP:

SNH:

CCLU:

ELS:

SFM:

PKI:

AANG:

LOC:

PSPA:

ARUT:

PSEX:

LCM:

CMK:

RTP:

CPLA:

HOC:

PMRN:

LRJ:

BFO:

BBEL:

CIN:

SCLV:

SPU:

LPIC:

APLC:

AJC:

SKO:	100373593(Bcs1l)

DME:	Dmel_CG4908(Bcs1)

DER:

6543296

DSE:

6611931

DSI:	Dsimw501_GD23665(Dsim_GD23665)

DYA:	Dyak_GE18907

DAN:

DSR:

DPO:

DPE:

DMN:

DWI:

DGR:

DMO:	Dmoj_GI18626

DAZ:

DNV:

DHE:

DVI:

CCAT:

BOD:

BDR:

RZE:

AOQ:

TDA:

MDE:	101895172 131800603 131806963 131806965

SCAC:

106085701

LCQ:

111685091

LSQ:	119611246 119611248

GFS:

ECOE:

CLON:

HIS:

AGA:

ACOZ:

AARA:

AMER:

ASTE:

AFUN:

AMOU:

AALI:

AAG:	110680973 5574412

AALB:

109415992

CQU:	CpipJ_CPIJ013393

CPII:

120426830

CNS:

116352327

BCOO:

119072349 119074626 119080249 119080251

AME:

ACER:

ALAB:

ADR:

AFLR:

BIM:

BBIF:

BVK:

BVAN:

BTER:

BAFF:

BPYO:

BPAS:

FVI:

CCAL:

OBB:

OLG:

MGEN:

NMEA:

CGIG:

SOC:

MPHA:

AEC:

ACEP:

PBAR:

VEM:

HST:

DQU:

CFO:

FEX:

LHU:

PGC:

OBO:

PCF:

PFUC:

VPS:

VCRB:

VVE:

NVI:

CSOL:

TPRE:

LHT:

LBD:

MDL:

CGLO:

FAS:

DAM:

AGIF:

CINS:

VCAN:

CCIN:

DSM:

NPT:

NFB:

NLO:

NVG:

AROA:

TCA:

DPA:

SOY:

AGRG:

ATD:

CSET:

AGB:

LDC:

NVL:

APLN:

PPYR:

OTU:

BMOR:

BMAN:

MSEX:

DPL:	KGM_204429

BANY:

MJU:

NIQ:

VCD:

MCIX:

PMAC:

PPOT:

PXU:

PRAP:

PBX:

PNAP:

ZCE:	119830176 119830273

CCRC:

LSIN:

AAGE:

HAW:

HZE:

TNL:

SLIU:

OFU:

PXY:

PGW:

CFEL:

CCRN:

API:	100162321 100169445

DNX:	107166059 107168560

AGS:	114120869 114128076

RMD:	113550892 113551515

ACOO:

126835010 126839728 126844263

DVT:	126895406 126905949

BTAB:

DCI:

CLEC:

HHAL:

NLU:

HVI:

MQU:

PHU:	Phum_PHUM137330

FOC:

TPAL:

ZNE:

CSEC:

SGRE:

BROR:

IEL:

FCD:	110844062 110849568 110854448 110854449 110854482 110862033 110863633

DPX:	DAPPUDRAFT_300604

DMK:

DPZ:

PVM:

PJA:

PCHN:

PMOO:

HAME:

PCLA:

CQD:

PTRU:

ESN:

MNZ:

HAZT:

EAF:	111698880 111702947

TCF:	131884679 131888818

PPOI:

119096782 119097252

DSV:	119435136 119441360

RSAN:

RMP:

VDE:

VJA:

TUT:	107359060 107371948

CSCU:

PTEP:

ABRU:

UDV:

SDM:

LPOL:

PMEO:

129593535 129594417 129595659 129595667 129597390 129600290 129601334

CEL:	CELE_F54C9.6(bcs-1)

CBR:

CBG_00560

CRQ:	GCK72_004937

NAI:	NECAME_15407

BMY:	BM_BM4351(Bma-bcs-1)

LOA:	LOAG_07266

TSP:	Tsp_03371 Tsp_13180

HRO:	HELRODRAFT_75858

LGI:	LOTGIDRAFT_185574

PVUL:

PCAN:

BGT:

GAE:

HRF:

HRJ:

CRG:

CVN:

CANU:

MYI:

PMAX:

MCAF:

MMER:

RPHI:

DPOL:

OBI:

OSN:	115225556 115231427

LAK:

106166292

SMM:	Smp_083120

SHX:	MS3_00001389(BCS1L_1)

OVI:	T265_10613

EGL:

NVE:

EPA:

ATEN:

ADF:

AMIL:

PDAM:

SPIS:

DGT:

XEN:	124433516 124451306

HSY:

130662540

TAD:	TRIADDRAFT_25447

AQU:

100639781

ALY:

110228681

CRB:	17885098 17885705

CSAT:

104699063 104711630 104711631 104770087 104780925 109133339

EUS:	EUTSA_v10010367mg EUTSA_v10023872mg

BRP:	103841016 103860682 103872670

BNA:	106375147 106442460 106442493

BOE:	106303130 106305218 106311854 106339216

RSZ:	108812162 108839382

THJ:

104824812

CPAP:

110810335 110810417 110820095 110822492

CIT:	102607572 102608161 102608458 102609232 102609517 102611810 102614646 102627619 102628180 102630983 107176527 127901748

CIC:	CICLE_v10003104mg CICLE_v10011614mg CICLE_v10023517mg CICLE_v10025208mg CICLE_v10028304mg CICLE_v10028341mg CICLE_v10028347mg CICLE_v10028551mg CICLE_v10028857mg CICLE_v100301432m CICLE_v10030371mg CICLE_v10031208mg CICLE_v10031520mg CICLE_v10031528mg CICLE_v10031756mg CICLE_v10033307mg

PVY:	116112575 116112845 116112852 116116358 116116376 116116688 116118136 116126472 116133245 116133943 116142183

MINC:

123195845 123197665 123206974 123206988 123206989 123210153 123211254 123214389 123217065 123217952

TCC:	108660716 18589153 18595598 18607743 18607747 18609719 18610782 18610783 18610857 18611857

GRA:	105762871 105770255 105775936 105787482 105788082 105795322 105802462 105803722 105803774 105803775

GAB:	108449934 108459626 108471167 108471959 108472028 108472767 108473396 108477799

HSYR:

120118007 120120073 120121283 120149476 120159529 120159531 120214492

DZI:	111275359 111281682 111285968 111292460 111292728 111299600 111303974 111308629 111317237

EGR:	104419336 104419707 104420545 104422716 104422717 104422719 104422720 104422723 104423953 104448781

GMX:	100776680 100778503 100783574 100787726 100787809 100788270 100788420 100788906 100789094 100789716 100792143 100792584 100796308 100797983 100805212 100819885 100820437

GSJ:	114368530 114375468 114376628 114379845 114380317 114382006 114383796 114387975 114389405 114389420 114400518 114400626 114407825 114410259 114415591 114418283 114420297 114422023

PVU:	PHAVU_002G165800g PHAVU_002G166000g PHAVU_002G166100g PHAVU_003G256600g PHAVU_004G025000g PHAVU_005G042400g PHAVU_006G115600g PHAVU_009G048600g PHAVU_010G116600g PHAVU_011G043100g

VRA:	106754012 106756553 106760959 106762237 106763159 106767789 106775234 106776662 106776663 106777068 106780337

VAR:	108319243 108330899 108334143 108334621 108334807 108335739 108335746 108338840 108341776 108345061

VUN:	114166213 114168568 114169015 114169025 114173997 114174225 114176043 114182754 114183447 114184159 114188779 114195912

VUM:	124822990 124826273 124831372 124831565 124832796 124833319 124833820 124839096 124842805

CCAJ:

109792810 109796982 109800682 109800710 109800923 109801020 109806128 109808729 109811941 109811942 109812475 109817558

APRC:

113849149 113850491 113855501 113855502 113856199 113859175 113863038 113865525 113867893 113869610 113869791

MTR:	11405732 11406855 11407637 11407773 11407775 11411859 11411864 11412855 11416461 11422577 11425695 11430808 11446305 25482136 25482137 25486874

TPRA:

123882141 123883462 123886394 123895067 123895071 123896455 123898795 123904195 123904735 123909211 123910328 123910372 123910373 123921616

CAM:	101489676 101498631 101498887 101503785 101505930 101511087 101512048

PSAT:

127074617 127076112 127081632 127083110 127086217 127096682 127096683 127096686 127120207 127120208 127132081 127134673

LJA:

Lj0g3v0195169.1(Lj0g3v0195169.1) Lj1g3v1032230.1(Lj1g3v1032230.1) Lj2g3v1024160.1(Lj2g3v1024160.1) Lj2g3v1729010.1(Lj2g3v1729010.1) Lj2g3v1729020.1(Lj2g3v1729020.1) Lj3g3v0933420.1(Lj3g3v0933420.1) Lj3g3v1061340.1(Lj3g3v1061340.1) Lj3g3v1061350.1(Lj3g3v1061350.1) Lj3g3v2478860.1(Lj3g3v2478860.1) Lj4g3v0548780.1(Lj4g3v0548780.1) Lj5g3v2300310.1(Lj5g3v2300310.1) Lj6g3v1527000.1(Lj6g3v1527000.1)

ADU:	107458863 107460428 107467334 107471069 107471101 107473036 107476241 107487954 107493080

AIP:	107605861 107610824 107610828 107613970 107621453 107623921 107624126 107625515 107637304 107642908 107642909 107646214

LANG:

109326649 109327045 109328754 109329732 109331625 109344617 109347318 109347957 109350917 109357734 109359667 109361381

PCIN:

129285244 129288574 129296439 129301884 129303194 129315636 129321570

QSA:	O6P43_004535 O6P43_004536 O6P43_004537 O6P43_009041 O6P43_009043 O6P43_011609 O6P43_014958 O6P43_018605 O6P43_024802 O6P43_026618 O6P43_026619 O6P43_026620 O6P43_026622 O6P43_026623 O6P43_027411 O6P43_029176 O6P43_029464 O6P43_030581 O6P43_033670

FVE:	101292542 101301749 101302277 101303104 101303881 101307344 101310167

RCN:	112171769 112172776 112181675 112183709 112184237 112188985 112203221 112203223

PPER:

18771454 18771516 18779647 18780471 18782123 18785150 18786969 18788536

PMUM:

103320879 103325451 103326156 103330202 103330578 103333595 103340124 103340284

PAVI:

110747990 110749667 110752449 110758857 110769576 110770626 110771573 110771576 110773658

PDUL:

117614281 117618602 117623234 117625324 117636449

MDM:	103409009 103416985 103418605 103423043 103431862 103439911 103440308 103442783 103444243 103452216 114820358

MSYL:

126583322 126583644 126589926 126611260 126624973 126629923 126632290

PXB:	103926912 103928489 103932226 103934292 103936737 103943379 103954926

ZJU:	107408462 107415586 107415587 107415588 107428124 107434240 125418132

MNT:	21386234 21388924 21392109

CSAV:

115698512 115698513 115701100 115704632 115715008 115717433 115724466 115724524

CSV:	101204309 101205613 101205839 101208666 101209401 101215623 101218419

CMO:	103482977 103485356 103498027 103500283 103503918

BHJ:	120067028 120069458 120069459 120079543 120081858 120086625 120089788

MCHA:

111005470 111006667 111009128 111012395 111019763

CMAX:

111472967 111478452 111482159 111493065 111497272 111497441

CMOS:

111430202 111441534 111452082 111453806 111463099 111463134

CPEP:

111781413 111781958 111781961 111787753 111790244 111803255 111808446

RCU:	8267100 8275763 8275997 8276861 8279145 8285346 8289321

JCU:	105628807 105628855 105630138 105633832 105639211 105639230 105639231 105641201 105642469 105645523 105645524 105645526 105650324

HBR:	110642729 110644268 110645155 110648587 110657795 110659366 110667265 110669304 110670318 110670361 110670362

MESC:

110601370 110601619 110601842 110601980 110602280 110604286 110616340 110617829 110623894 110625959 110626078 110629959

POP:	112323553 18095006 18095501 18099243 18102145 18109812 7455953 7456363 7472354 7474629 7475159 7479729 7480181 7487192 7489290 7494779

PEU:	105112502 105114707 105126636 105126638 105126706 105128511 105128772 105129272 105129353 105133880 105135347 105135428 105137805 105139071 105139793 105142217 105142235

PALZ:

118030004 118036480 118036481 118045636 118052794 118053212 118053779 118056970 118056974 118056975 118058918 118058920 118063149

JRE:	108980734 108980737 108986998 108989576 108991354 108992867 108993509 109001494 109007553 109012300 109012305

CILL:

122281707 122281708 122289643 122291236 122298442 122302505 122309467 122310917 122311244 122312961 122317027 122317476 122317812

CAVE:

132167956 132170735 132171285 132171754 132171883 132172852 132174608 132174609 132174613 132178483 132179321 132179436 132180856 132180952 132181060 132182571 132189921

QSU:	111984163 111987888 111996888 112003692 112005199 112008895 112011046 112034382

QLO:	115959344 115974378 115976788 115982260 115986931 115988773 115991333 115994041

TWL:	120000427 120000751 120000844 120007905 120014651

VVI:	100241090 100241723 100242191 100246206 100247372 100252443 100252727 100261022 100263212 100266235 109121427 132254745

VRI:	117911441 117921663 117921962 117922088 117924548 117926849 117926984 117927790 117929537 117929983 117929987 117931093

SLY:	101247583 101247855 101250479 101257322 101261461 101265127 101265639

SPEN:

107002792 107010749 107014207 107014809 107017690 107032489

SOT:	102579261 102584520 102585539 102592725 102596396 102600429 102605122

SSTN:

125848404 125853728 125855046 125860243 125866089 125866144 125866840

SDUL:

129876335 129880474 129884840 129896503 129902131

CANN:

107843264 107845651 107866970

LBB:	132608054 132628050 132629050 132641263 132645072

NTA:	107766870 107777233 107777406 107783559 107786408 107790138 107790730 107795112 107798380 107805115 107809561 107820547 107820818

NSY:	104213992 104232292 104238205 104239139 104242597

NTO:	104084611 104089700 104090770 104098718 104099402 104107364 104108476 104109568

NAU:	109205287 109218127 109223693 109228781 109233559

INI:	109146703 109149785 109163836 109165212 109177328 109177329 109188255 109188257

ITR:	116001638 116007253 116010203 116022768 116028085 116028498 116032352

SIND:

105162577 105165764 105165864 105166114 105169662 105169663 105173384

OEU:	111383694 111388216 111399659 111410071 111410073

EGT:	105962997 105965035 105965277

SSPL:

121754730 121775002 121775818 121776266 121789810 121792751

SMIL:

130990183 131005373 131005829 131010512 131010567 131022191

SHIS:

125186405 125217774 125218022 125223649

APAN:

127246245 127255870

HAN:	110868032 110868310 110868311 110868313 110868315 110879244 110904643 110904644 110906179 110908940 110908943 110908944 110908945 110920068 110926373 110941450

ECAD:

122579363 122586931 122601555 122605198

LSV:	111897353 111897364 111897373 111897374 111898003 111901602 111902002 111920638 111920639

CCAV:

112501238 112501699 112515720 112518533 112518829 112523333 112523662 112525536

DCR:	108193581 108195294 108195387 108196243 108200716 108208384 108217639 108218508

CSIN:

114283782 114288634 114298176 114298717 114298750 114305923 114305924 114310327 114311460 114311462 114311463 114314676 114316649 114323620

RVL:	131304744 131310077 131330989

AEW:	130769347 130774507 130775413 130779346 130779347 130779348 130781273

BVG:	104887423 104888200 104895067 104898072 104904323 109135151

SOE:	110783041 110795368 110803065 110804546

CQI:	110685834 110690980 110704426 110704917 110705116 110706386 110707733 110713248 110728342 110735224 110738851

ATRI:

130814864 130818816

MOF:	131156496 131162058 131165056

NNU:	104586579 104587469 104597594 104601811 104603159

MING:

122061546 122061609 122064590 122064591 122064593

TSS:	122642082 122662886

PSOM:

113293259 113295769 113295775 113299307 113299328 113299329 113299331 113299334 113332666 113349612 113357483 113358584 113358586 113360606 113360607

OSA:

4339775

DOSA:

Os05t0588900-01(Os05g0588900) Os09t0445700-00(Os09g0445700)

OBR:

102721080

OGL:

127773046

BDI:	100824372 100836199

ATS:	109738210 109742677 109742687 109742688

TDC:	119294579 119300285 119301763 119309855 119310404 119313376 119349787 119349788 119356795

TAES:

123057225 123070319 123107128 123108120 123112150 123121664 123125858 123149151 123149156 123149158 123161357 123161367 123178477 123183331

TUA:	125506204 125509503 125531843 125531866 125531875 125540740

LPER:

127301765 127327846 127327848 127327854 127329462

LRD:	124648148 124649227 124649260 124649266 124651173 124671398

SBI:	8065309 8065310 8081014

ZMA:	100278733 100281434

SITA:

101772252 101772653

SVS:

117848034

PVIR:

120664449 120664453 120700477 120700479

PHAI:

112884134

PDA:	103701965 103708667

EGU:	105041886 105056311 105056354

MUS:

103999190

ZOF:	122028214 122030498 122031075 122033609

DCT:

110110505

PEQ:	110026841 110027603

AOF:	109829018 109834774 109843890 109845701

MSIN:

131227576 131230740

NCOL:

116246712 116250754 116266799

ATR:	18434086 18435619 18435624 18435625 18437255 18437256 18439348 18443660

PPP:	112272747 112282920 112285474 112289230

CRE:	CHLRE_05g234661v5

MNG:

MNEG_0052

OLU:	OSTLU_32455

OTA:	OT_ostta07g00590

MIS:	MICPUN_99023

MPP:	MICPUCDRAFT_50635(JGI:MicpuC2_50635)

CCP:	CHC_T00006054001 CHC_T00006134001 CHC_T00007058001 CHC_T00007066001

SCE:	YDR375C(BCS1)

SEUB:

DI49_0552

SPAO:

SPAR_D05640

AGO:	AGOS_ACR200C

ERC:

Ecym_4643

KLA:	KLLA0_E02487g

KMX:	KLMA_20605

LTH:	KLTH0F15730g

VPO:	Kpol_1062p18

ZRO:	ZYRO0G01716g

CGR:	CAGL0A02992g

NCS:	NCAS_0H02120(NCAS0H02120)

NDI:	NDAI_0C01530(NDAI0C01530)

TPF:	TPHA_0E01660(TPHA0E01660)

TBL:	TBLA_0A02720(TBLA0A02720)

TGB:	HG536_0F02670

TDL:	TDEL_0D02530(TDEL0D02530)

KAF:	KAFR_0D05090(KAFR0D05090)

KNG:	KNAG_0B04170(KNAG0B04170)

ZMK:	HG535_0C04310

PPA:	PAS_chr3_0116

DHA:	DEHA2G10516g

PIC:	PICST_47614

PGU:	PGUG_04778

SPAA:

SPAPADRAFT_59502

LEL:	PVL30_002680(BCS1)

CAL:	CAALFM_CR05970CA(CaO19.458)

CTP:	CTRG_00657

COT:	CORT_0D05260

CDU:	CD36_31350

CTEN:

CANTEDRAFT_111981

YLI:	YALI0D03509g

CLU:	CLUG_03609

CLUS:

A9F13_01g05522

CAUR:

CJI96_0003437

SLB:	AWJ20_5248(BCS1)

PKZ:	C5L36_0C11030

BBRX:

BRETT_000146

OPA:	HPODL_00956

SLUD:

SCDLUD_003229

NCR:	NCU03231 NCU03921

NTE:	NEUTE1DRAFT124799(NEUTE1DRAFT_124799) NEUTE1DRAFT72346(NEUTE1DRAFT_72346)

SMP:	SMAC_02951 SMAC_06339

PAN:	PODANSg09459 PODANSg3026 PODANSg9009

PBEL:

QC761_102170(BCS1) QC761_211510 QC761_408300

PPSD:

QC762_102170(BCS1) QC762_211510 QC762_408300

PPSP:

QC763_102170(BCS1) QC763_211510 QC763_408300

PPSA:

QC764_102170(BCS1) QC764_211510 QC764_408300

TTT:	THITE_2108409 THITE_2109894 THITE_2120356 THITE_2120877

MTM:	MYCTH_2112991 MYCTH_2131445 MYCTH_2302213 MYCTH_2303320 MYCTH_2306553

CTHR:

CTHT_0043750 CTHT_0056430 CTHT_0061310

MGR:	MGG_02058 MGG_04018 MGG_10383 MGG_15496

PPEI:

PpBr36_00024 PpBr36_00115 PpBr36_04495 PpBr36_05765 PpBr36_05823 PpBr36_08114 PpBr36_10371 PpBr36_11036 PpBr36_11184 PpBr36_11264 PpBr36_11327

PGRI:

PgNI_01123 PgNI_02721 PgNI_05018 PgNI_05108 PgNI_06899 PgNI_08217 PgNI_12226 PgNI_12266 PgNI_12271

TMN:	UCRPA7_2017 UCRPA7_4687 UCRPA7_6887

SSCK:

SPSK_00784 SPSK_03063

FGR:	FGSG_02212 FGSG_02769 FGSG_05889 FGSG_07544 FGSG_09267

FPU:	FPSE_00225 FPSE_09659 FPSE_10319 FPSE_10591 FPSE_12249

FPOA:

FPOAC1_002358 FPOAC1_002908 FPOAC1_008852 FPOAC1_012430

FVN:	FVRRES_02601 FVRRES_03225 FVRRES_09466 FVRRES_12372 FVRRES_13513

FVR:	FVEG_01652 FVEG_03843 FVEG_04549 FVEG_07241 FVEG_08925 FVEG_12753

FOX:	FOXG_02822 FOXG_04127 FOXG_05975 FOXG_07622 FOXG_10276 FOXG_12511 FOXG_14028 FOXG_15422

NHE:	NECHADRAFT_1988 NECHADRAFT_49155 NECHADRAFT_56027 NECHADRAFT_62313 NECHADRAFT_63271 NECHADRAFT_91444 NECHADRAFT_94191

FFC:	NCS54_00304600 NCS54_00317200 NCS54_00790800 NCS54_01099100 NCS54_01175700

FKR:	NCS57_00300000 NCS57_00336000 NCS57_00346800 NCS57_00670600 NCS57_00833400 NCS57_01166500

FMU:	J7337_003852 J7337_005466 J7337_006590 J7337_010745

TRE:	TRIREDRAFT_56396 TRIREDRAFT_60378 TRIREDRAFT_68571

TRR:	M419DRAFT_12213 M419DRAFT_127450 M419DRAFT_50927

MAW:	MAC_06044 MAC_08267 MAC_08873

MAJ:	MAA_00280 MAA_01276 MAA_02020 MAA_03253 MAA_06175 MAA_09964

PCHM:

VFPPC_01684 VFPPC_05458 VFPPC_06174

CMT:	CCM_00312 CCM_00737 CCM_04955 CCM_07856 CCM_09618

AMUS:

LMH87_000553 LMH87_001017 LMH87_003097 LMH87_007615

PLJ:	VFPFJ_03168 VFPFJ_04093 VFPFJ_06594 VFPFJ_11410

PTKZ:

JDV02_001394 JDV02_004433 JDV02_005425(BCS1)

VAL:	VDBG_04049 VDBG_08199 VDBG_08974 VDBG_09104

VDA:	VDAG_01279 VDAG_02425 VDAG_05219 VDAG_07252 VDAG_07853 VDAG_10092

CFJ:	CFIO01_00929 CFIO01_02103 CFIO01_02317 CFIO01_06985 CFIO01_10139

CLUP:

CLUP02_07728 CLUP02_11704 CLUP02_12097 CLUP02_16493

CHIG:

CH63R_04054 CH63R_09751 CH63R_10605 CH63R_11211 CH63R_11525 CH63R_14149

SAPO:

SAPIO_CDS5453

ELA:	UCREL1_4431 UCREL1_470 UCREL1_6784 UCREL1_8674 UCREL1_9169 UCREL1_9428

PFY:	PFICI_00502 PFICI_04801 PFICI_08057 PFICI_14167 PFICI_15067

SSL:	SS1G_01232 SS1G_07866 SS1G_09686

BFU:	BCIN_07g05710 BCIN_11g01350(Bcbcs1) BCIN_15g01200

MBE:	MBM_00289 MBM_04271 MBM_05269 MBM_06925

PSCO:

LY89DRAFT_678561 LY89DRAFT_683146 LY89DRAFT_691695

GLZ:	GLAREA_06003 GLAREA_08666 GLAREA_11432

ANI:	ANIA_03131 ANIA_07549

AFM:	AFUA_2G14760 AFUA_3G13000

ACT:	ACLA_040740 ACLA_072720

NFI:	NFIA_064320 NFIA_089990

AOR:	AO090012000830 AO090026000803

ANG:	An02g08900 An15g03540

AFV:	AFLA_002545 AFLA_005485 AFLA_007616 AFLA_010014

ALUC:

AKAW2_10757A AKAW2_60373A

ACHE:

ACHE_20243A ACHE_31326S

APUU:

APUU_30381S APUU_80408A

PCS:	N7525_002311 N7525_002638

PDP:	PDIP_04100 PDIP_05600 PDIP_23210 PDIP_75210

POU:	POX_b02867 POX_c04563 POX_h09711

TMF:	EYB26_000759 EYB26_004931 EYB26_005072

TRG:	TRUGW13939_02344 TRUGW13939_08793 TRUGW13939_08803 TRUGW13939_10123 TRUGW13939_10157 TRUGW13939_10343

CIM:	CIMG_03460

CPW:	CPC735_007720 CPC735_054090

URE:	UREG_06573 UREG_07271

PBL:	PAAG_07167

PBN:	PADG_00929

ABE:	ARB_02245 ARB_05203 ARB_06889

TVE:	TRV_03619 TRV_05949 TRV_07953

BGH:	BDBG_00758 BDBG_02928 BDBG_08151 BDBG_16825

PNO:	SNOG_03232 SNOG_05174(SNOG_05173) SNOG_08322 SNOG_15480

PTE:	PTT_09336 PTT_14658 PTT_15640 PTT_18203 PTT_18957 PTT_19104

BZE:	COCCADRAFT_23237 COCCADRAFT_34683 COCCADRAFT_5582

BSC:	COCSADRAFT_163326 COCSADRAFT_182878 COCSADRAFT_94323

BOR:	COCMIDRAFT_3845 COCMIDRAFT_6825 COCMIDRAFT_91607

AALT:

CC77DRAFT_1098237 CC77DRAFT_555241 CC77DRAFT_931733 CC77DRAFT_982004 CC77DRAFT_993546

ARAB:

EKO05_0004698 EKO05_0010030

ZTR:	MYCGRDRAFT_110524 MYCGRDRAFT_30173 MYCGRDRAFT_67763 MYCGRDRAFT_77213

PFJ:	MYCFIDRAFT_125208 MYCFIDRAFT_138975 MYCFIDRAFT_146481 MYCFIDRAFT_39750

FFU:	CLAFUR5_05496 CLAFUR5_08611 CLAFUR5_10257

CBET:

CB0940_00527 CB0940_05938 CB0940_09888

BCOM:

BAUCODRAFT_112384 BAUCODRAFT_261705 BAUCODRAFT_56533

NPA:	UCRNP2_211 UCRNP2_6997

TML:	GSTUM_00002227001 GSTUM_00004552001 GSTUM_00009605001

SPO:	SPAC644.07

SOM:	SOMG_03525(bcs1)

CNE:

CNC04110

CNB:

CNBC3080

CNG:	CNAG_02792

CGI:	CGB_C6210W

CDEU:

CNBG_3447

TMS:	TREMEDRAFT_27280 TREMEDRAFT_39838 TREMEDRAFT_62261 TREMEDRAFT_73837

TASA:

A1Q1_01633

CCAC:

CcaHIS019_0403290(BCS1)

PPL:	POSPLDRAFT_24229

TVS:	TRAVEDRAFT_160965 TRAVEDRAFT_167458 TRAVEDRAFT_168153 TRAVEDRAFT_27987 TRAVEDRAFT_47707

DSQ:	DICSQDRAFT_123961 DICSQDRAFT_132726 DICSQDRAFT_139690 DICSQDRAFT_140557 DICSQDRAFT_69964

PCO:	PHACADRAFT_143806 PHACADRAFT_258919 PHACADRAFT_263985

SHS:	STEHIDRAFT_118952 STEHIDRAFT_157096 STEHIDRAFT_51737 STEHIDRAFT_57885 STEHIDRAFT_62902 STEHIDRAFT_64826 STEHIDRAFT_87633

HIR:	HETIRDRAFT_109007 HETIRDRAFT_155952 HETIRDRAFT_172230 HETIRDRAFT_58075 HETIRDRAFT_60257 HETIRDRAFT_63656

PSQ:	PUNSTDRAFT_104854 PUNSTDRAFT_106413 PUNSTDRAFT_127854 PUNSTDRAFT_50243 PUNSTDRAFT_75035 PUNSTDRAFT_86846

ADL:	AURDEDRAFT_112830 AURDEDRAFT_113059 AURDEDRAFT_145769 AURDEDRAFT_182372 AURDEDRAFT_77515 AURDEDRAFT_84193 AURDEDRAFT_90038

FME:	FOMMEDRAFT_112889 FOMMEDRAFT_18207 FOMMEDRAFT_22463 FOMMEDRAFT_86815

GTR:	GLOTRDRAFT_110317 GLOTRDRAFT_126816 GLOTRDRAFT_129183 GLOTRDRAFT_39873 GLOTRDRAFT_48634 GLOTRDRAFT_48749 GLOTRDRAFT_74861 GLOTRDRAFT_74864

RSX:	RhiXN_04678 RhiXN_04726 RhiXN_06627 RhiXN_09617 RhiXN_10051

LBC:	LACBIDRAFT_187928 LACBIDRAFT_244188 LACBIDRAFT_291958 LACBIDRAFT_318752 LACBIDRAFT_396180

CCI:	CC1G_00820 CC1G_00842 CC1G_01181 CC1G_01608 CC1G_02392 CC1G_04010 CC1G_09806 CC1G_11035 CC1G_11036

ABP:	AGABI1DRAFT108111(AGABI1DRAFT_108111) AGABI1DRAFT108687(AGABI1DRAFT_108687) AGABI1DRAFT116485(AGABI1DRAFT_116485) AGABI1DRAFT34350(AGABI1DRAFT_34350) AGABI1DRAFT36444(AGABI1DRAFT_36444) AGABI1DRAFT62968(AGABI1DRAFT_62968)

ABV:	AGABI2DRAFT180594(AGABI2DRAFT_180594) AGABI2DRAFT180828(AGABI2DRAFT_180828) AGABI2DRAFT196029(AGABI2DRAFT_196029) AGABI2DRAFT210088(AGABI2DRAFT_210088) AGABI2DRAFT63145(AGABI2DRAFT_63145) AGABI2DRAFT70517(AGABI2DRAFT_70517)

PCUB:

JR316_0003164 JR316_0007845

MPR:	MPER_04883 MPER_12612 MPER_15830

MRR:	Moror_10129 Moror_1040 Moror_14311 Moror_16541 Moror_2622 Moror_5007

E1B28_000029 E1B28_002070 E1B28_008974 E1B28_011207 E1B28_011416 E1B28_011830

SCM:	SCHCO_01186842(SCHCODRAFT_01186842) SCHCO_02620364(SCHCODRAFT_02620364) SCHCO_02634784(SCHCODRAFT_02634784) SCHCO_02691288(SCHCODRAFT_02691288)

CPUT:

CONPUDRAFT_112319 CONPUDRAFT_140136 CONPUDRAFT_148000 CONPUDRAFT_166050 CONPUDRAFT_169497 CONPUDRAFT_169502 CONPUDRAFT_81184 CONPUDRAFT_85412 CONPUDRAFT_97799

SLA:	SERLADRAFT_364293 SERLADRAFT_448902 SERLADRAFT_473328

WSE:	WALSEDRAFT_38133 WALSEDRAFT_59685

WIC:	J056_004291

UMA:	UMAG_04201

PFP:	PFL1_04409 PFL1_06072

SGRA:

MGL:

MRT:

MSYM:

PGR:	PGTG_19037

PTRC:

PtA15_8A430

PSTR:

Pst134EA_015828

MLR:	MELLADRAFT_65472

SRE:	PTSG_09789

DDI:	DDB_G0286765 DDB_G0289135(bcs1lA) DDB_G0291910(bcs1lB)

DPP:	DICPUDRAFT_28373 DICPUDRAFT_31265 DICPUDRAFT_49377

DFA:	DFA_01976(bcs1lB) DFA_03149 DFA_03225(bcs1lA)

ACAN:

ACA1_040870 ACA1_107600 ACA1_140770 ACA1_175540 ACA1_246080 ACA1_289200 ACA1_291670 ACA1_291780

PFA:	PF3D7_0603200

PFD:	PFDG_00238

PFH:	PFHG_01199

PREI:

PRSY57_0601800

PGAB:

PGSY75_0603200

PYO:	PY17X_0103600

PCB:	PCHAS_0102700

PBE:	PBANKA_0102000

PVV:	PVVCY_0100340

PKN:	PKNH_1147500

PVX:	PVX_113325

PCY:	PCYB_115320

PMAL:

PMUG01_11059600

PREL:

PRELSG_1145100

BMIC:

BMR1_02g00285

SMIN:

v1.2.026380.t1(symbB.v1.2.026380.t1)

AAF:	AURANDRAFT_30024 AURANDRAFT_5693 AURANDRAFT_5728 AURANDRAFT_62882

PSOJ:

PHYSODRAFT_474234 PHYSODRAFT_474654 PHYSODRAFT_475367 PHYSODRAFT_539927 PHYSODRAFT_551868 PHYSODRAFT_554980

SPAR:

SPRG_09317

EHX:	EMIHUDRAFT_104465 EMIHUDRAFT_212353 EMIHUDRAFT_369425 EMIHUDRAFT_41925 EMIHUDRAFT_66523 EMIHUDRAFT_68211 EMIHUDRAFT_68829 EMIHUDRAFT_74848 EMIHUDRAFT_77639 EMIHUDRAFT_96085 EMIHUDRAFT_96568

GTT:	GUITHDRAFT_111783 GUITHDRAFT_153155 GUITHDRAFT_74509 GUITHDRAFT_86537

TBR:	Tb927.8.3580

TBG:	TbgDal_VIII3290

TCR:	505945.50 509553.20

LMA:	LMJF_34_1330

LIF:	LINJ_34_1440

LDO:	LDBPK_341440

LMI:	LMXM_33_1330

LBZ:	LBRM_20_1360

LPAN:

LPMP_201420

NGR:	NAEGRDRAFT_2052 NAEGRDRAFT_3835 NAEGRDRAFT_59933 NAEGRDRAFT_70080 NAEGRDRAFT_70508 NAEGRDRAFT_72457

OTD:	J1M35_08860

HPSE:

HPF_17785(yjoB)

MBRY:

MPAR:

MALU:

BHAN:

CMP:	Cha6605_4543

DGO:	DGo_CA2897

DSW:	QR90_16245

DFC:

DFI_01405

DEIN:

DAAJ005_02450

DGA:	DEGR_30160

DTAE:

LAJ19_12070

LRS:	PX52LOC_05939

TSPH:

KIH39_04860

PBOR:

BSF38_05768(yjoB)

AGV:	OJF2_38590(yjoB)

ABA:	Acid345_2241

» show all

Reference

PMID:19162478

Authors

Blazquez A, Gil-Borlado MC, Moran M, Verdu A, Cazorla-Calleja MR, Martin MA, Arenas J, Ugalde C

Title

Infantile mitochondrial encephalomyopathy with unusual phenotype caused by a novel BCS1L mutation in an isolated complex III-deficient patient.

Journal

Neuromuscul Disord 19:143-6 (2009)
DOI:10.1016/j.nmd.2008.11.016

Sequence

[hsa:617]

Reference

PMID:18628306

Authors

Tamai S, Iida H, Yokota S, Sayano T, Kiguchiya S, Ishihara N, Hayashi J, Mihara K, Oka T

Title

Characterization of the mitochondrial protein LETM1, which maintains the mitochondrial tubular shapes and interacts with the AAA-ATPase BCS1L.

Journal

J Cell Sci 121:2588-600 (2008)
DOI:10.1242/jcs.026625

Sequence

[hsa:617]

LinkDB

DBGET integrated database retrieval system